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Dofetilide affects KCNH2
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Dofetilide inhibits KCNH2.
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"It should be mentioned that cisapride, dofetilide, and sotalol directly inhibit hERG channel activity whereas quinidine decreases the surface expression of hERG channels by suppressing hERG channel translocation to cell membrane surface XREF_BIBR."
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"In addition to vanoxerine we profiled one non torsadogenic MICE comparator verapamil, one torsadogenic MICE comparator bepridil and the selective hERG blocker dofetilide."
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"We identified a lower than reported EC 50 for the hERG blocker dofetilide, and sotalol (Peng, Lacerda, Kirsch, Brown, & Bruening-Wright) as well as for the Na + channel blocker flecainide."
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"Protocol 2 was applied and these cells showed no peak in their inward current, i.e. no HERG currents (n = 3); dofetilide blocks HERG current immediately when applied to the inside of the cell and when HERG channels have been opened by holding the cell at 0 mV.In a second group of SHSY5Y cells, -50 mV was applied to the patch pipette before and during the establishment of the whole-cell recording configuration and cells were subsequently held at -60 mV."
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"IC 50 variability (25/75 percentiles) differed for drugs and currents (e.g., 10.4-fold for dofetilide block of hERG current and 4-fold for mexiletine block of hNav1.5 current)."
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"HERG channel inhibition by dofetilide and its derivatives."
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"However, it is not yet proven whether dofetilide (blocker of the HERG like current) affects hypoxia induced depolarization and [Ca 2+] c."
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"Of note, the similar levels of hERG potassium channel block induced by 2-3 nM dofetilide and 6.9 muM ranolazine (approximately 52%) induced> 200 ms of APDc and FPDc prolongation and multiple arrhythmic events in dofetilide treated cells, but only APDc and FPDc prolongation (< 150 ms) without arrhythmias in ranolazine treated cells."
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"Dofetilide, cisapride, sotalol, terfenadine and verapamil blocked hERG channels at 37degreesC with an IC50 of 7nM, 18nM, 343muM, 165nM and 214nM, respectively."
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"Verapamil antagonized dofetilide block of HERG channels, which suggests that they may share a common binding site."
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"Thus, time series images were acquired for 20 s at 33 Hz to provide improved signal to noise as well as recording duration, and coupled with an automated image analysis to determine the effect of the hERG blockers dofetilide, E-4031 and sotalol."
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"Many of the hERG blockers including dofetilide contain an ionizable basic aliphatic amine."
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"Neither verapamil nor dofetilide inhibited trafficking of wild type hERG."
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"Novel High-Throughput Quantitation of Potent hERG Blocker Dofetilide in Human Plasma by Liquid Chromatography Tandem Mass Spectrometry : Application in a Phase 1 ECG Biomarker Validation Study."
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"This conclusion agrees with the experimental finding that application of the hERG antagonist dofetilide initiates prolonged depolarisations [XREF_BIBR]."
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"Acidification markedly potentiated dofetilide blockade of the HERG channels but weakened the inhibitory effects of quinidine and azimilide."
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"A second, selective hERG antagonist Dofetilide [XREF_BIBR] (at 1muM) produced similar bradycardia in hearts from wt flies, also characterized by significantly prolonged diastolic intervals and not observed in sei mutants (XREF_FIG)."
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"HERG channel inhibition by dofetilide and derivatives was studied in HEK293 cell lines stably expressing hERG channels using an automated planar patch system (see Methods)."
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"15 This effect was inhibited by the hERG1 blocker dofetilide."
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"Amiodarone, azimilide, dofetilide, quinidine and sotalol all produced a dose dependent inhibition of HERG current."
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"This contrasts with other hERG blockers, such as dofetilide, that do not prevent the channel from closing and therefore remain bound when the membrane is polarized."
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"All of the selected compounds, at both 10 and 50muM, significantly increased the dissociation of [3 H] dofetilide from the channel by 29-84% (XREF_SUPPLEMENTARY) implying their negative allosteric modulation of the channel inhibition by hERG blockers like dofetilide."
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"In a study on dofetilide induced hERG blockade, it was reported that a blockade of 10% was associated with a 20-ms [95% confidence interval (CI) 12-32] increase in QT interval [XREF_BIBR]."
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"Dofetilide and cisapride acutely inhibit hERG current."
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"Mean open time was 3.2 ms and closed times were 1.0 and 26 ms. In excised macro patches, HERG currents were blocked by the class III antiarrhythmic drug dofetilide, with an IC50 of 35 nmol/L."
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"When expressed heterologously, the HERG channel, like cardiac I Kr current, is inhibited by the methanesulfonanilide drugs, E-4031 and dofetilide."
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"Application of 10muM dofetilide for 10min caused complete inhibition of both the chimaera and the hERG channel (XREF_FIG)."
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"Dofetilide (n = 7), which inhibited hERG current with an IC 50 of 29nM, concentration-dependently prolonged APD in isolated Purkinje fibres, increased triangulation of the action potential and elicited early after-depolarizations starting at a concentration of 0.01 muM."
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"Dofetilide, a class III anti-arrhythmic drug is a potent blocker of hERG and is widely used to distinguish hERG currents from other currents XREF_BIBR XREF_BIBR."
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"These properties are compared with four known HERG channel blockers including verapamil, cisapride, ketoconazole and dofetilide in the XREF_TABLE."
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"Both DC031050 and dofetilide potently inhibited hERG currents with IC (50) values of 2.3 +/- 1.0 and 17.9 +/- 1.2 nmol/L, respectively."
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"While nonclinical studies have suggested that late sodium current block can reduce dispersion of repolarization from hERG block, we observed that ranolazine still had a dose dependent relationship with T wave morphology, in some cases having greater T wave morphology changes at equivalent amounts of QTc prolongation compa red with the pure hERG blocker dofetilide."
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"Drugs illustrating this could include verapamil (hERG + calcium block), ranolazine (hERG + late sodium block), and some of the human immunodeficiency virus (HIV) protease inhibitors such as lopinavir and ritonavir, which block hERG, late sodium, and calcium.19 Amiodarone and its metabolite cause potent hERG block and QTc prolongation, often> 60-90 ms; however, it has been associated with a low risk of TdP despite its profound effects on repolarization, probably because it also blocks both late sodium and calcium currents.19 Thus, late sodium and calcium block shorten the action potential duration of ventricular cells20 (and QTc13, 14, 15); and, in the presence of QTc prolongation, blockage of these inward currents can prevent the initiation of TdP.21 Other evidence of the importance of late sodium current block in preventing TdP comes from a canine model of TdP, where coadministration of mexiletine, a late sodium current blocker, reduced QTc prolongation and the number of TdP events associated with sotalol, a predominant hERG blocker.16 In addition, previous clinical studies have demonstrated that mexiletine can mitigate QTc prolongation caused by the strong hERG blocker quinidine.13, 14, 15 This has been confirmed in recent clinical studies demonstrating that late sodium current blockers (mexiletine, lidocaine) can reduce drug induced QTc prolongation caused by the selective hERG blocker dofetilide,22 and also that mexiletine can mitigate recurrent TdP caused by the acquired long QT syndrome.18 Because there is now a comprehensive understanding of the ionic currents that play a role in QTc prolongation and the development of TdP, the CiPA initiative proposes a new mechanistic, model informed approach to cardiac safety assessment of new drugs."
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"Under this paradigm, it will be important to differentiate QTc prolonging drugs with balanced ion channel effects, such as ranolazine (i.e. hERG potassium channel and late sodium current block), that are not associated with torsade from selective hERG potassium channel blockers, such as dofetilide, that are associated with torsade."
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"Our data demonstrates that hERG blockers such as dofetilide and further high risk categorized compounds prolong the field potential duration."
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"Our results confirm that in SHSY5Y cells dofetilide is unable to block HERG when the channels are closed."
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"For dofetilide the selective block of hERG accounts for the proarrhythmia markers we observed experimentally and in simulations and by extension the drug 's torsadogenicity."
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"For the selective hERG blockers dofetilide and sotalol, simulation predictions of AP prolongation and repolarization abnormality occurrence showed overall good agreement with experiments."
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"In contrast, dofetilide blocked HERG currents in a voltage- and time independent manner under the steady state because of very slow unblocking at negative potentials, which also caused frequency independent block."
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"In order to test the hypothesis that determinants of hERG activators might interact with hERG blockers, we mutated F557 and analysed the inhibition of potassium currents through mutant F557L by six " gold standard " hERG blockers dofetilide, haloperidol, terfenadine, astemizole, cisapride and amiodarone."
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"The HERG like current was blocked by dofetilide (DOF) in a concentration dependent manner (IC (50) = 13 +/- 4 nM, mean +/- SE) and high concentrations of Ba (2+) (1 and 10 mM)."
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"Model studies reproduced this feature in studies of hERG blockers such as dofetilide, KN-93 and other common high-affinity blockers (Durdagi etal."
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"Dofetilide (0.3 microM) inhibited HERG tail current by 34% +/- 3% and 1% +/- 2% at extracellular pH 7.4 and 6.2, respectively."
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"This latter point was subsequently confirmed through PK/pharmacodynamic modeling with the selective hERG blocker dofetilide."
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"With the use of inside-out macropatches from oocytes, however, higher affinity dofetilide block of HERG current has been obtained (IC 50 35 nM, Kiehn et al., 1996)."
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"Dofetilide, a class III antiarrhythmic drug with high potency and specificity for I Kr [5], inhibited HERG current with an IC 50 value of 1.53 x10 -8 mol/l."
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"These results confirm that dofetilide can not block HERG channels while they are held closed at -60 mV."
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"Imipramine a known Eag blocker induces apoptosis in acute myeloid leukaemia cells via the caspase-3 activation [XREF_BIBR] while it has been shown that HERG expressing cells are more sensitive to apoptosis induced by hydrogen peroxide, with reversal of effect on blocking with a HERG blocker dofetilide [XREF_BIBR]."
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"Dofetilide blocked hERG current with an IC 50 of 29nM."
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"XREF_FIG shows that dofetilide inhibited hERG current with an IC 50 of 29nm, markedly prolonged APD in isolated Purkinje fibres and largely prolonged APD and QT and elicited TdP in isolated hearts (XREF_FIG)."
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"Cells prepared from normal cultures and following cryopreservation were compared with regard to time course of Rb+ efflux response at different concentrations of KCl, overall cell morphology, signal-to noise assay window, assay robustness, and 50% inhibitory concentration (IC50) of the hERG blocker dofetilide."
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"In one simulation study, only a 10% hERG blockade by dofetilide corresponded to a QT prolongation of 20ms [95% confidence interval (CI) : 12-32ms] (Jonker et al., 2005)."
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"We recently developed a detailed kinetically based model of the hERG blocker dofetilide by extending the consensus five-state Markov chain model that includes three closed states (C 3, C 2 and C 1), a conducting open state and (O) an inactivation state (I) [XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR]."
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"This was measured by radioligand binding assays using the H-3 labeled class III antiarrhythmic drug and potent hERG blocker dofetilide together with HEK-293 cell membranes."
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"Dofetilide completely blocked the HERG current, leaving only a small plateau current and caused a significant reduction in peak current (control =-737+/-107 pA; after dofetilide =-163+/-43 pA, mean +/-SEM (n = 3); P < 0.05)."
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"Though majority of highly potent hERG blockers including dofetilide, astemizole, terfenadine, and cisapride, show from 2 to 70-fold higher affinity for the inactivated state than to the open conformational state of the channel."
Dofetilide inhibits KCNH2-S613C. 2 / 2
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"HERG S613C with thiol groups in the reduced state could be completely blocked by 1 muM dofetilide."
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"As illustrated in Fig. 4A (peak tail current amplitudes are plotted as a function of time), HERG S613C with thiol groups in the reduced state could be completely blocked by 1 muM dofetilide."
Dofetilide inhibits KCNH2-S631C. 1 / 1
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"Under identical recording conditions (i.e. thiol groups of Cys 631 in the reduced state), it was found that 1 muM of terfenadine and dofetilide also completely block HERG S631C channels, as measured on peak tail current amplitudes (n = 4 each)."
Dofetilide inhibits KCNH2-F656V. 1 / 1
| 1
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"For example, Lees-Miller et al. reported the IC 50 for dofetilide block of hERG F656V to be ~ 120-fold that of WT XREF_BIBR, whilst Mitcheson et al. reported values of 650-fold and 94-fold WT respectively, for F656A and Y652A mutations XREF_BIBR."
Dofetilide binds KCNH2.
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"Molecular determinant of high-affinity dofetilide binding to HERG1 expressed in Xenopus oocytes : involvement of S6 sites."
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"Similar to female predominance of arrhythmia in the acquired setting, which suggests interactions between hERG, dofetilide and oestradiol, the female predominance of inherited arrhythmia linked the the G604S mutations, suggests that oestradiol may differentially interact with the mutant hERG channel compared to WT."
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"High-affinity dofetilide binding to hERG expressed in Xenopus oocytes involves Phe656 residue."
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"Interestingly, WAY-123,398, which did not inhibit [3 H] dofetilide binding to whole HEK293 cells (Finlayson et al., 2001b), reduced [3 H] dofetilide binding to HERG membranes, although not completely."
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"GZ-11610-induced inhibition of [3 H] dofetilide binding to hERG channels assessed potential cardiotoxicity."
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"Utilizing medicinal chemistry first principles (e.g., introducing rigidity, lowering cLogD) a new benzthiazole series was designed, congeners of 1-3, which led to compounds 7a, 7c, 12a-d which exhibited LTA (4) H IC (50) = 3-6 nM and hERG Dofetilide Binding IC (50) = 8.9->> 10 muM."
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"[3 H] dofetilide binding to HERG transfected membranes was performed in a sodium buffer without bovine serum albumin, as for whole cell studies (Finlayson et al., 2001b)."
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"In this study, we show that [3 H] dofetilide binding to HERG transfected membranes is inhibited by antiarrhythmics and structurally unrelated compounds known to prolong the QT interval in man.Human embryonic kidney (HEK293) cells stably expressing HERG (Zhou et al., 1998) were maintained in culture and membranes prepared as described previously (Finlayson et al., 2001a)."
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"The method for determining [3 H] dofetilide binding to hERG protein expressed by the cell membranes was described previously."
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"In addition, [3 H] dofetilide binding to HERG membranes was also reduced in a concentration dependent manner by the antipsychotics pimozide (K i = 70.6 +/-11.8 nM, n H = 0.89 +/-0.12, n = 4) and haloperidol (K i = 549 +/-83.6 nM, n H = 0.75 +/-0.07, n = 4), and by the antihistamine terfenadine (K i = 381 +/-60.0 nM, n H = 0.76 +/-0.14, n = 4), all of which cause QT prolongation (Kang et al., 2000; Vandenberg et al., 2001)."
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"Also, GZ-11610 inhibited [3 H] dofetilide binding to hERG channels expressed on HEK-293 cell membranes, with a Ki of 9.50 muM and an Imax of> 80% (XREF_FIG)."
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"[3H] dofetilide binding to HERG transfected membranes : a potential high throughput preclinical screen."
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"Evaluation of GZ-793A for potential cardiac liabilities revealed that GZ-793A inhibited with high affinity (IC 50 = 0.81 +/- 0.11 muM) [3 H] dofetilide binding to hERG channels expressed by HEK-293 cells (XREF_FIG)."
Dofetilide binds KCNH2 and 10e. 1 / 1
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"10e blocks hERG channel current in electrophysiological patch clamp experiments, and computational docking experiments predict that the dofetilide core of 10e binds hERG channel in a conformation similar to that previously predicted for 1."
Dofetilide activates KCNH2.
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| 4
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"Additional application of dofetilide (500 nmol/L) led to complete suppression of I KCNH2."
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"Raising the extracellular potassium to 10 mmol/l, HERG block by azimilide, dofetilide, quinidine and sotalol was significantly decreased, while the block by amiodarone was unchanged."
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"Dofetilide corrected pentamidine induced hERG, but not K (IR) 2.1 trafficking defects."
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"Dofetilide block involves interactions with open and inactivated states of HERG channels."
Dofetilide increases the amount of KCNH2.
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Dofetilide increases the amount of KCNH2. 2 / 2
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"The increase in hERG surface expression by dofetilide is consistent with the increased trafficking efficiency observed by Varkevisser et al. (2013) XREF_BIBR."
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"Dofetilide analogues that displayed high channel affinity, mediated by pi-pi stacks and hydrophobic interactions, also restored hERG protein levels, whereas analogues with low affinity were ineffective."
KCNH2 affects Kr
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KCNH2 activates Kr.
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KCNH2 activates Kr. 39 / 39
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"Acetylcholine, a selective agonist of I Ach shortens the APD in atrial but not ventricular myocytes whereas E-4031, a selective blocker of I Kr mediated by hERG, prolonged APD in ventricular CMs but not atrial CMs."
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"Therefore, the investigators could conclude reasonably that increased I Kr, mediated by activation of HERG potassium channels, compensated for the action potential prolonging effects of ATX-II."
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"Functional expression studies have demonstrated that mutations in the KCNH2 gene cause a reduction of I Kr current."
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"HERG channels underlie the delayed-rectifier K + channel current (I Kr), which is crucial for membrane repolarization and therefore termination of the cardiac action potential."
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"In the heart, the rapidly activating component of the delayed rectifying K + current (I Kr) is mediated by HERG1 [XREF_BIBR]."
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"HERG produces I Kr the rapidly repolarizing potassium current in cardiomyocytes XREF_BIBR."
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"HERG channels underlie the cardiac delayed rectifier current, I Kr, and their unique voltage dependent gating properties are critical to normal repolarization during the cardiac action potential."
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"Mutations in KCNH2 cause a reduction of I Kr current, through mechanisms similar to the effects exhibited by KCNQ1 mutations on I Ks current."
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"XREF_BIBR Despite the evidence that heteromeric hERG 1a/1b channels underlie cardiac I Kr, we know little about the gating and pharmacological properties of these channels, how hERG 1a/1b channels differ from hERG 1a homomers, or what role the hERG 1b subunit might play in disease."
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"Another LQTS subtype, LQT2, is caused by mutations in the potassium-channel gene KCNH2 that lead to a reduction in I Kr."
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"Using patch clamp to study Na + and Ca 2 + currents, as well as whole-cell current clamp to measure AP, they found that LQTS cells have tendencies toward prolonged AP duration, smaller Na + current density, slower time to inactivation, and increased time to peak.At least three groups have studied LQTS using pluripotent cells from patients with LQTS Type 2, caused by mutations in KCNH2 (hERG channel, responsible for inwardly rectifying potassium current I Kr)."
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"As shown in Fig. 6, overexpression of HERG markedly increased I Kr, as recorded during action potential clamp, and suppressed APD alternans during rapid pacing."
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"Native I Kr and hERG channels exhibit sensitivity to pharmacological blockade by diverse drugs, including both Class Ia and Class III antiarrhythmic agents; excessive pharmacological inhibition of I Kr / hERG leads to acquired long QT syndrome."
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"Virtually all data on PIP 2 modulation of the EAG channel family comes from a single gene, the human Erg subfamily channel Erg1 (hErg1, Kv11.1), which underlies the I Kr current critical to cardiac action potential repolarization."
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"However, it was recently reported that coassembly of HERG and MiRP1 (minK related peptide) subunits induces a current with properties almost exactly like I Kr recorded in cardiac myocytes (Abbott et al. 1999)."
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"As it can not be proven that LR 50, dofetilide is equal in dog and human, however, only its relative consistency across drugs can be assumed (Black and Leff 1983); it could also generally be interpreted as a higher net contribution of hERG mediated I Kr current to cardiac repolarization."
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"Potassium channels encoded by human ether-a-go-go-related gene (hERG) mediate the cardiac rapid delayed rectifier K + current (I Kr), which participates in ventricular repolarization and has a protective role against unwanted premature stimuli late in repolarization and early in diastole."
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"HERG1 channels produce I Kr XREF_BIBR; XREF_BIBR, a potassium current important in repolarizing the ventricular action potential 23."
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"Alterations in hERG mediated I Kr current, whether drug induced or a result of the over 200 naturally occurring mutations of this channel, may induce or contribute to the development of long QT syndrome."
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"The WT HERG produced an I (Kr)-like, E-4031-sensitive conductance with an inward rectification."
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"LQTS2 is caused by mutations in KCNH2, a gene whose protein product contributes to I Kr (also known as HERG), which is the predominant repolarizing potassium current in CMs."
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"In addition, sustained functional reentry is seen to accelerate in cardiomyocytes ' monolayers infected by hERG to increase their I Kr."
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"This study also found Kv11.1 hERG 1a protein expression was reduced compared to controls, suggesting reduced functional expression of I Kr may be one mechanism contributing to HF induced I Kr downregulation."
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"The KCNH2 gene encodes the alpha-subunit of the voltage gated potassium channel and mediates the rapidly activating component of the delayed rectifying potassium current (I Kr)."
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"The HERG (human ether-a-go-go-related gene, alternative nomenclature KCNH2) is responsible for channels mediating I Kr which plays an important role in ventricular repolarization."
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"Mutations in the KCNQ1 and HERG genes cause the Long QT Syndromes, LQTS1 and LQTS2, due to reductions in the cardiac repolarizing I Ks and I Kr currents, respectively."
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"Analysis of the current generated following transfection of the mutated channel into human embryonic kidney (HEK) cells showed that the mutation shifted inactivation of the KCNH2 channels out of the range of the action potential, thus producing a large gain of function in I Kr."
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"In the heart, HERG K + channel subunits mediate a delayed rectifier K + current (I Kr) that aids cellular repolarization."
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"XREF_BIBR, XREF_BIBR The hERG potassium channel underlies the delayed rectifier potassium current (I Kr), and is the most common potassium channel associated with drug induced QT prolongation."
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"In these previous studies, we demonstrated that the underlying electrophysiological mechanism is secondary to the effect of the K897T polymorphism to accentuate the loss of function of delayed rectifier potassium current (I Kr) caused by other mutations in KCNH2."
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"A reduction of I Kr caused by long QT syndrome (LQTS)-associated mutations in KCNH2 can induce ventricular arrhythmia and cause sudden cardiac death."
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"HERG E1039X mutation caused an incomplete loss-of-function in ' I Kr '."
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"The hERG (human ether-a-go-go related gene) potassium channel (Kv11.1), encoded by the KCNH2 gene, underlies the rapidly activating delayed rectifier K + current (I Kr)."
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"The rapidly activating delayed rectifier K + channel (I Kr) is encoded by the human ether-a-go-go -related gene (hERG), which is important for the repolarization of the cardiac action potential."
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"HERG overexpression upregulates I Kr in NRVM."
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"The former terminology stems from the finding that HERG underlies a component of I Kr, a " delayed rectifier " current in cardiac muscle."
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"Work in several laboratories has contributed to our understanding of how the gating mechanisms of HERG channels enable I Kr to fulfill its physiological role in the heart."
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"Heterologous expression studies have shown that the N588K mutation in KCNH2 dramatically increases I Kr density and reduces the affinity of the channel to d-sotalol by 20-fold."
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"Erg channels are widely expressed, including the brain and heart, where cardiac herg1 underlies the I Kr current in the heart and its dysfunction can lead to dangerous arrhythmias."
Mutated KCNH2 activates Kr. 2 / 2
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"Loss-of-function (LOF) KCNH2 mutations decrease I Kr in type 2 LQTS (LQT2) XREF_BIBR, XREF_BIBR, XREF_BIBR."
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"As hERG underpins the rapid delayed rectifier channel current (I Kr) XREF_BIBR, the N588K ' gain-of-function ' hERG mutation is anticipated to increase greatly the contribution of I Kr to cardiac repolarization in SQT1 patients, thereby accounting for QT interval abbreviation XREF_BIBR, XREF_BIBR - XREF_BIBR."
KCNH2-P202L activates Kr. 1 / 1
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"V198E and P202L hERG produces WT I Kr."
KCNH2-V198E activates Kr. 1 / 1
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"V198E and P202L hERG produces WT I Kr."
KCNH2-N588K activates Kr. 1 / 1
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"However, neither of these pharmacological interventions reproduces precisely the changes to I Kr caused by the N588K hERG SQT1 mutation."
KCNH2-N996I activates Kr. 1 / 1
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"In summary, we have demonstrated that genetic correction of the N996I KCNH2 mutation associated with LQT2 restores I Kr density and normalizes APD in patient specific LQT2-hiPSC-CMs."
KCNH2 inhibits Kr.
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KCNH2 inhibits Kr. 13 / 13
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"In SQT1, a gain-of-function mutation in KCNH2 impairs the voltage dependent inactivation of I Kr."
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"These findings indicate that heterotetrameric HERG channels containing HERG1b-R25W impair the generation of I Kr."
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"The authors showed that the R311C mutation specifically disables the posttranscriptional activity of TBX20 over KCNH2, which decreases the I Kr and prolongs the AP, therefore, identifying TBX20 as an LQT2 modifying gene [XREF_BIBR]."
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"We have previously shown that the G1681A mutation in KCNH2 disrupts trafficking of the I Kr / HERG channel to the cell membrane [XREF_BIBR]."
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"To lengthen atrial refractory period, Amit et al. assessed gene transfer of a KCNH2 mutation (G628S) known to block the I Kr current with dominant negative effects."
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"This result indicates that a mutation in hERG not only can disrupt I Kr but can worsen I Ks function and superimpose to cause a synergistic lesion to the defective I Ks encoded with a mutant KCNQ1, leading to further prolongation of APD and the QT interval."
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"The effects of non hERG channels are thought to enhance or mitigate the torsadogenic effects of I Kr block."
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"Mutations in hERG channels reduce I Kr to cause congenital long-QT syndrome type 2, mostly by decreasing surface membrane expression of trafficking deficient channels."
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"Reduction of I Kr induced by mutations in hERG or drug block slows repolarization, causing long QT syndrome and sudden cardiac death."
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"Using cell biology and electrophysiologic techniques, we found that hypoxic culture of hERG expressing human embryonic kidney (HEK) cells and neonatal rat cardiomyocytes reduced hERG current / I Kr and mature ERG channel expression with a concomitant increase in calpain expression."
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"XREF_BIBR Block of hERG channels reduces the key repolarizing current, I Kr, to cause QT interval lengthening on EKG to potentially induce the life threatening cardiac arrhythmia torsades de pointes."
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"The potencies (IC 50 values) for E209 to inhibit the cardiac I Kr (hERG), Cav 1.2 and Nav 1.5 channels were determined in an electrophysiology based assays using IonWorks HT (CHO cells) XREF_BIBR."
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"The hERG channel blocker E-4031 is known to block the rapid delayed rectifier K + channel (I Kr), thereby decreasing K + efflux and increasing APD."
Mutated KCNH2 inhibits Kr. 4 / 4
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"26 In this particular case, it was possible that reduced repolarization reserves due to enhanced I Kr inhibition caused by a combination of KCNH2 mutation, hypokalemia and oral garenoxacin contributed to QT interval prolongation and arrhythmia development."
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"K897T was previously associated with a prolonged QT interval in several different populations and can alter the biophysical properties of mutant channels (current density, activation, inactivation, and recovery from inactivation) and exacerbate the I Kr reduction caused by other KCNH2 mutations [XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR]."
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"Most of hERG mutations underlying type 2 LQTS (LQTS2) suppress I Kr currents by causing trafficking defects XREF_BIBR, XREF_BIBR."
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"HERG mutations resulting in reduced I Kr cause type 2 long QT syndrome (LQT2), which predisposes individuals to life threatening arrhythmias."
KCNH2-G816V inhibits Kr. 1 / 1
| 1
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"Our companion article characterizes the HERG G816V mutation, which reduces I Kr current density via a trafficking error."
KCNH2-N996I inhibits Kr. 1 / 1
| 1
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"Our findings demonstrated that the N996I KCNH2 mutation caused a similar (~ 30-40%) I Kr reduction in both mutated hiPSC- and hESC derived CMs."
KCNH2-A561P inhibits Kr. 1 / 1
| 1
reach
"A561P HERG Mutation Impairs I Kr Contribution to AP in UhiPS-CMs."
KCNH2 binds Kr.
| 2
KCNH2 binds Kr. 2 / 2
| 2
sparser
"To validate our simulations of drug interactions with I Kr , the sensitivities of two hERG mutations, N588E and N588K, to I Kr dofetilide block were also simulated."
sparser
"To validate our simulations of drug interactions with I Kr , the sensitivities of two hERG mutations, N588E and N588K, to I Kr dofetilide block were also simulated."
KCNH2 decreases the amount of Kr.
| 1
KCNH2 decreases the amount of Kr. 1 / 1
| 1
reach
"Only a few studies reported that the loss-of-function in I Kr caused by hERG channel pore missense mutations (V644L 24, G584S 25, V603L and A614V 26) was associated with channel inactivation."
Pyraclofos affects KCNH2
| 4 53
Pyraclofos inhibits KCNH2.
| 2 28
| 2 28
sparser
"Increasing [K + ] e produced a +10 mV shift in voltage‐dependent inactivation of WT I hERG and slowed inactivation time course, while lowering [K + ] e from 4 to 1 mmol/L produced little change in inactivation voltage dependence, but accelerated inactivation time course."
reach
"The voltage dependent inhibition of the hERG currents by olanzapine increased steeply in the voltage range of channel activation."
reach
"HERG current was rapidly and reversibly suppressed by external acidosis in a voltage independent manner."
reach
"We interpret this to indicate that stabilization of the activated voltage sensor limits the return of hERG channels to rest."
reach
"XREF_FIG and XREF_FIG illustrate that Ca 2+ is not a voltage dependent blocker of HERG currents."
reach
"Together, these results suggest that voltage dependent block of HERG results from gating dependent changes in the accessibility of Y652, a critical component of the drug binding site."
reach
"In conclusion, the voltage sensor of the initial half is able to confer near normal voltage dependent properties to the assembled construct, and the functional properties of the pore domain leading to the characteristic voltage dependent inactivation of HERG are maintained in the co-assembled channels."
reach
"Thus, neither a time dependent nor -independent voltage dependent block of open HERG channels can explain the effect of extracellular Ca 2+."
reach
"To determine whether the Ca 2+ effect is due to a rapid voltage dependent block of open HERG channels, the method of XREF_BIBR was modified to accommodate HERG inactivation behavior."
sparser
"The data were fitted with equation xref to derive V 0.5 and k values for voltage‐dependent inactivation of I hERG ."
reach
"Voltage dependent blockade of HERG channels expressed in Xenopus oocytes by external Ca2+ and Mg2+."
reach
"Mutations in this loop affect the rapid voltage dependent inactivation of the HERG K + channel that is critical for its normal function [13]."
reach
"XREF_BIBR Concentration and voltage dependent inhibitions of the hERG channel by ASP A were further investigated."
reach
"Based on the data obtained from above three different types of I-V curves, tetra-n-octylammonium bromide exhibited a significant voltage dependent inhibition of HERG currents in all three experiments."
reach
"3.2 Voltage dependent inhibition of HERG channels."
reach
"However, similar changes in the voltage dependent profile for block of Y652F or Y652A HERG channels were observed with vesnarinone, a cardiotonic drug that is uncharged at physiological pH. Together, these results suggest that voltage dependent block of HERG results from gating dependent changes in the orientation of Y652, a critical component of the drug binding site, and not from a transmembrane field effect on a charged drug molecule."
reach
"The voltage dependent inactivation of hERG channels with 135 mM K + in the pipette solution (bath solution containing 5 mM K +) was also evaluated using the standard triple pulse protocol (XREF_FIG) and also plotted in XREF_FIG (O, n = 4)."
reach
"Second, the voltage dependent inhibition of HERG channels has been observed for both compounds although it is more significant by tetra-n-octylammonium bromide than benzethonium chloride."
reach
"The voltage dependent inhibition of hERG currents by endoxifen increased steeply in the voltage range of channel activation."
reach
"These results suggest that while intracellular Mg 2+ causes some voltage dependent block of the h-erg channel, Mg ` block may not necessarily account for all of the observed rectification of the instantaneous current."
reach
"This voltage shift reduces hERG channel inactivation at efflux assay potentials, and will reduce the affinity of hERG blocking drugs that bind to inactivated states of the channel."
reach
"We propose that the Q fast charge movement during activation accompanies transitions through early closed states of the hERG activation pathway, and that the weak voltage dependence of these transitions limits the overall activation rate of hERG channels."
reach
"Together these findings indicate a critical role for Tyr 652 in voltage dependent block of HERG channels."
reach
"Voltage dependent inhibition of hERG currents has been reported as a common characteristic of open-channel blocking compounds such as dofetilide (Snyders and Chaudhary, 1996)."
reach
"Using a ventricular action potential voltage clamp protocol, halofantrine and N-desbutylhalofantrine block of HERG current was greatest during phases 2 and 3 of the action potential waveform."
reach
"Coexpression of R863X with wild-type HERG showed reduced current densities and accelerated voltage dependent inactivation of HERG channels."
reach
"While molecular determinants for voltage dependent activation and inactivation can be different [XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR], the outer mouth of the pore loop has been implicated in voltage dependent inactivation of HERG K + channels [XREF_BIBR, XREF_BIBR, XREF_BIBR]."
reach
"The voltage dependent inhibition of hERG current resulted in the activation curve to be shifted to a negative voltage after primaquine exposure in a dose dependent manner."
reach
"Extracellular protons accelerate hERG channel deactivation by destabilizing voltage sensor relaxation."
reach
"Removing external divalents does not remove deactivation, eliminating the possibility that slow voltage dependent block by divalent cations causes HERG deactivation."
Pyraclofos activates KCNH2.
| 2 22
| 2 22
reach
"Although in situ Fuc editing had no apparent impact on the voltage dependent activation of hERG channel, it was detected to have a major influence on the hERG maximum current by whole-cell voltage-clamp experiments."
reach
"HERG K + currents were elicited by 1-s depolarizing voltage steps to +20 mV from a holding potential of -80 mV followed by a 1-s repolarization back to -40 mV."
reach
"Voltage dependent activation of HERG currents became faster at negative test voltages but there were no changes at positive voltages after cibenzoline."
reach
"Since hiPSC-CMs likely contain other voltage activated ionic currents, we investigated the hERG component of the voltage activated currents, by isolating hERG current as an E-4031-sensitive current."
sparser
"Similar to other Kv channels, hERG1 is activated by voltage."
reach
"The normalized I tail reflects a voltage dependent activation of the HERG channels."
reach
"The mutation A536W, which switches the voltage dependent activation of hERG K + channels to a much more negative potential 30, was expected to alter cell excitability and consequently induce behavioral defects in worms."
reach
"The insets to XREF_FIG A and B show the voltage protocol used to elicit I hERG, which was similar to that applied in prior hERG channel studies from our laboratory."
reach
"The I-V curve of I tail shows a voltage dependent activation of hERG channels that reached a steady-state at +30 mV."
reach
"Fig. 2 A (control) shows the HERG currents elicited by voltage steps ranging from -120 to +40 mV applied in 10 mV increments from the holding potential of -80 mV."
reach
"The HERG current was elicited by 0.4-s voltage steps from -80 to +20 mV, followed by a 0.4-s step to -60 mV to record outward tail currents at intervals of 2, 6 and 15 s."
reach
"Like other K v channels, hERG is activated by membrane voltage; however, distinct from other K v channels, hERG channels have unusually slow kinetics of closing (deactivation)."
reach
"Wild-type HERG channels treated with TMRM showed no voltage dependent changes in fluorescence (unpublished results); therefore, it is unlikely that the observed fluorescence changes are from TMRM labeling of native cysteines in other regions of the channel."
sparser
"Like other K v channels, hERG is activated by membrane voltage; however, distinct from other K v channels, hERG channels have unusually slow kinetics of closing (deactivation)."
reach
"Voltage activation of Kv11.1 (hErg1) is highly pH sensitive in low external Ca 2+."
reach
"Two voltage protocols were used to activate hERG channels (XREF_FIG)."
reach
"The voltage protocol shown in XREF_FIG was used to activate hERG channels and trigger I kr current (XREF_FIG)."
reach
"The fourth transmembrane segment (S4) contributes to form the voltage sensor domain (VSD), which sharply contributes to hERG1 biophysical properties [XREF_BIBR]."
reach
"The normalized I tail reflects the voltage dependent activation of the HERG channels."
reach
"Using several mutations as tools, we define key steps in the deactivation pathway that limit voltage sensor return to produce the physiologically relevant resurgent hERG current in cardiomyocytes.Wild-type (WT) and mutant hERG channel constructs were prepared for expression in Xenopus laevis oocytes as described in Cheng et al. (27)."
reach
"This indicates that maintenance of the consensus site for PKA phosphorylation in the amino-terminus is not necessary for the TRH induced modifications of HERG activation voltage dependence.The shifts in HERG activation kinetics induced by TRH in oocytes have been shown to be minimised by the protein kinase C (PKC) inhibitor GF109203X [13]."
reach
"First, voltage dependent block of the channel might decrease HERG current at potentials less than +50 mV, producing an apparent shift in the voltage dependent activation of the channels."
reach
"Our objective was to evaluate two potential sources of variability : the temperature at which recordings are performed and the voltage pulse protocol used to activate hERG K (+) channels expressed in HEK293 cells."
reach
"The present results are consistent with, and extend, the 2008 study showing that Src inhibition did not change the voltage dependent activation of hERG XREF_BIBR."
Pyraclofos binds KCNH2.
| 3
reach
"Those may be explained by state-, time-, and voltage dependent hERG binding and conductance changes (di Veroli etal."
reach
"For the latter, one has to postulate that hERG1 functionally interact with voltage dependent Ca 2+ entry pathways that exhibit increasing activity and conductivity with increasing depolarization of the membrane potential."
reach
"For the latter, one has to postulate that hERG1 functionally interact with voltage dependent Ca 2+ entry pathways that exhibit increasing activity and conductivity with increasing depolarization of the membrane potential."
| 2 56
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"The knockdown of hERG reversed proliferation in a time dependent manner, as the rate of viable cells gradually downgraded to 58.3% +/- 6.4% 72 hours after the administration of nano-siRNA complexes (XREF_FIG)."
reach
"To test if ER-G1 promotes proliferation in vitro, we generated a series of stable cell lines expressing GFP, Golgi-G1, or ER-G1 in HCC derived HepG2 cells."
reach
"In addition, the CCK-8 assay, apoptosis and cell cycle analysis were performed and showed that blockage of HERG K + channels decreased the proliferation of MDS cells but rarely had effects on cell apoptosis and cell cycle distribution."
reach
"Functionally, hERG1 may contribute to survival, proliferation, and metastasis of tumor cells."
reach
"Functionally, hERG1 may contribute to survival, proliferation, and metastasis of tumor cells."
reach
"Indeed, the knockdown of HERG1 inhibits cell proliferation, while its pharmacological inhibition by E4031 fails to affect cell proliferation."
reach
"HERG potassium channels enhance tumor invasiveness and breast cancer proliferation."
reach
"We also demonstrate that hERG blockers reduced GPDC proliferation, and improved survival in patients who received one or more hERG blocking drugs but only if their tumors exhibited high hERG expression levels."
reach
"HERG1 agonists cause irreversible inhibition of cell proliferation in human mammary gland adenocarcinoma derived cells."
reach
"Activation of hERG1 after 48 h of PD 118057 treatment (5 muM and 10 muM) increased proliferation of osteosarcoma cells."
reach
"HERG1 has also been shown to enhance GC cell invasion and proliferation, induce cell cycle progression in vitro, and promote tumor genesis and growth in vivo."
reach
"Our findings suggest that altered ERG1 expression may contribute to disease related smooth muscle proliferation and implicates these ion channels as potential targets as inhibitors of tumor driven neovascularization."
reach
"Interestingly, in primary cultures from leukaemia blasts, and in many cell lines, hERG1 inhibition tends to block cell proliferation (reviewed in Arcangeli, 2005; Arcangeli and Becchetti, 2005)."
reach
"To study whether inhibition of HERG channel protein expression would reduce SW2 cell proliferation, we first determined which members of the HERG channel family were expressed in SCLC cells."
reach
"Nevertheless, although HERG1 siRNA silencing caused a dramatic inhibition of cell proliferation, no major difference in cell proliferation was observed within the first 24 h."
reach
"However, siRNA inhibition of HERG1 protein expression almost abolished HERG currents and strongly reduced SCLC cell proliferation."
reach
"This suggests that ER-G1 stimulates cancer cell proliferation by enabling tumor expansion rather than directly stimulating cell growth and division.Based on tumor morphology, we hypothesized that ER-G1 stimulates tumor growth by facilitating tissue remodeling and invasion."
reach
"In the human neuroblastoma cell line SH-SY5Y [XREF_BIBR] and melanoma cells [XREF_BIBR], not only pharmacological ERG channel blockage but also inhibition of HERG channel protein expression effectively reduces cell proliferation."
reach
"The selective HERG channel blocker, E-4031, reduced proliferation of CEM, U937, and K562 cells, and this appears to be the first direct evidence of a functional role for the HERG current in cancer cells."
reach
"HERG blockers inhibit the proliferation at S and G2/M phase while Eag blocker impramine increases early apoptosis in ovarian cancer cells with no effect on cell cycle."
reach
"Inhibition of HERG1 K + channel protein expression decreases cell proliferation of human small cell lung cancer cells."
reach
"Yet, a significant number of Tn positive cells were detected in these livers, indicating that the expression of ER-G1, in the absence of NRas, is not toxic but does not induce cell growth or proliferation."
reach
"In melanoma cells, HERG is also expressed, and inhibition of HERG with the non specific channel inhibitor imipramine decreased proliferation [22,27]."
reach
"Inhibition of hERG1 with either E-4031 (10 muM and 20 muM) or knockdown with hERG1-siRNA reduced proliferation of osteosarcoma cells."
reach
"This supports our suggestion that HERG would modulate MDA-MB-435S cells through interactions with membrane proteins, rather than through a modulation of the membrane potential.In addition to modulating cancer cell proliferation, HERG channels have been considered important in enhancing tumor cell invasion and cancer metastasis [11,17]."
reach
"Blockade of the hERG potassium channel proteins by specific agents can inhibit the proliferation and metastasis of tumor cells and the corresponding [XREF_BIBR, XREF_BIBR], increasing the sensitivity of tumor cells to chemotherapeutic drugs."
reach
"HERG1 contributes to poor prognosis in patients with ESCC by promoting ESCC cell proliferation, migration, and invasion via TXNDC5 through the PI3K and AKT signaling pathway."
reach
"Inhibition of HERG1 protein expression by siRNA reduced cell proliferation."
reach
"HERG1 is over-expressed in various cancer cells and found to promote cell proliferation [XREF_BIBR - XREF_BIBR]."
reach
"XREF_BIBR, XREF_BIBR In addition, genetic deletion of KCNE2 is associated with gastric neoplasia and increased nuclear cyclin D1 levels in mice, revealing genetic manipulation of cell proliferation mediated by a hERG beta-subunit."
reach
"The proliferation of SK-OV-3 cells is significantly inhibited by both Eag and HERG blockers."
reach
"Thus, B-RAF-sensitive hERG K + channel up-regulation possibly contributes to cell proliferation and apoptosis of tumor cells."
reach
"Selective hERG channel blockade by E-4031 reduced proliferation in cancerous cell lines."
reach
"In contrast, siRNA induced inhibition of HERG1 protein expression decreased cell proliferation by about 50%."
reach
"However, we do not know to which degree heteromeric HERG channels are formed and whether all or only HERG1 channel subunits support cell proliferation."
reach
"Moreover, E-4031, a specific HERG channel blocker, reduced proliferation of uterine cancer cells."
reach
"To delineate the mechanism of action behind hERG1 promotion of osteosarcoma cell proliferation, we examined whether inhibition of hERG1 triggers apoptosis."
reach
"Based on hERG expression levels found in GSC derived xenografts, we wanted to determine whether hERG blockers could decrease proliferation rates in high hERG expressing GPDC lines more than low expressing hERG GPDC lines."
reach
"Silencing of hERG1 Gene Inhibits Proliferation and Invasion, and Induces Apoptosis in Human Osteosarcoma Cells by Targeting the NF-kappaB Pathway."
reach
"The hERG potassium channel can modulate the proliferation of the chronic myelogenous leukemic K562 cells, and its role in the erythroid differentiation of K562 cells still remains unclear."
reach
"11 It also has been shown that inhibition of hERG1 current activity can inhibit proliferation in leukemic cells by promoting cell cycle arrest."
reach
"In control experiments, overexpression of HERG channels in HEK-293 cells dramatically increased the proliferation and migration of the cells and blocking HERG in these cells attenuated both proliferation and migration."
reach
"Pharmacological inhibition of HERG channels reduces proliferation and impairs invasiveness in a variety of cancer cell types."
reach
"Furthermore, HERG small interfering (si) RNA attenuated the proliferation and migration of the cells."
reach
"For example, the HERG channels are associated with cell cycle and proliferation of several cancers; therefore, the use of HERG specific blockers could inhibit the proliferation of tumor cells [XREF_BIBR]."
reach
"Reduced expression of the hERG protein by siRNA transfection resulted in decreased cell proliferation in small cell lung cancer cells [XREF_BIBR], and a hERG channel promoted the proliferation of ovarian cancer cells by affecting the cell cycle [XREF_BIBR]."
reach
"We found that the hERG blocker E-4031 decreased proliferation as assayed by sphere formation in a GPDC line exhibiting high levels of hERG expression, whereas blocking hERG in low hERG expressing lines does not decrease proliferation to the same extent."
reach
"To further evaluate whether silencing herg gene in SH-SY5Y cells may inhibit cell growth and proliferation, the growth curves of cells nontransfected and transfected with shRNA-herg1, shRNA-herg1/1b or shRNA-control were determined and MTT assay and colony formation assay were performed."
reach
"Application of the hERG1 activator, the diphenylurea derivative NS1643, inhibits cell proliferation irreversibly."
reach
"Knockdown of hERG1 significantly suppressed cellular proliferation and invasion, and induced apoptosis, while inhibition of hERG1 significantly decreased activation of NF-kappaB."
reach
"Altogether, these results suggest that the hERG1 agonist NS1643 inhibits proliferation of SKBr3 cells by downregulating the expression of a plethora of important cell cycle phase specific biomarkers including an early decrease of cyclin E2."
reach
"[Downregulation of Herg1 suppresses osteosarcoma proliferation and invasion by targeting Hippo signaling pathway]."
reach
"Increased hERG1b levels are expected to depolarize cells, while high hERG1 levels will shift membrane potential toward more hyperpolarized values 35 and suppress cell proliferation."
reach
"HERG potassium channel blockers modulate proliferation."
reach
"In addition, leukemic cell proliferation was dramatically inhibited by HERG K+ channel special inhibitor E-4031."
reach
"XREF_FIG - XREF_FIG, hERG1 downregulation and/or inhibition prevented proliferation and invasion, and induced apoptosis of osteosarcoma cells."
| 1 46
KCNH2 activates potassium(1+).
| 33
| 32
reach
"However, ivabradine also inhibits human ether-a-go-go (hERG) mediated potassium currents."
reach
"The site mutation (p.N588K) in KCNH2 increases the expression of HERG channels and thus enhances outward potassium current, shortens action potential duration, and promotes proarrhythmic activity in short QT-syndrome-cardiomyocytes."
reach
"In humans, the delayed rectifier potassium current is mediated by the ion channel KCNH2 encoded by the human ether-a-go-go-related gene (HERG) [XREF_BIBR]."
reach
"The hERG channel mediates the rapid delayed rectifier potassium current (I Kr) and can be overexpressed in HEK293 (Human Embryonic Kidney 293) or CHO (Chinese Hamster Ovary) cell lines."
reach
"HERG current increased in direct proportion to [K+] e, although the shape of the I-V relationship was not altered."
reach
"Interestingly and in contrast to previous studies, when expressed in Xenopus oocytes, the interaction between Sig-1Rs and hERG channels resulted in increased hERG mediated K+ currents -- a mechanism that seemed to occur through a regulation of channels subunits maturation and stability [XREF_BIBR]."
reach
"(A) Expression of HERG channels in Xenopus oocytes induced K+ channels with characteristic properties, i.e. fast inactiva- tion at positive potentials and large, slowly decaying tail cur- rents upon repolarization [18]."
reach
"Lacosamide was tested in vitro on sodium and L-type calcium currents from isolated human atrial myocytes and on hERG mediated potassium currents from stably transfected HEK293 cells."
reach
"For these reasons we and others have attempted to define the functional role for HERG mediated K+ currents in repolarization of the action potential in the human ventricle."
reach
"Due to the presence of this characteristic PY motif, we investigated whether the potassium current mediated by hERG1 (I hERG1) is regulated by the ubiquitin ligase Nedd4-2, as it has been observed for two other cardiac ion channels, Na v 1.5 and KCNQ1 [11,12]."
reach
"We investigated the effects of DW-224a on the human ether-a-go-go-related gene (hERG) mediated potassium currents to evaluate its potential to induce QT interval prolongation."
reach
"Human ether-a-go-go-related gene (HERG) subunits mediate a K+ current that is required for normal repolarization of the cardiac action potential."
reach
"Inhibition of hERG channels will reduce the potassium efflux during repolarization, and will result in an increase in human cardiac AP duration, concomitantly leading to a prolongation of the QT interval (XREF_FIG) [XREF_BIBR]."
reach
"As blockade of the human Ether-a-go-go-Related Gene (hERG)-mediated potassium current is the most common mechanism of drug induced prolongation of the myocardial action potential and QT-interval prolongation, data showing that dabigatran did not modify the hERG mediated potassium current in human embryonic kidney cells agree with the previously mentioned pre-clinical results [XREF_BIBR]."
reach
"This includes (1) testing for blockade of I (Kr) or hERG mediated potassium current in heterologous cell systems, (2) measurement of effects on the myocardial action potential in vitro; and (3) assessment of effects on the ECG in a well conducted in vivo study."
reach
"Of these, the Kv11.1 (hERG, KCNH2) channel mediates the cardiac potassium current IKr, involved in the repolarization of the cardiac action potential and playing a crucial role to prevent arrhythmias induced by early after depolarizations or ectopic beats, such that mutations in Kv11.1 lead to inherited type 2 long QT syndrome."
reach
"This variant has subsequently been shown to slow I Ks potassium channel, when studied in Xenopus oocytes [XREF_BIBR], and to exhibit significant loss-of-function effects on both the KCNQ1- and KCNH2 mediated potassium currents, as measured in Chinese hamster ovarian cells [XREF_BIBR]."
reach
"Attenuation of repolarizing K+ current caused by mutations in HERG or channel block by common medications prolongs ventricular action potentials and increases the risk of arrhythmia and sudden death."
reach
"In vitro and animal studies with empagliflozin demonstrated no relevant interactions with the hERG mediated potassium current and no effect on action potentials (unpublished data)."
reach
"The human ether-a-go-go-related gene (hERG) channel mediates the rapid delayed rectifier potassium current (IKr) responsible for shaping the repolarization phase of cardiac action potentials."
reach
"HERG (human Ether-a-go-go Related Gene) is responsible for ion channels mediating rapid delayed rectifier potassium current, I Kr, which is key to cardiac action potential repolarization."
reach
"HERG mediates the cardiac delayed rectifier potassium current I Kr and mutations in the hERG gene and drug inhibition of hERG channels underlie inherited and acquired type 2 long-QT syndrome."
reach
"Paroxysmal atrial fibrillation (AF) can be caused by gain-of-function mutations in genes, encoding the cardiac potassium channel subunits KCNJ2, KCNE1, and KCNH2 that mediate the repolarizing potassium currents I k1, I ks, and I kr, respectively."
reach
"Raising the extracellular potassium to 10 mmol/l, HERG block by azimilide, dofetilide, quinidine and sotalol was significantly decreased, while the block by amiodarone was unchanged."
reach
"System specific maximal achievable Delta QTc was estimated to 28% from baseline in both dog and human, while% hERG block leading to half-maximal effects was 58% lower in human, suggesting a higher contribution of hERG mediated potassium current to cardiac repolarization."
reach
"At 1M concentration testosterone decreased the amplitude of HERG directed IKr (rapid component of cardiac delayed rectifier K+ current) by 30% within 30 min of exposure, while 17-estradiol had no effect."
reach
"The majority of drug induced arrhythmias are related to the prolongation of action potential duration following inhibition of rapidly activating delayed rectifier potassium current (I (Kr)) mediated by the hERG channel."
reach
"XREF_BIBR, XREF_BIBR The hERG potassium channel underlies the delayed rectifier potassium current (I Kr), and is the most common potassium channel associated with drug induced QT prolongation."
reach
"A hypothesis is that HERG produces the repolarizing cardiac potassium current IKr with the consequence that mutations in HERG prolong the QT interval by reducing IKr."
reach
"The HERG mediated potassium and the SCN5A mediated sodium currents, however, were only slightly reduced by estradiol at concentrations of up to 30 microM."
reach
"In addition to I to, f and I Kur, human atrial myocytes also exhibit a rapidly activating and inactivating current (I Kr) and a slowly activating current (I Ks), mediated by hERG1 and KCNQ1 channels, respectively, but they are much smaller outward potassium currents relative to I to, f and I Kur [XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR]."
reach
"Fluoxetine, a commonly used antidepressant, was reported to block the currents of several potassium channels, which are mediated by Kv1.1, Kv1.3, Kv1.4, Kv1.5, Kv3.1, Kv4.3, hERG and TREK-1 XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR."
Mutated KCNH2 activates potassium(1+). 1 / 1
| 1
reach
"In terms of electrophysiology, hERG mutations cause potassium ion channels to deactivate (close) much faster, blunting the normal rise in current (IKr) that results from rapid recovery from channel inactivation and slow deactivation [XREF_BIBR]."
KCNH2 inhibits potassium(1+).
| 1 9
| 1 7
reach
"CMX-2043 produced no inhibition of hERG mediated potassium current at its limit of solubility (3000muM; 1220mug/mL) when assessed using whole-cell patch-clamp electrophysiological methods."
sparser
"At 10 µM, aconitine, 14-benzoylaconine 8- O-palmitate, songoramine, gigactonine and neolinine demonstrated significant hERG K+ channel inhibition; all other compounds exerted only low (6-21%) inhibitory activity."
reach
"Lowering the extracellular potassium concentration ([K +] o) decreases the magnitude of I Kr and of outward HERG K + currents."
reach
"A Hodgkin-Huxley-style cardiac ionic model captured the different types of complex dynamics following blockage of the hERG mediated potassium current."
reach
"However, compared to other inward rectifiers which block potassium conductance via an intracellular polyamine block, HERG channels prevent potassium outflow by rapid inactivation."
reach
"These results demonstrate that hypoxia enhances the production of ROS in the mitochondria, resulting in down-regulation of hERG translation and decreased hERG mediated K+ conductance."
reach
"Furthermore, potassium channels were inhibited by 25D-NBOMe treatment in hERG assay."
reach
"Pharmacokinetic properties, druglikeness as well as other significant descriptors, such as molecular weight, H-bond donors, H-bond acceptors, solvent accessible surface area, log HERG (blockage of K+ channels), log S (aqueous solubility), log P (octanol and water), and human oral absorption, for the selected hits were determined by QikProp (XREF_TABLE)."
Mutated KCNH2 inhibits potassium(1+). 2 / 2
| 2
reach
"KvLQT1 and HERG mutations (one each) reduced K+ currents in vitro, consistent with the idea that they augment risk for aLQTS."
reach
"HERG mutations reduce the outward flow of potassium during repolarization and elongate the QT interval leading to polymorphic ventricular tachycardia, cardiac syncope, and sudden death."
| 4
reach
"Overall, i) several structures were found to be effectual for reducing hERG potassium ion channel binding affinity in this study."
reach
"The structure activity relationship (SAR) of the potency and selectivity, structure-metabolic stability relationship (SMR), and SAR of hERG (human ether-a-go-go related gene) potassium ion channel binding affinity for the analogs in the present studies invitro provided or suggested significant and/or useful structural determinants and insights for the respective purposes."
reach
"Thus, 1 demonstrates dose dependent inhibitory effect against mechanical allodynia in chronic constriction injury induced neuropathic pain model rats, robust metabolic stability and little hERG potassium ion channel binding affinity, with its unique and potentially safe profiles and mechanisms, which were distinctive from those of N/OFQ in terms of site-differential effects."
reach
"Design and SAR of the analogs for reducing hERG (human ether-a-go-go related gene) potassium ion channel binding affinity were also investigated in vitro as a safe-drug study."
Astemizole affects KCNH2
| 5 41
Astemizole inhibits KCNH2.
| 5 36
| 5 32
reach
"Astemizole, terfenadine and quinidine inhibited hERG currents with IC (50) values of 159nM, 224nM and 2muM, respectively (n = 51, 10 and 18)."
reach
"On the other hand terfenadine and astemizole effectively blocked HERG K+ channels with nanomolar affinities (330 and 480 nmol/L, respectively), whereas loratadine was about 300-fold less potent."
reach
"In fact, whole-cell voltage-clamp experiments revealed that the IC (50) for astemizole induced hERG blockade is about 300-fold lower than that for the inhibition of high K (+)-induced [3H] NE release."
reach
"Desmethylastemizole and astemizole blocked HERG current with similar concentration dependence (half-maximal block of 1.0 and 0.9 nM, respectively) and block was use dependent."
reach
"This is possibly a hypomorphic mutation that may be rescued by low incubation temperature or a hERG blocker such as astemizole."
reach
"Both terfenadine and astemizole mediated HERG blockade depended significantly on the voltage."
reach
"Astemizole rescued pentamidine and caused hERG trafficking inhibition via competitive interaction with F656 residue [XREF_BIBR]."
reach
"Several other potent hERG channel blockers, such as astemizole and cisapride, were later reported to rescue the trafficking of LQT2 associated hERG channels harboring the G601S mutation."
reach
"Fig. 2A shows an original trace : both terfenadine and astemizole blocked HERG channels at submicromolar concentrations."
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"50 nM astemizole blocked HERG tail currents by 54.5 2.9% (n = 6) and 84.5 1.5% (n = 6), after prior depolar- terfenadine control 200 ms IRK1 control terfenadine -, w,."
sparser
"Here, terfenadine and astemizole both inhibited the human ether-a-go-go related gene (HERG) encoded channels expressed in Xenopus oocytes at nanomolar concentrations in a use- and voltage-dependent fashion."
sparser
"In order to verify whether I HERG inhibition by astemizole might correlate with the ability of the second-generation H 1 receptor blocker to prevent high [K + ] e -induced [ 3 H]NE release from SH-SY5Y human neuroblastoma cells, we studied the concentration-dependence of I HERG blockade by astemizole in these cells."
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"On the other hand, terfenadine and astemizole blocked HERG channels in a concentration dependent manner with IC 50 of 431 nM and 69 nM, respectively, which are compatible with the recorded plasma levels of these drugs in the patients who developed the drug associated QT prolongation (Monahan et al., 1990; Wiley et al., 1992)."
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"On the other hand, terfenadine and astemizole effectively blocked HERG K+ channels with nanomolar affinities (the estimated IC50 values were 330 and 480 nM, respectively), whereas loratadine was approximately 300-fold less potent (IC50 approximately 100 microM)."
sparser
"Astemizole, an anti-histamine, is able to inhibit both Kv10.1 and Kv11.1 channels, contributing to inhibition of cancer cell proliferation in vitro and in vivo [ xref , xref , xref ]."
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"The data obtained demonstrated that, under depolarizing conditions, the inhibition of hERG K + channels by astemizole was unable to modify SH-SY5Y membrane potential, and therefore that the pharmacological inhibition of [3 H] NE release observed with these H 1 receptor blockers could not be ascribed to their interference with membrane depolarization."
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"As shown in XREF_FIG A, the user will find that astemizole inhibits the activities of the human hERG channel, which was stably expressed on HEK 293 cells, with an IC50 value of 0.0013 muM."
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"HERG channel blockers, such as E4031, fexofenadine and astemizole, facilitated maturation of hERG proteins by acting as chemical chaperones XREF_BIBR; however, these agents can not be used clinically for enhancing hERG channel currents, because they acutely block the rapidly activating delayed-rectifier K + channel current (I Kr)."
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"The extreme use dependence of terfenadine and astemizole suggests that drug binding can only occur to the open or inactivated state of HERG channels."
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"HERG blockade by terfenadine and astemizole occurred much faster at higher activation frequencies."
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"For this purpose, the hERG blocker astemizole (AST), an anti-histamine drug withdrawn from the market because of its cardiotoxic effect (Zhou etal, 1999; Chiu etal, 2004), was added to WT hiPSC-CMs (Fig XREF_FIG)."
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"We calculated that HERG channels are blocked by astemizole with an IC 50 value of 0.735 +/-0.223 nM and a Hill coefficient of 0.461 +/-0.041 (n = 4)."
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"The results of these studies have elegantly shown that both terfenadine [52] and astemizole [53] blocked HERG K + channels in a concentration range similar to that found in the plasma of subjects with cardiotoxic manifestations [43]."
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"Further, the user will also find that astemizole inhibits activities of the human hERG channel transiently expressed in the Xenopus oocyte with an IC50 value of 0.0484 muM (XREF_FIG B)."
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"This result illustrates the importance of the inactivated state in high-affinity block of HERG by astemizole and terfenadine as well as dofetilide, a drug requiring channel opening for block to occur."
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"In fact, both terfenadine and astemizole have been shown to block HERG K+ channels in a concentration range similar to that found in the plasma of subjects with cardiotoxic manifestations."
reach
"Terfenadine and astemizole suppressed the HERG current with IC50 of 431 nM and 69 nM, respectively."
reach
"HERG blockade by terfenadine and astemizole was also analyzed for its voltage dependence."
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"Incubation at lower temperature for R752W or with the hERG blocker astemizole for G601S dissociates channel-chaperone complexes and restores trafficking."
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"Use- dependent HERG channel blockade by 0.3 wM terfenadine (A) or 0.1 1tM astemizole (B)."
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"Block of HERG potassium channels by the antihistamine astemizole and its metabolites desmethylastemizole and norastemizole."
reach
"At the end of the light triggered depolarization to -20 mV we observed a clear hyperpolarization before return to the resting membrane potential, which was abolished by the hERG blocker astemizole (30muM)."
sparser
"The fact that the ic 50 for astemizole-induced blockade of I HERG was about 300-fold lower than that calculated for its inhibition of depolarization-induced [ 3 H]NE release from SH-SY5Y cells suggested that I HERG inhibition by astemizole was not responsible for such pharmacological effects."
sparser
"Another crucial point that should be underlined and which favors the hypothesis of SOC inhibition as a primary mechanism for [ 3 H]NE release inhibition by H 1 receptor antagonists is the existence of a 2- to 300-fold difference in the potency of astemizole-induced hERG inhibition ( ic 50 : 6 nM) versus [ 3 H]NE release ( ic 50 : 2.3 μM) or SOC ( ic 50 : 1.3 μM) inhibition."
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"Desmethylastemizole and astemizole cause equipotent block of HERG channels, and these are among the most potent HERG channel antagonists yet studied."
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"In this preparation, terfenadine and astemizole blocked the HERG channels expressed in Xenopus oocytes, whereas epinastine had little effect on that current (Chachin et al., 1998)."
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"In contrast to the K+ conductances described above, terfenadine (3 pM) and astemizole (1 1tM) almost completely abolished HERG channel tail currents."
Astemizole inhibits KCNH2-S631C. 3 / 3
| 3
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"Under these conditions, we found that HERG S631C currents, evoked by application of pulses to 0 mV with intervals of 8 s from a holding potential of -90 mV, could be completely blocked by 1 muM astemizole, as measured on the peak tail current amplitudes."
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"Surprisingly, under oxidizing conditions, we found that HERG S631C currents, evoked by application of pulses to +20 mV with intervals of 8 s from a holding potential of -90 mV, could not be blocked by 1 muM astemizole, as measured during the test pulse."
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"To investigate whether astemizole blocks HERG S631C channels, HERG S631C cRNA was expressed in oocytes and currents were investigated 2 days after injection."
| 1
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"Astemizole, terfenadine, cisapride, and MK-499 inhibited cERG and human ERG (hERG) currents with IC (50) values of 1.3, 13, 19, and 15 nM and 1.2, 9, 14, and 21 nM, respectively, and competitively displaced [(35) S] MK-499 binding from cERG and hERG with IC (50) values of 0.4, 12, 35, and 0.6 nM and 0.8, 5, 47, and 0.7 nM, respectively."
Astemizole activates KCNH2.
| 3
Astemizole activates KCNH2-N470D. 1 / 1
| 1
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"XREF_BIBR Astemizole is able to restore not only trafficking of hERG N470D and G601S mutants, XREF_BIBR, XREF_BIBR but also trafficking inhibition induced by pentamidine in which astemizole acts as a conformation sensitive chaperone and competes with pentamidine for overlapping binding sites."
Astemizole activates KCNH2-G601S. 1 / 1
| 1
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"Quinidine, astemizole, cisapride, and E4031 successfully rescued the trafficking deficient mutation G601S hERG, and the rescue relied on their interaction with F656 [XREF_BIBR]."
| 1
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"Another crucial point that should be underlined and which favors the hypothesis of SOC inhibition as a primary mechanism for [3 H] NE release inhibition by H 1 receptor antagonists is the existence of a 2- to 300-fold difference in the potency of astemizole induced hERG inhibition (ic 50 : 6 nM) versus [3 H] NE release (ic 50 : 2.3 muM) or SOC (ic 50 : 1.3 muM) inhibition.In addition, since it has been shown that terfenadine can interfere with voltage dependent Na + channels in guinea pig ventricular myocytes [38], the possibility existed that the inhibition of [3 H] NE release by this H 1 receptor antagonist could be ascribed to this pharmacological action."
Astemizole binds KCNH2.
| 2
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"Purified recombinant hERG binds Astemizole."
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"Astemizole binds with high affinity to membrane embedded hERG with a single binding site per tetramer."
PKA affects KCNH2
| 1 13 33
PKA phosphorylates KCNH2.
| 9 11
PKA phosphorylates KCNH2. 20 / 20
| 9 11
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"PKA dependent phosphorylation of hERG gives the channels a minor ability to open during action-potential voltages."
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"Activation of cAMP dependent protein kinase (PKA) causes phosphorylation of HERG accompanied by a rapid reduction in current amplitude, acceleration of voltage dependent deactivation, and depolarizing shift in voltage dependent activation."
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"Here, we report that the PKA-RII-specific AKAP inhibitory peptide AKAP-IS perturbs the distribution of PKA-RII and diminishes the PKA dependent phosphorylation of HERG protein."
sparser
"Direct PKA phosphorylation of the HERG protein was responsible for the cAMP-induced augmentation."
sparser
"14-3-3 accelerates and enhances HERG activation, an effect that requires PKA phosphorylation of HERG and dimerization of 14-3-3."
sparser
"Elevations of cAMP as seen in beta-adrenergic stimulation can result in PKA-dependent phosphorylation of hERG and direct binding of cAMP to the channel protein."
sparser
"AKAP- IS Decreases PKA-Dependent Phosphorylation of HERG Channels."
sparser
"PKA phosphorylation of HERG protein regulates the rate of channel synthesis."
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"Elevations of cAMP as seen in beta-adrenergic stimulation can result in PKA dependent phosphorylation of hERG and direct binding of cAMP to the channel protein."
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"AKAP-IS Decreases PKA Dependent Phosphorylation of HERG Channels."
sparser
"HERG/ I Kr responds to acute adrenergic signaling in a complex fashion that includes direct cAMP binding to the channel, PKA-dependent phosphorylation of HERG and phosphorylation-dependent binding to the adaptor protein 14-3-3 (Choe et al. xref ; Kagan et al. xref ; Thomas et al. xref )."
sparser
"Here, we report that the PKA-RII-specific AKAP inhibitory peptide AKAP- IS perturbs the distribution of PKA-RII and diminishes the PKA-dependent phosphorylation of HERG protein."
reach
"PKA phosphorylation of HERG protein regulates the rate of channel synthesis."
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"By shifting the voltage gated activation to more depolarized potentials, PKA dependent phosphorylation of HERG renders the channel less likely to open during action-potential voltages."
sparser
"PKA directly phosphorylates HERG, producing an inhibition of current at all voltages, accelerated deactivation and a rightward shift in voltage dependence of activation."
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"14-3-3 accelerates and enhances HERG activation, an effect that requires PKA phosphorylation of HERG and dimerization of 14-3-3."
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"Interestingly, a direct phosphorylation of the hERG cytoplasmic domains by PKA is involved in the regulation triggered by activation of beta-adrenergic receptors, and some signaling cross-talk between PKC and PKA can not be excluded."
sparser
"Interestingly, a direct phosphorylation of the hERG cytoplasmic domains by PKA is involved in the regulation triggered by activation of β-adrenergic receptors (Thomas et al., xref ; Cui et al., xref , xref ; Kiehn, xref ; Kagan et al., xref ; Karle et al., xref ), and some signaling cross-talk between PKC and PKA cannot be excluded."
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"HERG/I Kr responds to acute adrenergic signaling in a complex fashion that includes direct cAMP binding to the channel, PKA dependent phosphorylation of HERG and phosphorylation dependent binding to the adaptor protein 14-3-3."
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"Direct PKA phosphorylation of the HERG protein was responsible for the cAMP induced augmentation."
PKA activates KCNH2.
| 1 16
PKA activates KCNH2. 16 / 16
| 1 16
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"These results provide evidence for a novel mechanism which AKAP5 anchors PKA to up-regulate the HERG channel protein."
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"These results provide evidence for a novel mechanism which AKAP5 anchors PKA to up-regulate the HERG channel protein."
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"For the PKA mediated increase in HERG abundance, PKA activity must be localized to the surface of the ER [XREF_BIBR]."
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"For example, it is known that transcription levels of Kv1.5 are modulated by glucocorticoids, that Kv3.4 expression is upregulated by skeletal muscle innervation, and that PKA phosphorylation at the surface of the ER augments hERG biosynthesis."
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"Just how PKA activation enhances an already actively translating HERG channel is yet to be precisely determined."
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"Our finding that the in-vitro translation system was not able to recapitulate PKA dependent enhancement of HERG further points to the existence of a cellular co-factor that is not present in the reticulocyte lysate system."
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"3.8 MiRP (KCNE) proteins in the cAMP and PKA augmentation of HERG."
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"Activation of cAMP and PKA increased the abundance of HERG signal in both groups to a comparable degree as in cells transfected with HERG alone with no statistically significant difference."
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"A PKA inhibitor targeted to the ER surface (termed p4PKIg) completely abolished PKA mediated augmentation of HERG in HEK293 cells as well as rat neonatal cardiomyocytes."
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"3.7 14-3-3 interactions do not alter the PKA mediated increase in HERG abundance."
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"It is known that the hERG K + channel can be modulated by cAMP and PKA."
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"In light of the previous findings by Chen et al 2009 that the HERG mRNA remains stable and does not increase with 24 hours of kinase activation, our findings suggest that a short lived and/or newly transcribed protein is required for the PKA mediated increase in HERG protein abundance [XREF_BIBR]."
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"Our data suggest that mainly PKA is mediating the shift of the HERG activation kinetics."
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"AKAP5 anchors PKA to enhance regulation of the HERG channel."
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"AKAP5 anchors PKA to enhance regulation of the HERG channel."
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"Previous work showed that sustained protein kinase A (PKA) activity augments HERG protein abundance by a mechanism that includes enhanced protein translation."
PKA binds KCNH2.
| 4 2
PKA binds AKAP5 and KCNH2. 4 / 4
| 4
sparser
"The HERG channel protein, AKAP5, and PKA interacted with each other and appeared to form intracellular complexes."
sparser
"The HERG channel protein, AKAP5, and PKA interacted with each other and appeared to form intracellular complexes."
sparser
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
sparser
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
| 2
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"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
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"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
PKA inhibits KCNH2.
| 4
PKA inhibits KCNH2. 4 / 4
| 4
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"It has been demonstrated in the Xenopus laevis oocyte expression system that PKA can reduce hERG currents via direct phosphorylation of all four putative PKA consensus sites XREF_BIBR."
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"Furthermore, broad-specificity inhibitors of protein kinase A (PKA) or protein kinase C (PKC) failed to stimulate hERG down-regulation in the presence or absence of ouabain (unpublished data), suggesting that glycoside induced down-regulation of hERG is independent of PKA- and PKC dependent phosphorylation."
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"HERG current may be decreased by cAMP dependent activation of PKA; however, a putative direct binding of cAMP to the channel causes opposite effects."
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"Furthermore, broad-specificity inhibitors of protein kinase A (PKA) or protein kinase C (PKC) failed to stimulate hERG down-regulation in the presence or absence of ouabain (unpublished data), suggesting that glycoside induced down-regulation of hERG is independent of PKA- and PKC dependent phosphorylation."
| 3 40
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"HERG is blocked by bepridil (EC50 = 0.55 microM), verapamil (EC50 = 0.83 microM) and mibefradil (EC50 = 1.43 microM), whereas nitrendipine and diltiazem have negligible effects."
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"While quinidine, which blocks hERG, calcium and late sodium currents, and verapamil, which blocks hERG and calcium currents, are multichannel blockers, only quinidine was found to be associated with pro arrhythmic risk."
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"Verapamil block of HERG channels was use and frequency dependent, and verapamil unbound from HERG channels at voltages near the normal cardiac cell resting potential or with drug washout."
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"The treatment of the cells with hERG channel inhibitors such as nifekalant, E-4031, cisapride, terfenadine, and verapamil, recovered the prolonged AP and dose-dependently facilitated cell death upon ES."
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"Verapamil blocked hERG and hCav 1.2 in vitro at clinically relevant concentrations and showed no proarrhythmia markers in either experiments or simulations."
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"The ranolazine level obtained showed increased trough and peak levels, but the patient developed increasing episodes of TdP, which we attributed to high-affinity block of hERG by verapamil (XREF_TABLE)."
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"WT HERG is blocked in a concentration dependent manner by verapamil (half-maximal inhibition concentration [IC (50)] = 5.1 micromol/L), and the steady state activation and inactivation parameters are shifted to more negative values."
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"Dose response relationship characterizations of verapamil and rBeKm-1 blockage of hERG currents provided IC (50) values similar to values reported in the literature."
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"In some cases, compounds block hERG channels without prolonging the QT interval; for example, Verapamil blocks hERG potently, but does not prolong QT, probably due to the fact that this compound also blocks Ca channels.Arthur Brown (ChanTest; http://www.chantest.com) discussed some of the biophysical properties of hERG channels."
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"Neither verapamil nor dofetilide inhibited trafficking of wild type hERG."
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"These include false positives such as verapamil that are not cardiotoxic but block the hERG channel, as well as false negatives such as alfuzosin, which do not bind hERG but elicit QT prolongation through interactions with other ion channels XREF_BIBR, XREF_BIBR."
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"Verapamil and vanoxerine (GBR12909) which produce direct block of hERG current do not inhibit trafficking of wild type hERG after overnight exposure."
sparser
"Verapamil inhibits both hERG and calcium channels at therapeutic concentrations and does not induce a prolongation of the cardiac AP (e.g. ( xref ))."
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"This study investigated the mechanism by which verapamil, which blocks 10R1, l-type Ca2+ channel and the HERG channel, blocks ATP sensitive K+ (K (ATP)) channels."
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"Verapamil preferentially binds to and blocks open HERG channels."
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"Verapamil causes strong hERG potassium channel block, and even more potent L-type calcium channel block (XREF_FIG)."
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"For example, verapamil, which blocks both the HERG channel and a calcium channel, has a lower risk than expected from targeting the HERG channel alone."
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"Verapamil inhibits both hERG and calcium channels at therapeutic concentrations and does not induce a prolongation of the cardiac AP (e.g.)."
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"Verapamil is not associated with QT prolongation and TdP in humans, but inhibits hERG with an IC 50 of 0.94 muM (XREF_FIG and XREF_TABLE)."
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"However, as verapamil blocks cardiac calcium channels -- its primary mechanism, leading to QT shortening -- as well as hERG, the net effect on cardiac action potential duration is not markedly changed."
reach
"These properties are compared with four known HERG channel blockers including verapamil, cisapride, ketoconazole and dofetilide in the XREF_TABLE."
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"Likewise, verapamil enantiomers that blocked the L-type Ca 2+ channels also blocked the K + hERG1 channels, but they had equal potencies of inhibition when tested in Xenopus oocytes."
sparser
"One notable example is verapamil, which inhibits hERG in vitro but does not cause QT prolongation in vivo because of its additional calcium channel blocking properties. xref Although it inhibits hERG in vitro and causes QT prolongation, ranolazine is similarly free from proarrhythmia likely due to its additional late I Na channel blocking properties. xref The traditional gold standard is to measure I Kr in these heterologous expression systems by manual patch clamp, which is low throughput."
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"One notable example is verapamil, which inhibits hERG in vitro but does not cause QT prolongation in vivo because of its additional calcium channel blocking properties."
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"Verapamil, for instance, is a potent blocker of hERG repolarising current, but does not prolong the QT interval or cause TdP due to compensatory block of calcium channel depolarising current (Fauchier et al., 1999)."
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"An example is shown in XREF_FIG, hERG tail currents were blocked by verapamil in a concentration dependent manner with an IC 50 value of 0.94 muM."
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"In addition to blocking L-type Ca 2+ channels, verapamil has been found to block the hERG channel by binding to the helix residue Y652 and F656 in the S6 transmembrane domain."
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"N-methyl-verapamil, a membrane-impermeable, permanently charged verapamil analogue, blocked HERG channels only when applied intracellularly."
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"At clinically relevant concentrations, verapamil blocked hCav1.2 and hERG, as did vanoxerine and bepridil both of which also blocked hNav1.5."
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"The similar " crossover " on HERG tail currents has been reported for some known HERG channel blockers including the antiarrhythmics quinidine (Sanchez-Chapula et al., 2003) and verapamil, nervous system stimulant cocaine and some other quaternary ammonium compounds on the shaker potassium channels."
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"Besides affecting the calcium ion influx, verapamil also inhibits the hERG protein, similar to sotalol, but it does not increase the QT interval because the inhibition of both channels compensates [XREF_BIBR]."
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"Verapamil blocks both hERG and Cav 1.2 (I CaL)."
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"The verapamil metabolites D620 and D617 did not block HERG induced currents at concentrations of up to 30 microM (n = 3)."
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"Verapamil, for example, produces strong hERG inhibition without prolonging the QT interval in both animals and humans."
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"Verapamil was predicted to possibly cause bladder disorders and hERG channel inhibition."
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"In our experiments, verapamil caused high-affinity block of HERG current (IC50 = 143.0 nmol/L), a value close to those reported for verapamil block of L-type Ca2+ channels, whereas diltiazem weakly blocked HERG current (IC50 = 17.3 micromol/L), and nifedipine did not block HERG current."
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"Dofetilide, cisapride, sotalol, terfenadine and verapamil blocked hERG channels at 37degreesC with an IC50 of 7nM, 18nM, 343muM, 165nM and 214nM, respectively."
sparser
"For instance, verapamil inhibits hERG1 channels at clinically relevant concentrations, but it has no known risk for TdP due to its concomitant blockade of the depolarizing inward calcium current ( I Ca,L , through blockade of the calcium channel subunit Cav1.2), which alleviates the effects of reduced I Kr outward current xref , xref ."
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"Verapamil also produces high-affinity blockade of hERG currents, with an IC 50 of 143.0 nmol/L, close to its IC 50 for blockade of L-type calcium channels."
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"Verapamil blocks HERG channel by the helix residue Y652 and F656 in the S6 transmembrane domain."
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"When expressed in transfected COS cells, HERG is blocked in a concentration dependent manner by bepridil (EC50 = 0.55 microM), verapamil (EC50 = 0.83 microM), and mibefradil (EC50 = 1.43 microM), whereas nitrendipine and diltiazem have negligible effects."
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"However loss of indicator brightness represents a weakness in this strategy as although the anticipated CTD shortening with nifedipine was seen, the opposite trend due to off-target hERG block by verapamil was missed even though this was detected in parallel patching studies."
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"Verapamil antagonized dofetilide block of HERG channels, which suggests that they may share a common binding site."
Cisapride affects KCNH2
| 40
Cisapride inhibits KCNH2.
| 35
| 34
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"These values are similar to those observed for the inhibition of HERG by cisapride under identical experimental conditions."
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"The high-affinity intra-cavity blockade of hERG1 by cisapride depends on the hydrogen bonds formed by the pore-helix and on stabilizing aromatic interactions with residues in the S5 and S6 helices."
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"We tested the hypothesis that cisapride blocks HERG."
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"Under voltage-clamp conditions, cisapride block of HERG is dose dependent with a half-maximal inhibitory concentration of 6.5 nM at 22 degrees C (n = 25 cells)."
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"We found that although inactivation facilitated cisapride block of the HERG K+ current, it was not coupled with cisapride block of HERG when the Cs+ current was recorded."
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"Dofetilide, cisapride, sotalol, terfenadine and verapamil blocked hERG channels at 37degreesC with an IC50 of 7nM, 18nM, 343muM, 165nM and 214nM, respectively."
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"While cisapride inhibited potently the hERG channel currents, tegaserod failed to affect platelet aggregation, and had only a small contractile effect on the canine coronary artery at high concentrations."
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"The concentrations of cisapride needed to block HERG in the present study are likely to be encountered under certain clinical settings."
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"The observation that cisapride block of hERG loses its dependence upon the extent of inactivation when F656 is mutated, or when internal K + was substituted for Cs +, has added to this model to suggest that inactivation gating reconfigures the position of F656 to one that is conducive to high affinity binding of cisapride, and that the internal permeant ion influences this repositioning 38."
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"Furthermore, cisapride block of the HERG K+ current was not linked with inactivation in the mutant HERG channels F656V and F656M."
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"The postulated mechanism for this anti-proliferative effect is down-regulation of Cyclin D1, delaying progression through the cell cycle XREF_BIBR similar to what was observed with the hERG blocker cisapride XREF_BIBR."
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"Cisapride inhibited the HERG channels in a concentration dependent manner with an IC (50) of 2.4 10 (-7) M."
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"Using patch clamp electrophysiology, we found that cisapride was a potent inhibitor of HERG displaying an IC50 value of 44.5 nmol/l when tail currents at -40 mV were measured following a 2 s test depolarization to +20 mV."
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"One example of the latter has been documented by Di Diego et al XREF_BIBR who showed that cisapride (a potent blocker of HERG channel) induced transmural dispersion of repolarization and torsade de pointes in the canine left ventricular wedge preparation during epicardial stimulation."
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"Block of cardiac hERG K + channels by the antihistamine terfenadine and the prokinetic agent cisapride is associated with prolonged ventricular repolarization and an increased risk of ventricular arrhythmia."
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"The only compound that triggered EADs was hERG blocker Cisapride."
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"It should be mentioned that cisapride, dofetilide, and sotalol directly inhibit hERG channel activity whereas quinidine decreases the surface expression of hERG channels by suppressing hERG channel translocation to cell membrane surface XREF_BIBR."
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"Specifically, the KIC values were in agreement with the values reported for the L-type Ca 2+ channel blocker verapamil, the L-type Ca 2+ channel activator Bay K 8644, the K ATP channel opener levcromakalim, the hERG K + channel activator NS1463 and the hERG blockers cisapride and E-4031."
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"Our results suggest that inactivation facilitates cisapride block of HERG channels through affecting the positioning of Phe 656."
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"In the present study, we examined the effect of inactivation gating on cisapride block of HERG."
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"Finally, the IC 50 value for cisapride block of HERG under these conditions measured 6.70 nmol/l."
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"2 In a chronic transfection model using CHO-K1 cells, cisapride inhibited HERG tail currents after a step to +25 mV with similar potency at room and physiological temperatures (IC50 16."
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"At -20 mV, 10 nM cisapride reduced HERG tail-current amplitude by 5%, whereas, at + 20 mV, the tail-current amplitude was reduced by 45% (n = 4 cells)."
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"These results suggest that cisapride blocks an activated state of HERG, possibly the open state."
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"Blockage of the HERG human cardiac K+ channel by the gastrointestinal prokinetic agent cisapride."
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"These properties are compared with four known HERG channel blockers including verapamil, cisapride, ketoconazole and dofetilide in the XREF_TABLE."
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"As with dofetilide, HERG inhibition by cisapride required channel activation, which implies a predominant affinity for open and inactivated states of the HERG channel (Walker et al., 1999)."
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"Dofetilide and cisapride acutely inhibit hERG current."
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"Several other potent hERG channel blockers, such as astemizole and cisapride, were later reported to rescue the trafficking of LQT2 associated hERG channels harboring the G601S mutation."
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"These results demonstrate that at lower extracellular potassium concentrations, the permeant ion is almost exclusively responsible for the reduction in quinidine and cisapride block of HERG due to increases in extracellular potassium."
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"Cisapride at 6.3 muM reduced WT hERG channel currents by 80%, but only reduced S624A current by approximately 50% and Y652A current by approximately 15% (XREF_FIG)."
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"In this study, HERG block by quinidine and cisapride was assessed in extracellular solutions of calcium, potassium, rubidium, cesium and tetraethylammonium (TEA) using two-electrode voltage clamping of Xenopus oocytes."
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"XREF_BIBR Metoclopramide is also an antagonist at D 2 dopamine receptors and at 5-HT 3 receptors, while cisapride blocks 5-HT 2 and 5-HT 3 receptors and the human ether-a-go-go-related gene (hERG)-encoded K + channel."
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"This analysis shows that enhancements of endogenous HF oscillations in HR were also found in beagle dogs with dofetilide and with other hERG blockers such as cisapride, haloperidol, risperidone, DL sotalol, terfenadine and thioridazine."
| 1
reach
"Astemizole, terfenadine, cisapride, and MK-499 inhibited cERG and human ERG (hERG) currents with IC (50) values of 1.3, 13, 19, and 15 nM and 1.2, 9, 14, and 21 nM, respectively, and competitively displaced [(35) S] MK-499 binding from cERG and hERG with IC (50) values of 0.4, 12, 35, and 0.6 nM and 0.8, 5, 47, and 0.7 nM, respectively."
Cisapride activates KCNH2.
| 3
| 2
reach
"Cisapride dramatically enhanced the rate of HERG current decay while having no apparent effect on the initial phase of current activation."
reach
"The main effect of cisapride was to enhance the rate of HERG current decay thereby reducing current at the end of the voltage clamp pulse."
Cisapride activates KCNH2-G601S. 1 / 1
| 1
reach
"Quinidine, astemizole, cisapride, and E4031 successfully rescued the trafficking deficient mutation G601S hERG, and the rescue relied on their interaction with F656 [XREF_BIBR]."
Cisapride decreases the amount of KCNH2.
| 1
Cisapride decreases the amount of KCNH2. 1 / 1
| 1
reach
"Cisapride and quinidine do not inhibit the surface expression of hERG XREF_BIBR."
Cisapride binds KCNH2.
| 1
reach
"Intracellular K+ is required for the inactivation induced high-affinity binding of cisapride to HERG channels."
HSPA affects KCNH2
| 1 13 27
HSPA binds KCNH2.
| 13 11
| 8 11
reach
"The formation of the Hsp70 and hERG complex, on the other hand, was unaffected by hypoxia treatment (lane 5 and 6)."
reach
"It has been reported that hERG formed complexes with Hsp70 27."
reach
"These results indicate that THIO disturbed the folding process of the hERG channel by reducing the interaction between hERG and Hsp70, eventually leading to the degradation of disordered hERG proteins."
reach
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
reach
"Our data demonstrated that both Kv4.3 and hERG interacted with Hsp70, suggesting that Hsp70 may form complexes with hERG and Kv4.3."
reach
"To determine the mechanism of trafficking inhibition, we performed western blot and immunoprecipitation to test folding of hERG by assessing interaction between hERG and Hsp90 and Hsp70."
sparser
"Hsp70 interacts with the nascent hERG in the ER while Hsp90 interacts with the terminal hERG in the cytoplasm to facilitate folding [ xref ]."
reach
"Our coimmunoprecipitation results show that THIO aggravated the ubiquitination of the hERG protein (XREF_FIG), and the interactions between hERG and Hsp70 were decreased (XREF_FIG)."
reach
"Ficker et al. showed that the cytosolic chaperones Hsp70 interacted with hERG during maturation 27."
sparser
"This effect may have increased the interaction between the initial hERG and Hsp70."
reach
"Hsp70 interacts with the nascent hERG in the ER while Hsp90 interacts with the terminal hERG in the cytoplasm to facilitate folding [XREF_BIBR]."
sparser
"Our coimmunoprecipitation results show that THIO aggravated the ubiquitination of the hERG protein ( xref ), and the interactions between hERG and Hsp70 were decreased ( xref )."
reach
"As illustrated in Figures XREF_FIG and XREF_FIG, hERG and Hsp70 complexes were decreased in the presence of 3muM THIO."
sparser
"These results indicate that THIO disturbed the folding process of the hERG channel by reducing the interaction between hERG and Hsp70, eventually leading to the degradation of disordered hERG proteins."
sparser
"Meanwhile, THIO increased the degradation of hERG channels via disrupting hERG-Hsp70 interactions."
sparser
"We therefore turned to exploring whether THIO prevents maturation of hERG channels via inhibiting chaperone-hERG interactions; to this end, we performed coimmunoprecipitation experiments to determine the association of hERG protein with Hsp70."
sparser
"Therefore, it would be difficult for Hsp70 to recognize and interact with the hERG protein, thereby elongating the interaction of the early hERG protein with Hsp70 and reducing the interaction of hERG protein with Hsp90."
sparser
"The interaction between hERG protein and Hsp90 reduced while the interaction between hERG protein and Hsp70 increased by DHB."
reach
"This effect may have increased the interaction between the initial hERG and Hsp70."
HSP90 binds HSPA and KCNH2. 2 / 2
| 2
sparser
"Mutations such as R752W and G601S strengthen the interaction of hERG with Hsp70 and Hsp90."
sparser
"It could be that hypoxia inhibits Hsp90 binding to hERG by reducing steady state expression levels of endogenous Hsp90 and/or Hsp70."
HSPA binds HSPA8 and KCNH2. 1 / 1
| 1
sparser
"Interestingly, although both Hsp70 and Hsc70 associated with hERG channels, it was reported that Hsp70 enhanced the maturation of hERG channels while Hsc70 suppressed their maturation xref ."
HSPA binds KCND3 and KCNH2. 1 / 1
| 1
sparser
"In addition, Hsp70 interacted with hERG and Kv4.3 respectively, and formed complexes with hERG and Kv4.3."
| 1
sparser
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
HSPA increases the amount of KCNH2.
| 1 5
Modified HSPA increases the amount of KCNH2. 3 / 3
| 3
reach
"Li et al. reported that coexpression of Hsp70 increased the expression of hERG protein with a concomitant decrease in the ubiquitinated form of the protein [XREF_BIBR]."
reach
"Finally, coexpression of RNF207 and HSP70 increased HERG expression compared with HSP70 alone."
reach
"Since previous study showed that overexpression of Hsp70 increased the expression of hERG protein 27, we therefore hypothesized that Kv4.3 increased the hERG protein expression via upregulation of Hsp70."
HSPA increases the amount of KCNH2. 2 / 2
| 1 2
reach
"It has been reported that heat shock protein 70 (Hsp70) increases Kv1.5 and hERG protein expressions by stabilizing the proteins [10,11]."
reach
"These data indicate that Hsp70 increases hERG protein expression and forms complexes with hERG via two independent mechanisms."
HSPA decreases the amount of KCNH2.
| 4
HSPA decreases the amount of KCNH2. 4 / 4
| 4
reach
"Knockdown of HSP70 reduced overall levels of WT hERG, but knockdown of HSC70 increased hERG levels."
reach
"However, although downregulation of Hsp70 decreased hERG protein expression in cells co-transfected with Kv4.3 and hERG, Hsp70 did not play a critical role in the complex formation between hERG and Kv4.3."
reach
"The upregulation of hERG expression by Kv4.3 is dependent on Hsp70, as Hsp70 siRNA could prevent the Kv4.3-induced hERG expression."
reach
"The results showed that downregulation of Hsp70 using siRNA or VER155008 effectively abolished the elevation of matured hERG protein expression in the cells co-transfected with hERG and Kv4.3."
HSPA activates KCNH2.
| 4
HSPA activates KCNH2. 3 / 3
| 3
reach
"Furthermore, it is possible that combined manipulation of HSC70, HSP70 and DNAJA1 could enhance their assistance of hERG folding, for at least some of the LQT2 mutants."
reach
"A concern to be addressed will be pleiotropic effects of such therapies - for example, inhibition of HSP70 to relieve CHIP mediated degradation of DeltaF508 CFTR could also impair HSP70 dependent folding of hERG, leading to cardiac arrhythmias in CF patients."
reach
"Interestingly, although both Hsp70 and Hsc70 associated with hERG channels, it was reported that Hsp70 enhanced the maturation of hERG channels while Hsc70 suppressed their maturation 59."
Modified HSPA activates KCNH2. 1 / 1
| 1
reach
"Coexpression of Hsp70 with hERG in HEK293 cells suppressed hERG ubiquitination and increased the levels of both immature and mature forms of hERG."
HSPA inhibits KCNH2.
| 2
HSPA inhibits KCNH2. 2 / 2
| 2
reach
"In contrast, another member of the Hsp70 family, heat shock cognate protein 70 (Hsc70) was shown to initiate degradation of hERG and CFTR [11,12]."
reach
"Here, we demonstrate that the Hsp70 nucleotide exchange factor Bag1 promotes hERG degradation by the ubiquitin-proteasome system at the endoplasmic reticulum to regulate hERG levels and channel activity."
HSPA deubiquitinates KCNH2.
| 1
Modified HSPA leads to the deubiquitination of KCNH2. 1 / 1
| 1
reach
"Coexpression of Hsp70 with hERG in HEK293 cells suppressed hERG ubiquitination and increased the levels of both immature and mature forms of hERG."
HSP90 affects KCNH2
| 3 21 16
HSP90 binds KCNH2.
| 1 20 10
| 1 15 10
sparser
"To further confirm the role of ROS in Hsp90 binding to hERG, normoxic cells were exposed to xanthine/xanthine oxidase (X/XO; 500µm/5milliunits/ml), which generates O 2 − ."
sparser
"The modulation of Hsp90 interaction with hERG during hypoxia is mediated by ROS generated during prolonged hypoxic exposure."
sparser
"Our pulse chase studies show that hypoxia inhibits progression of the cg form into the fg form of hERG due to a direct consequence of the interference of Hsp90 binding to nascent hERG molecules."
sparser
"The complete absence of Hsp90 binding to hERG during hypoxia observed in our studies is in contrast to what is observed with trafficking-deficient LQT2 mutants (hERG R752W and G601S), in which the interactions of Hsp90 and Hsp70 are increased for both mutants [ xref ]."
sparser
"Moreover, enhancement of the HERG:HSP90 interaction is responsible for the increased membrane trafficking induced by estradiol xref ."
sparser
"The decrease in translation may be an important adaptive response of cells, triggered by the hERG protein that cannot bind to Hsp90 and fold successfully."
reach
"The modulation of Hsp90 interaction with hERG during hypoxia is mediated by ROS generated during prolonged hypoxic exposure."
reach
"It could be that hypoxia inhibits Hsp90 binding to hERG by reducing steady state expression levels of endogenous Hsp90 and/or Hsp70."
sparser
"Hsp70 interacts with the nascent hERG in the ER while Hsp90 interacts with the terminal hERG in the cytoplasm to facilitate folding [ xref ]."
reach
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
sparser
"Hsp90 was downregulated by DHB, which may have directly decreased the interaction between the terminal hERG protein and Hsp90 and resulted in an accumulation of a large quantity of hERG protein that folded incorrectly."
sparser
"Prolonged association of hERG with molecular chaperone Hsp90 resulting in complex oligomeric insoluble aggregates contributed to ER accumulation and trafficking defect."
reach
"To further confirm the role of ROS in Hsp90 binding to hERG, normoxic cells were exposed to xanthine and xanthine oxidase (X/XO; 500microm/5milliunits/ml), which generates O 2 -."
sparser
"Therefore, it would be difficult for Hsp70 to recognize and interact with the hERG protein, thereby elongating the interaction of the early hERG protein with Hsp70 and reducing the interaction of hERG protein with Hsp90."
reach
"To determine the mechanism of trafficking inhibition, we performed western blot and immunoprecipitation to test folding of hERG by assessing interaction between hERG and Hsp90 and Hsp70."
sparser
"Two mechanisms could account for how ROS regulates hERG protein interaction with Hsp90."
sparser
"The interaction between hERG protein and Hsp90 reduced while the interaction between hERG protein and Hsp70 increased by DHB."
reach
"However, Hsp90 preferably interacted with hERG in cells co-transfected with hERG and Kv4.3 and enhanced the expression of 135kDa hERG."
reach
"Immunoprecipitation with anti-Hsp90 showed that Hsp90 interacted with hERG in cells co-transfected with hERG and Kv4.3."
reach
"The complete absence of Hsp90 binding to hERG during hypoxia observed in our studies is in contrast to what is observed with trafficking deficient LQT2 mutants (hERG R752W and G601S), in which the interactions of Hsp90 and Hsp70 are increased for both mutants [XREF_BIBR]."
reach
"Two mechanisms could account for how ROS regulates hERG protein interaction with Hsp90."
sparser
"Our finding that ROS scavengers restore hERG interaction with Hsp90 could account for the stabilization of hERG protein by antioxidants during hypoxia."
sparser
"This was supported by demonstration of a unique and specific KCNH2 interaction with Hsp90 over several other K channels lacking these domains."
sparser
"We therefore investigated whether ROS, by modulating the interaction of hERG with Hsp90, mediates hypoxia-induced hERG downregulation."
reach
"Hsp70 interacts with the nascent hERG in the ER while Hsp90 interacts with the terminal hERG in the cytoplasm to facilitate folding [XREF_BIBR]."
HSP90 binds HSPA and KCNH2. 2 / 2
| 2
sparser
"Mutations such as R752W and G601S strengthen the interaction of hERG with Hsp70 and Hsp90."
sparser
"It could be that hypoxia inhibits Hsp90 binding to hERG by reducing steady state expression levels of endogenous Hsp90 and/or Hsp70."
sparser
"For example, the reactive oxygen species (ROS) generated during hypoxia have been shown to inhibit protein folding and maturation by interfering with the interaction between hERG and the Hsp90 chaperone complex [ xref ]."
HSP90 binds CTSG and KCNH2. 1 / 1
| 1
sparser
"More importantly, addition of MnTMPyP during hypoxia restored Hsp90 interaction with cg form of hERG (lane 3 vs lane 4, xref )."
| 1
sparser
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
HSP90 activates KCNH2.
| 1 3
HSP90 activates KCNH2. 3 / 3
| 1 3
reach
"Hsp90 induced increase of functional HERG proteins was verified by their increased expression on the cell surface and enhanced HERG channel currents."
reach
"Inhibition of Hsp90 chaperone prevents maturation and increases proteasomal degradation of hERG, reducing the number of mature channels available to be incorporated into the cell membrane."
reach
"Inhibition of Hsp90 prevents maturation and reduces hERG and IKr currents."
HSP90 increases the amount of KCNH2.
| 2
HSP90 increases the amount of KCNH2. 2 / 2
| 2
reach
"HSP90 inhibition impaired hERG trafficking, and HSP70 overexpression increased overall hERG levels moderately."
reach
"Hsp90 was also reported to enhance hERG protein expression 30."
HSP90 inhibits KCNH2.
| 1 1
HSP90 inhibits KCNH2. 1 / 1
| 1 1
sparser
"It has previously been demonstrated that the Hsp90 inhibitor, geldanamycin, inhibits hERG trafficking, presumably through an Hsp90-dependent mechanism. xref Given the intense pharmaceutical interest in the development of Hsp90 inhibitors as therapies for cancer and other diseases, the importance of identifying the isoform dependency of this client protein is clear, as pan -inhibition may result in undesired effects."
HSP90 deubiquitinates KCNH2.
| 1
Modified HSP90 leads to the deubiquitination of KCNH2. 1 / 1
| 1
reach
"Co-expression of Hsp90 counteracted the effects of Hsp90 inhibitors and suppressed ubiquitination of HERG proteins."
BBR affects KCNH2
| 2 29
BBR inhibits KCNH2.
| 2 14
BBR inhibits KCNH2. 16 / 16
| 2 14
reach
"It has been confirmed that BBR could block the hERG channel and prolong action potential duration (APD) [XREF_BIBR, XREF_BIBR]."
reach
"Previous report illustrated that BBR acutely block hERG channel by interacting with specific residues (Tyr652 and Phe656)."
reach
"XREF_BIBR However, there was no report to elucidate that the binding sites mediate hERG reduction triggered by BBR incubation."
reach
"BBR decreased the expression of cav-1 (XREF_FIG) and knocking down the basal expression of cav-1 alleviated BBR induced hERG decrease on plasma membrane (XREF_FIG)."
reach
"At concentrations similar to the IC 50 of = ~ 3 microM for CGN viability, BBR inhibits delayed rectifier currents and HERG channels XREF_BIBR, XREF_BIBR, XREF_BIBR."
sparser
"In this report, we tested three drugs for their ability to rescue BBR-induced hERG inhibition."
reach
"Previous studies have demonstrated that BBR blocks hERG channels and prolongs action potential duration (APD)."
reach
"In summary, we clarified that disruption of cav-1 and binding to the residues, Tyr652 and Phe656, are responsible for BBR induced hERG reduction on the membrane, which contribute to better understanding of the mechanisms underlying drug induced LQTS."
reach
"XREF_BIBR Hence, we conclude that BBR reduces surface hERG protein through promoting hERG internalization due to its co-localization with cav-1 on the membrane."
sparser
"As shown in xref , the fully glycosylated 155 kDa hERG protein inhibited by 10 μM BBR was successfully restored by all these drugs and there was no distinct difference among their ability to rescue hERG trafficking."
reach
"Considering both our previous and present work, we propose that BBR reduces hERG membrane stability with multiple mechanisms."
reach
"Knocking down the basal expression of caveolin-1 alleviates BBR induced hERG reduction."
reach
"BBR has been reported previously to block hERG currents expressed in HEK-293 cells and Xenopus oocytes after acute application."
reach
"XREF_BIBR Recently, we found that long-term application of BBR induced hERG channel reduction by disrupting channel trafficking."
reach
"Previous researches showed that BBR acutely blocks hERG channel in Xenopus oocytes by interacting with the two aromatic amino acid residues (tyrosine [Tyr652] and phenylalanine [Phe656], which are thought as the universal binding sites for various hERG channel blockers) located in S6 transmembrane helix."
reach
"BBR inhibited hERG channel on membrane via cav-1 interference."
BBR activates KCNH2.
| 12
BBR activates KCNH2. 12 / 12
| 12
reach
"Moreover, we first investigated the pharmacological rescue of BBR triggered hERG defect and provided reference for clinical safety of BBR."
reach
"Our study demonstrates that BBR induces hERG channel deficiency by inhibiting channel trafficking after incubation for 24h."
reach
"In this study, we tested three drugs that have previously been reported to rescue trafficking deficient hERG channel for restoration of BBR induced hERG defect."
reach
"The result surprisingly manifested that binding to the two residues accounts for BBR induced hERG defect."
reach
"Pharmacological rescue of BBR induced hERG channel deficiency."
reach
"Mature hERG (155 kDa) was reduced, whereas ER located hERG (135 kDa) was increased by BBR."
reach
"Together, these data illustrate that resveratrol and fexofenadine showed functional rescue of hERG channel deficiency triggered by BBR, while astemizole only recovered protein expression."
reach
"To seek rescue strategies for BBR induced hERG channel deficiency, we chose three drugs (resveratrol, astemizole, and fexofenadine, which were previously used to correct trafficking of hERG channel) to test whether the misprocessed hERG channel by BBR could be transported to the cell surface."
reach
"Phe656 and Tyr652 binding accounts for BBR induced hERG channel deficiency."
reach
"These results suggest that BBR induced hERG channel deficiency was on account of Phe656 and Tyr652 binding."
reach
"To clarify whether hERG channel deficiency caused by BBR incubation was also on account of Phe656 and Tyr652 binding similar to acute application of BBR."
reach
"In this study, we demonstrated that 1) cav-1 participates in BBR induced hERG deficiency on cell surface; 2) residues Tyr652 and Phe656, essential components of hERG binding sites, mediate hERG surface expression inhibition by BBR incubation; and 3) fexofenadine and resveratrol can shorten APD of ventricular cardiomyocytes prolonged by BBR."
BBR decreases the amount of KCNH2.
| 3
BBR decreases the amount of KCNH2. 3 / 3
| 3
reach
"XREF_BIBR In addition, we recently reported that BBR reduces hERG plasma membrane expression, through disrupting trafficking after long-term exposure."
reach
"This study was designed to investigate in detail how BBR decreased hERG expression on cell surface and further explore its pharmacological rescue strategies."
reach
"Together, these results suggested that BBR could reduce hERG expression on membrane by interfering with cav-1."
KCNH2 affects HSP90
| 1 20 10
| 1 15 10
sparser
"To further confirm the role of ROS in Hsp90 binding to hERG, normoxic cells were exposed to xanthine/xanthine oxidase (X/XO; 500µm/5milliunits/ml), which generates O 2 − ."
sparser
"The modulation of Hsp90 interaction with hERG during hypoxia is mediated by ROS generated during prolonged hypoxic exposure."
sparser
"Our pulse chase studies show that hypoxia inhibits progression of the cg form into the fg form of hERG due to a direct consequence of the interference of Hsp90 binding to nascent hERG molecules."
sparser
"The complete absence of Hsp90 binding to hERG during hypoxia observed in our studies is in contrast to what is observed with trafficking-deficient LQT2 mutants (hERG R752W and G601S), in which the interactions of Hsp90 and Hsp70 are increased for both mutants [ xref ]."
sparser
"Moreover, enhancement of the HERG:HSP90 interaction is responsible for the increased membrane trafficking induced by estradiol xref ."
sparser
"The decrease in translation may be an important adaptive response of cells, triggered by the hERG protein that cannot bind to Hsp90 and fold successfully."
reach
"The modulation of Hsp90 interaction with hERG during hypoxia is mediated by ROS generated during prolonged hypoxic exposure."
reach
"It could be that hypoxia inhibits Hsp90 binding to hERG by reducing steady state expression levels of endogenous Hsp90 and/or Hsp70."
sparser
"Hsp70 interacts with the nascent hERG in the ER while Hsp90 interacts with the terminal hERG in the cytoplasm to facilitate folding [ xref ]."
reach
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
sparser
"Hsp90 was downregulated by DHB, which may have directly decreased the interaction between the terminal hERG protein and Hsp90 and resulted in an accumulation of a large quantity of hERG protein that folded incorrectly."
sparser
"Prolonged association of hERG with molecular chaperone Hsp90 resulting in complex oligomeric insoluble aggregates contributed to ER accumulation and trafficking defect."
reach
"To further confirm the role of ROS in Hsp90 binding to hERG, normoxic cells were exposed to xanthine and xanthine oxidase (X/XO; 500microm/5milliunits/ml), which generates O 2 -."
sparser
"Therefore, it would be difficult for Hsp70 to recognize and interact with the hERG protein, thereby elongating the interaction of the early hERG protein with Hsp70 and reducing the interaction of hERG protein with Hsp90."
reach
"To determine the mechanism of trafficking inhibition, we performed western blot and immunoprecipitation to test folding of hERG by assessing interaction between hERG and Hsp90 and Hsp70."
sparser
"Two mechanisms could account for how ROS regulates hERG protein interaction with Hsp90."
sparser
"The interaction between hERG protein and Hsp90 reduced while the interaction between hERG protein and Hsp70 increased by DHB."
reach
"However, Hsp90 preferably interacted with hERG in cells co-transfected with hERG and Kv4.3 and enhanced the expression of 135kDa hERG."
reach
"Immunoprecipitation with anti-Hsp90 showed that Hsp90 interacted with hERG in cells co-transfected with hERG and Kv4.3."
reach
"The complete absence of Hsp90 binding to hERG during hypoxia observed in our studies is in contrast to what is observed with trafficking deficient LQT2 mutants (hERG R752W and G601S), in which the interactions of Hsp90 and Hsp70 are increased for both mutants [XREF_BIBR]."
reach
"Two mechanisms could account for how ROS regulates hERG protein interaction with Hsp90."
sparser
"Our finding that ROS scavengers restore hERG interaction with Hsp90 could account for the stabilization of hERG protein by antioxidants during hypoxia."
sparser
"This was supported by demonstration of a unique and specific KCNH2 interaction with Hsp90 over several other K channels lacking these domains."
sparser
"We therefore investigated whether ROS, by modulating the interaction of hERG with Hsp90, mediates hypoxia-induced hERG downregulation."
reach
"Hsp70 interacts with the nascent hERG in the ER while Hsp90 interacts with the terminal hERG in the cytoplasm to facilitate folding [XREF_BIBR]."
HSP90 binds HSPA and KCNH2. 2 / 2
| 2
sparser
"Mutations such as R752W and G601S strengthen the interaction of hERG with Hsp70 and Hsp90."
sparser
"It could be that hypoxia inhibits Hsp90 binding to hERG by reducing steady state expression levels of endogenous Hsp90 and/or Hsp70."
sparser
"For example, the reactive oxygen species (ROS) generated during hypoxia have been shown to inhibit protein folding and maturation by interfering with the interaction between hERG and the Hsp90 chaperone complex [ xref ]."
HSP90 binds CTSG and KCNH2. 1 / 1
| 1
sparser
"More importantly, addition of MnTMPyP during hypoxia restored Hsp90 interaction with cg form of hERG (lane 3 vs lane 4, xref )."
| 1
sparser
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
KCNH2 affects LQT2
| 29
KCNH2 activates LQT2.
| 26
KCNH2 activates LQT2. 21 / 21
| 21
reach
"Mutations in HERG on chromosome 7q35-36, encoding potassium channels (Ikr), cause LQT2, and block of Ikr is a known mechanism for drug induced prolongation of cardiac action potentials, which provides a mechanistic link between LQT2 and certain forms of acquired LQT."
reach
"We identified a novel BP mutation in KCNH2 that disrupts the intron 9 acceptor splice site definition and causes LQT2."
reach
"Several reports described mutations in the C-terminus region exhibiting a loss of function in the HERG channel to cause LQT2 [8-12]."
reach
"Mutations in hERG channel can cause LQT2 and several disease related mutations have been identified in the CNBHD."
reach
"Mutations in hERG cause the congenital form of long QT syndrome type 2 (LQT2), an inherited autosomal dominant disorder characterized by prolonged QT interval on the electrocardiogram."
reach
"Among them most common are LQT1, LQT2, and LQT3, caused by mutations in KCNQ1, KCNH2, and SCN5A genes, respectively (Splawski etal."
reach
"XREF_BIBR In addition, a wide variety of potentially dangerous proarrhythmic effects of antiarrhythmic or nonantiarrhythmic drugs have been recognized to inhibit hERG channels, which could induce acquired LQT2."
reach
"Its stability was partially restored by HSF-1, indicating that HSF-1 is a target for the treatment for LQT2 caused by the A78T mutation in HERG."
reach
"The stability of the mutant was partially restored by HSF-1, indicating that HSF-1 is a target for the treatment for LQT2 caused by the A78T mutation in HERG."
reach
"LQT1 and LQT2 are caused by missense mutations of the KCNH1 and KCNH2 gene, respectively."
reach
"Failure of HERG trafficking is known to cause LQT2, and this identified a molecular mechanism underlying this defect."
reach
"According to the on-line inherited arrhythmias database (http://www.fsm.it/cardmoc/), 291 different mutations in hERG1 were reported to cause LQT2 as of September 2009."
reach
"LQT2 is caused by mutations in the hERG gene, most of which are missense mutations resulting in a single amino acid change."
reach
"Its stability was partially restored by HSF-1, indicating that HSF-1 is a potential target for the treatment for LQT2 caused by the A78T mutation in HERG."
reach
"LQT1 and LQT2 are caused by gene mutations in KCNQ1 and KCNH2, respectively, and mutations in these 2 genes are responsible for about 85% of LQTS linked mutations."
reach
"Defects in KCNQ and hERG channels have been shown to cause LQT1 and LQT2, respectively and cardiac arrhythmias in humans."
reach
"LQT1, LQT2, and LQT3 are caused by mutations in KCNQ1 (LQT1), KCNH2 (LQT2), and SCN5A (LQT3), which account for approximately 90% of genotyped LQTS patients."
reach
"The majority of hERG trafficking studies target LQT2 clinically relevant missense mutations and PAS truncations XREF_BIBR."
reach
"LQT2 is caused by mutations in the KCNH2 (also known as human Ether-a-go-go Related Gene; HERG) gene, which forms the alpha-subunit of the rapid acting inward rectifying potassium (I kr) channel."
reach
"However, mutations in three genes (KCNQ1 mediated LQT1, KCNH2 mediated LQT2, and SCN5A mediated LQT3) account for 75% of clinically definite LQTS."
reach
"[XREF_BIBR] A total of 16 genes associate with LQTS, and mutations in KCNQ1 or KCNH2 genes cause the most common subtypes LQT1 and LQT2, respectively."
Mutated KCNH2 activates LQT2. 5 / 5
| 5
reach
"LQT2 is caused by mutations of the HERG or KCNE2 genes."
reach
"In the case of LQT type 1 (LQT1), the mutations are present in the KCNQ1 gene which encodes the alpha-subunit of the slow component of the delayed rectifier potassium current (K v 7.1), whereas LQT2 is caused by mutations of the KCNH2 gene which encodes the alpha-subunit of the rapid component of the delayed rectifier potassium current (K v 11.1)."
reach
"More than 500 hERG mutations having been identified, amongst which majority caused LQT2 due to HERG protein trafficking deficiency [XREF_BIBR]."
reach
"[31] reported an I593R mutation in HERG, all confirming that mutation of HERG causes LQT2."
reach
"Functional impairment of the hERG channel can result in inherited and acquired long QT syndrome type 2 (LQT2), caused by mutations of the hERG or off-target effects of diverse therapeutic agents, respectively [XREF_BIBR]."
KCNH2 inhibits LQT2.
| 2
Mutated KCNH2 inhibits LQT2. 1 / 1
| 1
reach
"Loss-of-function hERG mutations are well established to underlie the LQT2 form of congenital Long QT syndrome and, within the last decade, gain-of-function hERG mutations have been linked to the SQT1 form of the short QT syndrome."
KCNH2 inhibits LQT2. 1 / 1
| 1
reach
"LQT2 induced by hERG drug block (acquired LQT2) has received considerable attention over the past twenty years as hERG has been found to be uniquely susceptible to block by a wide array of drugs across multiple pharmaceutical classes XREF_BIBR, XREF_BIBR."
KCNH2 binds LQT2.
| 1
KCNH2 binds LQT2. 1 / 1
| 1
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"We demonstrate that both K + depletion and selected LQT2 associated mutations compromise hERG structural stability at the PM."
Sodium atom affects KCNH2
| 6 21
Sodium atom inhibits KCNH2.
| 6 16
| 16
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"(d) C-type inactivation in Shaker is associated with a decrease in P K / P Na, whereas in HERG a disruption of C-type inactivation is associated with a decrease in P K / P Na (this report)."
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"Most voltage gated K + currents are relatively insensitive to extracellular Na + (Na + o), but Na + o potently inhibits outward human ether-a-go-go-related gene (HERG)-encoded K + channel current (Numaguchi, H., J.P. Johnson, Jr., C.I. Petersen, and J.R. Balser."
reach
"Quantitatively similar effects of Na + i to inhibit HERG current were seen in the WT and S624A channels."
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"Na + Permeation through Inactivated hERG Channels."
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"External Na + has been reported to block hERG K + current and the S624 residue was believed to be involved in the block."
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"We also found that external Na + potently blocked the hERG outward Na + current with an IC 50 of 3.5 mM."
reach
"Inhibition of the hERG Na + Current by External Na + Ions."
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"We further found that the hERG Na + current can be blocked by external Na +, and the residues in the channel pore and S6 regions, including the serine residues at 624 and 641 as well as the phenylalanine in the signature motif of the selectivity filter, are involved in the block."
reach
"Although Na + o blocked hERG Na + current, a robust outward hERG Na + current indicates that intracellular Na + (Na + i) does not block the channels."
reach
"Although the physiological relevance of Na + i block in other K + channels has remained somewhat unclear, a functional role for block of HERG by Na + i can be rationalized in a satisfying way."
reach
"The Na + o block of hERG K + currents has been reported previously, and the IC 50 value for Na + o to block the hERG Na + current is close to that for Na + o to block hERG K + currents."
reach
"Since the F627Y and S641A significantly accelerated hERG inactivation, whereas S624A slightly decelerated it, inactivation gating seems not to be involved in the Na + o block of hERG channels."
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"In addition to these direct anti-chaperone effects on HERG processing, the Na + / K + ATPase inhibitor digoxin indirectly disrupts HERG biogeneisis via a [K+] i -dependent conformational defect in HERG folding [XREF_BIBR], underscoring the intricacies of studying pharmacological chaperoning."
reach
"The data suggest that Ba 2+ sweeps Na + o from the pore as it exits inactivated HERG channels (XREF_FIG B, cartoon)."
reach
"Our experiments in this study support the conclusion that Na + o inhibits HERG current by binding to an outer pore site."
reach
"Physiologic [Na +] i blocks HERG current at depolarized potentials (XREF_FIG) and block is relieved by physiologic [K +] o (XREF_FIG)."
| 6
sparser
"The time constants of the hERG Na + current inactivation (τ inact ) were plotted against the test voltages ( xref )."
sparser
"Further, Ba 2+ o was found to relieve Na + o inhibition of HERG ( xref ), and Na + o was able to protect against onset of Ba 2+ o effects ( xref )."
sparser
"Inhibition of WT HERG by Na(+)(o) was not strongly dependent on the voltage during activating pulses."
sparser
"The relief of Na + o inhibition of WT HERG by Ba 2+ o ( xref ) could conceivably be explained by competition of the two cations for a common site."
sparser
"The predictable outward tail currents recorded from WT channels in those conditions (data not shown) were small due to the fact that extracellular sodium potently inhibits hERG channels when extracellular K + is removed ( 33,34 )."
sparser
"To examine the voltage dependence of the hERG Na + current inactivation, a depolarizing step to 70 mV for 250 ms was used to induce the peak Na + current."
| 5
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"Our studies of the Na + o interaction with HERG began with attempts to understand the anti-Nernstian effect of K + o and suggested that K + o acts to potently relieve inhibition of outward HERG K + current by Na + o."
reach
"Although such effects could be consistent with a mechanism in which Na + o preferentially interacts with the HERG inactivated state, the permeability of these mutant channels to Na + limits their utility for studying inhibition of outward HERG K + current by Na + o."
reach
"Here we have focused directly on the interaction between Na + o and HERG, with a view to developing a more precise biophysical understanding of the Na + o effect and thereby illuminating the Na + o -K + o interaction."
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"The ability of Na + o to occupy the HERG outer pore as demonstrated in this study does not exclude the possibility that Na + o preferentially interacts with the HERG inactivated state."
reach
"We studied wild-type (WT) and mutant HERG currents and used two strategic probes, intracellular Na + (Na + i) and extracellular Ba 2+ (Ba 2+ o), to define a site where Na + o interacts with HERG."
| 3 1 26
| 2 17
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"We hypothesized that pharmacological targeting of hERG protein would inhibit tumor growth by inducing apoptosis of GB cells."
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"Silencing HERG inhibited the apoptosis induced by cisplatin both in vitro and in vivo, by attenuating the cisplatin effects on Bcl-2, Bax and active caspase-3."
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"XREF_BIBR By the silencing method, we found that downregulation of hERG caused cell death and apoptosis in HTC/3 cells."
reach
"The small molecule hERG ligand doxazosin induced concentration dependent apoptosis of human LNT-229 (EC 50 = 35 microM) and U87MG (EC 50 = 29 microM) GB cells, accompanied by cell cycle arrest in the G0/G1 phase."
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"HERG potassium channels, previously recognized to regulate cardiac action potential repolarization, modulate GB cell apoptosis."
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"SiRNA Inactivation of hERG K + Channels Triggers Apoptosis of GB Cells."
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"37 Cell type- and environment specific effects on apoptosis are suggested by reports of hERG activity promoting apoptosis."
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"Also, Staudacher et al. found that the hERG1 small molecule ligand doxazosin induces the apoptosis of glioblastoma cells XREF_BIBR."
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"RNA interference of hERG also modulated HTC/3 cell apoptosis, since a 72-hour treatment of nano-siRNA significantly increased the portion of early apoptosis cells (annexin V +/PI-) versus the control (15.5% +/- 0.8% versus 3.2% +/- 0.3%, P < 0.01, XREF_FIG)."
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"XREF_BIBR, XREF_BIBR, XREF_BIBR In our experimental conditions, hyperstimulation of the hERG1 channel did not induce apoptosis after arresting the cells in the G0/G1 phase."
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"The study indicated that siRNA was successfully transferred to the target cells and knocked down hERG that inhibited cell growth and induced apoptosis in ATC cells in vitro."
reach
"XREF_FIG - XREF_FIG, hERG1 downregulation and/or inhibition prevented proliferation and invasion, and induced apoptosis of osteosarcoma cells."
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"Here, we show that HERG conductance markedly promotes H2O2 induced apoptosis of various tumor cells, whereas HERG expression facilitates the tumor cell proliferation caused by tumor necrosis factor (TNF) ligand (TNF-alpha)."
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"HERG K channel conductance promotes H2O2 induced apoptosis in HEK293 cells : cellular mechanisms."
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"Knockdown of hERG1 significantly suppressed cellular proliferation and invasion, and induced apoptosis, while inhibition of hERG1 significantly decreased activation of NF-kappaB."
reach
"Furthermore, specific siRNA mediated knock down of hERG expression triggered apoptosis, confirming the mechanistic role of small molecule induced hERG protein suppression."
reach
"Thus, B-RAF-sensitive hERG K + channel up-regulation possibly contributes to cell proliferation and apoptosis of tumor cells."
| 1 1 9
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"Because KCNE2 partially suppresses hERG currents by reducing unitary conductance and speeding deactivation XREF_BIBR, it is an intriguing possibility that the observed anti-proliferative effects of KCNE2 overexpression in vitro XREF_BIBR are due to hERG current suppression promoting apoptosis, and conversely that KCNE2 down-regulation or genetic disruption may favor gastric cellular proliferation by increasing hERG current density."
reach
"In this study, it was found that hERG1 silencing induced apoptosis in osteosarcoma cells."
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"HERG channel blockers have been shown to induce apoptosis in different cell types."
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"Silencing of hERG1 Gene Inhibits Proliferation and Invasion, and Induces Apoptosis in Human Osteosarcoma Cells by Targeting the NF-kappaB Pathway."
reach
"Given that GB cells express hERG channels and that hERG suppression by doxazosin induces apoptosis, we hypothesized that pharmacological targeting of hERG channels would induce apoptosis of GB cells."
reach
"Moreover, knockdown of hERG inhibits cell growth and induces apoptosis in ATC cells in vitro."
sparser
"Silencing HERG inhibited the apoptosis induced by cisplatin both in vitro and in vivo, by attenuating the cisplatin effects on Bcl-2, Bax and active caspase-3."
reach
"To delineate the mechanism of action behind hERG1 promotion of osteosarcoma cell proliferation, we examined whether inhibition of hERG1 triggers apoptosis."
reach
"In addition, hERG channel blockers can lead to apoptosis; however, this event appears to be independent of their ability to arrest the cell cycle."
reach
"Furthermore, gene knockdown of hERG elicited growth suppression as well as activated apoptosis by means of abolishing vascular endothelial growth factor secretion and triggering caspase-3 cascade in anaplastic thyroid carcinoma cells."
NEDD4L affects KCNH2
2 | 24
NEDD4L ubiquitinates KCNH2.
| 8
NEDD4L ubiquitinates KCNH2. 8 / 8
| 8
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"Nedd4-2 ubiquitinates the epithelial sodium channel ENaC [XREF_BIBR], the chloride channel ClC-5, voltage gated potassium and the cardiac potassium channel hERG1 [XREF_BIBR]."
reach
"These two complementary methods enabled us to confirm that hERG1 was most likely directly ubiquitylated by Nedd4-2, since Nedd4-2 co-expression robustly increased the ubiquitylation of the channel."
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"In conclusion, the results of the present work indicate that ubiquitylation of hERG1 by the ubiquitin ligase Nedd4-2 is a potentially constitutive physiological mechanism for the regulation of hERG1 channel membrane density and that it contributes to the regulation of cardiac repolarization.The authors declare that they have no competing financial interests."
reach
"Moreover, they also suggest that, at least in expression systems, the formation of a complex ubiquitin ligase-target protein is not inevitably followed by ubiquitylation of the protein.The present study suggests that Nedd4-2 promotes poly-ubiquitylation of hERG1 since upon Nedd4-2 co-expression, the ubiquitylation pattern of the channel reveals an increase of high-molecular weight forms of ubiquitylated hERG1."
reach
"Further experiments will be needed to confirm these results.In addition, hERG1 channels ubiquitylated by Nedd4-2 appear to be targeted to the proteasomal rather than to the lysosomal pathway, although caution in interpreting these results is clearly necessary since MG132 may inhibit other proteases, too."
reach
"Finally, we determined that Nedd4-2 mediates ubiquitylation of hERG1 and that deletion of this motif affects Nedd4-2-dependent regulation."
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"As quantified in Fig. 5 B, only Nedd4-2 significantly increased the basal ubiquitylation of hERG1, while Nedd4-2-C801S and the other ubiquitin ligases had no effect."
reach
"These results suggest that ubiquitylation of the hERG1 protein by Nedd4-2, and its subsequent down-regulation, could represent an important mechanism for modulation of the duration of the human cardiac action potential."
NEDD4L binds KCNH2.
2 | 5
2 | 5
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"Here, we provide evidence of an interaction between hERG1 and Nedd4-2 in guinea pig hearts, suggesting that ubiquitylation of the channel by this ubiquitin ligase could play a role in its regulation in vivo and hence to the regulation of the cardiac AP duration."
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"As shown in Fig. 3 C, a specific signal for Nedd4-2 was found when ERG1 was immunoprecipitated, thus indicating an interaction between ERG1 and Nedd4-2 in the guinea pig heart.We investigated whether the decrease of I hERG1 could be due to a depletion of hERG1 protein at the plasma membrane."
reach
"The biochemical interactions between hERG1 and Nedd4-2 were investigated by co-immunoprecipitation experiments."
reach
"Our data demonstrate that Cav3, hERG, and ubiquitin-ligase Nedd4-2 interact with each other and form a complex."
reach
"Similar to Nedd4-2, WWP2 but not Nedd4-1 was present in the fraction immunoprecipitated with the anti-hERG1 antibody, when expressed with the WT channel, demonstrating that hERG1 can interact both with Nedd4-2 and WWP2."
biogrid
No evidence text available
biogrid
No evidence text available
NEDD4L inhibits KCNH2.
| 6
NEDD4L inhibits KCNH2. 6 / 6
| 6
reach
"The increase in hERG protein was associated with PKC induced phosphorylation (inhibition) of Nedd4-2, an E3 ubiquitin ligase that mediates hERG degradation."
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"The major findings of this study are as follows : 1) hERG1 interacts via its PY motif with the ubiquitin ligase Nedd4-2, 2) this interaction promotes the down-regulation of the functional form of the channel at the plasma membrane through Nedd4-2 ubiquitylation of the channel, and 3) I hERG1 is strongly decreased by Nedd4-2 catalytic dependent activity.The hERG1 PY motif is a highly conserved sequence across animal species lines, highlighting its crucial role in the regulation of the hERG1 channel at the cell surface."
reach
"We previously showed that the E3 ubiquitin ligase Nedd4-2 mediates degradation of hERG channels."
reach
"Our results show that the ubiquitin ligase Nedd4-2 down-regulates I hERG1 measured in a mammalian cell line."
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"We have previously shown that mature hERG channels are degraded by ubiquitin ligase Nedd4-2 via enhanced channel ubiquitination."
reach
"Although both immature and mature hERG channels contain the PY motif, Nedd4-2 selectively mediates the degradation of mature hERG channels."
NEDD4L activates KCNH2.
| 4
NEDD4L activates KCNH2. 4 / 4
| 4
reach
"We have previously shown that the E3 ubiquitin (Ub) ligase Nedd4-2 (neural precursor cell expressed developmentally down-regulated protein 4-2) targets the PY motif of hERG channels to initiate channel degradation."
reach
"Although Ndfip2 directs Nedd4-2 to the Golgi apparatus, it also recruits Nedd4-2 to the multivesicular bodies (MVBs), which may impair MVB function and impede the degradation of mature hERG proteins mediated by Nedd4-2."
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"HERG1 modulation by Nedd4-2 leads to the specific reduction of functional channel levels at the cell surface and the subsequent decrease of hERG1 mediated currents.Guinea pigs were obtained from the group of Prof. E. Niggli (University of Bern, Switzerland)."
reach
"Rab4 interferes with Nedd4-2 degradation, resulting in an increased expression level of Nedd4-2, which targets hERG."
NEDD4L deglycosylates KCNH2.
| 1
Modified NEDD4L leads to the deglycosylation of KCNH2. 1 / 1
| 1
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"Western blots of hERG1 protein from total HEK293 lysates revealed that Nedd4-2 co-expression specifically decreased the fully glycosylated (fg) or mature form of hERG1 observed at 155 kDa [23], whereas the lower band at 135 kDa, known as the core glycosylated (cg) or non mature form [23], was not changed upon Nedd4-2 co-expression."
KCNH2 affects cell death
| 1 25
KCNH2 activates cell death.
| 1 16
| 1 16
reach
"To understand HERG mediated cardiac sudden death at the molecular level, it is important to determine which regions in the HERG protein participate in subunit interaction."
reach
"Mutations of the human eag related gene (HERG) result in a form of cardiac arrhythmia that can lead to ventricular fibrillation and sudden death."
reach
"The human Ether-a-go-go-Related-Gene (hERG) potassium (K (+)) channel is liable to drug inducing blockage that prolongs the QT interval of the cardiac action potential, triggers arrhythmia and possibly causes sudden cardiac death."
reach
"Indeed, it is now known that structurally different drugs (e.g., Class III antiarrhythmics, antibiotics, antihistamines, antidepressants, and antipsychotic agents) are able to block the hERG channel, causing a concomitant risk of sudden death, as a side effect; for this reason hERG inhibition is an important antitarget during the drug discovery process."
reach
"These might explain that shRNA-herg1/1b was more effective than shRNA-herg1 when used in herg gene silence.As mentioned in the Introduction, dysfunction of HERG might cause long QT syndrome and induce the episode of cardiac arrhythmias and an increasing risk of sudden death (Sanguinetti and Mitcheson, 2005; Witchel, 2007)."
reach
"To gain more insights into a possible hERG1 agonist driven cell death mechanism, we also monitored apoptosis by using AnnexinV based immunofluorescence (XREF_FIG)."
reach
"HERG mediated sudden death as a side effect of non antiarrhthmic drugs has been receiving increased attention by the regulatory bodies XREF_BIBR XREF_BIBR XREF_BIBR XREF_BIBR."
reach
"XREF_BIBR By the silencing method, we found that downregulation of hERG caused cell death and apoptosis in HTC/3 cells."
reach
"Dysfunction of hERG causes long QT syndrome and sudden death, which occur in patients with cardiac ischemia."
reach
"However, the hERG K (+) channel poses a special challenge in drug discovery, since block of this channel by a plethora of diverse chemical entities can lead to long QT syndrome and sudden death."
reach
"Cisparide is an antiemetic drug that was withdrawn from the market due to its potent hERG blocking activity that led to arrhythmias and sudden death."
reach
"HERG mediated sudden death as a side effect of non antiarrhythmic drugs has been receiving increased regulatory attention."
reach
"There are many literature references supporting the strong correlation between the clinical safety margin over human ether-a-go-go (hERG) inhibitory potency and the risk of drug induced arrhythmia and sudden death."
reach
"Mutations in HERG cause human long QT2 syndrome (LQT2) which is a heart condition in which delayed repolarization of the heart, characterized by a prolongation of the electrocardiogram QT interval, increases the risk of life threatening arrhythmias and sudden death XREF_BIBR, XREF_BIBR."
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"Reduction of hERG currents caused by mutations or drug induced blockade of hERG channel produces hereditary or acquired long QT syndrome, a potentially lethal repolarization disorder associated with syncope, torsade de points arrhythmias, and sudden cardiac death [2-5]."
reach
"In rare cases, creation of isogenic pairs was used to study role of mutations in genes such as KCNH2, which underlies the sudden cardiac death condition of LQTS2 XREF_BIBR."
KCNH2 inhibits cell death.
| 9
| 9
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"Blockade of central and/or peripheral muscarinic receptors with atropine or N-methyl scopolamine prevents thermal seizure induced bradycardia and sporadic death in Scn1a +/- animals suggesting that lethality in this model is related to parasympathetic hyperactivation."
reach
"Blockade of hERG K+ channels in the heart is an unintentional side effect of many drugs and can induce cardiac arrhythmia and sudden death."
reach
"Reduced levels of hERG protein and the corresponding repolarizing current I Kr can cause arrhythmia and sudden cardiac death, but the underlying cellular mechanisms controlling hERG surface expression are not well understood."
reach
"The human Ether-a-go-go-related gene (hERG)-encoded K (+) current, I (Kr) is essential for cardiac repolarization but is also a source of cardiotoxicity because unintended hERG inhibition by diverse pharmaceuticals can cause arrhythmias and sudden cardiac death."
reach
"Inhibition of hERG K + channels by structurally diverse drugs prolongs the ventricular action potential and increases the risk of torsade de pointes arrhythmias and sudden cardiac death."
reach
"HERG blockade by small molecules can induce " torsade de pointes " arrhythmias and sudden death; as such, it is an important off-target to avoid during drug discovery."
reach
"In contrast, a reduction in hERG currents due to either genetic defects or adverse drug effects can lead to hereditary or acquired long QT syndromes characterized by action potential prolongation, lengthening of the QT interval on the surface ECG, and an increased risk for " torsade de pointes " arrhythmias and sudden death."
reach
"Reduction of hERG currents caused by mutations or drug induced blockade of hERG channel produces hereditary or acquired long QT syndrome, a potentially lethal repolarization disorder associated with syncope, torsade de points arrhythmias, and sudden cardiac death [2-5]."
reach
"Suppression of hERG and Kv11.1 (I Kr) can prolong the APD and cause drug induced LQT syndrome and fatal ventricular tachyarrhythmia or TdP and consequently sudden cardiac death."
KCNH2 affects HSPA
| 13 11
| 8 11
reach
"The formation of the Hsp70 and hERG complex, on the other hand, was unaffected by hypoxia treatment (lane 5 and 6)."
reach
"It has been reported that hERG formed complexes with Hsp70 27."
reach
"These results indicate that THIO disturbed the folding process of the hERG channel by reducing the interaction between hERG and Hsp70, eventually leading to the degradation of disordered hERG proteins."
reach
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
reach
"Our data demonstrated that both Kv4.3 and hERG interacted with Hsp70, suggesting that Hsp70 may form complexes with hERG and Kv4.3."
reach
"To determine the mechanism of trafficking inhibition, we performed western blot and immunoprecipitation to test folding of hERG by assessing interaction between hERG and Hsp90 and Hsp70."
sparser
"Hsp70 interacts with the nascent hERG in the ER while Hsp90 interacts with the terminal hERG in the cytoplasm to facilitate folding [ xref ]."
reach
"Our coimmunoprecipitation results show that THIO aggravated the ubiquitination of the hERG protein (XREF_FIG), and the interactions between hERG and Hsp70 were decreased (XREF_FIG)."
reach
"Ficker et al. showed that the cytosolic chaperones Hsp70 interacted with hERG during maturation 27."
sparser
"This effect may have increased the interaction between the initial hERG and Hsp70."
reach
"Hsp70 interacts with the nascent hERG in the ER while Hsp90 interacts with the terminal hERG in the cytoplasm to facilitate folding [XREF_BIBR]."
sparser
"Our coimmunoprecipitation results show that THIO aggravated the ubiquitination of the hERG protein ( xref ), and the interactions between hERG and Hsp70 were decreased ( xref )."
reach
"As illustrated in Figures XREF_FIG and XREF_FIG, hERG and Hsp70 complexes were decreased in the presence of 3muM THIO."
sparser
"These results indicate that THIO disturbed the folding process of the hERG channel by reducing the interaction between hERG and Hsp70, eventually leading to the degradation of disordered hERG proteins."
sparser
"Meanwhile, THIO increased the degradation of hERG channels via disrupting hERG-Hsp70 interactions."
sparser
"We therefore turned to exploring whether THIO prevents maturation of hERG channels via inhibiting chaperone-hERG interactions; to this end, we performed coimmunoprecipitation experiments to determine the association of hERG protein with Hsp70."
sparser
"Therefore, it would be difficult for Hsp70 to recognize and interact with the hERG protein, thereby elongating the interaction of the early hERG protein with Hsp70 and reducing the interaction of hERG protein with Hsp90."
sparser
"The interaction between hERG protein and Hsp90 reduced while the interaction between hERG protein and Hsp70 increased by DHB."
reach
"This effect may have increased the interaction between the initial hERG and Hsp70."
HSP90 binds HSPA and KCNH2. 2 / 2
| 2
sparser
"Mutations such as R752W and G601S strengthen the interaction of hERG with Hsp70 and Hsp90."
sparser
"It could be that hypoxia inhibits Hsp90 binding to hERG by reducing steady state expression levels of endogenous Hsp90 and/or Hsp70."
HSPA binds HSPA8 and KCNH2. 1 / 1
| 1
sparser
"Interestingly, although both Hsp70 and Hsc70 associated with hERG channels, it was reported that Hsp70 enhanced the maturation of hERG channels while Hsc70 suppressed their maturation xref ."
HSPA binds KCND3 and KCNH2. 1 / 1
| 1
sparser
"In addition, Hsp70 interacted with hERG and Kv4.3 respectively, and formed complexes with hERG and Kv4.3."
| 1
sparser
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
Probucol affects KCNH2
| 1 23
Probucol decreases the amount of KCNH2.
| 7
Probucol decreases the amount of KCNH2. 7 / 7
| 7
reach
"Probucol, a cholesterol lowering drug, induces LQTs by inhibiting the expression of the hERG channel."
reach
"Our data are consistent with the report that probucol, also a cholesterol lowering drug, decreases hERG expression through accelerating cav-1 degradation."
reach
"Thus, probucol reduces hERG expression through accelerating Cav1 turnover."
reach
"To demonstrate further whether CCh impeded probucol induced reduction of 155 kDa hERG expression was the result of alteration of p-Nedd4-2, we detected the p-Nedd4-2 expression level under equivalent conditions."
reach
"In summary, the present study provides evidence that probucol does not block the hERG channel, but accelerates degradation of the mature hERG channel and inhibit hERG current by decreasing SGK1 expression level and eventually enhancing the ubiquitination of the hERG channel through the E3 ubiquitin ligase Nedd4-2, whereas CCh can rescue probucol disrupted hERG surface expression by enhancing the phosphorylation level of Nedd4-2 as an alternative to SGK1."
reach
"In the present study, we confirmed that Nedd4-2 is involved in the process of probucol disrupted hERG surface expression."
reach
"Recent in vitro studies have indicated that probucol reduces hERG expression in the plasma membrane and does not directly block human ether-a-go-go-related gene (hERG) channels."
Probucol inhibits KCNH2.
| 1 6
| 1 6
reach
"Probucol also disrupted hERG trafficking and did not block hERG channels expressed in human embryonic kidney 293 cells."
reach
"XREF_BIBR By decreasing hERG channel-membrane density, probucol can cause LQTS and torsades de pointes arrhythmia in patients and sudden cardiac death in experimental animals."
reach
"Probucol induced hERG channel reduction can be rescued by matrine and oxymatrine in vitro."
reach
"Our data demonstrate that probucol accelerated the degradation of mature hERG channels, which associated with caveolin-1 (Cav1) in hERG expressing HEK cells."
reach
"XREF_BIBR, XREF_BIBR Our data show that probucol (30, 50, and 100 muM) treatment decreases the mature 155 kDa band of hERG, but does not reduce the intracellular forms of the immature hERG 135 kDa band (XREF_FIG), suggesting that probucol may not block hERG forward trafficking."
reach
"For example, the antiarrhythmic agents ketoconazole and fluoxetine have been shown to reduce hERG density by at least 50% following 48 hours of treatment, XREF_BIBR - XREF_BIBR whereas pentamidine and probucol reduce cell-surface hERG without affecting ion conduction."
Probucol activates KCNH2.
| 6
| 6
reach
"To identify the damage of hERG current induced by probucol depended on the decrease of protein level but not channel functions, patch-clamp recordings were used to detect the long-term effect of probucol on hERG-channel kinetics."
reach
"This seems to be a result of enhanced degradation of plasma membrane hERG protein induced by probucol treatment."
reach
"Therefore, these results demonstrate that matrine and oxymatrine could rescue probucol induced hERG deficiency, which may lead to potentially effective clinical therapeutic drugs for treating cardiotoxicity in the future."
reach
"We also demonstrated that matrine and oxymatrine were able to upregulate Sp1 expression which may be one of the possible mechanisms that by which matrine and oxymatrine rescued probucol induced hERG channel deficiency."
reach
"On the contrary, carbachol could enhance the phosphorylation level of Nedd4-2 as an alternative to SGK1, and thus rescue the ubiquitin mediated degradation of hERG channels caused by probucol."
reach
"Likewise, CCh (25 and 50 muM) reversed the downregulation of I hERG induced by 100 muM probucol (XREF_FIG)."
Probucol increases the amount of KCNH2.
| 2
Probucol increases the amount of KCNH2. 2 / 2
| 2
reach
"In hERG expressing HEK cells, overexpression of Cav1 enhanced, whereas knockdown of Cav1 impeded, probucol induced reduction of mature hERG channels."
reach
"Although diverse compounds reduce the hERG current (I (hERG)) by blocking the channel, probucol, a cholesterol lowering drug that causes LQTS, reduces I (hERG) by decreasing plasma-membrane hERG protein expression."
Probucol deubiquitinates KCNH2.
| 2
Probucol leads to the deubiquitination of KCNH2. 2 / 2
| 2
reach
"In summary, the present study provides evidence that probucol does not block the hERG channel, but accelerates degradation of the mature hERG channel and inhibit hERG current by decreasing SGK1 expression level and eventually enhancing the ubiquitination of the hERG channel through the E3 ubiquitin ligase Nedd4-2, whereas CCh can rescue probucol disrupted hERG surface expression by enhancing the phosphorylation level of Nedd4-2 as an alternative to SGK1."
reach
"Therefore we proposed the hypothesis that probucol treatment decreases hERG-channel expression by increasing Nedd4-2-mediated hERG ubiquitination."
| 1 23
Potassium(1+) activates KCNH2.
| 13
| 13
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"We found that changes in [K+] e over a physiologic range significantly modulated the amplitude of HERG current."
reach
"For example, elevation of [K+] e from 2 to 5 mM increased HERG current by 40%."
reach
"Mutations in genes encoding the major potassium ion channels mediating this event, KCNQ1 and HERG, therefore account for ~ 90% of cases of inherited long QT syndrome."
reach
"Consistent with previous reports we show that increases in extracellular potassium reduce HERG block by quinidine and cisapride."
reach
"HERG channels are paradoxically activated by a modest increase in extracellular potassium concentration."
reach
"The modulation of HERG (and IK ~) by [K+] e may have physiologic importance."
reach
"HERG current is K+ selective, declines with depolarizations above 0 mV, is activated by extracellular K+, and is blocked by lanthanum."
reach
"First, lowering of extracellular potassium directly decreases hERG currents in the heart [XREF_BIBR, XREF_BIBR, XREF_BIBR]."
reach
"Modulation of HERG and IK, by [K+], and Blockers Blockers Methanesulfonanilides (IC ~ o) Modulation of Current Current by [K *] ~ La ~- Co2+ E-4031 MK-499 Dofetilide HERGa + + 1 p.Mb 1 pMb ND IK, (guinea pig) c + + 397 nM 44 nM 32 nM IKr (rabbit) d ND ND < 0.1 p.M ND 4 nM IKr (AT-1 cells) e ND + ND ND 12 nM ND, not determined."
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"The observation that HERG current inhibition was reduced by 17% in the presence of 10 mM external potassium is significant, given that such an increase in extracellular potassium may be observed in ischemia."
reach
"This elevation in [K+] e would increase the contribution of HERG (IKr) to net repolarizing current."
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"HERG Current Is Activated by Extracellular K+ The K+ selectivity of HERG was determined by measuring the reversal potential of currents in oocytes bathed in ND96 solution containing different concentrations of KCI (0.5-20 raM)."
reach
"The left panel of XREF_FIG shows whole cell lysate and Western blot of stable HEK-WT HERG cells treated with low potassium media."
Potassium(1+) inhibits KCNH2.
| 1 4
| 1 4
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"Secondly, low extracellular potassium can also increase the blockade of hERG currents by drugs [XREF_BIBR, XREF_BIBR]."
reach
"These results demonstrate that [K+] o does not directly modulate drug block of hERG channels expressed in an HEK-293 cell line."
reach
"As first reported by Guo and colleagues, low-extracellular potassium causes degradation of the 155 kD form of HERG through an endocytic mechanism involving mono-ubiquitination."
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"We have addressed whether some of the beta-adrenoceptor blockers commonly used to prevent the development of these arrhythmias could per se block the cardiac HERG (Human Ether-a-go-go-Related Gene) potassium channels, which would be a most unwanted side effect."
| 4
reach
"Overall, i) several structures were found to be effectual for reducing hERG potassium ion channel binding affinity in this study."
reach
"The structure activity relationship (SAR) of the potency and selectivity, structure-metabolic stability relationship (SMR), and SAR of hERG (human ether-a-go-go related gene) potassium ion channel binding affinity for the analogs in the present studies invitro provided or suggested significant and/or useful structural determinants and insights for the respective purposes."
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"Thus, 1 demonstrates dose dependent inhibitory effect against mechanical allodynia in chronic constriction injury induced neuropathic pain model rats, robust metabolic stability and little hERG potassium ion channel binding affinity, with its unique and potentially safe profiles and mechanisms, which were distinctive from those of N/OFQ in terms of site-differential effects."
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"Design and SAR of the analogs for reducing hERG (human ether-a-go-go related gene) potassium ion channel binding affinity were also investigated in vitro as a safe-drug study."
Potassium(1+) decreases the amount of KCNH2.
| 2
Potassium(1+) decreases the amount of KCNH2. 2 / 2
| 2
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"By facilitating expression of channel protein HERG, potassium ions may prevent cells from being shunted to procancerous pathways and overbalance the mitochondrial membrane potential through upregulating expression of VDAC1 or breaking the balance of Bcl-2 and Bax ratio and then induced cytochrome c released from mitochondria, caspase activation, and caspase-3/7 ration imbalance, finally resulting in cell apoptosis."
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"By facilitating expression of channel protein HERG, potassium ions may prevent it from being shunted to procancerous pathways by inducing apoptosis."
PKC affects KCNH2
| 1 4 18
PKC activates KCNH2.
| 1 1 13
PKC activates KCNH2. 14 / 14
| 1 1 13
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"Protein kinases C (PKC) modulate the activity of the Kv11.1 ion channel current (hERG)."
reach
"In addition to the known effects of PKA and cAMP, HERG channels are also modulated by PKC."
reach
"We previously showed that PKC activation also increased the abundance of HERG channel by a mechanism (s) that only partially overlap with those for PKA [XREF_BIBR]."
reach
"Subsequently, it has been proposed that the PKC dependent modulation of hERG is exerted either independently of direct phosphorylation of the channel protein itself in Xenopus oocytes, or via a direct phosphorylation of the pore forming hERG subunits in mammalian cells."
reach
"The protein kinase C (PKC) inhibitor bisindolylmaleimide 1 (1muM) antagonized the reduction of mature hERG channel protein induced by Ang II."
reach
"It has been reported that sustained alpha 1A -adrenergic stimulation produced a profound augmentation of hERG channel protein mediated by PKC [32]."
reach
"The protein kinase C (PKC) inhibitor bisindolylmaleimide 1 (1muM) antagonized the reduction of mature hERG channel protein induced by Ang II."
reach
"Our results are consistent with calcium and/or DAG sensitive isotypes of PKC modulating hERG currents through a mechanism that involves direct phosphorylation of sites on the amino terminus of hERG."
reach
"We identified a specific role for the PKCepsilon inhibitory peptidomimmetics in decreasing PKC induced hERG tau activation (80%) and half-maximum activation voltage (90%) at steady state; a specific PKCepsilon activator exhibited the opposite effect."
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"Regulation of HERG potassium channel activation by protein kinase C independent of direct phosphorylation of the channel protein."
reach
"Stimulation of alpha1A-AR with phenylephrine or direct activation of PKC with phorbol ester increased HERG channel protein abundance and K (+) current density in a time- and dose dependent manner."
sparser
"We identified a specific role for the PKCε inhibitory peptidomimmetics in decreasing PKC-induced hERG τ activation (80%) and half-maximum activation voltage (90%) at steady state; a specific PKCε activator exhibited the opposite effect."
reach
"Protein kinase A and protein kinase C modulate cardiac hERG channels and/or I Kr [6,7]."
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"Acute activation of PKC by PMA (30 nM, 30 min) reduced both hERG current (I hERG) and I Kr Chronic activation of PKC by PMA (30 nM, 16 h) increased I Kr in cardiomyocytes and the expression level of hERG proteins."
PKC inhibits KCNH2.
| 4
PKC inhibits KCNH2. 4 / 4
| 4
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"Furthermore, broad-specificity inhibitors of protein kinase A (PKA) or protein kinase C (PKC) failed to stimulate hERG down-regulation in the presence or absence of ouabain (unpublished data), suggesting that glycoside induced down-regulation of hERG is independent of PKA- and PKC dependent phosphorylation."
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"Furthermore, broad-specificity inhibitors of protein kinase A (PKA) or protein kinase C (PKC) failed to stimulate hERG down-regulation in the presence or absence of ouabain (unpublished data), suggesting that glycoside induced down-regulation of hERG is independent of PKA- and PKC dependent phosphorylation."
reach
"Our results suggest that PKC may enhance hERG channel protein degradation via proteasomal pathway."
reach
"Several papers have reported that either alpha-adrenergic or non selective PKC stimulation by PMA reduces hERG currents in cardiomyocyte."
PKC phosphorylates KCNH2.
| 1 1
PKC phosphorylates KCNH2. 2 / 2
| 1 1
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"PKC can directly phosphorylate hERG channel protein and thus enhance synthesis and/or translation rates of the channel proteins [32]."
sparser
"PKC can directly phosphorylate hERG channel protein and thus enhance synthesis and/or translation rates of the channel proteins [32] ."
PKC binds KCNH2.
| 2
| 1
sparser
"The direct interaction of the commonly used protein kinase C (PKC) inhibitor bisindolylmaleimide I (BIM I) with hERG, KvLQT1/minK, and I(Kr) currents was investigated in this study."
PKC binds KCNH2 and NEDD4. 1 / 1
| 1
sparser
"The increase in hERG protein was associated with PKC-induced phosphorylation (inhibition) of Nedd4-2, an E3 ubiquitin ligase that mediates hERG degradation."
DHB affects KCNH2
| 22
DHB inhibits KCNH2.
| 10
DHB inhibits KCNH2. 10 / 10
| 10
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"In our study, DHB inhibited the hERG current in a concentration dependent manner after immediate perfusion, and the IC 50 was 10.50 muM."
reach
"DHB immediate perfusion inhibits hERG current concentration-dependently."
reach
"Finally, trafficking inhibition activated UPR, and mature hERG channel degradation was increased by DHB."
reach
"Furthermore, we also examined whether DHB inactivated hERG channel."
reach
"In conclusion, we demonstrated that DHB acutely blocked hERG channels by binding the aromatic Tyr652 and Phe656."
reach
"The results indicated that DHB inhibited the hERG channel by shortening the time constant of the onset of inactivation."
reach
"In summary, we demonstrated that DHB directly blocked the hERG channel by binding to the aromatic Tyr652 and Phe656."
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"DHB treatment decreases hERG current but not hERG channel kinetics."
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"DHB acutely blocks hERG channel by binding to aromatic Tyr652 and Phe656 in S6 helix."
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"In the current study, we first demonstrated that DHB acutely blocked hERG channel by binding to the aromatic Tyr652 and Phe656."
DHB decreases the amount of KCNH2.
| 6
DHB decreases the amount of KCNH2. 6 / 6
| 6
reach
"DHB may decrease hERG plasma membrane expression through two pathways involving disruption of forward trafficking of immature hERG channels and enhanced degradation of mature hERG channels."
reach
"DHB inhibited the hERG current concentration-dependently after instantaneous perfusion, accelerated channel inactivation by directly binding tyrosine (Tyr652) and phenylalanine (Phe656), and decreased mature (155-kDa) and simultaneously increased immature (135-kDa) hERG expression, respectively."
reach
"In short, our date demonstrated that DHB acutely blocked hERG channels and poteintially decreased hERG plasma membrane expression through two pathways involving disruption of forward trafficking of immature hERG channels and enhanced degradation of mature hERG channels."
reach
"Further, we suggested that DHB decreased hERG plasma membrane expression through two pathways : the disruption of the forward trafficking of immature hERG channels and the enhancement of the degradation of the mature hERG channels."
reach
"DHB decreases hERG plasma membrane expression through two pathways involving the disruption of the forward trafficking of immature hERG channels and the enhancement of the degradation of the mature hERG channels."
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"DHB reduces mature hERG protein level by inhibiting its trafficking."
DHB activates KCNH2.
| 5
DHB activates KCNH2. 5 / 5
| 5
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"These findings demonstrated that the hERG trafficking defect induced by DHB activates UPR."
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"HEK293 cells transiently transfected with hERG cDNA was used to identify the binding sites that induce the acute inhibition of hERG channel triggered by immediate DHB perfusion."
reach
"DHB accelerates hERG channel inactivation."
reach
"These findings suggested that DHB induced hERG trafficking defect results from protein misfolding, which may due to the reduction of Hsp90 expression and the aberrant interaction between hERG protein and molecular chaperones."
reach
"Together, our findings shed light on the potential mechanisms of the DHB induced hERG channel deficiency which may provide a better understanding of drug induced LQTS."
DHB binds KCNH2.
| 1
KCNH2 binds DHB. 1 / 1
| 1
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"We speculated that DHB was bound to the hERG channels and caused a conformational change that led to abnormal trafficking."
| 21
Moxifloxacin inhibits KCNH2.
| 20
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"Because the ability of moxifloxacin to inhibit HERG channels is unknown, this study explored the effect of moxifloxacin on HERG channel currents and glucose metabolism in mice."
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"In contrast, moxifloxacin clearly blocked HERG current amplitude with an IC 50 value of 74.7 muM."
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"Mechanistically, moxifloxacin treatment and LQT-2 patients share a common pathophysiology in that moxifloxacin blocks the hERG potassium channel XREF_BIBR and LQT2 patients have mutations in the gene encoding the hERG channel XREF_BIBR, XREF_BIBR."
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"In common with other QT prolonging agents, moxifloxacin is known to inhibit the hERG potassium K+ channel, but at present there is little mechanistic information available on this action."
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"Grepafloxacin and moxifloxacin suppressed the HERG current with EC 50 of 37.5 +/-3.3 mug/ml and 41.2 +/-2.0 mug/ml and n H = 1.4 +/-0.2 and 1.1 +/-0.1, respectively."
reach
"In contrast, moxifloxacin blocked HERG current amplitude with an IC50 value of 74.7 microM."
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"Block of hERG by moxifloxacin was found to be voltage dependent, occurred rapidly and was independent of stimulation frequency."
reach
"Ciprofloxacin was found to have little interaction with the HERG channel at concentrations up to 100 mug/ml, whilst sparfloxacin, grepafloxacin and moxifloxacin inhibited HERG currents with IC 50 values of 13, 37 and 41 mug/ml, respectively."
reach
"Our data demonstrate that moxifloxacin blocks the hERG channel with a preference for the activated channel state."
reach
"The same was true for other hERG channel blockers (like erythromycin, moxifloxacin and sematilide) and multi-ion channel blockers."
reach
"In contrast, moxifloxacin blocked HERG current amplitude with an IC 50 value of 74.7 muM."
reach
"The Tyr652 but not Phe656 S6 residue is involved in moxifloxacin block of hERG, concordant with an interaction in the channel inner cavity."
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"At standard clinical concentrations moxifloxacin induces approximately 5% hERG potassium channel block and 10 ms of QTc prolongation, and in our clinical study a supratherapeutic dose of intravenous moxifloxacin caused a QTc prolongation of 30 ms. At similar concentrations, the iPSC cardiomyocytes did not show statistically significant APDc or FPDc prolongation, but moxifloxacin caused concentration dependent APDc and FPDc prolongation above this range (21-200 muM), and arrhythmias were detected in in both cell types at approximately 50-fold clinical Cmax."
reach
"Moxifloxacin inhibited the hERG current with an IC50 of 35.7 microM."
reach
"Bath application of sparfloxacin, moxifloxacin and grepafloxacin produced an inhibition of HERG outward currents at -40 mV with EC (50) of 13.5 +/-0.8, 41."
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"We demonstrated that the time dependent and tail currents for HERG decreased in response to 100mumol/L of moxifloxacin indicating that moxifloxacin inhibits the HERG channel in HEK293 cells."
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"Indeed, moxifloxacin (40), fluvoxamine (41), and, recently, doxepin (42) have been reported to inhibit hERG with a mixed state-dependence of inhibition (with components of both closed- and open-channel block, including a very rapid open-channel block)."
reach
"The comparison of potencies from grepafloxacin, moxifloxacin, and sparfloxacin to block the HERG channel shows the latter to have the greatest inhibition effect on the HERG current amplitude."
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"Moxifloxacin Induced Inhibition of the HERG Channel in HEK293 Cells."
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"Our data demonstrate that hERG channel blockers, such as E4031 and moxifloxacin, prolonged field potential duration (FPD) at low concentration and induced arrhythmic beating activity as measured by field potential (FP) recording and impedance (IMP) recordings at higher concentrations."
Moxifloxacin activates KCNH2.
| 1
| 1
reach
"There were no significant differences in blood glucose or insulin concentrations in HERG knockout mice treated with moxifloxacin or saline."
SIGMAR1 affects KCNH2
| 9 12
SIGMAR1 binds KCNH2.
| 9 6
| 9 6
reach
"Homogeneous time resolved fluorescence (HTRF (R)) allowed the detection of the interaction between the sigma-1 receptor and hERG within the plane of the plasma membrane."
reach
"Our aim was to investigate the nature of the interaction between the sigma-1 receptor and hERG."
sparser
"Atomic force microscopy imaging of the isolated protein confirmed the direct binding of the sigma-1 receptor to hERG monomers, dimers, and tetramers."
sparser
"The findings of the Sig-1R interacting with hERG in the ER and potentiating hERG maturation and translocation to the plasma membrane suggest that the Sig-1R may exert chaperoning activities in the ER to facilitate proper protein sorting to their final destinations."
sparser
"Inasmuch Sig1R co-immunoprecipitates with both immature and mature forms of the channel α-subunits, it is suggested that Sig1R not only associates with hERG in the ER, but also drives it to the plasma membrane (Crottes et al., xref )."
reach
"The authors clarify that the direct interaction between the Sig-1R and hERG in the plasma membrane is not Sig-1R ligand dependent but is reduced by cholesterol depletion, suggesting that Sig-1R may bind to hERG in the ER and facilitate hERG assembly and trafficking perhaps in a lipid-raft related fashion [XREF_BIBR]."
sparser
"Our aim was to investigate the nature of the interaction between the sigma-1 receptor and hERG."
sparser
"We suggest that the sigma-1 receptor may bind to hERG in the endoplasmic reticulum, aiding its assembly and trafficking to the plasma membrane."
reach
"The distribution of angles between pairs of sigma-1 receptors bound to hERG tetramers had two peaks, at ~ 90 and ~ 180degrees in a ratio of ~ 2:1, indicating that the sigma-1 receptor interacts with hERG with 4-fold symmetry."
reach
"We suggest that the sigma-1 receptor may bind to hERG in the endoplasmic reticulum, aiding its assembly and trafficking to the plasma membrane."
sparser
"Homogeneous time-resolved fluorescence (HTRF®) allowed the detection of the interaction between the sigma-1 receptor and hERG within the plane of the plasma membrane."
reach
"Atomic force imaging and homogenous time resolved fluorescence approaches later identified that the Sig-1R interacts with hERG with a four-fold symmetry."
sparser
"The authors clarify that the direct interaction between the Sig-1R and hERG in the plasma membrane is not Sig-1R ligand-dependent but is reduced by cholesterol depletion, suggesting that Sig-1R may bind to hERG in the ER and facilitate hERG assembly and trafficking perhaps in a lipid-raft related fashion [ xref ]."
sparser
"Atomic force imaging and homogenous time-resolved fluorescence approaches later identified that the Sig-1R interacts with hERG with a four-fold symmetry."
sparser
"The distribution of angles between pairs of sigma-1 receptors bound to hERG tetramers had two peaks, at ∼90 and ∼180° in a ratio of ∼2:1, indicating that the sigma-1 receptor interacts with hERG with 4-fold symmetry."
SIGMAR1 activates KCNH2.
| 6
SIGMAR1 activates KCNH2. 6 / 6
| 6
reach
"Sigma 1 R potentiates hERG current by stimulating channel subunit biosynthesis and sigma 1 R silencing does not modify hERG mRNA contents but reduces hERG mature form densities."
reach
"Delving into the molecular mechanisms, we observed that the silencing of Sig1R decreases hERG maturation efficiency and diminishes the alpha-subunit channel stability at the plasma membrane, in turn reducing the number of ion channels available."
reach
"In human leukaemic cells, our group found that the silencing of Sig1R by shRNA reduces the endogenous human ether-a-gogo-related gene (hERG; Kv11.1) current density without altering channel voltage dependency or kinetic parameters."
reach
"Sig1R promoted the formation of hERG and beta1-integrin signaling complexes upon extracellular matrix stimulation, triggering the activation of the PI3K and AKT pathway."
reach
"Heterologous expression in Xenopus oocytes demonstrates that Sig1R potentiates hERG current by stimulating channel subunit biosynthesis."
reach
"As stated above, we recently showed that Sig1R expression stimulates hERG maturation and membrane stability in the chronic myeloid leukaemia cell line K562."
Bromide affects KCNH2
| 1 19
Bromide inhibits KCNH2.
| 1 18
| 18
reach
"In consistent with the " crossover " phenomenon, tetra-n-octylammonium bromide slowed the deactivation rate of HERG channel tail current (XREF_FIG)."
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"Use dependent inhibition of HERG channels by tetra-n-octylammonium bromide and benzethonium chloride."
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"Domiphen bromide and didecyl dimethylammonium bromide inhibited HERG channel currents in a dose dependent manner with IC 50 values of 9 nM and 5 nM, respectively."
reach
"Inhibition of HERG potassium channels by domiphen bromide and didecyl dimethylammonium bromide."
reach
"The properties of HERG channel inhibition by tetra-n-octylammonium bromide and benzethonium chloride are highly similar to verapamil and cisapride (XREF_TABLE)."
reach
"The result indicates that tetra-n-octylammonium bromide blocks HERG channels in a use dependent manner."
reach
"Overall, we suspected that the HERG blockade by domiphen bromide and didecyl dimethylammonium bromide were mainly associated with the binding of the compounds to open channels."
reach
"First, both domiphen bromide and didecyl dimethylammonium bromide blocked HERG channel currents expressed in CHO cells in a voltage dependent and use dependent manner."
reach
"In summary, our results demonstrate that tetra-n-octylammonium bromide and benzethonium chloride inhibit HERG channel currents in the voltage dependent and use dependent manners."
reach
"Our data indicated that tetra-n-octylammonium bromide blocks HERG channels in both open and inactivated states (XREF_FIG), whereas benzethonium chloride preferentially blocks HERG channels in the open states."
reach
"In this study, we found that benzethonium chloride, domiphen bromide, and tetra-n-octylammonium bromide significantly inhibited hERG channel activity in both the thallium influx assay and the patch clamp experiment."
reach
"In the present study, the potential mechanisms for HERG channel inhibition by tetra-n-octylammonium bromide and benzethonium chloride, two most potent HERG channel inhibitors found among the QACs examined, were studied using whole-cell patch clamp experiments in a CHO cell line stably expressing HERG channels."
reach
"The results indicate that domiphen bromide blocks HERG channels in a use dependent manner."
reach
"In addition, the domiphen bromide and didecyl dimethylammonium bromide inhibition of heterologously expressed HERG channels was voltage sensitive, increasing for steps more depolarized than -40 mV and reaching a maximum at approximately 0 mV (XREF_FIG)."
reach
"Concentration dependent inhibition of HERG channel by tetra-n-octylammonium bromide and benzethonium chloride."
reach
"The study of mechanism of HERG channel inhibition by tetra-n-octylammonium bromide and benzethonium chloride can provide additional insight of structure activity relationship of HERG channel inhibition and the molecular determinants of the interaction between the compounds and HERG channel proteins."
reach
"The use dependency of HERG channel blockade by 3 nM domiphen bromide and didecyl dimethylammonium bromide were examined with the voltage pulses shown in XREF_FIG."
reach
"Our data demonstrated that domiphen bromide and didecyl dimethylammonium bromide blocked the HERG channel with a preference for the activated channel state."
| 1
sparser
"In addition, the domiphen bromide and didecyl dimethylammonium bromide inhibition of heterologously expressed HERG channels was voltage sensitive, increasing for steps more depolarized than −40 mV and reaching a maximum at approximately 0 mV ( xref )."
Bromide activates KCNH2.
| 1
Bromide activates KCNH2. 1 / 1
| 1
reach
"Third, both domiphen bromide and didecyl dimethylammonium bromide did not cause any shift in HERG inactivation I-V curve in transfected CHO cells."
Amiodarone affects KCNH2
| 1 20
Amiodarone inhibits KCNH2.
| 1 17
| 1 16
reach
"Amiodarone blocks hERG and prolongs the QT interval, but is a rare cause of TdP (Yang et al., 2001)."
reach
"Amiodarone inhibited HERG K+ and late Na+ currents with IC50s of 0.8 +/- 0.1 and 3.0 +/- 0.9 microM, respectively."
reach
"In order to test whether the amiodarone derivative KB130015 (2-methyl-3-(3,5-diiodo-4-carboxymethoxybenzyl) benzofuran, XREF_BIBR) blocks hERG1 channels similarly, we expressed hERG1 in HEK 293 cells and measured whole-cell currents using the patch-clamp technique."
reach
"Amiodarone, azimilide, dofetilide, quinidine and sotalol all produced a dose dependent inhibition of HERG current."
reach
"KB130015 presumably binds to the hERG1 pore from the cytosolic side and functionally competes with hERG1 block by amiodarone, E4031 (N-[4-[[1-[2-(6-methyl-2-pyridinyl) ethyl] -4-piperidinyl] carbonyl] phenyl] methanesulfonamide dihydrochloride), and sertindole."
reach
"A prior study, conducted utilising Xenopus oocyte expression, has suggested that hERG channel inhibition by amiodarone exhibits both gated-state and closed-state components XREF_BIBR."
reach
"Amiodarone blocked HERG channels with an IC50 of 9.8 microM with a maximum outward tail current reduction of 62.8%."
reach
"Vice versa, amiodarone attenuates hERG1 activation by KB130015."
reach
"On the other hand, amiodarone blocks the hERG potassium and calcium and sodium channels, resulting in substantial QT prolongation, but carries a very low risk of degenerating into torsade de pointes 60."
reach
"These results indicate that HERG channels can be blocked by amiodarone in closed, open and inactivated states."
reach
"HERG current in oocytes was reduced by amiodarone (IC (50) = 38 micromol/L), whereas KvLQT1 and minK current was unaffected by 300 micromol/L amiodarone."
reach
"Since they are targets of various drugs with cardiac side effects we tested whether the amiodarone derivative 2-methyl-3-(3,5-diiodo-4-carboxymethoxybenzyl) benzofuran (KB130015) blocks hERG1 channels like its parent compound."
reach
"These observations raise the possibility that binding determinants of amiodarone inhibition of hERG channels may be qualitatively or quantitatively different from those for canonical high affinity hERG inhibitors."
reach
"In XREF_FIG we can compare the results of the two types of inference for real data on amiodarone block of the hERG current."
reach
"As shown in XREF_FIG, 1 muM amiodarone blocked hERG1 channels of oocytes pretreated with the vehicle (0.1% DMSO) to 55.6 +/- 5.5% (n = 6) of the control current."
reach
"Amiodarone has been reported to block hERG channels expressed in Xenopus oocytes in closed, open, and inactivated states XREF_BIBR."
Amiodarone inhibits KCNH2-G648A. 1 / 1
| 1
reach
"The reduction in amiodarone block of G648A hERG is similar to the effect of this mutation on high affinity blockers such as dofetilide, ibutilide and MK-499 but not cisapride XREF_BIBR."
Amiodarone activates KCNH2.
| 2
| 2
reach
"The amiodarone derivative KB130015 activates hERG1 potassium channels via a novel mechanism."
reach
"Like nifekalant, amiodarone, quinidine and carvedilol, but not by dofetilide, caused the current facilitation of hERG, suggesting that the facilitation is a common effect to a subset of hERG blockers."
Amiodarone decreases the amount of KCNH2.
| 1
Amiodarone decreases the amount of KCNH2. 1 / 1
| 1
reach
"In the hERG-Lite assay 47, amiodarone inhibits hERG surface expression which may result from impaired forward or enhanced backward trafficking or translation interference."
KCN affects KCNH2
| 12 8
KCN inhibits KCNH2.
| 7
KCN inhibits KCNH2. 7 / 7
| 7
sparser
"Results of compound 1G showed no hERG (human ether-a-go-go-related gene) potassium channel inhibition in human, similar to standard drug topotecan, which otherwise may cause risk of cardiotoxicity."
sparser
"Screening of drug candidates for hERG potassium channel inhibition has become an early step in testing for potential drug dependent long QT syndrome that is linked to sudden death [ xref ]."
sparser
"Moreover, the hepatotoxicity, skin sensitization, the hERG potassium channel inhibition, AMES toxicity, human maximum tolerated dose, carcinogenicity, oral rate acute, and chronic toxicity were predicted via pkCSM web server [13] at the default settings via submitting of the chemical structures in smile format."
sparser
"While testing for hERG potassium channel inhibition and QT prolongation has prevented torsade de pointes (TdP) inducing drugs from reaching the market, other new drugs are dropped from development, sometimes inappropriately ( xref )."
sparser
"GSK693 did not show any sign of cytotoxicty and no hERG potassium channel inhibition ( xref ), suggesting a low risk for general toxicity and cardiotoxicity."
sparser
"Further biological evaluation revealed that it did not show obvious cytotoxicity and hERG potassium channel inhibition at micromolar concentration."
sparser
"We demonstrated a high vulnerability to tachycardia of optically tachypaced hiPSC-CMs in EHT and the effective termination by ryanodine receptor stabilization, sodium or hERG potassium channel inhibition."
KCN binds KCNH2.
| 5 2
| 3 2
sparser
"Furthermore, this soluble peptide of N-terminus (1-135 AA) was shown to bind to membrane bound KCNH2 ( xref ) suggesting that the truncated mutant KCNH2 protein may affect formation of KCNH2 tetramer leading to abnormal function of potassium channel."
sparser
"Unfortunately, hERG1 potassium channel antagonists are strongly associated with cardiac arrhythmias: acquired long QT (aLQT2) and cardiac ventricular fibrillation; these potentially fatal events limit the use of hERG1 blockers for anticancer therapy."
sparser
"5HT 1 receptor subtypes have been suggested to account for adverse events due to interactions with HERG cardiac potassium channel and 5-hydroxytryptamine [ xref ]."
reach
"Clarithromycin inhibits autophagy in colorectal cancer by regulating the hERG1 potassium channel interaction with PI3K."
reach
"Correction : Clarithromycin inhibits autophagy in colorectal cancer by regulating the hERG1 potassium channel interaction with PI3K."
KCN binds KCNE2 and KCNH2. 1 / 1
| 1
sparser
"KvLQT1 and minK associate to form the functional slowly activated delayed rectifier potassium channel ( I Ks ) [12,13] while HERG and MiRP1 associate to form the rapidly activated delayed rectifier potassium channel ( I Kr ) [10] ."
| 1
sparser
"In acute myeloid leukemia cells, β1 integrin, VEGFR1 and hERG potassium channel form a macromolecular signaling complex that promotes cell migration and metastasis [ xref ]."
KCN activates KCNH2.
| 6
KCN activates KCNH2. 6 / 6
| 6
reach
"XREF_BIBR - XREF_BIBR Among these agents, astemizole and terfenadine are no longer in use because of cardio-toxicity caused by their potassium channel blocker activity (hERG encoded by KCNH2), which may lead to fatal cardiac arrhythmia."
reach
"Most medications that prolong the QT interval, including aminoquinolines, act by binding to and inhibiting the potassium channel protein product of the gene KCNH2 (also known as hERG), thereby blocking the rapid component of the delayed rectifier potassium current (I Kr)."
| PMC
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"C unbound plasma concentration E maximal hERG mediated QT prolongation f fraction unbound hERGhuman ether-a-go-go-related gene I repolarizing potassium current mediated by the delayed rectifier potassium channel K receptor affinity Lligand LRligand and receptor complex (receptor occupancy) LR ligand and receptor complex concentration leading to half-maximal system effect NONMEMnonlinear mixed effect modeling QTcQT interval corrected for heart rate and circadian variation DeltaQTcdrug induced QTc prolongation R receptor density gammaslope (sigmodicity) of transducer function DeltaOFVdifference in NONMEM objective function value tautransducer ratio f relative transducer ratio Introduction."
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"In particular, the correction of the trafficking of KCNH2 (LQTS2) potassium channel through intracellular mechanisms restored hERG currents and reduced arrhythmia in LQTS2 patient derived cardiomyocytes, also documenting the usefulness of iPSC-cardiomyocytes in LQTS2 modeling and drug testing."
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"Because most LQTS associated drugs interact with the HERG potassium channel (the product of KCNH2), we asked if this was the only target contributing to the observed enrichment."
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"Such unique role of hERG potassium channel was also supported by the evidence that the effect of the toxin BmKKx2 on cell differentiation was nullified in hERG deficient cell lines."
AGT affects KCNH2
| 20
AGT inhibits KCNH2.
| 9
AGT inhibits KCNH2. 9 / 9
| 9
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"In the present study, RNF4 knockdown further decreased ATO- or Ang- II induced HERG channel degradation due to PML accumulation, independent of its E3 ligase activity."
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"Correspondingly, we find that Ang II significantly enhances the time dependent reduction of mature hERG channel protein under the condition of inhibiting forward protein trafficking."
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"Ang II significantly enhanced the time dependent reduction of mature hERG channel protein."
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"To investigate the possible mechanism underlying the hERG channel protein reduction induced by Ang II, we performed parallel experiment to compare the Western blots phenotypes of fluoxetine treatment, channel mutants and Ang II treatment."
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"Ang II further significantly accelerated the degradation of the mature hERG protein."
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"Ang II decreased hERG current in HEK293 cells and significantly delayed channel activation, deactivation and recovery from inactivation."
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"In addition, the proteasomal inhibitor lactacystin (5muM) inhibited Ang II mediated the reduction of mature hERG channel protein, but the lysosomal inhibitor bafilomycin A1 (1muM) had no effect on the protein."
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"The data in Fig. 3 C summarized the time course of relative values of mature hERG channel protein and showed that Ang II significantly decreased the mature hERG channel protein compared to the control from 4 to 24 h. Thus, the results indicate that Ang II promotes the degradation of mature hERG channel protein by sustained stimulation of AT 1 receptor.Intracellular proteolysis of channel protein can take place either in the endosome and lysosome or in the cytosol by the proteasome [30]."
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"The data in Fig. 4 A illustrates the effects of lactacystin, a proteasome inhibitor, and bafilomycin A1, a lysosomal inhibitor, on hERG channel protein degradation induced by Ang II in HEK293 and hERG cells."
AGT decreases the amount of KCNH2.
| 6
AGT decreases the amount of KCNH2. 6 / 6
| 6
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"Mechanistically, an increase in PML SUMOylation by ATO or Ang II dramatically enhanced the formation of PML and Pin1 complexes in PML-NBs, leading to the upregulation of TGF-beta1 protein, eventually inhibiting HERG expression through activation of protein kinase A."
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"Cai et al. also showed that Ang II reduced the expression of mature HERG channel protein by accelerating channel proteasomal degradation through AT1 receptor by PKC activation in HEK-293 cells with stably expressed HERG channel proteins [XREF_BIBR]."
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"Immunoblot analysis indicated that GA treatment partially abolished PML SUMOylation that was induced by ATO or Ang II, consequently reversing the decreased HERG protein expression caused by ATO and Ang II."
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"Western-blot analysis showed that Ang II significantly decreased the expression of mature hERG channel protein (155-kDa band) in a time- and dose dependent manner without affecting the level of immature hERG channel protein (135-kDa band)."
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"Both arsenic trioxide (ATO) and angiotensin II (Ang II) were able to significantly reduce HERG protein expression, while also increasing PML SUMOylation and accelerating the formation of PML-NBs."
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"ATO or Ang II inhibited HERG protein expression in cardiomyocytes."
AGT activates KCNH2.
| 3
AGT activates KCNH2. 3 / 3
| 3
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"Pre-exposure of cardiomyocytes to a SUMOylation chemical inhibitor, ginkgolic acid, or the silencing of UBC9 suppressed PML SUMOylation, subsequently preventing the downregulation of HERG induced by ATO or Ang II."
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"Conversely, knockdown of RNF4 led to a remarkable increase in PML SUMOylation and the function of PML-NBs, further promoting ATO- or Ang II induced HERG protein downregulation."
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"The protein kinase C (PKC) inhibitor bisindolylmaleimide 1 (1muM) antagonized the reduction of mature hERG channel protein induced by Ang II."
AGT increases the amount of KCNH2.
| 1
AGT increases the amount of KCNH2. 1 / 1
| 1
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"Immunoblot analysis indicated that GA treatment partially abolished PML SUMOylation that was induced by ATO or Ang II, consequently reversing the decreased HERG protein expression caused by ATO and Ang II."
AGT binds KCNH2.
| 1
| 1
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"The inhibition of I kr was realized via its phosphorylation by ANGII-AT1R-PKC pathway or Ang II directly interact with KCNH2, and that was not influenced by the change of Ca 2+ concentration or PKA pathway."
PRKACA affects KCNH2
4 8 7 |
PRKACA phosphorylates KCNH2.
4 4 5 |
PRKACA phosphorylates KCNH2 on S1137. 5 / 5
1 1 3 |
hprd
No evidence text available
hprd
No evidence text available
signor
"Deletion of protein kinase a phosphorylation sites in the herg potassium channel inhibits activation shift by protein kinase afour consensus pka phosphorylation sites (s283a, s890a, t895a, s1137a)"
biopax:phosphositeplus
No evidence text available
hprd
No evidence text available
PRKACA phosphorylates KCNH2 on S283. 4 / 4
1 1 2 |
hprd
No evidence text available
biopax:phosphositeplus
No evidence text available
signor
"Deletion of protein kinase a phosphorylation sites in the herg potassium channel inhibits activation shift by protein kinase afour consensus pka phosphorylation sites (s283a, s890a, t895a, s1137a)"
hprd
No evidence text available
PRKACA phosphorylates KCNH2 on S890. 2 / 2
1 1 |
signor
"Deletion of protein kinase a phosphorylation sites in the herg potassium channel inhibits activation shift by protein kinase afour consensus pka phosphorylation sites (s283a, s890a, t895a, s1137a)"
biopax:phosphositeplus
No evidence text available
PRKACA phosphorylates KCNH2 on T895. 2 / 2
1 1 |
signor
"Deletion of protein kinase a phosphorylation sites in the herg potassium channel inhibits activation shift by protein kinase afour consensus pka phosphorylation sites (s283a, s890a, t895a, s1137a)"
biopax:phosphositeplus
No evidence text available
PRKACA activates KCNH2.
4 |
PRKACA activates KCNH2. 4 / 4
4 |
signor
"Deletion of protein kinase a phosphorylation sites in the herg potassium channel inhibits activation shift by protein kinase afour consensus pka phosphorylation sites (s283a, s890a, t895a, s1137a)"
signor
"Deletion of protein kinase a phosphorylation sites in the herg potassium channel inhibits activation shift by protein kinase afour consensus pka phosphorylation sites (s283a, s890a, t895a, s1137a)"
signor
"Deletion of protein kinase a phosphorylation sites in the herg potassium channel inhibits activation shift by protein kinase afour consensus pka phosphorylation sites (s283a, s890a, t895a, s1137a)"
signor
"Deletion of protein kinase a phosphorylation sites in the herg potassium channel inhibits activation shift by protein kinase afour consensus pka phosphorylation sites (s283a, s890a, t895a, s1137a)"
PRKACA binds KCNH2.
2 |
2 |
hprd
No evidence text available
hprd
No evidence text available
KCNH2 affects dofetilide
| 2 19
KCNH2 binds dofetilide.
| 2 14
| 2 13
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"Molecular determinant of high-affinity dofetilide binding to HERG1 expressed in Xenopus oocytes : involvement of S6 sites."
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"Similar to female predominance of arrhythmia in the acquired setting, which suggests interactions between hERG, dofetilide and oestradiol, the female predominance of inherited arrhythmia linked the the G604S mutations, suggests that oestradiol may differentially interact with the mutant hERG channel compared to WT."
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"High-affinity dofetilide binding to hERG expressed in Xenopus oocytes involves Phe656 residue."
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"Interestingly, WAY-123,398, which did not inhibit [3 H] dofetilide binding to whole HEK293 cells (Finlayson et al., 2001b), reduced [3 H] dofetilide binding to HERG membranes, although not completely."
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"GZ-11610-induced inhibition of [3 H] dofetilide binding to hERG channels assessed potential cardiotoxicity."
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"Utilizing medicinal chemistry first principles (e.g., introducing rigidity, lowering cLogD) a new benzthiazole series was designed, congeners of 1-3, which led to compounds 7a, 7c, 12a-d which exhibited LTA (4) H IC (50) = 3-6 nM and hERG Dofetilide Binding IC (50) = 8.9->> 10 muM."
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"[3 H] dofetilide binding to HERG transfected membranes was performed in a sodium buffer without bovine serum albumin, as for whole cell studies (Finlayson et al., 2001b)."
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"In this study, we show that [3 H] dofetilide binding to HERG transfected membranes is inhibited by antiarrhythmics and structurally unrelated compounds known to prolong the QT interval in man.Human embryonic kidney (HEK293) cells stably expressing HERG (Zhou et al., 1998) were maintained in culture and membranes prepared as described previously (Finlayson et al., 2001a)."
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"The method for determining [3 H] dofetilide binding to hERG protein expressed by the cell membranes was described previously."
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"In addition, [3 H] dofetilide binding to HERG membranes was also reduced in a concentration dependent manner by the antipsychotics pimozide (K i = 70.6 +/-11.8 nM, n H = 0.89 +/-0.12, n = 4) and haloperidol (K i = 549 +/-83.6 nM, n H = 0.75 +/-0.07, n = 4), and by the antihistamine terfenadine (K i = 381 +/-60.0 nM, n H = 0.76 +/-0.14, n = 4), all of which cause QT prolongation (Kang et al., 2000; Vandenberg et al., 2001)."
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"Also, GZ-11610 inhibited [3 H] dofetilide binding to hERG channels expressed on HEK-293 cell membranes, with a Ki of 9.50 muM and an Imax of> 80% (XREF_FIG)."
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"[3H] dofetilide binding to HERG transfected membranes : a potential high throughput preclinical screen."
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"Evaluation of GZ-793A for potential cardiac liabilities revealed that GZ-793A inhibited with high affinity (IC 50 = 0.81 +/- 0.11 muM) [3 H] dofetilide binding to hERG channels expressed by HEK-293 cells (XREF_FIG)."
Dofetilide binds KCNH2 and 10e. 1 / 1
| 1
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"10e blocks hERG channel current in electrophysiological patch clamp experiments, and computational docking experiments predict that the dofetilide core of 10e binds hERG channel in a conformation similar to that previously predicted for 1."
KCNH2 inhibits dofetilide.
| 4
| 2
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"Doxepin is quite distinct in this regard from a number of other drugs, including the archetypal high affinity HERG blocking methanesulphonanilide drugs E-4031 and dofetilide, for which I HERG inactivation exerts a strong influence on blocking potency - either as a direct consequence of inactivation-state dependent block, or due to conformational changes during inactivation facilitating optimal orientation of S6 helical residues to which drugs bind XREF_BIBR."
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"Of note, the similar levels of hERG potassium channel block induced by 2-3 nM dofetilide and 6.9 muM ranolazine (approximately 52%) induced> 200 ms of APDc and FPDc prolongation and multiple arrhythmic events in dofetilide treated cells, but only APDc and FPDc prolongation (< 150 ms) without arrhythmias in ranolazine treated cells."
KCNH2-S620T inhibits dofetilide. 1 / 1
| 1
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"In contrast, the S631A and S620T HERG mutations both eliminated inward rectification and reduced dofetilide affinity by approximately 10- and approximately 100-fold respectively."
KCNH2-S631A inhibits dofetilide. 1 / 1
| 1
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"In contrast, the S631A and S620T HERG mutations both eliminated inward rectification and reduced dofetilide affinity by approximately 10- and approximately 100-fold respectively."
KCNH2 activates dofetilide.
| 1
| 1
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"Co-expressing KCNH2 with KCR1 E33D and KCR1 WT to approximate the heterozygous condition enhanced the effects of dofetilide on the KCNH2 current, similar to expressing KCNH2 alone or co-expressing KCNH2 and KCR1 E33D (Figs. 3B, D, 4, and 5)."
Ion channel affects KCNH2
| 14 4
| 7 3
sparser
"For this reason it was desired to lower interactions with the hERG and other ion channels."
sparser
"The authors hypothesize that the inhibitory mechanism might be mediated via an interaction between Na,K,ATPase and other ion channels like the voltage-gated K+ channel hERG, whose expression is induced by CMV infection and downregulated by cardiac glycoside treatment [15]."
sparser
"The oxacyclic group effect of compound 33 against hERG ion channel binding might be associated with σ-electron withdrawing effect of the ether oxygen atom for reducing electron density of the adjacent aryl moiety, lower lipophilic effect that is similar to the above examples, and/or electron lone-pair effect of the oxygen atom, compared to the carbocyclic moiety of compound 38 ."
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"As supporting data in the previous study in vitro in terms of the electron effects, MCOPPB that has NH -piperidine (electron-poor ring) as 2-substituent on its benzimidazole moiety showed little hERG ion channel binding affinity, contrary to the corresponding 2-aryl group (electron rich ring) analogs that showed higher binding affinities [5]."
sparser
"The human ether-a-go-go-related gene (HERG) protein forms the ion channel responsible for the rapidly acting delayed rectifier potassium current, I(Kr), and its blockade is a significant contributor to prolongation of the QT interval."
sparser
"The hERG ion channel is formed by the KCNH2 protein that consists of six transmembrane alpha helices, a pore helix and cytoplasmically located N- and C-termini."
sparser
"In this issue Yarema and co-workers use a dual in silico/experimental approach to address this challenge, systematically defining the impact of variables such as acyl chain length and ester regiochemistry on important pharmacological parameters including solubility and hERG ion channel binding."
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"The oxacyclic group effect of compound 33 against hERG ion channel binding might be associated with sigma-electron withdrawing effect of the ether oxygen atom for reducing electron density of the adjacent aryl moiety, lower lipophilic effect that is similar to the above examples, and/or electron lone-pair effect of the oxygen atom, compared to the carbocyclic moiety of compound 38."
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"In the design and SAR studies of the analogs against hERG ion channel binding affinity in vitro, several effective structures and significant and/or useful contributing-factors for reducing affinities were found or suggested."
sparser
"The KCNH2 and KCNQ1 mutations are associated with different ion channel dysfunctions, xref , xref and gene specific triggers of arrhythmias. xref In LQT-1, it is recognized that exercise (catecholamine) is the primary trigger because of the malfunctioning I Ks channels that leads to less effective shortening of the QT intervals during tachycardia than in normal individuals."
Ion channel inhibits KCNH2.
| 7 1
| 7 1
sparser
"It exhibits a low human ether-a-go-go-related gene (hERG) ion channel inhibition, excellent systemic exposure, crosses the blood-brain barrier in mice when administered orally, and BKI-1553 treatment lead to reduced parasite burden in the brain, lungs and liver of T. gondii infected mice ( xref )."
sparser
"The results indicate that considering only the hERG ion channel inhibition of only the parent drug is potentially misleading, and the inclusion of active metabolite data and the influence of other ion channel currents should be considered to improve the prediction of potential cardiac toxicity."
sparser
"Containers 26 and 27 show no evidence of hERG ion channel inhibition up to 25 mM which paves the way for their further development."
reach
"SAR studies of this ion channel have shed light on the structural requirements for hERG interaction but most importantly may reveal drug design principles to reduce hERG affinity."
sparser
"Both CHK1 potency and off-target human ether-a-go-go-related gene (hERG) ion channel inhibition were dependent on lipophilicity and basicity in this series."
sparser
"Incorporation of a 6-azaindole afforded a marked increase in cellular potency but was associated with poor PK and hERG ion channel inhibition."
sparser
"The compounds are structurally related to a series we disclosed previously, but are improved with respect to cytochrome P-450 enzyme (CYP) and potassium ion channel Kv11.1 (hERG) inhibition and synthetic accessibility."
sparser
"Moderate in vitro cytochrome P450 (CYP) and potassium ion channel Kv11.1 (hERG) inhibition were uncovered as potential liabilities for the chemical series."
KCNH2 affects calcium(2+)
| 18
KCNH2 activates calcium(2+).
| 13
| 13
reach
"Therefore, we tested the hypothesis that, stimulation of hERG1 activity could promote calcium influx in breast cancer cells."
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"The cytotoxic chemotherapeutics doxorubicin and epirubicin, known to cause cardiomyopathy, preferentially reduced Ca (i) (2+) transient amplitude and sarcoplasmic reticulum (SR) Ca (2+) content, whereas Torsade de Pointes (TdP) inducers and potent hERG channel blockers (amiodarone, cisapride, dofetilide, E-4031 and terfenadine) predominately suppressed diastolic Ca (i) (2+) and contraction rate, and prolonged Ca (i) (2+) transient duration."
reach
"In addition, the blockage of hERG potassium channel by toxin BmKKx2 was able to decrease the intracellular Ca 2+ concentration during the K562 cell differentiation, providing an insight into the mechanism of hERG potassium channel regulating this cellular process."
reach
"Importantly, hERG1 inhibition by E4031 (1 microM) prevented radiation induced CaMKIIs activation and cdc2 inactivation (XREF_FIG, 5 th -8 th lane and XREF_FIG, closed bars) suggesting that Ca 2+ signals modulated by hERG1 were required for radiation induced CaMKIIs activation and inhibition of cdc2."
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"Importantly, hERG1 inhibition by E4031 (1 microM) prevented radiation induced CaMKIIs activation and cdc2 inactivation (XREF_FIG, 5 th -8 th lane and XREF_FIG, closed bars) suggesting that Ca 2+ signals modulated by hERG1 were required for radiation induced CaMKIIs activation and inhibition of cdc2."
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"Next, we analyzed by immunoblotting potential hERG stimulated signaling pathways in K562 cells by analyzing the activities of the Ca 2+ effector proteins CaMKIIs (Ca 2+ / calmodulin dependent protein kinase II isoforms) and their downstream target cdc2 (cyclin dependent kinase 1, CDK1) (XREF_FIG)."
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"Next, we analyzed by immunoblotting potential hERG stimulated signaling pathways in K562 cells by analyzing the activities of the Ca 2+ effector proteins CaMKIIs (Ca 2+ / calmodulin dependent protein kinase II isoforms) and their downstream target cdc2 (cyclin dependent kinase 1, CDK1) (XREF_FIG)."
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"In addition we have also reveal that hERG1 stimulation induces an increase in intracellular calcium that is required for cyclin E2 degradation."
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"In this work, the inhibition of hERG channel currents by scorpion toxin BmKKx2 was found to decrease the intracellular Ca 2+ concentration during the differentiation process of K562 cells (XREF_FIG)."
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"Having established that NS1643 treatment increases intracellular calcium levels, we investigated on the role of hERG1 driven calcium entry on cyclin E2 degradation."
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"HERG contributes to phase three repolarization by opposing the depolarizing Ca 2+ influx during the plateau phase [6]."
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"Moreover, the KCNH2 potassium channels may directly regulate the characteristics of sodium and calcium channels XREF_BIBR."
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"Blockage of hERG channel by BmKKx2 causing the Ca 2+ concentration decrease during the erythroid differentiation of K562 cells."
KCNH2 inhibits calcium(2+).
| 4
| 4
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"Furthermore, the specific blockage of scorpion toxin BmKKx2 could suppress the expression of hERG potassium channel and decrease the Ca 2+ concentration during the erythroid differentiation of K562 cells."
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"Stimulation of hERG1 channel activity promotes a calcium dependent degradation of cyclin E2, but not cyclin E1, in breast cancer cells."
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"Reduction of IKr caused by hERG block delays repolarization, increasing the probability of L-type calcium current triggering extra beats called early afterdepolarizations (EADs; Figure XREF_FIG b), which can initiate TdP."
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"Altogether, our findings strongly suggest that stimulation of the hERG1 potassium channels in breast cancer cells induces a calcium dependent degradation of cyclin E2 via activation of an ubiquitin dependent proteasome pathway."
KCNH2 ubiquitinates calcium(2+).
| 1
KCNH2 ubiquitinates calcium(2+). 1 / 1
| 1
reach
"Similar to hERG1, the E3-ligases that ubiquitinate L-type Ca 2+ -channels remain to be identified with further investigations, although a role for CSN5 in the inhibition of cardiac L-type Ca 2+ -channel activity has been shown, suggesting cullin E3-ligases function at this location [XREF_BIBR]."
Methadone affects KCNH2
| 1 17
Methadone inhibits KCNH2.
| 1 16
| 1 16
reach
"Methadone, buprenorphine and many structurally diverse drugs can block the hERG XREF_BIBR, XREF_BIBR resulting in a prolonged QTc interval XREF_BIBR."
reach
"While methadone is known to prolong the QT interval by blocking the cardiac human ether-a-go-go-related (hERG) potassium channel, the effect of methadone on QTc is associated with chronic dosing in adults rather than an isolated dose and it is the daily methadone dose that correlates positively with the QTc interval."
reach
"The opioid agonist methadone has previously been demonstrated to inhibit hERG currents, and there are reports of serious cardiac arrhythmias and deaths from TdP and ventricular fibrillation in patients taking methadone."
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"Furthermore, methadone blocks hERG in a concentration dependent manner (Katchman et al., 2002)."
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"Methadone is the most prescribed heroin maintenance treatment and is known to inhibit the cardiac potassium channel hERG, which recapitulates IKr."
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"Both S- and R-form of methadone inhibit the cardiac potassium channel hERG (S-methadone is more potent blocker) [XREF_BIBR], which may increase heart risk."
reach
"Methadone inhibition of hERG has been suggested to be caused possibly by direct binding to the hERG channel, perhaps at the voltage sensor [XREF_BIBR]."
reach
"Inhibition of hERG by methadone is problematic, as methadone treatment may lead to cardiotoxicity (long QT syndrome) [XREF_BIBR, XREF_BIBR]."
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"Using patch clamp recording in human stem cell derived cardiomyocytes and stably transfected mammalian cells, we found that methadone produced concentration dependent AP prolongation and ion channel block at low micromolar concentrations : hERG (IC50 = 1.7 muM), hNav1.5 (11.2 muM tonic block; 5.5 muM phasic block), and hCav1.2 (26.7 muM tonic block; 7.7 muM phasic block)."
reach
"QTc prolongation by hERG channel blockers such as methadone provides the substrate for torsade de pointes arrhythmia, but an additional trigger is typically required to initiate arrhythmia."
reach
"Additionally, unsuspected polymorphisms in the gene for the hERG channel occur in 2% of the healthy population and may be associated with increased sensitivity to hERG channel blockade by methadone or similar compounds."
reach
"Methadone causes the blockade of hERG current and causes clinically significant QTc prolongation."
reach
"It was without surprise that methadone racemate was demonstrated to block I hERG1 in transfected HEK293 cells with an IC 50 of ~ 10 muM."
reach
"Methadone inhibits the cardiac potassium channel hERG and can cause a prolonged QT interval."
reach
"Methadone blocks the cardiac ionic channels hERG, the human ether-a-Go-Go tetrameric channel encoded by KCNH2 and responsible for the IKr current, in a concentration dependent manner (Katchman et al., 2002)."
reach
"Both methadone and heroin inhibit hERG currents in a concentration dependent manner."
Methadone activates KCNH2.
| 1
| 1
reach
"The objectives of this study are to determine : (1) whether the administration of intravenous (i.v.) methadone causes QTc prolongation in humans; (2) whether methadone and/or chlorobutanol block cardiac HERG potassium currents (IHERG) in vitro."
BeKm-1 affects KCNH2
| 17
BeKm-1 inhibits KCNH2.
| 10
| 10
reach
"BeKm-1 blockade of HERG varies inversely with temperature, time, voltage, use and frequency, and this has not been shown before for this or any other HERG blocking compound."
reach
"Our focus here is BeKm-1, a HERG specific peptide toxin that can suppress HERG in the low nM concentration range."
reach
"BeKm-1 inhibited hERG1 channels with an IC (50) of 3.3 nm, but had no effect at 100 nm on hEAG, hSK1, rSK2, hIK, hBK, KCNQ1 and KCNE1, KCNQ2 and KCNQ3, KCNQ4 channels, and minimal effect on rELK1."
reach
"As summarized in Fig. 5 C, inhibition of hERG by BeKm-1 was higher at negative voltages and declined at more positive voltages."
reach
"However, as for BeKm-1, it is feasible that alternative conformational changes independent of inactivation could contribute to the rapid diminution of ergtoxin block upon depolarisation to +80 mV.Collectively, the data in Figs. 2 and 3 suggest that BeKm-1 inhibits I HERG by a mechanism that includes closed channel state blockade."
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"Previous data showed that the maximum degree of hERG current suppression by BeKm-1 was 90 +/- 1% (28)."
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"Examples include charybdotoxin (ChTX), which is targeted toward Kv1.3 and BKCa channels XREF_BIBR, scyllatoxin (ScyTx), which inhibits SKCa channels XREF_BIBR, maurotoxin (MTX), which is targeted toward IKCa channels XREF_BIBR, and BeKm-1, which inhibits Herg channels XREF_BIBR."
reach
"BeKm-1 does not totally suppress hERG currents : even in the presence of 1000 nM BeKm-1 (100-fold its IC 50) there remained some residual hERG current amounting to ~ 10% of the control amplitude (28)."
reach
"For WT BeKm-1 binding to the WT hERG channel, we have shown that the maximal degree of BeKm-1 suppression of WT hERG was ~ 90%, and the K d value estimated based on a single toxin concentration (10 nM) was not different from that determined by a complete dose response relationship (from 1 to 1000 nM) (28)."
reach
"Rapid superfusion of 25 nM BeKm-1 onto cells during depolarisation led to HERG blockade (~ 23 +/-1%, which is of similar magnitude to that seen at the end of depolarisations in Fig. 2F), suggesting that BeKm-1 can block HERG channels in the open state."
BeKm-1 binds KCNH2.
| 6
| 6
reach
"Therefore, these aspects are where we begin to characterize BeKm-1 and HERG interaction and to deduce the mechanism of toxin action.We examine the effects of 1-1000 nM BeKm-1 on the HERG current amplitude, using the same voltage clamp protocol and data analysis as those described for Fig. 2."
reach
"This result is consistent with our hypothesis that the structure of the S5-P linker is highly dynamic, and can be easily perturbed by mutations, toxin binding, or conformational changes in other parts of the protein.The structural model presented here not only matches seven out of eight pairs of interacting residues identified in the mutant cycle analysis, but also provides mechanistic insights into the unique features of BeKm-1 and hERG interaction."
reach
"To study the mechanism of BeKm-1 action, we characterize BeKm-1 and HERG interaction in terms of its sensitivity to changes in the extracellular or intracellular ionic composition and to changes in membrane voltage."
reach
"The models were further restrained based on mutant cycle analysis of BeKm-1 and hERG interactions."
reach
"It is important to point out that although such a strong state dependence of BeKm-1 and hERG interactions appears similar to that of " gating modifying toxins " that bind to the S3-S4 linkers of target channels (43,44), the BeKm-1 binding site is in the outer vestibule region of the hERG channel."
reach
"Starting from the hERG and BeKm-1 structures, a considerably reasonable BeKm-1 and hERG complex structure was then screened out and identified by protein protein docking, molecular dynamics (MD) simulations, and calculation of relative binding free energies."
BeKm-1 activates KCNH2.
| 1
BeKm-1 activates KCNH2. 1 / 1
| 1
reach
"Both BeKm-1 and ErgTx1 can suppress the HERG current in a concentration dependent and reversible manner."
Tat affects KCNH2
| 1 15
Tat inhibits KCNH2.
| 1 7
Tat inhibits KCNH2. 8 / 8
| 1 7
reach
"Results showed that treatment of HIV Tat protein (200 ng/ml) for 24 h significantly increased ROS generation and the antioxidant tempol prevented HIV Tat induced hERG channel inhibition (Figs. 2 E and F)."
reach
"Since HIV Tat protein had no the acute effect on hERG K + currents, but inhibited hERG currents after 24 h incubation, we speculated that HIV Tat protein might inhibit hERG K + currents through the inhibition of hERG channel expression."
reach
"Therefore, we thought that the kinetics changes of hERG channels in HIV Tat incubated cells contributed negligibly to the HIV Tat induced decreases of hERG K + currents."
reach
"As shown in Fig. 1 E of the representative recordings, compared with the control and inactivated HIV Tat protein (HIV Tat protein was inactivated by heating), HIV Tat protein (200 ng/ml) significantly inhibited the hERG K + currents."
sparser
"Results showed that treatment of HIV Tat protein (200 ng/ml) for 24 h significantly increased ROS generation and the antioxidant tempol prevented HIV Tat induced hERG channel inhibition ( Figs."
reach
"Results were shown in Figs. 2 G and H. Although we found HIV Tat protein inhibited hERG K + channels but not Kv4.3 and Kv4.2 K + channels, we did not think it only specifically affected hERG K + channels.IKr (hERG K + currents) is the main component of IK currents in cardiomyocytes of guinea pigs."
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"HIV Tat protein inhibits hERG K+ channels : a potential mechanism of HIV infection induced LQTs."
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"HIV Tat protein at 200 ng/ml concentration showed no acute effect on hERG currents, but HIV Tat protein (200 ng/ml) incubation for 24 h significantly inhibited hERG currents."
Tat decreases the amount of KCNH2.
| 6
Tat decreases the amount of KCNH2. 6 / 6
| 6
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"The MTT assay showed that HIV Tat protein at 50 and 200 ng/ml had no effect on the cell viability, indicating that inhibition of hERG channel expression by HIV Tat protein is not related to the cytotoxicity."
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"HIV Tat protein incubation (200 ng/ml) for 24h had no effect on the hERG mRNA expression, but dose-dependently inhibited hERG protein expression."
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"The present data showed that HIV Tat protein inhibited hERG channel protein expression but had no effect on hERG channel mRNA expression, indicating that HIV Tat protein inhibits the translation step of hERG protein synthesis."
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"HIV Tat protein increased reactive oxygen species (ROS) generation and the inhibition of hERG channel protein expression by HIV Tat protein was prevented by antioxidant tempol."
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"We found that HIV Tat protein, the product of regulatory HIV genes, inhibited hERG K + currents and hERG channel protein expression."
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"We further performed the immunocytochemistry analysis and the results confirmed that HIV Tat protein inhibited hERG protein expression."
Tat increases the amount of KCNH2.
| 1
Tat increases the amount of KCNH2. 1 / 1
| 1
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"We also found that HIV Tat protein significantly increased ROS generation and antioxidant tempol prevented HIV Tat induced downregulation of hERG protein expression."
Tat activates KCNH2.
| 1
Tat activates KCNH2. 1 / 1
| 1
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"In myocytes, Tat accelerates hERG and KCNE1 and KCNQ1 deactivation, thereby increasing action potential duration 22."
SSM4 affects KCNH2
| 16
SSM4 inhibits KCNH2.
| 15
SSM4 inhibits KCNH2. 15 / 15
| 15
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"The Doa10 mediated degradation of Erg1 is stimulated by lanosterol, which is a downstream product of this pathway."
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"Moreover, Doa10 dependent degradation of Erg1 requires a single lysine residue that is poorly conserved outside fungi, while proteasomal dependent degradation of SM depends on an N-terminal fragment conserved only in higher animals."
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"Taken together, these data demonstrate that Doa10 dependent degradation of Erg1 is regulated by the levels of sterols, most likely lanosterol."
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"The degradation of Erg1 by Doa10 does not involve proteins that are involved in degrading misfolded proteins but does involve proteins that are involved in ERAD, specifically Cdc48, which is an ATPase involved in extruding proteins from the ER membrane."
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"Thus, the lysine residue at position 311 is essential for Doa10 dependent degradation of Erg1."
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"These experiments indicate that sterol depletion specifically affects the Doa10 dependent degradation of Erg1 but not other Doa10 substrates, such as misfolded proteins."
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"Altogether, the data presented so far indicate that sterol dependent degradation of Erg1 by Doa10 is part of a feedback system essential for sterol homeostasis."
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"We then asked whether the Doa10 dependent degradation of Erg1 had an effect on sterol homeostasis."
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"Besides the Doa10 dependent degradation of Erg1 in yeast, we show that the Doa10 homologue Teb4 also promotes the degradation of SM in mammalian cells."
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"In sum, these data show that Are1, Are2 dependent sterol esterification and Doa10 dependent degradation of Erg1 are parallel mechanisms preventing abnormal accumulation of potentially toxic sterol intermediates."
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"Therefore, lanosterol accumulation induced by fluconazole treatment stimulates Doa10 dependent degradation of Erg1."
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"The Doa10 dependent degradation of Erg1 is regulated by lanosterol."
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"We have now found that in yeast, high levels of lanosterol also lead to a decrease in flux through the sterol pathway, in this case by the Doa10 dependent degradation of Erg1."
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"We then tested whether Doa10 dependent degradation of Erg1 was affected by the levels of cellular sterols."
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"We show that Doa10 dependent degradation of Erg1 is regulated by the levels of lanosterol and that, together with sterol esterification, it is essential for preventing the accumulation of toxic sterol intermediates."
SSM4 activates KCNH2.
| 1
SSM4 activates KCNH2. 1 / 1
| 1
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"This modulation of Erg1 by Doa10 is important in dictating membrane fluidity."
| 16
| 12
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"HERG1 contributes to poor prognosis in patients with ESCC by promoting ESCC cell proliferation, migration, and invasion via TXNDC5 through the PI3K and AKT signaling pathway."
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"HERG1 can increase oncogenic potential in leukemias by affecting one of several ways facilitating leukemogenesis : (1) balance between proliferation and cell death; (2) invasiveness, depending on the fine balance between adhesion and motility, the latter being in turn dependent on polarized volume changes; (3) resistance to chemotherapy [XREF_BIBR, XREF_BIBR]; (4) angiogenesis, via secretion of vascular endothelial growth factor (VEGF) and positively feedbacked microvesicles release [XREF_BIBR, XREF_BIBR]."
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"HERG1 silencing, as well as miR-96 over-expression inhibits the PDAC cell growth and invasiveness in vitro, and reduces tumorigenicity in vivo."
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"For instance, in human acute myeloid leukemia cells, hERG1 channels appear to mediate the vascular endothelial growth factor receptor-1-dependent cell migration and invasion, both in vitro and in vivo."
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"This suggests that ER-G1 stimulates cancer cell proliferation by enabling tumor expansion rather than directly stimulating cell growth and division.Based on tumor morphology, we hypothesized that ER-G1 stimulates tumor growth by facilitating tissue remodeling and invasion."
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"The herg1 gene and HERG1 protein are expressed in many colon cancer cell lines, and the activity of HERG channels modulates colon cancer cell invasiveness."
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"HERG potassium channels enhance tumor invasiveness and breast cancer proliferation."
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"Silencing of hERG1 Gene Inhibits Proliferation and Invasion, and Induces Apoptosis in Human Osteosarcoma Cells by Targeting the NF-kappaB Pathway."
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"HERG1 has also been shown to enhance GC cell invasion and proliferation, induce cell cycle progression in vitro, and promote tumor genesis and growth in vivo."
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"We conclude that in AML, hERG1 channels mediate the FLT-1-dependent cell migration and invasion, and hence confer a greater malignancy."
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"Pharmacological inhibition of HERG channels reduces proliferation and impairs invasiveness in a variety of cancer cell types."
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"Invitro cell growth was unaffected, but ER-G1 strongly enabled matrix degradation and tissue invasion."
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"[Downregulation of Herg1 suppresses osteosarcoma proliferation and invasion by targeting Hippo signaling pathway]."
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"XREF_FIG - XREF_FIG, hERG1 downregulation and/or inhibition prevented proliferation and invasion, and induced apoptosis of osteosarcoma cells."
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"Knockdown of hERG1 significantly suppressed cellular proliferation and invasion, and induced apoptosis, while inhibition of hERG1 significantly decreased activation of NF-kappaB."
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"Effects of hERG potassium channel protein on the biological behavior of the tumor that can inhibit the growth of tumor cells by inhibiting the expression or channel current of IhERG and promote tumor cell differentiation or apoptosis, reduce its invasiveness."
E-4031 affects KCNH2
| 16
E-4031 inhibits KCNH2.
| 15
E-4031 inhibits KCNH2. 15 / 15
| 15
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"No effect of HERG channel blockage by E-4031 on cell proliferation."
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"Use of HERG blockers including E-4031 and ergtoxin have still not been tested in vivo studies but do show a promising role in potential use with chemotherapeutic agents or in chemoresistant disease."
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"The selective hERG blocker E-4031 increased arrhythmogenicity in control cardiac cells and even more frequently in LQT2 cardiomyocytes (XREF_FIG)."
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"However, neither E-4031 nor MK-499 at a concentration of 1 IIM blocked HERG current, even after the incubation of the oocytes for up to 4 hr in these drugs."
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"E-4031 is an inhibitor of the K V 11.1 (hERG), which mediates the repolarizing I Kr current in the action potential [XREF_BIBR]."
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"To determine the effect of E-4031 (an inhibitor of the KCNH2 channel) on beating frequency, videos were taken at the baseline (drug-free culture medium), with the drug, and following washout of the drug."
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"Experimental results XREF_BIBR shown in XREF_FIG (top) illustrate that E2 (1 nM) considerably increased the suppression of hERG by E-4031 (light gray line)."
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"E-4031 could specifically block hERG1 channels when applied to cells maintained in standard extracellular saline solutions at concentrations of approximately 1 muM [26], so 1 muM E-4031 was therefore applied in all subsequent experiments."
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"The resulting dose response curve shows an increase in the IC 50 for E-4031 inhibition of hERG 1a/1b vs. 1a currents, from 6.2 +/- 1.1 nM to 25.6 +/- 4.3 nM, respectively (XREF_FIG)."
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"Because this drug is no longer available, we used the HERG blocker E-4031 to evaluate susceptibility to arrhythmia in control and A561P-UhiPS CMs."
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"Selective hERG channel blockade by E-4031 reduced proliferation in cancerous cell lines."
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"In the present experiments in HEK 293 cells, we found that E-4031 blocked HERG current in similarly low concentrations (IC 50 7.7 nM)."
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"HERG current was blocked by low concentrations of E-4031 (IC50 7.7 nM), a value close to that reported for I (Kr) in native cardiac myocytes."
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"E-4031 has also been shown to inhibit HERG channels [XREF_BIBR] while ergtoxin is a specific HERG blocker [XREF_BIBR]."
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"In line with previous findings that hERG channel blockage by E-4031 did not affect the K562 apoptosis [XREF_BIBR], our work showed scorpion toxin BmKKx2 could not cause the apoptosis by itself."
E-4031 activates KCNH2.
| 1
E-4031 activates KCNH2. 1 / 1
| 1
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"Pharmacological experiments showed that the hERG channels could be blocked by the chemical molecule blockers of E-4031 or Way123,398."
| 1 15
Protriptyline inhibits KCNH2.
| 1 14
| 1 14
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"In this study, we used the HERG channel expressed in Xenopus oocytes or HEK cells to test whether protriptyline would block the HERG channel and to examine inhibiting mechanisms.HERG (accession no."
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"We found that the time course of the channel blockade was dependent on the activation frequency, with HERG blockade by protriptyline occurring more quickly at higher activation frequencies."
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"Therefore, to understand the mechanisms underlying protriptyline induced electrophysiological changes in the action potential and ECG, it is important to determine the effects of this drug on ion channels other than HERG.We have shown here that the protriptyline blockade of HERG, and possibly I Kr, was more prominent at higher frequencies, which may not be consistent with the reverse use dependent repolarization lengthening by other I Kr blockers in cardiac cells (Hondeghem and Snyders, 1990)."
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"We found that protriptyline blocked HERG in a mammalian cell line with an IC 50 of ~ 1.1 muM, which is at the supra-therapeutic level compared with the reports of both the therapeutic serum concentration (Risch et al., 1979) and that in which the drug causes QTc prolongation and ventricular tachycardia (Magorien et al., 1979)."
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"In this series of experiments, 50 muM protriptyline reduced HERG outward currents at the end of the 0 mV pulse by 45.1% +/- 5.0% (n = 8)."
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"The HERG-current inhibition by 50 muM protriptyline at different voltages (- 40, - 20, 0, + 20, and + 40 mV) was 10.2% +/- 10.1%, 20.6% +/- 6.1%, 27.7% +/- 2.4%, 35.1% +/- 2.7%, and 50.2% +/- 6.7%, respectively, suggesting that the protriptyline induced blockade of HERG currents progressively increases with increasing depolarization."
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"HERG blockade by protriptyline was use dependent, exhibiting a more rapid onset and a greater steady-state block at higher frequencies of activation."
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"Taken together, these results indicate that it is necessary to test each TCA experimentally to evaluate its potential to block the HERG channel since the HERG blocking potencies and inhibitory mechanisms of TCAs vary widely and can not be predicted based on structure alone.In the present work we have shown that the antidepressant drug, protriptyline, blocks HERG channels in Xenopus oocytes and HEK cells, suggesting that the drug induced arrhythmias observed in protriptyline treated patients may be due, at least in part, to protriptyline inhibition of I Kr."
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"Computer simulation of HERG blocking by protriptyline suggested that protriptyline binds the HERG channel at the internal chamber and makes a hydrogen bond to the carbonyl oxygen of Leu622."
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"Taken together, protriptyline inhibits HERG channels predominantly in the open and inactivated state rather than in the closed state.To examine the use-dependence of the protriptyline effect, HERG channels were activated by 0.3 s depolarizing steps up to + 20 mV from a holding potential of - 90 mV followed by a repolarizing step to - 40 mV (300 ms) to elicit outward tail currents."
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"The IC (50) for protriptyline block of HERG current in Xenopus oocytes progressively decreased relative to the degree of depolarization, from 142.0 microM at -40 mV to 91.7 microM at 0 mV to 52.9 microM at +40 mV."
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"This raises the possibility that protriptyline may prolong the action potential duration in vivo, and may increase the QT interval by inhibiting the HERG current, which can eventually result in torsades de pointes and sudden cardiac death.It is necessary to test chemical entities experimentally for potential blockade of the HERG channel because the drugs that inhibit HERG channels are structurally diverse (Haverkamp et al., 2000), making predictions based on structure alone difficult."
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"To address the question of whether HERG channels are also blocked by protriptyline in its inactivated state, a long test pulse to + 80 mV (4 s) from a holding potential of - 90 mV was applied to inactivate the channels, followed by a second voltage step (0 mV, 3.5 s) to open HERG channels (n = 8)."
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"Additionally, at the beginning of the pulse, the fractional sustained current (obtained by normalizing the currents with protriptyline relative to control currents) was 0.87 +/- 0.05 of the control (n = 8), indicating that HERG channels are only slightly blocked by protriptyline while remaining at the holding potential."
| 1
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"Computer simulation of HERG blocking by protriptyline suggested that protriptyline binds the HERG channel at the internal chamber and makes a hydrogen bond to the carbonyl oxygen of Leu622."
Pentamidine affects KCNH2
| 15
Pentamidine inhibits KCNH2.
| 9
| 9
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"Pentamidine and desipramine were reported to suppress hERG forward trafficking to the cell surface, and the aromatic amino F656 mediated the effects of pentamidine [XREF_BIBR, XREF_BIBR]."
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"For example, the antiarrhythmic agents ketoconazole and fluoxetine have been shown to reduce hERG density by at least 50% following 48 hours of treatment, XREF_BIBR - XREF_BIBR whereas pentamidine and probucol reduce cell-surface hERG without affecting ion conduction."
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"Subsequently, the antimicrobial agent pentamidine was also found to impair hERG function by acting as a trafficking inhibitor (Kuryshev et al., 2005; Cordes et al., 2005)."
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"In contrast, pentamidine had no direct effect on the hERG channel current but reduced trafficking of hERG channels."
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"Pentamidine and desipramine were reported to suppress hERG forward trafficking from the endoplasmic reticulum, and the aromatic amino F656 in S6 domain mediated the effects of pentamidine [XREF_BIBR, XREF_BIBR]."
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"Molecular determinants of pentamidine induced hERG trafficking inhibition."
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"The drug pentamidine, at near therapeutic concentrations that do not cause direct KCNH2 channel block, disrupts normal KCNH2 channel protein processing and maturation to reduce its surface membrane expression."
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"As expected, pentamidine (10muM), a reference compound known to inhibit hERG trafficking, significantly inhibited the hERG tail current amplitude by 57%, a value in good agreement with the literature (Kuryshev et al., 2005)."
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"XREF_BIBR Pentamidine impedes hERG trafficking from endoplasmic reticulum (ER) to cell membrane."
Pentamidine decreases the amount of KCNH2.
| 4
Pentamidine decreases the amount of KCNH2. 4 / 4
| 4
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"Taken together, our data imply that chronic administration of pentamidine at clinically relevant exposure reduces the membrane expression of the hERG channel, which may most likely be the major mechanism of QT prolongation and torsade de pointes reported in man."
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"Pentamidine reduces hERG expression to prolong the QT interval."
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"In XREF_FIG, pentamidine markedly reduced hERG expression on the membrane, but application of 1, 10, and 30 muM quinidine (A) or quinine (B) did not increase the 155-kDa hERG level in the presence of 30 muM pentamidine."
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"The present study was designed to provide a more complete picture of how hERG surface expression is disrupted by pentamidine at the cellular and molecular levels."
Pentamidine activates KCNH2.
| 2
| 2
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"Pentamidine induced long QT syndrome and block of hERG trafficking."
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"Dofetilide corrected pentamidine induced hERG, but not K (IR) 2.1 trafficking defects."
| 15
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"Disruption of C-type inactivation also suppressed block of hERG1 by ivabradine."
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"These findings demonstrate that ivabradine induces a concentration dependent inhibition of hERG channels with an IC 50 similar to that reported for native I f and HCN channels."
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"Ivabradine blocks hERG and prolongs action potential duration."
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"A possible lipophilic access route has been established for ivabradine blockade of hERG in a recent study that implicated a lipid facing residue (M651) as critical for drug induced blockade."
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"5 The present study demonstrates unequivocally that ivabradine can inhibit hERG, with an IC 50 of = ~ 2 to 3 mumol/L, concordant with an ability to inhibit native I Kr."
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"The concentration response relation for ivabradine inhibition of hERG 1a/1b I hERG is also included in XREF_FIG B, with a derived IC 50 of 3.31 mumol/L (CI : 2.97 to 3.70); and n H of 1.06 (CI : 0.93 to 1.19)."
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"HERG potassium channel inhibition by ivabradine requires channel gating."
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"HERG potassium channel blockade by the HCN channel inhibitor bradycardic agent ivabradine."
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"XREF_BIBR - XREF_BIBR The voltage dependence and " envelope of tails " data in this study indicate that hERG block by ivabradine requires channel gating to occur, with a comparatively modest impact on inhibition of inactivation attenuation, consistent with preferential open (activated) channel block."
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"The resulting data demonstrate that ivabradine both inhibits hERG with a potency similar to that reported previously for native I f and cloned HCN channels and, furthermore, at therapeutically relevant levels can produce a delay in ventricular repolarization and changes electrical restitution properties in intact perfused hearts."
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"Ivabradine, ajmaline and mexiletine inhibited KCNH2 channel currents significantly, which may underlie their APD prolonging effects."
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"HERG potassium channel inhibition by ivabradine may contribute to QT prolongation and risk of torsades de pointes."
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"Ivabradine Inhibits I hERG."
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"42 The modest effect of the hERG S624A mutation (XREF_FIG) and lack of close proximity of the drug to S624 in docking simulations (XREF_FIG) are consistent with an indirect role for this residue in ivabradine binding to hERG."
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"The mutation Y652A significantly suppressed pharmacologic block of hERG by ivabradine."
| 1 15
| 1 15
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"Erythromycin block of the HERG K+ channel : accessibility to F656 and Y652."
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"The same was true for other hERG channel blockers (like erythromycin, moxifloxacin and sematilide) and multi-ion channel blockers."
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"XREF_BIBR Hyperthermia exaggerates block of HERG by erythromycin in LTC cells as well as APD prolongation by this drug in mouse isolated ventricular myocytes."
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"Pretreatment with erythromycin induced an approximately 14-22-fold reduction in hERG affinity for pore binding drugs at concentrations of erythromycin, which by themselves only block hERG by 10% or less."
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"The results of this study document that both erythromycin and clarithromycin significantly inhibit the HERG potassium current at clinically relevant concentrations."
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"A metabolite of erythromycin, des-methyl erythromycin, was also found to inhibit HERG current with an IC (50) of 147.1 microM."
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"Here we used whole-cell patch-clamp recording at 37 degrees C from heterologously expressed HERG channels in a mammalian cell line to show that erythromycin either produces a rapid open-state-dependent HERG channel inhibition, or components of both open-state-dependent and closed-state-dependent inhibition."
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"Compounds with strong APD prolonging ability include Ca 2+ channel agonists like Bay K8644; class Ia antiarrhythmics (e.g., quinidine); unintended hERG channel blockers like the antibiotic erythromycin; certain class III antiarrhythmics (e.g., E4031); and a large variety of neurotoxins (e.g., anemone toxin)."
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"At a concentration of 100muM, erythromycin causes no significant block of hERG currents at RT but significantly blocks currents at physiological temperature."
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"[Erythromycin inhibits the proliferation of HERG K+ channel highly expressing cancer cells and shows synergy with anticancer drugs]."
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"XREF_BIBR - XREF_BIBR, XREF_BIBR, XREF_BIBR Similar to AZA1 (C 47 H 71 NO 12), the macrolide antibiotic erythromycin (C 37 H 67 NO 13) also blocks hERG1 rapidly in an open-state dependent manner and analysis of mutant channels and molecular modeling indicate that it interacts with phenylalanine reside at position 656 but not with tyrosine reside at position 652."
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"At 300muM, erythromycin blocked hERG currents at 35degreesC by 70% and the IC 50 at this temperature was calculated to be 30.7 muM (n = 18)."
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"At higher concentrations (300muM), erythromycin did block hERG currents at RT by approximately 40% and gave an IC 50 of 427.5 muM calculated from the graph (n = 12)."
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"Erythromycin has been shown to block hERG channels at physiological temperature with an IC 50 of approximately 40muM."
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"It is noteworthy that the hERG blocker erythromycin blocks cell cycle in G2 phase if administered together with vincristine."
KCNH2 affects pyraclofos
| 15
KCNH2 inhibits pyraclofos.
| 7
| 6
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"In the micromolar concentration range NS309 blocks hERG channels (IC 50 = 1.3 muM) and CyPPA blocks voltage gated sodium channels (IC 50 = 11 muM), whereas NS13001 had no effect on these channels at concentrations as high as 10 muM (data not shown)."
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"In SQT1, a gain-of-function mutation in KCNH2 impairs the voltage dependent inactivation of I Kr."
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"Gating current studies suggest that a slow component of hERG gating charge, Q on, underlies S4 voltage sensor movement with a time constant of ~ 50 ms at +10 mV which is slightly faster than channel activation, and a V (1/2) that is about 20 mV hyperpolarized compared to the conductance-voltage (G-V) relationship in both WT and S631A inactivation removed channels XREF_BIBR."
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"Therefore, S631 mutations that disrupted C-type inactivation also facilitated hERG channel activation in the negative voltage range."
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"In experimental systems varying from Drosophila to primary mammalian and human cell lines, celecoxib inhibits many voltage activated Na (+), Ca (2+), and K (+) channels, including NaV1.5, L- and T-type Ca (2+) channels, KV1.5, KV2.1, KV4.3, KV7.1, KV11.1 (hERG), while stimulating other K (+) channels-KV7.2 -5 and, possibly, KV11.1 (hERG) channels under certain conditions."
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"The results of our study can be summarized as follows : 1) acepromazine inhibited the hERG channels in a concentration dependent manner; 2) the drug also blocked hERG channels voltage dependently between -40 mV and +60 mV; 3) acepromazine inhibited the hERG currents by acting on both the inactivated (during the depolarization) and open (during the repolarization) states of the channels; 4) the result of fast drug application study was consistent with the open-channel block mechanism of hERG channel by acepromazine."
KCNH2-N588K inhibits pyraclofos. 1 / 1
| 1
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"Although the N588K HERG mutation does not eliminate entirely voltage dependent rectification of the channel, little if any rectification occurs over the range of physiologically relevant membrane potentials."
KCNH2 activates pyraclofos.
| 5
| 5
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"HERG channel blockers have been shown to inhibit the channels in a voltage dependent manner, suggesting that these drugs bind to the open or inactivated state of HERG channels."
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"Erg1 mediated outward currents displayed voltage dependent activation and C-type inactivation."
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"This indicates that maintenance of the consensus site for PKA phosphorylation in the amino-terminus is not necessary for the TRH induced modifications of HERG activation voltage dependence.The shifts in HERG activation kinetics induced by TRH in oocytes have been shown to be minimised by the protein kinase C (PKC) inhibitor GF109203X [13]."
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"A common structural feature shared by our three inactivating rEag1 mutant constructs is the lack of the rEag1 eag domain, which implies that the rEag1 eag domain, but not the hERG1 eag domain, may somehow modulate an inherent voltage dependent inactivation of rEag1 K + channels."
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"This observation demonstrates that voltage sensor return is less energetically favorable than pore closure upon repolarization and demonstrates the important role for voltage sensor relaxation is stabilizing the hERG activated voltage sensor and limiting its return."
KCNH2 binds pyraclofos.
| 3
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"Those may be explained by state-, time-, and voltage dependent hERG binding and conductance changes (di Veroli etal."
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"For the latter, one has to postulate that hERG1 functionally interact with voltage dependent Ca 2+ entry pathways that exhibit increasing activity and conductivity with increasing depolarization of the membrane potential."
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"For the latter, one has to postulate that hERG1 functionally interact with voltage dependent Ca 2+ entry pathways that exhibit increasing activity and conductivity with increasing depolarization of the membrane potential."
KCNH2 affects dTDP
| 15
KCNH2 inhibits dTDP.
| 8
KCNH2 inhibits dTDP. 8 / 8
| 8
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"The results of the nonclinical and clinical validation studies described in this article will inform how CiPA may result in modification to the ICH guidelines to shift from focusing on hERG block and QT prolongation to informing proarrhythmic risk, as not all hERG blocking and QT prolonging drugs cause TdP."
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"In a survey of the literature, Redfern et al. reported that the margin between the hERG IC 50 value and plasma exposure of the drug might be a valuable parameter for predicting the risk of QT prolongation and TdP induced by a hERG blocker."
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"Not all hERG channel blockers induce TdP because they can also modulate other channels that counteract the hERG channel mediated effect."
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"The robust association between I Kr / hERG blocking propensity and TdP makes it essential that drug candidates are screened for I Kr / hERG blockade."
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"Therefore while almost all drugs that cause TdP block hERG, the converse is not true."
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"The current paradigm of cardiac safety screening for, primarily, hERG activity to eliminate TdP causing drugs from reaching the market has reduced incidence of adverse drug induced TdP."
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"Further, even though all drug induced torsadogenic compounds have a low IC 50 (strong blockers of hERG), not all hERG blockers with strong potencies lead to TdP."
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"Suppression of hERG and Kv11.1 (I Kr) can prolong the APD and cause drug induced LQT syndrome and fatal ventricular tachyarrhythmia or TdP and consequently sudden cardiac death."
KCNH2 activates dTDP.
| 7
KCNH2 activates dTDP. 6 / 6
| 6
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"XREF_BIBR Loss-of-function mutations in hERG cause a reduction in the I Kr current of up to 97%, XREF_BIBR which causes QT prolongation, and usually increases risk of TdP."
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"To date, in patients with LQT2, the majority of mutations in hERG increase the transmural dispersion of repolarization and eventually induce prolongation of the QT interval, a notched T wave, re-entry and TdP."
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"In the second step, the role of non hERG channels to modulate TdP risk are considered by constructing classifiers based on direct or derived features at critical hERG block concentrations that generates EADs in the computational cardiac cell models."
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"However, not all drugs that block hERG cause TdP."
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"Despite being of such importance for drug discovery, the relevance and impact of hERG data are sometimes misinterpreted, as there are drugs that block the hERG coded ion channel but do not cause TdP, and drugs that cause TdP but do not block the hERG channel."
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"Sparfloxacin is a fluoroquinone antibiotic and HERG channel antagonist that is known to cause QT prolongation, Tdp and ventricular fibrillation [XREF_BIBR, XREF_BIBR]."
KCNH2-T473P activates dTDP. 1 / 1
| 1
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"Genetic mutations in KCNH2 (T473P) and KCNE1 (G38S) increase susceptibility to hypokalemia induced TdP by reducing repolarization reserve and QT interval prolongation, demonstrating a drug independent, genetic predisposition to hypokalemia related TdP risk."
KCNH2 affects cell growth
| 2 15
KCNH2 activates cell growth.
| 2 12
| 2 12
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"This suggests that ER-G1 stimulates cancer cell proliferation by enabling tumor expansion rather than directly stimulating cell growth and division.Based on tumor morphology, we hypothesized that ER-G1 stimulates tumor growth by facilitating tissue remodeling and invasion."
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"In the same experiment, i.e., using the same controls, cell growth was reduced to a similar degree as with siHERG1 by inhibition of HERG channel protein expression with the short hairpin RNA against ERG1 (shRNA-U6)."
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"Silencing of herg gene by shRNA inhibits SH-SY5Y cell growth in vitro and in vivo."
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"Moreover, the blocking of HERG channels dramatically impairs cell growth of HERG bearing tumor cells."
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"When the oxygen supply was restored, the HERG1B and HERG1ratio could be increased by a remodeling of HERG channels on the plasma membrane, thus leading to depolarize V m and sustain cell growth (Crociani et al., 2003)."
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"Indeed in the present paper we provide evidence that hERG1 blockers could inhibit PDAC cell growth and migration in vitro."
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"In addition, functional studies in head and neck squamous cell carcinoma derived cell lines further revealed that HERG1 expression promotes anchorage dependent and -independent cell growth and invasive capability, although independently of its ion conducting function."
reach
"(i) hERG1 was expressed at high levels in 59% of primary PDAC; (ii) hERG1 blockade decreased PDAC cell growth and migration; (iii) hERG1 was physically and functionally linked to the Epidermal Growth Factor-Receptor pathway; (iv) in transgenic mice, ERG1 was expressed in PanIN lesions, reaching high expression levels in PDAC; (v) PDAC patients whose primary tumour showed high hERG1 expression had a worse prognosis; (vi) the alpha-hERG1-MoAb could detect PDAC in vivo."
reach
"HERG1 silencing, as well as miR-96 over-expression inhibits the PDAC cell growth and invasiveness in vitro, and reduces tumorigenicity in vivo."
reach
"Yet, a significant number of Tn positive cells were detected in these livers, indicating that the expression of ER-G1, in the absence of NRas, is not toxic but does not induce cell growth or proliferation."
reach
"Indeed, hERG1 blockage impairs tumor cell growth both in vitro and in vivo in preclinical mouse model."
reach
"Moreover, knockdown of hERG inhibits cell growth and induces apoptosis in ATC cells in vitro."
KCNH2 inhibits cell growth.
| 3
| 3
reach
"Interestingly, hERG, another partner of KCNE2, is expressed in gastric cancer cells but not normal gastric epithelia, and the hERG channel blocker cisapride was previously found to suppress gastric cancer cell growth by inhibiting entry into S phase from G (1) phase in the cell cycle, increasing apoptosis XREF_BIBR."
reach
"The study indicated that siRNA was successfully transferred to the target cells and knocked down hERG that inhibited cell growth and induced apoptosis in ATC cells in vitro."
reach
"To further evaluate whether silencing herg gene in SH-SY5Y cells may inhibit cell growth and proliferation, the growth curves of cells nontransfected and transfected with shRNA-herg1, shRNA-herg1/1b or shRNA-control were determined and MTT assay and colony formation assay were performed."
KCNH2 affects SIGMAR1
| 9 6
| 9 6
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"Homogeneous time resolved fluorescence (HTRF (R)) allowed the detection of the interaction between the sigma-1 receptor and hERG within the plane of the plasma membrane."
reach
"Our aim was to investigate the nature of the interaction between the sigma-1 receptor and hERG."
sparser
"Atomic force microscopy imaging of the isolated protein confirmed the direct binding of the sigma-1 receptor to hERG monomers, dimers, and tetramers."
sparser
"The findings of the Sig-1R interacting with hERG in the ER and potentiating hERG maturation and translocation to the plasma membrane suggest that the Sig-1R may exert chaperoning activities in the ER to facilitate proper protein sorting to their final destinations."
sparser
"Inasmuch Sig1R co-immunoprecipitates with both immature and mature forms of the channel α-subunits, it is suggested that Sig1R not only associates with hERG in the ER, but also drives it to the plasma membrane (Crottes et al., xref )."
reach
"The authors clarify that the direct interaction between the Sig-1R and hERG in the plasma membrane is not Sig-1R ligand dependent but is reduced by cholesterol depletion, suggesting that Sig-1R may bind to hERG in the ER and facilitate hERG assembly and trafficking perhaps in a lipid-raft related fashion [XREF_BIBR]."
sparser
"Our aim was to investigate the nature of the interaction between the sigma-1 receptor and hERG."
sparser
"We suggest that the sigma-1 receptor may bind to hERG in the endoplasmic reticulum, aiding its assembly and trafficking to the plasma membrane."
reach
"The distribution of angles between pairs of sigma-1 receptors bound to hERG tetramers had two peaks, at ~ 90 and ~ 180degrees in a ratio of ~ 2:1, indicating that the sigma-1 receptor interacts with hERG with 4-fold symmetry."
reach
"We suggest that the sigma-1 receptor may bind to hERG in the endoplasmic reticulum, aiding its assembly and trafficking to the plasma membrane."
sparser
"Homogeneous time-resolved fluorescence (HTRF®) allowed the detection of the interaction between the sigma-1 receptor and hERG within the plane of the plasma membrane."
reach
"Atomic force imaging and homogenous time resolved fluorescence approaches later identified that the Sig-1R interacts with hERG with a four-fold symmetry."
sparser
"The authors clarify that the direct interaction between the Sig-1R and hERG in the plasma membrane is not Sig-1R ligand-dependent but is reduced by cholesterol depletion, suggesting that Sig-1R may bind to hERG in the ER and facilitate hERG assembly and trafficking perhaps in a lipid-raft related fashion [ xref ]."
sparser
"Atomic force imaging and homogenous time-resolved fluorescence approaches later identified that the Sig-1R interacts with hERG with a four-fold symmetry."
sparser
"The distribution of angles between pairs of sigma-1 receptors bound to hERG tetramers had two peaks, at ∼90 and ∼180° in a ratio of ∼2:1, indicating that the sigma-1 receptor interacts with hERG with 4-fold symmetry."
CANX affects KCNH2
2 | 1 6 7
CANX binds KCNH2.
2 | 1 6 2
2 | 1 3 2
biogrid
No evidence text available
biogrid
No evidence text available
reach
"To assess the physical interaction between hERG and Calnexin and Calreticulin, immunoprecipitation was done with anti-Calnexin or anti-Calreticulin antibody, followed by Western blot analysis with anti-hERG antibody."
sparser
"Importantly, Calnexin interacted with hERG proteins in the ER in HEK293T cells."
reach
"The calnexin and hERG interaction was preserved in reciprocal pulldown immunoaffinity assays."
sparser
"Coimmunoprecipitation assays showed that Calnexin only interacted with the ER-residing form of hERG proteins ( xref ), suggesting that Calnexin interacts with hERG proteins in the ER."
sparser
"The calnexin and hERG interaction was preserved in reciprocal pulldown immunoaffinity assays."
CALR binds CANX and KCNH2. 1 / 1
| 1
sparser
"As shown in xref , treatment with lactacystin or ALLN but not leupeptin (a lysosome inhibitor) results in an increase in the levels of core-glycosylated, immature form of hERG, Calnexin and Calreticulin."
sparser
"Coimmunoprecipitation assays showed that Calnexin only interacted with the ER-residing form of hERG proteins ( xref ), suggesting that Calnexin interacts with hERG proteins in the ER."
| 1
sparser
"Furthermore, the interaction between mutant hERG proteins and chaperone proteins, Calnexin and Calreticulin, play crucial roles in these processes."
CANX inhibits KCNH2.
| 2
CANX inhibits KCNH2. 2 / 2
| 2
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"Down-regulation of its human homologue, Calnexin, significantly decreased the protein level and current density of the hERG K + channel in human SH-SY5Y cells."
reach
"In HEK293T cells expressing hERG proteins, down-regulation of calnexin by siRNA markedly decreased the protein level (XREF_FIG) and current density (XREF_FIG) of hERG K + channels."
CANX activates KCNH2.
| 2
CANX activates KCNH2. 2 / 2
| 2
reach
"Importantly, they found that knockdown of calnexin expression reduced hERG current when recorded in vitro."
reach
"Deletion of calnexin reduced the expression and current densities of endogenous hERG K + channels in SH-SY5Y cells."
CANX increases the amount of KCNH2.
| 1
CANX increases the amount of KCNH2. 1 / 1
| 1
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"In human neuroblastoma SH-SY5Y cells that endogenously express hERG K + channels, deletion of calnexin by CRISPR-Cas9-mediated genome editing significantly decreased the endogenous hERG protein level (XREF_FIG)."
| 2 1 13
3',5'-cyclic AMP activates KCNH2.
| 1 1 8
| 1 1 8
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"Activation of cAMP and PKA increased the abundance of HERG signal in both groups to a comparable degree as in cells transfected with HERG alone with no statistically significant difference."
reach
"It is known that the hERG K + channel can be modulated by cAMP and PKA."
reach
"3.6 Transcriptional inhibition abrogates the cAMP mediated HERG enhancement."
sparser
"Cyclic AMP may also activate HERG, thereby increasing net out- ward current and accelerating the rate of myocellular repo- larization."
reach
"Elevation of cAMP can modulate HERG K+ channels both by direct binding and indirect regulation through protein kinase A. To assess the physiological significance of cAMP binding to HERG, we introduced mutations to disrupt the cyclic nucleotide binding domain."
reach
"Although our results were most consistent with cAMP and PKA enhancement of HERG abundance from accelerated synthesis awe sought to carefully examine possible contribution of channel degradation changes."
reach
"Cyclic AMP may also activate HERG, thereby increasing net out- ward current and accelerating the rate of myocellular repo- larization."
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"3.8 MiRP (KCNE) proteins in the cAMP and PKA augmentation of HERG."
reach
"That the polysome profile shapes are not significantly changed upon kinase stimulation is consistent with our previous observation that cAMP dependent increase of HERG protein was specific and did not alter other proteins we assayed [XREF_BIBR],."
| 3
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"Elevation of the intracellular cAMP concentration by incubation with the adenylate cyclase activator, forskolin (10 micromol/L), and the broad range phosphodiesterase inhibitor, IBMX (100 micromol/L), caused a HERG tail current reduction of 83.2%."
reach
"HERG current may be decreased by cAMP dependent activation of PKA; however, a putative direct binding of cAMP to the channel causes opposite effects."
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"CAMP therefore decreases effective HERG activity through current inhibition and accelerated deactivation kinetics with minimal alteration of voltage dependent activation.To assess whether cAMP was acting on HERG through PKA, the specific peptide inhibitor PKI was included in the patch pipette and cells were studied after pre-incubation with membrane-permeable myristolated PKI."
3',5'-cyclic AMP phosphorylates KCNH2.
| 1
3',5'-cyclic AMP leads to the phosphorylation of KCNH2. 1 / 1
| 1
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"Activation of cAMP dependent protein kinase (PKA) causes phosphorylation of HERG accompanied by a rapid reduction in current amplitude, acceleration of voltage dependent deactivation, and depolarizing shift in voltage dependent activation."
| 1 1
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"Elevation of cAMP can modulate HERG K+ channels both by direct binding and indirect regulation through protein kinase A. To assess the physiological significance of cAMP binding to HERG, we introduced mutations to disrupt the cyclic nucleotide binding domain."
| 1 12
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"PIP (2) increased the hERG maximal current and concomitantly slowed deactivation."
reach
"Erg1 is not modulated by PIP 2 in a bimodal fashion and like all Erg and Eag subfamily channels intriguingly lacks a basic residue at the equivalent position of R479 (XREF_FIG)."
reach
"In this study, the giant-patch experiments on COS cells confirmed the activating effect of PIP 2 on hERG and showed that PIP 2 could strongly increase hERG current, notably by increasing its maximal amplitude by up to three times."
reach
"PIP 2 modulates hERG by increasing its maximal current, concomitantly slowing deactivation, and changing activation and inactivation gating; at low PIP 2 levels, a marginal hERG current persists [XREF_BIBR]."
reach
"The application of exogenous PIP 2 enhances hErg1 activation, and depletion of native PIP 2 causes a small reduction in hErg1 currents."
reach
"PIP 2 does appear to enhance hErg1 through open-state stabilization, but currently only the distal C terminus of hErg1 has been linked to PIP 2 -depenent modulation."
reach
"In this configuration, hERG and KCNQ1 biophysical changes induced by PIP 2 insertion are quite similar (slowed deactivation with no effect on activation)."
reach
"To confirm the PIP 2 modulation of hERG, we added 5 mu mol/L PIP 2 when the biophysical parameters were stable."
reach
"The application of exogenous PIP 2 enhances hErg1 activation, and depletion of native PIP 2 causes a small reduction in hErg1 currents."
reach
"Based on these results, we confirmed that acute depletion of PIP 2 inhibits HERG K + current."
reach
"Inclusion of PIP 2 in the whole-cell pipette solution also prevented cholesterol effect (XREF_FIG), which may suggest that the acute depletion of PIP 2 suffices to suppress PIP 2 -sensitive HERG channels."
reach
"Interestingly, the proposed site of PIP 2 interaction with hErg1 is a cluster of positive charges in the C terminus downstream of the CNBHD in an area that is poorly conserved even within the Erg channel subfamily, and thus it is not clear how PIP 2 might regulate other EAG family channels."
sparser
"Interestingly, the proposed site of PIP 2 interaction with hErg1 is a cluster of positive charges in the C terminus downstream of the CNBHD ( xref ) in an area that is poorly conserved even within the Erg channel subfamily, and thus it is not clear how PIP 2 might regulate other EAG family channels."
Haloperidol affects KCNH2
| 13
Haloperidol inhibits KCNH2.
| 10
| 8
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"This analysis shows that enhancements of endogenous HF oscillations in HR were also found in beagle dogs with dofetilide and with other hERG blockers such as cisapride, haloperidol, risperidone, DL sotalol, terfenadine and thioridazine."
reach
"Haloperidol, pimozide, and fluspirilene inhibited HERG current with IC (50) of 1.36, 1.74, and 2.34 microM, and maximal block of 73%, 76% and 65%, respectively."
reach
"In contrast, haloperidol blocked HERG channels potently with an IC50 value of approximately 1 microM."
reach
"For comparison, haloperidol (30 nM) and olanzapine (300 nM) reduced hERG current amplitude by 44.2 +/-3.9% and 49.7 +/-4.2%, respectively."
reach
"The inactivation attenuated mutant S631A reduces hERG drug block by haloperidol."
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"However, with up to 5 muM testosterone and up to 12 hr of incubation, enough oocytes with acceptable membrane properties (input resistance of no less than 2 x 10 5 Omega at -80 mV) were available.Application of any of the three antipsychotic drugs, haloperidol, pimozide, or fluspirilene, to the control HERG expressing oocytes non treated with the hormone produced a dose dependent inhibition of HERG current with effective concentration ranges between 0.1 muM and 30 muM for all of them."
reach
"One of these agents, haloperidol, has already been shown to produce a high affinity blockade of HERG K + channels [22] but the effects of the two others still remain poorly investigated."
reach
"The mechanism of HERG blockade by haloperidol may also involve interaction with the channel in inactivated state [22]."
Haloperidol inhibits KCNH2-S631A. 2 / 2
| 2
reach
"It was previously shown that haloperidol block of HERG S631A, a channel mutant with greatly reduced C-type inactivation, was 4-fold weaker than for wild-type (WT) HERG channels [4]."
reach
"Haloperidol block of HERG S631A at 0 mV was four fold weaker than for HERG wild-type channels."
Haloperidol decreases the amount of KCNH2.
| 1
Haloperidol decreases the amount of KCNH2. 1 / 1
| 1
reach
"An analysis of haloperidol block of hERG overexpressed in oocytes indicates that block is strongly attenuated in both Y652A hERG and F656A hERG, supporting the expectation that valid docking poses should show significant interaction with these residues."
| 1
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"Haloperidol binds hERG channels more potently than other cardiac potassium channels, whereas terfenadine also has the potential to block other ion channels XREF_BIBR."
Haloperidol activates KCNH2.
| 1
| 1
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"As haloperidol increased the degree and rate of HERG inactivation, binding to inactivated HERG channels is suggested."
| 13
| 7
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"Consistent with these findings, in this study, we reported that As2O3 inhibited hERG channel at both protein and mRNA levels and damaged hERG current but did not affect channel kinetics."
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"Arsenic trioxide (As (2) O (3)), which is used to treat acute promyelocytic leukemia, can cause LQTS type 2 (LQT2) by reducing the hERG current through the diversion of hERG trafficking to the cytoplasmic membrane."
reach
"Arsenic trioxide inhibits the trafficking of hERG channels from the endoplasmic reticulum to the cell membrane [XREF_BIBR]."
reach
"In addition, knock-down of miR-21 by its specific antisense molecules AMO-21 was able to rescue Sp1 and hERG inhibition caused by As2O3."
reach
"In our study, we found a new pathway underlying As2O3 induced cardiotoxicity that As2O3 accelerates lysosomal degradation of hERG on plasma membrane after using brefeldin A (BFA) to block protein trafficking."
reach
"This finding revealed that regulation of the NF-kappaB-miR-21-Sp1 signalling pathway is a novel mechanism for As2O3 induced hERG inhibition."
reach
"And the hERG channel inhibition induced by As2O3 was rescued after being transfected with AMO-23a, which may be a molecular mechanism for the role of As2O3 in hERG trafficking deficiency."
| 4
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"Arsenic trioxide induced hERG K (+) channel deficiency can be rescued by matrine and oxymatrine through up-regulating transcription factor Sp1 expression."
reach
"This discovery may provide a novel mechanism of As2O3 induced hERG channel deficiency, and these miRNAs may serve as potential therapeutic targets for the handling of As2O3 cardiotoxicity."
reach
"The rescuable function and mechanism of resveratrol on As2O3 induced hERG K+ channel deficiency."
reach
"In brief, our study revealed that miR-21 and miR-23a are involved in As2O3 induced hERG deficiency at transcriptional and transportational levels."
Diarsenic trioxide decreases the amount of KCNH2.
| 2
Diarsenic trioxide decreases the amount of KCNH2. 2 / 2
| 2
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"Further investigation using western blot analysis and reverse transcription-quantitative polymerase chain reaction revealed that As2O3 downregulated hERG expression via upregulation of miR-328 expression in MCF-7 cells."
reach
"The combination of As2O3 with resveratrol, on the one hand reduced the expression of hERG channels on the membrane, and on the other hand weaken the binding between hERG and integrin beta 1, which may be the main cause of downstream signaling pathways alterations, including the activation of the apoptotic pathway."
STUB1 affects KCNH2
2 | 1 10
STUB1 activates KCNH2.
| 5
STUB1 activates KCNH2-G601S. 1 / 1
| 1
reach
"CHIP ablation increased the abundance of mature G601S and F805C hERG in post-ER and PM compartments (XREF_FIG and Supplemental Figure S5B)."
STUB1 activates KCNH2-F805C. 1 / 1
| 1
reach
"CHIP ablation increased the abundance of mature G601S and F805C hERG in post-ER and PM compartments (XREF_FIG and Supplemental Figure S5B)."
STUB1 bound to HSPA activates KCNH2. 1 / 1
| 1
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"This conclusion is supported by the observation that disruption of Hsp70 and Hsp90 binding to CHIP prevented CHIP mediated down-regulation of hERG from the PM."
STUB1 bound to HSP90 activates KCNH2. 1 / 1
| 1
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"This conclusion is supported by the observation that disruption of Hsp70 and Hsp90 binding to CHIP prevented CHIP mediated down-regulation of hERG from the PM."
STUB1 activates mutated KCNH2. 1 / 1
| 1
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"CHIP targets CFTR channel for ubiquitination and subsequent proteasomal degradation [19], and also promotes wild-type and mutant hERG degradation [7,9]."
STUB1 ubiquitinates KCNH2.
| 1 2
STUB1 ubiquitinates KCNH2. 3 / 3
| 1 2
reach
"The CHIP ablation effect could be attributed to CHIP dependent ubiquitination of hERG, since siCHIP reduced ouabain induced polyubiquitination of wt-hERG (XREF_FIG, lanes 3 and 6, and Supplemental Figure S5D)."
sparser
"The CHIP ablation effect could be attributed to CHIP-dependent ubiquitination of hERG, since siCHIP reduced ouabain-induced polyubiquitination of wt-hERG ( xref , lanes 3 and 6, and Supplemental Figure S5D)."
reach
"The documented CHIP dependent polyubiquitination of hERG, regardless of whether structural destabilization was attained by missense mutations or extracellular and intracellular K + depletion, suggests that the conformational defect recognized by the QC converges onto to the cytosolic domains."
STUB1 binds KCNH2.
2 | 1
2 | 1
biogrid
No evidence text available
biogrid
No evidence text available
reach
"CHIP recruitment to nonnative hERG is probably mediated via Hsc/Hsp70/Hsp90 binding to exposed hydrophobic residues that are otherwise buried in the native channel, similar to that described for other misfolded ER, cytosolic, and PM polypeptides."
STUB1 inhibits KCNH2.
| 2
STUB1 inhibits KCNH2. 2 / 2
| 2
reach
"CHIP overexpression decreased the immature form of HERG (1122fs/147) proteins."
reach
"This conclusion is supported by the observation that disruption of Hsp70 and Hsp90 binding to CHIP prevented CHIP mediated down-regulation of hERG from the PM."
KCNH2 affects ion channel
| 7 6
| 7 3
sparser
"For this reason it was desired to lower interactions with the hERG and other ion channels."
sparser
"The authors hypothesize that the inhibitory mechanism might be mediated via an interaction between Na,K,ATPase and other ion channels like the voltage-gated K+ channel hERG, whose expression is induced by CMV infection and downregulated by cardiac glycoside treatment [15]."
sparser
"The oxacyclic group effect of compound 33 against hERG ion channel binding might be associated with σ-electron withdrawing effect of the ether oxygen atom for reducing electron density of the adjacent aryl moiety, lower lipophilic effect that is similar to the above examples, and/or electron lone-pair effect of the oxygen atom, compared to the carbocyclic moiety of compound 38 ."
reach
"As supporting data in the previous study in vitro in terms of the electron effects, MCOPPB that has NH -piperidine (electron-poor ring) as 2-substituent on its benzimidazole moiety showed little hERG ion channel binding affinity, contrary to the corresponding 2-aryl group (electron rich ring) analogs that showed higher binding affinities [5]."
sparser
"The human ether-a-go-go-related gene (HERG) protein forms the ion channel responsible for the rapidly acting delayed rectifier potassium current, I(Kr), and its blockade is a significant contributor to prolongation of the QT interval."
sparser
"The hERG ion channel is formed by the KCNH2 protein that consists of six transmembrane alpha helices, a pore helix and cytoplasmically located N- and C-termini."
sparser
"In this issue Yarema and co-workers use a dual in silico/experimental approach to address this challenge, systematically defining the impact of variables such as acyl chain length and ester regiochemistry on important pharmacological parameters including solubility and hERG ion channel binding."
reach
"The oxacyclic group effect of compound 33 against hERG ion channel binding might be associated with sigma-electron withdrawing effect of the ether oxygen atom for reducing electron density of the adjacent aryl moiety, lower lipophilic effect that is similar to the above examples, and/or electron lone-pair effect of the oxygen atom, compared to the carbocyclic moiety of compound 38."
reach
"In the design and SAR studies of the analogs against hERG ion channel binding affinity in vitro, several effective structures and significant and/or useful contributing-factors for reducing affinities were found or suggested."
sparser
"The KCNH2 and KCNQ1 mutations are associated with different ion channel dysfunctions, xref , xref and gene specific triggers of arrhythmias. xref In LQT-1, it is recognized that exercise (catecholamine) is the primary trigger because of the malfunctioning I Ks channels that leads to less effective shortening of the QT intervals during tachycardia than in normal individuals."
KCNH2 activates ion channel.
| 2
| 2
reach
"Fluoxetine is a compound with hERG channel blocking effects 28 as well as other off target ion channel block, including : Nav1.5 29, and voltage gated calcium channels 30."
reach
"Mutations in the KCNH2 gene were reported to cause type 2 long QT syndrome (LQT2), a rare inherited ion channel disorder characterized by prolonged QT interval and predisposing patients to ventricular arrhythmias that can lead to syncope and sudden cardiac death (SCD)."
KCNH2 inhibits ion channel.
| 1
| 1
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"To date, these formats have largely been used by pharmaceutical companies to screen for human ether-a-gogo-related gene (hERG) induced cardiac ion channel blockade."
Doxazosin affects KCNH2
| 2 12
Doxazosin inhibits KCNH2.
| 1 9
| 1 9
reach
"29 In addition, hERG blockers doxazosin and terazosin did not cause cell cycle arrest despite hERG expression in distinct cell lines, for example, LNCaP prostate carcinoma cells."
reach
"Finally, antagonism of doxazosin induced hERG protein suppression and glioblastoma cell death by co-treatment of terazosin and doxazosin indicates the functional relevance of hERG protein in GB cell apoptosis."
reach
"The antihypertensive agent, doxazosin pharmacologically blocks the hERG channel [XREF_BIBR]."
reach
"An unexpected finding was revealed : simultaneous application of 100 microM terazosin attenuated doxazosin induced hERG suppression to 24.5 +/-11.4% (n = 3; p = 0.07; XREF_FIG)."
reach
"In conclusion, this study demonstrates that HERG potassium channels are blocked by prazosin, doxazosin, and terazosin."
reach
"Furthermore, additional reduction of hERG viability in the presence of anti-HERG siRNA may be caused by doxazosin induced suppression of residual hERG protein (~ 42%)."
reach
"XREF_BIBR reported that doxazosin can directly block KCNH2, and the sensitivity is influenced by the mutation of KCNH2 (1956, C> T), while other research found that celiprolol involved in modulating the function of endothelial cells and had certain antioxidant stress effects XREF_BIBR, XREF_BIBR."
reach
"Given that GB cells express hERG channels and that hERG suppression by doxazosin induces apoptosis, we hypothesized that pharmacological targeting of hERG channels would induce apoptosis of GB cells."
reach
"The hERG blocker doxazosin has been proven as a proapoptotic agent in a wide range of in vitro and in vivo studies."
Doxazosin decreases the amount of KCNH2.
| 2
Doxazosin decreases the amount of KCNH2. 2 / 2
| 2
reach
"The data imply that doxazosin related reduction of hERG protein expression may be linked to increased apoptosis rates."
reach
"Consistent with this notion, terazosin (100 microM; 24 h) exhibited weak effects on hERG protein levels in LNT-229 cells (-20.4 +/-2.8%; n = 3; p = 0.03), while doxazosin (30 microM; 24 h) suppressed hERG expression by 48.2 +/-1.7% (n = 3; p = 0.002; XREF_FIG)."
Doxazosin activates KCNH2.
| 1 1
| 1 1
reach
"Furthermore, it was recently shown that HERG K + channel blockage induced by doxazosin directly results in HEK cell apoptosis."
VCL affects KCNH2
| 12
VCL activates KCNH2.
| 9
VCL activates KCNH2. 9 / 9
| 9
reach
"Taken together, protriptyline inhibits HERG channels predominantly in the open and inactivated state rather than in the closed state.To examine the use-dependence of the protriptyline effect, HERG channels were activated by 0.3 s depolarizing steps up to + 20 mV from a holding potential of - 90 mV followed by a repolarizing step to - 40 mV (300 ms) to elicit outward tail currents."
reach
"Briefly, a three pulse protocol was used as follows : The pulse comprises a holding potential of -80 mV and a 2-sec pulse to +60 mV to activate and inactivate the hERG channels, followed by a hyperpolarized pulse to -100 mV for 10 msec to recover from inactivation."
reach
"The hERG currents were elicited by a 3-second depolarizing step in 10 mV increments from -60 mV to 40 mV, from a holding potential of -80 mV, followed by a 3-second step to -50 mV record tail current."
reach
"To assess the inactivation time course of hERG currents, cells were depolarized from a holding potential of aeuro " 80 mV to +60 mV for 2 s, hyperpolarized to aeuro " 100 mV for 10 ms to allow the hERG channel to recover from inactivation, and then depolarized to test voltages between aeuro " 60 mV and +60 mV in 10 mV decrements to record inactivating cur- rents."
reach
"The hERG channels were then activated by applying a depolarising step to + 40 mV for 5 s and then clamped at - 50 mV for 4 s to elicit the hERG tail current, before returning to - 80 mV for 0.3 s. Test compounds were then added automatically to the upper wells of the PatchPlateTM from a 96-well microtitre plate containing a range of concentrations of each compound."
reach
"To compare the rate of recovery from inactivation between the two channels, we used a protocol used in prior I hERG studies : a 500-ms depolarisation to +40 mV was applied from a holding potential of -80 mV to activate and inactivate I hERG."
reach
"We then used a conventional voltage step protocol, comprised of a 2-second depolarization to +20 mV followed by repolarization to -40 mV to elicit I hERG tails."
reach
"HERG currents were activated by a 4.8-s depolarizing pulse to + 20 mV from a holding potential of - 80 mV, and the tail current was recorded at - 60 mV."
reach
"After an initial depolarising command to +40 mV to activate and inactivate I hERG, brief (2 ms) repolarising commands to a range of membrane potentials (in 10 mV increments down to -140 mV) were used to alleviate I hERG inactivation to differing extents and then the amplitude of the rapid I hERG transient during the third step (to +40 mV) was measured."
VCL inhibits KCNH2.
| 3
VCL inhibits KCNH2. 3 / 3
| 3
reach
"Residue S631 is located towards the outer mouth of the HERG channel pore, and the S631A (serine --> alanine) mutation has been reported to shift I HERG inactivation by ~ +100 mV XREF_BIBR."
reach
"The hERG channels were inactivated by a holding potential of 60 mV."
reach
"A fast application of norquetiapine inhibited the hERG current elicited by a 5s depolarizing pulse to +60 mV, which fully inactivated the hERG currents, suggesting an inactivated-state block."
RPS6 affects KCNH2
| 5 7
RPS6 activates KCNH2.
| 1 6
RPS6 activates KCNH2. 5 / 5
| 1 4
sparser
"One S6 T peptide activates hERG channels."
reach
"In contrast to HCN channel inactivation, however, HERG inactivation is not mediated by a loose coupling of S4-S5 linker and S6 T but by conformational changes at the outer pore region."
reach
"The S6 residue HERG mutant Y652A and F656C largely reduced the blocking potency of HERG current."
reach
"One S6 T peptide activates hERG channels."
reach
"The apparently large size of the central cavity below the selectivity filter, and the positioning of the aromatic side chains of Y652 and F656 on S6 allow hERG to accommodate diverse drugs XREF_BIBR, XREF_BIBR."
RPS6-F656A activates KCNH2. 1 / 1
| 1
reach
"The S6 mutations Y652A and F656A partially attenuated (Y652A) or abolished (F656A) HERG current blockade, indicating that prazosin binds to a common drug receptor within the pore-S6 region."
RPS6-Y652A activates KCNH2. 1 / 1
| 1
reach
"The S6 mutations Y652A and F656A partially attenuated (Y652A) or abolished (F656A) HERG current blockade, indicating that prazosin binds to a common drug receptor within the pore-S6 region."
RPS6 binds KCNH2.
| 4
| 3
sparser
"Thus, it seems reasonable to propose that lidocaine is also likely to interact with S6 aromatic residues of hERG and our docking data ( xref and S5) support such a conclusion."
sparser
"Altogether, these observations confirmed that the paradoxical activation effect initially observed when S4-S5 L (0) peptide was co-transfected with WT hERG channel was not due to an interaction of this peptide with the S6 T region of hERG."
sparser
"The direct block was mediated by drug binding to S6 domain of the hERG subunit, while trafficking deficiency was mediated by binding to a different site or a related protein. xref In this study, we used site-directed mutagenesis to test whether Y652A or F656V mutation alter the BBR sensitivity of hERG after long-term treatment."
RPS6 binds KCNH2 and cooH. 1 / 1
| 1
sparser
"Furthermore, other channel segments might be involved in gating since several studies have provided evidence for interactions between the S4–S5 linker and residues in the COOH-terminal part of S6 in HERG, HCN, and Shaker ( xref ; xref ; xref ; xref )."
RPS6 decreases the amount of KCNH2.
| 1
RPS6 decreases the amount of KCNH2. 1 / 1
| 1
reach
"The inhibition of GSK and S6 (RPS6KB1) kinases results in a small increase in PMA induced Erg1 expression only during the early time points."
NS1643 affects KCNH2
| 12
NS1643 activates KCNH2.
| 8
NS1643 activates KCNH2. 8 / 8
| 8
reach
"When assessed with 2-s depolarizations, NS1643 enhanced the magnitude of wild-type hERG current in a concentration- and voltage dependent manner with an EC (50) of 10.4 microM at -10 mV."
reach
"Nevertheless, NS1643 then continued to produce concentration- and voltage dependent increases in hERG current amplitude."
reach
"Casis et al. (11) reported that NS1643 activates hERG channels expressed in Xenopus oocytes in a concentration- and voltage dependent manner and strongly affects channel inactivation by shifting the voltage inactivation curve by +35 mV at 30 mu M."
reach
"HERG channels treated with NS1643 behave in a very similar way to WT channels in the absence of NS1643 : following depolarization, NS1643 activated HERG channels inactivate rapidly and recover from inactivation, passing an outward current as the membrane potential recovers."
reach
"NS1643, which activated hERG current by 55% at 3muM in hERG transfected HEK293 cells, significantly shortened APD and increased coronary flow at 1 and 10muM."
reach
"In this study, we showed that both mallotoxin and NS1643 activated hERG current by 87% and 55% at 3muM, respectively."
reach
"In the absence of channel inactivation, NS1643 did not enhance hERG current magnitude."
reach
"As expected, mallotoxin activated hERG current by 87% at 3muM, and NS1643 activated hERG current by 55% at 3muM."
NS1643 inhibits KCNH2.
| 3
NS1643 inhibits KCNH2. 3 / 3
| 3
reach
"12 Surprisingly, results from the present study demonstrate that prolonged stimulation of hERG1 channel in the ER negative breast cancer SKBr3 cells treated with NS1643 arrested the cells in the G0/G1 phase."
reach
"Binding of NS1643 to the central cavity site appears to mediate pharmacologic block of hERG1 XREF_BIBR."
reach
"NS1643 reduces the rectification of hERG through fast channel inactivation, thus slowing the onset of hERG inactivation."
NS1643 binds KCNH2.
| 1
KCNH2 binds NS1643. 1 / 1
| 1
reach
"There are limited data available about the NS1643 binding to hERG (2,31)."
MINK1 affects KCNH2
2 | 10
MINK1 binds KCNH2.
1 | 5
1 | 5
reach
"It is already known, for example, that minK can interact with KVLQT1 and HERG when overexpressed in heterologeous systems (McDonald et al., 1997)."
reach
"A minK and HERG complex regulates the cardiac potassium current I (Kr)."
reach
"Alanine at codon 8 is next to threonine at 7 7 and caused a significant modulation on the MinK and HERG complex."
reach
"10 Thus, minK interacts with both KCNQ1 and HERG, and KCNE1-3 proteins interact with Kv3.1 and Kv3.2 causing diversification of channel gating."
reach
"Thus, minK and MiRP1 interaction with HERG are not mediators of regulators of the kinase dependent enhancement of channel synthesis."
signor
"Herg, a human homologue of the ether-a-go-go gene of the fruitfly drosophila melanogaster, encodes aproteinthat produces the rapidly activating cardiac delayed rectifier (i[kr]). / our results show that mink physically associates with herg and that the interaction leads to increased ikr current density."
MINK1 activates KCNH2.
1 | 5
MINK1 activates KCNH2. 6 / 6
1 | 5
reach
"In addition, D76N and D85N KCNE1 (Mink) mutations also increased the in vitro sensitivity of IKr and hERG to inhibition by clarithromycin [XREF_BIBR]."
signor
"Herg, a human homologue of the ether-a-go-go gene of the fruitfly drosophila melanogaster, encodes aproteinthat produces the rapidly activating cardiac delayed rectifier (i[kr]). / our results show that mink physically associates with herg and that the interaction leads to increased ikr current density."
reach
"MiRP1 encoded by KCNE2 is thought to regulate KCNH2 in the human heart; MinK encoded by KCNE1 may also modulate KCNH2 in vivo; 14-3-3epsilon binding to KCNH2 channels shifts the activation curve towards more hyperpolarized potentials; GM130, a Golgi associated protein, interacts with KCNH2 as the channel is transported between the endoplasmic reticulum and the plasma membrane [7-10]."
reach
"Although MinK most likely functions as the accessory subunit for KCNQ1 to form I Ks channels in the heart [XREF_BIBR, XREF_BIBR], MinK can also modulate hERG1 channel density when overexpressed in heterologous expression systems [XREF_BIBR, XREF_BIBR]."
reach
"MinK increases hERG currents by an unknown mechanism."
reach
"These studies indicate that, as in KVLQT1, mutations in minK can cause both autosomal dominant (Romano-Ward syndrome) and autosomal-recessive (JLN) LQT.Identification of SCN5A, HERG, KVLQT1 and minK as LQT genes has led to the identification of three critical electrical currents involved in the cardiac action potential."
KCNH2 affects KCN
| 5 7
KCNH2 binds KCN.
| 5 2
| 3 2
sparser
"Furthermore, this soluble peptide of N-terminus (1-135 AA) was shown to bind to membrane bound KCNH2 ( xref ) suggesting that the truncated mutant KCNH2 protein may affect formation of KCNH2 tetramer leading to abnormal function of potassium channel."
sparser
"Unfortunately, hERG1 potassium channel antagonists are strongly associated with cardiac arrhythmias: acquired long QT (aLQT2) and cardiac ventricular fibrillation; these potentially fatal events limit the use of hERG1 blockers for anticancer therapy."
sparser
"5HT 1 receptor subtypes have been suggested to account for adverse events due to interactions with HERG cardiac potassium channel and 5-hydroxytryptamine [ xref ]."
reach
"Clarithromycin inhibits autophagy in colorectal cancer by regulating the hERG1 potassium channel interaction with PI3K."
reach
"Correction : Clarithromycin inhibits autophagy in colorectal cancer by regulating the hERG1 potassium channel interaction with PI3K."
KCN binds KCNE2 and KCNH2. 1 / 1
| 1
sparser
"KvLQT1 and minK associate to form the functional slowly activated delayed rectifier potassium channel ( I Ks ) [12,13] while HERG and MiRP1 associate to form the rapidly activated delayed rectifier potassium channel ( I Kr ) [10] ."
| 1
sparser
"In acute myeloid leukemia cells, β1 integrin, VEGFR1 and hERG potassium channel form a macromolecular signaling complex that promotes cell migration and metastasis [ xref ]."
KCNH2 activates KCN.
| 3
KCNH2 activates KCN. 3 / 3
| 3
reach
"mRNA levels of the KCNH2 unit of the rapidly (I Kr) activating delayed rectifier potassium channel and KCNQ1/2 [(two members of the potassium voltage gated channel subfamily Q of the slowly (I Ks) activating delayed rectifier potassium channels)] were differentially regulated when hPSCs-CLCs were cultured on matrigel or vdECMs conditions."
reach
"For example, congenital long QT syndrome is caused by mutations in the human ether-a-go-go-related gene (HERG) encoding a potassium channel."
reach
"HERG codes for a voltage activated potassium channel that is especially important during the repolarization phase of the action potential."
KCNH2 inhibits KCN.
| 2
Mutated KCNH2 inhibits KCN. 1 / 1
| 1
reach
"Importantly, reduction of the cardiac rapid delayed rectifier potassium channel caused by loss-of-function mutations of the hERG channel will prolong the ventricular action potential, elongate the QTc interval, and cause a lethal arrhythmia."
KCNH2 inhibits KCN. 1 / 1
| 1
reach
"In contrast with findings described by others (Matsa etal, 2011), hERG modulation by LUF7346 completely reversed the severe effects of the potassium channel blocker AST in LQT2 N996I hiPSC-CMs, confirming the efficacy of LUF7346 compared to other molecules reported so far in the literature."
KCNH2 affects Integrins
| 1 9 3
KCNH2 binds Integrins.
| 9
sparser
"β 1 integrins and hERG1 channels form a functional plasma membrane complex."
sparser
"On the whole, these data indicate that the hERG1 protein associates with beta(1) integrins and modulates adhesion receptor signaling."
sparser
"This interaction was not detected in cardiomyocytes because of the presence of the hERG1 auxiliary subunit KCNE1 (potassium voltage-gated channel subfamily E regulatory subunit 1), which blocked the β 1 integrin-hERG1 interaction."
sparser
"We conclude that the interaction of β 1 integrins with hERG1 channels in cancer cells stimulated distinct signaling pathways that depended on the conformational state of hERG1 and affected different aspects of tumor progression."
sparser
"HERG1 is often dysregulated in cancer and physically interacts with integrin to modulate adhesion dependent intracellular signalling cascades, including cell adhesion, invasion, and proliferation [ xref , xref ]."
sparser
"Physical and functional interaction between integrins and hERG potassium channels."
sparser
"These results indicate that the p85 subunit of PI3K associates with hERG1 and the β 1 integrin, to constitute a single macromolecular complex and that its phosphorylation depends on (i) integrin activation and (ii) hERG1 channel activity."
| 1
sparser
"In acute myeloid leukemia cells, β1 integrin, VEGFR1 and hERG potassium channel form a macromolecular signaling complex that promotes cell migration and metastasis [ xref ]."
sparser
"Importantly, they demonstrated that upon β1 integrin stimulation, hERG forms signaling macro-complexes with β1-integrin, the VEGF receptor Flt-1 or the cytokine receptor CXCR4 in lipid rafts."
KCNH2 activates Integrins.
| 1 3
| 1 3
reach
"HERG1 channels modulate integrin signaling to trigger angiogenesis and tumor progression in colorectal cancer."
reach
"Preliminary results suggest that a macromolecular signalling complex indeed occurs between integrins and the hERG1 protein and that hERG channel activity can modulate integrin downstream signalling."
reach
"As shown by Teng et al, KCNH2 mediates integrin and TGFbeta signaling."
KCNH2 affects E2
| 12
KCNH2 inhibits E2.
| 5
KCNH2 inhibits E2. 5 / 5
| 5
reach
"In this work, we demonstrate that stimulation of hERG1 promotes an ubiquitin-proteasome-dependent degradation of cyclin E2 in multiple breast cancer cell lines representing Luminal A, HER2+ and Trastuzumab resistant breast cancer cells."
reach
"Altogether, our findings strongly suggest that stimulation of the hERG1 potassium channels in breast cancer cells induces a calcium dependent degradation of cyclin E2 via activation of an ubiquitin dependent proteasome pathway."
reach
"Stimulation of hERG1 channel activity promotes a calcium dependent degradation of cyclin E2, but not cyclin E1, in breast cancer cells."
reach
"Interestingly, MG132 strongly inhibited the effect of NS1643 on cyclin E2, suggesting that that stimulation of hERG1 channel promotes degradation of cyclin E2 via the proteasome."
reach
"Altogether, our data suggests that stimulation of the hERG1 channel in breast cancer cells activates ubiquitin-proteasome-dependent degradation of cyclin E2 that is independent of GSK3-beta."
KCNH2 decreases the amount of E2.
| 4
KCNH2 decreases the amount of E2. 4 / 4
| 4
reach
"Stimulation of hERG1 channel activity selectively down-regulates cyclin E2 protein level."
reach
"In contrast, we observed that cyclin E2 protein level was significantly reduced after only 2 hours of drug treatment, indicating that acute hERG1 channel activation inhibits cyclin E2 protein expression in a manner that is distinct from the chronic effects exerted on other cell cycle regulators."
reach
"We have previously shown that, acute stimulation of hERG1 ion channels in breast cancer cells promotes reduction (60%) of cyclin E2 protein level, whereas chronic stimulation down-regulated other cell cycle regulators [XREF_BIBR]."
reach
"Interestingly, our experiments showed that stimulation of hERG1 channel dramatically reduced cyclin E2 protein level in Trastuzumab resistant SKBr3 cells as well."
KCNH2 binds E2.
| 2
| 2
reach
"The result of E2 interaction with hERG is an increase in ventricular action potential duration, consistent with the longer QT interval observed in women during the follicular phase of the menstrual cycle."
reach
"An important limitation in the interpretation of structural modes of E2 binding to hERG is an absence of a high-resolution experimental structure of the channel."
KCNH2 ubiquitinates E2.
| 1
KCNH2 leads to the ubiquitination of E2. 1 / 1
| 1
reach
"To determine whether stimulation of hERG channels induces ubiquitination of cyclin E2, endogenous cyclin E2 was immunoprecipitated from cells treated with MG132 alone or MG132 + NS1643 and then immunoblotted with anti-ubiquitin antibodies."
KCNH2 affects Ala-Pro
| 12
KCNH2 inhibits Ala-Pro.
| 9
| 9
reach
"At 1muM ibogaine, the simulations revealed that hERG current inhibition slightly prolongs the duration of the AP, when compared to the drug-free control condition (XREF_FIG a)."
reach
"First hERG blockade prolonged the AP."
reach
"Applying multivariable regression to this pseudo-dataset quantified the contribution of each channel property to the AP prolongation produced by HERG block."
reach
"Computational modeling supported the concept that this bupivacaine induced AP instability and the AP prolongations in the control and LQT1 like myocytes were caused by inhibition of hERG channels."
reach
"Blockade of the hERG potassium channel prolongs the ventricular action potential (AP) and QT interval, and triggers early after depolarizations (EADs) and torsade de pointes (TdP) arrhythmia."
reach
"The ' selective inhibition ' of the hERG channels by Dofe45 would induce a substantial prolongation of the AP."
reach
"Hence, as illustrated in Figure XREF_FIG D, selective hERG inhibition by 300nM Dofe45 would induce a more pronounced AP prolongation."
reach
"Compared with the AP prolongation produced by HERG block in the control myocyte (23.7 ms), Trial # 97 showed a smaller response (DeltaAPD = 15.9 ms) whereas Trial # 270 exhibited a more dramatic response (DeltaAPD = 45.3 ms)."
reach
"HERG channel inhibition and concomitant retardation of AP repolarization caused by therapeutic plasma concentrations of any drug are well-known predictors of an increased risk for TdP arrhythmias and sudden cardiac death [XREF_BIBR]."
KCNH2 activates Ala-Pro.
| 3
KCNH2 activates Ala-Pro. 2 / 2
| 2
reach
"The authors showed that the R311C mutation specifically disables the posttranscriptional activity of TBX20 over KCNH2, which decreases the I Kr and prolongs the AP, therefore, identifying TBX20 as an LQT2 modifying gene [XREF_BIBR]."
reach
"The addition of the hERG blocker E-4031 and the sodium channel modulator veratridine significantly prolonged the AP duration."
KCNH2-R56Q activates Ala-Pro. 1 / 1
| 1
reach
"HERG R56Q channels prolonged the AP of hiPSCs, and the AP was shortened by co-expression of i-eag domains and hERG R56Q channels."
KB130015 affects KCNH2
| 12
KB130015 activates KCNH2.
| 9
KB130015 activates KCNH2. 9 / 9
| 9
reach
"KB130015 activates and blocks hERG1 channels independently of inactivation gating."
reach
"While we can not exclude that KB130015 binding in the central cavity partly underlies the inhibitory effects of KB130015 and its competition with pore blockers, the lack of use-dependence for hERG1 activation by KB130015 requires an " activator " site outside the inner cavity."
reach
"We conclude that KB130015 activates hERG1 channels via a novel mechanism that is not directed to removal of inactivation or to slow-down of deactivation but rather involves an acceleration of hERG1 activation."
reach
"Increasing KB130015 concentrations enhanced hERG1 outward current amplitudes at -20 mV (XREF_FIG)."
reach
"We conclude that MTx and KB130015 synergically activate hERG1 channels, requiring the existence of at least two functionally coupled activator sites."
reach
"The effective concentration in the micromolar range of hERG1 activation by KB130015 is comparable to that of RPR260243, NS1643, and PD-118057, whereas mallotoxin, the only known natural hERG1 activator, is active even in the sub-micromolar range."
reach
"As shown in XREF_FIG, hERG1 activation is significantly accelerated by KB130015 in a voltage dependent manner (e.g., 3.8-fold at -20 mV compared to 2.4-fold at +40 mV)."
reach
"We assume that KB130015 mediated hERG1 activation depends on conformational transitions that require a tyrosine at position 652."
reach
"KB130015 accelerates hERG1 activation gating."
KB130015 inhibits KCNH2.
| 2
KB130015 inhibits KCNH2. 2 / 2
| 2
reach
"Using patch-clamp and two-electrode voltage-clamp techniques we found that KB130015 blocks native and recombinant hERG1 channels at high voltages, but it activates them at low voltages."
reach
"In addition, hERG1 current inhibition by KB130015 at high voltages was almost completely abolished."
KB130015 binds KCNH2.
| 1
KCNH2 binds KB130015. 1 / 1
| 1
reach
"It is conceivable that KB130015 binding to hERG1 induces either activation or inhibition, depending on the " gating status " of the channel, which may be affected by mutation (Y652A / Delta2-373) or drug (mallotoxin) binding."
Integrins affects KCNH2
| 10 2
Integrins binds KCNH2.
| 9
sparser
"β 1 integrins and hERG1 channels form a functional plasma membrane complex."
sparser
"On the whole, these data indicate that the hERG1 protein associates with beta(1) integrins and modulates adhesion receptor signaling."
sparser
"This interaction was not detected in cardiomyocytes because of the presence of the hERG1 auxiliary subunit KCNE1 (potassium voltage-gated channel subfamily E regulatory subunit 1), which blocked the β 1 integrin-hERG1 interaction."
sparser
"We conclude that the interaction of β 1 integrins with hERG1 channels in cancer cells stimulated distinct signaling pathways that depended on the conformational state of hERG1 and affected different aspects of tumor progression."
sparser
"HERG1 is often dysregulated in cancer and physically interacts with integrin to modulate adhesion dependent intracellular signalling cascades, including cell adhesion, invasion, and proliferation [ xref , xref ]."
sparser
"Physical and functional interaction between integrins and hERG potassium channels."
sparser
"These results indicate that the p85 subunit of PI3K associates with hERG1 and the β 1 integrin, to constitute a single macromolecular complex and that its phosphorylation depends on (i) integrin activation and (ii) hERG1 channel activity."
| 1
sparser
"In acute myeloid leukemia cells, β1 integrin, VEGFR1 and hERG potassium channel form a macromolecular signaling complex that promotes cell migration and metastasis [ xref ]."
sparser
"Importantly, they demonstrated that upon β1 integrin stimulation, hERG forms signaling macro-complexes with β1-integrin, the VEGF receptor Flt-1 or the cytokine receptor CXCR4 in lipid rafts."
Integrins activates KCNH2.
| 1 2
| 1 1
reach
"The link between hERG1 and integrins is twofold : integrins, mainly the beta1 integrin subunit, can activate hERG1."
sparser
"Cell adhesion via integrin β 1 causes activation of hERG1, which is essential for direct FAK phosphorylation ( xref ). xref "
Integrins bound to FN1 activates KCNH2. 1 / 1
| 1
reach
"Previous work has demonstrated that cell surface integrins can regulate the activity of K + channels when mediated by endogenous ligands; for example, the binding of fibronectin to cell surface integrins has been shown to promote activation of hERG K + channels, laminin binding has been demonstrated to promote inwardly rectifying K + currents, and voltage gated K + channels such as K v 1.3 have also been linked to integrin activation."
Sotalol affects KCNH2
| 1 10
Sotalol inhibits KCNH2.
| 1 8
| 1 8
sparser
"Fig. 5 C shows an example of the use of a step-ramp protocol to assess I hERG inhibition by the low potency inhibitor sotalol (followed by application of a supramaximal concentration of cisapride to inhibit I hERG remaining following exposure to sotalol ( Kirsch et al., 2004 ))."
reach
"In whole-cell voltage clamp studies we found : 1) 60 muM A-935142 enhanced hERG current in the presence of 150 muM sotalol (57.5 +/-5.8%) to a similar extent as seen with A-935142 alone (55.6 +/-5.1%); 2) 150 muM sotalol blocked hERG current in the presence of 60 muM A-935142 (43.5 +/-1.5%) to a similar extent as that seen with sotalol alone (42.0 +/-3.2%) and 3) during co-application, hERG current enhancement was followed by current blockade."
reach
"Torsadogenic hERG blockers such as sotalol and quinidine produced statistically and physiologically significant effects, consistent with patch-clamp studies on human embryonic stem cell derived cardiomyocytes (hESC-CMs)."
reach
"Amiodarone, azimilide, dofetilide, quinidine and sotalol all produced a dose dependent inhibition of HERG current."
reach
"This analysis shows that enhancements of endogenous HF oscillations in HR were also found in beagle dogs with dofetilide and with other hERG blockers such as cisapride, haloperidol, risperidone, DL sotalol, terfenadine and thioridazine."
reach
"To analyse the rate-dependency of this effect, we tested the beta-blocker Sotalol that is known to also inhibit hERG channels and prolong the QT duration in patients 45."
reach
"Dofetilide, cisapride, sotalol, terfenadine and verapamil blocked hERG channels at 37degreesC with an IC50 of 7nM, 18nM, 343muM, 165nM and 214nM, respectively."
reach
"First, we investigated the beta-blocker Sotalol, which is known to block also hERG K + channels and thereby induce a pharmacological Long QT syndrome with the high risk of arrhythmia [XREF_BIBR, XREF_BIBR]."
reach
"It should be mentioned that cisapride, dofetilide, and sotalol directly inhibit hERG channel activity whereas quinidine decreases the surface expression of hERG channels by suppressing hERG channel translocation to cell membrane surface XREF_BIBR."
Sotalol activates KCNH2.
| 2
Sotalol activates KCNH2. 2 / 2
| 2
reach
"Raising the extracellular potassium to 10 mmol/l, HERG block by azimilide, dofetilide, quinidine and sotalol was significantly decreased, while the block by amiodarone was unchanged."
reach
"KCNH2 encodes for the hERG potassium channel that is targeted by sotalol and this variant was identified in a large genome-wide association study on the physiological regulation of QT interval."
Desipramine affects KCNH2
| 2 11
Desipramine inhibits KCNH2.
| 2 9
| 2 9
reach
"The antidepressant drug desipramine that blocks hERG protein trafficking to the plasma membrane XREF_BIBR exhibited pro apoptotic effects similar to doxazosin (XREF_FIG)."
reach
"Moreover, desipramine produced acute blockage of the hERG channel at the binding sites of Y652 and F656 [XREF_BIBR]."
reach
"We found that desipramine reduced hERG currents by binding to a receptor site inside the channel pore."
reach
"To further assess pro apoptotic effects of hERG antagonism, we applied the antidepressant drug desipramine that has previously been shown to reduce hERG currents and prevent hERG protein trafficking to the plasma membrane XREF_BIBR."
reach
"In rescue experiments, we found that they exert no reverse effect on pentamidine- or desipramine induced hERG trafficking defect, although quinidine has been reported to rescue trafficking deficient pore mutation hERG G601S based on the interaction with F656."
reach
"Pentamidine and desipramine were reported to suppress hERG forward trafficking to the cell surface, and the aromatic amino F656 mediated the effects of pentamidine [XREF_BIBR, XREF_BIBR]."
reach
"Pentamidine and desipramine were reported to suppress hERG forward trafficking from the endoplasmic reticulum, and the aromatic amino F656 in S6 domain mediated the effects of pentamidine [XREF_BIBR, XREF_BIBR]."
reach
"In this regard, the serotonin selective reuptake inhibitor fluoxetine, its metabolite norfluoxetine, and the tricyclic antidepressant desipramine disrupt ER processing of HERG, an effect thought to underlie drug induced (acquired) long QT syndrome [XREF_BIBR, XREF_BIBR]."
reach
"The IC (50) for desipramine needed to block the hERG current in Xenopus oocytes decreased progressively relative to the degree of depolarization."
Desipramine decreases the amount of KCNH2.
| 2
Desipramine decreases the amount of KCNH2. 2 / 2
| 2
reach
"XREF_BIBR, XREF_BIBR Desipramine reduces hERG expression via inhibiting trafficking and promoting endocytosis and degradation."
reach
"Here, we have studied in detail how desipramine inhibits hERG surface expression."
Curcumin affects KCNH2
| 1 11
Curcumin inhibits KCNH2.
| 1 10
| 1 10
reach
"Results of the manual patch clamp assay of HEK 293 cells clearly illustrated that our hybrid nanocurcumin formulation prevented the curcumin induced inhibition of hERG K + channel at concentrations higher than the therapeutic concentrations of curcumin."
reach
"The liposomal curcumin formulation, at a curcumin concentration of 6muM, induced a statistically significant inhibition of the hERG tail current (30%) at I +20 (n = 3) (not included in figure)."
reach
"In whole-cell patch-clamp experiments, we found that curcumin inhibited hERG K+ currents in HEK293 cells stably expressing hERG channels in a dose dependent manner, with IC50 value of 5.55 muM."
reach
"Curcumin inhibits hERG potassium channels in vitro."
reach
"In the present study, our formulation of lipopolymeric hybrid nanocurcumin formulation was conceptualized based on the protective effects of liposomes on curcumin dependent inhibition of the hERG current."
reach
"The manual patch clamp assay of HEK 293 cells clearly illustrated that this hybrid nanocurcumin formulation prevented the curcumin induced inhibition of hERG K + channel at concentrations higher than the therapeutic concentrations of curcumin."
reach
"Studies revealed that curcumin inhibited the hERG K + channel in a concentration dependent manner with an IC 50 as low as 5.5 muM."
reach
"Class 3 inhibition of hERG K+ channel by caffeic acid phenethyl ester (CAPE) and curcumin."
reach
"We conclude that curcumin inhibits hERG K+ channels in vitro."
reach
"Unfortunately, curcumin has been reported to block the hERG K + potassium channel [XREF_BIBR, XREF_BIBR]."
Curcumin activates KCNH2.
| 1
| 1
reach
"The results of the Manual Patch Clamp assay reveal that lipopolymeric hybrid nanocurcumin formulations were able to protect against the inhibition of hERG current caused by curcumin."
Calcium(2+) affects KCNH2
| 11
Calcium(2+) inhibits KCNH2.
| 6
| 6
reach
"XREF_FIG and XREF_FIG also demonstrate that Ca 2+ does not block HERG directly."
reach
"Increasing extracellular Ca 2+ slowed the rate of HERG activation and accelerated deactivation (Figs."
reach
"Ca 2+ Slows the Rate of HERG Channel Activation."
reach
"Ca 2+ Decreases HERG Current Amplitude and Shifts the Isochronal Activation Curve."
reach
"Elevated Ca 2+ decreased the rate of HERG activation at all potentials measured (+60 to 0 mV)."
reach
"Furthermore, we found that Ca 2+ greatly reduces the pH sensitivity of Kv11.1, or hErg1."
Calcium(2+) activates KCNH2.
| 5
| 5
reach
"We recently found that extracellular Ca 2+ can modulate the voltage dependence of HERG channel activation independently of inactivation (Johnson et al., 1999)."
reach
"Elevated extracellular K + (20 mM) decreases the shift in the HERG channel isochronal current-voltage curve caused by Ca 2+."
reach
"These changes reflect altered hERG1 gating because no rapid currents were induced in uninjected oocytes treated with these concentrations of Ca 2+ or Cd 2+ (XREF_FIG)."
reach
"Although we can not definitively rule out the possibility that Ca 2+ causes an allosteric change in HERG channels that mimics a specific association near the activation voltage sensor, our data are consistent with a simple Ca 2+ -induced change in membrane potential sensed specifically by the activation process."
reach
"Several preclinical studies suggest an important role for sodium, potassium (Ca activated, outward rectifying, and hERG) and chloride ion-channels as well as Na-K-Cl cotransporter on GBM cell migration and parenchymal invasion, possibly through effects on cellular volume and shape."
| 11
reach
"The ROS scavenger N-acetyl cysteine (NAC) significantly attenuated hERG reduction induced by THIO and abolished the upregulation of ER stress marker proteins."
reach
"In fact, it seems possible to speculate that the increase of the outward currents mediated by HERG caused by the burst of ROS production that follows the reperfusion of the tissue after an ischemic period would tend to repolarize the membrane potential and shorten the action potential duration."
reach
"These results suggested that histidines in the S 5 -S 6 linker are crucial players in iron dependent ROS production modulating KCNH2 K + channel function."
reach
"These results suggested that endogenous iron ions are possibly involved in controlling resting ROS production which, in turn, modulate KCNH2 channel function."
reach
"The modulation of HERG K + channels by ROS, occurring in both resting and stimulated conditions, may represent an important functional mechanism linking the changes in the levels of O 2 and ROS in heart tissue with the electrophysiological modifications occurring during ischemia-reperfusion phenomena."
reach
"We therefore investigated whether ROS, by modulating the interaction of hERG with Hsp90, mediates hypoxia induced hERG downregulation."
reach
"Recent evidence has shown that ROS can specifically modulate the function of HERG K + channels [58] : an enhancement of ROS production increases HERG outward K + currents, whereas a decrease in ROS levels can inhibit the resting outward K + currents and prevent their increase induced by oxidizing conditions."
reach
"We consider this highly unlikely, as hERG can be modulated by ROS generated by various experimental means."
reach
"These results suggest that the involvement of ROS in triggering ER stress by THIO decreased the level of mature hERG channel proteins."
reach
"It was reported that HIV Tat protein induced ROS production [12] and ROS decreased hERG K + currents and channel protein expression without affecting hERG mRNA level [13]."
Reactive Oxygen Species decreases the amount of KCNH2.
| 1
Reactive Oxygen Species decreases the amount of KCNH2. 1 / 1
| 1
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"We also found that HIV Tat protein significantly increased ROS generation and antioxidant tempol prevented HIV Tat induced downregulation of hERG protein expression."
NCIT:C17764 affects KCNH2
| 11
sparser
"Pharmacological chaperones may serve to disrupt the interaction of immature Kv11.1 proteins with ER chaperone and quality-control proteins including Hsp40 (40-kDa heat shock protein), Hsc70 (70-kDa heat shock cognate protein), Hsp90 (90-kDa heat shock protein), FLBP38, calnexin, and numerous other chaperones, thereby protecting mutant proteins from degradation and alternatively by attenuating digestion by enzymes such as trypsin xref – xref ."
sparser
"Co-immunoprecipitation experiments revealed that hypoxia inhibited interaction of hERG with Hsp90 chaperone required for maturation, which was restored in the presence of ROS scavengers."
sparser
"Effect of Prop on the binding of HERG protein and molecular chaperone CNX/CRT in each cell model."
sparser
"Effect of ALLN on the binding of HERG protein and molecular chaperone CNX/CRT in each cell model."
sparser
"To determine the role of chaperone CNX/CRT in the process of ALLN to correct the translocation of HERG-A561V mutant protein, the binding of HERG protein and molecular chaperone CNX/CRT in the HERG-WT, HERG- A561V, HERG-L539fs/47, HERG-WT/A561V, HERG-WT/L539fs/47 cell models were detected by immunoprecipitation after 24-h treatment with or without ALLN (10 μmol/l)."
sparser
"We therefore turned to exploring whether THIO prevents maturation of hERG channels via inhibiting chaperone-hERG interactions; to this end, we performed coimmunoprecipitation experiments to determine the association of hERG protein with Hsp70."
sparser
"Alternatively, ROS could interact with a conserved thiol pair of Hsp90 rendering it nonfunctional, thereby interfering with chaperone binding to hERG."
sparser
"Further investigation is necessary to determine each of the chaperones that interact with HERG and if the chaperone-HERG interactions are regulated by increased cAMP or PKA activation."
sparser
"Maturation of hERG protein in turn is inhibited by preventing the binding of hERG to HSP chaperone complexes, which is again mediated by ROS xref ."
sparser
"For example, the reactive oxygen species (ROS) generated during hypoxia have been shown to inhibit protein folding and maturation by interfering with the interaction between hERG and the Hsp90 chaperone complex [ xref ]."
| 1
sparser
"Furthermore, the interaction between mutant hERG proteins and chaperone proteins, Calnexin and Calreticulin, play crucial roles in these processes."
Kv4.3 affects KCNH2
| 11
Kv4.3 activates KCNH2.
| 5
Kv4.3 activates KCNH2. 5 / 5
| 5
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"These results suggest that Kv4.3 enhances hERG protein trafficking through Hsp70."
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"In the presence of Kv4.3, more hERG protein localized on the surface of the cells, thus suggesting that Kv4.3 enhances hERG trafficking."
reach
"Co-expression of Kv4.3 with hERG increased hERG current density (tail current after a step to +10 mV : 26 +/-3 versus 56 +/-7 pA/pF, p < 0.01)."
reach
"Based on aforementioned studies, we hypothesize that Hsp70 may be involved in the maturation of hERG induced by Kv4.3."
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"Co-transfection of Kv4.3 increased I hERG densities, compared with cells transfected with hERG alone."
Kv4.3 increases the amount of KCNH2.
| 3
Kv4.3 increases the amount of KCNH2. 3 / 3
| 3
reach
"In summary, these results suggest that Kv4.3 enhances hERG protein expression through Hsp70."
reach
"The upregulation of hERG expression by Kv4.3 is dependent on Hsp70, as Hsp70 siRNA could prevent the Kv4.3-induced hERG expression."
reach
"Since previous study showed that overexpression of Hsp70 increased the expression of hERG protein 27, we therefore hypothesized that Kv4.3 increased the hERG protein expression via upregulation of Hsp70."
Kv4.3 binds KCNH2.
| 3
KCNH2 binds Kv4.3. 3 / 3
| 3
reach
"Because Hsp70 was reported to interact with hERG 27 and the present study showed that hERG interacts with Kv4.3, we hypothesize that Hsp70 may form complexes with hERG and Kv4.3."
reach
"We observed that Kv4.3 interacted with hERG and increased hERG expression through Hsp70."
reach
"The result showed that hERG and Kv4.3 bind to each other and form a complex."
KCNH2 affects NCIT:C17764
| 11
sparser
"Pharmacological chaperones may serve to disrupt the interaction of immature Kv11.1 proteins with ER chaperone and quality-control proteins including Hsp40 (40-kDa heat shock protein), Hsc70 (70-kDa heat shock cognate protein), Hsp90 (90-kDa heat shock protein), FLBP38, calnexin, and numerous other chaperones, thereby protecting mutant proteins from degradation and alternatively by attenuating digestion by enzymes such as trypsin xref – xref ."
sparser
"Co-immunoprecipitation experiments revealed that hypoxia inhibited interaction of hERG with Hsp90 chaperone required for maturation, which was restored in the presence of ROS scavengers."
sparser
"Effect of Prop on the binding of HERG protein and molecular chaperone CNX/CRT in each cell model."
sparser
"Effect of ALLN on the binding of HERG protein and molecular chaperone CNX/CRT in each cell model."
sparser
"To determine the role of chaperone CNX/CRT in the process of ALLN to correct the translocation of HERG-A561V mutant protein, the binding of HERG protein and molecular chaperone CNX/CRT in the HERG-WT, HERG- A561V, HERG-L539fs/47, HERG-WT/A561V, HERG-WT/L539fs/47 cell models were detected by immunoprecipitation after 24-h treatment with or without ALLN (10 μmol/l)."
sparser
"We therefore turned to exploring whether THIO prevents maturation of hERG channels via inhibiting chaperone-hERG interactions; to this end, we performed coimmunoprecipitation experiments to determine the association of hERG protein with Hsp70."
sparser
"Alternatively, ROS could interact with a conserved thiol pair of Hsp90 rendering it nonfunctional, thereby interfering with chaperone binding to hERG."
sparser
"Further investigation is necessary to determine each of the chaperones that interact with HERG and if the chaperone-HERG interactions are regulated by increased cAMP or PKA activation."
sparser
"Maturation of hERG protein in turn is inhibited by preventing the binding of hERG to HSP chaperone complexes, which is again mediated by ROS xref ."
sparser
"For example, the reactive oxygen species (ROS) generated during hypoxia have been shown to inhibit protein folding and maturation by interfering with the interaction between hERG and the Hsp90 chaperone complex [ xref ]."
| 1
sparser
"Furthermore, the interaction between mutant hERG proteins and chaperone proteins, Calnexin and Calreticulin, play crucial roles in these processes."
KCNH2 affects CANX
2 | 1 6 3
KCNH2 binds CANX.
2 | 1 6 2
2 | 1 3 2
biogrid
No evidence text available
biogrid
No evidence text available
reach
"To assess the physical interaction between hERG and Calnexin and Calreticulin, immunoprecipitation was done with anti-Calnexin or anti-Calreticulin antibody, followed by Western blot analysis with anti-hERG antibody."
sparser
"Importantly, Calnexin interacted with hERG proteins in the ER in HEK293T cells."
reach
"The calnexin and hERG interaction was preserved in reciprocal pulldown immunoaffinity assays."
sparser
"Coimmunoprecipitation assays showed that Calnexin only interacted with the ER-residing form of hERG proteins ( xref ), suggesting that Calnexin interacts with hERG proteins in the ER."
sparser
"The calnexin and hERG interaction was preserved in reciprocal pulldown immunoaffinity assays."
CALR binds CANX and KCNH2. 1 / 1
| 1
sparser
"As shown in xref , treatment with lactacystin or ALLN but not leupeptin (a lysosome inhibitor) results in an increase in the levels of core-glycosylated, immature form of hERG, Calnexin and Calreticulin."
sparser
"Coimmunoprecipitation assays showed that Calnexin only interacted with the ER-residing form of hERG proteins ( xref ), suggesting that Calnexin interacts with hERG proteins in the ER."
| 1
sparser
"Furthermore, the interaction between mutant hERG proteins and chaperone proteins, Calnexin and Calreticulin, play crucial roles in these processes."
KCNH2 decreases the amount of CANX.
| 1
KCNH2 decreases the amount of CANX. 1 / 1
| 1
reach
"Furthermore, the high-glucose-induced inhibition of hERG channel trafficking could activate the unfolded protein response (UPR) by up-regulating the expression levels of activating transcription factor-6 (ATF-6) and the ER chaperone protein calnexin."
Flecainide affects KCNH2
| 2 10
Flecainide inhibits KCNH2.
| 1 9
| 1 9
reach
"Flecainide has also been shown to block hERG channels at physiologically relevant concentrations (Paul et al., 2002), and QX-FL and NU-FL have been used to demonstrate that, as is the case in the Na + channel, hERG block requires entry of a cationic blocking molecule from the cell interior (Melgari et al., 2015)."
reach
"HERG inhibition by flecainide [XREF_BIBR] at this clinical dose is reported, at higher doses this effect is less marked (XREF_FIG) reflecting the integrated sum of other off-target effects."
reach
"Thus, flecainide inhibits hERG currents by 81% at 10mum and lidocaine inhibits hERG by 25% at 100 muM."
reach
"The inactivation-dependence of flecainide block of hERG was studied further using mutants with impaired inactivation (XREF_FIG)."
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"10muM flecainide blocks 80% and 1muM only 20% of wild-type hERG current in a HEK293 cell model [XREF_BIBR]."
reach
"Independent support for the idea that flecainide acts to inhibit hERG from the cell interior comes from the observation that the drug 's action is potentiated in cells transfected with the drug uptake transporter OCTN1 XREF_BIBR."
reach
"Moreover, Flecainide blocks the rapid component of the delayed rectifier potassium current (IKr) (KCNH2 and KCNQ1), prolonging the action potential duration (APD) in ventricular and atrial muscle fibers [82]."
reach
"This is probably a consequence of the ability of flecainide to block I Kr / hERG [XREF_BIBR] : decreased repolarization rate of CM membrane leads to prolongation in APD."
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"HERG channels were blocked by D,L-sotalol, quinidine and flecainide (IC (50) : 69, 0.33 and 0.74 micromol/L, respectively)."
Flecainide binds KCNH2.
| 1 1
| 1 1
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"In further experiments, the extent to which C-type inactivation might stabilize the binding of flecainide to hERG channels was investigated by washing the drug off during sustained depolarization."
Cis-doxepin affects KCNH2
| 10
Cis-doxepin inhibits KCNH2.
| 8
| 8
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"TCAs are associated with QT c interval lengthening in clinical use XREF_BIBR, and I HERG inhibition by doxepin observed in the present study is consistent both with documented cases of QT interval prolongation and TdP with doxepin XREF_BIBR and with QT interval increases seen in anaesthetised guinea-pigs receiving doxepin infusion XREF_BIBR."
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"XREF_FIG shows the effects on doxepin inhibition of I HERG of the mutation Y652A (tyrosine --> alanine)."
reach
"Therefore, we also investigated I HERG blockade by doxepin using an action potential (AP) voltage waveform XREF_BIBR."
reach
"The lack of a strong dependence of HERG channel blockade by doxepin on I HERG inactivation suggests that gating dependent blockade by this drug is likely to arise predominantly to activated and open channels."
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"Indeed, moxifloxacin (40), fluvoxamine (41), and, recently, doxepin (42) have been reported to inhibit hERG with a mixed state-dependence of inhibition (with components of both closed- and open-channel block, including a very rapid open-channel block)."
reach
"Doxepin inhibited I HERG with an IC 50 value of 6.5 +/-1.4 muM and native I Kr with an IC 50 of 4.4 +/-0.6 muM."
reach
"For example, amitriptyline, imipramine, and doxepin block the HERG channel with the IC 50 s of 10 muM, 3.4 muM, and 6.5 muM, respectively (Cavalli et al., 2002; Duncan et al., 2007)."
reach
"Inhibition of the HERG potassium channel by the tricyclic antidepressant doxepin."
| 2
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"Whilst obligatory molecular determinants of doxepin binding to HERG remain to be found, the fact that I HERG inhibition by doxepin developed progressively over several minutes following rapid external solution exchange is consistent with the drug crossing the cell membrane to reach its site of action."
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"Neither the Y652A nor F656A mutations attenuated blockade by doxepin concentrations producing very high levels (> 90%) of blockade of WT I HERG, suggesting that neither residue is absolutely obligatory for doxepin binding to HERG channels to occur."
| 10
Cadmium atom activates KCNH2.
| 8
| 5
reach
"At low concentrations (10-200 mu M), Cd 2+ enhanced HERG currents without shifting the voltage dependence of activation."
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"The ability of Cd 2+ to increase HERG K + current appeared critically dependent upon channel inactivation, and both the increase in current and the accelerated rate of current decay were lost when inactivation was removed."
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"A simple mechanism by which Cd 2+ could increase HERG currents is to decrease the probability that the channels inactivate."
reach
"Surprisingly, 200 mu M Cd 2+ enhanced HERG outward currents at most tested membrane potentials."
reach
"The present study illustrates that low concentrations of extracellular Cd 2+ modulated voltage dependent HERG inactivation independently of channel activation."
Cadmium atom activates mutated KCNH2. 1 / 1
| 1
reach
"However, in contrast to WT hERG1 (XREF_FIG), Cd 2+ did not induce the appearance of I Cd-out in the two mutant hERG1 channels."
Cadmium atom activates KCNH2-D509C. 1 / 1
| 1
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"I Cd-out was also not observed in D456C or D509C hERG1 channels treated with Cd 2+ at concentrations that shifted the voltage dependence of channel activation."
Cadmium atom activates KCNH2-D456C. 1 / 1
| 1
reach
"I Cd-out was also not observed in D456C or D509C hERG1 channels treated with Cd 2+ at concentrations that shifted the voltage dependence of channel activation."
Cadmium atom increases the amount of KCNH2.
| 2
Cadmium atom increases the amount of KCNH2. 2 / 2
| 2
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"Specifically, studies have shown that Cd 2+ exposure increases transcription of c- jun, c- myc, c- fos, and erg-1 (see Refs."
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"Cd 2+ exposure also increases transcription of c- jun, c- myc, c- fos, erg-1, and gadd 153 [1,11,13,17-20]."
Berberine affects KCNH2
| 1 10
Berberine inhibits KCNH2.
| 6
| 5
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"(2) The combination of Berberine with Azithromycin reduced hERG currents, producing an inhibitive effect stronger than use of a single drug alone, due to the high binding affinity for the onset of inactivation."
reach
"These results indicate that berberine in combination with statins can increase cardiotoxicity by inhibiting CYP3A4 and hERG channel."
reach
"HERG1 is involved in the pathophysiological process and inhibited by berberine in SKOV3 cells."
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"Berberine blocked the HERG channels potently with an IC50 value of approximately 75 micromol/L."
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"Together these findings indicate that berberine preferentially blocks the open state of hERG channels by interacting with specific residues that were previously reported to be important for binding of more potent antagonists."
Berberine inhibits mutated KCNH2. 1 / 1
| 1
reach
"An inactivation deficient mutant hERG channel (G628C and S631C) was also blocked by berberine."
Berberine activates KCNH2.
| 1 4
| 1 4
reach
"Mechanism and pharmacological rescue of berberine induced hERG channel deficiency."
reach
"Mechanism and pharmacological rescue of berberine induced hERG channel deficiency [Corrigendum]."
reach
"Berberine induces hERG channel deficiency through trafficking inhibition."
reach
"Erratum : Mechanism and pharmacological rescue of berberine induced hERG channel deficiency [Corrigendum]."
MiRP1 affects KCNH2
| 10
MiRP1 binds KCNH2.
| 5
KCNH2 binds MiRP1. 5 / 5
| 5
reach
"KvLQT1 and minK associate to form the functional slowly activated delayed rectifier potassium channel (I Ks) [12,13] while HERG and MiRP1 associate to form the rapidly activated delayed rectifier potassium channel (I Kr) [10]."
reach
"While MinK and KvLQT1 complexes recreate the behaviors of I Ks channels, MiRP1 and HERG complexes recapitulate those of I Kr channels."
reach
"Third, MiRP1 and HERG complexes, like I Kr channels in murine atrial and guinea pig ventricular myocytes, are less sensitive to regulation by external K + than HERG channels (Shibasaki 1987; Scamps and Carmeliet 1989; Sanguinetti and Jurkiewicz 1992; Sanguinetti et al. 1995; Yang and Roden 1996; Yang et al. 1997)."
reach
"Thus, minK and MiRP1 interaction with HERG are not mediators of regulators of the kinase dependent enhancement of channel synthesis."
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"Second, MiRP1 and HERG complexes and I Kr channels in murine and human cardiac myocytes deactivate 3-fold more rapidly than channels formed only of HERG subunits (Yang et al. 1994; Sanguinetti et al. 1995; London et al. 1997; Wang et al. 1997a)."
MiRP1 activates KCNH2.
| 5
MiRP1 activates KCNH2. 5 / 5
| 5
reach
"MiRP1 and Cterm-MinK modulated HERG much like wild-type MiRP1 (XREF_FIG C, right), suggesting that our chimera is indeed expressed and that it can not modulate KvLQT1."
reach
"MinK associates with the KCNQ1 Kv channel alpha subunit to form the I Ks ventricular repolarization current in human heart; MiRP1 modulates the hERG alpha subunit which forms the cardiac I Kr repolarization current in human heart."
reach
"The patient was found to harbour a KCNE2 gene mutation encoding a T10M amino acid substitution in MiRP1, an ancillary subunit that co-assembles with and functionally modulates hERG."
reach
"MiRP1 modulates hERG function and pharmacology, and MiRP1-hERG complexes may contribute to generating I Kr in human heart."
reach
"MiRP1 also modulates the response to external K + and, more importantly, MiRP1 appears to modulate the response of HERG K + channels to drugs 13,15 (see below)."
KCNH2 affects IKr
| 10
KCNH2 inhibits IKr.
| 6
Mutated KCNH2 inhibits IKr. 3 / 3
| 3
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"Mutation of HERG causes a decrease and a loss of function of IKr resulting in long QT syndrome 2 (LQT2)."
reach
"Functional expression studies have demonstrated that KCNH2 mutations cause a reduction of IKr current, but, similarly to LQT1 mutations, this effect is realized through different biophysical mechanisms and also though trafficking abnormalities of the mutant proteins [XREF_BIBR]."
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"Mutations of HERG cause the autosomal dominant long-QT syndrome (LQTS), presumably by disrupting the normal function of IKr."
KCNH2 inhibits IKr. 3 / 3
| 3
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"A lesser number of membrane hERG channels reduce IKr, prolonging the QT interval."
reach
"Mutations in hERG channels reduce IKr to cause congenital long-QT syndrome type 2, mostly by decreasing surface membrane expression of trafficking deficient channels."
reach
"Heterologous expression of HERG in Xenopus oocytes revealed that HERG current was similar to a well characterized cardiac delayed rectifier K+ current, IKr, and led to the hypothesis that mutations in HERG reduced IKr, causing prolonged myocellular action potentials."
KCNH2 activates IKr.
| 4
KCNH2 activates IKr. 4 / 4
| 4
reach
"Human ether-a-go-go-related gene (hERG) channels conduct the rapidly activating current IKr; KCNQ1 and KCNE1 channels conduct the slowly activating current IKs; and Kv1.5 channels conduct an ultrarapid activating current IKur."
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"The N588K mutation in the KCNH2 gene causes a gain of function of IKr, and shortens the action potential duration and the QT interval."
reach
"The elementary properties of HERG are unknown, and as a test of the hypothesis that HERG produces IKr, we compared their elementary properties."
reach
"Potassium channels encoded by human ether-a-go-go-related gene (hERG) mediate the cardiac rapid delayed rectifier K (+) current (IKr), which participates in ventricular repolarization and has a protective role against unwanted premature stimuli late in repolarization and early in diastole."
KCNH2 affects Cyclin
| 10
KCNH2 inhibits Cyclin.
| 5
KCNH2 inhibits Cyclin. 5 / 5
| 5
reach
"Altogether, our data suggests that stimulation of the hERG1 channel in breast cancer cells activates ubiquitin-proteasome-dependent degradation of cyclin E2 that is independent of GSK3-beta."
reach
"Interestingly, MG132 strongly inhibited the effect of NS1643 on cyclin E2, suggesting that that stimulation of hERG1 channel promotes degradation of cyclin E2 via the proteasome."
reach
"In this work, we demonstrate that stimulation of hERG1 promotes an ubiquitin-proteasome-dependent degradation of cyclin E2 in multiple breast cancer cell lines representing Luminal A, HER2+ and Trastuzumab resistant breast cancer cells."
reach
"Stimulation of hERG1 channel activity promotes a calcium dependent degradation of cyclin E2, but not cyclin E1, in breast cancer cells."
reach
"Altogether, our findings strongly suggest that stimulation of the hERG1 potassium channels in breast cancer cells induces a calcium dependent degradation of cyclin E2 via activation of an ubiquitin dependent proteasome pathway."
KCNH2 decreases the amount of Cyclin.
| 4
KCNH2 decreases the amount of Cyclin. 4 / 4
| 4
reach
"We have previously shown that, acute stimulation of hERG1 ion channels in breast cancer cells promotes reduction (60%) of cyclin E2 protein level, whereas chronic stimulation down-regulated other cell cycle regulators [XREF_BIBR]."
reach
"Interestingly, our experiments showed that stimulation of hERG1 channel dramatically reduced cyclin E2 protein level in Trastuzumab resistant SKBr3 cells as well."
reach
"Stimulation of hERG1 channel activity selectively down-regulates cyclin E2 protein level."
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"In contrast, we observed that cyclin E2 protein level was significantly reduced after only 2 hours of drug treatment, indicating that acute hERG1 channel activation inhibits cyclin E2 protein expression in a manner that is distinct from the chronic effects exerted on other cell cycle regulators."
KCNH2 ubiquitinates Cyclin.
| 1
KCNH2 leads to the ubiquitination of Cyclin. 1 / 1
| 1
reach
"To determine whether stimulation of hERG channels induces ubiquitination of cyclin E2, endogenous cyclin E2 was immunoprecipitated from cells treated with MG132 alone or MG132 + NS1643 and then immunoblotted with anti-ubiquitin antibodies."
CnErg1 affects KCNH2
| 10
CnErg1 inhibits KCNH2.
| 5
CnErg1 inhibits KCNH2. 5 / 5
| 5
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"Collectively, our data provides a plausible kinetic explanation for incomplete blockade of hERG by CnErg1 that is consistent with the proposed highly dynamic conformation of the outer pore domain of hERG."
reach
"ErgTx1 inhibit human and rat ERG1 in a similar manner (IC 50 4-7 nM), however, it was unable to affect human ERG2 current while completely blocked the rat ERG2 channel with poor recuperation (~ IC 50 1 nM)."
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"However, rapid superfusion of 10 nM ergtoxin onto cells during depolarisation did not lead to blockade (~ 2 +/-1%), suggesting that ergtoxin can not block HERG channels in the open state, except when the toxin has been previously allowed to interact with channels in the closed state."
reach
"Use of HERG blockers including E-4031 and ergtoxin have still not been tested in vivo studies but do show a promising role in potential use with chemotherapeutic agents or in chemoresistant disease."
reach
"The goals of this study are to investigate the mechanism and site of action whereby a human ether-a-go-go-related gene (HERG)-specific scorpion peptide toxin, ErgTx, suppresses HERG current."
CnErg1 binds KCNH2.
| 5
| 5
reach
"Electrostatic interactions are much less important for ErgTx1 binding to HERG channels than for AgTx2 binding to Shake r channels, although these interactions can not be ruled out completely."
reach
"Analysis of the kinetics of CnErg1 interaction with hERG indicated that CnErg1 binding is not diffusion limited."
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"We have also examined the temperature-dependence of CnErg1 binding to hERG."
reach
"It is therefore likely that hydrophobic interactions will play a more important role in Ergtoxin binding to HERG than is the case for other scorpion toxins binding to their respective ion-channel receptors."
reach
"The binding of Ergtoxin to HERG channels, however, is not influenced by the extracellular [K +] and does not involve strong electrostatic interactions [12]."
AKAP5 affects KCNH2
| 4 6
AKAP5 binds KCNH2.
| 4 2
PKA binds AKAP5 and KCNH2. 4 / 4
| 4
sparser
"The HERG channel protein, AKAP5, and PKA interacted with each other and appeared to form intracellular complexes."
sparser
"The HERG channel protein, AKAP5, and PKA interacted with each other and appeared to form intracellular complexes."
sparser
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
sparser
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
| 2
reach
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
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"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
AKAP5 activates KCNH2.
| 4
AKAP5 activates KCNH2. 4 / 4
| 4
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"These results provide evidence for a novel mechanism which AKAP5 anchors PKA to up-regulate the HERG channel protein."
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"These results provide evidence for a novel mechanism which AKAP5 anchors PKA to up-regulate the HERG channel protein."
reach
"AKAP5 anchors PKA to enhance regulation of the HERG channel."
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"AKAP5 anchors PKA to enhance regulation of the HERG channel."
Lidocaine affects KCNH2
| 6 3
| 6 3
sparser
"The effects of all of the studied hERG mutants on the potency of inhibition of I hERG by both ranolazine and lidocaine are summarized in supplementary Tables S1 and S2."
sparser
"Lidocaine inhibited hERG current in a concentration-dependent manner at 0.3-1 000 μmol·L(-1), the IC(50) value was 88.63 ±7.99 μmol·L(-1)."
reach
"Lidocaine inhibited hERG current in a concentration dependent manner at 0.3-1 000 mumol.L (-1), the IC (50) value was 88.63 +/-7.99 mumol.L (-1)."
sparser
"The IC 50 for outward I hERG tail inhibition by lidocaine in 4 mM [K + ] e was 141.77 ± 9.81 μM ( h  = 0.98 ± 0.07), with an IC 50 for inward I hERG in high [K + ] e increased to 735.32 ± 54.03 μM ( h  = 0.82 ± 0.05)."
reach
"Thus, flecainide inhibits hERG currents by 81% at 10mum and lidocaine inhibits hERG by 25% at 100 muM."
sparser
"The IC 50 for inhibition of Y652A I hERG by lidocaine was 554.33 ± 34.03 μM ( h  = 0.95 ± 0.06), ~ 3.8-fold the corresponding value for WT hERG."
sparser
"The effect of Y652A on I hERG inhibition by ranolazine and lidocaine is shown in xref C and D (with the standard voltage protocol used for WT I hERG )."
sparser
"However, lidocaine inhibited hERG current in a frequency-dependent manner."
reach
"However, lidocaine inhibited hERG current in a frequency dependent manner."
DauA affects KCNH2
| 9
DauA inhibits KCNH2.
| 7
DauA inhibits KCNH2. 7 / 7
| 7
reach
"In the fully activated I - V relationships, where the full conductance of the HERG channels was induced, Dau inhibited I HERG ~ 40% even at a hyperpolarizing potential of -100 mV."
reach
"Because Dau inhibits I Ca, I Ks, I Kl and HERG, the effect would result in a lengthening of the refractory period and a decrease of cardiac excitability, thus contributing to its anti-arrhythmic effects.We showed that I HERG block occurred rapidly to reach a steady-state level within 1-3 min."
reach
"HERG channel may be one of the key target sites explaining both the therapeutic effects and the potential cardiotoxicity with these herbs.In summary, we have shown that Dau directly blocks HERG channels in the open and inactivated state."
reach
"Taken together, Dau inhibits HERG channels predominantly in the open and inactivated state rather than in the closed state.In this study, we have examined the pharmacological effects of Dau on the electrophysiology of cloned HERG potassium channels."
reach
"We found that Dau directly inhibited I HERG in a concentration dependent manner with an IC 50 of 3.5 muM, indicating that Dau has the potential to induce APD prolongation."
reach
"We found that Dau inhibits I HERG in the open and inactivated states and induces a marked shift of HERG activation curves towards more negative potentials.Experiments were performed on a HEK293 cell line that stably expressing HERG gene (purchased from Avian Company, Canada)."
reach
"Dau inhibits HERG encoded potassium channels and this action might be a molecular mechanism for the previously reported APD prolongation with this drug."
DauA binds KCNH2.
| 2
| 2
reach
"These findings suggested that Dau binds to HERG channels that are in the inactivated state.In clinical practice, for the treatment of arrhythmias, the usual oral daily dosage range of Dau is 150-900 mg."
reach
"These results suggest that Dau binds to HERG channels that are in the open state."
Chaperones affects KCNH2
| 9
sparser
"We first chose the cardioprotective drug, resveratrol, which was used to correct trafficking defect caused by arsenic trioxide via acceleration of interaction between hERG and chaperones, and alleviation of ER stress. xref In addition, resveratrol shortened APD 50 and APD 90 recorded in freshly isolated guinea pig ventricular myocytes by inhibition of I ca-L and restoration of I kr when co-incubated with arsenic trioxide."
sparser
"Furthermore, forward trafficking was disrupted by impaired channel folding associated with altered interactions between hERG proteins and chaperones."
sparser
"Data suggest that pharmacological chaperones bind to the high affinity drug-binding site in the Kv11.1 pore to stabilize Kv11.1 channel conformations suitable for ER export into the secretory pathway ( xref ; xref ; xref ; xref ; xref )."
sparser
"The forward trafficking disruption was caused by impaired channel folding, which was associated with changes in the interactions between hERG proteins and chaperones."
sparser
"Our findings suggested that the forward trafficking disruption was caused by the impairment of channel folding, which was associated with the changes in the interactions between hERG proteins and chaperones."
sparser
"These findings suggested that DHB-induced hERG trafficking defect results from protein misfolding, which may due to the reduction of Hsp90 expression and the aberrant interaction between hERG protein and molecular chaperones."
sparser
"The relative band density of 135 kDa hERG signal identified by anti-Hsp70 antibodies over that identified by an anti-hERG antibody was determined to indicate the changes of interactions between hERG and chaperones."
sparser
"Quantitative RT-PCR, Western blot analysis, immunofluorescence and co-immunoprecipitation methods were used to determine the effects of mitragynine on hERG1a/1b expression and hERG1-cytosolic chaperones interaction."
| 1
sparser
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
TEA affects KCNH2
| 1 8
TEA inhibits KCNH2. 9 / 9
| 1 8
reach
"Both K + channel blockers, 4-AP and TEA, significantly inhibited the proliferation of Eag and HERG positive SK-OV-3 cells, confirming data by Zhanping et al., on the A2780 ovarian cancer line [XREF_BIBR]."
reach
"Like other voltage gated K + channels, HERG channels are blocked by internal TEA (Smith et al. 1996)."
reach
"On average, 30 mM TEA inhibited the tail currents of hERG channels by 36% +/- 4% (n = 14; Fig. 1 A)."
sparser
"Both TEA and 4-AP are non selective K + channel blockers capable of inhibiting Eag and HERG as well as other voltage gated K + channels."
reach
"EAG channels have been described as channels with low sensitivity to classical channel blockers like tetraethylammonium (TEA) or 4-amino-pyridine or the HERG blocker E4031 [15,21]."
reach
"The ratio of the inactivation rate in the absence of QA (k inact -QA) to the inactivation rate in the presence of QA at its K i value (k inact + QA) is presented in Fig. 4 B. Small QAs such as TMA slowed hERG channel inactivation like TEA although its effect was about half that of TEA."
reach
"However, TEA containing external solutions are known to inhibit hERG channel inactivation (50), making that possibility less likely in our experiments."
reach
"Because external TEA + slows fast closing of HERG channels at positive potentials, this closing has been considered analogous to C-type inactivation."
reach
"Application of external TEA slows the kinetics of HERG inactivation, as though channels can not inactivate when TEA is bound."
SRC affects KCNH2
| 1 1 8
SRC activates KCNH2.
| 4
SRC activates KCNH2. 4 / 4
| 4
reach
"The hERG current was decreased by an EGFR inhibitor (AG556) and a broad-spectrum inhibitor of Src family tyrosine kinases (PP2) XREF_BIBR."
reach
"It is unknown whether this opposite regulatory effect of Kir2.1 channels by PTKs is due to different expression systems, cell types and/or experimental conditions.Both EGFR kinase and Src related kinases modulate the alpha-subunit hERG current of human cardiac I Kr [17]."
reach
"These results suggest that reduction of cardiac I hERG.tail by AG556 is likely mediated by EGFR kinase.The Src family kinase inhibitor PP2 was applied to determine whether Src family kinases modulate hERG current."
reach
"First, we show that tyrosine kinase inhibitor, PP1, and the selective Src inhibitory peptide, Src40-58, reduce the hERG current amplitude, without altering its voltage dependence or kinetics."
SRC inhibits KCNH2.
| 1 3
SRC inhibits KCNH2. 3 / 3
| 1 3
reach
"A Src family kinase inhibitor (PP2) and an EGFR kinase inhibitor (AG556) modulated hERG XREF_BIBR, but only the EGFR inhibitor regulated hEAG1 XREF_BIBR."
reach
"We found that the broad-spectrum PTK inhibitor genistein (30 microM), the selective EGFR (epidermal growth factor receptor) kinase inhibitor AG556 (10 microM) and the Src family kinase inhibitor PP2 (10 microM) remarkably inhibited hERG channel current (I (hERG)), and the effects were significantly countered by the protein tyrosine phosphatase (PTP) inhibitor orthovanadate (1 mM)."
reach
"The Src family kinase inhibitor PP2, but not the PTK-inactive analogue PP3, reversibly suppressed hERG channels, and the effect was significantly antagonized by the PTP inhibitor orthovanadate."
SRC phosphorylates KCNH2.
| 1 1
SRC phosphorylates KCNH2 on tyrosine. 1 / 1
| 1
reach
"These results indicate that the membrane protein of hERG channels is phosphorylated by EGFR kinase and Src tyrosine kinases.The potential PTK phosphorylation sites were predicted with the software NetPhos 2.0 (www.cbs.dtu.dk/cgi-bin)."
SRC phosphorylates KCNH2. 1 / 1
| 1
sparser
"We do not know which site(s) in hERG were phosphorylated by Src and affected by the Src inhibitors."
KCNH2 affects chaperones
| 9
sparser
"We first chose the cardioprotective drug, resveratrol, which was used to correct trafficking defect caused by arsenic trioxide via acceleration of interaction between hERG and chaperones, and alleviation of ER stress. xref In addition, resveratrol shortened APD 50 and APD 90 recorded in freshly isolated guinea pig ventricular myocytes by inhibition of I ca-L and restoration of I kr when co-incubated with arsenic trioxide."
sparser
"Furthermore, forward trafficking was disrupted by impaired channel folding associated with altered interactions between hERG proteins and chaperones."
sparser
"Data suggest that pharmacological chaperones bind to the high affinity drug-binding site in the Kv11.1 pore to stabilize Kv11.1 channel conformations suitable for ER export into the secretory pathway ( xref ; xref ; xref ; xref ; xref )."
sparser
"The forward trafficking disruption was caused by impaired channel folding, which was associated with changes in the interactions between hERG proteins and chaperones."
sparser
"Our findings suggested that the forward trafficking disruption was caused by the impairment of channel folding, which was associated with the changes in the interactions between hERG proteins and chaperones."
sparser
"These findings suggested that DHB-induced hERG trafficking defect results from protein misfolding, which may due to the reduction of Hsp90 expression and the aberrant interaction between hERG protein and molecular chaperones."
sparser
"The relative band density of 135 kDa hERG signal identified by anti-Hsp70 antibodies over that identified by an anti-hERG antibody was determined to indicate the changes of interactions between hERG and chaperones."
sparser
"Quantitative RT-PCR, Western blot analysis, immunofluorescence and co-immunoprecipitation methods were used to determine the effects of mitragynine on hERG1a/1b expression and hERG1-cytosolic chaperones interaction."
| 1
sparser
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
| 9
| 8
reach
"Ketoconazole directly blocked the hERG channel current and reduced the amount of hERG channel protein trafficked to the cell surface in a concentration dependent manner."
reach
"For example, the antiarrhythmic agents ketoconazole and fluoxetine have been shown to reduce hERG density by at least 50% following 48 hours of treatment, XREF_BIBR - XREF_BIBR whereas pentamidine and probucol reduce cell-surface hERG without affecting ion conduction."
reach
"Recent studies demonstrated that ketoconazole prolonged the QT not only through direct blockade of the IKr, but also by reducing the density (number of) of HERG potassium channels in the cell membrane."
reach
"Several studies suggest that ketoconazole inhibits hERG preferentially in the closed state (14,16)."
reach
"These properties are compared with four known HERG channel blockers including verapamil, cisapride, ketoconazole and dofetilide in the XREF_TABLE."
reach
"The much lower ketoconazole block of hERG at negative potentials indicates that ketoconazole binds less to hERG closed state than open and inactivated ones.In this study, we described the biophysical properties of a rolf-hERG S3-S4 chimera."
reach
"The mechanism of hERG inhibition by ketoconazole remains controversial (14-16)."
reach
"For example, ketoconazole was initially suggested inhibit hERG without a requirement for prior channel activation (Dumaine et al., 1998), but more recently it has been found to bind with a dependency on S6 aromatic amino-acid residues (and hence to be contingent upon channel gating; Ridley et al., 2006a; Takemasa et al., 2008)."
reach
"Two arguments suggest that the binding of ketoconazole to hERG is not modified by the S3-S4 substitution."
Tamoxifen affects KCNH2
| 2 6
| 6
reach
"This study demonstrates that HERG potassium channels are blocked by the antiestrogenic drug tamoxifen."
reach
"Tamoxifen and endoxifen inhibited the hERG channel protein trafficking to the plasma membrane in a concentration dependent manner with endoxifen being more potent than tamoxifen."
reach
"Tamoxifen and endoxifen inhibited hERG tail currents at -50 mV in a concentration dependent manner with IC50 values of 1.2 and 1.6 muM, respectively."
reach
"These results indicated that tamoxifen and endoxifen inhibited the hERG current by direct channel blockage and by the disruption of channel trafficking to the plasma membrane in a concentration dependent manner."
reach
"Tamoxifen blocked HERG potassium channels with an IC (50) value of 45.3 microM."
reach
"It is worth recalling here that Tamoxifen (one of the most used drugs for BC treatment) was shown to block hERG1 currents [XREF_BIBR], a fact that could explain the QT interval elongation observed in Tamoxifen treated patients."
| 2
sparser
"Tamoxifen and endoxifen inhibited the hERG channel protein trafficking to the plasma membrane in a concentration-dependent manner with endoxifen being more potent than tamoxifen."
sparser
"For example, the hERG inhibitory activity of dactinomycin from cytotoxic antibiotics and tamoxifen from endocrine therapy had been validated by in vitro assays. xref , xref Tamoxifen inhibited hERG at −50mV in a concentration-dependent manner with IC 50 value of 1.2 μM. xref Dactinomycin markedly reduced the hERG mRNA levels as well. xref Moreover, amsacrine, an antineoplastic agent used in acute lymphoblastic leukemia, had been confirmed to block hERG in HEK 293 cells with IC 50 values of 209.4 nM. xref Finally, we computationally identified multiple novel hERG blockers by deephERG, such as picamycin and bleommycin."
| 8
Rosuvastatin inhibits KCNH2.
| 3
| 3
reach
"Rosuvastatin blocks hERG current and prolongs cardiac repolarization."
reach
"The results showed that rosuvastatin reduced hERG currents by accelerating the inactivation and prolonged action potential duration (APD) in hiPSC-CMs."
reach
"Since chemical structure of rosuvastatin is similar to that of several IKr blockers (ibutilide and E-4031), the present study aimed to reveal the mechanism that underlies rosuvastatin induced hERG current reduction and to evaluate the possibility of cardiac toxicity."
Rosuvastatin decreases the amount of KCNH2.
| 3
Rosuvastatin decreases the amount of KCNH2. 3 / 3
| 3
reach
"In conclusion, Rosuvastatin reduced the expression of hERG plasma membrane by two pathways, the first is to disrupt the transport of immature hERG channels to the membrane, and the second is to increase the degradation of mature hERG channels."
reach
"These results indicated that rosuvastatin could potentially inhibit transcription and reduce hERG mRNA expression."
reach
"Meanwhile, it was observed that rosuvastatin reduced the expression of the mature hERG."
Rosuvastatin increases the amount of KCNH2.
| 1
Rosuvastatin increases the amount of KCNH2. 1 / 1
| 1
reach
"These results indicated that rosuvastatin could potentially inhibit transcription and reduce hERG mRNA expression."
Rosuvastatin activates KCNH2.
| 1
| 1
reach
"Transcription factor Sp1 was involved in hERG protein downregulation induced by rosuvastatin, and the result was verified by Sp1 siRNA and Sp1 agonist epicatechin."
Pimozide affects KCNH2
| 8
Pimozide inhibits KCNH2.
| 7
| 7
reach
"The IC 50 value for pimozide block of peak HERG tail currents measured 18.1 nM (13.7-23.9 nM, 95% C.L., Fig. 1B)."
reach
"Pimozide also inhibits hERG (human Ether-a-go-go-related) K + -Channel (Kongsamut et al., 2002)."
reach
"These results suggest that pimozide inhibits HERG with high affinity and is selective for this channel relative to other human cardiac K + channels.Pimozide has been shown to prolong the QT interval and may be associated with torsades de pointes type ventricular arrhythmia (Fulop et al., 1987; Krahenbuhl et al., 1995; Desta et al., 1999)."
reach
"Haloperidol, pimozide, and fluspirilene inhibited HERG current with IC (50) of 1.36, 1.74, and 2.34 microM, and maximal block of 73%, 76% and 65%, respectively."
reach
"However, with up to 5 muM testosterone and up to 12 hr of incubation, enough oocytes with acceptable membrane properties (input resistance of no less than 2 x 10 5 Omega at -80 mV) were available.Application of any of the three antipsychotic drugs, haloperidol, pimozide, or fluspirilene, to the control HERG expressing oocytes non treated with the hormone produced a dose dependent inhibition of HERG current with effective concentration ranges between 0.1 muM and 30 muM for all of them."
reach
"Using patch clamp electrophysiology, we found that pimozide was a potent inhibitor of HERG displaying an IC (50) value of 18 nM."
reach
"Pimozide and sertindole, for example, have previously been shown to block HERG in the low nanomolar range (Rampe et al., 1998; Kang et al., 2000)."
Pimozide activates KCNH2.
| 1
| 1
reach
"During prolonged depolarizing pulses to +20 mV, pimozide was shown to enhance the rate of HERG current decay suggesting some interaction with an activated state of the channel."
Mexiletine affects KCNH2
| 8
| 8
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"With regard to our data and in accordance to the literature, we can speculate that the low documented cardiotoxicity of mexiletine could be due to the fact that mexiletine inhibition of I NaL may counteract any simultaneous prolongation of the QT interval induced by the block of I Kr / hERG channel."
reach
"In our study, the IC 50 for hERG inhibition by mexiletine was 2.5 greater than that for blocking hNav1.4 in the myotonia like condition (43 versus 17muM, respectively)."
reach
"Ivabradine, ajmaline and mexiletine inhibited KCNH2 channel currents significantly, which may underlie their APD prolonging effects."
reach
"Voltage- and time dependent block of hERG channel by mexiletine and MHM."
reach
"Given these observations, we conclude that mexiletine blocks the hERG channel preferentially in an open state, with features similar to those of other open-channel blockers, for example, miconazole, mesoridazine, and ketanserin."
reach
"Inhibition of hERG potassium channel by the antiarrhythmic agent mexiletine and its metabolite m-hydroxymexiletine."
reach
"Finally, in the light of our results, it is important to observe that, even though our data show that mexiletine inhibits hERG at physiologically relevant concentration, mexiletine has not been documented to significantly affect cardiac repolarization (normal QT-interval in the ECG) and is generally a drug well tolerated in man at low doses."
reach
"Our data show that mexiletine inhibits hERG in a time- and voltage dependent manner, with an IC 50 of 3.7 +/-0.7 mumol/L."
Gate affects KCNH2
| 8
Gate activates KCNH2. 8 / 8
| 8
reach
"This would place the gate more than one helical turn below that described in Kir3.4 (24) and Shaker (11,12) channels and is consistent with previous predictions of hERG activation gate architecture (18)."
reach
"This suggests that the structure of the hERG activation gate and its coupling to the voltage sensing unit is different from that in Kv channels such as Shaker."
reach
"Subsequent studies showed that cross linking of cysteine residues engineered at D540 in the S4-S5 linker and L666 in the distal S6 segment stabilized the closed conformation of the hERG activation gate."
reach
"This is of principal interest, because hERG channels are targeted by many pharmaceutical agents, the majority of which block by entering the pore via the intracellular activation gate and are limited by the unusually slow opening of the pore gate."
reach
"Most likely, the activation gate in the HERG channel is similar to the activation gate in the Kv channels, because the HERG activation gate can trap intracellular blockers in a similar manner to the activation gate in Kv channels."
reach
"Here, we define the location of the hERG activation gate by introducing a proline induced kink at positions along the length of the inner S6 helix from, Ile 655 to Tyr 667."
reach
"This ligand and receptor model implies that when S4-S5 L is absent, the hERG activation gate should be in the open state, independent of the potential, as observed in one potassium 22 and one sodium 23 bacterial channels."
reach
"Based upon the observation that the dependence of binding on the presence of S6 aromatic residues was decreased when inactivation was reduced by the S631A mutation 20, a model was proposed in which high affinity drug coordination requires conformational rearrangements associated with inactivation in addition to opening of the hERG activation gate 20."
Clenbuterol affects KCNH2
| 8
Clenbuterol inhibits KCNH2.
| 5
| 5
reach
"In addition, the hERG channel 's drug binding sites mutant Y652A and F656A abolished clenbuterol mediated hERG reduction and current blockade."
reach
"In the presence of Brefeldin A (BFA), which was used to block hERG channel trafficking to cell membrane, clenbuterol reduced hERG on plasma membrane to a greater extent than BFA alone."
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"Clenbuterol Attenuates hERG Channel by Promoting the Mature Channel Degradation."
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"We found that clenbuterol decreases the mature form of the hERG protein at the cell membrane in a concentration- and time dependent manner, without affecting the immature form."
reach
"Correspondingly, clenbuterol chronic treatment reduced hERG current to a greater extent compared to acute treatment."
Clenbuterol activates KCNH2.
| 2
Clenbuterol activates KCNH2-F656A. 1 / 1
| 1
reach
"HEK 293 cells were transfected with wild type and Y652A or F656A mutants of the hERG channel and treated with clenbuterol."
Clenbuterol activates KCNH2-Y652A. 1 / 1
| 1
reach
"HEK 293 cells were transfected with wild type and Y652A or F656A mutants of the hERG channel and treated with clenbuterol."
Clenbuterol decreases the amount of KCNH2.
| 1
Clenbuterol decreases the amount of KCNH2. 1 / 1
| 1
reach
"In conclusion, clenbuterol reduces hERG channel expression and current by promoting the channel degradation."
Chloroquine affects KCNH2
| 8
Chloroquine inhibits KCNH2.
| 7
| 7
reach
"Our experimental findings and modeling suggest that chloroquine preferentially blocks open HERG channels by cation-pi and pi stacking interactions with Tyr 652 and Phe 656 of multiple subunits."
reach
"As IC 50 values for chloroquine inhibition of both Kir2.1 and hERG seen under our conditions fall within this clinical range, it seems likely that inhibition of both these channel types may contribute to observed QT C interval prolongation."
reach
"Chloroquine can be anticipated also to inhibit KCNH2 encoded hERG channel subunits (which underlie native I Kr) [e.g. XREF_BIBR] and in additional experiments (not shown) we found chloroquine to inhibit WT-hERG channels at overlapping concentrations (IC 50 of 2.18 muM; 95% C.I. 1.98 to 2.39 muM; though, in contrast to Kir2.1, blocking potency of the SQT1 linked N588K hERG mutation was reduced ~ 8.5-fold in our hands; data not shown)."
reach
"The estimated IC 25 -value for chloroquine block of the hERG tail current was 0.3 mug/ml (0.94 muM), the estimated IC 50 -value was 0.8 mug/ml (2.5 muM) and the IC 75 -value for chloroquine block of the hERG tail current was determined to be 2.6 mug/ml (8.11 muM)."
reach
"Chloroquine has been shown to inhibit the hERG K + channels in aconcentration- and time dependent manner [XREF_BIBR]."
reach
"Chloroquine inhibited the hERG tail current also in a concentration dependent manner, with a significant inhibition of tail current observed at concentrations of> = 0.5 mug/ml."
reach
"If multiple ECGs were recorded during chloroquine therapy, the ECG recording which was closest to the time to reach the maximum plasma concentration (T max) of the drug (4-5h after oral administration) was selected, since chloroquine blocks the hERG channel in aconcentration dependent manner and therefore the maximal blocking effect is expected to be at the T max of the drug [XREF_BIBR]."
Chloroquine activates KCNH2.
| 1
| 1
reach
"Chloroquine also slowed the apparent rate of HERG deactivation, reflecting the inability of drug bound channels to close."
Bepridil affects KCNH2
| 8
Bepridil inhibits KCNH2.
| 6
| 5
reach
"When expressed in transfected COS cells, HERG is blocked in a concentration dependent manner by bepridil (EC50 = 0.55 microM), verapamil (EC50 = 0.83 microM), and mibefradil (EC50 = 1.43 microM), whereas nitrendipine and diltiazem have negligible effects."
reach
"HERG is blocked by bepridil (EC50 = 0.55 microM), verapamil (EC50 = 0.83 microM) and mibefradil (EC50 = 1.43 microM), whereas nitrendipine and diltiazem have negligible effects."
reach
"We considered longer term exposure as a possibility since we showed previously that bepridil inhibited hERG trafficking whereas verapamil and vanoxerine did not and we have confirmed these results in this study."
reach
"Bepridil on the other hand blocks both hERG and Cav1.2 currents."
reach
"Of the MICE drugs only bepridil inhibited hERG trafficking following overnight exposure."
Bepridil inhibits KCNH2-D540K. 1 / 1
| 1
reach
"We also show that bepridil block of the HERG mutant D540K, a mutant channel that is unable to trap drugs, is dependent on extracellular potassium, correlates with the permeant ion, and is independent of HERG inactivation."
Bepridil decreases the amount of KCNH2.
| 1
Bepridil decreases the amount of KCNH2. 1 / 1
| 1
reach
"While bepridil and vanoxerine had comparable MICE profiles only bepridil reduced surface expression of wild type hERG following overnight exposure."
Bepridil activates KCNH2.
| 1
| 1
reach
"For example, bepridil appears not to interact with G648, Y652, or V659 and mutation of F656 and/or Y652 only slightly reduced hERG block by fluvoxamine and dronedarone."
| 8
reach
"In summary, our results demonstrate that tetra-n-octylammonium bromide and benzethonium chloride inhibit HERG channel currents in the voltage dependent and use dependent manners."
reach
"The properties of HERG channel inhibition by tetra-n-octylammonium bromide and benzethonium chloride are highly similar to verapamil and cisapride (XREF_TABLE)."
reach
"In this study, we found that benzethonium chloride, domiphen bromide, and tetra-n-octylammonium bromide significantly inhibited hERG channel activity in both the thallium influx assay and the patch clamp experiment."
reach
"In the present study, the potential mechanisms for HERG channel inhibition by tetra-n-octylammonium bromide and benzethonium chloride, two most potent HERG channel inhibitors found among the QACs examined, were studied using whole-cell patch clamp experiments in a CHO cell line stably expressing HERG channels."
reach
"Our data indicated that tetra-n-octylammonium bromide blocks HERG channels in both open and inactivated states (XREF_FIG), whereas benzethonium chloride preferentially blocks HERG channels in the open states."
reach
"Concentration dependent inhibition of HERG channel by tetra-n-octylammonium bromide and benzethonium chloride."
reach
"Use dependent inhibition of HERG channels by tetra-n-octylammonium bromide and benzethonium chloride."
reach
"The study of mechanism of HERG channel inhibition by tetra-n-octylammonium bromide and benzethonium chloride can provide additional insight of structure activity relationship of HERG channel inhibition and the molecular determinants of the interaction between the compounds and HERG channel proteins."
NEDD4 affects KCNH2
| 6 2
NEDD4 binds KCNH2.
| 5 1
| 4 1
sparser
"The biochemical interactions between hERG1 and Nedd4-2 were investigated by co-immunoprecipitation experiments ( Fig. 3 )."
sparser
"To confirm the down-regulation of the functional form of hERG1 by Nedd4-2, we quantified the amount of hERG1 localized at the plasma membrane by cell surface biotinylation assays."
sparser
"As shown in Fig. 3 C, a specific signal for Nedd4-2 was found when ERG1 was immunoprecipitated, thus indicating an interaction between ERG1 and Nedd4-2 in the guinea pig heart."
sparser
"Here, we provide evidence of an interaction between hERG1 and Nedd4-2 in guinea pig hearts, suggesting that ubiquitylation of the channel by this ubiquitin ligase could play a role in its regulation in vivo and hence to the regulation of the cardiac AP duration ."
reach
"It is possible that several PY motifs of hERG1 interact with several WW domains of Nedd4-2 simultaneously.We also demonstrated that WWP2, but not Nedd4-1, interacts with hERG1."
PKC binds KCNH2 and NEDD4. 1 / 1
| 1
sparser
"The increase in hERG protein was associated with PKC-induced phosphorylation (inhibition) of Nedd4-2, an E3 ubiquitin ligase that mediates hERG degradation."
NEDD4 ubiquitinates KCNH2.
| 1 1
NEDD4 ubiquitinates KCNH2. 2 / 2
| 1 1
sparser
"These results suggest that ubiquitylation of the hERG1 protein by Nedd4-2, and its subsequent down-regulation, could represent an important mechanism for modulation of the duration of the human cardiac action potential."
reach
"Nedd4, in association with caveolin-3 (Cav3), binds and ubiquitinates hERG channels, targeting them for degradation [XREF_BIBR]."
MK-499 affects KCNH2
| 8
MK-499 inhibits KCNH2. 6 / 6
| 6
reach
"The mean channel open times at -90 mV were 2.9 +/- 0.5 and 11.8 +/- 1.0 ms, and the mean channel closed times were 0.54 +/- 0.02 and 14.5 +/- 5.3 ms. Single HERG channels were blocked by MK-499, a class III antiarrhythmic agent that blocks I (Kr) in cardiac myocytes."
reach
"However, MK-499 did block HERG current if oocytes were repetitively pulsed, or clamped at a voltage positive to the threshold potential for channel activation."
reach
"1 For example, calcium activated IKCa1 channels are blocked by TRAM-34, 2 HERG1 is blocked by MK-499, 3 and voltage gated channels are blocked by bupivacaine."
reach
"Under steady state conditions, block of HERG by MK-499 was half maximal at 123 +/- 12 nmol/L at a test potential of -20 mV."
reach
"However, neither E-4031 nor MK-499 at a concentration of 1 IIM blocked HERG current, even after the incubation of the oocytes for up to 4 hr in these drugs."
reach
"Using the hERG1 D540K mutant that has the unusual property of opening in response to hyperpolarization, they confirmed that MK-499 blocked the hERG1 channel in the inner vestibule, as MK-499 was trapped by closure of the activation gate."
MK-499 inhibits KCNH2. 1 / 1
| 1
reach
"Astemizole, terfenadine, cisapride, and MK-499 inhibited cERG and human ERG (hERG) currents with IC (50) values of 1.3, 13, 19, and 15 nM and 1.2, 9, 14, and 21 nM, respectively, and competitively displaced [(35) S] MK-499 binding from cERG and hERG with IC (50) values of 0.4, 12, 35, and 0.6 nM and 0.8, 5, 47, and 0.7 nM, respectively."
MK-499 inhibits KCNH2-D540K. 1 / 1
| 1
reach
"WT and D540K HERG channels were blocked by MK-499 in a concentration dependent manner (XREF_FIG)."
L. erythrocarpa affects KCNH2
| 8
L. erythrocarpa inhibits KCNH2. 8 / 8
| 8
reach
"These findings indicate that HERG channels are also greatly blocked by BuOH fraction of L. erythrocarpa while remaining at the holding potential."
reach
"These findings indicate that HERG channels are greatly blocked by H 2 O fraction of L. erythrocarpa at the holding potential."
reach
"Consistent results were that L. erythrocarpa blocks HERG channel at the holding potential rather than at the depolarizing pulse (XREF_FIG)."
reach
"We found that L. erythrocarpa blocked the HERG channel, resulting in a shift in voltage-dependence of channel activation and reduction of maximum conductance (g max)."
reach
"Although it has not been reported that L. erythrocarpa prolongs the APD or induces cardiac arrhythmia to our knowledge, our results suggest that L. erythrocarpa blocks the HERG channel, a major component of the I Kr, which could make the heart prone to arrhythmia since I Kr is one of the targets for antiarrhythmic therapy and the blocking of this current is expected to increase the APD and thereby increase the refractory period."
reach
"Voltage dependent HERG channel blockade by L. erythrocarpa."
reach
"In conclusion, we have shown here that L. erythrocarpa blocks HERG channel, resulting in a shift of voltage-dependence of channel activation and reduction of g max, and that the H 2 O and BuOH fractions exhibits the strongest changes in V 1/2 and g max among the solvent fractions."
reach
"Fraction dependent inhibition of HERG channels by L. erythrocarpa."
KCNH2 affects sodium atom
| 8
| 5
reach
"Our studies of the Na + o interaction with HERG began with attempts to understand the anti-Nernstian effect of K + o and suggested that K + o acts to potently relieve inhibition of outward HERG K + current by Na + o."
reach
"Although such effects could be consistent with a mechanism in which Na + o preferentially interacts with the HERG inactivated state, the permeability of these mutant channels to Na + limits their utility for studying inhibition of outward HERG K + current by Na + o."
reach
"Here we have focused directly on the interaction between Na + o and HERG, with a view to developing a more precise biophysical understanding of the Na + o effect and thereby illuminating the Na + o -K + o interaction."
reach
"The ability of Na + o to occupy the HERG outer pore as demonstrated in this study does not exclude the possibility that Na + o preferentially interacts with the HERG inactivated state."
reach
"We studied wild-type (WT) and mutant HERG currents and used two strategic probes, intracellular Na + (Na + i) and extracellular Ba 2+ (Ba 2+ o), to define a site where Na + o interacts with HERG."
KCNH2 activates sodium atom.
| 3
| 3
reach
"Na (+) (o) inhibition of HERG current was relieved by physiological [K (+)] (o), while Na (+) (o) speeded recovery from inactivation similarly in the absence or presence of physiological [K (+)] (o)."
reach
"Since hERG inactivation resembles the C-type inactivation of Shaker channels, we proposed that the hERG channel allows Na + to permeate during the inactivation process."
reach
"Whereas hERG channels are highly selective for K +, we have found that inactivated hERG channels allow Na + to permeate in the absence of K +."
KCNH2 affects cell cycle
| 8
KCNH2 inhibits cell cycle.
| 4
| 4
reach
"11 It has also been shown that constitutive inhibition of the hERG1 channel activity can induce cell cycle arrest in G0/G1 phase in several cancer cells."
reach
"Reduced expression of the hERG protein by siRNA transfection resulted in decreased cell proliferation in small cell lung cancer cells [XREF_BIBR], and a hERG channel promoted the proliferation of ovarian cancer cells by affecting the cell cycle [XREF_BIBR]."
reach
"In many tumor cells, HERG channel inhibitors induce antiproliferative properties by retarding the cell cycle progression through a partial block of the cells in the G1 phase of the cell cycle [15,16]."
reach
"It is noteworthy that the hERG blocker erythromycin blocks cell cycle in G2 phase if administered together with vincristine."
KCNH2 activates cell cycle.
| 4
| 4
reach
"Cell cycle analysis further confirmed this observation, indicating that HERG1 siRNA transfection induced cell cycle arrest in the G1 phase with a significant increase in the percentage of cells in this phase (~ 16.7% in PANC-1 and ~ 16.1% in CFPAC-1)."
reach
"HERG1 agonist induces cell cycle arrest in G0/G1 phase."
reach
"HERG1 has also been shown to enhance GC cell invasion and proliferation, induce cell cycle progression in vitro, and promote tumor genesis and growth in vivo."
reach
"11 It also has been shown that inhibition of hERG1 current activity can inhibit proliferation in leukemic cells by promoting cell cycle arrest."
KCNH2 affects PKA
| 4 4
KCNH2 binds PKA.
| 4 2
PKA binds AKAP5 and KCNH2. 4 / 4
| 4
sparser
"The HERG channel protein, AKAP5, and PKA interacted with each other and appeared to form intracellular complexes."
sparser
"The HERG channel protein, AKAP5, and PKA interacted with each other and appeared to form intracellular complexes."
sparser
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
sparser
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
| 2
reach
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
reach
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
KCNH2 activates PKA.
| 2
KCNH2 activates PKA. 2 / 2
| 2
reach
"Although these cells have proven quite useful for studying many types of PKA modulation including HERG XREF_BIBR, K V 1.1 and nicotinic receptors XREF_BIBR, they appear less ideal for studying the modulation of L-type Ca 2+ channels."
reach
"We show that HERG associates with 14-3-3epsilon to potentiate cAMP and PKA effects upon HERG."
KCNH2 affects NEDD4L
2 | 6
KCNH2 binds NEDD4L.
2 | 5
2 | 5
reach
"Here, we provide evidence of an interaction between hERG1 and Nedd4-2 in guinea pig hearts, suggesting that ubiquitylation of the channel by this ubiquitin ligase could play a role in its regulation in vivo and hence to the regulation of the cardiac AP duration."
reach
"As shown in Fig. 3 C, a specific signal for Nedd4-2 was found when ERG1 was immunoprecipitated, thus indicating an interaction between ERG1 and Nedd4-2 in the guinea pig heart.We investigated whether the decrease of I hERG1 could be due to a depletion of hERG1 protein at the plasma membrane."
reach
"The biochemical interactions between hERG1 and Nedd4-2 were investigated by co-immunoprecipitation experiments."
reach
"Our data demonstrate that Cav3, hERG, and ubiquitin-ligase Nedd4-2 interact with each other and form a complex."
reach
"Similar to Nedd4-2, WWP2 but not Nedd4-1 was present in the fraction immunoprecipitated with the anti-hERG1 antibody, when expressed with the WT channel, demonstrating that hERG1 can interact both with Nedd4-2 and WWP2."
biogrid
No evidence text available
biogrid
No evidence text available
KCNH2 inhibits NEDD4L.
| 1
KCNH2 inhibits NEDD4L. 1 / 1
| 1
reach
"We investigated whether a mutation in the PY motif of hERG1 could abolish the Nedd4-2 effect on I hERG1."
FKBP8 affects KCNH2
3 | 1 5
FKBP8 activates KCNH2.
| 4
FKBP8 activates KCNH2. 4 / 4
| 4
reach
"Overexpression of FKBP38 was also able to partially rescue a hERG trafficking mutant, F805C."
reach
"FKBP8 is reported to promote the maturation of HERG channel and cystic fibrosis transmembrane conductance regulator (CFTR) XREF_BIBR, XREF_BIBR."
reach
"Co-chaperone FKBP38 promotes HERG trafficking."
reach
"Additionally, siRNA knock-down of FKBP38 causes a reduction in HERG trafficking and overexpression of wild type FKBP38 partially rescues HERG trafficking in the presence of F805C disease causing KCNH2 mutation XREF_BIBR."
FKBP8 binds KCNH2.
3 |
3 |
biogrid
No evidence text available
biogrid
No evidence text available
biogrid
No evidence text available
FKBP8 inhibits KCNH2.
| 1 1
FKBP8 inhibits KCNH2. 1 / 1
| 1 1
reach
"Additionally, siRNA knock-down of FKBP38 causes a reduction in HERG trafficking and overexpression of wild type FKBP38 partially rescues HERG trafficking in the presence of F805C disease causing KCNH2 mutation XREF_BIBR."
E2 affects KCNH2
| 8
E2 inhibits KCNH2.
| 6
E2 inhibits KCNH2. 4 / 4
| 4
reach
"MD simulations suggest that E2 dissociates rapidly from this site in WT and hence is unlikely to impair function of WT hERG channel."
reach
"Experimental results XREF_BIBR shown in XREF_FIG (top) illustrate that E2 (1 nM) considerably increased the suppression of hERG by E-4031 (light gray line)."
reach
"All this suggests that a presence of E2 can potentially enhance hERG block by dofetilide, and thus enhance its proclivity to promote arrhythmia."
reach
"Our current study reveals the first mechanistic models of how E2 could potentially enhance hERG blockade."
E2 inhibits KCNH2-F656T. 1 / 1
| 1
reach
"(2008) have shown that E2 does not inhibit both F656T and F656M mutant hERG currents, which is in agreement with the theoretical results presented here."
E2 inhibits KCNH2-F656M. 1 / 1
| 1
reach
"(2008) have shown that E2 does not inhibit both F656T and F656M mutant hERG currents, which is in agreement with the theoretical results presented here."
E2 binds KCNH2.
| 2
| 2
reach
"The result of E2 interaction with hERG is an increase in ventricular action potential duration, consistent with the longer QT interval observed in women during the follicular phase of the menstrual cycle."
reach
"An important limitation in the interpretation of structural modes of E2 binding to hERG is an absence of a high-resolution experimental structure of the channel."
CTNNB1 affects KCNH2
| 8
CTNNB1 activates KCNH2.
| 6
CTNNB1 activates KCNH2. 6 / 6
| 6
reach
"Beta-catenin did not alter HERG channel kinetics but apparently increased the HERG protein abundance within the cell membrane."
reach
"As a result, expression of beta-catenin markedly upregulated HERG channel activity, an effect not sensitive to inhibition of transcription with actinomycin D (10 microM)."
reach
"According to chemiluminescence, beta-catenin may increase HERG channel abundance within the oocyte cell membrane."
reach
"Coexpression of beta-catenin Increased HERG Current."
reach
"The results reveal that the coexpression of beta-catenin leads to marked upregulation of HERG activity by enhancing the plasma membrane abundance of the channel protein."
reach
"Stimulation of HERG Channel Activity by beta-catenin."
CTNNB1 increases the amount of KCNH2.
| 2
CTNNB1 increases the amount of KCNH2. 2 / 2
| 2
reach
"As previous studies from Carlos Munoz 's laboratory showed that beta-catenin increased the hERG1 protein levels within the oocyte cell membrane XREF_BIBR, the increased hERG1 channel activity detected in the polyps of Apc min/+ mice could be attributed to the overexpression of beta-catenin, widely described in this animal model XREF_BIBR."
reach
"Beta-catenin Increased the Surface Expression of HERG."
AZA1 affects KCNH2
| 8
AZA1 inhibits KCNH2.
| 7
AZA1 inhibits KCNH2. 7 / 7
| 7
reach
"To determine if AZA1 inhibition of hERG1 current depends on the state of the channel, we compared the time-course of currents recorded during single test pulses applied in the absence of AZA1 and again after a prolonged pulse-free period of AZA1 exposure."
reach
"We propose that AZA1 physically blocks the K + conductance pathway of hERG1 channels by occluding the cytoplasmic mouth of the open pore."
reach
"At a saturating concentration (10 muM), AZA1 reduced the peak outward hERG1 current measured at -10 mV in oocytes to 19.0 +/- 2.4% of control (n = 6)."
reach
"These findings suggest that AZA1 preferentially blocks the open state of hERG1 channels."
reach
"Representative traces and replicated experimental data illustrate that hERG currents were inhibited by AZA1 in a concentration dependent manner with a maximum inhibition of 79.5 +/- 1.8% (mean +/- SEM, n = 3) elicited by 1.9 muM AZA1 (XREF_FIG)."
reach
"The mechanism of hERG channel inhibition by AZA1 was investigated further in Xenopus oocytes where it was shown to be an open state dependent blocker and, using mutant channels, to interact with F656 but not with Y652 within the S6 transmembrane domain that forms the channel 's central pore."
reach
"AZA1 blocks hERG1 channels heterologously expressed in oocytes."
AZA1 binds KCNH2.
| 1
KCNH2 binds AZA1. 1 / 1
| 1
reach
"Relative to vehicle controls, hERG binding by AZA1, AZA2, and AZA3 (10 muM) was reduced to 19.7 +/- 1.4% (n = 2), 22.3 +/- 1.0% (n = 3), and 29.3 +/- 1.6% (n = 3) with IC 50 values of 2.1 muM, 2.6 muM, and 6.6 muM; respectively (XREF_TABLE)."
Trazodone affects KCNH2
| 7
Trazodone inhibits KCNH2.
| 6
| 6
reach
"Trazodone block of HERG channels was state dependent."
reach
"Trazodone inhibited HERG currents in a dose dependent manner with an IC50 of 2.9 microM in HEK cells and 13.2 microM in Xenopus oocytes."
reach
"However, trazodone blocks hERG channels at clinically relevant concentrations and therefore increases the QT duration [XREF_BIBR XREF_BIBR]."
reach
"Inhibition of cardiac HERG potassium channels by the atypical antidepressant trazodone."
reach
"In summary, the atypical antidepressant trazodone blocks cardiac HERG channels at concentrations that are probably relevant in vivo, particularly in overdosage."
reach
"Trazodone inhibited hERG channel current in a concentration dependent manner with an IC50 of 0.69 microM."
Trazodone activates KCNH2.
| 1
| 1
reach
"Trazodone accelerated inactivation of HERG currents without markedly affecting activation."
Taxifolin affects KCNH2
| 7
Taxifolin inhibits KCNH2. 7 / 7
| 7
reach
"In this study, we found that taxifolin glycoside directly inhibits hERG K + currents in a concentration dependent manner, with an EC 50 of 9.6 +/-0.7 microM."
reach
"The present study demonstrated that taxifolin glycoside directly blocks hERG K + channels in hERG-CHO cells."
reach
"We found that taxifolin glycoside directly blocked hERG K + current in a concentration dependent manner (EC 50 = 9.6 +/-0.7 microM)."
reach
"To determine whether taxifolin glycoside would block hERG K + channels, we recorded hERG K + currents using a whole-cell patch clamp technique."
reach
"In conclusion, taxifolin glycoside inhibited hERG K + currents that function by facilitating activation and inactivation process."
reach
"These data indicate that the activation of hERG K + channels was accelerated by taxifolin glycoside and that taxifolin glycoside may block the hERG K + channel when it is open."
reach
"However, taxifolin glycoside of high concentration (more than 100 microM) did not produce further decrease of hERG K + currents."
| 7
| 7
reach
"Sparfloxacin blocked HERG currents half-maximally (IC (50) value) at a concentration of 33.2 microM, whereas norfloxacin and lomefloxacin each tested at a concentration of 300 microM inhibited HERG currents only by 2.8 +/-3.6% and 12.3 +/-4.7%, respectively."
reach
"Ciprofloxacin was found to have little interaction with the HERG channel at concentrations up to 100 mug/ml, whilst sparfloxacin, grepafloxacin and moxifloxacin inhibited HERG currents with IC 50 values of 13, 37 and 41 mug/ml, respectively."
reach
"Sparfloxacin inhibited HERG currents with an EC 50 of 13.5 +/-0.8 mug/ml and n H of 1.3 +/-0.1."
reach
"Bath application of sparfloxacin, moxifloxacin and grepafloxacin produced an inhibition of HERG outward currents at -40 mV with EC (50) of 13.5 +/-0.8, 41."
reach
"Block of HERG by sparfloxacin displayed a positive voltage dependence."
reach
"For example, XREF_SUPPLEMENTARY shows the development of highly asynchronous calcium transients over a 12 seconds recording at 33 Hz of NRVMs stimulated at 2 Hz after T 3 treatment in presence of hERG blocker sparfloxacin (100 microM)."
reach
"The comparison of potencies from grepafloxacin, moxifloxacin, and sparfloxacin to block the HERG channel shows the latter to have the greatest inhibition effect on the HERG current amplitude."
Imipramine affects KCNH2
| 7
| 7
reach
"For example, amitriptyline, imipramine, and doxepin block the HERG channel with the IC 50 s of 10 muM, 3.4 muM, and 6.5 muM, respectively (Cavalli et al., 2002; Duncan et al., 2007)."
reach
"Imipramine blocks several cardiac and neuronal voltage gated and Ca 2+ -activated K + channels as well as EGL-2 channels, hERG channels, neuronal and cardiac Na + channels, and Ca 2+ channels."
reach
"Once maximal channel activation was achieved after 320 ms (as demonstrated by maximal tail currents), further prolongation of depolarization did not increase imipramine mediated HERG channel inhibition."
reach
"Amitriptyline, quinidine, compound A, fluoxetine and imipramine inhibited hERG with IC 50 values (all paired values denote constantly cultured and frozen, respectively) of 4.8 +/- 0.4 and 5.1 +/- 0.4, 1.4 +/- 0.1 and 1.1 +/- 0.1, 24.4 +/- 2.4 and 21.9 +/- 1.8, 2.1 +/- 0.4 and 2.1 +/- 0.1, 5.2 +/- 0.4 and 4.0 +/- 0.2 muM."
reach
"HERG tail currents (IHERG) following test pulses to +20 mV were inhibited by imipramine with an IC50 of 3.4 +/-0.4 microM (mean +/-s.e.mean) and a Hill coefficient of 1.17 +/-0.03 (n = 5)."
reach
"Previously, imipramine has been reported to inhibit I HERG recorded in experiments using a mammalian expression system with an IC 50 of 3.4 muM XREF_BIBR whilst an IC 50 of 10muM was reported for amitriptyline XREF_BIBR."
reach
"Amitriptyline, quinidine, compound A, fluoxetine and imipramine inhibited hERG with IC (50) s (paired values denote constantly cultured and frozen, respectively) of 4.8 +/-0.4 and 5.1 +/-0.4, 1.4 +/-0.1 and 1.1 +/-0.1, 24.4 +/-2.4 and 21.9 +/-1.8, 2.1 +/-0.4 and 2.1 +/-0.1, 5.2 +/-0.4 and 4.0 +/-0.2 muM."
Cholesterol affects KCNH2
| 1 7
Cholesterol inhibits KCNH2.
| 1 3
| 1 3
reach
"A recent study has reported that hERG and KCNQ channels are decreased by cholesterol enrichment via a reduced activity of phosphatidylinositol 4, 5-bisphosphate (PIP2) XREF_BIBR."
reach
"Extraction of cholesterol with MbetaCD indeed inhibited internalisation of HA-hERG hERG in HeLa cells (XREF_FIG) and also of ERG in ventricular myocytes (XREF_FIG)."
reach
"These results suggest that cholesterol enrichment inhibits either endogenous MIC current or exogenous HERG current via the membrane PIP 2 depletion by PLC activation."
Cholesterol decreases the amount of KCNH2.
| 2
Cholesterol decreases the amount of KCNH2. 2 / 2
| 2
reach
"Probucol, a cholesterol lowering drug, induces LQTs by inhibiting the expression of the hERG channel."
reach
"Our data are consistent with the report that probucol, also a cholesterol lowering drug, decreases hERG expression through accelerating cav-1 degradation."
Cholesterol increases the amount of KCNH2.
| 1
Cholesterol increases the amount of KCNH2. 1 / 1
| 1
reach
"Although diverse compounds reduce the hERG current (I (hERG)) by blocking the channel, probucol, a cholesterol lowering drug that causes LQTS, reduces I (hERG) by decreasing plasma-membrane hERG protein expression."
Cholesterol activates KCNH2.
| 1
| 1
reach
"Kv11.1 (ERG1) K+ channels localize in cholesterol and sphingolipid enriched membranes and are modulated by membrane cholesterol."
YWHAE affects KCNH2
3 1 | 2 2 1
YWHAE binds KCNH2.
3 1 | 1 2
3 1 | 1 2
hprd
No evidence text available
sparser
"We show that HERG associates with 14-3-3epsilon to potentiate cAMP/PKA effects upon HERG."
biogrid
No evidence text available
biogrid
No evidence text available
sparser
"We recently identified a novel protein-protein interaction between hERG and the adaptor protein 14-3-3epsilon."
biogrid
No evidence text available
YWHAE activates KCNH2.
| 1 1
YWHAE activates KCNH2. 1 / 1
| 1 1
reach
"However, some literature, including in endothelial cell biology, suggests PPARdelta pathway agonists stimulate expression of YWHAE [XREF_BIBR], whose gene product, 14-3-3 epsilon, activates the HERG channel [XREF_BIBR]."
Ubiquitin affects KCNH2
| 7
Ubiquitin inhibits KCNH2.
| 4
| 4
reach
"Extracellular K + -depletion and high salt or acidity also triggered Ub dependent degradation of the wild-type HERG channel and LDL receptor, respectively, presumably by conformational destabilization [XREF_BIBR, XREF_BIBR]."
reach
"We have previously shown that mature hERG channels are degraded by ubiquitin ligase Nedd4-2 via enhanced channel ubiquitination."
reach
"Ubiquitin dependent recruitment of membrane proteins to lipid rafts has been described previously 81 and could be involved in the ubiquitin dependent degradation of WT-hERG following extracellular K + -depletion 82."
reach
"Our results show that the ubiquitin ligase Nedd4-2 down-regulates I hERG1 measured in a mammalian cell line."
Ubiquitin activates KCNH2.
| 2
| 2
reach
"Mechanistically, our data demonstrate that overexpression of Rab4 increases the expression level of endogenous Nedd4-2, a ubiquitin ligase that targets hERG but not Kv1.5 or EAG channels for ubiquitination and degradation."
reach
"We have previously shown that the E3 ubiquitin (Ub) ligase Nedd4-2 (neural precursor cell expressed developmentally down-regulated protein 4-2) targets the PY motif of hERG channels to initiate channel degradation."
Ubiquitin decreases the amount of KCNH2.
| 1
Ubiquitin decreases the amount of KCNH2. 1 / 1
| 1
reach
"Deletion of the ubiquitin ligase Doa10 or any of the components of the Doa10 complex strongly impaired the degradation of Erg1 expressed from its own promoter (XREF_FIG) or from the heterologous glyceraldehyde-3-phosphate dehydrogenase (GAPDH) promoter (XREF_FIG)."
TRH affects KCNH2
| 7
TRH inhibits KCNH2.
| 4
TRH inhibits KCNH2. 4 / 4
| 4
reach
"TRH reduced the maximal available erg current amplitude by 12% (erg1), 13% (erg2) and 39% (erg3) and accelerated the time course of erg1 and erg2 channel deactivation, whereas erg3 deactivation kinetics were not significantly altered."
reach
"This demonstrates that the presence of the proximal domain sequence between residues 325 and 346 is required for the TRH induced slowing of HERG activation."
reach
"In cells of two tumours tested, thyrotropin releasing hormone significantly reduced the amplitude of the HERG currents."
reach
"Rat erg1 currents recorded in the cell attached configuration were reduced by application of TRH to the extra-patch membrane in the majority of the experiments, confirming the involvement of a diffusible second messenger."
TRH activates KCNH2.
| 3
TRH activates KCNH2. 3 / 3
| 3
reach
"This indicates that maintenance of the consensus site for PKA phosphorylation in the amino-terminus is not necessary for the TRH induced modifications of HERG activation voltage dependence.The shifts in HERG activation kinetics induced by TRH in oocytes have been shown to be minimised by the protein kinase C (PKC) inhibitor GF109203X [13]."
reach
"In addition, coinjection of rat MiRP1 with HERG cDNA did not influence the TRH induced modulation of HERG channels."
reach
"Addition of TRH caused clear modifications of HERG channel gating kinetics."
Proteasome affects KCNH2
| 7
Proteasome inhibits KCNH2.
| 5
| 3
reach
"Most of its mutations give rise to unstable hERG proteins degraded by the proteasome."
reach
"To assess the involvement of proteasome mediated degradation of hERG proteins, we examined the effects of proteasome inhibitors (lactacystin and ALLN) on the steady state protein levels of WT-hERG, G572R-hERG and E637K-hERG."
reach
"7 hERG has been previously identified as an Hsp90 and Hsp70 dependent client protein, and studies have shown that inhibition of Hsp90 with geldanamycin resulted in proteasome mediated degradation of hERG which prevented maturation of a fully functional hERG channel."
Proteasome inhibits KCNH2-A561V. 1 / 1
| 1
reach
"Our preliminary test results showed that the HERG A561V mutant protein was degraded by proteasome pathway."
Proteasome inhibits mutated KCNH2. 1 / 1
| 1
reach
"When expressed in HEK293 cells, this mutant hERG FLAG was degraded by the proteasome and failed to be transported to the cell surface."
Proteasome ubiquitinates KCNH2.
| 1
Proteasome ubiquitinates KCNH2. 1 / 1
| 1
reach
"The homologue of Erg1 in mammals, SM, is ubiquitinated and degraded by the proteasome."
Proteasome deubiquitinates KCNH2.
| 1
Proteasome leads to the deubiquitination of KCNH2. 1 / 1
| 1
reach
"We found that proteasome inhibition increases levels of hERG poly-ubiquitination and to a greater extent for G572R-hERG or E637K-hERG than WT-hERG (XREF_FIG)."
MYC affects KCNH2
| 2 5
MYC decreases the amount of KCNH2.
| 2
MYC decreases the amount of KCNH2. 2 / 2
| 2
reach
"Here, we demonstrate through electrophysiology techniques and immunochemistry, that both N-terminal and C-terminal myc fusion tags may perturb hERG protein channel expression and kinetics of the I Kr current."
reach
"Here, we demonstrate through electrophysiology techniques and immunohistochemistry, that both N-terminal and C-terminal myc fusion tags may perturb hERG protein channel expression and kinetics of the I Kr current."
MYC binds KCNH2.
| 2
| 1
sparser
"Thus, rMinK and rMiRP1 could each assemble with HERG-cmyc."
KCNE1 binds KCNE2, KCNH2, and MYC. 1 / 1
| 1
sparser
"To compare the binding of MinK and MiRP1 to HERG-cmyc, an assay was performed using 35 S-labeled MinK and MiRP1 subunits synthesized in vitro."
MYC inhibits KCNH2.
| 1
MYC inhibits KCNH2. 1 / 1
| 1
reach
"C-Terminal Myc Tag does not affect total protein expression, but modestly decreases hERG channel trafficking."
MYC increases the amount of KCNH2.
| 1
MYC increases the amount of KCNH2. 1 / 1
| 1
reach
"Both the N-terminal myc tag and the double mutations cause an increase in the hERG protein expression that may have corrected for the decrease in total protein expression caused by the D219V mutation."
MYC activates KCNH2.
| 1
MYC activates KCNH2. 1 / 1
| 1
reach
"Although there were significant changes caused by the C-terminal-myc fusion tag, the changes were less severe than the changes in hERG function and protein expression caused by the N-terminal myc fusion tag."
MTX1 affects KCNH2
| 2 5
MTX1 activates KCNH2. 7 / 7
| 2 5
reach
"MTX increased both step and tail hERG currents with EC (50) values of 0.34 and 0.52 microM, respectively."
sparser
"We conclude that MTx and KB130015 synergically activate hERG1 channels, requiring the existence of at least two functionally coupled activator sites."
reach
"In addition, MTX increased hERG deactivation time constants."
reach
"Similar to KB130015, mallotoxin (MTx) activates the hERG1 channel by shifting its voltage dependence to the left and by accelerating activation."
reach
"In conclusion, MTX activates hERG channels through distinct mechanisms and with significantly higher potency than previously reported hERG channel activators."
sparser
"In conclusion, MTX activates hERG channels through distinct mechanisms and with significantly higher potency than previously reported hERG channel activators."
reach
"We conclude that MTx and KB130015 synergically activate hERG1 channels, requiring the existence of at least two functionally coupled activator sites."
KCNH2 affects wave
| 7
KCNH2 inhibits wave.
| 6
KCNH2 inhibits wave. 6 / 6
| 6
reach
"In addition to causing significant concentration dependent QTc prolongation, pure hERG potassium channel block (dofetilide) caused concentration dependent T wave flatness, asymmetry, and notching (see XREF_FIG for ECG examples), consistent with ECG findings from LQT2 patients (abnormal hERG potassium channel)."
reach
"Pure hERG block (dofetilide) and strong hERG block with lesser calcium and late sodium block (quinidine) caused substantial T wave morphology changes (P < 0.001)."
reach
"Hua et al XREF_BIBR showed that 6-fold overexpression of native hERG eliminates T wave alternans in isolated canine ventricular myocytes and in computer simulations."
reach
"Strong calcium and hERG block (verapamil) did not cause T wave morphology changes."
reach
"Strong late sodium current and hERG block (ranolazine) still caused T wave morphology changes (P < 0.01)."
reach
"This study observed that pure hERG potassium channel block with dofetilide causes substantial concentration dependent T wave flatness, asymmetry, and notching, along with a decrease in the maximum magnitude of the T vector."
KCNH2 activates wave.
| 1
KCNH2 activates wave. 1 / 1
| 1
reach
"To date, in patients with LQT2, the majority of mutations in hERG increase the transmural dispersion of repolarization and eventually induce prolongation of the QT interval, a notched T wave, re-entry and TdP."
KCNH2 affects miR-96
| 7
KCNH2 activates miR-96. 7 / 7
| 7
reach
"HERG1 is a direct target of miR-96."
reach
"Collectively, these data suggest that HERG1 is a direct target of miR-96 in pancreatic cancer cell lines."
reach
"Based on these findings, we hypothesized that HERG1 might be a direct target of miR-96."
reach
"Previous results have verified that HERG1 is a direct target of miR-96 and therefore we wanted to further assess the biological role of miR-96 in pancreatic cancer cell lines."
reach
"HERG1 was an important target of miR-96."
reach
"This result indicates that miR-96 can suppress the HERG1 expression in vivo and further demonstrates that HERG1 is a direct target of miR-96."
reach
"Next, we wanted to examine whether HERG1 is a direct target of miR-96."
KCNH2 affects gate
| 7
KCNH2 activates gate. 7 / 7
| 7
reach
"This ligand and receptor model implies that when S4-S5 L is absent, the hERG activation gate should be in the open state, independent of the potential, as observed in one potassium 22 and one sodium 23 bacterial channels."
reach
"Here, we define the location of the hERG activation gate by introducing a proline induced kink at positions along the length of the inner S6 helix from, Ile 655 to Tyr 667."
reach
"This suggests that the structure of the hERG activation gate and its coupling to the voltage sensing unit is different from that in Kv channels such as Shaker."
reach
"Based upon the observation that the dependence of binding on the presence of S6 aromatic residues was decreased when inactivation was reduced by the S631A mutation 20, a model was proposed in which high affinity drug coordination requires conformational rearrangements associated with inactivation in addition to opening of the hERG activation gate 20."
reach
"Most likely, the activation gate in the HERG channel is similar to the activation gate in the Kv channels, because the HERG activation gate can trap intracellular blockers in a similar manner to the activation gate in Kv channels."
reach
"This would place the gate more than one helical turn below that described in Kir3.4 (24) and Shaker (11,12) channels and is consistent with previous predictions of hERG activation gate architecture (18)."
reach
"Subsequent studies showed that cross linking of cysteine residues engineered at D540 in the S4-S5 linker and L666 in the distal S6 segment stabilized the closed conformation of the hERG activation gate."
| 2 5
| 4
| 3
reach
"These results suggest that trafficking deficient G572R-hERG and E637K hERG mutant proteins can activate ER stress pathways and are targeted to the proteasome for degradation."
reach
"We demonstrated that trafficking deficient G572R-hERG and E637K hERG mutant proteins activate ER stress pathways and target the proteasome for degradation."
reach
"Since Calnexin and Calreticulin are chaperone proteins with important regulatory roles in the ER quality control pathways, we want to test whether the trafficking deficient G572R-hERG and E637K hERG mutants can activate ER stress responses."
| 1
reach
"Coexpression of I593R HERG with wild-type HERG also results in ER stress pathway activation."
sparser
"Coimmunoprecipitation assays showed that Calnexin only interacted with the ER-residing form of hERG proteins ( xref ), suggesting that Calnexin interacts with hERG proteins in the ER."
sparser
"Coimmunoprecipitation assays showed that Calnexin only interacted with the ER-residing form of hERG proteins ( xref ), suggesting that Calnexin interacts with hERG proteins in the ER."
reach
"Blockers of hERG channels somehow rescue the channels stuck in the ER, resulting in incorporation in the plasma membrane."
KCNH2 affects cisapride
| 7
KCNH2 inhibits cisapride.
| 4
| 4
reach
"These results indicate that cisapride produced anti-hypertrophic effects in neonatal rat ventricular cells.To unravel the mechanisms underlying the anti-hypertrophic property of cisapride, we first tested whether the HERG channel blocking action of cisapride has any connection to the anti-hypertrophic effects of this agent."
reach
"High-affinity hERG channel blocking drugs E4031, astemizole, cisapride and quinidine all produced reverse effects, and the rescue was dependent on their interaction with F656."
reach
"Diseases characterized by an elevated baseline of arrhythmia such as LQT and HCM exhibited a particular propensity for exhibition of drug induced EADs by hERG blockade with cisapride."
reach
"Compared to PSS, the IC 50 values, conducted at room temperature, of the classic hERG blocking drugs cisapride, moxifloxacin, and terfenadine were shifted to the right by an extent predicted by their known plasma protein binding, but we did not detect any differences in IC 50 s between male and female serum."
KCNH2 activates cisapride.
| 2
| 1
reach
"E-4031 's defined boundaries did not match or include those of cisapride, another hERG K + channel blocker, causing classification of cisapride to be closer to that of the cardiac glycoside family."
KCNH2-F656A activates cisapride. 1 / 1
| 1
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"Thus, Cavalli-2 should be a useful probe of the spatial configuration of drug binding groups, especially the aromatic side chains of Tyr 652 and Phe 656; substantial interactions with multiple (at least two) Phe 656 side chains seem to be required to understand the large attenuations of block seen with several high-affinity blockers, including flecainide, Cavalli-2 (this study), E-4031, and cisapride in hERG F656A overexpressing mammalian cells and MK-499, cisapride, chloroquine, and clofilium in hERG F656A overexpressing oocytes."
KCNH2 binds cisapride.
| 1
reach
"Intracellular K+ is required for the inactivation induced high-affinity binding of cisapride to HERG channels."
| 7
| 6
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"Blockade of the hERG potassium channel proteins by specific agents can inhibit the proliferation and metastasis of tumor cells and the corresponding [XREF_BIBR, XREF_BIBR], increasing the sensitivity of tumor cells to chemotherapeutic drugs."
reach
"HERG1 knockdown reduced tumor growth and metastasis in athymic mice."
reach
"Functionally, hERG1 may contribute to survival, proliferation, and metastasis of tumor cells."
reach
"Functionally, hERG1 may contribute to survival, proliferation, and metastasis of tumor cells."
reach
"For example, inhibition of the potassium channels, KCNK9 [XREF_BIBR], Kv10.1 [XREF_BIBR], hEag1 [XREF_BIBR], and HERG1 [XREF_BIBR] inhibited tumor metastasis, as did inhibition of the sodium channels, Na (v1.4) [XREF_BIBR] and Na (v) 1.5 [XREF_BIBR] and the sodium proton exchanger, NHE1 [XREF_BIBR, XREF_BIBR]."
reach
"HERG1 promotes esophageal squamous cell carcinoma growth and metastasis through TXNDC5 by activating the PI3K and AKT pathway."
| 1
reach
"Stable depletion of HERG1 suppresses tumorigenicity and metastasis of pancreatic cancer cells in vivo."
KCNH2 affects MINK1
1 | 6
KCNH2 binds MINK1.
1 | 5
1 | 5
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"It is already known, for example, that minK can interact with KVLQT1 and HERG when overexpressed in heterologeous systems (McDonald et al., 1997)."
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"A minK and HERG complex regulates the cardiac potassium current I (Kr)."
reach
"Alanine at codon 8 is next to threonine at 7 7 and caused a significant modulation on the MinK and HERG complex."
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"10 Thus, minK interacts with both KCNQ1 and HERG, and KCNE1-3 proteins interact with Kv3.1 and Kv3.2 causing diversification of channel gating."
reach
"Thus, minK and MiRP1 interaction with HERG are not mediators of regulators of the kinase dependent enhancement of channel synthesis."
signor
"Herg, a human homologue of the ether-a-go-go gene of the fruitfly drosophila melanogaster, encodes aproteinthat produces the rapidly activating cardiac delayed rectifier (i[kr]). / our results show that mink physically associates with herg and that the interaction leads to increased ikr current density."
KCNH2 activates MINK1.
| 1
KCNH2 activates MINK1. 1 / 1
| 1
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"Another obvious family of HERG interacting proteins to consider as playing a role in the kinase mediated augmentation of channel translation is that encoded by the KCNE1 and KCNE2 genes -- minK and MiRP1 [XREF_BIBR, XREF_BIBR]."
CXCL12 affects KCNH2
| 2 7
CXCL12 activates KCNH2.
| 2 4
CXCL12 activates KCNH2. 4 / 4
| 2 4
reach
"Our electrophysiologic results showed that SDF-1 significantly increased hERG tail current, which suggested that SDF-1 enhance functional role of hERG1 K + channels."
reach
"SDF-1 increased hERG1 K (+) current expressed in oocytes and HEK293T cells transfected with herg-pEGFP."
reach
"According to our observations, SDF-1 increased hERG current which could engender an increased malignancy of hERG."
reach
"Current-voltage relationship of outward of peak tail currents had been shown in Fig. 4 C. SDF-1 (100 ng/ml) significantly increased hERG tail currents."
CXCL12 increases the amount of KCNH2.
| 2
CXCL12 increases the amount of KCNH2. 2 / 2
| 2
reach
"RT-PCR showed that SDF-1a enhanced hERG1 expression in a dose dependent manner."
reach
"Herg1 was constitutively expressed in all the leukemic cell lines and samples we used in this report and other group showed that hERG1 protein correlated with the invasion capacity of colon cancer cells [17], so the migration difference among subsets might be explained by the different herg expression in the subsets that would be explored in the future, but here in this report we did not compare the amount of hERG1 K + channels expression.In the BM, SDF-1 activates the CXCR4 expressed in leukemic cells of diverse biological responses [30]."
CXCL12 inhibits KCNH2.
| 1
CXCL12 inhibits KCNH2. 1 / 1
| 1
reach
"Blocking hERG1 K + channels inhibited the hERG current induced by SDF-1, which might consequently inhibit cell migration triggered by SDF-1."
ALG10B affects KCNH2
1 1 | 1 5
ALG10B inhibits KCNH2.
| 1 3
ALG10B inhibits KCNH2. 3 / 3
| 1 3
reach
"Previous reports demonstrated that K (+) channel regulator 1 (KCR1) diminishes KCNH2 drug sensitivity and may protect susceptible patients from developing aLQTS."
reach
"Functionally, KCR1 reduces the sensitivity of HERG to classic proarrhythmic HERG blockers (sotalol, quinidine, dofetilide) in both cardiac and noncardiac cell lines."
reach
"We propose that KCR1, when coupled to HERG, may limit the sensitivity of HERG to proarrhythmic drug blockade and may be a rational target for modifying the proarrhythmic effects of otherwise clinically useful compounds."
ALG10B binds KCNH2.
1 1 |
1 1 |
biogrid
No evidence text available
hprd
No evidence text available
ALG10B activates KCNH2.
| 2
ALG10B activates KCNH2. 2 / 2
| 2
reach
"Transmembrane ancillary subunits include the MinK related proteins (MiRPs) encoded by KCNE genes, which modulate members of most Kv alpha subunit subfamilies, and the putative 12-transmembrane domain KCR1 protein, which modulates hERG."
reach
"The ALG10B gene (also known as KCR1) modulates HERG, reducing the sensitivity of cardiac cells to arrhythmic disturbance [XREF_BIBR, XREF_BIBR]."
AKT affects KCNH2
| 7
AKT activates KCNH2.
| 6
AKT activates KCNH2. 6 / 6
| 6
reach
"Whether these sites are responsible for HERG modulation by PKB merits further studies with site directed mutagenesis."
reach
"There are three possible mechanisms for the pilsicainide induced increase of hERG proteins via post-translational modifications : (1) phosphorylation of Akt, (2) activation of hsp expressions, and (3) direct action as a chemical chaperone."
reach
"Moreover, our data from caPKB experiments indicate that any further increase in PKB activation may further increase I HERG beyond the basal conditions."
reach
"Our data clearly indicate that HERG K + channel function in HEK293 cells is enhanced by PKB activation and also provide the evidence for the first time that PKB phosphorylation participates in K + channel modulation.WMN, used to inhibit PI3K activation and thereby the downstream PI3K dependent PKB activation, produced remarkable depression (~ 30% reduction) of I HERG stably expressed in HEK293 cells."
reach
"HERG channel activity was further increased by coexpression of PKB, an effect augmented by additional coexpression of PIKfyve, but not by additional coexpression of PKB and Akt resistant PIKfyve mutant PIKfyve (S318A)."
reach
"The quantitative data are presented in Fig. 4C where the ratios of staining intensity in positively stained cells over non stained control cells are shown.We demonstrated here that prevention of PI3K and PKB activation by pharmacological inhibition (WMN) or molecular inactivation (dnPI3K and dnPKB) significantly suppressed HERG function, whereas direct activation of PKB by introducing caPKB into the cell markedly enhanced HERG function."
AKT inhibits KCNH2.
| 1
AKT inhibits KCNH2. 1 / 1
| 1
reach
"The quantitative data are presented in Fig. 4C where the ratios of staining intensity in positively stained cells over non stained control cells are shown.We demonstrated here that prevention of PI3K and PKB activation by pharmacological inhibition (WMN) or molecular inactivation (dnPI3K and dnPKB) significantly suppressed HERG function, whereas direct activation of PKB by introducing caPKB into the cell markedly enhanced HERG function."
| 1 6
| 1 6
reach
"Inhibition of HERG K+ current and prolongation of the guinea-pig ventricular action potential by 4-aminopyridine."
reach
"Although inhibition of hERG by 4-aminopyridine was observed, the clinical relevance of these data needs to be considered."
reach
"At the two lowest concentrations, 0.1 mM had no effect and inhibition of hERG by 4-aminopyridine 0.3 mM was minimal (8.2 +/- 0.9%; N = 3)."
reach
"HERG K + current and ventricular I to are blocked by 4-AP XREF_BIBR, XREF_BIBR."
reach
"As demonstrated in the experimental data, 4-aminopyridine induced a concentration dependent inhibition of the hERG channel currents."
reach
"Both K + channel blockers, 4-AP and TEA, significantly inhibited the proliferation of Eag and HERG positive SK-OV-3 cells, confirming data by Zhanping et al., on the A2780 ovarian cancer line [XREF_BIBR]."
sparser
"Both TEA and 4-AP are non selective K + channel blockers capable of inhibiting Eag and HERG as well as other voltage gated K + channels."
| 7
(S)-naringenin inhibits KCNH2.
| 6
reach
"The IC50 value for HERG block by naringenin, the most potent inhibitor, was 102.3 micromol/L in Xenopus oocytes and 36.5 micromol/L in HEK cells."
reach
"Naringenin blocked HERG current dose dependently with an IC (50) of 173.3 +/- 3.1 microM."
reach
"HERG blockade by grapefruit flavonoid naringenin is most likely to be the mechanism underlying this effect."
reach
"Therefore, the electrophysiological properties of HERG blockade by naringenin were analysed in detail."
reach
"Naringenin blocked HERG potassium channels with an IC50 value of 102.6 microM in Xenopus oocytes."
reach
"Naringenin 100 microM alone inhibited HERG current by 31 +/- 6%, and this inhibitory effect was increased with coadministration of 1 or 10 microM antiarrhythmic drugs."
| 1
(S)-naringenin binds KCNH2 and F656. 1 / 1
| 1
reach
"Naringenin binding to HERG required aromatic residue F656 in the putative pore binding site."
Vandetanib affects KCNH2
| 6
Vandetanib inhibits KCNH2.
| 4
| 3
reach
"Vandetanib inhibited WT-hERG current by approximately 86.4 +/- 7.3% (XREF_FIG)."
reach
"Vandetanib at concentrations of 0.3, 1, and 3 muM reduced I hERG current amplitude by 17.04, 45.32, and 76.05%, respectively (n = 4; XREF_FIG)."
reach
"Purkinje fiber assays and ion channel studies showed that vandetanib at concentrations of 1 and 3 muM inhibited the hERG currents and prolonged the action potential duration."
Vandetanib inhibits mutated KCNH2. 1 / 1
| 1
reach
"Inhibition of wild type (WT) and mutant hERG channels by vandetanib."
Vandetanib binds KCNH2.
| 1
reach
"The binding of vandetanib to hERG channel is further stabilized by T shaped pi-pi interactions with F656."
Vandetanib activates KCNH2.
| 1
| 1
reach
"An ion channel study of the effects of vandetanib in hiPSC-CMs showed that the vandetanib induced prolongation of the APD and decrease in V max were caused by inhibition of I hERG and I Na, respectively (XREF_FIG)."
| 1 2 4
| 1 2 4
reach
"HERG K+ channel blockade by the antipsychotic drug thioridazine : An obligatory role for the S6 helix residue F656."
reach
"Especially, it has been reported that thioridazine and chlorpromazine directly inhibited hERG channels, through which these drugs could induce long QT syndrome [XREF_BIBR XREF_BIBR XREF_BIBR XREF_BIBR]."
reach
"Thioridazine, perphenazine, trifluoperazine, and chlorpromazine blocked hERG potassium channels with the following IC (50) values : IC (50) values were 224 +/- 42 nM for thioridazine, 1003 +/- 71 nM for perphenazine, 1406 +/- 124 nM for trifluoperazine, and 1561 +/- 281 nM for chloropromazine."
sparser
"To our best knowledge, no information has been published previously on molecular determinants of I hERG inhibition by thioridazine or other phenothiazine antipsychotic drugs."
reach
"This analysis shows that enhancements of endogenous HF oscillations in HR were also found in beagle dogs with dofetilide and with other hERG blockers such as cisapride, haloperidol, risperidone, DL sotalol, terfenadine and thioridazine."
sparser
"Especially, it has been reported that thioridazine and chlorpromazine directly inhibited hERG channels, through which these drugs could induce long QT syndrome [ xref xref xref xref ]."
ThiO affects KCNH2
| 6
ThiO inhibits KCNH2.
| 3
ThiO inhibits KCNH2. 3 / 3
| 3
reach
"Importantly, we found that THIO increased surface hERG degradation (XREF_FIG), which indicates that THIO may increase lysosome mediated mature hERG degradation."
reach
"Whilst THIO produced a substantial inhibition of WT-hERG, it produced virtually no inhibition of the F656A hERG mutant."
reach
"These results indicate that THIO inhibited the hERG current without altering the kinetics of channel gating, suggesting that THIO mediated hERG channel damage is dependent on a decrease in protein levels."
ThiO activates KCNH2.
| 3
ThiO activates KCNH2. 3 / 3
| 3
reach
"Our results demonstrated that THIO induced hERG channel deficiency but did not alter channel kinetics."
reach
"These results indicate that THIO inhibited the hERG current without altering the kinetics of channel gating, suggesting that THIO mediated hERG channel damage is dependent on a decrease in protein levels."
reach
"These data provide evidence that THIO promotes hERG misfolding and degradation by inducing the dissociation of Hsp70 from hERG."
| 6
Testosterone inhibits KCNH2.
| 4
| 4
reach
"[Testosterone modulation of HERG potassium channel blockade induced by neuroleptics]."
reach
"Here by using neuroleptic agents haloperidol, pimozide, and fluspirilene, all of which can induce TdP, and a steroid hormone sensitive system Xenopus oocytes for HERG channels expression we show that testosterone is able to reduce HERG blocking potency of neuroleptics."
reach
"Testosterone mediated modulation of HERG blockade by proarrhythmic agents."
reach
"Given that testosterone can downregulate HERG channels, we examined whether it may also modify the channel sensitivity to neuroleptics."
Testosterone decreases the amount of KCNH2.
| 1
Testosterone decreases the amount of KCNH2. 1 / 1
| 1
reach
"The fact that minK can be directly affected by sex steroid hormones as well as the dependence of minK expression on the overall hormonal status [15,38,39] strongly suggests that minK may be the key molecule determining modulation of QT c interval by sex steroid hormones.An important result of our study is that testosterone not only decreases HERG current expression in Xenopus oocytes, but also modulates the characteristics of the blockade of this current by haloperidol, pimozide and fluspirilene."
Testosterone activates KCNH2.
| 1
| 1
reach
"Modulation by testosterone of an endogenous hERG potassium channel current."
Terbinafine affects KCNH2
| 6
Terbinafine inhibits KCNH2.
| 2
| 2
reach
"These include terbinafine (TER) that inhibits the ERG1 gene product, fenpropimorph (FEN) that inhibits Erg2p, and lovastatin (LOV) that inhibits Hmg1p."
reach
"Terbinafine, an allylamine, inhibits the erg1 + product squalene epoxidase XREF_BIBR, which acts upstream of the erg11 + product lanosterol demethylase that is inhibited by azoles XREF_BIBR."
Terbinafine decreases the amount of KCNH2.
| 2
Terbinafine decreases the amount of KCNH2. 2 / 2
| 2
reach
"With respect to the genes involved in ergosterol synthesis, trans-chalcone, alpha-solanine, and terbinafine inhibited the expression of the ERG1 and ERG11 genes."
reach
"Our findings have demonstrated that the combination of fluconazole and terbinafine could also significantly reduce the expression of ERG1, 3, and 11 in the cell membrane of Candida in all concentrations tested ranging from 1.73- to 6.99-fold."
Terbinafine activates KCNH2.
| 2
| 2
reach
"Terbinafine targets ERG1, which is the upstream gene for ERG11, the target for posaconazole."
reach
"Synergy with geldanamycin was also observed between the allylamine terbinafine (FIC 90 = 0.25), which targets Erg1, and the morpholine fenpropimorph (FIC 90 = 0.016), which targets Erg24 and Erg2 (XREF_FIG)."
Rottlerin affects KCNH2
| 1 6
| 1 6
reach
"Similar to KB130015, mallotoxin (MTx) activates the hERG1 channel by shifting its voltage dependence to the left and by accelerating activation."
reach
"Mallotoxin, an alkaloid isolated from the tree Mallotus phillippinensis, increases hERG1 current amplitude by causing a hyperpolarizing shift in the voltage dependence of channel activation, with a maximum shift of -24 mV at 10 muM and an EC 50 of 0.5 muM [XREF_BIBR]."
reach
"As expected, mallotoxin activated hERG current by 87% at 3muM, and NS1643 activated hERG current by 55% at 3muM."
reach
"In contrast to KB130015, mallotoxin slows down hERG1 deactivation, suggesting a different mode of action."
reach
"In this study, we showed that both mallotoxin and NS1643 activated hERG current by 87% and 55% at 3muM, respectively."
reach
"Mallotoxin, which activated hERG current by 87% at 3muM in hERG transfected HEK293 cells, significantly shortened the QT interval, JT interval and APD and increased Tp-Te and rTp-Te and coronary flow at 0.1 muM."
Propranolol affects KCNH2
| 6
| 6
reach
"The present study demonstrated that propranolol can inhibit hERG channels."
reach
"Previous studies have shown that hERG, a frequent target of many drugs, is blocked by propranolol with an IC 50 of between 10 muM and 53 muM [XREF_BIBR, XREF_BIBR]."
reach
"We previously demonstrated that propranolol inhibits hERG potassium channels with an IC 50 of 10muM, which is about 300- to 530-fold higher than its maximum free plasma concentration at therapeutic doses."
reach
"Carvedilol (nonselective), propranolol (nonselective) and ICI 118551 (beta (2)-selective) inhibited HERG current in a concentration dependent manner (IC (50) 0.51, 3.9 and 9.2 microM, respectively)."
reach
"We found that propranolol blocked hERG currents in a concentration dependent manner with an IC50 of 9.9 +/-1.3 microM which is relevant to the predicted plasma level of propranolol in this case report."
reach
"Propranolol caused a concentration dependent inhibition of HERG current with an IC50 value of 81 microM at -10 mV."
Propafenone affects KCNH2
| 6
| 6
reach
"In conclusion, propafenone has been found to block HERG potassium channels."
reach
"In the early 2000s, racemic propafenone was demonstrated to block overexpressed hERG1 channels in cellular models and native I Kr current from isolated rabbit ventricular myocytes at IC 50 values comparable with those of quinidine 0.4-0.8 muM in mammals) and within therapeutic plasma concentrations."
reach
"The data show that extending the size of a trapped HERG blocker like propafenone by adding a bulky side chain may impede channel closure and thereby facilitate drug dissociation at rest."
reach
"The low-potency, voltage dependent HERG blocker propafenone -- molecular determinants and drug trapping."
reach
"In this study, the trapping mechanisms of a trapped hERG blocker propafenone and a bulky derivative (MW : 647.24 g mol -1) were studied by making use of electrophysiological measurements in combination with molecular dynamics simulations."
reach
"Propafenone and 5-hydroxypropafenone (2 microM) inhibited HERG current by 78.7 +/-2.3% (n = 7) and 71.1 +/-4.1% (n = 7, P> 0.05) when measured at the end of 5-s depolarizing pulses to -10 mV."
P14_3_3 affects KCNH2
| 4 5 1
P14_3_3 binds KCNH2.
| 1 4
| 1 3
sparser
"A second level of β-AR/PKA regulation of HERG may occur with the association of adaptor proteins such as 14-3-3, which binds to HERG when the channel is phosphorylated and affects channel gating and duration of the response [ xref , xref ]."
sparser
"Thus, 14-3-3 interactions with HERG may provide a unique mechanism for plasticity in the control of membrane excitability and cardiac rhythm."
sparser
"Thus, 14-3-3 interactions with hERG provide a unique mechanism for plasticity in the autonomic control of stress-dependent regulation of cardiac membrane excitability."
| 1
sparser
"Our results suggest that the dynamic association of 14-3-3 proteins to both beta(1)AR and Kv11.1 channels is involved in the adrenergic modulation of this critical regulator of cardiac repolarization and refractoriness."
P14_3_3 phosphorylates KCNH2.
| 1
P14_3_3 phosphorylates KCNH2. 1 / 1
| 1
sparser
"While this mechanism has not yet been demonstrated for KCNH2, 14-3-3 has also been implicated in the regulation of KCNH2 channel activity, possibly via 14-3-3-dependent KCNH2 channel phosphorylation."
P14_3_3 activates KCNH2.
| 3 1
P14_3_3 activates KCNH2. 1 / 1
| 3 1
reach
"14-3-3 accelerates and enhances HERG activation, an effect that requires PKA phosphorylation of HERG and dimerization of 14-3-3."
| 6
Isocyanic acid activates KCNH2.
| 4
reach
"ICA strongly inhibits inactivation and thereby increases the magnitude of hERG1 channel currents, especially at positive potentials."
reach
"ICA increases the magnitude of outward hERG1 currents by profound attenuation of inactivation."
reach
"The same concatenation strategy used to characterize PD was used to study ICA, a compound which enhances hERG1 current by strongly inhibiting channel inactivation."
reach
"We took advantage of our previous finding that L646E and F557L mutations nearly abolish the ability of PD and ICA, respectively, to enhance hERG1 currents."
Isocyanic acid inhibits KCNH2.
| 2
reach
"ICA at 10 microM induced a much larger increase in I test magnitude and slowed current deactivation in both WT and WT 4 hERG1 channels (XREF_FIG)."
Isocyanic acid inhibits mutated KCNH2. 1 / 1
| 1
reach
"This was confirmed by showing that the noninactivating mutant hERG1 channel (G628C and S631C) was inhibited by ICA and that the addition of the F557L mutation rendered the channel drug-insensitive."
Gallic acid affects KCNH2
| 6
| 6
reach
"These effects of GA on channel kinetics were consistent with affinity for the inactivated state, suggesting that GA blocks the HERG channel by affecting its inactivation but not its activation."
reach
"The results confirmed that GA blocks HERG."
reach
"The inhibition of I Kr, I Ks, and HERG by GA would induce a prolongation of APD, which could contribute to its antiarrhythmic actions because prolongation of APD could prevent or terminate the reentrant excitation and prolong the refractory period."
reach
"GA blocked the HERG currents and the tail current in a concentration dependent manner."
reach
"GA (1, 5, and 10muM) inhibited I K (I Kr, I Ks) and the HERG K + current in a concentration dependent manner."
reach
"GA not only blocks the HERG channel, I K (I Kr, I Ks), but also inhibits I Na, so the results reveal that it has significant potential for development as a novel antiarrhythmic agent, particularly targeting the genesis of arrhythmias."
| 6
| 3
reach
"In this study, we demonstrated that 1) cav-1 participates in BBR induced hERG deficiency on cell surface; 2) residues Tyr652 and Phe656, essential components of hERG binding sites, mediate hERG surface expression inhibition by BBR incubation; and 3) fexofenadine and resveratrol can shorten APD of ventricular cardiomyocytes prolonged by BBR."
reach
"HERG channel blockers, such as E4031, fexofenadine and astemizole, facilitated maturation of hERG proteins by acting as chemical chaperones XREF_BIBR; however, these agents can not be used clinically for enhancing hERG channel currents, because they acutely block the rapidly activating delayed-rectifier K + channel current (I Kr)."
reach
"In XREF_FIG, application of 10 muM resveratrol and 1 muM fexofenadine rescued hERG tail current reduction in the presence of 10 muM BBR."
Fexofenadine inhibits KCNH2-K897T. 2 / 2
| 2
reach
"Even at a concentration of 100 micro M, fexofenadine did not inhibit wild-type or K897T HERG channels."
reach
"In the present study the ability of fexofenadine to block the K897T HERG channel variant was investigated."
Fexofenadine inhibits KCNH2-N470D. 1 / 1
| 1
reach
"Terfenadine and fexofenadine reversed N470D hERG mutation [XREF_BIBR]."
Fentanyl affects KCNH2
| 6
| 6
reach
"As well, high pH potentiated the fentanyl mediated block of hERG channels, with an IC 50 at pH 8.4 being 7-fold lower than that at pH 7.4."
reach
"When hERG tail currents upon -50 mV repolarization following a 50 mV depolarization were analyzed, fentanyl and naloxone blocked hERG current (I hERG) with an IC 50 of 0.9 muM and 74.3 muM, respectively, while norfentanyl did not block."
reach
"35 Oxycodone and fentanyl reduce HERG current in vitro, XREF_BIBR, XREF_BIBR and as do cocaine and cocaine metabolites, XREF_BIBR, XREF_BIBR but none of these drugs affect the I Ks current."
reach
"Thus, in addition to a greater susceptibility due to the presence of hERG1b in the human heart, hERG channel block by fentanyl can be exacerbated by certain conditions such as hypoxia, hypokalemia, or alkalosis, which may increase the risk of fentanyl induced ventricular arrhythmias and sudden death."
reach
"We have demonstrated that fentanyl blocks hERG current (I hERG) at concentrations that overlap with the upper range of postmortem blood concentrations in fentanyl related deaths."
reach
"When a voltage protocol that mimics a human ventricular action potential (AP) was used, fentanyl blocked I hERG with an IC 50 of 0.3 muM."
| 6
Escitalopram inhibits KCNH2.
| 5
| 5
reach
"Both escitalopram and citalopram produced a reduction of hERG channel protein trafficking to the plasma membrane but did not affect the short-term internalization of the hERG channel."
reach
"Fluoxetine and its metabolite, norfluoxetine, citalopram and escitalopram prolong the QT interval by directly inhibiting the hERG potassium channels and by disrupting channel protein trafficking reducing the number of channels on the cell membrane [XREF_BIBR]."
reach
"Escitalopram block of hERG potassium channels."
reach
"The blocking of hERG by escitalopram was voltage dependent, with a steep increase across the voltage range of channel activation."
reach
"These results suggest that escitalopram blocked hERG currents at a supratherapeutic concentration and that it did so by preferentially binding to both the open and the inactivated states of the channels and by inhibiting the trafficking of hERG channel protein to the plasma membrane."
Escitalopram activates KCNH2.
| 1
| 1
reach
"A rapid application of escitalopram induced a rapid and reversible blocking of the tail current of hERG."
Droperidol affects KCNH2
| 6
| 6
reach
"HERG tail currents following test pulses to 50 mV were inhibited by droperidol with an IC (50) of 77.3 +/- 9.6 nM (n = 8)."
reach
"Molecular mechanisms of HERG current inhibition by droperidol were established using two-electrode voltage clamp recordings of Xenopus laevis oocytes expressing wild-type and mutant channels."
reach
"The hERG K+ current was blocked by D,L-sotalol (IC50 approximately 1.2 mM, IC20 approximately 250 microM) and droperidol (IC50 approximately 0.1 microM, IC20 approximately 0.02 microM)."
reach
"In conclusion, the higher sensitivity of anesthetized dogs towards sotalol induced QT prolongation is due to a reduced cardiac repolarization reserve caused by the hERG blocker droperidol."
reach
"Finally, HERG K+ current elicited in HEK293 cells expressing high levels of HERG protein was decreased 50% by droperidol 32.2 nmol/L."
reach
"The repolarization reserve of the latter was reduced by neurolept anesthesia using the hERG blocker droperidol (0.25 mg/kg/h yielding mean plasma concentrations of 0.5 microM)."
| 6
reach
"Thioridazine, perphenazine, trifluoperazine, and chlorpromazine blocked hERG potassium channels with the following IC (50) values : IC (50) values were 224 +/- 42 nM for thioridazine, 1003 +/- 71 nM for perphenazine, 1406 +/- 124 nM for trifluoperazine, and 1561 +/- 281 nM for chloropromazine."
reach
"Especially, it has been reported that thioridazine and chlorpromazine directly inhibited hERG channels, through which these drugs could induce long QT syndrome [XREF_BIBR XREF_BIBR XREF_BIBR XREF_BIBR]."
reach
"IC50 for chlorpromazine block of HERG current was progressively decreased according to depolarization : IC50 values at -30, 0, and +30 mV were 10.5, 8.8, and 4.9 microM, respectively."
reach
"The decrease became more pronounced at increasingly positive potential, suggesting that the blockade of HERG by chlorpromazine is voltage dependent."
reach
"(3) Chlorpromazine blocked HERG potassium channels with an IC (50) value of 21.6 micro M and a Hill coefficient of 1.11."
reach
"The antipsychotic drug chlorpromazine inhibits HERG potassium channels."
Chloride affects KCNH2
| 4 2
| 4
sparser
"We found some similarities as well as differences in the electrophysiological properties of HERG channel inhibitions by tetra-n-octylammonium bromide and benzethonium chloride ( xref )."
sparser
"In the present study, the potential mechanisms for HERG channel inhibition by tetra-n-octylammonium bromide and benzethonium chloride, two most potent HERG channel inhibitors found among the QACs examined ( xref ), were studied using whole-cell patch clamp experiments in a CHO cell line stably expressing HERG channels."
sparser
"The study of mechanism of HERG channel inhibition by tetra-n-octylammonium bromide and benzethonium chloride can provide additional insight of structure-activity relationship of HERG channel inhibition and the molecular determinants of the interaction between the compounds and HERG channel proteins."
sparser
"The properties of HERG channel inhibition by tetra-n-octylammonium bromide and benzethonium chloride are highly similar to verapamil and cisapride ( xref )."
| 2
reach
"For example, decamethonium dibromide and benzyltrimethylammonium chloride did not inhibit the hERG channel, presumably because the charged nitrogen (s) in these compounds are exposed."
reach
"In Xenopus oocytes, endogenous chloride currents, insufficient superfusate flow, diminished HERG current and HERG current ' run up ' may create difficulties."
TNF affects KCNH2
| 1 6
TNF inhibits KCNH2.
| 1 3
TNF inhibits KCNH2. 3 / 3
| 1 3
reach
"Wang et al. previously demonstrated that TNF-alpha decreased hERG current density in HEK293 cells, significantly depressed I Kr density and prolonged APD in canine ventricular myocytes, primarily due to changes in reactive oxygen species (ROS)."
reach
"TNF-alpha consistently and reversibly decreased HERG current (I (HERG))."
reach
"Tumor necrosis factor-alpha (TNF-alpha), a critical factor causing heart failure and when overexpressed prolonging APD and promoting ventricular arrhythmias, suppresses HERG function XREF_BIBR."
TNF increases the amount of KCNH2.
| 1
TNF increases the amount of KCNH2. 1 / 1
| 1
reach
"Immunoblotting analysis demonstrated that HERG protein level was slightly higher in canine hearts with tachypacing induced CHF than in healthy hearts, and TNF-alpha slightly increased HERG protein level in CHF but not in healthy hearts."
TNF decreases the amount of KCNH2.
| 1
TNF decreases the amount of KCNH2. 1 / 1
| 1
reach
"We conclude that the TNF-alpha and TNFR1 system impairs HERG/I (Kr) function mainly by stimulating reactive oxygen species, particularly superoxide anion, but not by altering HERG expression; the effect may contribute to APD prolongation by TNF-alpha and may be a novel mechanism for electrophysiological abnormalities and sudden death in CHF."
TNF activates KCNH2.
| 1
TNF activates KCNH2. 1 / 1
| 1
reach
"Moreover, Wang and coll showed that TNFalpha down-regulates in vitro IKr by impairing the function of the hERG potassium channel via the stimulation of reactive oxygen species."
NF2 affects KCNH2
| 6
| 6
sparser
"We also present the association of HERG1 with SCH in Turkish population, as was shown by Huffaker et al. [ xref ] in American and German populations, but not in Armenians and Italians."
sparser
"As an independent research group we confirm Huffaker et al. [ xref ] regarding the association of SCH with HERG1 and specifically the HERG1 SNP rs3800779 which shows higher significance in their study and unique significance in ours towards the same direction of association."
sparser
"Our results indicate that the potassium channel gene HERG1 is associated with SCH, although this needs to be reproduced in a larger sample size and in other ethnic groups."
sparser
"In mechanism, Herg1 protein interacted with NF2 protein."
sparser
"Although the number of our study subjects is generally regarded as small for association studies, we were able to confirm the findings reported in larger populations by Huffaker et al. [ xref ] regarding the association of SCH with HERG1 and specifically the HERG1 SNP rs3800779."
sparser
"This assumption led us to investigate the putative association of HERG1 gene with SCH."
LQT2 affects KCNH2
| 6
LQT2 activates KCNH2.
| 3
LQT2 activates KCNH2. 3 / 3
| 3
reach
"Like noncardiac organ phenotypes observed in other LQTS-susceptibility genes such as KCNQ1 and deafness and SCN5A and gastrointestinal symptoms, this novel LQT2-epilepsy association raises the possibility that LQT2 causing perturbations in the KCNH2 encoded potassium channel may confer susceptibility for recurrent seizure activity."
reach
"LQT2 is caused by loss of function (LOF) mutations in KCNH2 (also known as the human Ether-a-go-go-Related Gene or hERG)."
reach
"LQT1 and LQT2 are caused due to mutations in the potassium channel genes, KCNQ1 (OMIM # 607542) and KCNH2 (OMIM # 152427) respectively, while LQT3 is caused by mutations in a sodium channel gene, SCN5A (OMIM # 600163) XREF_BIBR."
LQT2 inhibits KCNH2.
| 2
Mutated LQT2 inhibits KCNH2. 1 / 1
| 1
reach
"The majority of LQT2 mutations reduce hERG currents by the trafficking deficient mechanism."
LQT2 inhibits KCNH2. 1 / 1
| 1
reach
"Furthermore, particular C-terminal HERG mutations lacking the 1137 residue and clinically associated with stress induced arrhythmias in LQT2 disrupt 14-3-3epsilon-induced enhancement of HERG channel activity."
LQT2 binds KCNH2.
| 1
KCNH2 binds LQT2. 1 / 1
| 1
reach
"We demonstrate that both K + depletion and selected LQT2 associated mutations compromise hERG structural stability at the PM."
KCNH2 affects side
| 6
KCNH2 inhibits side.
| 5
KCNH2 inhibits side. 5 / 5
| 5
reach
"Our findings suggest that the arrhythmogenic side effects of maprotiline are caused by a blockade of HERG and possibly by a blockade of delayed rectifier K+ channel."
reach
"Abnormal cardiac electrical activity is a common side effect caused by unintended block of the promiscuous drug target hERG1; the pore forming domain of the delayed rectifier K+ channel in the heart."
reach
"Our findings suggest that the arrhythmogenic side effects of prochlorperazine are caused by a blockade of HERG and the rapid component of the delayed rectifier K+ current rather than by a blockade of the slow component."
reach
"Our findings suggest that the arrhythmogenic side effect of chlorpromazine is caused by blockade of HERG and rapid component of delayed rectifier K current rather than by blockade of the slow component."
reach
"Our findings suggest the arrhythmogenic side effect of trifluoperazine is caused by a blockade of HERG and the rapid component of the delayed rectifier K (+) current rather than by the blockade of the slow component."
KCNH2 activates side.
| 1
KCNH2 activates side. 1 / 1
| 1
reach
"In hERG, F463 can be replaced by M, L, or V with small effects on channel gating (17), indicating that the hERG CTC requires only a bulky nonpolar side chain to seal the hydrophobic center of the VS and allow passage of the Arg side chain through the CTC."
| 1 6
| 1 4
reach
"By using the CML cell line K562 with high hERG channel expression [XREF_BIBR, XREF_BIBR], the blockage of hERG channel by a potent scorpion toxin BmKKx2 blocker was found to enhance the erythroid differentiation."
reach
"Furthermore, hERG expression is implicated in enhanced cell proliferation, invasiveness, lymph node dissemination, and reduced cell differentiation and prognosis."
reach
"The hERG potassium channel blockage by a new 36-residue scorpion toxin BmKKx2, a potent hERG channel blocker with IC 50 of 6.7 +/-1.7 nM, enhanced the erythroid differentiation of K562 cells."
reach
"HERG Potassium Channel Blockage by Scorpion Toxin BmKKx2 Enhances Erythroid Differentiation of Human Leukemia Cells K562."
| 2
reach
"The hERG potassium channel blockage by a new 36-residue scorpion toxin BmKKx2, a potent hERG channel blocker with IC 50 of 6.7 +/-1.7 nM, enhanced the erythroid differentiation of K562 cells."
reach
"Here, we show that differentiation of hESCs into embryonic ECs is driven by the expression of ETV2, ERG1 and FLI1."
KCNH2 affects YWHAE
3 1 | 1 2
3 1 | 1 2
hprd
No evidence text available
sparser
"We show that HERG associates with 14-3-3epsilon to potentiate cAMP/PKA effects upon HERG."
biogrid
No evidence text available
biogrid
No evidence text available
sparser
"We recently identified a novel protein-protein interaction between hERG and the adaptor protein 14-3-3epsilon."
biogrid
No evidence text available
KCNH2 affects VEGFA
| 1 2 4
KCNH2 activates VEGFA.
| 1 3
KCNH2 activates VEGFA. 3 / 3
| 1 3
reach
"Moreover, inhibition of hERG1 (with channel blockers or RNA interference) decreased VEGF-A secretion."
reach
"HERG1 activity modulated VEGF-A secretion, through an AKT dependent regulation of the transcriptional activity of the hypoxia inducible factor."
reach
"Moreover, in GC cell lines it was shown that hERG1 modulates VEGF-A secretion through an AKT dependent pathway [XREF_BIBR]."
KCNH2 binds VEGFA.
| 2
| 1
sparser
"A similar approach might be applied to VEGF-A whose high expression is associated with poor prognosis [ xref ]: in fact, we showed that in colorectal [ xref ] and gastric [ xref ] cancers hERG1 expression is significantly associated with VEGF-A expression and the combined therapy with bevacizumab and hERG1 blockers impairs tumor growth in mouse models [ xref ]."
| 1
sparser
"All the proteins were expressed in the samples, with statistically significant associations of VEGF-A with PDGFRβ and Flt1 and hERG1 with CA IX."
KCNH2 increases the amount of VEGFA.
| 1
KCNH2 increases the amount of VEGFA. 1 / 1
| 1
reach
"HERG1 inhibition, obtained applying a mix of three anti-herg1 (alpha-herg1) siRNAs (whose effects on hERG1 expression are reported in XREF_SUPPLEMENTARY) to HCT116 and HCT8 cells, significantly decreased VEGF-A expression, that was constitutively depressed in HCT116-Sh-hERG1 cells (XREF_FIG)."
KCNH2 affects UPR
| 2 4
KCNH2 activates UPR. 4 / 4
| 2 2
sparser
"Our results suggest that trafficking-deficient G572R-hERG and E637K-hERG mutant proteins can activate UPR and are targeted to the proteasome for degradation."
reach
"These findings demonstrated that the hERG trafficking defect induced by DHB activates UPR."
reach
"The accumulation of the misfolded or imperfectly folded hERG proteins could cause UPR, which is an endoplasmic reticulum stress response that promotes the generation of the chaperones and serves a vital role in the prevention of unfolded proteins accumulation [XREF_BIBR]."
sparser
"Both mutant hERG proteins could activate the UPR by upregulating levels of active ATF6."
KCNH2-N996I activates UPR. 1 / 1
| 1
reach
"Moreover, there was no evidence of an increase in the expression of the chaperones Calnexin and Calreticulin in NKX2.5 eGFP/w hESC N996I CMs (XREF_FIG), indicating that the N996I HERG mutation does not appear to stimulate the UPR pathway."
KCNH2-E637K activates UPR. 1 / 1
| 1
reach
"Our results suggest that trafficking deficient G572R-hERG and E637K hERG mutant proteins can activate UPR and are targeted to the proteasome for degradation."
KCNH2 affects PSMD4
| 3 3
KCNH2 binds PSMD4.
| 3
| 2
sparser
"In addition, AF has been associated with rare gain of function mutations in KCNQ1, hERG and KCNJ2 causing the short QT syndrome and sudden death."
sparser
"This is largely due to reduced L-type Ca 2+ current, although rare gain-of-function mutations in KCNQ1 [ xref ], hERG [ xref ], Kir2.1 [ xref ] and KCNE ancillary subunits [ xref ] have also been associated with AF due to increases in channel conductance."
| 1
sparser
"Indeed, KCNH2 has been associated with AF in a candidate-gene association study. xref "
KCNH2 activates PSMD4.
| 3
KCNH2 activates PSMD4. 2 / 2
| 2
reach
"42 The fact that KCNH2 resequencing revealed both rare variants and common SNPs, but no novel mutations, suggests that KCNH2 only very rarely causes monogenic forms of AF."
reach
"Soucek et al. performed a comparable study confirming that inhibition of KCNH2 function could prevent AF."
Mutated KCNH2 activates PSMD4. 1 / 1
| 1
reach
"A gain-of-function mutation of HERG, a K + channel, caused not only short QT syndrome but also AF [34]."
KCNH2 affects NF2
| 6
| 6
sparser
"We also present the association of HERG1 with SCH in Turkish population, as was shown by Huffaker et al. [ xref ] in American and German populations, but not in Armenians and Italians."
sparser
"As an independent research group we confirm Huffaker et al. [ xref ] regarding the association of SCH with HERG1 and specifically the HERG1 SNP rs3800779 which shows higher significance in their study and unique significance in ours towards the same direction of association."
sparser
"Our results indicate that the potassium channel gene HERG1 is associated with SCH, although this needs to be reproduced in a larger sample size and in other ethnic groups."
sparser
"In mechanism, Herg1 protein interacted with NF2 protein."
sparser
"Although the number of our study subjects is generally regarded as small for association studies, we were able to confirm the findings reported in larger populations by Huffaker et al. [ xref ] regarding the association of SCH with HERG1 and specifically the HERG1 SNP rs3800779."
sparser
"This assumption led us to investigate the putative association of HERG1 gene with SCH."
KCNH2 affects NEDD4
| 5 1
| 4 1
sparser
"The biochemical interactions between hERG1 and Nedd4-2 were investigated by co-immunoprecipitation experiments ( Fig. 3 )."
sparser
"To confirm the down-regulation of the functional form of hERG1 by Nedd4-2, we quantified the amount of hERG1 localized at the plasma membrane by cell surface biotinylation assays."
sparser
"As shown in Fig. 3 C, a specific signal for Nedd4-2 was found when ERG1 was immunoprecipitated, thus indicating an interaction between ERG1 and Nedd4-2 in the guinea pig heart."
sparser
"Here, we provide evidence of an interaction between hERG1 and Nedd4-2 in guinea pig hearts, suggesting that ubiquitylation of the channel by this ubiquitin ligase could play a role in its regulation in vivo and hence to the regulation of the cardiac AP duration ."
reach
"It is possible that several PY motifs of hERG1 interact with several WW domains of Nedd4-2 simultaneously.We also demonstrated that WWP2, but not Nedd4-1, interacts with hERG1."
PKC binds KCNH2 and NEDD4. 1 / 1
| 1
sparser
"The increase in hERG protein was associated with PKC-induced phosphorylation (inhibition) of Nedd4-2, an E3 ubiquitin ligase that mediates hERG degradation."
KCNH2 affects MiRP1
| 6
KCNH2 binds MiRP1.
| 5
KCNH2 binds MiRP1. 5 / 5
| 5
reach
"KvLQT1 and minK associate to form the functional slowly activated delayed rectifier potassium channel (I Ks) [12,13] while HERG and MiRP1 associate to form the rapidly activated delayed rectifier potassium channel (I Kr) [10]."
reach
"While MinK and KvLQT1 complexes recreate the behaviors of I Ks channels, MiRP1 and HERG complexes recapitulate those of I Kr channels."
reach
"Third, MiRP1 and HERG complexes, like I Kr channels in murine atrial and guinea pig ventricular myocytes, are less sensitive to regulation by external K + than HERG channels (Shibasaki 1987; Scamps and Carmeliet 1989; Sanguinetti and Jurkiewicz 1992; Sanguinetti et al. 1995; Yang and Roden 1996; Yang et al. 1997)."
reach
"Thus, minK and MiRP1 interaction with HERG are not mediators of regulators of the kinase dependent enhancement of channel synthesis."
reach
"Second, MiRP1 and HERG complexes and I Kr channels in murine and human cardiac myocytes deactivate 3-fold more rapidly than channels formed only of HERG subunits (Yang et al. 1994; Sanguinetti et al. 1995; London et al. 1997; Wang et al. 1997a)."
KCNH2 activates MiRP1.
| 1
KCNH2 activates MiRP1. 1 / 1
| 1
reach
"Another obvious family of HERG interacting proteins to consider as playing a role in the kinase mediated augmentation of channel translation is that encoded by the KCNE1 and KCNE2 genes -- minK and MiRP1 [XREF_BIBR, XREF_BIBR]."
KCNH2 affects INS
| 6
KCNH2 inhibits INS.
| 5
KCNH2 inhibits INS. 5 / 5
| 5
reach
"Pharmacological Kv11.1 blockade (dofetilide) in rats had similar effects and inhibition of hERG in beta and L cells directly increased insulin and GLP-1 secretion up to 50%."
reach
"Selective blockage of hERG K + channels increased firing frequency and insulin secretion in human beta cells."
reach
"In the latter extensive study, inhibition of herg channels was shown to have mechanistically distinct, but physiologically complementary, functions to enhance insulin secretion from beta cells and inhibit glucagon secretion from alpha-cells."
reach
"We also show that inhibition of hERG directly increases secretion of both insulin and GLP-1 from cultured beta and L cells, respectively."
reach
"Pharmacological Kv11.1 blockade (dofetilide) in rats had similar effects and inhibition of hERG in beta and L cells directly increased insulin and GLP-1 secretion by up to 50%."
KCNH2 activates INS.
| 1
KCNH2 activates INS. 1 / 1
| 1
reach
"Furthermore, we assessed the effect of the variants in hERG on glucose stimulated insulin secretion."
KCNH2 affects CTSG
| 6
| 5
sparser
"This may explain why the cg form of hERG is decreased during hypoxia but results in ER retention in the case of mutants."
sparser
"Taken together these results suggest that hypoxia inhibits maturation of the hERG cg form to the fg form, which does not result in an increased degradation rate nor in accumulation of the ER form."
sparser
"More importantly, addition of MnTMPyP during hypoxia restored Hsp90 interaction with cg form of hERG (lane 3 vs lane 4, xref )."
sparser
"Considering that 60% of the cg form of wild type hERG is processed to the fg form and the remaining 40% cg form is degraded by the ubiquitin proteasome pathway [17] , we examined whether the decreased expression of hERG during hypoxia is due to accelerated degradation of the cg form."
sparser
"Exposure of cells to hypoxia at lower temperatures (30°C and 23°C), fully restored the expression of the cg form of hERG to normoxic levels ( xref )."
HSP90 binds CTSG and KCNH2. 1 / 1
| 1
sparser
"More importantly, addition of MnTMPyP during hypoxia restored Hsp90 interaction with cg form of hERG (lane 3 vs lane 4, xref )."
KCNH2 affects BeKm-1
| 6
| 6
reach
"Therefore, these aspects are where we begin to characterize BeKm-1 and HERG interaction and to deduce the mechanism of toxin action.We examine the effects of 1-1000 nM BeKm-1 on the HERG current amplitude, using the same voltage clamp protocol and data analysis as those described for Fig. 2."
reach
"This result is consistent with our hypothesis that the structure of the S5-P linker is highly dynamic, and can be easily perturbed by mutations, toxin binding, or conformational changes in other parts of the protein.The structural model presented here not only matches seven out of eight pairs of interacting residues identified in the mutant cycle analysis, but also provides mechanistic insights into the unique features of BeKm-1 and hERG interaction."
reach
"To study the mechanism of BeKm-1 action, we characterize BeKm-1 and HERG interaction in terms of its sensitivity to changes in the extracellular or intracellular ionic composition and to changes in membrane voltage."
reach
"The models were further restrained based on mutant cycle analysis of BeKm-1 and hERG interactions."
reach
"It is important to point out that although such a strong state dependence of BeKm-1 and hERG interactions appears similar to that of " gating modifying toxins " that bind to the S3-S4 linkers of target channels (43,44), the BeKm-1 binding site is in the outer vestibule region of the hERG channel."
reach
"Starting from the hERG and BeKm-1 structures, a considerably reasonable BeKm-1 and hERG complex structure was then screened out and identified by protein protein docking, molecular dynamics (MD) simulations, and calculation of relative binding free energies."
KCNH2 affects AKAP5
| 4 2
PKA binds AKAP5 and KCNH2. 4 / 4
| 4
sparser
"The HERG channel protein, AKAP5, and PKA interacted with each other and appeared to form intracellular complexes."
sparser
"The HERG channel protein, AKAP5, and PKA interacted with each other and appeared to form intracellular complexes."
sparser
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
sparser
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
| 2
reach
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
reach
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
HSPA8 affects KCNH2
2 | 1 3
HSPA8 binds KCNH2.
2 | 1
2 |
biogrid
No evidence text available
biogrid
No evidence text available
HSPA binds HSPA8 and KCNH2. 1 / 1
| 1
sparser
"Interestingly, although both Hsp70 and Hsc70 associated with hERG channels, it was reported that Hsp70 enhanced the maturation of hERG channels while Hsc70 suppressed their maturation xref ."
HSPA8 activates KCNH2.
| 2
HSPA8 activates KCNH2. 1 / 1
| 1
reach
"Furthermore, it is possible that combined manipulation of HSC70, HSP70 and DNAJA1 could enhance their assistance of hERG folding, for at least some of the LQT2 mutants."
HSPA8 activates mutated KCNH2. 1 / 1
| 1
reach
"Knockdown of Hsc70 by small interfering RNA or heat shock prevented degradation of mutant hERG proteins with mutations in intracellular domains."
HSPA8 decreases the amount of KCNH2.
| 1
HSPA8 decreases the amount of KCNH2. 1 / 1
| 1
reach
"Knockdown of HSP70 reduced overall levels of WT hERG, but knockdown of HSC70 increased hERG levels."
Glu-Phe-Val affects KCNH2
| 3 3
| 3 3
sparser
"Most drugs that clinically prolong the QTc interval are inhibitors of the rapid component of the delayed rectifier current which is encoded by the hERG gene. xref A concentration-dependent inhibition of I hERG by EFV was observed with an IC 50 estimated to be approximately 0.2 µg/mL (i.e. unbound EFV IC 50 )."
sparser
"The observed concentration-response relationship and the gene-dose effect in the clinical trial coupled with the in vitro demonstration of EFV induced hERG inhibition were important findings to support the observed QTc prolongation in the relatively small number of CYP2B6*6 homozygotes."
reach
"EFV concentrations exceeding 0.4 microg/mL significantly inhibited outward hERG tail currents (P < 0.05)."
reach
"The observed concentration response relationship and the gene-dose effect in the clinical trial coupled with the in vitro demonstration of EFV induced hERG inhibition were important findings to support the observed QTc prolongation in the relatively small number of CYP2B6 * 6 homozygotes."
sparser
"EFV also inhibited inward and outward I hERG when applied to the culture media for 24 hours."
reach
"EFV concentrations exceeding 0.4 mug/mL significantly inhibited outward hERG tail currents (P < 0.05)."
FOXH1 affects KCNH2
| 6
FOXH1 inhibits KCNH2. 6 / 6
| 6
sparser
"Although lowering K + o accelerates the fast inactivation of hERG channels ( xref , xref ; xref ), and this effect was initially thought to be responsible for the effect of K + o on the hERG current magnitude ( xref ), a quantitative analysis by xref suggested that the changed fast-inactivation rate is not responsible for the altered current amplitude."
sparser
"The structural analysis indicates that KCNQ1 Val162Met is oriented away from functionally important regions, while Ser55Leu is positioned at domains critical for KCNH2 fast inactivation."
sparser
"Fast inactivation of HERG and the resulting rectification are partly responsible for the prolonged plateau phase typical of ventricular action potentials."
sparser
"Due to fast inactivation of hERG1 channels, strong depolarizations elicited rather small outward currents, whereas subsequent repolarization to −120 mV led to large slowly deactivating inward tail currents ( xref )."
sparser
"Interestingly, when residue Ile470 is mutated to a tyrosine in Shaker , an inverted inactivating phenotype was observed, reminiscent of the fast inactivation of hERG channels xref ."
sparser
"In the absence of drug, the I - V relationship exhibited the characteristic bell-shaped curve increasing from −40 to 0 mV, and owing to the fast C-type inactivation of HERG channels, it decreased with further depolarization."
ERMAP affects KCNH2
| 3 3
ERMAP inhibits KCNH2. 6 / 6
| 3 3
reach
"SC inhibited HERG channels in a concentration dependent manner, with an IC50 of 100-300 microM."
reach
"It is concluded that SC inhibited the transfected HERG channels by influencing the inactivation state, which is the probable anti-arrhythmic mechanism."
sparser
"As the result, it was found that SC inhibited HERG current in a concentration-dependent manner (10, 30, 100, and 300 micromol x L(-1))."
reach
"As the result, it was found that SC inhibited HERG current in a concentration dependent manner (10, 30, 100, and 300 micromol x L (-1))."
sparser
"It is concluded that SC inhibited the transfected HERG channels by influencing the inactivation state, which is the probable anti-arrhythmic mechanism."
sparser
"SC inhibited HERG channels in a concentration-dependent manner, with an IC50 of 100-300 microM."
EGFR affects KCNH2
| 3 3
EGFR binds KCNH2.
| 3 1
| 3 1
sparser
"We demonstrate for the first time that a physical and functional interaction of hERG1 with EGF-R occurs in PDAC."
reach
"As activating the mutations of Kras can concomitantly upregulate EGF-R and its downstream signalling pathways, we studied such pathway, providing evidence that hERG1 interacted with EGF-R."
sparser
"As activating the mutations of Kras can concomitantly upregulate EGF-R and its downstream signalling pathways ( xref ), we studied such pathway, providing evidence that hERG1 interacted with EGF-R. Overall, hERG1 turned out to contribute to the control of EGF-R-triggered intracellular signalling pathways, and, by this way, to the regulation of PDAC cell proliferation and migratory activity."
sparser
"These findings are of particular interest within our research field, since we demonstrated that hERG1 channel expression is significantly associated with EGFR expression in pancreatic ductal adenocarcinomas [ xref ] and colorectal cancers [ xref ]."
EGFR phosphorylates KCNH2.
| 1
EGFR phosphorylates KCNH2 on tyrosine. 1 / 1
| 1
reach
"These results indicate that the membrane protein of hERG channels is phosphorylated by EGFR kinase and Src tyrosine kinases.The potential PTK phosphorylation sites were predicted with the software NetPhos 2.0 (www.cbs.dtu.dk/cgi-bin)."
EGFR inhibits KCNH2.
| 1
EGFR inhibits KCNH2. 1 / 1
| 1
reach
"A Src family kinase inhibitor (PP2) and an EGFR kinase inhibitor (AG556) modulated hERG XREF_BIBR, but only the EGFR inhibitor regulated hEAG1 XREF_BIBR."
CTSG affects KCNH2
| 6
| 5
sparser
"This may explain why the cg form of hERG is decreased during hypoxia but results in ER retention in the case of mutants."
sparser
"Taken together these results suggest that hypoxia inhibits maturation of the hERG cg form to the fg form, which does not result in an increased degradation rate nor in accumulation of the ER form."
sparser
"More importantly, addition of MnTMPyP during hypoxia restored Hsp90 interaction with cg form of hERG (lane 3 vs lane 4, xref )."
sparser
"Considering that 60% of the cg form of wild type hERG is processed to the fg form and the remaining 40% cg form is degraded by the ubiquitin proteasome pathway [17] , we examined whether the decreased expression of hERG during hypoxia is due to accelerated degradation of the cg form."
sparser
"Exposure of cells to hypoxia at lower temperatures (30°C and 23°C), fully restored the expression of the cg form of hERG to normoxic levels ( xref )."
HSP90 binds CTSG and KCNH2. 1 / 1
| 1
sparser
"More importantly, addition of MnTMPyP during hypoxia restored Hsp90 interaction with cg form of hERG (lane 3 vs lane 4, xref )."
CAV1 affects KCNH2
| 4 2 4
CAV1 binds KCNH2.
| 3 2 1
| 3 1
reach
"Together with the findings that caveolin-1 interacts with potassium channels Kir2.1, KCNH2, and HCN4 and sodium channels Nav1.5 and Nav1.8, CAV1 becomes a strong candidate susceptibility gene for AF across different ethnic populations."
sparser
"The human inward rectifying voltage-gated HERG K + channel (Trudeau et al., xref ) interacts with caveolin-1 and reduces its activity when caveolin is up-regulated (Lin et al., xref )."
CAV1 binds HCN4, KCNH2, and KCNJ2. 1 / 1
| 1
sparser
"Together with the findings that caveolin-1 interacts with potassium channels Kir2.1, KCNH2, and HCN4 and sodium channels Nav1.5 and Nav1.8, CAV1 becomes a strong candidate susceptibility gene for AF across different ethnic populations."
CAV1 inhibits KCNH2.
| 1 2
CAV1 inhibits KCNH2. 2 / 2
| 1 2
reach
"Compounds 1-3 displayed activity as cardiac calcium channel blockers (Cav1.2) but did not inhibit the hERG potassium channel and were not cytotoxic."
reach
"The CAV1 protein colocalizes with and negatively regulates the activity of KCNH2, a potassium channel involved in cardiac repolarization; the corresponding KCNH2 gene was found to be associated with atrial fibrillation in a candidate gene association study, although not in our present analysis 14."
CAV1 decreases the amount of KCNH2.
| 1
CAV1 decreases the amount of KCNH2. 1 / 1
| 1
reach
"Cav-1, an integral membrane protein known to modulate numerous proteins at the plasma membrane including ion channels, has been reported to interact with hERG channel and negatively regulate hERG expression."
BmKKx2 affects KCNH2
| 1 5
BmKKx2 inhibits KCNH2.
| 3
BmKKx2 inhibits KCNH2. 3 / 3
| 3
reach
"BmKKx2 was found to block hERG channel with an IC 50 of 6.7 +/-1.7 nM and share similar functional surface with the known hERG channel inhibitor BeKm-1."
reach
"When scorpion toxin BmKKx2 reduced the proliferation of K562 cells, it was beneficial to investigate whether BmKKx2 would enhance erythroid differentiation of K562 cells by inhibiting the hERG potassium channel."
reach
"As shown in Figure XREF_FIG A, BmKKx2 could effectively block hERG channel with an IC 50 of 6.7 +/-1.7 nM, which was comparable to that of BeKm-1, an effective blocker of hERG channel [XREF_BIBR]."
BmKKx2 decreases the amount of KCNH2.
| 2
BmKKx2 decreases the amount of KCNH2. 2 / 2
| 2
reach
"During the K562 cell differentiation, BmKKx2 could also suppress the expression of hERG channels at both mRNA and protein levels."
reach
"BmKKx2 suppressed the expression of hERG channel during the erythroid differentiation of K562 cells."
BmKKx2 binds KCNH2.
| 1
KCNH2 binds BmKKx2. 1 / 1
| 1
sparser
"Here, the roles of these three regions were respectively investigated during the toxin BmKKx2-hERG channel interaction."
Sodium(1+) affects KCNH2
| 4 5
Sodium(1+) inhibits KCNH2.
| 4 4
| 4 4
reach
"The predictable outward tail currents recorded from WT channels in those conditions (data not shown) were small due to the fact that extracellular sodium potently inhibits hERG channels when extracellular K + is removed (33,34)."
reach
"Intracellular Sodium Inhibits HERG Current in a Manner Consistent with Voltage dependent Block and Independent of Extracellular Sodium."
reach
"Due to the possibility that these small organic counterions contributed to the inhibition produced by pergolide and sumanirole, sodium methanesulfonate and maleic acid were tested for the ability to inhibit hERG mediated currents."
reach
"Sodium channel blockers that shorten the APD, even when devoid of hERG blocking properties, can yield torsade de pointes."
Sodium(1+) activates KCNH2.
| 1
| 1
reach
"In this study we assessed the effects of drug induced late sodium current block on ECG changes caused by drug induced selective hERG potassium channel block."
Scorpion toxin BmKKx2 affects KCNH2
| 5
Scorpion toxin BmKKx2 inhibits KCNH2.
| 4
Scorpion toxin BmKKx2 inhibits KCNH2. 4 / 4
| 4
reach
"Next, we investigated whether scorpion toxin BmKKx2 could inhibit the hERG channel currents in K562 cells, a chronic myelogenous leukemic cell line experessing hERG potassium channels [XREF_BIBR - XREF_BIBR]."
reach
"HERG potassium channel blockage by scorpion toxin BmKKx2 enhances erythroid differentiation of human leukemia cells K562."
reach
"This data showed that the scorpion toxin BmKKx2 could moderately inhibit hERG channel currents in K562 cells, which is different from the nearly complete inhibition of hERG channel currents by the chemical molecules [XREF_BIBR - XREF_BIBR]."
reach
"The hERG potassium channel blockage by a new 36-residue scorpion toxin BmKKx2, a potent hERG channel blocker with IC 50 of 6.7 +/-1.7 nM, enhanced the erythroid differentiation of K562 cells."
Scorpion toxin BmKKx2 increases the amount of KCNH2.
| 1
Scorpion toxin BmKKx2 increases the amount of KCNH2. 1 / 1
| 1
reach
"Furthermore, the specific blockage of scorpion toxin BmKKx2 could suppress the expression of hERG potassium channel and decrease the Ca 2+ concentration during the erythroid differentiation of K562 cells."
| 5
Rosiglitazone inhibits KCNH2.
| 4
reach
"The present study suggests that rosiglitazone blocks HERG channels by binding to activated and inactivated channels, and rosiglitazone use should thus be carefully monitored in patients with pre-existing QT prolongation."
reach
"Blockade of human HERG K+ channels by rosiglitazone, an antidiabetic drug."
reach
"Rosiglitazone did not change the steady-state activation or inactivation curves or the activation or deactivation kinetics, implying that rosiglitazone blocks HERG channels predominantly in the open and inactivated state rather than in the closed state."
reach
"Rosiglitazone inhibited HERG channels in a concentration dependent manner, with an IC50 value of 18.8 muM and a Hill coefficient of 1.0."
| 1
reach
"Using the whole-cell patch-clamp technique, interaction between rosiglitazone and HERG in HEK293 cells was studied."
Paroxetine affects KCNH2
| 5
| 5
reach
"Although the reasons for this rare adverse event are not clear, we postulated that HERG channel blockade by paroxetine, some genetic changes, or autonomic nervous factors may have been involved in this rare event induced by paroxetine."
reach
"SSRIs can induce QTc prolongation via blockade of the delayed potassium rectifier current (IKr).7 Paroxetine blocks HERG channels that encode IKr in vitro.8 Niemeijer etal.9 reviewed categories of genetic factors related to drug induced QTc prolongation."
reach
"Blockade of HERG human K+ channels by the antidepressant drug paroxetine."
reach
"These results suggest that paroxetine blocks the HERG channels by binding to these channels in the open and inactivated states."
reach
"Paroxetine inhibited the peak tail currents of the HERG channel in a concentration dependent manner, with an IC50 value of 0.45 microM and a Hill coefficient of 0.85."
Ketanserin affects KCNH2
| 5
Ketanserin inhibits KCNH2.
| 4
| 4
reach
"In conclusion, ketanserin blocks WT HERG currents in voltage- and concentration dependent manner and preferentially blocks open-state HERG channels."
reach
"Ketanserin blocked hERG current (I (hERG)) in a concentration dependent manner (IC50 = 0.11 microM)."
reach
"The results showed that ketanserin blocked WT HERG currents in voltage- and concentration dependent manner and showed minimal tonic blockade of HERG current evaluated by the envelope of tails test."
reach
"These results suggest that ketanserin binds to and blocks the open hERG channels in the pore helix and the S6 domain; channel inactivation is also involved in the blockade of hERG channels."
Ketanserin activates KCNH2.
| 1
| 1
reach
"Ketanserin could also modulate the inactivation of HERG channel, which shifted the voltage-dependence of WT HERG channel inactivation curve from (-51.71 +/-2.15) mV to (-80.76 +/-14.98) mV (P < 0.05, n = 4)."
Fluconazole affects KCNH2
| 1 4
Fluconazole inhibits KCNH2.
| 1 3
| 1 3
sparser
"Whether fluconazole also inhibits hERG is currently unknown."
reach
"Whether fluconazole also inhibits hERG is currently unknown."
reach
"Fluconazole inhibited wild type hERG currents in a concentration dependent manner, with a half-maximum block concentration (IC (50)) of 48.2 +/-9.4 muM."
reach
"In addition, fluconazole inhibited the trafficking of hERG protein by Western blot analysis and confocal microscopy, respectively."
Fluconazole decreases the amount of KCNH2.
| 1
Fluconazole decreases the amount of KCNH2. 1 / 1
| 1
reach
"Our findings have demonstrated that the combination of fluconazole and terbinafine could also significantly reduce the expression of ERG1, 3, and 11 in the cell membrane of Candida in all concentrations tested ranging from 1.73- to 6.99-fold."
Entinostat affects KCNH2
| 5
Entinostat increases the amount of KCNH2.
| 4
Entinostat increases the amount of KCNH2. 4 / 4
| 4
reach
"Interestingly, KCNH2 and Cav1.3 protein expression levels could be partially restored by Entinostat in failing, stimulated hearts."
reach
"Entinostat treatment partially restored KCNH2 and Cav1.3 gene expressions in failing hearts, and inhibited the development of cardiac fibrosis in vivo."
reach
"KCNH2 and Cav1.3 were downregulated in response to pacing, and Entinostat was able to partly restore KCNH2 and Cav1.3 expression in failing hearts."
reach
"In a rabbit model of heart failure, Entinostat diminishes heart failure related prolongation of repolarization and partially restores KCNH2 and Cav1.3 expression."
Entinostat decreases the amount of KCNH2.
| 1
Entinostat decreases the amount of KCNH2. 1 / 1
| 1
reach
"In failing hearts, Entinostat could partially restore the reduction of Cav1.3 and KCNH2 expression."
Donepezil affects KCNH2
| 5
| 5
reach
"These results suggest that donepezil inhibited the hERG at a supratherapeutic concentration, and that it did so by preferentially binding to the activated (open and/or inactivated) states of the channels and by inhibiting the trafficking and expression of the hERG channel protein in the plasma membrane."
reach
"Donepezil inhibited the tail current of the hERG in a concentration dependent manner with an IC50 of 1.3 muM."
reach
"A fast application of donepezil during the tail currents inhibited the open state of the hERG in a concentration dependent manner with an IC50 of 2.7 muM."
reach
"The metabolites of donepezil, 6-ODD and 5-ODD, inhibited the hERG currents in a similar concentration dependent manner; the IC50 values were 1.0 and 1.5 muM, respectively."
reach
"A fast drug perfusion system demonstrated that donepezil interacted with both the open and inactivated states of the hERG."
Cocaine affects KCNH2
| 5
| 5
reach
"At clinically relevant doses, cocaine inhibits the HERG channel, but not the KvLQT1+ mink K + channel (Ferreira et al., 2001; Zhang et al., 2001)."
reach
"These results indicate that cocaine suppresses HERG, but not KvLQT1+ minK, channels by preferentially blocking activated channels, that it unblocks upon repolarization, and does so with unique ultrarapid kinetics."
reach
"Blockade of HERG by cocaine, cocaethylene, and methylecgonidine increased significantly over the voltage range where HERG activates, but became constant at voltages where HERG activation was maximal, indicating that all three drugs block open channels, but by a mechanism that is not highly sensitive to voltage per se."
reach
"Although Peles et al. [XREF_BIBR] did not find a significant correlation between methadone dose and QTc duration in their overall sample, a significant correlation was found among patients who tested positive for cocaine (r = 0.4, P = 0.003), which is known to block the HERG potassium channel that contributes to cardiac repolarization [XREF_BIBR - XREF_BIBR]."
reach
"In contrast, cocaine reversibly blocked HERG current with half-maximal block of peak tail current of 7.2 microM."
Celecoxib affects KCNH2
| 5
| 5
reach
"Inhibition of hERG Potassium Channels by Celecoxib and Its Mechanism."
reach
"Indeed, celecoxib significantly decreased the tau act of hERG below +30 mV, tau inact below +40 mV, and tau rec between -60 and -20 mV where the electrical driving forces for the respective transitions were relatively small."
reach
"Inhibition of HERG potassium channels by celecoxib and its mechanism."
reach
"Extra cellular application of celecoxib causes rapid suppression of hERG channels which induces the cardiac disturbances [XREF_BIBR]."
reach
"Celecoxib inhibited the hERG, SCN5A, KCNQ1 and KCNQ1 and MinK channels expressed in HEK-293 cells with IC 50 s of 6.0 microM, 7.5 microM, 3.5 microM and 3.7 microM respectively, and the KCND3 and KChiP2 channels expressed in CHO cells with an IC 50 of 10.6 microM."
Carvedilol affects KCNH2
| 5
Carvedilol inhibits KCNH2.
| 4
| 4
reach
"This is the first study demonstrating that carvedilol blocks HERG potassium channels."
reach
"Carvedilol at a concentration of 10 microM blocked HERG potassium tail currents by 47%."
reach
"Antiarrhythmic drug carvedilol inhibits HERG potassium channels."
reach
"Carvedilol (nonselective), propranolol (nonselective) and ICI 118551 (beta (2)-selective) inhibited HERG current in a concentration dependent manner (IC (50) 0.51, 3.9 and 9.2 microM, respectively)."
Carvedilol activates KCNH2.
| 1
| 1
reach
"Like nifekalant, amiodarone, quinidine and carvedilol, but not by dofetilide, caused the current facilitation of hERG, suggesting that the facilitation is a common effect to a subset of hERG blockers."
Carbachol affects KCNH2
| 5
Carbachol increases the amount of KCNH2.
| 2
Carbachol increases the amount of KCNH2. 2 / 2
| 2
reach
"The carbachol mediated increase in hERG expression was abolished by the selective M3 antagonist 4-DAMP (1,1-dimethyl-4-diphenylacetoxypiperidinium iodide) but not by the M2 antagonist AF-DX 116 (11 [[2-[(diethylamino) methyl]-1-piperidinyl]-acetyl] -5,11-dihydro-6H-pyrido [2,3-b] [1,4] benzodiazepine-6-one)."
reach
"Using cell biology and electrophysiological methods, we found that the muscarinic receptor agonist carbachol increased the expression and function of hERG, but not ether-a-go-go or Kv1.5 channels stably expressed in human embryonic kidney cells."
Carbachol activates KCNH2.
| 2
Carbachol activates mutated KCNH2. 2 / 2
| 2
reach
"Carbachol restored stability of the mutant hERG FLAG and facilitated cell-surface expression."
reach
"Both a M3-mAChR antagonist, 4-DAMP, and a PKC inhibitor, bisindolylmaleimide, abolished carbachol induced stabilization of the mutant hERG FLAG."
Carbachol inhibits KCNH2.
| 1
| 1
reach
"Blockade of the protein kinase C (PKC) pathway abolished the carbachol induced enhancement of hERG channels."
Caffeine affects KCNH2
| 5
| 5
reach
"Further experiments showed caffeine directly blocks hERG in an open state dependent manner."
reach
"Caffeine dependent inhibition of hERG current is not altered by raising cAMP with forskolin, buffering cytosolic calcium with 1,2-bis (2-aminophenoxy) ethane-N, N, N ', N '-tetraacetic acid, or inhibition of protein kinase C. Thus, the effects of caffeine are unlikely to be mediated by cAMP or intracellular calcium dependent mechanisms."
reach
"Thus, caffeine attenuates hERG currents by binding to a drug receptor located within the inner cavity of the channel."
reach
"Propoxyphene blocked HERG currents by slowing down channel activation and accelerating channel deactivation kinetics (Ulens et al., 1999)."
reach
"Propoxyphene blocked HERG currents by slowing down channel activation and accelerating channel deactivation kinetics (Ulens et al., 1999)."
| 5
reach
"IC (50) for amitriptyline block of HERG current was progressively decreased according to depolarization : IC (50) values at -30, -10, +10 and +30 mV were 23.0, 8.71, 5.96 and 4.66 microM, respectively."
reach
"For example, amitriptyline, imipramine, and doxepin block the HERG channel with the IC 50 s of 10 muM, 3.4 muM, and 6.5 muM, respectively (Cavalli et al., 2002; Duncan et al., 2007)."
reach
"Block of HERG by amitriptyline was use dependent : exhibiting a much faster block at higher activation frequency."
reach
"The decrease became more pronounced at more positive potential, suggesting that the block of HERG by amitriptyline is voltage dependent."
reach
"Amitriptyline, quinidine, compound A, fluoxetine and imipramine inhibited hERG with IC (50) s (paired values denote constantly cultured and frozen, respectively) of 4.8 +/-0.4 and 5.1 +/-0.4, 1.4 +/-0.1 and 1.1 +/-0.1, 24.4 +/-2.4 and 21.9 +/-1.8, 2.1 +/-0.4 and 2.1 +/-0.1, 5.2 +/-0.4 and 4.0 +/-0.2 muM."
Ajmalinium affects KCNH2
| 5
| 5
reach
"Binding of ajmaline to inactivated HERG channels may also be possible."
reach
"Ajmaline blocked HERG channels in the open, but not in the closed states."
reach
"Ivabradine, ajmaline and mexiletine inhibited KCNH2 channel currents significantly, which may underlie their APD prolonging effects."
reach
"Ajmaline blocked HERG currents with an IC (50) of 1.0 micromol/l in HEK cells and 42.3 micromol/l in Xenopus oocytes."
reach
"Class Ia anti-arrhythmic drug ajmaline blocks HERG potassium channels : mode of action."
ST8SIA2 affects KCNH2
| 5
ST8SIA2 inhibits KCNH2.
| 2
| 2
reach
"STX Reduces hERG K + Currents."
reach
"STX decreased hERG K + currents by stabilizing closed channel states visualized as shifts in the voltage dependence of channel opening to more depolarized membrane potentials."
ST8SIA2 activates KCNH2.
| 2
ST8SIA2 activates KCNH2. 2 / 2
| 2
reach
"The behavior of STX modulating hERG K + channels is in some regards similar to hanatoxin (a Kv2.1 K + channel gating modifier) and omega-Aga-IVA toxin (a calcium channel gating modifier)."
reach
"STX Modulates hERG K + Channel Gating."
ST8SIA2 binds KCNH2.
| 1
| 1
reach
"Large depolarizations, e.g., 50 mV, applied to the STX bound hERG K + channel, caused the STX bound channel to open."
PSMD4 affects KCNH2
| 3 2
PSMD4 binds KCNH2.
| 3
| 2
sparser
"In addition, AF has been associated with rare gain of function mutations in KCNQ1, hERG and KCNJ2 causing the short QT syndrome and sudden death."
sparser
"This is largely due to reduced L-type Ca 2+ current, although rare gain-of-function mutations in KCNQ1 [ xref ], hERG [ xref ], Kir2.1 [ xref ] and KCNE ancillary subunits [ xref ] have also been associated with AF due to increases in channel conductance."
| 1
sparser
"Indeed, KCNH2 has been associated with AF in a candidate-gene association study. xref "
PSMD4 inhibits KCNH2.
| 2
PSMD4 inhibits KCNH2. 2 / 2
| 2
reach
"For example, drugs used to treat AF, such as quinidine and sotalol, block the hERG potassium channel and increase the APD."
reach
"Application of AF 3013, the active metabolite of prulifloxacin, produced only minor reduction of HERG current amplitude (tail current = -40 mV), producing a maximum blockade of 12.3 +/- 3.3% at the highest concentration tested (335 microM)."
PROC affects KCNH2
| 2 3
PROC inhibits KCNH2.
| 2 2
PROC inhibits KCNH2. 4 / 4
| 2 2
reach
"Thus, relatively little I HERG blockade by PROC (~ 10%) might normally be anticipated to occur at clinically relevant concentrations.The comparatively lower potency blockade of I HERG for PROC than that observed previously for either QUIN and DISO under similar conditions [17,20] might be explained if the mechanism by which PROC blocks I HERG differs from those of the other two Class Ia agents."
sparser
"Second, this study details for the first time the mechanism of I HERG inhibition by PROC."
sparser
"First, they provide information regarding potency of inhibition of I HERG by PROC under conditions that allow direct and reliable comparison with previous data on the other Class Ia agents DISO and QUIN."
reach
"In order to assess I HERG blockade by PROC, the voltage protocol shown in Fig. 1A (lower trace) was employed and I HERG tail amplitude was measured on repolarisation to -40 mV after voltage commands to +20 mV."
PROC binds KCNH2.
| 1
| 1
reach
"Therefore, in this study, interactions between PROC and HERG K (+) channels were investigated, with particular reference to potency and mechanism of drug action."
PPY affects KCNH2
| 5
PPY inhibits KCNH2.
| 4
PPY inhibits KCNH2. 4 / 4
| 4
reach
"Acidic pH inhibits hERG channel maximal conductance and accelerates deactivation, likely by different mechanisms."
reach
"For each of the three expression conditions, pH 6.3 accelerated I hERG deactivation, with both fast and slow time-constants of deactivation being markedly reduced."
reach
"As reported previously (41,42), acidic pH accelerated deactivation of WT hERG."
reach
"Our findings show that low external pH accelerates hERG channel deactivation by altering both fast and slow reconfigurations of the voltage sensor."
PPY activates KCNH2.
| 1
PPY activates KCNH2. 1 / 1
| 1
reach
"For example, Wang et al. reported that low pH increased the extent and speed of dofetilide induced block in hERG currents XREF_BIBR."
PLA1A affects KCNH2
| 1 4
PLA1A inhibits KCNH2.
| 3
PLA1A inhibits mutated KCNH2. 2 / 2
| 2
reach
"In heterozygous Q1070X carriers, NMD eliminates most of the mutant HERG mRNA and leads to haploinsufficiency, thereby reducing the dominant negative effect of the mutant protein."
reach
"In the present study, we tested the hypothesis that inhibition of NMD can restore functional expression of the hERG mutations associated with long QT syndrome."
PLA1A inhibits KCNH2. 1 / 1
| 1
reach
"Thus, in homozygous Q1070X patients, most hERG mRNA transcripts are degraded by NMD before they form functional channels leading to a severe clinical phenotype [XREF_BIBR, XREF_BIBR]."
PLA1A binds KCNH2.
| 1
| 1
sparser
"When combined with environmental triggers and genetic modifiers, LQT2 frameshift mutations associated with NMD can manifest with a severe clinical phenotype."
PLA1A activates KCNH2.
| 1
PLA1A activates KCNH2. 1 / 1
| 1
reach
"In contrast, when we employed a minigene construct that could generate the full-length hERG mRNA and protein, and importantly, could undergo RNA splicing, the same mutation caused a marked reduction in mutant protein levels and hERG current, a finding consistent with degradation of mutant mRNA by NMD."
| 5
KCNH2 activates localization.
| 4
| 3
reach
"XREF_BIBR that HERG increases membrane localization of KCNQ1 in transfected CHO cells, we hypothesized that the " I HERG booster " effect mediated by KCNQ1 may be linked to an event during the biogenesis of the channel, rather than through regulation of HERG biophysical properties at the membrane."
reach
"Moreover, overexpression of hERG1 in MG-63 cells also led to increased nuclear localization of NF-kappaB p65."
reach
"Immunoblots and confocal microscopy indicated increased plasma membrane localization of KCNH2 alpha-subunits in cells cotransfected with KCNQ1-WT plasmid, while total KCNH2 protein synthesis and KCNH2 glycosylation remained unaffected, which suggests a chaperone effect of KCNQ1-WT to enhance the membrane localization of KCNH2."
KCNH2 bound to KCNQ1 activates localization. 1 / 1
| 1
reach
"In 2004, Ehrlich et al. demonstrated that the alpha subunit of I Ks KvLQT1 could interact with the alpha subunit of I Kr hERG to enhance hERG current densities and increase hERG protein membrane localization 20."
KCNH2 inhibits localization.
| 1
| 1
reach
"This is accomplished without any effect on HERG1 current.To address whether the mutations in KCNQ1 and HERG1 impede the subcellular localization of the channels, immunocytochemical analysis of transfected COS-1 cells was conducted."
| 4 1
| 3 1
| 3 1
sparser
"The number of carbocyclic aromatic rings is correlated with lower solubility, higher logD, higher plasma protein binding, hERG inhibition and inhibition of some major cytochrome P450s (3A4, 2C9, 2C19). (3) For compounds required to reach the CNS, there are additional criteria."
sparser
"Compound 24 demonstrated overall favorable in vitro safety profiles with respect to CYP isoform and hERG inhibition."
reach
"In this review we discuss the utility of protein-structure-based design and docking approaches aimed at overcoming issues related to plasma protein binding, active transport via P-glycoprotein, hERG channel mediated cardiotoxicity and cytochrome P450 inhibition, metabolism and induction."
sparser
"Results demonstrated weak hERG inhibition (50.1% inhibition at 25 μM) and marginal inhibition of CYP enzymes at 10 μM ()."
| 1
sparser
"To identify off-target effects we investigated whether sc1o interacts with safety-relevant molecules such as cytochrome P450 (CYP) enzymes, phosphodiesterases (PDE), histone deacteylases (HDAC) and human ether-a-go-go related gene ( h ERG)."
KCNH2 affects VEGF
| 1 4
KCNH2 activates VEGF.
| 4
KCNH2 activates VEGF. 4 / 4
| 4
reach
"In addition, we present evidence that, in GBM cell lines, hERG1 channel activity actively contributes to malignancy by promoting vascular endothelial growth factor secretion, thus stimulating the neoangiogenesis typical of high-grade gliomas."
reach
"HERG1 channels are overexpressed in glioblastoma multiforme and modulate VEGF secretion in glioblastoma cell lines."
reach
"HERG1 can increase oncogenic potential in leukemias by affecting one of several ways facilitating leukemogenesis : (1) balance between proliferation and cell death; (2) invasiveness, depending on the fine balance between adhesion and motility, the latter being in turn dependent on polarized volume changes; (3) resistance to chemotherapy [XREF_BIBR, XREF_BIBR]; (4) angiogenesis, via secretion of vascular endothelial growth factor (VEGF) and positively feedbacked microvesicles release [XREF_BIBR, XREF_BIBR]."
reach
"For instance, in human acute myeloid leukemia cells, hERG1 channels appear to mediate the vascular endothelial growth factor receptor-1-dependent cell migration and invasion, both in vitro and in vivo."
KCNH2 binds VEGF.
| 1
VEGF binds CASP3 and KCNH2. 1 / 1
| 1
sparser
"However, these results are still tentative and imperfect, and the question how hERG mRNA or hERG protein physiologically interacts with VEGF or caspase-3 is unanswered."
KCNH2 affects RPS6
| 4 1
KCNH2 binds RPS6.
| 4
| 3
sparser
"Thus, it seems reasonable to propose that lidocaine is also likely to interact with S6 aromatic residues of hERG and our docking data ( xref and S5) support such a conclusion."
sparser
"Altogether, these observations confirmed that the paradoxical activation effect initially observed when S4-S5 L (0) peptide was co-transfected with WT hERG channel was not due to an interaction of this peptide with the S6 T region of hERG."
sparser
"The direct block was mediated by drug binding to S6 domain of the hERG subunit, while trafficking deficiency was mediated by binding to a different site or a related protein. xref In this study, we used site-directed mutagenesis to test whether Y652A or F656V mutation alter the BBR sensitivity of hERG after long-term treatment."
RPS6 binds KCNH2 and cooH. 1 / 1
| 1
sparser
"Furthermore, other channel segments might be involved in gating since several studies have provided evidence for interactions between the S4–S5 linker and residues in the COOH-terminal part of S6 in HERG, HCN, and Shaker ( xref ; xref ; xref ; xref )."
KCNH2 inhibits RPS6.
| 1
KCNH2 inhibits RPS6. 1 / 1
| 1
reach
"This study reports that the affinity of HERG1 A for dofetilide is decreased from 0.125 +/- 0.003 microM for wild-type (WT) channels to 15 +/- 3 microM for F656V, a mutation in the COOH-terminal half of the S6."
KCNH2 affects PI3K
| 2 3
KCNH2 binds PI3K.
| 1 1
| 1
reach
"The beta 1 / hERG1 and PI3K complex, through Akt, induces HIF (s) transcriptional activation."
| 1
sparser
"Furthermore, by sequestering the channel in the closed conformation, Cla inhibited the formation of a macromolecular complex between hERG1 and the p85 subunit of PI3K. This strongly reduced Akt phosphorylation, and stimulated the p53-dependent cell apoptosis, as witnessed by late caspase activation."
KCNH2 activates PI3K.
| 2
KCNH2 activates PI3K. 2 / 2
| 2
reach
"HERG1 recruits and activates PI3K and Akt."
reach
"HERG1 promotes esophageal squamous cell carcinoma growth and metastasis through TXNDC5 by activating the PI3K and AKT pathway."
KCNH2 phosphorylates PI3K.
| 1
KCNH2 phosphorylates PI3K. 1 / 1
| 1
sparser
"In addition to the increase in hERG1 currents, β1 activation leads hERG1 to form a macromolecular membrane complex that comprises the β 1 integrin subunit and the p85 subunit of PI3K. Recruitment of p85 inside the complex has two major consequences: i) it facilitates translocation of PI3K towards its physiological membrane substrates; ii) it determines a hERG1-dependent PI3K phosphorylation, without the need of intermediate cytosolic proteins (e.g. FAK, ILK, Src)."
KCNH2 affects LQTS type 2
| 5
KCNH2 activates LQTS type 2. 5 / 5
| 5
reach
"LQTS type 2 (LQTS2) is caused by mutations in the KCNH2 gene, leading to a reduction of the rapidly activating delayed rectifier K + current and loss of human ether-A -go-go-related gene (hERG) channel function by different mechanisms."
reach
"LQTS type 2 (LQT2) is caused by mutations in KCNH2, which encodes the potassium channel hERG."
reach
"Mutations in hERG (also known as KCNH2), cause LQTS type 2 (LQT2) because of impaired function of the pore forming alpha-subunit of the voltage gated K v 11.1 channel, which is a key player of repolarization in cardiac cells."
reach
"Mutations in HERG, located on chromosome 7q35-q36, cause LQTS type 2 (LQT2) and represent 45% of the known LQTS defects."
reach
"LQTS type 2 (LQT2) is caused by mutations in HERG XREF_BIBR."
KCNH2 affects LQT
| 5
KCNH2 activates LQT.
| 3
Mutated KCNH2 activates LQT. 2 / 2
| 2
reach
"The identification of intragenic dele- tions of HERG in two LQT families suggests that HERG mutations can cause LQT."
reach
"De Novo Mutation of HERG in a Sporadic Case of LQT To substantiate that HERG mutations cause LQT, we used SSCP analysis to screen for mutations in sporadic cases."
KCNH2 activates LQT. 1 / 1
| 1
reach
"Mutations in KVLQT1, HERG, SCN5A, and KCNE1, genes encoding cardiac ion channels, cause LQT."
KCNH2 inhibits LQT.
| 1
KCNH2 inhibits LQT. 1 / 1
| 1
reach
"Acquired LQT is far more common and is most often caused by block of cardiac HERG K (+) channels by commonly used medications [Roden, D. M., Lazzara, R., Rosen, M., Schwartz, P. J., Towbin, J. & Vincent, G. M. (1996) Circulation 94, 1996-2012]."
KCNH2 binds LQT.
| 1
KCNH2 binds LQT. 1 / 1
| 1
reach
"Three HERG Point Mutations Associated with LQT To identify additional HERG mutations in LQT2, we contin- ued SSCP analyses in linked kindreds and sporadic cases."
KCNH2 affects GCG
| 5
KCNH2 inhibits GCG.
| 4
KCNH2 inhibits GCG. 4 / 4
| 4
reach
"Pharmacological Kv11.1 blockade (dofetilide) in rats had similar effects and inhibition of hERG in beta and L cells directly increased insulin and GLP-1 secretion up to 50%."
reach
"Pharmacological Kv11.1 blockade (dofetilide) in rats had similar effects and inhibition of hERG in beta and L cells directly increased insulin and GLP-1 secretion by up to 50%."
reach
"We also show that inhibition of hERG directly increases secretion of both insulin and GLP-1 from cultured beta and L cells, respectively."
reach
"Moreover, small interfering RNA mediated knockdown of Kcnh2 in the GLUTag enteroendocrine cell line increased the magnitude of glucose stimulated GLP-1 release, implicating a direct role for hERG in control of GLP-1 secretion."
KCNH2 activates GCG.
| 1
KCNH2 activates GCG. 1 / 1
| 1
reach
"In the latter extensive study, inhibition of herg channels was shown to have mechanistically distinct, but physiologically complementary, functions to enhance insulin secretion from beta cells and inhibit glucagon secretion from alpha-cells."
KCNH2 affects CnErg1
| 5
| 5
reach
"Electrostatic interactions are much less important for ErgTx1 binding to HERG channels than for AgTx2 binding to Shake r channels, although these interactions can not be ruled out completely."
reach
"Analysis of the kinetics of CnErg1 interaction with hERG indicated that CnErg1 binding is not diffusion limited."
reach
"We have also examined the temperature-dependence of CnErg1 binding to hERG."
reach
"It is therefore likely that hydrophobic interactions will play a more important role in Ergtoxin binding to HERG than is the case for other scorpion toxins binding to their respective ion-channel receptors."
reach
"The binding of Ergtoxin to HERG channels, however, is not influenced by the extracellular [K +] and does not involve strong electrostatic interactions [12]."
Hsp90 inhibitors affects KCNH2
| 5
Hsp90 inhibitors activates KCNH2.
| 3
Hsp90 inhibitors activates KCNH2. 3 / 3
| 3
reach
"Hsp90 inhibitors have been shown to disrupt proper trafficking and function of hERG [XREF_BIBR]."
reach
"XREF_BIBR - XREF_BIBR Hsp90 inhibitors have been shown to disrupt hERG function and cause a reduction in hERG related membrane currents in in-vitro studies."
reach
"Previously, it was shown that Hsp90 inhibitors, such as geldanamycin and radicicol, cause both a dose dependent reduction in the hERG associated current amplitudes in patch clamp experiments and in the trafficking efficiency of hERG, or the ratio of fg hERG over total hERG (fg+ cg) (XREF_FIG)."
Hsp90 inhibitors inhibits KCNH2.
| 1
Hsp90 inhibitors inhibits KCNH2. 1 / 1
| 1
reach
"Previously, it was shown that Hsp90 inhibitors, such as geldanamycin and radicicol, cause both a dose dependent reduction in the hERG associated current amplitudes in patch clamp experiments and in the trafficking efficiency of hERG, or the ratio of fg hERG over total hERG (fg+ cg) (XREF_FIG)."
Hsp90 inhibitors glycosylates KCNH2.
| 1
Hsp90 inhibitors leads to the glycosylation of KCNH2. 1 / 1
| 1
reach
"XREF_BIBR - XREF_BIBR Hsp90 inhibitors appear to prevent the glycosylation of hERG and halt translocation from the ER to the cell surface, which results in non functional hERG accumulation in the cytosol."
CAV3 affects KCNH2
2 | 1 2
CAV3 binds KCNH2.
2 | 1 1
2 | 1
biogrid
No evidence text available
reach
"Our data demonstrate that Cav3, hERG, and ubiquitin-ligase Nedd4-2 interact with each other and form a complex."
biogrid
No evidence text available
| 1
sparser
"We showed that ATP1B1 interacts with KCNH2, CACNA1C, KCNQ1and CAV3."
CAV3 decreases the amount of KCNH2.
| 1
CAV3 decreases the amount of KCNH2. 1 / 1
| 1
reach
"Cav3 decreases the expression of HERG via recruiting Nedd4-2 from the cytosol to the membrane and prevents its interaction with mature HERG channels [XREF_BIBR]."
| 1 4
reach
"Roxithromycin was found to inhibit wild-type (WT) hERG currents in a concentration dependent manner with a half-maximum block concentration (IC50) of 55.8 +/- 9.1 mumol/L."
sparser
"In addition, roxithromycin inhibits hERG channels and disrupts hERG protein trafficking [ xref ] (Table xref )."
reach
"Roxithromycin also inhibited the trafficking of hERG protein to the cell membrane, as confirmed by Western blot analysis and confocal microscopy."
reach
"In addition, roxithromycin inhibits hERG channels and disrupts hERG protein trafficking [XREF_BIBR]."
reach
"Mutations in drug binding sites (Y652A or F656C) of the hERG channel were found to attenuate hERG current blockage by roxithromycin, but did not significantly alter the disruption of trafficking."
Zolpidem affects KCNH2
| 4
Zolpidem inhibits KCNH2.
| 3
| 3
reach
"Zolpidem caused acute hERG channel blockade in oocytes (IC (50) = 61.5 muM) and in HEK 293cells (IC (50) = 65.5 muM)."
reach
"In contrast to the majority of hERG inhibitors, hERG cell surface trafficking was not impaired by zolpidem."
reach
"Zolpidem inhibits cardiac hERG K (+) channels."
Zolpidem activates KCNH2.
| 1
| 1
reach
"Zolpidem accelerated hERG channel inactivation but did not affect I-V relationships of steady-state activation and inactivation."
Ziprasidone affects KCNH2
| 4
| 4
reach
"In conclusion, ziprasidone preferentially binds to and blocks open hERG channels."
reach
"In this study, we examined the biophysical properties and the molecular determinants of the ziprasidone block of wild-type hERG potassium channels stably expressed in HEK-293 cells or wild-type and mutant hERG channels expressed in Xenopus oocytes."
reach
"Although ziprasidone has been shown to block the HERG channel in vitro and prolong the QTc interval in vivo in man, there have been no reported cases of TdP associated with its clinical use to date."
reach
"In stably transfected HEK-293 cells, ziprasidone blocked wild-type hERG current in a voltage- and concentration dependent manner (IC (50) = 120nM, 0mV, 37 degrees C)."
Vanoxerine affects KCNH2
| 4
Vanoxerine inhibits KCNH2.
| 2
| 2
reach
"Verapamil and vanoxerine (GBR12909) which produce direct block of hERG current do not inhibit trafficking of wild type hERG after overnight exposure."
reach
"Vanoxerine produces potent block of cardiac hERG, sodium, and L-type calcium channels."
Vanoxerine increases the amount of KCNH2.
| 2
Vanoxerine increases the amount of KCNH2. 2 / 2
| 2
reach
"It is possible that the increase in hERG surface expression by vanoxerine could mitigate its channel blocking properties."
reach
"Over the same concentration range, vanoxerine increased surface expression of wild type hERG by 30% and dofetilide by 26%."
Terazosin affects KCNH2
| 4
Terazosin inhibits KCNH2.
| 2
| 2
reach
"In conclusion, this study demonstrates that HERG potassium channels are blocked by prazosin, doxazosin, and terazosin."
reach
"The mechanistic role of small molecule induced hERG protein suppression in apoptosis of GB cells was tested using terazosin, an alpha 1 -adrenoceptor antagonist that reduces hERG currents in culture cells XREF_BIBR."
Terazosin increases the amount of KCNH2.
| 1
Terazosin increases the amount of KCNH2. 1 / 1
| 1
reach
"In the presence of doxazosin, terazosin rescued hERG protein expression and protected from apoptosis (XREF_FIG)."
Terazosin decreases the amount of KCNH2.
| 1
Terazosin decreases the amount of KCNH2. 1 / 1
| 1
reach
"Terazosin did not reduce hERG protein expression (XREF_FIG) and did not show pro apoptotic effects (XREF_FIG) despite structural similarities between terazosin and doxazosin."
Sensor affects KCNH2
| 4
Sensor inhibits KCNH2.
| 2
Sensor inhibits KCNH2. 2 / 2
| 2
reach
"Extracellular protons accelerate hERG channel deactivation by destabilizing voltage sensor relaxation."
reach
"We interpret this to indicate that stabilization of the activated voltage sensor limits the return of hERG channels to rest."
Sensor activates KCNH2.
| 2
Sensor activates KCNH2. 2 / 2
| 2
reach
"Using several mutations as tools, we define key steps in the deactivation pathway that limit voltage sensor return to produce the physiologically relevant resurgent hERG current in cardiomyocytes.Wild-type (WT) and mutant hERG channel constructs were prepared for expression in Xenopus laevis oocytes as described in Cheng et al. (27)."
reach
"The fourth transmembrane segment (S4) contributes to form the voltage sensor domain (VSD), which sharply contributes to hERG1 biophysical properties [XREF_BIBR]."
Seliciclib affects KCNH2
| 1 3
| 1 3
sparser
"R-roscovitine inhibits open hERG channels but does not become trapped in the pore."
reach
"R-roscovitine quickly and reversibly blocks hERG at clinically relevant concentrations."
reach
"R-roscovitine inhibits open hERG channels but does not become trapped in the pore."
reach
"In the present study we show that R-roscovitine blocks HERG potassium current (human embryonic kidney-293 cells stably expressing HERG) at clinically relevant concentrations."
Saquinavir affects KCNH2
| 4
| 4
reach
"Anson et al. [XREF_BIBR] demonstrated that RTV, LPV, NFV, and saquinavir substantially suppress HERG currents expressed in HEK293 cells and the corresponding endogenous current, I Kr, in mouse neonatal myocytes."
reach
"In silico test to measure whether Saquinavir and its analogs may (not) block the HERG K + ion channels of the heart suggest S2 to be a better molecule with minimum HERG inhibition value of 0.12 followed by S1 (0.13) and Saquinavir drug (0.14)."
reach
"Drug induced QT prolongation is usually caused by block of human ether-a-go-go-related gene (HERG) potassium channels, and we showed that lopinavir, nelfinavir, ritonavir, and saquinavir caused dose dependent block of HERG channels heterologously expressed in HEK293 cells in vitro."
reach
"Thus, a potentially complex contribution and interplay between direct hERG blocking and hERG trafficking by saquinavir may potentially contribute to the day-to-day variability seen in mean maximum incrementQTcF dense."
Resveratrol affects KCNH2
| 4
Resveratrol inhibits KCNH2.
| 3
| 3
reach
"In this study, we demonstrated that 1) cav-1 participates in BBR induced hERG deficiency on cell surface; 2) residues Tyr652 and Phe656, essential components of hERG binding sites, mediate hERG surface expression inhibition by BBR incubation; and 3) fexofenadine and resveratrol can shorten APD of ventricular cardiomyocytes prolonged by BBR."
reach
"In XREF_FIG, application of 10 muM resveratrol and 1 muM fexofenadine rescued hERG tail current reduction in the presence of 10 muM BBR."
reach
"Resveratrol is able to rescue the trafficking inhibition of hERG and relieve the ER stress triggered by arsenic trioxide."
Resveratrol activates KCNH2.
| 1
| 1
reach
"The rescuable function and mechanism of resveratrol on As2O3 induced hERG K+ channel deficiency."
Primaquine affects KCNH2
| 1 3
| 1 3
reach
"Blockade of hERG by primaquine was also found to be time dependent, occurring rather rapidly."
reach
"In conclusion, these results indicate that primaquine preferentially inhibits the hERG potassium channel, but blockade of hERG channel by primaquine may not be related to the S6 residue or the pore region, but may be induced through other pathways such as binding other region or effect by drug binding receptor which indicates a need for further exploration."
sparser
"Primaquine inhibited hERG current in a concentration-dependent manner with the half-maximal inhibitory concentration (IC(50)) of 21.5 microM."
reach
"Primaquine inhibited hERG current in a concentration dependent manner with the half-maximal inhibitory concentration (IC (50)) of 21.5 microM."
| 1 1 3
| 1 1 3
reach
"Class 3 inhibition of hERG K+ channel by caffeic acid phenethyl ester (CAPE) and curcumin."
reach
"CAPE dose-dependently decreased repolarization tail current of hERG (I hERG, tail; IC50, 10.6 +/-0.5 muM)."
sparser
"The CAPE inhibition of I hERG,tail was not attenuated in the pore-blocker site mutants of hERG (Y652A and F656A)."
reach
"Taken together, CAPE inhibits hERG channel by class 3 mechanism, i.e., modification of gating, not by blocking the pore."
Nefazodone affects KCNH2
| 4
| 4
reach
"Nefazodone inhibited the hERG channel in a concentration dependent manner with an IC50 of 45.3 nM in HEK-293 cells."
reach
"Nefazodone inhibited hERG channel activity in our system."
reach
"However, nefazodone induced hERG inhibition indicated only a theoretical risk of cardiotoxicity."
reach
"A novel assessment of nefazodone induced hERG inhibition by electrophysiological and stereochemical method."
| 4
Molybdenum atom activates KCNH2.
| 2
reach
"For the Q1070X and R1005fs +50 X mutant minigenes, the hERG current was significantly increased by the antisense MO treatment (XREF_FIG)."
reach
"HERG current was significantly increased by the antisense MO treatment as compared to that observed in invert MO treated cells."
| 1
reach
"3.3 Antisense MO inhibition of the KCNH2 intron 9 polyadenylation."
Molybdenum atom increases the amount of KCNH2.
| 1
Molybdenum atom increases the amount of KCNH2. 1 / 1
| 1
reach
"To test whether antisense MO treatment can restore protein expression of hERG frameshift mutations, we analyzed two LQT2 mutations R1005fs +50 X and Q1010fs +45 X by immunoblot."
MiR-96 affects KCNH2
| 5 4
MiR-96 decreases the amount of KCNH2.
| 2 2
MiR-96 decreases the amount of KCNH2. 1 / 1
| 2 1
reach
"This result indicates that miR-96 can suppress the HERG1 expression in vivo and further demonstrates that HERG1 is a direct target of miR-96."
Modified miR-96 decreases the amount of KCNH2. 1 / 1
| 1
reach
"Ectopic expression of miR-96 represses the HERG1 expression in pancreatic cancer and significantly inhibits malignant behavior of pancreatic cancer cells in vitro and in vivo."
MiR-96 inhibits KCNH2.
| 2 1
MiR-96 inhibits KCNH2. 1 / 1
| 2 1
reach
"It is also the first study to demonstrate that HERG1 gene is negatively regulated by miR-96 via a specific target site (nt427-440) within the 3 '-UTR region of the HERG1 gene."
MiR-96 activates KCNH2.
| 1 1
MiR-96 activates KCNH2. 1 / 1
| 1 1
reach
"The results of the dual-luciferase reporter assay indicated that miR-96 directly targeted wild-type HERG1."
| 4
| 4
reach
"Lumefantrine inhibited the hERG tail current in a concentration dependent manner, with a significant inhibition of the tail current observed at concentrations of 3 mug/ml and above."
reach
"In conclusion, lumefantrine and desbutyl-lumefantrine inhibited significantly the hERG tail current with a higher IC50-value than mefloquine, chloroquine and halofantrine."
reach
"The estimated IC 25 -value for lumefantrine block of the hERG tail current was 1.2 mug/ml (2.27 muM)."
reach
"We showed that lumefantrine and desbutyl-lumefantrine inhibited the hERG tail current with similar IC 50 -values."
| 2 2
eidos
"Hydroxychloroquine is known to block Kv11.1 ( HERG ) and can cause drug-induced long-QT syndrome [ 5 ] ."
eidos
"Hydroxychloroquine is known to block Kv11.1 ( HERG ) and can cause drug-induced long-QT syndrome [ 5 ] ."
reach
"Additionally, for hydroxychloroquine, a recent study pointed out that hydroxychloroquine could lead to unwanted QT interval prolongation by blocking the KCNH2 encoded hERG and Kv11.1 potassium channel, thereby increasing the risk of drug induced torsade de pointes and sudden cardiac death."
reach
"Finally, hydroxychloroquine blocks the KCNH2 encoded hERG and Kv11.1 potassium channel and can potentially prolong the corrected QT interval, with potentially severe consequences, such as sudden cardiac death and cardiac arrhythmia in patients with covid-19."
HMiRP1 affects KCNH2
| 4
HMiRP1 binds KCNH2.
| 2
KCNH2 binds hMiRP1. 2 / 2
| 2
reach
"Like channels with rMiRP1, hMiRP1 and HERG complexes required depolarization to more positive potentials to achieve half-maximal activation and showed no change in slope factor compared to channels formed by HERG subunits alone."
reach
"Like those with rMiRP1, hMiRP1 and HERG complexes deactivated ~ 3-fold faster than HERG channels."
HMiRP1 inhibits KCNH2.
| 1
HMiRP1 inhibits KCNH2. 1 / 1
| 1
reach
"At high HERG channel density, at which the effects of endogenous xMiRP2 are minimal, hMiRP1 reduced HERG current."
HMiRP1 activates KCNH2.
| 1
HMiRP1 activates KCNH2. 1 / 1
| 1
reach
"At low HERG current density, hMiRP1 paradoxically up-regulated HERG current, a result consistent with hMiRP1 rescuing HERG from suppression by endogenous xMiRP2."
Genistein affects KCNH2
| 4
Genistein phosphorylates KCNH2.
| 2
Genistein leads to the phosphorylation of KCNH2 on tyrosine. 2 / 2
| 2
reach
"The constitutive tyrosine phosphorylation of the ERG1 protein, detected by co-immunoprecipitation, was reduced by the protein-tyrosine kinase inhibitors, lavendustin A, herbimycin A, or genistein (but not daidzein)."
reach
"Immunoprecipitation and Western blot analysis demonstrated that membrane protein tyrosine phosphorylation of hERG channels was reduced by genistein, AG556, and PP2."
Genistein inhibits KCNH2.
| 1
| 1
reach
"This observation makes it unlikely that the broad-spectrum PTK inhibitor genistein directly blocks hERG channels."
Genistein decreases the amount of KCNH2.
| 1
Genistein decreases the amount of KCNH2. 1 / 1
| 1
reach
"The reduction of hERG channel phosphorylation level by genistein, AG556 or PP2 was antagonized by orthovanadate."
Etomidate affects KCNH2
| 4
| 4
reach
"In the in vitro Langendorff preparation, none of the cardiac parameters were abnormal, and the hERG recordings showed that ET-26 HCl and etomidate inhibited the tail current of the hERG in a concentration dependent manner with an IC 50 of 742.51 muM and 263.60 muM, respectively."
reach
"XREF_FIG demonstrates that etomidate inhibited the tail current of the hERG in a concentration dependent manner, i.e., etomidate at concentrations of 10, 30, 100, 300, and 1000 muM reduced the tail current by 3.83 +/- 2.36%, 14.13 +/- 5.09%, 27.03 +/- 4.24%, 51.72 +/- 4.12% and 80.06 +/- 3.26% (n = 3), respectively."
reach
"In addition, the electrophysiology study indicated that ET-26 HCl and etomidate inhibited the hERG at a supra-therapeutic concentration."
reach
"The etomidate analogue, ET-26 HCl, inhibited the hERG current in a similar concentration dependent manner (XREF_FIG)."
Ergosterol affects KCNH2
| 4
Ergosterol decreases the amount of KCNH2.
| 2
Ergosterol decreases the amount of KCNH2. 2 / 2
| 2
reach
"Inhibition of ergosterol biosynthesis with the antifungal drug terbinafine at squalene epoxidase step can trigger increased level of ERG1 expression in a concentration dependent manner to a maximum of sevenfold [XREF_BIBR]."
reach
"Inhibition of ergosterol biosynthesis with terbinafine increases the expression of ERG1 in a concentration dependent manner to a maximum of sevenfold."
Ergosterol inhibits KCNH2.
| 1
| 1
reach
"Ergosterol biosynthesis inhibitors that target Erg11, Erg24, Erg2 and Erg1 can also induce the responses."
Ergosterol activates KCNH2.
| 1
| 1
reach
"Redirecting the flux from FPP and sterols, by means of the ergosterol sensitive promoter of ERG1, allowed for plasmid based casbene production of 81.4 mg/L."
| 2 2
sparser
"Coimmunoprecipitation assays showed that Calnexin only interacted with the ER-residing form of hERG proteins ( xref ), suggesting that Calnexin interacts with hERG proteins in the ER."
sparser
"Coimmunoprecipitation assays showed that Calnexin only interacted with the ER-residing form of hERG proteins ( xref ), suggesting that Calnexin interacts with hERG proteins in the ER."
| 2
reach
"For example, it is known that transcription levels of Kv1.5 are modulated by glucocorticoids, that Kv3.4 expression is upregulated by skeletal muscle innervation, and that PKA phosphorylation at the surface of the ER augments hERG biosynthesis."
reach
"ER retention of hERG 125kDa form by CH was due to defective trafficking and was rescued by exposing cells to hypoxia at low temperatures or treatment with E-4031, a hERG channel blocker."
Dihydrogen affects KCNH2
| 4
Dihydrogen activates KCNH2.
| 3
| 3
reach
"Tightening of a Hydrogen Bond Induces Collapse of the hERG Selectivity Filter."
reach
"However, our results also emphasize that presence of one hydrogen bond acceptor group at a certain distance from a hydrophobic group within a chemical scaffold may increases the hERG liability (IC 50)."
reach
"Proton block of the pore underlies the inhibition of hERG cardiac K+ channels during acidosis."
Dihydrogen inhibits KCNH2.
| 1
| 1
reach
"Thus, it reflects that presence of two hydrogen bond acceptor groups in NCEs that complements N1-N1 hotspots of hydrogen bond donor probes at a distance of 5.6-6.0 Adegrees may reduce the hERG inhibition potential."
Digoxin affects KCNH2
| 4
Digoxin activates KCNH2. 4 / 4
| 4
reach
"Digitoxin, ouabain, and digoxin appear to inhibit IKr by reducing the density of HERG dependent potassium channels in the cell membrane."
reach
"Ouabain or digoxin treatment (300 nM for 1.5 h) accelerated hERG internalization by greater than twofold in HeLa and H9C2 i cells, as determined by anti-HA Ab uptake assay (XREF_FIG)."
reach
"Digitoxin, ouabain, and digoxin seem to inhibit IKr by decreasing the density of hERG dependent potassium channels on the cell membrane."
reach
"CHIP ablation partially suppressed ouabain- or digoxin induced hERG disposal from the PM (XREF_FIG)."
| 4
reach
"Pretreating cells with 1 mM L-NAME (1 h, 37degreesC) to prevent NO formation abolished the inhibitory effects of CORM-2 (XREF_FIG), which indicates that CO inhibition of hERG requires NO formation."
reach
"The dependence of CO inhibition of hERG on both ROS and NO raised the possibility that CO stimulates formation of peroxynitrite (ONOO -); therefore, we investigated whether CO could generate detectable levels of ONOO - by using the ONOO - -sensitive fluoroprobe, APF."
reach
"Our findings strongly suggest that CO inhibited hERG via ONOO - -mediated oxidation."
reach
"We also investigated the role of NO in CO inhibition of hERG, as NO mediates increases in I NaL by CO in rat cardiac myocytes."
Barium(2+) affects KCNH2
| 4
Barium(2+) inhibits KCNH2.
| 3
| 3
reach
"State dependent barium block of wild-type and inactivation deficient HERG channels in Xenopus oocytes."
reach
"Extracellular barium (Ba 2+ o) block of HERG exhibits strong voltage dependence consistent with a binding site deep in the pore, similar to the site now confirmed crystallographically for KcsA."
reach
"The HERG like current was blocked by dofetilide (DOF) in a concentration dependent manner (IC (50) = 13 +/- 4 nM, mean +/- SE) and high concentrations of Ba (2+) (1 and 10 mM)."
Barium(2+) activates KCNH2.
| 1
| 1
reach
"Further, Ba 2+ o was found to relieve Na + o inhibition of HERG (XREF_FIG), and Na + o was able to protect against onset of Ba 2+ o effects (XREF_FIG)."
| 1 3
| 2
reach
"Finally, both AA and DHA induced a use dependent inhibition of HERG channels."
reach
"At 10 microM, AA and DHA blocked HERG channels, at the end of 5-s pulses to -10 mV, to a similar extent (37.7 +/- 2.4% vs. 50.2 +/- 8.1%, n = 7-10, P> 0.05)."
Arachidonic acid activates KCNH2.
| 1 1
| 1 1
sparser
"Besides EAG1, AA also activates EAG2 and ERG1 channels, implicating a conserved mechanism involved in AA-mediated activation of the EAG channel family [ xref , xref ]."
reach
"Besides EAG1, AA also activates EAG2 and ERG1 channels, implicating a conserved mechanism involved in AA mediated activation of the EAG channel family [XREF_BIBR, XREF_BIBR]."
UBA2 affects KCNH2
| 4
| 4
sparser
"To establish the molecular nature of the PIP2-HERG interaction, we examined a segment of the HERG COOH terminus with a high concentration of positively charged amino acids (nos."
sparser
"Here we investigated the molecular determinants of PIP2 interactions with HERG channel protein."
sparser
"The physiological relevance of PIP2-HERG interactions is supported by our finding that phenylephrine reduced the K(+) current density in cells coexpressing alpha1A-receptor and HERG."
sparser
"Here, we review the evidence for PIP2-HERG interactions, its potential biological significance, and unfilled gaps in our understanding of this regulatory mechanism."
SAR affects KCNH2
| 4
SAR inhibits KCNH2.
| 2
SAR inhibits KCNH2. 2 / 2
| 2
reach
"41 Extensive SAR studies commenced to reduce the hERG channel affinity of the molecules while retaining all other desirable pharmacological properties."
reach
"SAR studies of this ion channel have shed light on the structural requirements for hERG interaction but most importantly may reveal drug design principles to reduce hERG affinity."
SAR binds KCNH2.
| 1
| 1
reach
"HERG binding SAR shows that variation in the RCQ structure can be used to minimize potential cardiotoxicity issues."
| PMC
SAR activates KCNH2.
| 1
SAR activates KCNH2. 1 / 1
| 1
reach
"The preliminary SAR studies presented here also suggest that this hERG liability may be addressed through medicinal chemistry to significantly improve compound potency and/or reduce hERG inhibition."
RAB11A affects KCNH2
2 | 2
RAB11A binds KCNH2.
2 |
2 |
biogrid
No evidence text available
biogrid
No evidence text available
RAB11A activates KCNH2.
| 2
RAB11A activates KCNH2. 2 / 2
| 2
reach
"These results show that SGK enhances the expression level of mature hERG channels by inhibiting Nedd4-2 as well as by promoting Rab11 mediated hERG recycling."
reach
"This is pertinent as robust Rab11 mediated recycling of hERG channels has been observed."
PRKCA affects KCNH2
1 | 2 1
PRKCA phosphorylates KCNH2 on S890. 4 / 4
1 | 2 1
sparser
"In addition, a newly discovered and as yet uncharacterized LQT2-associated nonsynonymous single nucleotide polymorphism 2660 G→A within the human ether-á-go-go-related gene 1 coding sequence, which replaces arginine 887 with a histidine residue (R887H), strongly inhibits PKCα-dependent phosphorylation of residue Ser890 on Kv11.1, and ultimately inhibits surface expression and current density."
biopax:phosphositeplus
No evidence text available
rlimsp
"In addition, a newly discovered and as yet uncharacterized LQT2-associated nonsynonymous single nucleotide polymorphism 2660 G→A within the human ether-á-go-go-related gene 1 coding sequence, which replaces arginine 887 with a histidine residue (R887H), strongly inhibits PKCα-dependent phosphorylation of residue Ser890 on Kv11.1, and ultimately inhibits surface expression and current density."
rlimsp
"Then, we demonstrate by a phospho-detection immunoassay combined with genetic manipulation that PKCα phosphorylates Ser890. Furthermore, we show that Ser890 phosphorylation is associated with an increase in Kv11.1 membrane density with alteration of recovery from inactivation. In addition, a newly discovered and as yet uncharacterized LQT2-associated nonsynonymous single nucleotide polymorphism 2660 G→A within the human ether-á-go-go-related gene 1 coding sequence, which replaces arginine 887 with a histidine residue (R887H), strongly inhibits PKCα-dependent phosphorylation of residue Ser890 on Kv11.1, and ultimately inhibits surface expression and current density."
PRKAC affects KCNH2
4 |
PRKAC phosphorylates KCNH2.
3 |
Kinase-active PRKAC phosphorylates KCNH2 on S1137. 1 / 1
1 |
bel
"11953308;10837251"
Kinase-active PRKAC leads to the phosphorylation of KCNH2. 1 / 1
1 |
bel
"14-3-3 accelerates and enhances HERG activation, an effect that requires PKA phosphorylation of HERG"
Kinase-active PRKAC phosphorylates KCNH2 on S283. 1 / 1
1 |
bel
"PhosphoElm data from PMID 15212693"
PRKAC activates KCNH2.
1 |
Kinase-active PRKAC activates KCNH2. 1 / 1
1 |
bel
"14-3-3 accelerates and enhances HERG activation, an effect that requires PKA phosphorylation of HERG"
PPP2 affects KCNH2
| 4
PPP2 inhibits KCNH2.
| 2
PPP2 inhibits KCNH2. 2 / 2
| 2
reach
"A Src family kinase inhibitor (PP2) and an EGFR kinase inhibitor (AG556) modulated hERG XREF_BIBR, but only the EGFR inhibitor regulated hEAG1 XREF_BIBR."
reach
"The Src family kinase inhibitor PP2, but not the PTK-inactive analogue PP3, reversibly suppressed hERG channels, and the effect was significantly antagonized by the PTP inhibitor orthovanadate."
PPP2 dephosphorylates KCNH2.
| 1
PPP2 leads to the dephosphorylation of KCNH2 on tyrosine. 1 / 1
| 1
reach
"Immunoprecipitation and Western blot analysis demonstrated that membrane protein tyrosine phosphorylation of hERG channels was reduced by genistein, AG556, and PP2."
PPP2 decreases the amount of KCNH2.
| 1
PPP2 decreases the amount of KCNH2. 1 / 1
| 1
reach
"The reduction of hERG channel phosphorylation level by genistein, AG556 or PP2 was antagonized by orthovanadate."
PD-307243 affects KCNH2
| 4
PD-307243 activates KCNH2. 4 / 4
| 4
reach
"Inside-out patch experiments revealed that PD-307243 increased hERG tail currents by 2.1 +/- 0.6 (n = 7) and 3.4 +/- 0.3-fold (n = 4) at 3 and 10 muM, respectively, by slowing the channel deactivation but had no effect on channel activation."
reach
"At more positive voltages, PD-307243 induced an I (to)-like upstroke of hERG current."
reach
"In the whole-cell recordings, the extracellular application of PD-307243 concentration-dependently increased the hERG current and markedly slowed hERG channel deactivation and inactivation."
reach
"PD-307243 slowed the rate inactivation and increased hERG tail currents by 3.4-fold at 10 muM, but had no effect on rates of channel activation or deactivation [XREF_BIBR] [XREF_BIBR]."
PD-118057 affects KCNH2
| 4
PD-118057 activates KCNH2. 4 / 4
| 4
reach
"We conclude that direct interaction of PD-118057 with the pore helix attenuates fast P-type inactivation and increases open probability of hERG1 channels."
reach
"PD-118057 enhances hERG1 current by increasing channel open probability and causing a positive shift in the voltage dependence of inactivation 80."
reach
"It had been previously established by experiment that PD-118057 and ICA-105574, drugs that inhibits inactivation and thus increase hERG current, bind near F619 and L622 XREF_BIBR, XREF_BIBR."
reach
"Although recent studies can not rule out the possibility that PD-118057 acts through indirect mechanisms to increase hERG currents, our results showing the failure of PD-118057 to significantly affect the gating and kinetic properties of the hERG channel cause us to speculate that PD-118057 increases current amplitude by binding to the channel directly and increasing its open probability and activation potential."
Kr affects KCNH2
| 2 2
Kr binds KCNH2.
| 2
KCNH2 binds Kr. 2 / 2
| 2
sparser
"To validate our simulations of drug interactions with I Kr , the sensitivities of two hERG mutations, N588E and N588K, to I Kr dofetilide block were also simulated."
sparser
"To validate our simulations of drug interactions with I Kr , the sensitivities of two hERG mutations, N588E and N588K, to I Kr dofetilide block were also simulated."
Kr increases the amount of KCNH2.
| 1
Kr increases the amount of KCNH2. 1 / 1
| 1
reach
"The decrease in I Kr accompanied reduced expression of hERG, combined with reduced surface expression of the channel."
Kr activates KCNH2.
| 1
Kr activates KCNH2. 1 / 1
| 1
reach
"Acute activation of PKC by PMA (30 nM, 30 min) reduced both hERG current (I hERG) and I Kr Chronic activation of PKC by PMA (30 nM, 16 h) increased I Kr in cardiomyocytes and the expression level of hERG proteins."
KCNH2 affects terbinafine
| 4
KCNH2 activates terbinafine.
| 3
| 3
reach
"Terbinafine targets ERG1, which is the upstream gene for ERG11, the target for posaconazole."
reach
"Terbinafine resistance in a pleiotropic yeast mutant is caused by a single point mutation in the ERG1 gene."
reach
"Highest squalene levels (over 1000mug squalene per 10 (9) cells) were induced by specific point mutations in ERG1 gene that reduced activity of squalene epoxidase and caused hypersensitivity to terbinafine."
KCNH2 inhibits terbinafine.
| 1
| 1
reach
"In S. cerevisiae, Erg1 activity had been successfully decreased in several studies utilizing the inhibitor terbinafine, which resulted in clearly enhanced levels of squalene, while this study represents the first analysis of the effects of terbinafine on Erg1p in P. pastoris."
KCNH2 affects squalene
| 4
KCNH2 inhibits squalene.
| 2
| 2
reach
"The overexpression of the gene ERG1 (squalene epoxidase) induced a significant decrease of the direct substrate squalene, a high increase of lanosterol, and a small increase of later sterols."
reach
"The production of EPT by the transgenic tri4 strain raised levels of erg1 expression and reduced squalene accumulation while not affecting levels of ergosterol."
KCNH2 activates squalene.
| 2
| 2
reach
"Two copies of GgBAS were co-expressed with CYP716A12 and AtATR1, together with overexpression of tHMG1 and the native genes ERG9 and ERG1, which produce squalene from farnesyl pyrophosphate (FPP, a product of the mevalonate pathway) and convert it to 2,3-oxidosqualene, respectively."
reach
"Two copies of GgBAS were co-expressed with CYP716A12 and AtATR1, together with overexpression of tHMG1 and the native genes ERG9 and ERG1, which produce squalene from farnesyl pyrophosphate (FPP, a product of the mevalonate pathway) and convert it to 2,3-oxidosqualene, respectively."
| 4
reach
"Combined, the data indicate that hERG1 channels contribute to the stress response and clonogenic survival of irradiated K562 cells but do not promote DNA repair."
reach
"Combined, the data indicate that hERG1 channels contribute to the stress response and clonogenic survival of irradiated K562 cells but do not promote DNA repair."
reach
"This suggests that radiation induced hERG1 activity contributes to the cellular stress response in primary CML cells similar to its function observed in K562 cells (compare XREF_FIG)."
reach
"This suggests that radiation induced hERG1 activity contributes to the cellular stress response in primary CML cells similar to its function observed in K562 cells (compare XREF_FIG)."
KCNH2 affects p14_3_3
| 1 4
| 1 3
sparser
"A second level of β-AR/PKA regulation of HERG may occur with the association of adaptor proteins such as 14-3-3, which binds to HERG when the channel is phosphorylated and affects channel gating and duration of the response [ xref , xref ]."
sparser
"Thus, 14-3-3 interactions with HERG may provide a unique mechanism for plasticity in the control of membrane excitability and cardiac rhythm."
sparser
"Thus, 14-3-3 interactions with hERG provide a unique mechanism for plasticity in the autonomic control of stress-dependent regulation of cardiac membrane excitability."
| 1
sparser
"Our results suggest that the dynamic association of 14-3-3 proteins to both beta(1)AR and Kv11.1 channels is involved in the adrenergic modulation of this critical regulator of cardiac repolarization and refractoriness."
KCNH2 affects long QT syndrome type 2
| 4
KCNH2 activates long QT syndrome type 2.
| 3
KCNH2 activates long QT syndrome type 2. 3 / 3
| 3
reach
"The long QT syndrome type 2 (LQT2) is caused by mutations in the human ether-a-go-go-related gene (hERG, KCNH2)."
reach
"Dysfunction of the HERG channel can cause long QT syndrome type 2 (LQT2)."
reach
"Mutations in hERG cause the congenital form of long QT syndrome type 2 (LQT2), an inherited autosomal dominant disorder characterized by prolonged QT interval on the electrocardiogram."
KCNH2 inhibits long QT syndrome type 2.
| 1
Mutated KCNH2 inhibits long QT syndrome type 2. 1 / 1
| 1
reach
"Functional impairment of the hERG channel can result in inherited and acquired long QT syndrome type 2 (LQT2), caused by mutations of the hERG or off-target effects of diverse therapeutic agents, respectively [XREF_BIBR]."
KCNH2 affects clemizole
| 4
KCNH2-Y652A activates clemizole. 1 / 1
| 1
reach
"The S631A, S636A, Y652A and F656V hERG mutant channels reduced the inhibitory effect of clemizole (IC 50 : 0.82, 0.89, 1.49 and 2.98 muM, respectively), suggesting that clemizole is a pore blocker of hERG channels."
KCNH2-S631A activates clemizole. 1 / 1
| 1
reach
"The S631A, S636A, Y652A and F656V hERG mutant channels reduced the inhibitory effect of clemizole (IC 50 : 0.82, 0.89, 1.49 and 2.98 muM, respectively), suggesting that clemizole is a pore blocker of hERG channels."
KCNH2-F656V activates clemizole. 1 / 1
| 1
reach
"The S631A, S636A, Y652A and F656V hERG mutant channels reduced the inhibitory effect of clemizole (IC 50 : 0.82, 0.89, 1.49 and 2.98 muM, respectively), suggesting that clemizole is a pore blocker of hERG channels."
KCNH2-S636A activates clemizole. 1 / 1
| 1
reach
"The S631A, S636A, Y652A and F656V hERG mutant channels reduced the inhibitory effect of clemizole (IC 50 : 0.82, 0.89, 1.49 and 2.98 muM, respectively), suggesting that clemizole is a pore blocker of hERG channels."
KCNH2 affects barium(2+)
| 1 3
| 1 3
reach
"Ba 2+ o block is relieved by HERG inactivation, a feature critical to the interpretation of our experiments combining Ba 2+ o and Na + o."
sparser
"Here, we utilize this unusual interaction between Ba 2+ and HERG inactivation to distinguish between a model in which Na + o reaches the HERG pore and a simple remote allosteric model in which Na + o stabilizes the inactivated state."
reach
"HERG channel inactivation promotes relief of Ba 2+ block (Weerapura, M., S. Nattel, M. Courtemanche, D. Doern, N. Ethier, and T. Hebert."
reach
"HERG channel inactivation promotes relief of Ba (2+) block (Weerapura, M., S. Nattel, M. Courtemanche, D. Doern, N. Ethier, and T. Hebert."
KCNH2 affects UBA2
| 4
| 4
sparser
"To establish the molecular nature of the PIP2-HERG interaction, we examined a segment of the HERG COOH terminus with a high concentration of positively charged amino acids (nos."
sparser
"Here we investigated the molecular determinants of PIP2 interactions with HERG channel protein."
sparser
"The physiological relevance of PIP2-HERG interactions is supported by our finding that phenylephrine reduced the K(+) current density in cells coexpressing alpha1A-receptor and HERG."
sparser
"Here, we review the evidence for PIP2-HERG interactions, its potential biological significance, and unfilled gaps in our understanding of this regulatory mechanism."
KCNH2 affects SLC2A1
| 3 1
KCNH2 binds SLC2A1.
| 3
| 3
sparser
"Moreover, hERG1 presence associated with Glut-1 absence represents an independent negative prognostic factor in TNM I and II colorectal adenocarcinomas [ xref ]."
sparser
"Finally, in a cohort of primary nonmetastatic CRC samples it was shown that hERG1 expression was associated with Glut-1 (glucose transporter 1), VEGF-A, CA-IX (carbonic anhydrase IX), and EGF-R expression [ xref ]."
sparser
"The expressions of hERG1 and Glut-1 were significantly associated ( P =0.001), whereas no significant association between KCa3.1 and the other two biomarkers emerged."
KCNH2 increases the amount of SLC2A1.
| 1
KCNH2 increases the amount of SLC2A1. 1 / 1
| 1
reach
"Both integrin and hERG1 inhibition significantly decreased the transcription of the HIF dependent genes GLUT-1, LDHA, and of a specific HIF-2 target, ANGPTL-4 XREF_BIBR."
KCNH2 affects PPP3
| 1 1 3
KCNH2 inhibits PPP3.
| 1 3
KCNH2 inhibits PPP3. 3 / 3
| 1 3
reach
"However, no difference in spontaneous contraction rates was observed between the different groups.In summary, our results suggest the following : (1) During the neonatal rabbit myocyte hypertrophy induced by PE, AP prolongation as a result of ionic current alterations is not secondary to but precedes myocyte hypertrophy; (2) HERG overexpression could enhance the repolarization and inhibit the CaN activation and myocyte hypertrophy induced by PE."
reach
"As described above, 48 h of exposure to PE stimulated the cell hypertrophy and CaN activation; however, HERG overexpression significantly decreased the cell volume, protein content per well, membrane capacitance, and CaN activity (P <.05, Table 2); these parameters, however, were still larger than untreated cells (P <.05, Table 2)."
reach
"HERG gene transfection also accelerated and repolarization and a shortened APD (90) and inhibited myocyte hypertrophy and CaN activation induced by Ang II."
KCNH2 binds PPP3.
| 1
| 1
sparser
"In conclusion, our study demonstrated that clinical dosage of isoflurane blocked fear memory formation partly through CaN/p-ERK/Erg-1 signaling pathway in both hippocampus and amygdala."
KCNH2 affects LQTS2
| 4
KCNH2 activates LQTS2. 4 / 4
| 4
reach
"LQTS2 is caused by mutations in KCNH2, a gene whose protein product contributes to I Kr (also known as HERG), which is the predominant repolarizing potassium current in CMs."
reach
"LQTS2 is caused by mutations in the KCNH2 gene, encoding the alpha subunit of the human ether-A -go-go - related gene (hERG) potassium channel underlying the rapidly activating delayed rectifier K + current (I Kr)."
reach
"Mutations in KCNQ1 and HERG cause the congenital LQTS1 XREF_BIBR and LQTS2, XREF_BIBR respectively."
reach
"Long QT syndrome 2 (LQTS2) caused by missense mutations in hERG channel is clinically associated with abnormally prolonged ventricular repolarization and sudden cardiac deaths."
KCNH2 affects ER
| 2 2
KCNH2 binds ER.
| 2
KCNE2 binds KCNH2 and ER. 1 / 1
| 1
sparser
"BFA treatment also resulted in enhanced KCNE2-ER binding to HERG but to a much lower degree than that seen with wild type KCNE2 ( xref )."
KCNE1 binds KCNE2, KCNH2, and ER. 1 / 1
| 1
sparser
"The overall degree of association of HERG with KCNE1-ER and KCNE2-ER was comparable however, the increase over wild type was greater for KCNE2 than for KCNE1."
KCNH2 inhibits ER.
| 1
KCNH2 inhibits ER. 1 / 1
| 1
reach
"Blocking the ER associated degradation (ERAD) pathway with a dominant negative form of the ERAD core component, valosin containing protein (VCP), in 293A cells partially abolished RFFL mediated hERG degradation."
KCNH2 activates ER.
| 1
KCNH2 activates ER. 1 / 1
| 1
reach
"In the long QT-2 syndrome (where Q and T denote characteristic peaks on the electrocardiogram), several mutations in HERG cause retention in the ER leading to abnormal electrical cardiac impulses and ventricular tachycardia [12,13]."
KCNH2 affects EGFR
| 3 1
| 3 1
sparser
"We demonstrate for the first time that a physical and functional interaction of hERG1 with EGF-R occurs in PDAC."
reach
"As activating the mutations of Kras can concomitantly upregulate EGF-R and its downstream signalling pathways, we studied such pathway, providing evidence that hERG1 interacted with EGF-R."
sparser
"As activating the mutations of Kras can concomitantly upregulate EGF-R and its downstream signalling pathways ( xref ), we studied such pathway, providing evidence that hERG1 interacted with EGF-R. Overall, hERG1 turned out to contribute to the control of EGF-R-triggered intracellular signalling pathways, and, by this way, to the regulation of PDAC cell proliferation and migratory activity."
sparser
"These findings are of particular interest within our research field, since we demonstrated that hERG1 channel expression is significantly associated with EGFR expression in pancreatic ductal adenocarcinomas [ xref ] and colorectal cancers [ xref ]."
KCNH2 affects CAV3
2 | 1 1
2 | 1
biogrid
No evidence text available
reach
"Our data demonstrate that Cav3, hERG, and ubiquitin-ligase Nedd4-2 interact with each other and form a complex."
biogrid
No evidence text available
| 1
sparser
"We showed that ATP1B1 interacts with KCNH2, CACNA1C, KCNQ1and CAV3."
KCNH2 affects CALR
1 | 2 1
1 | 1
reach
"To assess the physical interaction between hERG and Calnexin and Calreticulin, immunoprecipitation was done with anti-Calnexin or anti-Calreticulin antibody, followed by Western blot analysis with anti-hERG antibody."
biogrid
No evidence text available
CALR binds CANX and KCNH2. 1 / 1
| 1
sparser
"As shown in xref , treatment with lactacystin or ALLN but not leupeptin (a lysosome inhibitor) results in an increase in the levels of core-glycosylated, immature form of hERG, Calnexin and Calreticulin."
| 1
sparser
"Furthermore, the interaction between mutant hERG proteins and chaperone proteins, Calnexin and Calreticulin, play crucial roles in these processes."
| 4
reach
"Arsenic interferes with the formation of hERG and chaperone complexes and inhibits hERG maturation causing ECG abnormalities."
reach
"Terfenadine is an antihistamine compound that also blocks the hERG channel Terfenadine is classified as a compound with intermediate risk to cause QT prolongation of the human ECG."
reach
"As illustrated in Fig. 1, the R1135H mutation not only shortens the action potential, in accordance with the short QT interval associated with the mutation, but also increases the susceptibility to all-or-none repolarization (epicardial loss-of-dome) in the right ventricle, particularly at a faster beating rate.In conclusion, it seems reasonable to assume that the R1135H KCNH2 mutation itself contributes to the Brugada-type ECG that Itoh et al. observed in their patient."
reach
"As expected, XREF_FIG shows that hERG block results in QT prolongation and changes in the T wave in the 12 leads of the simulated ECG."
ICA-105574 affects KCNH2
| 4
ICA-105574 activates KCNH2. 4 / 4
| 4
reach
"The primary mechanism by which ICA-105574 potentiates hERG channel activity is by removing hERG channel inactivation, because ICA-105574 (2 microM) shifts the midpoint of the voltage-dependence of inactivation by> 180 mV from -86 to +96 mV."
reach
"It had been previously established by experiment that PD-118057 and ICA-105574, drugs that inhibits inactivation and thus increase hERG current, bind near F619 and L622 XREF_BIBR, XREF_BIBR."
reach
"ICA-105574 increases outward hERG1 currents (EC 50 of 0.5 muM, Hill slope of 3.3) far more than any other known agonist [XREF_BIBR]."
reach
"ICA-105574 (ICA), a 3-Nitro-n-(4-phenoxyphenyl) benzamide derivative activates hERG1 by strongly attenuating pore-type inactivation."
HGF affects KCNH2
| 1 3
HGF inhibits KCNH2.
| 2
HGF inhibits KCNH2. 2 / 2
| 2
reach
"The gain-of-function mutation N629D at the outer mouth of the selectivity filter (SF) disrupts inactivation and K + -selective transport in hERG1, leading to arrhythmogenic phenotypes associated with long-QT syndrome."
reach
"Therefore another goal of this work was to investigate the role of the SF in the drug induced blockade of hERG leading to ALQTS."
HGF binds KCNH2.
| 1
| 1
sparser
"Finally, the high affinity of the cardiotoxic drugs for the lipid membrane as well as their effect on the membrane interaction of hERG's SF segment supports the possibility of an indirect role of the membrane in the ALQTS."
HGF activates KCNH2.
| 1
Mutated HGF activates KCNH2. 1 / 1
| 1
reach
"Collectively these results suggest that the SF mutations can partially rescue the low [K +] cy -induced SF collapse and global destabilization of hERG."
FHND004 affects KCNH2
| 4
FHND004 inhibits KCNH2. 4 / 4
| 4
reach
"Therefore, these results illustrated an open channel block of hERG by FHND004."
reach
"In this study, our results elucidated that FHND004 was able to directly block hERG channels in a time- and concentration dependent manner."
reach
"Overall, FHND004 is able to directly block hERG channels at open state but shows less potency for inhibiting the channels than the marketed AZD9291."
reach
"FHND004 inhibited hERG K + currents in a concentration dependent manner with IC 50 values of 8.46 +/- 0.33 muM in HEK293 cells and 7.52 +/- 1.27 muM in HL-1 cells, respectively."
ET-26 HCl affects KCNH2
| 4
ET-26 HCl inhibits KCNH2. 4 / 4
| 4
reach
"In the in vitro Langendorff preparation, none of the cardiac parameters were abnormal, and the hERG recordings showed that ET-26 HCl and etomidate inhibited the tail current of the hERG in a concentration dependent manner with an IC 50 of 742.51 muM and 263.60 muM, respectively."
reach
"In addition, the electrophysiology study indicated that ET-26 HCl and etomidate inhibited the hERG at a supra-therapeutic concentration."
reach
"The results suggest that etomidate and ET-26 HCl inhibited the tail current of the hERG in a concentration dependent manner, but the concentrations decreased the channel protein expression at a supra-therapeutic concentration or overdose, with an IC 50 of 263.60 muM and 742.51 muM, respectively."
reach
"The etomidate analogue, ET-26 HCl, inhibited the hERG current in a similar concentration dependent manner (XREF_FIG)."
CALR affects KCNH2
1 | 2 1
1 | 1
reach
"To assess the physical interaction between hERG and Calnexin and Calreticulin, immunoprecipitation was done with anti-Calnexin or anti-Calreticulin antibody, followed by Western blot analysis with anti-hERG antibody."
biogrid
No evidence text available
CALR binds CANX and KCNH2. 1 / 1
| 1
sparser
"As shown in xref , treatment with lactacystin or ALLN but not leupeptin (a lysosome inhibitor) results in an increase in the levels of core-glycosylated, immature form of hERG, Calnexin and Calreticulin."
| 1
sparser
"Furthermore, the interaction between mutant hERG proteins and chaperone proteins, Calnexin and Calreticulin, play crucial roles in these processes."
BRAF affects KCNH2
| 1 4
BRAF activates KCNH2. 4 / 4
| 1 4
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"Wild-type BRAF increased hERG channel protein abundance in the cell membrane and consequently it increased the hERG mediated current through the cell membrane."
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"At least in theory, up-regulation of hERG K + channels by B-RAF may further influence cardiac repolarization XREF_BIBR, XREF_BIBR."
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"Up-Regulation of hERG K + Channels by B-RAF."
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"At least in theory, B-RAF could up-regulate hERG activity by increasing hERG channel protein abundance in the Xenopus oocytes plasma membrane."
BANF1 affects KCNH2
| 1 3
BANF1 ubiquitinates KCNH2.
| 1 1
BANF1 leads to the ubiquitination of KCNH2-F805C. 1 / 1
| 1
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"Whereas Baf promoted F805C hERG ubiquitination (XREF_FIG and Supplemental Figure S4C, lanes 1 and 2), this was blunted by inhibiting ER-to-Golgi vesicular transport with brefeldin A (XREF_FIG, lanes 3 and 4)."
BANF1 ubiquitinates KCNH2. 1 / 1
| 1
sparser
"Whereas Baf promoted F805C hERG ubiquitination ( xref and Supplemental Figure S4C, lanes 1 and 2), this was blunted by inhibiting ER-to-Golgi vesicular transport with brefeldin A ( xref , lanes 3 and 4)."
BANF1 inhibits KCNH2.
| 1
BANF1 inhibits KCNH2-G601S. 1 / 1
| 1
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"Baf inhibition of G601S hERG lysosomal targeting from the PM was confirmed by anti-HA Ab capture in live HeLa cells for 3 h, followed by indirect immunofluorescence (XREF_FIG)."
BANF1 activates KCNH2.
| 1
BANF1 activates KCNH2-F805C. 1 / 1
| 1
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"Baf also enhanced the accumulation of poly-Ub adducts of F805C hERG in ouabain treated cells, a phenomenon that was suppressed by brefeldin A (XREF_FIG, lanes 5-8), in accord with the post-ER origin of ubiquitination."
AZA-2 affects KCNH2
| 4
AZA-2 inhibits KCNH2.
| 2
AZA-2 inhibits KCNH2. 2 / 2
| 2
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"The IC 50 reported by Twiner et al. for AZA-2 blockade of hERG was 0.64 muM (moderate blockers IC 50 : 0.1-1 muM)."
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"In summary, AZA-2 blocks the hERG cardiac potassium channel in vitro and, although no QT c interval prolongation is observed in vivo, AZA-2 clearly causes prolongation of PR interval and the appearance of arrhythmias in rat ECGs, indicating an alteration of heart electrophysiology in vivo."
AZA-2 increases the amount of KCNH2.
| 1
AZA-2 increases the amount of KCNH2. 1 / 1
| 1
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"Actually, AZA-2 induces a significant increase of hERG channel levels on the cell surface of hERG-CHO cells."
AZA-2 activates KCNH2.
| 1
AZA-2 activates KCNH2. 1 / 1
| 1
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"Conversely, after 12 h of incubation 50 and 200 nM AZA-2 induced a statistically significant increase of hERG channels on the cell surface when compared to carrier controls (XREF_FIG)."
AMPK affects KCNH2
| 4
AMPK inhibits KCNH2.
| 2
AMPK inhibits KCNH2. 2 / 2
| 2
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"The multi targeted TKi sunitinib showed decreased cardiomyocyte viability, AMPK inhibition, increased lipid accumulation, disrupted beat pattern, and hERG block."
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"Pharmacological activation of AMPK with AICAR or with phenformin inhibited hERG currents in Xenopus oocytes, an effect abrogated by AMPK inhibitor compound C. (gammaR70Q) AMPK enhanced the Nedd4-2-dependent downregulation of hERG currents."
AMPK decreases the amount of KCNH2.
| 1
Modified AMPK decreases the amount of KCNH2. 1 / 1
| 1
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"Coexpression of constitutively active (gammaR70Q) AMPK decreased membrane expression of hERG in Xenopus oocytes."
AMPK activates KCNH2.
| 1
AMPK activates KCNH2. 1 / 1
| 1
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"Pharmacological activation of AMPK with AICAR or with phenformin inhibited hERG currents in Xenopus oocytes, an effect abrogated by AMPK inhibitor compound C. (gammaR70Q) AMPK enhanced the Nedd4-2-dependent downregulation of hERG currents."
AKAP5 affects KCNH2, and PKA
| 4
PKA binds AKAP5 and KCNH2. 4 / 4
| 4
sparser
"The HERG channel protein, AKAP5, and PKA interacted with each other and appeared to form intracellular complexes."
sparser
"The HERG channel protein, AKAP5, and PKA interacted with each other and appeared to form intracellular complexes."
sparser
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
sparser
"Immunofluorescence and immunoprecipitation indicated that HERG bound to PKA and AKAP5 and was colocalized at the cell membrane."
A-935142 affects KCNH2
| 4
A-935142 activates KCNH2.
| 3
A-935142 activates KCNH2. 3 / 3
| 3
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"In conclusion, A-935142 enhances hERG current in a complex manner by facilitation of activation, reduction of inactivation, and slowing of deactivation, and abbreviates atrial and ventricular repolarization."
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"In a previous study we found that A-935142 enhanced hERG current in a concentration dependent manner by facilitating activation, reducing inactivation, and slowing deactivation (Su et al., 2009)."
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"A-935142 shortened cardiac action potentials and enhanced the amplitude of the hERG current in a concentration- and voltage dependent manner."
A-935142 inhibits KCNH2.
| 1
A-935142 inhibits KCNH2. 1 / 1
| 1
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"A-935142 significantly reduced the time constants (tau) of hERG channel activation at two example voltages (-10 mV : tau = 100 +/-17 ms vs. 164 +/-24 ms, n = 6, P < 0.01; +30 mV : tau = 16.7 +/-1.8 ms vs. 18.9 +/-1.8 ms, n = 5, P < 0.05) and shifted the voltage-dependence for hERG activation in the hyperpolarizing direction by 9 mV."
| 4
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"Both escitalopram and citalopram produced a reduction of hERG channel protein trafficking to the plasma membrane but did not affect the short-term internalization of the hERG channel."
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"No statistical difference between citalopram blockade of HERG (tail current maximum at -40 mV) in the two heterologous systems in the two sets of recording conditions was observed at the two concentrations tested (3 muM and 100 muM; unpaired t -test, P> 0.2 for both, n = 3-8)."
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"Using whole-cell patch clamp recording of heterologous HERG mediated currents in transfected mammalian cells, we observed that the selective serotonin re-uptake inhibitor citalopram blocks HERG with an IC (50) of 3.97 microM."
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"Fluoxetine and its metabolite, norfluoxetine, citalopram and escitalopram prolong the QT interval by directly inhibiting the hERG potassium channels and by disrupting channel protein trafficking reducing the number of channels on the cell membrane [XREF_BIBR]."
| 3
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"Thioridazine, perphenazine, trifluoperazine, and chlorpromazine blocked hERG potassium channels with the following IC (50) values : IC (50) values were 224 +/- 42 nM for thioridazine, 1003 +/- 71 nM for perphenazine, 1406 +/- 124 nM for trifluoperazine, and 1561 +/- 281 nM for chloropromazine."
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"The IC (50) for a trifluoperazine block of HERG current progressively decreased according to depolarization : IC (50) values at -40, 0, and +40 mV were 21.6, 16.6, and 9.29 microM, respectively."
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"The block of HERG by trifluoperazine was use dependent, exhibiting more rapid onset and greater steady-state block at higher frequencies of activation; there was partial relief of the block with decreasing frequency."
| 3
Thapsigargin activates KCNH2-E637K. 2 / 2
| 2
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"Moreover, our study is the first to demonstrate that thapsigargin fails to rescue the dominant negative suppression of the E637K hERG mutant on WT-hERG channel function."
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"However, our study shows that thapsigargin fails to rescue trafficking defects of the E637K hERG mutant, which is a novel missense mutation located in the pore-S6 loop transmembrane segment of hERG, nearby the C-terminus XREF_BIBR."
| 1
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"Interestingly, Delisle et al reported that the sarco and endoplasmic reticulum ATPase inhibitor thapsigargin can rescue trafficking of mutated hERG channels possibly through altered Ca 2+ -dependent chaperone activity in the ER XREF_BIBR."
Tadalafil affects KCNH2
| 3
| 3
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"Because the maximum soluble concentration of tadalafil (100 microM) produced only a 50.9% inhibition of the HERG current amplitude, the IC50 value for tadalafil could not be determined with the Hill equation."
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"It was shown that tadalafil also inhibits the hERG channel by concentration dependent manner with an IC 50 value of 100muM XREF_BIBR."
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"Since tadalafil blocks hERG1 K channels in concentration dependent manner, the cardiotoxicity prediction of the hit molecules was also tested."
Sertindole affects KCNH2
| 3
| 3
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"Using patch clamp electrophysiology, we found sertindole blocked HERG currents with an IC50 value of 14.0 nM when tail currents at -40 mV were measured after a 2-sec depolarization to +20 mV."
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"A study using the HERG blocker Sertindole showed that the T wave attained minimum height just before the onset of TdP [XREF_BIBR]."
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"Pimozide and sertindole, for example, have previously been shown to block HERG in the low nanomolar range (Rampe et al., 1998; Kang et al., 2000)."
Serotonin affects KCNH2
| 3
| 3
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"This is the first study demonstrating that HERG potassium channels are blocked by the selective serotonin reuptake inhibitor fluoxetine."
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"Using whole-cell patch clamp recording of heterologous HERG mediated currents in transfected mammalian cells, we observed that the selective serotonin re-uptake inhibitor citalopram blocks HERG with an IC (50) of 3.97 microM."
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"Cisapride is a serotonin 5-HT4 receptor agonist that has been reported to block the hERG potassium channel."
Protease inhibitors affects KCNH2
| 3
Protease inhibitors activates KCNH2. 3 / 3
| 3
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"Our data show that four protease inhibitors block HERG channels, suggesting that protease inhibitors could predispose individuals to QT prolongation and torsade de pointes."
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"It has been suggested that LQTs in AIDS patients is the acquired LQTs caused by the clinically used drugs, HIV protease inhibitors, because HIV protease inhibitors have been reported to block hERG K + channels responsible for cardiac repolarization [2]."
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"Blockade of HERG channels by HIV protease inhibitors."
Propofol affects KCNH2
| 3
| 3
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"Mutations in drug binding sites (Y652A or F656C) of the hERG channel were found to attenuate hERG current blockage by propofol."
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"However, propofol did not inhibit the trafficking of hERG protein to the cell membrane."
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"Propofol inhibits hERG K"
| 1 3
Progesterone activates KCNH2.
| 2
| 2
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"Application of 2-hydroxypropyl-beta-cyclodextrin (a sterol binding agent) or overexpression of Rab9 rescued the progesterone induced HERG trafficking defect and ER stress."
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"Further, it has been demonstrated that progesterone may modulate hERG folding in the ER and Golgi trafficking by regulating intracellular cholesterol homeostasis, thus offering a possible mechanism for arrhythmic risk in late-stage pregnancy 87."
Progesterone inhibits KCNH2.
| 1 1
| 1 1
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"Progesterone also concentration-dependently decreased HERG current density, but had no effect on voltage gated L-type Ca (2+) and K (+) channels."
| 3
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"The IC50 for a prochlorperazine block of HERG current in Xenopus oocytes progressively decreased relative to the degree of depolarization, from 42.1 microM at -40 mV to 37.4 microM at 0 mV to 22.6 microM at +40 mV."
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"The block of HERG by prochlorperazine was use dependent, exhibiting a more rapid onset and a greater steady-state block at higher frequencies of activation, while there was partial relief of the block with reduced frequencies."
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"Blockade of HERG human K+ channel and IKr of guinea pig cardiomyocytes by prochlorperazine."
Procaine affects KCNH2
| 3
| 3
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"Procaine, a state dependent blocker, inhibits HERG channels by helix residue Y652 and F656 in the S6 transmembrane domain."
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"Conclusively, procaine state-dependently inhibits HERG channels (WT, Y652A, and F656A)."
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"The results revealed that WT HERG is blocked in a concentration-, voltage-, and state dependent manner by procaine ([IC50] = 34.79 muM)."
Phenytoin affects KCNH2
| 3
| 3
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"Phenytoin has been shown to inhibit HERG channels at significantly higher concentrations (IC 50 for HERG> 300muM, vs. IC 50 for VGSC ~ 10muM) [XREF_BIBR, XREF_BIBR]."
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"Phenytoin and phenobarbital inhibit human HERG potassium channels."
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"Danielsson BR, Lansdell K, Patmore L, Tomson T. Phenytoin and phenobarbital inhibit human HERG potassium channels."
Oxycodone affects KCNH2
| 3
| 3
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"The authors of the study speculated that high levels of oxycodone could lead to hERG channel inhibition, QTc prolongation, and sudden cardiac death [XREF_BIBR]."
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"35 Oxycodone and fentanyl reduce HERG current in vitro, XREF_BIBR, XREF_BIBR and as do cocaine and cocaine metabolites, XREF_BIBR, XREF_BIBR but none of these drugs affect the I Ks current."
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"Methadone is the opiod most tightly associated with QTc prolongation; with much lesser potency buprenorphine and oxycodone can block HERG channels and depress the IKr current in vitro.Antineoplastic chemotherapy like anthracyclines, alkylating drugs, alkilants and cisplatin are associated with electrocardiographic alterations including prolongation of QT and emesis of different grades."
Mianserin affects KCNH2
| 3
| 3
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"Inhibition of cardiac hERG potassium channels by tetracyclic antidepressant mianserin."
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"Mianserin inhibited hERG currents in the open and inactivated state, but not in the closed states."
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"Mianserin inhibited hERG currents in a dose dependent manner with an IC (50) of 3.2 micromol/l in HEK cells."
MiR-493 affects KCNH2
| 3
MiR-493 decreases the amount of KCNH2.
| 2
MiR-493 decreases the amount of KCNH2. 2 / 2
| 2
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"As shown in XREF_FIG, overexpression of miR-493 led to the obvious suppression of hERG1, while knockdown of miR-493 enhances the expression of hERG1 in both mRNA and protein levels."
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"In conclusion, our results confirmed that miR-493 could suppress hERG1 expression through direct binding sequences at the 3 ' UTR of hERG1 mRNA."
MiR-493 binds KCNH2.
| 1
KCNH2 binds miR-493. 1 / 1
| 1
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"Then we conducted luciferase assay to investigate the direct interaction between miR-493 and hERG1."
MiR-17-5p affects KCNH2
| 3
MiR-17-5p inhibits KCNH2.
| 2
MiR-17-5p inhibits KCNH2. 2 / 2
| 2
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"Finally, our whole-cell patch-clamp recordings demonstrated that transfection of miR-17-5p suppressed h-ERG current (I h-ERG) in HEK293 cell with stable h-ERG expression, an effect reversed by co-transfection of miR-17-5p-I, but not by the mutant inhibitor (XREF_FIG)."
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"Upregulation of miR-17-5p in turn downregulates the related chaperones to reduce h-ERG trafficking leading to associated electrical disturbance of the heart."
MiR-17-5p activates KCNH2.
| 1
MiR-17-5p activates KCNH2. 1 / 1
| 1
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"Upregulation of miR-17-5p in turn downregulates the related chaperones to reduce h-ERG trafficking leading to associated electrical disturbance of the heart."
MiR-133 affects KCNH2
| 3
MiR-133 decreases the amount of KCNH2.
| 2
Modified miR-133 decreases the amount of KCNH2. 1 / 1
| 1
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"85 Furthermore, miR-133 overexpression reduced HERG protein levels, while miR-133 inhibition partially reversed this."
MiR-133 decreases the amount of KCNH2. 1 / 1
| 1
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"Furthermore, miR-133 can also inhibit the expression of KCNH2 (potassium voltage gated channel subfamily H member 2), which encodes the ether-a-go-go related gene (ERG) channel subunit responsible for delayed rectifier K + current (I kr), resulting in slowed repolarization and prolonged QT interval in the heart [XREF_BIBR]."
MiR-133 activates KCNH2.
| 1
MiR-133 activates KCNH2. 1 / 1
| 1
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"KCNQ1 and KCNH2 mRNA and protein are directly negatively modulated by miR-133, which can target the 3 ' UTR of KCNQ1 and KCNH2 mRNA [XREF_BIBR, XREF_BIBR, XREF_BIBR]."
Loperamide affects KCNH2
| 3
| 3
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"Characterization of loperamide mediated block of hERG channels at physiological temperature and its proarrhythmia propensity."
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"The 50% inhibitory concentration for loperamide inhibition of hERG ionic tail currents was approximately 40 nmol/l."
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"Loperamide suppressed hERG current in a use- and voltage dependent but frequency independent manner, with a half-maximal inhibitory concentration < 90nM."
| 3
| 3
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"In the laboratory, we found that, in combination, lansoprazole and ceftriaxone block the hERG channel up to 57.6%, corresponding with an APD70 increase of 50 ms. At these higher lansoprazole concentrations, it is likely that, if treated as a single entity, the combination would not have received regulatory approval."
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"Notably, it has been demonstrated that also lansoprazole alone significantly inhibits hERG potassium channel and related current IKr (-14%), although to a lesser extent when compared to the drug combination (-58%)."
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"In combination, ceftriaxone and lansoprazole block the hERG channel."
Imatinib affects KCNH2
| 3
| 3
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"According to the formal studies, imatinib could preferentially block the open HERG channel, contributing to QT interval prolongation [XREF_BIBR]."
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"Furthermore, imatinib markedly reduced hERG currents in HEK293T-hERG cells, this effect was accompanied by inhibition of CML cell proliferation and apoptosis, as well as suppression of vascular endothelial growth factor (VEGF) secretion."
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"The results demonstrated that hERG1 was highly detected in K562 cells and primary CML cells, and down-regulated by imatinib at mRNA and protein levels."
Hydroxyzine affects KCNH2
| 3
| 3
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"The results suggest that hydroxyzine could block hERG channels and prolong APD."
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"Hydroxyzine was found to block peak hERG channel tail currents in a concentration dependent manner, with an IC 50 of 0.39 mumol/L at near-physiological temperature (n = 4; Fig."
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"In line with previous reports that hydroxyzine can inhibit hERG potassium channels with IC 50 values ranging from 0.62 mumol/L down to 0.16 mumol/L, (Sakaguchi etal."
| 1 2
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"[Chinfloxacin hydrochloride inhibits HERG potassium channel at open state]."
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"Considering that K + channel has relatively high selectivity for the permeating ion, K + rather than Na +, Ca 2+, and Cl -, the MeOH extract at relatively high concentrations of 100 and 300 microg/mL, could perturb the ion-selectivity of HERG channel by inducing non specific membrane permeabilization or membrane leakage."
sparser
"In addition, the electrophysiology study indicated that ET-26 HCl and etomidate inhibited the hERG at a supra-therapeutic concentration."
Halothane affects KCNH2
| 3
Halothane inhibits KCNH2.
| 2
| 2
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"Halothane inhibits HERG currents expressed in oocytes in a concentration dependent manner."
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"The authors ' results demonstrate that halothane decreased HERG currents by modulating kinetic properties of HERG channels, decreasing their open probability."
Halothane activates KCNH2.
| 1
| 1
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"Kinetic modulation of HERG potassium channels by the volatile anesthetic halothane."
HERG inhibitors affects KCNH2
| 3
HERG inhibitors inhibits KCNH2.
| 2
HERG inhibitors inhibits KCNH2. 2 / 2
| 2
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"High hERG expressing GPDCs showed a reduction in sphere formation when treated with hERG inhibitors compared to low hERG expressing GPDCs."
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"High hERG expressing GPDCs showed a reduction in sphere formation when treated with hERG inhibitors compared with low hERG expressing GPDCs."
HERG inhibitors decreases the amount of KCNH2.
| 1
HERG inhibitors decreases the amount of KCNH2. 1 / 1
| 1
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"These results advance the hypothesis that structurally diverse hERG inhibitors mediate similar physiological effects revealed by transcriptional response profiles, even in cell lines not derived from a cardiac lineage and potentially independent of hERG expression."
| 3
Geldanamycin inhibits KCNH2.
| 2
| 2
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"The specific Hsp90 inhibitor geldanamycin prevents maturation and increases proteasomal degradation of hERG WT, while reducing hERG currents in heterologous expression systems."
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"In our previous study, we found that geldanamycin, an Hsp90 inhibitor, abolished the kinase dependent increase in HERG abundance."
Geldanamycin activates KCNH2.
| 1
| 1
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"It has previously been demonstrated that the Hsp90 inhibitor, geldanamycin, inhibits hERG trafficking, presumably through an Hsp90 dependent mechanism."
Extracellular K affects KCNH2
| 3
Extracellular K inhibits KCNH2. 3 / 3
| 3
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"Elevated extracellular K + (20 mM) decreases the shift in the HERG channel isochronal current-voltage curve caused by Ca 2+."
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"Though elevated extracellular K + clearly slows the rate of HERG inactivation, Wang et al. (1997b) showed that the reduction in channel inactivation induced by extracellular K + did not account for the current increase seen."
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"Elevated extracellular K + slows inactivation and deactivation gating of HERG."
Erlotinib affects KCNH2
| 3
| 3
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"In contrast, erlotinib, the least cardiotoxic of the 4 drugs tested, was a less potent inhibitor of hERG and only inhibited 35% (mean) of hERG current at the concentration of 10 muM, which was the solubility limit in HBPS."
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"In these studies, sunitinib decreased cardiomyocyte viability, inhibited AMPK, increased lipid accumulation, disrupted beat pattern, and blocked hERG activity); in contrast, erlotinib demonstrated only minor changes (increased acetyl-CoA carboxylase (ACC) phosphorylation, the rate limiting step in fatty acid biosynthesis), did not impact ROS, caspase, or lipid levels, and did not affect beat patterns [XREF_BIBR]."
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"Data in XREF_FIG reveal that at 6 microM concentration, erlotinib does not block the hERG K+ channel, as should be expected for an approved drug."
Epinastine affects KCNH2
| 3
| 3
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"We further examined the possibility that epinastine may inhibit HERG channels in a use dependent manner."
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"The IC 50 concentration of epinastine to block HERG channels was 1000 times higher than that needed to block histamine H 1 receptors.Structural differences between epinastine, astemizole and terfenadine may be related to the different magnitudes of suppression of HERG channel currents by these compounds."
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"In contrast, 100 microM epinastine inhibited the HERG current by only 11 +/-2.1%."
Dronedarone affects KCNH2
| 1 2
| 1 2
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"The half-maximal activation voltage was shifted by -6.1 mV, and HERG current block by dronedarone was voltage dependent, but not use dependent."
sparser
"The L532P mutation produced an ~ 5-fold increase in the IC 50 for dronedarone inhibition of I hERG ."
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"Dronedarone blocked HERG channels with an IC50 value of 9.2 microM and a maximum tail current reduction of 85.2%."
Dioxygen affects KCNH2
| 3
Dioxygen activates KCNH2.
| 2
| 2
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"Both L-arginine (10 mM) and NOC-18 (0.3 mM) counteracted the stimulatory effect on hERG1 outward currents induced by the radical oxygen species generating system FeSO (4) (25 microM)/ascorbic acid (50 microM; Fe/Asc)."
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"Mitochondrial reactive oxygen species mediate hypoxic down-regulation of hERG channel protein."
Dioxygen inhibits KCNH2.
| 1
| 1
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"Notably, prolonged exposure to PKA activators was found to stimulate the production of intracellular reactive oxygen species, which in turn significantly impaired the HERG K + channel function, a critical regulator of cardiac action potential repolarization, possibly leading to electrical disturbance in failing hearts."
Diltiazem affects KCNH2
| 3
Diltiazem inhibits KCNH2.
| 2
| 2
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"In our experiments, verapamil caused high-affinity block of HERG current (IC50 = 143.0 nmol/L), a value close to those reported for verapamil block of L-type Ca2+ channels, whereas diltiazem weakly blocked HERG current (IC50 = 17.3 micromol/L), and nifedipine did not block HERG current."
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"XREF_BIBR reported for verapamil caused high-affinity block of KCNH2 channel current is close to its block of L-type Ca2+ channels ', whereas diltiazem only weakly suppresses KCNH2 current, and nifedipine has no effect."
Diltiazem activates KCNH2.
| 1
| 1
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"Verapamil was discontinued and diltiazem, a CYP3A inhibitor that weakly blocks hERG, was started."
| 3
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"Pretreatment with cypermethrine, a calcineurin inhibitor, had no effect on the CsA induced inhibition of the HERG channel."
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"CsA inhibited the HERG channel in a concentration dependent manner, with an IC (50) value and a Hill coefficient of 3.17 microM and 0.89, respectively."
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"CsA blocked the HERG channels predominantly in the open and inactivated states rather than in the closed state."
Clozapine affects KCNH2
| 3
| 3
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"For example, the blockade of HERG by clozapine (Lee et al., 2006) and trifluoperazine (Choi et al., 2005) resulted in IC 50 values 10- to 20-fold higher when the drug was applied to the Xenopus oocytes rather than mammalian cells."
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"Blockade of HERG human K+ channels and IKr of guinea-pig cardiomyocytes by the antipsychotic drug clozapine."
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"The IC (50) for the clozapine blockade of HERG currents in Xenopus oocytes progressively decreased relative to depolarization (39.9 microM at -40 mV, 28.3 microM at 0 mV and 22.9 microM at +40 mV), whereas the IC (50) for the clozapine induced blockade of HERG currents in HEK293 cells at 36 degrees C was 2.5 microM at +20 mV."
| 1 3
Clarithromycin activates KCNH2.
| 2
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"Our findings indicate that the antibiotic clarithromycin can target hERG1 and modulate autophagy to promote the death of chemoresistant colorectal cancer cells."
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"Our findings indicate that the antibiotic clarithromycin can target hERG1 and modulate autophagy to promote the death of chemoresistant colorectal cancer cells."
Clarithromycin inhibits KCNH2.
| 1 1
| 1 1
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"The results of this study document that both erythromycin and clarithromycin significantly inhibit the HERG potassium current at clinically relevant concentrations."
Clamp affects KCNH2
| 3
Clamp inhibits KCNH2.
| 2
Clamp inhibits KCNH2. 2 / 2
| 2
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"The data obtained from the TurboSol test was used to select the appropriate concentrations of each drug to be tested in the patch clamp studies.The 3 drugs with known cardiac adverse events in patients (crizotinib, sunitinib, and nilotinib) potently blocked the hERG channel, resulting in IC 50 values of 1.7 muM, 0.5 muM, and 0.7 muM, respectively."
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"Using a ventricular action potential voltage clamp protocol, halofantrine and N-desbutylhalofantrine block of HERG current was greatest during phases 2 and 3 of the action potential waveform."
Clamp increases the amount of KCNH2.
| 1
Clamp increases the amount of KCNH2. 1 / 1
| 1
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"The development of high-throughput automated patch clamp assays has increased the amount of hERG associated data available in public databases."
| 3
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"In comparison, ciprofloxacin also produced little reduction of HERG current amplitude, although the inhibitory effect was more marked (47.6 +/-1.9% max, P < 0.05, at 335 muM."
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"In comparison, ciprofloxacin also failed to produce a 50% inhibition of HERG current amplitude, although the maximum blockade was greater than that observed with prulifloxacin (47.6 +/- 1.9% at the highest concentration tested (335 microM)."
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"Ciprofloxacin also failed to produce a 50% inhibition of HERG current amplitude, although the maximum blockade (47.6 +/-1.9% at 335 muM, the highest concentration tested) was greater than that observed with AF 3013."
Chloroform affects KCNH2
| 3
Chloroform inhibits KCNH2.
| 2
| 2
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"The methanolic extract of the TCM herbal drug Coptidis rhizoma (Coptis chinensis Franch., Ranunculaceae) reduced the peak tail hERG current by 31.7 +/- 2.0% at 100 microg/mL."
reach
"In HEK 293 cells stably expressing cardiac ion channel genes, trichloromethane reduced hNav1.5, HCN2, and hERG currents with IC (50) s of 8.2, 3.3, and 4.0 mM, respectively."
Chloroform activates KCNH2.
| 1
| 1
reach
"Further optimization resulted in the replacement of the 2-fluoro substituent by a CF 3 -group, which reduced hERG inhibition."
Ceramide affects KCNH2
| 2 3
Ceramide inhibits KCNH2.
| 1 1
| 1 1
reach
"For instance, ceramide down-regulates the HERG potassium channel XREF_BIBR, and affect the resting membrane potential of thyroid FRTL-cells by processes involving protein kinase C zeta XREF_BIBR."
Ceramide decreases the amount of KCNH2.
| 1 1
Ceramide decreases the amount of KCNH2. 1 / 1
| 1 1
reach
"Surface expression of the HERG channel protein was reduced by ceramide as shown by biotinylation of surface proteins, western blotting and immunocytochemistry."
Ceramide activates KCNH2.
| 1
| 1
reach
"Chapman et al. confirmed that ceramide induced modification of HERG currents and an associated rapid decline in HERG protein can be caused by protein ubiquitinylation and subsequent lysosomal degradation [XREF_BIBR]."
Celastrol affects KCNH2
| 1 3
Celastrol inhibits KCNH2.
| 1 2
| 1 2
reach
"In addition, celastrol blocks ion conduction of cardiac Kir2.1 and hERG potassium channels and reduces channel density on cell surface upon chronic treatment, which may predict cardiotoxicity."
reach
"Chronic inhibition of cardiac Kir2.1 and HERG potassium channels by celastrol with dual effects on both ion conductivity and protein trafficking."
Celastrol decreases the amount of KCNH2.
| 1
Celastrol decreases the amount of KCNH2. 1 / 1
| 1
reach
"Additionally, the elevated hERG1 level by miR-493 inhibitors could be partially reversed by celastrol, which is a well-known hERG channel inhibitor."
Capsaicin affects KCNH2
| 3
| 3
reach
"XREF_BIBR found that capsaicin, a pungent irritant occurring in peppers, enhances hERG block upon mutation of Y652A 4-fold, while F656 was suggested to be relatively unimportant for block."
reach
"The results show that capsaicin blocks WT hERG in a concentration dependent manner, with an IC (50) of 17.45 microM and a negative shift in the steady-state inactivation curve."
reach
"In conclusion, capsaicin blocks hERG channels by binding to both the closed and open channel states.Y652 was important as a molecular determinant of blockade."
| 3
Buprenorphine inhibits KCNH2.
| 2
reach
"Methadone, buprenorphine and many structurally diverse drugs can block the hERG XREF_BIBR, XREF_BIBR resulting in a prolonged QTc interval XREF_BIBR."
reach
"Methadone is the opiod most tightly associated with QTc prolongation; with much lesser potency buprenorphine and oxycodone can block HERG channels and depress the IKr current in vitro.Antineoplastic chemotherapy like anthracyclines, alkylating drugs, alkilants and cisplatin are associated with electrocardiographic alterations including prolongation of QT and emesis of different grades."
Buprenorphine activates KCNH2.
| 1
| 1
reach
"Buprenorphine may potentiate the effects of other hERG blocking agents, and our results suggest that the combination of buprenorphine and methadone may be associated with a higher risk of QTc prolongation and torsade de pointes than methadone alone."
| 1 1 2
| 1 1 2
trips
"Inhibition of HERG current by brompheniramine showed time-dependence."
reach
"Brompheniramine inhibited HERG current in a concentration dependent manner with the half-maximal inhibitory concentration (IC50) value of 1.7 microm at 0 mV."
reach
"These results indicate that brompheniramine mainly inhibited the HERG potassium channel through the residue Y652 and F656 and these residues may be an obligatory determinant in inhibition of HERG current for brompheniramine."
Beta1 integrin affects KCNH2
| 3
KCNH2 binds beta1 integrin. 3 / 3
| 3
reach
"Overall, hERG1 may stimulate nuclear translocation of p65, thus regulating the NF-kappaB pathway through the activation of the hERG1 and beta1 integrin complex and PI3K and AKT signaling."
reach
"Our preliminary results suggest that the HERG channel proteins form a complex with the beta1 integrin, in a manner similar to that in SH-SY5Y neuroblastoma cells and HEK-293 cells stably transfected with HERG [31]."
reach
"Both effects are mediated by the formation of a hERG1 and beta1 integrin complex."
BetA1 affects KCNH2
| 3
BetA1 activates KCNH2.
| 2
BetA1 activates KCNH2. 2 / 2
| 2
reach
"In addition to the increase in hERG1 currents, beta1 activation leads hERG1 to form a macromolecular membrane complex that comprises the beta 1 integrin subunit and the p85 subunit of PI3K."
reach
"Beta 1 engagement increased the hERG1 current density (XREF_FIG upper panel), reaching average amplitudes of more than 3pA/pF at -120 mV, after 120min of incubation."
BetA1 binds KCNH2.
| 1
| 1
reach
"Hence, both an activated integrin and a functional channel are required for the hERG1 and beta 1 complex formation (see the cartoon bottom right in XREF_FIG)."
| 1 2
| 1 2
reach
"(1) Azithromycin reduced hERG currents by accelerated channel inactivation."
eidos
"Azithromycin weakly blocks hERG from conducting potassium ions across the cardiac membrane while chloroquine and hydroxychloroquine decrease the number of ions available for transit ."
| PMC
reach
"Azithromycin weakly blocks hERG from conducting potassium ions across the cardiac membrane while chloroquine and hydroxychloroquine decrease the number of ions available for transit."
| PMC
Ato affects KCNH2
| 3
Ato decreases the amount of KCNH2. 3 / 3
| 3
reach
"Mechanistically, an increase in PML SUMOylation by ATO or Ang II dramatically enhanced the formation of PML and Pin1 complexes in PML-NBs, leading to the upregulation of TGF-beta1 protein, eventually inhibiting HERG expression through activation of protein kinase A."
reach
"Immunoblot analysis indicated that GA treatment partially abolished PML SUMOylation that was induced by ATO or Ang II, consequently reversing the decreased HERG protein expression caused by ATO and Ang II."
reach
"ATO or Ang II inhibited HERG protein expression in cardiomyocytes."
| 3
Arsenous acid activates KCNH2.
| 2
| 2
reach
"In contrast to other drugs, which result in blockade via binding to specific sites within the channel, arsenic trioxide appears to produce hERG liability by inhibition of ion-channel trafficking resulting in reduced channel expression on the cell surface."
reach
"This man was positive for both the KCNQ1 p.L353L variant and the KCNH2 p.K897T variant, but had been treated with arsenic trioxide, a chemotherapeutic agent which is also a potent QT prolonging drug."
Arsenous acid decreases the amount of KCNH2.
| 1
Arsenous acid decreases the amount of KCNH2. 1 / 1
| 1
reach
"Both arsenic trioxide (ATO) and angiotensin II (Ang II) were able to significantly reduce HERG protein expression, while also increasing PML SUMOylation and accelerating the formation of PML-NBs."
Amoxicillin affects KCNH2
| 3
Amoxicillin inhibits KCNH2.
| 2
| 2
reach
"In comparison with sparfloxacin (SPX), levofloxacin lactate (LVFX), the potency of AX to inhibit HERG tail currents was the least one, with an IC (50) value of 460.37 microM."
reach
"Taken together, our data suggest that AX only causes a minor reduction of I (HERG and MiRP1) at the estimated free plasma level."
Amoxicillin activates KCNH2.
| 1
| 1
reach
"The administration of AX caused voltage- and time dependent inhibition of HERG K+ current (I (HERG and MiRP1)) in a concentration dependent manner but did not markedly modify the properties of channel kinetics, including activation, inactivation, deactivation and recovery from inactivation as well."
UPF1 affects KCNH2
| 3
UPF1 inhibits KCNH2. 3 / 3
| 3
reach
"In addition, UPF1 knockdowns restored partial hERG channel function in cells expressing hERG transcripts containing PTCs that are associated with the cardiac disorder long-QT syndrome type 2."
reach
"Patch clamp analysis revealed that UPF1 knockdown significantly increased hERG current amplitude of the Q1070X mutant (XREF_FIG)."
reach
"Patch clamp analysis revealed that UPF1 suppression significantly increased the hERG current amplitude in the mutant cells (XREF_FIG)."
TRIOBP-1 affects KCNH2
| 3
TRIOBP-1 decreases the amount of KCNH2.
| 1
Modified TRIOBP-1 decreases the amount of KCNH2. 1 / 1
| 1
reach
"TRIOBP-1 overexpression reduced hERG surface expression and current density, whereas reducing TRIOBP-1 expression via shRNA knockdown resulted in increased hERG protein levels."
TRIOBP-1 binds KCNH2.
| 1
KCNH2 binds TRIOBP-1. 1 / 1
| 1
reach
"These findings establish that TRIOBP-1 interacts directly with hERG and can affect protein levels, I Kr magnitude, and cardiac membrane excitability."
TRIOBP-1 activates KCNH2.
| 1
TRIOBP-1 activates KCNH2. 1 / 1
| 1
reach
"In human stem cell derived cardiomyocytes, TRIOBP-1 overexpression caused intracellular co-sequestration of hERG signal, reduced native I Kr, and disrupted action potential repolarization."
State affects KCNH2
| 3
State inhibits KCNH2. 3 / 3
| 3
reach
"State dependent barium block of wild-type and inactivation deficient HERG channels in Xenopus oocytes."
reach
"State dependent inhibition of hERG channel currents and slow kinetics for recovery from block suggest that many drugs bind within the inner cavity of the channel and are trapped by closure of the activation gate upon repolarization."
reach
"State dependent block of HERG potassium channels by R-roscovitine : implications for cancer therapy."
SLC2A1 affects KCNH2
| 3
| 3
sparser
"Moreover, hERG1 presence associated with Glut-1 absence represents an independent negative prognostic factor in TNM I and II colorectal adenocarcinomas [ xref ]."
sparser
"Finally, in a cohort of primary nonmetastatic CRC samples it was shown that hERG1 expression was associated with Glut-1 (glucose transporter 1), VEGF-A, CA-IX (carbonic anhydrase IX), and EGF-R expression [ xref ]."
sparser
"The expressions of hERG1 and Glut-1 were significantly associated ( P =0.001), whereas no significant association between KCa3.1 and the other two biomarkers emerged."
SGK3 affects KCNH2
| 2 3
SGK3 activates KCNH2.
| 2 2
SGK3 activates KCNH2. 2 / 2
| 2 2
reach
"Interestingly, it has been reported that the serum and glucocorticoid inducible kinase 3 (SGK3) up-regulates I hERG1 by increasing protein levels in the plasma membrane, without affecting the K + channel activating kinetics [31]."
reach
"HERG channel activity is up-regulated by the serum- and glucocorticoid inducible kinase isoforms SGK1 and SGK3."
SGK3 inhibits KCNH2.
| 1
SGK3 inhibits KCNH2. 1 / 1
| 1
reach
"In their study, Maier et al. concluded that SGK3 down-regulation of hERG1 is not achieved through direct phosphorylation of the K + channel, but might result from the phosphorylation and inactivation of Nedd4-2 which decreases substrate affinity and ubiquitylation [31]."
S4 affects KCNH2
| 3
S4 activates KCNH2.
| 2
S4 activates KCNH2. 2 / 2
| 2
reach
"Thus, these electrical measurements supported the conclusion from the fluorescence measurements that slow S4 movement underlies hERG gating kinetics."
reach
"There are two obvious possibilities : (1) either the slow fluorescence reflects S4 movements that underlie HERG activation gating, or (2) the probe is able to sense conformational changes occurring in or near the pore and, thus, simply reports the opening and closing of the pore."
S4 inhibits KCNH2.
| 1
S4 inhibits KCNH2. 1 / 1
| 1
reach
"We have examined whether hERG channels possess a transfer center similar to that described in Shaker and if these S4 charge differences contribute to slow gating in hERG channels."
RNF207 affects KCNH2
1 | 2
RNF207 binds KCNH2.
1 | 1
1 | 1
biogrid
No evidence text available
reach
"Functional investigation to investigate any interaction between KCNH2 and RNF207 is necessary."
RNF207 increases the amount of KCNH2.
| 1
Modified RNF207 increases the amount of KCNH2. 1 / 1
| 1
reach
"Finally, coexpression of RNF207 and HSP70 increased HERG expression compared with HSP70 alone."
Prostratin affects KCNH2
| 3
Prostratin activates KCNH2. 2 / 2
| 2
reach
"Strikingly, either Prostratin or IDB treatment enhanced the current density of hERG K + channels in a dose dependent pattern when we co-expressed hERG WT and hERG A561V at a ratio of 2:1."
reach
"Western blotting experiments showed that both Prostratin and IDB promoted trafficking of hERG WT -hERG A561V channels in a dose dependent pattern, as reflected by the elevated 155kD hERG proteins, which distributed outside the ER."
Prostratin activates mutated KCNH2. 1 / 1
| 1
reach
"Together, Prostratin and IDB specifically promote the function of some trafficking defective hERG mutant channels."
PTPN6 affects KCNH2
2 | 1
PTPN6 inhibits KCNH2.
1 |
PTPN6 inhibits KCNH2. 1 / 1
1 |
signor
"Our results show that erg-1 is a shp-1 substrate constituting the first report that an ion current is regulated by shp-1."
PTPN6 dephosphorylates KCNH2.
1 |
PTPN6 dephosphorylates KCNH2. 1 / 1
1 |
signor
"Our results show that erg-1 is a shp-1 substrate constituting the first report that an ion current is regulated by shp-1."
PTPN6 binds KCNH2.
| 1
| 1
sparser
"Next, we determined that this motif is necessary for the interaction of hERG with SHP-1 tyrosine phosphatase."
PML affects KCNH2
| 3
PML decreases the amount of KCNH2.
| 2
Sumoylated PML decreases the amount of KCNH2. 2 / 2
| 2
reach
"Mechanistically, an increase in PML SUMOylation by ATO or Ang II dramatically enhanced the formation of PML and Pin1 complexes in PML-NBs, leading to the upregulation of TGF-beta1 protein, eventually inhibiting HERG expression through activation of protein kinase A."
reach
"PML SUMOylation decreased HERG protein expression."
PML increases the amount of KCNH2.
| 1
PML increases the amount of KCNH2. 1 / 1
| 1
reach
"Immunoblot analysis indicated that GA treatment partially abolished PML SUMOylation that was induced by ATO or Ang II, consequently reversing the decreased HERG protein expression caused by ATO and Ang II."
PK affects KCNH2
| 3
PK inhibits KCNH2.
| 2
PK inhibits KCNH2. 2 / 2
| 2
reach
"Our present study revealed that while PK cleaves hERG at the S5-S6 linker and abolishes I hERG, it cleaves Kv1.5 at the S1-S2 linker and does not decrease I Kv1.5."
reach
"However, due to differences between hERG and Kv1.5 in terms of their three extracellular linkers (length, sequence, and 3D structure), PK cleaves hERG in the S5-S6 linker and eliminates I hERG, whereas PK cleaves Kv1.5 in S1-S2 linker and does not hinder Kv1.5 function.Our data show that the immature core glycosylated 68-kDa channels are not the form conducting I Kv1.5."
PK activates KCNH2.
| 1
PK activates KCNH2. 1 / 1
| 1
reach
"Twenty-four hours after transfection, cells were collected following trypsinization, and GFP positive cells were selected for patch clamp experiments.Live HEK cells stably expressing Kv1.5 or hERG channels were treated with PK (200 mug/ml in MEM) (Sigma-Aldrich, St. Louis, MO) in the cell culture medium at 37 degreesC for 20 min."
PIKFYVE affects KCNH2
| 3
PIKFYVE activates KCNH2.
| 2
PIKFYVE activates KCNH2. 2 / 2
| 2
reach
"Coexpression of PIKfyve increased hERG channel protein abundance in the cell membrane."
reach
"HERG is up-regulated by PIKfyve, which is in turn activated by PKB and Akt."
PIKFYVE increases the amount of KCNH2.
| 1
Modified PIKFYVE increases the amount of KCNH2. 1 / 1
| 1
reach
"Coexpression of wild type PIKfyve increased hERG channel activity in hERG expressing Xenopus oocytes."
PI3K affects KCNH2
| 1 2
PI3K binds KCNH2.
| 1 1
| 1
reach
"The beta 1 / hERG1 and PI3K complex, through Akt, induces HIF (s) transcriptional activation."
| 1
sparser
"Furthermore, by sequestering the channel in the closed conformation, Cla inhibited the formation of a macromolecular complex between hERG1 and the p85 subunit of PI3K. This strongly reduced Akt phosphorylation, and stimulated the p53-dependent cell apoptosis, as witnessed by late caspase activation."
PI3K inhibits KCNH2.
| 1
PI3K inhibits KCNH2. 1 / 1
| 1
reach
"The quantitative data are presented in Fig. 4C where the ratios of staining intensity in positively stained cells over non stained control cells are shown.We demonstrated here that prevention of PI3K and PKB activation by pharmacological inhibition (WMN) or molecular inactivation (dnPI3K and dnPKB) significantly suppressed HERG function, whereas direct activation of PKB by introducing caPKB into the cell markedly enhanced HERG function."
PBA affects KCNH2
| 3
PBA activates KCNH2. 3 / 3
| 3
reach
"Activation by the boronic acid moiety has some specificity for the Kv7 family members (KCNQ1, KCNQ2/3, and KCNQ4) since PBA does not activate Shaker or hERG channels."
reach
"HERG inhibition is a concern for small molecule drug design; however, PBA inhibition of hERG does not appear to occur by classic inner vestibule block XREF_BIBR."
reach
"Activation appears to be somewhat specific for KCNQ channels, as Shaker and hERG are not activated by PBA."
NS3623 affects KCNH2
| 3
NS3623 activates KCNH2. 3 / 3
| 3
reach
"The results show that I hERG is quickly, and reversibly, activated by NS3623."
reach
"3.7 Effect of KChIP2 and DPP6 in the NS3623 mediated I hERG activation."
reach
"In contrast, application of NS3623 to the mutant F656M increased HERG1 current to a larger extent than what was observed with wild-type HERG1 channels."
NH affects KCNH2
| 1 2
NH inhibits KCNH2.
| 1
NH inhibits KCNH2. 1 / 1
| 1
reach
"In contrast to N-type inactivation in Shaker, however, there was no indication that the NH 2 terminus blocks the HERG pore."
NH binds KCNH2.
| 1
KCNH2 binds NH. 1 / 1
| 1
sparser
"We tested the hypothesis that the HERG NH 2 terminus interacts with the S4–S5 linker in a manner analogous to the interaction of the Shaker NH 2 terminus with the corresponding residues at the internal mouth of the pore."
NH activates KCNH2.
| 1
NH activates KCNH2. 1 / 1
| 1
reach
"The goal of this study was to explore the mechanism by which the NH 2 terminus modulates deactivation rate in HERG channels."
| 3
reach
"Proteasome inhibitors, N-acetyl-L-leucyl-L-leucyl-L-norleucinal and MG132 prevented the 5alpha-DHT- dependent enhancement of HERG, as did the lysosome inhibitor, bafilomycin A1."
reach
"The proteasome inhibitor MG132 increased the expression of immature A78T-HERG and increased both the immature and mature forms of WT-HERG."
reach
"Furthermore, THIO treatment in the presence of MG132 increased the steady-state level of ubiquitylated hERG protein, suggesting that THIO stimulates the degradation of the misprocessed hERG protein by the ubiquitination-proteasome pathway (XREF_FIG)."
Matrine affects KCNH2
| 3
Matrine inhibits KCNH2.
| 2
| 2
reach
"Unlike most other blockers exerting blocking effect at the intracellular sites by entering the cell with the opening of HERG channel, matrine blocked HERG channels at the extracellular sites."
reach
"Matrine had no significant effect on the activation kinetics, and mainly blocked HERG channels in their closed state."
Matrine increases the amount of KCNH2.
| 1
Matrine increases the amount of KCNH2. 1 / 1
| 1
reach
"In this study, we demonstrated that 1 muM matrine and oxymatrine could rescue the hERG current and hERG surface expression inhibited by probucol."
Loratadine affects KCNH2
| 3
| 3
reach
"Finally, loratadine (10 microM) failed to inhibit HERG K+ channel currents expressed in Xenopus laevis oocytes."
reach
"However, loratadine (10 mumol/L) failed to inhibit HERG potassium channel and HERG K+."
reach
"According to the Canadian FDA report 64, loratadine does not significantly block hERG potassium channels under the same in vitro conditions for terfenadine which showed a strong hERG inhibition 64."
La affects KCNH2
| 3
La inhibits KCNH2. 3 / 3
| 3
reach
"La 3+, which reportedly blocks HERG like currents in a voltage dependent manner, inhibited the microglial current."
reach
"HERG Current Is Blocked by La ~ * (A) Control currents activated by 4 s pulses to potentials ranging from -50 to +50 inV."
reach
"The HERG like current in rat microglia was inhibited by La 3+ with a K i of ~ 40 muM."
LY97241 affects KCNH2
| 3
LY97241 inhibits KCNH2.
| 2
LY97241 inhibits KCNH2. 2 / 2
| 2
reach
"The extremely slow reversal of HERG block by clofilium and LY97241 suggests a similar mechanism for these compounds."
reach
"Our results contradict the claim that LY97241 blocks HERG channels exclusively (Suessbrich et al. 1997); however, the higher doses of LY97241 used in our work suggest that this compound may be a more potent blocker of HERG than Kv1.5 channels.Recovery of Kv1.5 channels from block by clofilium was optimal at -45 mV (at pH 7.3), near the threshold for channel activation."
LY97241 activates KCNH2.
| 1
LY97241 activates KCNH2. 1 / 1
| 1
reach
"In addition, LY97241 increases the rate of HERG channel inactivation, similarly as previously reported for the antipsychotic drug haloperidol [20]."
KCNH2 affects voltage-gated potassium channel
| 3
KCNH2 binds voltage-gated potassium channel.
| 2
KCNH2 binds voltage-gated potassium channel. 1 / 1
| 1
sparser
"The voltage-gated potassium channel formed by hERG pore-forming alpha subunits generates the IKr cardiac potassium current, and is considered essential for human ventricular repolarization."
KCNH2 binds KCNQ1 and voltage-gated potassium channel. 1 / 1
| 1
sparser
"Both LQT1 and LQT2 are associated with loss of function of voltage-gated potassium channels (I Ks and I Kr ). xref "
KCNH2 inhibits voltage-gated potassium channel.
| 1
KCNH2 inhibits voltage-gated potassium channel. 1 / 1
| 1
sparser
"Broccatelli et al. [ xref ] used the BDDCS to help consider for which drugs hERG voltage-gated potassium channel inhibition is likely to lead to Torsade de Pointes."
KCNH2 affects type 2 long QT syndrome
| 3
KCNH2 activates type 2 long QT syndrome.
| 2
KCNH2 activates type 2 long QT syndrome. 1 / 1
| 1
reach
"Mutations in the KCNH2 gene were reported to cause type 2 long QT syndrome (LQT2), a rare inherited ion channel disorder characterized by prolonged QT interval and predisposing patients to ventricular arrhythmias that can lead to syncope and sudden cardiac death (SCD)."
Mutated KCNH2 activates type 2 long QT syndrome. 1 / 1
| 1
reach
"Most of mutant hERG proteins causing the type 2 long QT syndrome (LQT2) fail to mature in the endoplasmic reticulum (ER) and Golgi apparatus XREF_BIBR."
KCNH2 inhibits type 2 long QT syndrome.
| 1
Mutated KCNH2 inhibits type 2 long QT syndrome. 1 / 1
| 1
reach
"Loss-of-function KCNH2 mutations cause the type 2 long QT syndrome (LQT2), and most LQT2 linked missense mutations inhibit the trafficking of Kv11.1 channels."
| 1 3
| 1 2
reach
"These data suggest that prolonged stimulation of the hERG1 potassium channel may activate a senescence program and offers a compelling opportunity to develop a potential antiproliferative cancer therapy."
reach
"HERG1 agonist treatment increases protein level of cellular senescence markers."
| 1
reach
"In addition, although HERG channel blockers inhibit the growth of multiple cancer cell types, application of the HERG channel activator also impairs mammary gland adenocarcinoma growth by inducing a senescence program."
| 1 3
| 1 3
reach
"For instance, in human acute myeloid leukemia cells, hERG1 channels appear to mediate the vascular endothelial growth factor receptor-1-dependent cell migration and invasion, both in vitro and in vivo."
reach
"We conclude that in AML, hERG1 channels mediate the FLT-1-dependent cell migration and invasion, and hence confer a greater malignancy."
reach
"Activation of HERG with PD118057 stimulated cell migration."
| 1 3
| 1 3
reach
"Moreover, K v 3.3 may also be involved in the cell adhesion process, similar to the function of hERG potassium channels [XREF_BIBR], even if the effect is in the opposite direction; the hERG potassium channels enhance cell adhesion, whereas K v 3.3 inhibits cell adhesion."
reach
"HERG K+ channels activation during beta (1) integrin mediated adhesion to fibronectin induces an up-regulation of alpha (v) beta (3) integrin in the preosteoclastic leukemia cell line FLG 29.1."
reach
"We have recently shown that hERG1 is physically linked to beta1 integrins and thereby modulate adhesion dependent signaling (Cherubini et al, 2005)."
KCNH2 affects beta1 integrin
| 3
KCNH2 binds beta1 integrin. 3 / 3
| 3
reach
"Overall, hERG1 may stimulate nuclear translocation of p65, thus regulating the NF-kappaB pathway through the activation of the hERG1 and beta1 integrin complex and PI3K and AKT signaling."
reach
"Our preliminary results suggest that the HERG channel proteins form a complex with the beta1 integrin, in a manner similar to that in SH-SY5Y neuroblastoma cells and HEK-293 cells stably transfected with HERG [31]."
reach
"Both effects are mediated by the formation of a hERG1 and beta1 integrin complex."
KCNH2 affects autophagy
| 3
KCNH2 inhibits autophagy.
| 2
| 2
reach
"Hence, silencing hERG1 triggers autophagy but, at difference with hERG1 blockade, does not impair the autophagy flux."
reach
"Hence, blocking hERG1 triggers autophagy and blocks the autophagic flux, similarly to MAs."
KCNH2 activates autophagy.
| 1
| 1
reach
"Hence, silencing hERG1 triggers autophagy but, at difference with hERG1 blockade, does not impair the autophagy flux."
KCNH2 affects astemizole
| 3
KCNH2 binds astemizole.
| 2
reach
"Purified recombinant hERG binds Astemizole."
reach
"Astemizole binds with high affinity to membrane embedded hERG with a single binding site per tetramer."
KCNH2 inhibits astemizole.
| 1
| 1
reach
"High-affinity hERG channel blocking drugs E4031, astemizole, cisapride and quinidine all produced reverse effects, and the rescue was dependent on their interaction with F656."
KCNH2 affects STUB1
2 | 1
2 | 1
biogrid
No evidence text available
biogrid
No evidence text available
reach
"CHIP recruitment to nonnative hERG is probably mediated via Hsc/Hsp70/Hsp90 binding to exposed hydrophobic residues that are otherwise buried in the native channel, similar to that described for other misfolded ER, cytosolic, and PM polypeptides."
KCNH2 affects SQT1
| 1 2
KCNH2 inhibits SQT1.
| 1
KCNH2-N588K inhibits SQT1. 1 / 1
| 1
reach
"The attenuated inactivation N588K HERG mutant used in this study has been shown recently to underlie the SQT1 familial form of the recently identified genetic ' Short QT syndrome ', which carries a risk of cardiac arrhythmia and sudden death XREF_BIBR."
KCNH2 binds SQT1.
| 1
| 1
sparser
"It has been suggested that class IA drugs may provide the best therapeutic avenue for treatment of SQT1 form of SQTS caused by N588K mutation in HERG ."
KCNH2 activates SQT1.
| 1
KCNH2 activates SQT1. 1 / 1
| 1
reach
"SQTS has been associated with the gain-of-function mutations in 3 distinct potassium channels, KCNH2, KCNQ1 and KCNJ2, which cause SQT1, SQT2 and SQT3, respectively [111-114]."
KCNH2 affects QTc
| 2 3
KCNH2 activates QTc.
| 2 2
KCNH2 activates QTc. 2 / 2
| 2 2
reach
"A retrospective analysis of 34 TQT studies40 followed by two prospective clinical trials22, 41 including eight drugs demonstrated that drugs that predominantly block hERG prolong QTc by prolonging both J-Tpeakc (early repolarization) and Tpeak-Tend (late repolarization), while drugs that block hERG along with calcium and/or late sodium (balanced ion channel block) prolonged QTc by prolonging Tpeak-Tend with no or limited effect on the J-Tpeakc interval.22, 40, 41 Figure XREF_FIG b shows data from the first prospective clinical trial,41 where dofetilide (predominant hERG blocker) prolonged QTc by prolonging both J-Tpeakc and Tpeak-Tend."
reach
"The primary objectives of the study are : To confirm that exposure response analysis of the electrocardiographic QTc and J-Tpeakc intervals in phase I clinical pharmacology studies can be used to confirm that balanced ion channel blocking drugs do not cause J-Tpeakc prolongation and predominant hERG blocking drugs cause QTc prolongation."
KCNH2 inhibits QTc.
| 1
KCNH2 inhibits QTc. 1 / 1
| 1
reach
"While predominant hERG blockers prolonged QTc and J-Tpeakc, " balanced " ion channel blocking drugs (hERG+ late sodium and/or calcium block) prolonged QTc without prolonging J-Tpeakc."
KCNH2 affects MMP14
| 3
KCNH2 glycosylates MMP14.
| 2
KCNH2 glycosylates MMP14. 2 / 2
| 2
reach
"To test whether ER-G1 stimulates the glycosylation of MMP14, Tn modified proteins were pulled down using VVL and probed for MMP14 from liver tumors derived from ER-G1-expressing tumors at 6 wpi."
reach
"Unlike its Golgi localized counterpart, ER-G1 glycosylates the matrix metalloproteinase MMP14, a process required for tumor expansion."
KCNH2 activates MMP14.
| 1
KCNH2 activates MMP14. 1 / 1
| 1
reach
"Overall, these data suggest that ER-G1 expression upregulates MMP14 activity.MMP14 is known to be O glycosylated on five residues located in the hinge domain between residues T291 and S304, with glycosylation of S304 still debated (Ludwig et al., 2008)."
KCNH2 affects Lys-Ser
| 3
KCNH2 activates Lys-Ser.
| 2
KCNH2 activates Lys-Ser. 2 / 2
| 2
reach
"However, the presence of WT HERG decreased the deactivation time constant for I Ks and the presence of G816V HERG decreased the I Ks time constant to a greater degree (XREF_FIG)."
reach
"Mutations in the KCNQ1 and HERG genes cause the Long QT Syndromes, LQTS1 and LQTS2, due to reductions in the cardiac repolarizing I Ks and I Kr currents, respectively."
KCNH2 inhibits Lys-Ser.
| 1
KCNH2-G816V inhibits Lys-Ser. 1 / 1
| 1
reach
"However, the presence of WT HERG decreased the deactivation time constant for I Ks and the presence of G816V HERG decreased the I Ks time constant to a greater degree (XREF_FIG)."
KCNH2 affects Kv4.3
| 3
KCNH2 binds Kv4.3. 3 / 3
| 3
reach
"Because Hsp70 was reported to interact with hERG 27 and the present study showed that hERG interacts with Kv4.3, we hypothesize that Hsp70 may form complexes with hERG and Kv4.3."
reach
"We observed that Kv4.3 interacted with hERG and increased hERG expression through Hsp70."
reach
"The result showed that hERG and Kv4.3 bind to each other and form a complex."
KCNH2 affects HSPA8
2 | 1
2 |
biogrid
No evidence text available
biogrid
No evidence text available
HSPA binds HSPA8 and KCNH2. 1 / 1
| 1
sparser
"Interestingly, although both Hsp70 and Hsc70 associated with hERG channels, it was reported that Hsp70 enhanced the maturation of hERG channels while Hsc70 suppressed their maturation xref ."
KCNH2 affects HSP90AA1
3 |
biogrid
No evidence text available
biogrid
No evidence text available
biogrid
No evidence text available
KCNH2 affects GST
| 1 2
| 1 2
reach
"To test for interactions, H 6 hERG 666-872 Flag was added to the bead bound GST N1-135 or GST proteins and allowed to incubate overnight."
reach
"The next day, the beads were washed to remove any unbound fusion proteins, and hERG 666-872 fusion proteins that were associated with bead bound GST N1-135 were analyzed by SDS-PAGE and identified with a Western blot."
sparser
"The next day, the beads were washed to remove any unbound fusion proteins, and hERG 666–872 fusion proteins that were associated with bead-bound GST N1–135 were analyzed by SDS-PAGE and identified with a Western blot."
KCNH2 affects FN1
| 3
KCNH2 activates FN1.
| 2
KCNH2 activates FN1. 2 / 2
| 2
reach
"HERG K+ channels activation during beta (1) integrin mediated adhesion to fibronectin induces an up-regulation of alpha (v) beta (3) integrin in the preosteoclastic leukemia cell line FLG 29.1."
reach
"In leukemic osteoclastic progenitors, hERG1 activates during cell adhesion to fibronectin."
KCNH2 inhibits FN1.
| 1
KCNH2 inhibits FN1. 1 / 1
| 1
reach
"Among the 35 compounds analyzed, we have detected a low rate (8.5%) of false negatives (FN) : Of the three FN found (Ziprasidone, L-768763 and Chromanol 293b), Ziprasidone was the only HERG blocker undetected out of 15 tested."
KCNH2 affects FKBP8
3 |
3 |
biogrid
No evidence text available
biogrid
No evidence text available
biogrid
No evidence text available
KCNH2 affects ERG
| 2 1
KCNH2 binds ERG.
| 2
| 1
sparser
"Proliferation of arterial smooth muscle cells was associated with a marked increase in ERG1 expression and ERG blockers suppressed proliferation significantly."
AP1 binds ERG and KCNH2. 1 / 1
| 1
sparser
"C is -elements contributing to this inducibility were mapped to the proximal promoter region and these elements were shown to interact with transcription factors Erg-1, Erg-3, ATF-3/CREB and AP-1 upon stimulation ( xref )."
KCNH2 inhibits ERG.
| 1
KCNH2 inhibits ERG. 1 / 1
| 1
reach
"Using cell biology and electrophysiologic techniques, we found that hypoxic culture of hERG expressing human embryonic kidney (HEK) cells and neonatal rat cardiomyocytes reduced hERG current / I Kr and mature ERG channel expression with a concomitant increase in calpain expression."
KCNH2 affects CXCR4
| 1 2
KCNH2 activates CXCR4.
| 2
KCNH2 activates CXCR4. 2 / 2
| 2
reach
"HERG channels reportedly contribute to outside-in signaling in complexes with beta1 integrin (see Introduction) and CXCR4 in the plasma membrane."
reach
"HERG channels reportedly contribute to outside-in signaling in complexes with beta1 integrin (see Introduction) and CXCR4 in the plasma membrane."
KCNH2 binds CXCR4.
| 1
sparser
"Importantly, they demonstrated that upon β1 integrin stimulation, hERG forms signaling macro-complexes with β1-integrin, the VEGF receptor Flt-1 or the cytokine receptor CXCR4 in lipid rafts."
KCNH2 affects CAV1
| 3 2 1
| 3 1
reach
"Together with the findings that caveolin-1 interacts with potassium channels Kir2.1, KCNH2, and HCN4 and sodium channels Nav1.5 and Nav1.8, CAV1 becomes a strong candidate susceptibility gene for AF across different ethnic populations."
sparser
"The human inward rectifying voltage-gated HERG K + channel (Trudeau et al., xref ) interacts with caveolin-1 and reduces its activity when caveolin is up-regulated (Lin et al., xref )."
CAV1 binds HCN4, KCNH2, and KCNJ2. 1 / 1
| 1
sparser
"Together with the findings that caveolin-1 interacts with potassium channels Kir2.1, KCNH2, and HCN4 and sodium channels Nav1.5 and Nav1.8, CAV1 becomes a strong candidate susceptibility gene for AF across different ethnic populations."
KCNH2 affects ANK2
| 1 2
| 1 2
reach
"ANK2 functionally interacts with KCNH2 aggravating long QT syndrome in a double mutation carrier."
reach
"Our data suggest that ANK2 functionally interacts with KCNH2 leading to a stronger current suppression and marked aggravation of long QT syndrome in the patient carrying variants in both proteins."
sparser
"Our data suggest that ANK2 functionally interacts with KCNH2 leading to a stronger current suppression and marked aggravation of long QT syndrome in the patient carrying variants in both proteins."
KCNH2 affects AKT
| 3
KCNH2 activates AKT. 3 / 3
| 3
reach
"The beta 1 / hERG1 complex modulates the PI3K-Akt pathway."
reach
"HERG1 recruits and activates PI3K and Akt."
reach
"HERG1 promotes esophageal squamous cell carcinoma growth and metastasis through TXNDC5 by activating the PI3K and AKT pathway."
KB-R7943 affects KCNH2
| 3
KB-R7943 inhibits KCNH2. 3 / 3
| 3
reach
"This study investigated KB-R7943 inhibition of hERG (human ether-a-go-go-related gene) K (+) channels that underpin the cardiac rapid delayed rectifier potassium current, I (Kr)."
reach
"High potency inhibition of hERG potassium channels by the sodium-calcium exchange inhibitor KB-R7943."
reach
"For example, KB-R7943, a widely used I NCX inhibitor, was found to inhibit the hERG channel 32 and L-type Ca 2+ channels 33 with a similar potency as I NCX antagonist actions."
Ile-His affects KCNH2
| 3
Ile-His inhibits KCNH2.
| 2
| 2
reach
"IH increased reactive oxygen species (ROS) levels, intracellular Ca (2+) concentration ([Ca (2+)] i), calpain enzyme activity, and hERG protein degradation, and all these effects were prevented by manganese-(111)-tetrakis-(1-methyl-4-pyridyl)-porphyrin pentachloride, a membrane-permeable ROS scavenger."
reach
"These results demonstrate that activation of calpains by ROS dependent elevation of [Ca (2+)] i mediates hERG protein degradation by IH."
Ile-His decreases the amount of KCNH2.
| 1
Ile-His decreases the amount of KCNH2. 1 / 1
| 1
reach
"IH decreased hERG protein expression in a stimulus dependent manner."
Ibogaine affects KCNH2
| 3
| 3
sparser
"This observation goes along with noribogaine’s inhibitory action on hERG potassium channels (IC 50  = 3 µM: Fig.  xref ; [ xref ]), which very closely resembles hERG inhibition by ibogaine [ xref , xref , xref ]."
sparser
"Preliminary experiments in our laboratory do in fact suggest that also hERG channel inhibition by ibogaine is reinforced under low external potassium (unpublished data)."
sparser
"The concentration-dependence of hERG channel inhibition by ibogaine and 18-MC was determined as in our previous study ( xref ) by the pulse protocol shown in xref a, applied at a frequency of 1 Hz."
INS affects KCNH2
| 3
INS increases the amount of KCNH2. 3 / 3
| 3
reach
"In addition, we demonstrated that 100 nM insulin up-regulated the expression of the hERG channel and rescued the hERG channel repression caused by high glucose."
reach
"XREF_BIBR Furthermore, insulin treatment restored expression of HERG in diabetic myocardium."
reach
"Furthermore, insulin promotes the expression of the hERG channel and ameliorates the high-glucose-induced inhibition of the hERG channel."
IDB affects KCNH2
| 3
IDB activates KCNH2. 2 / 2
| 2
reach
"Western blotting experiments showed that both Prostratin and IDB promoted trafficking of hERG WT -hERG A561V channels in a dose dependent pattern, as reflected by the elevated 155kD hERG proteins, which distributed outside the ER."
reach
"Strikingly, either Prostratin or IDB treatment enhanced the current density of hERG K + channels in a dose dependent pattern when we co-expressed hERG WT and hERG A561V at a ratio of 2:1."
IDB activates mutated KCNH2. 1 / 1
| 1
reach
"Together, Prostratin and IDB specifically promote the function of some trafficking defective hERG mutant channels."
IC 50 affects KCNH2
| 3
IC 50 inhibits KCNH2.
| 2
IC 50 inhibits KCNH2. 2 / 2
| 2
reach
"Such noncardiovascular drugs included antipsychotics which block HERG with different degree of block : the concentrations required to produce 50% block of HERG (IC 50) were in nanomolar range for sertindole and haloperidol and in micromolar range for risperidone (Frederiksen and Adamantidis, 2000)."
reach
"Such noncardiovascular drugs included antipsychotics which block HERG with different degree of block : the concentrations required to produce 50% block of HERG (IC 50) were in nanomolar range for sertindole and haloperidol and in micromolar range for risperidone (Frederiksen and Adamantidis, 2000)."
IC 50 activates KCNH2.
| 1
IC 50 activates KCNH2. 1 / 1
| 1
reach
"The Na + o block of hERG K + currents has been reported previously, and the IC 50 value for Na + o to block the hERG Na + current is close to that for Na + o to block hERG K + currents."
Hsp90 inhibitor affects KCNH2
| 3
Hsp90 inhibitor activates KCNH2. 3 / 3
| 3
reach
"It has previously been demonstrated that the Hsp90 inhibitor, geldanamycin, inhibits hERG trafficking, presumably through an Hsp90 dependent mechanism."
reach
"The specific Hsp90 inhibitor geldanamycin prevents maturation and increases proteasomal degradation of hERG WT, while reducing hERG currents in heterologous expression systems."
reach
"In our previous study, we found that geldanamycin, an Hsp90 inhibitor, abolished the kinase dependent increase in HERG abundance."
HTR4 affects KCNH2
| 2 1
HTR4 binds KCNH2.
| 2
| 2
sparser
"From the network, we can find that 5-HT4 is interacting with the human ether-a-go-go related gene (HERG), since the two proteins share five compounds with pChEMBL above 6 ( Figure xref )."
sparser
"Several types of analogs were obtained and screened for 5-HT4 binding, hERG blocking, agonism, and gastric emptying assessment."
HTR4 inhibits KCNH2.
| 1
HTR4 inhibits KCNH2. 1 / 1
| 1
reach
"Cisapride is a serotonin 5-HT4 receptor agonist that has been reported to block the hERG potassium channel."
HSP90AA1 affects KCNH2
3 |
biogrid
No evidence text available
biogrid
No evidence text available
biogrid
No evidence text available
GST affects KCNH2
| 1 2
| 1 2
reach
"To test for interactions, H 6 hERG 666-872 Flag was added to the bead bound GST N1-135 or GST proteins and allowed to incubate overnight."
reach
"The next day, the beads were washed to remove any unbound fusion proteins, and hERG 666-872 fusion proteins that were associated with bead bound GST N1-135 were analyzed by SDS-PAGE and identified with a Western blot."
sparser
"The next day, the beads were washed to remove any unbound fusion proteins, and hERG 666–872 fusion proteins that were associated with bead-bound GST N1–135 were analyzed by SDS-PAGE and identified with a Western blot."
GS26575 affects KCNH2
| 3
| 3
reach
"Consequently, the IC 50 value for M1 is higher than 25 microM, indicating that M1 does not inhibit the hERG channel."
reach
"It was shown that both AVN-101 and M1 can block the hERG channel with IC 50 of 0.58 muM and 1.63 muM, respectively."
reach
"4 The results of the hERG assay show that M1 does not inhibit the hERG channel and, therefore, does not seem to present a serious risk of cardiac toxicity in humans."
GOLGA2 affects KCNH2
| 1 2
GOLGA2 binds KCNH2.
| 1 1
| 1 1
sparser
"MiRP1 encoded by KCNE2 is thought to regulate KCNH2 in the human heart; MinK encoded by KCNE1 may also modulate KCNH2 in vivo; 14-3-3ε binding to KCNH2 channels shifts the activation curve towards more hyperpolarized potentials; GM130, a Golgi-associated protein, interacts with KCNH2 as the channel is transported between the endoplasmic reticulum and the plasma membrane [7–10] ."
reach
"MiRP1 encoded by KCNE2 is thought to regulate KCNH2 in the human heart; MinK encoded by KCNE1 may also modulate KCNH2 in vivo; 14-3-3epsilon binding to KCNH2 channels shifts the activation curve towards more hyperpolarized potentials; GM130, a Golgi associated protein, interacts with KCNH2 as the channel is transported between the endoplasmic reticulum and the plasma membrane [7-10]."
GOLGA2 inhibits KCNH2.
| 1
GOLGA2 inhibits KCNH2. 1 / 1
| 1
reach
"Overexpression of GM130 suppressed HERG current amplitude in Xenopus oocytes, as if by providing an excess of substrate at the Golgi checkpoint."
FB213 affects KCNH2
| 3
FB213 inhibits KCNH2. 3 / 3
| 3
reach
"The concentration of FB213 required to block 50% (IC 50) of the hERG current was 47.1 +/- 5.1 muM."
reach
"FB213 inhibits hERG currents and is trapped in the cavity."
reach
"9 Recovery from the hERG channel block by FB213 was determined by applying a test pulse after a resting period of 300 s at a holding potential of -100 mV, where the channels are in a closed resting state."
| 1 2
sparser
"According to our data, caution must nonetheless be taken when using these pleiotropic agents with widespread effects, as in addition to derepressing TSGs silenced in cancer, HDACi could activate and promote HERG1 and hEAG1 oncogenic potential."
reach
"According to our data, caution must nonetheless be taken when using these pleiotropic agents with widespread effects, as in addition to derepressing TSGs silenced in cancer, HDACi could activate and promote HERG1 and hEAG1 oncogenic potential."
reach
"An HDAC inhibitor that structurally can not inhibit HDAC3 and can not bind hERG, then, would be of considerable therapeutic interest."
| 2 1
E3_Ub_ligase ubiquitinates KCNH2.
| 1
E3_Ub_ligase ubiquitinates KCNH2. 1 / 1
| 1
sparser
"Guo et al. reported that another E3 ubiquitin ligase, Nedd4-2, ubiquitinates and eliminates mature HERG channels [ xref ]."
E3_Ub_ligase inhibits KCNH2.
| 1
| 1
reach
"We previously showed that the E3 ubiquitin ligase Nedd4-2 mediates degradation of hERG channels."
| 1
sparser
"Ablation of the neural precursor cell–expressed developmentally down-regulated protein 4 long isoform (Nedd4-2) E3 ligase, which associates with the C-terminal PY motif of hERG ( xref ), failed to counteract the metabolic instability in the presence of glycosides or hERG mutations (Supplemental Figure S5, C and F, and unpublished data)."
DNAJA1 affects KCNH2
1 | 2
DNAJA1 inhibits KCNH2.
| 1
DNAJA1 inhibits KCNH2. 1 / 1
| 1
reach
"Our observations are thus similar to those described by Walker and colleagues, who reported that DnaJA1, DnaJA2 and DnaJA4 reduced hERG channel maturation, whereas over-expression of Hsc70 alone had no effect on maturation events XREF_BIBR."
DNAJA1 binds KCNH2.
1 |
1 |
biogrid
No evidence text available
DNAJA1 activates KCNH2.
| 1
DNAJA1 activates KCNH2. 1 / 1
| 1
reach
"Furthermore, it is possible that combined manipulation of HSC70, HSP70 and DNAJA1 could enhance their assistance of hERG folding, for at least some of the LQT2 mutants."
CORM-2 affects KCNH2
| 3
CORM-2 inhibits KCNH2. 3 / 3
| 3
reach
"Pretreatment of cells with FeTPPS (1 h at 37degreesC, 25 muM) also prevented the inhibition of hERG by CORM-2 (XREF_FIG)."
reach
"Pretreatment of cells with either antimycin A (XREF_FIG) or myxothiazol (XREF_FIG) -- both applied at 1 muM for 1 h at 37degreesC -- almost fully prevented the inhibition of hERG by CORM-2, which suggests that CO-mediated inhibition of hERG involves mitochondria derived ROS."
reach
"The ability of CORM-2 to inhibit recombinant hERG was blocked by the antioxidant ebselen (100 nM; XREF_FIG), which indicates the likely involvement of reactive oxygen species (ROS)."
BDNF affects KCNH2
| 1 2
BDNF increases the amount of KCNH2.
| 1
BDNF increases the amount of KCNH2. 1 / 1
| 1
reach
"Differentiation of NB cells was accompanied by an increase in herg gene transcription, which attained its maximum after 6 days of treatment with RA and was not further increased by BDNF."
BDNF binds KCNH2.
| 1
BDNF binds COMT, GRM3, and KCNH2. 1 / 1
| 1
sparser
"Cognitive control tasks (designed to challenge executive function of goal-directed behavior in the presence of conflict) have identified abnormal engagement of the anterior cingulate cortex associated with COMT,DRD2, and MAOA; of the dorsolateral prefrontal cortex (DLPFC) associated with DTNBPl,DRD2,MAOA, COMT: and of the parietal cortex associated with DRD2, andMAOA. xref Memory encoding tasks recently identified abnormal engagement of hippocampus parahlppocampus region xref and association of the hippocampus with BDNF, COMT, DISCI, GRM3, and KCNH2."
BDNF activates KCNH2.
| 1
BDNF activates KCNH2. 1 / 1
| 1
reach
"This effect evidently reflected on HERG currents : In fact, RA produced an increase in HERG current density which was strongly potentiated by BDNF."
Akap1 affects KCNH2
| 1 2
Akap1 binds KCNH2.
| 1 1
| 1 1
sparser
"If more than one AKAP could associate with HERG, adrenergic and PKA-mediated modification of channels may differentially occur at various stages of channel synthesis, assembly, trafficking and regulation of I Kr at the surface."
reach
"If more than one AKAP could associate with HERG, adrenergic and PKA mediated modification of channels may differentially occur at various stages of channel synthesis, assembly, trafficking and regulation of I Kr at the surface."
Akap1 phosphorylates KCNH2.
| 1
Akap1 leads to the phosphorylation of KCNH2. 1 / 1
| 1
reach
"Transfection with AKAP-IS, however, resulted in an increase in the amount of back phosphorylation after treatment of cells with CPT-cAMP, indicating that disruption of AKAP and PKA-RII targeting reduced intracellular phosphorylation of HERG."
AP1 affects KCNH2
| 1 2
AP1 inhibits KCNH2.
| 1
AP1 inhibits KCNH2. 1 / 1
| 1
reach
"AP1 Activation Underlies MiR-17-5p Upregulation and H-ERG Trafficking Impairment."
AP1 binds KCNH2.
| 1
AP1 binds ERG and KCNH2. 1 / 1
| 1
sparser
"C is -elements contributing to this inducibility were mapped to the proximal promoter region and these elements were shown to interact with transcription factors Erg-1, Erg-3, ATF-3/CREB and AP-1 upon stimulation ( xref )."
AP1 activates KCNH2.
| 1
AP1 activates KCNH2. 1 / 1
| 1
reach
"Particularly notable is that sequestration of AP1 by its decoy molecule rescued the defective trafficking of h-ERG proteins."
ANK2 affects KCNH2
| 1 2
| 1 2
reach
"ANK2 functionally interacts with KCNH2 aggravating long QT syndrome in a double mutation carrier."
reach
"Our data suggest that ANK2 functionally interacts with KCNH2 leading to a stronger current suppression and marked aggravation of long QT syndrome in the patient carrying variants in both proteins."
sparser
"Our data suggest that ANK2 functionally interacts with KCNH2 leading to a stronger current suppression and marked aggravation of long QT syndrome in the patient carrying variants in both proteins."
ADRB2 affects KCNH2
1 | 1 1
ADRB2 binds KCNH2.
| 1 1
| 1 1
sparser
"These results indicate that potential toxicities in this chemotype, as predicted by hERG and β2-adrenergic receptor interactions, can be addressed by suitable molecular modification."
reach
"These results indicate that potential toxicities in this chemotype, as predicted by hERG and beta2-adrenergic receptor interactions, can be addressed by suitable molecular modification."
ADRB2 activates KCNH2.
1 |
Catalytically active ADRB2 activates KCNH2. 1 / 1
1 |
bel
"Previous studies have revealed that hERG channel activation is modulated by activation of the beta-adrenergic system."
| 1 2
reach
"Heterologous hERG currents were inhibited by EGCG with an IC50 of 6.0 micromol/l in HEK293 cells and an IC50 of 20.5 micromol/l in Xenopus laevis oocytes."
reach
"In X. laevis oocytes EGCG inhibited hERG channels in the open and inactivated states, but not in the closed states."
sparser
"In X. laevis oocytes EGCG inhibited hERG channels in the open and inactivated states, but not in the closed states."
Voltage-gated potassium channel affects KCNH2
| 2
KCNH2 binds voltage-gated potassium channel. 1 / 1
| 1
sparser
"The voltage-gated potassium channel formed by hERG pore-forming alpha subunits generates the IKr cardiac potassium current, and is considered essential for human ventricular repolarization."
KCNH2 binds KCNQ1 and voltage-gated potassium channel. 1 / 1
| 1
sparser
"Both LQT1 and LQT2 are associated with loss of function of voltage-gated potassium channels (I Ks and I Kr ). xref "
Ubiquitin-proteasome affects KCNH2
| 2
Ubiquitin-proteasome inhibits KCNH2.
| 1
Ubiquitin-proteasome inhibits mutated KCNH2. 1 / 1
| 1
reach
"These trafficking deficient hERG mutants are retained in the endoplasmic reticulum due to prolonged association with chaperone proteins calnexin, Hsp70 or Hsp90, and are rapidly degraded by the ubiquitin-proteasome pathway [29-31]."
Ubiquitin-proteasome activates KCNH2.
| 1
Ubiquitin-proteasome activates KCNH2. 1 / 1
| 1
reach
"Sorted by the ER quality control system, the mutant HERG protein is reverse transported from the ER to the cytoplasm where it is degraded by the ubiquitin-proteasome system, resulting in reduced HERG channel currents and impaired repolarization of ventricular action potentials XREF_BIBR."
Toxin BmKKx2 affects KCNH2
| 2
Toxin BmKKx2 inhibits KCNH2.
| 1
Toxin BmKKx2 inhibits KCNH2. 1 / 1
| 1
reach
"HERG channel blockage by toxin BmKKx2 suppressing proliferation and enhancing erythroid differentiation of K562 cells."
Toxin BmKKx2 increases the amount of KCNH2.
| 1
Toxin BmKKx2 increases the amount of KCNH2. 1 / 1
| 1
reach
"These data showed that the blockage of toxin BmKKx2 could relatively suppress the hERG channel expression while enhancing K562 cell differentiation."
Tolterodine affects KCNH2
| 2
| 2
reach
"The IC50 for hERG block (37 degrees C) by tolterodine was 9.6 nM and by terodiline was 375 nM, values near or below clinical concentrations."
reach
"Tolterodine block of HERG displayed a positive voltage dependence, suggesting an interaction with an activated state."
Sunitinib affects KCNH2
| 2
| 2
reach
"This study highlights the complexity of dissecting sunitinib mediated cardiotoxicity from adverse conduction effects, as an extensive electrophysiological analysis of sunitinib mediated inhibition of the sodium and hERG channels and examination of field potential changes were performed."
reach
"In these studies, sunitinib decreased cardiomyocyte viability, inhibited AMPK, increased lipid accumulation, disrupted beat pattern, and blocked hERG activity); in contrast, erlotinib demonstrated only minor changes (increased acetyl-CoA carboxylase (ACC) phosphorylation, the rate limiting step in fatty acid biosynthesis), did not impact ROS, caspase, or lipid levels, and did not affect beat patterns [XREF_BIBR]."
| 2
Sulfanediyl group ubiquitinates KCNH2.
| 1
| 1
sparser
"THIO Induces Ubiquitination and Degradation of hERG."
| 1
sparser
"Therefore, wide variations between studies in observed IC 50 for I hERG inhibition by THIO are difficult to explain purely on the basis of different protocols used."
Stress-activated chaperone Sigma 1 receptor affects KCNH2
| 2
Stress-activated chaperone Sigma 1 receptor binds KCNH2.
| 1
KCNH2 binds stress-activated chaperone Sigma 1 receptor. 1 / 1
| 1
reach
"HERG channel protein maturation, stability, and current density can be enhanced by the stress activated chaperone Sigma 1 receptor, which physically associates with HERG and represents a novel pharmacological target in a membrane signaling channel macrocomplex that is involved in cancer progression."
Stress-activated chaperone Sigma 1 receptor activates KCNH2.
| 1
Stress-activated chaperone Sigma 1 receptor bound to KCNH2 activates KCNH2. 1 / 1
| 1
reach
"HERG channel protein maturation, stability, and current density can be enhanced by the stress activated chaperone Sigma 1 receptor, which physically associates with HERG and represents a novel pharmacological target in a membrane signaling channel macrocomplex that is involved in cancer progression."
| 2
Staurosporine increases the amount of KCNH2.
| 1
Staurosporine increases the amount of KCNH2. 1 / 1
| 1
reach
"Additionally, apoptosis is not necessarily linked to alterations of plasma membrane hERG, because staurosporine, a well-known apoptosis inducer in CHO cells [XREF_BIBR], did not cause a change of surface hERG amount before or after the appearance of externalized annexin-V."
Staurosporine activates KCNH2.
| 1
| 1
reach
"A concentration of 0.5 muM staurosporine did not cause an increase of hERG- or annexin-V related fluorescence at any time."
Solanine affects KCNH2
| 2
Solanine decreases the amount of KCNH2. 2 / 2
| 2
reach
"In the present study, alpha-solanine and trans-chalcone inhibited the expression of the ERG1 and ERG11 genes."
reach
"With respect to the genes involved in ergosterol synthesis, trans-chalcone, alpha-solanine, and terbinafine inhibited the expression of the ERG1 and ERG11 genes."
ShRNA-herg1/1b affects KCNH2
| 2
ShRNA-herg1/1b increases the amount of KCNH2.
| 1
ShRNA-herg1/1b increases the amount of KCNH2. 1 / 1
| 1
reach
"shRNA-herg1 was targeted to inhibit herg1 expression, shRNA-herg1/1b was to inhibit herg1 and herg1b expression, and shRNA-control, the scrambled version of siRNA, was not to affect herg1 or herg1b expression."
ShRNA-herg1/1b decreases the amount of KCNH2.
| 1
ShRNA-herg1/1b decreases the amount of KCNH2. 1 / 1
| 1
reach
"As shown in Fig. 1 A and B, HERG mRNA expression was effectively suppressed by shRNA-herg1 and shRNA-herg1/1b, compared with nontransfected (untreated-control) cells, whereas shRNA-control transfection could not affect the HERG mRNA expression."
Sevoflurane affects KCNH2
| 2
Sevoflurane inhibits KCNH2.
| 1
| 1
reach
"Sevoflurane inhibits HERG (human ether-a-go-go-related gene) currents (I Kr), LQT1 and minK currents (I Ks), and Kv4.3 currents (Ito) [XREF_BIBR, XREF_BIBR], and induces significant QT interval prolongation."
Sevoflurane activates KCNH2.
| 1
| 1
reach
"In conclusion, compared with steady-state currents, sevoflurane was more potent in inhibiting the outward tail currents, suggesting that sevoflurane may modulate the HERG channel kinetics in its inactivated state."
Ropinirole affects KCNH2
| 2
| 2
reach
"Apomorphine and ropinirole blocked hERG channels and prolonged action potential duration over similar concentrations suggesting that these drug interact primarily with the hERG K + channel."
reach
"Stock solutions were prepared fresh daily and diluted into the bath solution containing a final concentration of 0.1% DMSO.The dopamine receptor agonists apomorphine, ropinirole, pergolide and sumanirole were each evaluated for the ability to block hERG K + channels stably expressed in CHO-K1 cells."
Risperidone affects KCNH2
| 2
| 2
reach
"This analysis shows that enhancements of endogenous HF oscillations in HR were also found in beagle dogs with dofetilide and with other hERG blockers such as cisapride, haloperidol, risperidone, DL sotalol, terfenadine and thioridazine."
reach
"Risperidone and paliperidone inhibited the hERG tail currents in a concentration dependent manner with IC 50 values of 0.16 and 0.57 muM, respectively."
| 2
| 2
reach
"In contrast to the K+ conductances described above, terfenadine (3 pM) and astemizole (1 1tM) almost completely abolished HERG channel tail currents."
reach
"potential of 0 mY, 10 pM La3+ reduced HERG current by 92% + 3% (n = 4; Figure 6)."
Pyridine affects KCNH2
| 2
| 2
reach
"The major findings of this study are as follows : 1) hERG1 interacts via its PY motif with the ubiquitin ligase Nedd4-2, 2) this interaction promotes the down-regulation of the functional form of the channel at the plasma membrane through Nedd4-2 ubiquitylation of the channel, and 3) I hERG1 is strongly decreased by Nedd4-2 catalytic dependent activity.The hERG1 PY motif is a highly conserved sequence across animal species lines, highlighting its crucial role in the regulation of the hERG1 channel at the cell surface."
reach
"We investigated whether a mutation in the PY motif of hERG1 could abolish the Nedd4-2 effect on I hERG1."
| 2
reach
"In Xenopus laevis oocytes coexpressed by alpha1-adrenoceptor and HERG channel, PE caused HERG current reduction via protein kinase A (PKA) and C (PKC) [24]."
reach
"Stimulation of alpha (1A)-receptors by applying 20 microM phenylephrine caused hERG current reduction due to a 9.6-mV shift of the activation curve towards more positive potentials."
Perhexiline affects KCNH2
| 1 1
| 1 1
sparser
"In conclusion, perhexiline potently inhibits transfected HERG channels and this is the probable mechanism for QT prolongation and torsades de pointes."
reach
"Perhexiline caused voltage- and frequency dependent block of HERG (IC50 7.8 microM)."
Olanzapine affects KCNH2
| 2
Olanzapine inhibits KCNH2.
| 1
| 1
reach
"For comparison, haloperidol (30 nM) and olanzapine (300 nM) reduced hERG current amplitude by 44.2 +/-3.9% and 49.7 +/-4.2%, respectively."
Olanzapine activates KCNH2.
| 1
| 1
reach
"A fast application of olanzapine induced a reversible inhibition of the hERG tail currents during repolarization in a concentration dependent manner with an IC50 value of 11.9 muM, suggesting an open-channel block."
Nilotinib affects KCNH2
| 2
| 2
reach
"Nilotinib, a second generation Bcr-Abl inhibitor, led to increased ROS generation, caspase activation, hERG block, and an arrhythmic beat pattern."
reach
"However, nilotinib is a potent inhibitor of hERG, a cardiac K + channel whose inhibition increases risk of sudden death."
Nifekalant affects KCNH2
| 2
Nifekalant inhibits KCNH2.
| 1
Nifekalant inhibits KCNH2. 1 / 1
| 1
reach
"Thus, nifekalant inhibits HERG channels in a voltage dependent and frequency dependent manner, and the inhibitory effect may underlie the clinical efficacy of the drug against ventricular tachyarrhythmias."
Nifekalant binds KCNH2.
| 1
KCNH2 binds nifekalant. 1 / 1
| 1
reach
"These findings suggest that nifekalant binds to HERG channels that are in the open state.The magnitude of HERG current inhibition by nifekalant decreased at more depolarizing potentials, where the fraction of the inactivated HERG channels increased."
Nifedipine affects KCNH2
| 2
| 2
reach
"Nifedipine mediated reduction of both HERG and Kv1.5 channels could lead to the suppressions of both I Kr and I to currents in cardiomyocytes."
reach
"In our experiments, verapamil caused high-affinity block of HERG current (IC50 = 143.0 nmol/L), a value close to those reported for verapamil block of L-type Ca2+ channels, whereas diltiazem weakly blocked HERG current (IC50 = 17.3 micromol/L), and nifedipine did not block HERG current."
Muscarinic receptor affects KCNH2
| 2
Muscarinic receptor increases the amount of KCNH2. 2 / 2
| 2
reach
"Using cell biology and electrophysiological methods, we found that the muscarinic receptor agonist carbachol increased the expression and function of hERG, but not ether-a-go-go or Kv1.5 channels stably expressed in human embryonic kidney cells."
reach
"A recent report has revealed that chronic activation of muscarinic receptor increases the mature hERG channel protein expression by slowing protein degradation via PKC pathway [33]."
| 2
Magnesium atom inhibits KCNH2.
| 1
reach
"These results suggest that while intracellular Mg 2+ causes some voltage dependent block of the h-erg channel, Mg ` block may not necessarily account for all of the observed rectification of the instantaneous current."
| 1
Magnesium atom binds KCNH2 and D456. 1 / 1
| 1
reach
"In contrast, Mg 2+ binding to hERG1 was largely determined by D456, with a lesser contribution from D460 and D509."
Lumacaftor affects KCNH2
| 2
| 2
reach
"Having shown that Lumacaftor rescued the hERG trafficking defect in the induced pluripotent stem cell derived cardiomyocytes (iPSC-CMs) of two LQT2 patients, we tested whether the commercial association Lumacaftor + Ivacaftor (LUM + IVA) could shorten the QTc in the same two patients."
reach
"Incubation with E-4031, but not lumacaftor, rescued defective hERG-T634S channel trafficking and I hERG density."
Losartan affects KCNH2
| 2
| 2
reach
"Losartan decreased HERG currents elicited at 0 mV (23.3 +/-4.8%), whereas E3174 increased the current (30.5 +/-6.2%)."
reach
"Furthermore, selective AT 1 receptor blocker losartan attenuates Ether-A-Go-Go Related Gene (HERG) currents (or I Kr), as well as prolongs the duration of APs and affects QT dispersion [XREF_BIBR]."
Lapatinib affects KCNH2
| 2
| 2
reach
"Lapatinib can block the HERG channel in transfected HEK293 cells and prolong the action potential duration [XREF_BIBR], prolonging the QT interval."
reach
"In ion channel studies, lapatinib inhibited the hERG current in a concentration dependent manner, with a half-maximum inhibition concentration (IC (50)) of 0.8 +/- 0.09 microm."
Lanosterol affects KCNH2
| 2
| 2
reach
"Therefore, lanosterol accumulation induced by fluconazole treatment stimulates Doa10 dependent degradation of Erg1."
reach
"High level of lanosterol promotes the degradation of Erg1."
| 2
| 2
reach
"In addition, HERG is not activated by 8-Br-cAMP, consistent with the finding that isoproterenol does not increase IKr in cardiac myocytes (Sanguinetti et al., 1991)."
reach
"Controversially, Chen et al. also demonstrated that isoproterenol administration increased HERG abundance in HEK-293 cells co-transfected with HERG and beta-adrenergic receptor."
Iron atom affects KCNH2
| 2
Iron atom inhibits KCNH2.
| 1
| 1
reach
"In addition, the two iron chelators desferrioxamine (1 mm) and o-phenanthroline (0.2 mm) significantly inhibited hERG1 outward K (+) currents and prevented hERG1 inhibition induced by the ROS scavenging enzyme catalase (1000 units/ml)."
Iron atom activates KCNH2.
| 1
| 1
reach
"These results suggested that histidines in the S 5 -S 6 linker are crucial players in iron dependent ROS production modulating KCNH2 K + channel function."
Iloperidone affects KCNH2
| 2
| 2
reach
"Our results show two interesting new findings : (1) that iloperidone prolongs cardiac repolarization in a reverse rate dependent manner by blocking the HERG current and (2) that a single oral administration of the drug causes significant prolongation of the QTc.Interestingly, its action potential prolonging effect is potentiated by the concomitant use of a well characterized I Ks blocker; chromanol 293B, further illustrating the potentially deleterious effect of combined lesions of the repolarization reserve (I Kr + I Ks blockade)."
reach
"Average reduction of HERG tail current amplitude by iloperidone 100 nmol/L was 31.5 +/- 5.7%."
2 |
Transcriptionally active hsa-miR-133b decreases the amount of KCNH2. 2 / 2
2 |
biopax:mirtarbase
No evidence text available
biopax:mirtarbase
No evidence text available
2 |
Transcriptionally active hsa-miR-133a-3p decreases the amount of KCNH2. 2 / 2
2 |
biopax:mirtarbase
No evidence text available
biopax:mirtarbase
No evidence text available
Hesperetin affects KCNH2
| 2
Hesperetin inhibits KCNH2.
| 1
| 1
reach
"Hesperetin blocked hERG potassium channels in a concentration dependent manner."
Hesperetin activates KCNH2.
| 1
| 1
reach
"Orange flavonoid hesperetin modulates cardiac hERG potassium channel via binding to amino acid F656."
| 1 1
Heat shock protein 70 increases the amount of KCNH2.
| 1
Heat shock protein 70 increases the amount of KCNH2. 1 / 1
| 1
reach
"It has been reported that heat shock protein 70 (Hsp70) increases Kv1.5 and hERG protein expressions by stabilizing the proteins [10,11]."
Heat shock protein 70 binds KCNH2.
| 1
KCNH2 binds heat shock protein 70. 1 / 1
| 1
sparser
"We found that rosuvastatin reduces the interaction of heat shock protein 70 (Hsp70) with the hERG protein, thereby affecting the folding of the hERG channel."
HERG1a-G628S affects KCNH2
| 2
HERG1a-G628S inhibits KCNH2. 2 / 2
| 2
reach
"The non functional hERG1a-G628S and hERG1b-G628S channels co-assembled with wild-type hERG1a and dominantly suppressed hERG1 current."
reach
"HERG1a-G628S and hERG1b-G628S were both shown to decrease hERG1 current by 85% when co-expressed with hERG1a at a 1:1 ratio."
HERG1a USO -G628S affects KCNH2
| 2
HERG1a USO -G628S inhibits KCNH2. 2 / 2
| 2
reach
"In contrast, hERG1a USO -G628S did not readily associate with hERG1a, and consequently, did not suppress hERG1 current when co-expressed at a 1:1 ratio or at ratios that approximate those found in cardiac tissue."
reach
"We performed patch-clamp analysis to test whether hERG1 current was dominantly suppressed by the increased relative expression of hERG1a USO -G628S (XREF_FIG)."
Glucose affects KCNH2
| 2
Glucose inhibits KCNH2.
| 1
| 1
reach
"In addition, we demonstrated that 100 nM insulin up-regulated the expression of the hERG channel and rescued the hERG channel repression caused by high glucose."
Glucose activates KCNH2.
| 1
Glucose activates KCNH2. 1 / 1
| 1
reach
"Reduced serum glucose blocks the repolarizing K (+) channel HERG, which leads to action potential and QT prolongation and is uniformly associated with risk for torsades de pointes ventricular tachycardia."
Fluvoxamine affects KCNH2
| 2
| 2
reach
"Indeed, moxifloxacin (40), fluvoxamine (41), and, recently, doxepin (42) have been reported to inhibit hERG with a mixed state-dependence of inhibition (with components of both closed- and open-channel block, including a very rapid open-channel block)."
reach
"Milnes et al. [XREF_BIBR] reported that fluvoxamine inhibits HERG potassium channels with rapid onset and its inhibition is only partially reduced in F656A mutant channels, which are known to profoundly attenuate the inhibition of HERG channels by many known QT prolonging drugs."
Estradiol affects KCNH2
| 2
Estradiol inhibits KCNH2.
| 1
| 1
reach
"Experiments have previously shown that physiologically relevant application of estradiol increased hERG block by E-4031, whereas testosterone did not."
Estradiol activates KCNH2.
| 1
| 1
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"They were able to show that estradiol treatment strongly induces ERG1 gene in rat uterus and oviduct and that its overexpression is restricted to surface epithelium [XREF_BIBR]."
Equol affects KCNH2
| 2
Equol inhibits KCNH2. 2 / 2
| 2
reach
"Equol at 10 muM significantly inhibited both hERG current and IKs, which implies a potential to cause prolongation of QT interval by increasing ventricular action potential duration, a well-known cardiac toxicity."
reach
"In the present study, we found that equol significantly decreased hERG and IKs."
Efsevin affects KCNH2
| 2
Efsevin inhibits KCNH2. 2 / 2
| 2
reach
"To rule out the possibility that the observed prolongation of APD50 by efsevin in mice could be relevant for human therapy, we showed that efsevin does not influence action potential duration in human iPSC derived cardiomyocytes and does not block hERG activity."
reach
"To rule out that the observed prolongation of APD50 by efsevin in mice is not relevant for human therapy, we showed that efsevin does not influence action potential duration in human iPSC derived cardiomyocytes and does not block hERG."
| 2
| 1
reach
"Meanwhile, disopyramide was demonstrated to block I hERG1 at clinically relevant concentrations (IC 50 < 10 muM), and this action was proposed to constitute the molecular basis of its proarrhythmic effect."
Disopyramide inhibits mutated KCNH2. 1 / 1
| 1
reach
"In vivo effects of mutant HERG K+ channel inhibition by disopyramide in patients with a short QT-1 syndrome : a pilot study."
Dinitrogen affects KCNH2
| 2
Dinitrogen inhibits KCNH2.
| 1
| 1
reach
"XREF_BIBR, XREF_BIBR In pharmacophore models for hERG blockade, it is reported that a basic nitrogen in lipophilic molecules can increase hERG inhibitory potency via pi cation stacking."
Dinitrogen activates KCNH2.
| 1
| 1
reach
"The general transformations in XREF_FIG show some changes in the environment of the amine nitrogen can reduce hERG inhibition."
DTDP affects KCNH2
| 2
DTDP inhibits KCNH2.
| 1
DTDP inhibits KCNH2. 1 / 1
| 1
reach
"However, although most drugs that cause TdP do so via hERG channel blockade, TdP is not necessarily a potential consequence of all drugs blocking the hERG pathway."
DTDP activates KCNH2.
| 1
DTDP activates KCNH2. 1 / 1
| 1
reach
"However, not all drugs that block hERG cause TdP."
Cocaine(1+) affects KCNH2
| 2
| 2
reach
"Cocaine blocked HERG encoded potassium channels with an IC50 of 4.4 +/- 1.1 microM (22 degrees C)."
reach
"Cocaine blocks HERG, but not KvLQT1+ minK, potassium channels."
Clemizole affects KCNH2
| 2
| 2
reach
"Our results provide the first evidence that clemizole potently blocks hERG channels, moderately inhibits cardiac I Ks, delays cardiac repolarization and thereby prolongs QT interval."
reach
"Clemizole decreased hERG current by blocking both open and closed states of the channel in a concentration dependent manner (IC 50 : 0.07 muM)."
Ceftriaxone affects KCNH2
| 2
| 2
reach
"In combination, ceftriaxone and lansoprazole block the hERG channel."
reach
"In the laboratory, we found that, in combination, lansoprazole and ceftriaxone block the hERG channel up to 57.6%, corresponding with an APD70 increase of 50 ms. At these higher lansoprazole concentrations, it is likely that, if treated as a single entity, the combination would not have received regulatory approval."
Cariprazine affects KCNH2
| 2
| 2
reach
"Our results indicated that cariprazine concentration-dependently inhibited hERG 1A and hERG 1A/3.1 currents by preferentially interacting with the open states of the hERG 1A channel, but not by the disruption of hERG 1A and hERG 1A/3.1 channel protein trafficking."
reach
"Cariprazine inhibited the hERG 1A and hERG 1A/3.1 tail currents at -50 mV in a concentration dependent manner with IC 50 values of 4.1 and 12.2 muM, respectively."
Butan-1-ol affects KCNH2
| 2
| 2
reach
"These findings indicate that HERG channels are also greatly blocked by BuOH fraction of L. erythrocarpa while remaining at the holding potential."
reach
"Also, the voltage dependence of the HERG channel blockade by the BuOH (XREF_FIG) and H 2 O fractions (XREF_FIG) indicate that this drug preferentially blocks HERG channels in the closed state rather than either the open or inactivated states."
Brefeldin A affects KCNH2
| 2
Brefeldin A inhibits KCNH2.
| 1
| 1
reach
"In the presence of Brefeldin A (BFA), which was used to block hERG channel trafficking to cell membrane, clenbuterol reduced hERG on plasma membrane to a greater extent than BFA alone."
Brefeldin A activates KCNH2.
| 1
Brefeldin A activates glycosylated KCNH2. 1 / 1
| 1
reach
"One method uses the biochemical approach to follow the loss of the fully glycosylated hERG protein band in cells treated with brefeldin A."
Beta1-integrin affects KCNH2
| 2
KCNH2 binds beta1-integrin. 2 / 2
| 2
reach
"Moreover, plasmalemmal hERG1 and beta1-integrin complexes seem to be specific for tumor cells which -- at least in theory -- increases the possibility to develop tumor specific inhibitors that target hERG1 and beta1-integrin complexes."
reach
"Moreover, plasmalemmal hERG1 and beta1-integrin complexes seem to be specific for tumor cells which -- at least in theory -- increases the possibility to develop tumor specific inhibitors that target hERG1 and beta1-integrin complexes."
Azanide affects KCNH2
| 2
Azanide inhibits KCNH2.
| 1
| 1
reach
"The amide local anaesthetics bupivacaine, levobupivacaine and ropivacaine inhibited HERG channels at toxicologically relevant concentrations, with IC (50) values of 20 (SEM 2) micro M (n = 29), 10 (1) micro M (n = 40) and 20 (2) micro M (n = 49), respectively."
Azanide activates KCNH2.
| 1
Azanide activates KCNH2. 1 / 1
| 1
reach
"Amide local anaesthetics target HERG and HERG and MiRP1 channels with identical potency."
| 2
reach
"Selective noradrenaline reuptake inhibitor atomoxetine directly blocks hERG currents."
reach
"In human embryonic kidney cells, atomoxetine inhibited hERG current with an IC (50) of 6.3 micromol.L (-1)."
Apomorphine affects KCNH2
| 2
| 2
reach
"Stock solutions were prepared fresh daily and diluted into the bath solution containing a final concentration of 0.1% DMSO.The dopamine receptor agonists apomorphine, ropinirole, pergolide and sumanirole were each evaluated for the ability to block hERG K + channels stably expressed in CHO-K1 cells."
reach
"Apomorphine and ropinirole blocked hERG channels and prolonged action potential duration over similar concentrations suggesting that these drug interact primarily with the hERG K + channel."
Anti-Ro52 antibody affects KCNH2
| 2
Anti-Ro52 antibody inhibits KCNH2.
| 1
Anti-Ro52 antibody inhibits KCNH2. 1 / 1
| 1
reach
"Specifically, anti-Ro52 antibody did not acutely block hERG current but chronically facilitated hERG endocytic degradation."
Anti-Ro52 antibody decreases the amount of KCNH2.
| 1
Anti-Ro52 antibody decreases the amount of KCNH2. 1 / 1
| 1
reach
"Our results indicate that anti-Ro52 antibody acts on the hERG S5-pore linker to chronically decrease hERG expression and current."
Amsacrine affects KCNH2
| 2
| 2
reach
"3 Amsacrine blocked HERG currents in HEK 293 cells and Xenopus oocytes in a concentration dependent manner, with IC50 values of 209.4 nm and 2.0 microm, respectively."
reach
"HERG current block by amsacrine was not frequency dependent."
Allitridin affects KCNH2
| 2
Allitridin inhibits KCNH2. 2 / 2
| 2
reach
"Allitridin does not alter the voltage- and time dependent activation of hERG channels, the gating properties of hERG channel inactivation over time or the recovery from inactivation, but allitridin does cause alterations in the steady-state inactivation and the deactivation of hERG channels."
reach
"Other reports show that allitridin impairs the trafficking of hERG channels to reduce the IKr current [XREF_BIBR]."
Alizarin affects KCNH2
| 2
| 2
reach
"Firstly, HC and AZ induce inhibition of cardiac hERG and IKr (rapid IK) potassium channel, inducing mild QT prolongation, with subsequent risk of ventricular arrhythmia and even cardiac arrest, thus needing QT monitoring."
reach
"Firstly, HC and AZ induce inhibition of cardiac hERG and IKr (rapid IK) potassium channel, inducing mild QT prolongation, with subsequent risk of ventricular arrhythmia and even cardiac arrest, thus needing QT monitoring."
Alfuzosin affects KCNH2
| 2
| 2
reach
"Alfuzosin very weakly inhibits hERG current tested in CHO or HEK293 cells stably overexpressing hERG, hence the readout is " safe " using the hERG blockade assay."
reach
"Alfuzosin treatment demonstrated little potential to block hERG (IC 50 = 11.3 +/- 0.7 muM; XREF_FIG, XREF_SUPPLEMENTARY)."
| 2
reach
"In HEK 293 cells expressing HERG channels, AMP 579 (10 microM) significantly blocked the HERG current at +10 mV by 34.9 +/-7.0% (n = 4, p < 0.05), and the degree of inhibition was comparable with that observed in guinea-pig ventricular myocytes (36.8 +/-6.0%, n = 4)."
reach
"AMP activated protein kinase regulates hERG potassium channel."
Aconitine affects KCNH2
| 2
| 2
reach
"Aconitine blocks HERG and Kv1.5 potassium channels."
reach
"A few recent works have suggested that aconitine blocks HERG and Kv1.5 potassium channels, and this compound has a time- and concentration dependent blocking effect on the ultra-rapid delayed rectifier potassium channel (IKur) in H9c2 myogenic cells and in ventricular myocytes of neonatal rats."
| 2
| 2
reach
"Replacement of the phenyl ring with a 4-pyridyl ring system at the 2-amino position improved solubility (830muM) and reduced the hERG liability (IC 50 85muM)."
reach
"The other was the replacement of the phenyl ring with a pyridine ring to improve in vivo potency and reduce hERG affinity."
Wave affects KCNH2
| 2
| 2
sparser
"KCNH2 mutations L413P and L559H are associated with the bifid T waves on ECGs."
sparser
"A mutation in HERG associated with notched T waves in long QT syndrome."
WWP2 affects KCNH2
| 1 1
| 1 1
reach
"Similar to Nedd4-2, WWP2 but not Nedd4-1 was present in the fraction immunoprecipitated with the anti-hERG1 antibody, when expressed with the WT channel, demonstrating that hERG1 can interact both with Nedd4-2 and WWP2."
sparser
"It is also noteworthy that despite the interaction of hERG1 with WWP2, the functional effect of the ligase on I hERG1 is strongly reduced when compared to the effect mediated by Nedd4-2 (data not shown)."
VEGFA affects KCNH2
| 2
| 1
sparser
"A similar approach might be applied to VEGF-A whose high expression is associated with poor prognosis [ xref ]: in fact, we showed that in colorectal [ xref ] and gastric [ xref ] cancers hERG1 expression is significantly associated with VEGF-A expression and the combined therapy with bevacizumab and hERG1 blockers impairs tumor growth in mouse models [ xref ]."
| 1
sparser
"All the proteins were expressed in the samples, with statistically significant associations of VEGF-A with PDGFRβ and Flt1 and hERG1 with CA IX."
Tax affects KCNH2
| 1 1
| 1 1
reach
"To detect interactions between Tax or Tax mutants and ERG1 using the ERG1 antibody, 293T cells were transfected with Tax- or Tax mutants expressing plasmids and pcDNA3.0-ERG1 for 48 h. Immunoprecipitation assay results showed that Tax, but not its mutants, co-precipitated with ERG1, indicating direct Tax binding to ERG1."
sparser
"Immunoprecipitation assay results showed that Tax, but not its mutants, co-precipitated with ERG1 (Figure xref ), indicating direct Tax binding to ERG1."
TOR1 affects KCNH2
| 2
| 2
reach
"The observed synergies between sterol inhibitors are reflected in homozygous synthetic lethalities that are internal to the pathway, and rapamycin 's synergy with terbinafine agrees with the reported interaction between TOR1 and ERG1."
reach
"For example, terbinafine and rapamycin exhibit drug synergy due to a synergistic genetic interaction between their target genes, ERG1 and TOR1 respectively."
TGFB1 affects KCNH2
1 | 1
TGFB1 decreases the amount of KCNH2. 1 / 1
| 1
reach
"Chu et al. demonstrated that TGF-beta1 inhibited the expression of hERG and down-regulated Kir2.1 protein level, thus reducing I Kr and I K1 repolarizing currents 21."
Transcriptionally active TGFB1 decreases the amount of KCNH2. 1 / 1
1 |
biopax:ctd
No evidence text available
TFPI affects KCNH2
| 2
TFPI increases the amount of KCNH2.
| 1
TFPI increases the amount of KCNH2. 1 / 1
| 1
reach
"We found that 3muM EPI obviously increased protein expression and current of HERG channel."
TFPI activates KCNH2.
| 1
TFPI activates KCNH2. 1 / 1
| 1
reach
"In this study, we examined whether EPI could rescue the As 2 O 3 -induced HERG channel deficiency."
TCN1 affects KCNH2
| 2
TCN1 inhibits KCNH2. 2 / 2
| 2
reach
"Firstly, HC and AZ induce inhibition of cardiac hERG and IKr (rapid IK) potassium channel, inducing mild QT prolongation, with subsequent risk of ventricular arrhythmia and even cardiac arrest, thus needing QT monitoring."
reach
"Firstly, HC and AZ induce inhibition of cardiac hERG and IKr (rapid IK) potassium channel, inducing mild QT prolongation, with subsequent risk of ventricular arrhythmia and even cardiac arrest, thus needing QT monitoring."
TBX20 affects KCNH2
| 2
TBX20 increases the amount of KCNH2.
| 1
TBX20 increases the amount of KCNH2. 1 / 1
| 1
reach
"Conversely, p.R311C Tbx20 did not increase KCNH2 expression in hiPSC-CMs, which led to decreased I hERG and increased APD."
TBX20 activates KCNH2.
| 1
TBX20 activates KCNH2. 1 / 1
| 1
reach
"In human induced pluripotent stem cell derived cardiomyocytes (hiPSC-CMs), Tbx20 enhanced human KCNH2 gene expression and hERG currents (I hERG) and shortened action-potential duration (APD)."
TAC1 affects KCNH2
| 1 1
TAC1 binds KCNH2.
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sparser
"We collected evidence to support that bufadienolides such as BF possess NKA inhibition-independent proarrhythmic effects associated with LTCC and hERG blocking."
TAC1 activates KCNH2.
| 1
TAC1 activates KCNH2. 1 / 1
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"We report here that CK decelerated HERG K + channel deactivation, whereas PPT accelerated HERG K + channel deactivation."
SP affects KCNH2
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SP inhibits KCNH2. 2 / 2
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"Both spironolactone (SP) and its main metabolite, canrenoic acid (CA), prolong cardiac action potential duration and decrease the Kv11.1 (HERG) current."
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"SP decreased HERG currents in a concentration dependent manner (IC50 = 23.0 +/-1.5 micromol/L) and shifted the midpoint of the activation curve to more negative potentials (Vh = -13.1 +/-3.4 versus -18.9 +/-3.6 mV, P < 0.05) without modifying the activation and deactivation kinetics."
SLC22A4 affects KCNH2
| 1 2
SLC22A4 inhibits KCNH2.
| 1 1
| 1 1
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"We then tested the hypothesis that coexpression of OCTN1 would potentiate block of the HERG potassium channel."
SLC22A4 activates KCNH2.
| 1
SLC22A4 activates KCNH2. 1 / 1
| 1
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"The Organic Cation Transporter, OCTN1, Expressed in the Human Heart, Potentiates Antagonism of the HERG Potassium Channel."
SH2B2 affects KCNH2
| 2
SH2B2 activates KCNH2. 2 / 2
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"The use in vitro of the action potential (AP) voltage clamp technique showed that the impaired inactivation of N588K hERG channels altered significantly the profile of I hERG during the plateau and repolarisation phases of ventricular APs, leading to increased I hERG occurring much earlier during the ventricular AP waveform XREF_BIBR, XREF_BIBR, XREF_BIBR."
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"Nonetheless, this exercise showed that I KCNQ or I hERG, could contribute to the development of long duration burstings APs in uterine cells."
SGK1 affects KCNH2
| 2
SGK1 activates KCNH2. 2 / 2
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"XREF_BIBR It has been demonstrated that overexpression of SGK1 increased the current and expression level of the membrane localized mature proteins of hERG channels stably expressed in hERG-HEK293 cells."
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"HERG channel activity is up-regulated by the serum- and glucocorticoid inducible kinase isoforms SGK1 and SGK3."
S4-S5 L (0) peptide affects KCNH2
| 2
S4-S5 L (0) peptide activates KCNH2. 2 / 2
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"HERG activation by S4-S5 L (0) peptide is not reinforced by its covalent binding through a disulfide bond."
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"S4-S5 L (0) peptide increased WT hERG current density, but this effect is due to an increased expression of hERG protein, suggesting no effect of S4-S5 L (0) on channel gating."
RXFP2 affects KCNH2
| 2
RXFP2 inhibits KCNH2. 2 / 2
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"Surprisingly, at a very low concentration of 100-fold dilution, green tea Lung Ching or red wine Great Wall inhibited hERG currents by ~ 90%, and significantly shifted the voltage dependent activation to more positive potentials (Figs XREF_FIG and XREF_FIG), which showed very similar pharmacological characteristics with tannic acid."
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"We found that red wine (Great Wall, China) significantly inhibited hERG currents at 1%, and the effect could not be washed out (XREF_FIG)."
RPR260243 affects KCNH2
| 2
RPR260243 activates KCNH2. 2 / 2
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"RPR260243 and ginsenoside Rg3 slow the rate of hERG1 channel deactivation."
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"The first hERG1 activator to be discovered, RPR260243 ((3R,4 R)-4-[3-(6-methoxyquinolin-4-yl)-3-oxo-propyl]-1-[3-(2,3,5-trifluorophenyl)-prop-2-ynyl]-piperidine-3-carboxylic acid) (RPR) induces a pronounced, voltage dependent slowing of hERG1 deactivation."
REC8 affects KCNH2
| 1 1
| 1 1
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"Therefore, we demonstrated the effects of REC8 on gastric cancer cell proliferation and migration, and revealed that REC8 inhibited cell EMT by downregulating EGR1 in gastric cancer via REC8 and ERG1 interactions."
sparser
"Therefore, we demonstrated the effects of REC8 on gastric cancer cell proliferation and migration, and revealed that REC8 inhibited cell EMT by downregulating EGR1 in gastric cancer via REC8 and ERG1 interactions."
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"(Additional file XREF_SUPPLEMENTARY : Table S1) While the removal of some functional groups from cisapride did not significantly reduce the docking scores of compounds at A 2A, their hERG PD bindings were still too high (i.e., Cisapride-D4, Cisapride-D5)."
| 1
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"We took advantage of our previous finding that L646E and F557L mutations nearly abolish the ability of PD and ICA, respectively, to enhance hERG1 currents."
PTKs affects KCNH2
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PTKs activates KCNH2. 2 / 2
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"In the present study we have demonstrated that suppression of PTKs (EGFR kinase and Src family kinases) decreases the current amplitude of hERG channels stably expressed in HEK 293 cells, and negatively shifts the activation V 0.5 of the current."
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"This result suggests that the reduction of hERG current by genistein may be mainly via PTK inhibition.If the genistein effect on I hERG is mediated by PTKs, the action should be reversed or antagonized by the PTP inhibitor orthovanadate [15,17,22]."
PTCH1 affects KCNH2
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PTCH1 inhibits KCNH2.
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PTCH1 inhibits KCNH2. 1 / 1
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sparser
"We then evaluated IPAG and compounds 1 , 4 ,and 5 for hERG binding (performed at Reaction Biology Corporation, Malvern, PA) and hERG functional Patch clamp inhibition (QPatch; performed at Eurofins Panlabs, Inc., St."
PTCH1 binds KCNH2.
| 1
| 1
sparser
"Such cleavage is associated with a complete loss of hERG function as revealed by patch clamp analysis [10] ."
PRKCE affects KCNH2
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PRKCE activates KCNH2. 2 / 2
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"Furthermore, over-expression of PKCepsilon enhanced current densities and promoted protein trafficking of hERG WT -hERG A561V channels."
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"We identified a specific role for the PKCepsilon inhibitory peptidomimmetics in decreasing PKC induced hERG tau activation (80%) and half-maximum activation voltage (90%) at steady state; a specific PKCepsilon activator exhibited the opposite effect."
PPP1 affects KCNH2
| 1 1 1
PPP1 inhibits KCNH2.
| 1 1
PPP1 inhibits KCNH2. 1 / 1
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sparser
"Inhibiting Src action with PP1 or Src40-58 inhibited hERG ( xref – xref ), supporting the hypothesis that de-phosphorylation of one or more tyrosine residues reduce channel activity."
PPP1 activates KCNH2.
| 1
PPP1 activates KCNH2. 1 / 1
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"First, we show that tyrosine kinase inhibitor, PP1, and the selective Src inhibitory peptide, Src40-58, reduce the hERG current amplitude, without altering its voltage dependence or kinetics."
PLX-4720 affects KCNH2
| 1 2
PLX-4720 inhibits KCNH2.
| 1 1
| 1 1
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"Thus, PLX-4720 treatment decreased hERG cell membrane protein abundance in rhabdomyosarcoma RD cells."
PLX-4720 activates KCNH2.
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"No statistically significant difference was observed between hERG tail currents in Xenopus oocytes co-expressing hERG together with B-RAF and treated with 10 microM PLX-4720 and Xenopus oocytes expressing hERG alone."
PLD affects KCNH2
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PLD inhibits KCNH2. 2 / 2
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"The results indicated that a positively charged hERG blocker has a greater chance to induce PLD than a neutral compound, and a neutral or negatively charged PLD inducer is less likely to inhibit hERG function."
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"77.0% of PLD positive compounds also blocked hERG channel; 3."
Olanzapine affects KCNH2
| 2
| 2
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"Olanzapine also decreased the hERG current elicited by a 5s depolarizing pulse to +60 mV to inactivate the hERG currents, suggesting an inhibition of the activated (open and/or inactivated) states of the channels."
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"Olanzapine inhibited hERG tail currents at -50 mV in a concentration dependent manner with an IC50 value of 8.0 muM and a Hill coefficient of 0.9."
NDUFS6 affects KCNH2
1 1 |
1 1 |
hprd
No evidence text available
biogrid
No evidence text available
NAC affects KCNH2
| 2
NAC decreases the amount of KCNH2.
| 1
NAC decreases the amount of KCNH2. 1 / 1
| 1
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"Moreover, NAC reversed the downregulation of hERG expression caused by THIO treatment."
NAC activates KCNH2.
| 1
NAC activates KCNH2. 1 / 1
| 1
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"The ROS scavenger N-acetyl cysteine (NAC) significantly attenuated hERG reduction induced by THIO and abolished the upregulation of ER stress marker proteins."
| 2
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"Maturation of hERG protein in turn is inhibited by preventing the binding of hERG to HSP chaperone complexes, which is again mediated by ROS XREF_BIBR."
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"Heat shock protein (Hsp) 70 is known to promote maturation of hERG."
MicroRNA miR-133 affects KCNH2
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MicroRNA miR-133 decreases the amount of KCNH2. 2 / 2
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"MicroRNA miR-133 represses HERG K+ channel expression contributing to QT prolongation in diabetic hearts."
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"MicroRNA miR-133 represses HERG K+ channel expression contributing to QT prolongation in diabetic hearts."
MiRP2 affects KCNH2
| 2
MiRP2 inhibits KCNH2.
| 1
MiRP2 inhibits KCNH2. 1 / 1
| 1
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"MiRP2 also suppresses hERG currents in Xenopus oocyte expression experiments."
MiRP2 activates KCNH2.
| 1
MiRP2 activates KCNH2. 1 / 1
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"While the expression of MiRP2 in heart tissue suggests a role in cardiac excitability, it is not yet known whether MiRP2 modulates hERG, KCNQ1 or any other channels in vivo in mammalian heart."
MiR-17-5p affects KCNH2
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MiR-17-5p inhibits KCNH2. 2 / 2
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"MiR-17-5p Impairs Trafficking of H-ERG K + Channel Protein by Targeting Multiple ER Stress Related Chaperones during Chronic Oxidative Stress."
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"MiR-17-5p Impairs h-ERG Trafficking."
MAS1 affects KCNH2
| 2
MAS1 inhibits KCNH2. 2 / 2
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"This is consistent with the fact that MAs block hERG1 currents by binding a site different from the one targeted by E4031."
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"MAs can block hERG1 currents in reconstitued cellular models."
LUM affects KCNH2
| 2
LUM activates KCNH2. 2 / 2
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"[XREF_BIBR] The mechanisms by which LUM may rescue hERG trafficking defects are still unknown and these results will require extensive confirmation from clinical data and from other hiPSC lines from more LQT2 donors to verify whether these effects could be cell-line- or mutation specific or whether their mechanism could be exploited for broader applications."
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"We hypothesize that LUM might rescue also hERG trafficking defects in LQT2 and exert anti-arrhythmic effects."
LUF7346 affects KCNH2
| 2
LUF7346 activates KCNH2. 2 / 2
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"In contrast with findings described by others (Matsa etal, 2011), hERG modulation by LUF7346 completely reversed the severe effects of the potassium channel blocker AST in LQT2 N996I hiPSC-CMs, confirming the efficacy of LUF7346 compared to other molecules reported so far in the literature."
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"Collectively, these data suggested that LUF7346 activates the native hERG channels in hiPSC-CMs."
L539fs/47 affects KCNH2
| 2
L539fs/47 inhibits KCNH2-A561V. 1 / 1
| 1
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"These results suggest that ALLN can correct the transport barrier of A561V mutant proteins, and the molecular chaperones may promote the degradation of HERG A561V mutant proteins, but not L539fs/47."
L539fs/47 inhibits KCNH2. 1 / 1
| 1
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"L539fs/47, a truncated mutation of human ether-a-go-go-related gene (hERG), decreases hERG ion channel currents in HEK 293 cells."
KCNH2 affects stress responses
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KCNH2 activates stress responses. 2 / 2
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sparser
"G572R-hERG and E637K-hERG activate ER stress responses via activation of ATF6."
sparser
"Since Calnexin/Calreticulin are chaperone proteins with important regulatory roles in the ER quality control pathways, we want to test whether the trafficking-deficient G572R-hERG and E637K-hERG mutants can activate ER stress responses."
KCNH2 affects stavudine
| 2
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"Consequently, few arrhythmic hERG blockers have been shown to increase beat-to-beat repolarization STV in healthy animals."
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"To quantify repolarization reserve, QT length is not optimal and other techniques have been applied in the scientific community : (1) exaggerated increase in QT after a hERG blocking drug, (2) parameters of temporal repolarization dispersion quantified as temporal QTVI/N and STV, (3) alterations in T wave morphology after the administration of a hERG blocking drug."
KCNH2 affects sensor
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KCNH2 inhibits sensor.
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KCNH2 inhibits sensor. 1 / 1
| 1
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"Gating current studies suggest that a slow component of hERG gating charge, Q on, underlies S4 voltage sensor movement with a time constant of ~ 50 ms at +10 mV which is slightly faster than channel activation, and a V (1/2) that is about 20 mV hyperpolarized compared to the conductance-voltage (G-V) relationship in both WT and S631A inactivation removed channels XREF_BIBR."
KCNH2 activates sensor.
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KCNH2 activates sensor. 1 / 1
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"This observation demonstrates that voltage sensor return is less energetically favorable than pore closure upon repolarization and demonstrates the important role for voltage sensor relaxation is stabilizing the hERG activated voltage sensor and limiting its return."
| 1 1
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"Interestingly, the proposed site of PIP 2 interaction with hErg1 is a cluster of positive charges in the C terminus downstream of the CNBHD in an area that is poorly conserved even within the Erg channel subfamily, and thus it is not clear how PIP 2 might regulate other EAG family channels."
sparser
"Interestingly, the proposed site of PIP 2 interaction with hErg1 is a cluster of positive charges in the C terminus downstream of the CNBHD ( xref ) in an area that is poorly conserved even within the Erg channel subfamily, and thus it is not clear how PIP 2 might regulate other EAG family channels."
| 2
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"In addition, the rate of onset of hERG channel blockade of Moxifloxacin was compared to Dofetilide by whole cell patch clamp technique in HEK-293 cells stably expressing the hERG channels."
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"Compared to PSS, the IC 50 values, conducted at room temperature, of the classic hERG blocking drugs cisapride, moxifloxacin, and terfenadine were shifted to the right by an extent predicted by their known plasma protein binding, but we did not detect any differences in IC 50 s between male and female serum."
KCNH2 affects haloperidol
| 2
KCNH2 inhibits haloperidol.
| 1
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"Although the quantitative characteristics are very close, the three neuroleptics may be placed in the following order of HERG blocking potency : haloperidol> = pimozide> fluspirilene."
| 1
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"Haloperidol binds hERG channels more potently than other cardiac potassium channels, whereas terfenadine also has the potential to block other ion channels XREF_BIBR."
KCNH2 affects hMiRP1
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KCNH2 binds hMiRP1. 2 / 2
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"Like channels with rMiRP1, hMiRP1 and HERG complexes required depolarization to more positive potentials to achieve half-maximal activation and showed no change in slope factor compared to channels formed by HERG subunits alone."
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"Like those with rMiRP1, hMiRP1 and HERG complexes deactivated ~ 3-fold faster than HERG channels."
KCNH2 affects hERG1a
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KCNH2 increases the amount of hERG1a.
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KCNH2 increases the amount of hERG1a. 1 / 1
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"We identified an intrinsically weak, noncanonical poly (A) signal, AGUAAA, within intron 9 of hERG1 that modulates the expression of hERG1a and hERG1a (USO)."
KCNH2 activates hERG1a.
| 1
KCNH2 activates hERG1a. 1 / 1
| 1
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"The co-expression of differentially tagged hERG1 isoforms using the Flp-Cre system allowed us to directly compare the assembly of hERG1a and hERG1a USO to homomeric hERG1a and heteromeric hERG1a and hERGb channels."
KCNH2 affects flecainide
| 1 2
KCNH2 inhibits flecainide.
| 1
| 1
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"However, besides the hERG blocking effect of flecainide, these abnormalities could be also due to reduced intercellular coupling in small cell aggregates due to the sodium channel blocking effect of flecainide."
KCNH2 binds flecainide.
| 1 1
| 1 1
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"In further experiments, the extent to which C-type inactivation might stabilize the binding of flecainide to hERG channels was investigated by washing the drug off during sustained depolarization."
KCNH2 affects effect
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KCNH2 inhibits effect. 2 / 2
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sparser
"In agreement with data obtained from HEK 293 cells, partial (S631A, data not shown) or complete (S620T, xref ) attenuation of inactivation by channel mutagenesis did not abolish the activating potency of KB130015 but slightly reduced its hERG1 inhibiting effect."
sparser
"In contrast, it also has been reported that a H 2 O 2 -dependent increase of hERG1 current activity promoted caspase-3 activation in several cancer cell lines including SKBr3. xref This effect was inhibited by the hERG1 blocker dofetilide. xref "
KCNH2 affects doxazosin
| 2
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"HERG suppression via siRNA mediated knock down mimicked pro apoptotic effects of doxazosin."
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"Suppression of hERG protein expression via siRNA mediated knock down mimicked pro apoptotic effects of doxazosin."
KCNH2 affects disulfur
| 2
Mutated KCNH2 activates disulfur. 1 / 1
| 1
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"This hypothesis is supported by the finding that arrhyth- HERG Mutations Cause Long QT Syndrome 801 S1 S2 $ 3 $ 4 $ 5 Pore $ 6 Extracel [ular Frameshift Intracellular domain Splice error Figure 7."
| 1
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"S2 oscillations were proportionally increased by torsadogenic hERG blocking drugs, whereas smoking caused an increase in S3 oscillations."
KCNH2 affects deoxyelephantopin
| 2
KCNH2 inhibits deoxyelephantopin. 2 / 2
| 2
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"The data presented in this article are related to the research article entitled " The effects of deoxyelephantopin on the cardiac delayed rectifier potassium channel current (I Kr) and human ether-a-go-go-related gene (hERG) expression " (Y.F. Teah, M.A. Abduraman, A. Amanah, M.I. Adenan, S.F. Sulaiman, M.L. Tan) [1], which the possible hERG blocking properties of deoxyelephantopin were investigated."
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"The data presented in this article are related to the research article entitled " The effects of deoxyelephantopin on the cardiac delayed rectifier potassium channel current (I Kr) and human ether-a-go-go-related gene (hERG) expression " (Y.F. Teah, M.A. Abduraman, A. Amanah, M.I. Adenan, S.F. Sulaiman, M.L. Tan) XREF_BIBR, which the possible hERG blocking properties of deoxyelephantopin were investigated."
KCNH2 affects dauA
| 2
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"These findings suggested that Dau binds to HERG channels that are in the inactivated state.In clinical practice, for the treatment of arrhythmias, the usual oral daily dosage range of Dau is 150-900 mg."
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"These results suggest that Dau binds to HERG channels that are in the open state."
KCNH2 affects cisplatin
| 2
| 2
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"Silencing HERG inhibited the apoptosis induced by cisplatin both in vitro and in vivo, by attenuating the cisplatin effects on Bcl-2, Bax and active caspase-3."
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"The role of hERG1 ion channels in epithelial-mesenchymal transition and the capacity of riluzole to reduce cisplatin resistance in colorectal cancer cells."
KCNH2 affects cis-doxepin
| 2
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"Whilst obligatory molecular determinants of doxepin binding to HERG remain to be found, the fact that I HERG inhibition by doxepin developed progressively over several minutes following rapid external solution exchange is consistent with the drug crossing the cell membrane to reach its site of action."
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"Neither the Y652A nor F656A mutations attenuated blockade by doxepin concentrations producing very high levels (> 90%) of blockade of WT I HERG, suggesting that neither residue is absolutely obligatory for doxepin binding to HERG channels to occur."
KCNH2 affects bromide
| 1 1
| 1
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"To further investigate the potential mechanisms for the efficacy of HERG inhibition of domiphen bromide and didecyl dimethylammonium bromide, two QACs, we performed detailed studies to explore the effects of domiphen bromide and didecyl dimethylammonium bromide on the use-dependence, voltage-dependence and state-dependence of HERG channels expressed in Chinese hamster ovary (CHO) cells."
| 1
sparser
"To further investigate the potential mechanisms for the efficacy of HERG inhibition of domiphen bromide and didecyl dimethylammonium bromide, two QACs, we performed detailed studies to explore the effects of domiphen bromide and didecyl dimethylammonium bromide on the use-dependence, voltage-dependence and state-dependence of HERG channels expressed in Chinese hamster ovary (CHO) cells."
KCNH2 affects beta1-integrin
| 2
KCNH2 binds beta1-integrin. 2 / 2
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"Moreover, plasmalemmal hERG1 and beta1-integrin complexes seem to be specific for tumor cells which -- at least in theory -- increases the possibility to develop tumor specific inhibitors that target hERG1 and beta1-integrin complexes."
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"Moreover, plasmalemmal hERG1 and beta1-integrin complexes seem to be specific for tumor cells which -- at least in theory -- increases the possibility to develop tumor specific inhibitors that target hERG1 and beta1-integrin complexes."
KCNH2 affects amiodarone
| 2
KCNH2 inhibits amiodarone.
| 1
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"Milberg et al. [XREF_BIBR] compared the TdP induction ability of two hERG blocking drugs, DL-sotalol and amiodarone."
KCNH2 activates amiodarone.
| 1
| 1
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"Inactivation of the HERG channel at very positive potentials could not prevent amiodarone block."
KCNH2 affects Wave
| 2
| 2
sparser
"KCNH2 mutations L413P and L559H are associated with the bifid T waves on ECGs."
sparser
"A mutation in HERG associated with notched T waves in long QT syndrome."
KCNH2 affects WWP2
| 1 1
| 1 1
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"Similar to Nedd4-2, WWP2 but not Nedd4-1 was present in the fraction immunoprecipitated with the anti-hERG1 antibody, when expressed with the WT channel, demonstrating that hERG1 can interact both with Nedd4-2 and WWP2."
sparser
"It is also noteworthy that despite the interaction of hERG1 with WWP2, the functional effect of the ligase on I hERG1 is strongly reduced when compared to the effect mediated by Nedd4-2 (data not shown)."
KCNH2 affects Tax
| 1 1
| 1 1
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"To detect interactions between Tax or Tax mutants and ERG1 using the ERG1 antibody, 293T cells were transfected with Tax- or Tax mutants expressing plasmids and pcDNA3.0-ERG1 for 48 h. Immunoprecipitation assay results showed that Tax, but not its mutants, co-precipitated with ERG1, indicating direct Tax binding to ERG1."
sparser
"Immunoprecipitation assay results showed that Tax, but not its mutants, co-precipitated with ERG1 (Figure xref ), indicating direct Tax binding to ERG1."
KCNH2 affects TOR1
| 2
| 2
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"The observed synergies between sterol inhibitors are reflected in homozygous synthetic lethalities that are internal to the pathway, and rapamycin 's synergy with terbinafine agrees with the reported interaction between TOR1 and ERG1."
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"For example, terbinafine and rapamycin exhibit drug synergy due to a synergistic genetic interaction between their target genes, ERG1 and TOR1 respectively."
| 2
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"HERG1 has also been shown to enhance GC cell invasion and proliferation, induce cell cycle progression in vitro, and promote tumor genesis and growth in vivo."
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"Notable are hERG1 upregulation in PC, gastric cancer (GC) and CRC, leading to enhanced cancer angiogenesis and invasion, and KCNQ1 down-regulation in CRC, where KCNQ1 expression is associated with enhanced disease-free survival in stage II, III, and IV disease."
KCNH2 affects SQTS
| 2
KCNH2-V141M activates SQTS. 1 / 1
| 1
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"A benign variety of the disease has been observed in children with atrial fibrillation and a KCNH2 V141M mutation, and recently a mutation in the cardiac Cl/HCO 3 exchanger AE3 was found to cause SQTS."
Mutated KCNH2 activates SQTS. 1 / 1
| 1
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"Removal of inactivation by ICA-105574 mimics the gating effects caused by hERG1 mutations that cause SQTS and would therefore be expected to be proarrhythmic at high concentrations."
KCNH2 affects RNF207
1 | 1
1 | 1
biogrid
No evidence text available
reach
"Functional investigation to investigate any interaction between KCNH2 and RNF207 is necessary."
KCNH2 affects REC8
| 1 1
| 1 1
reach
"Therefore, we demonstrated the effects of REC8 on gastric cancer cell proliferation and migration, and revealed that REC8 inhibited cell EMT by downregulating EGR1 in gastric cancer via REC8 and ERG1 interactions."
sparser
"Therefore, we demonstrated the effects of REC8 on gastric cancer cell proliferation and migration, and revealed that REC8 inhibited cell EMT by downregulating EGR1 in gastric cancer via REC8 and ERG1 interactions."
KCNH2 affects RAB11A
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2 |
biogrid
No evidence text available
biogrid
No evidence text available
KCNH2 affects PTPN6
| 2
KCNH2 binds PTPN6.
| 1
| 1
sparser
"Next, we determined that this motif is necessary for the interaction of hERG with SHP-1 tyrosine phosphatase."
KCNH2 activates PTPN6.
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KCNH2 activates PTPN6. 1 / 1
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sparser
"Of note, then, only when tyrosine phosphorylated, the ITIM region of hERG1 activated SHP-1."
KCNH2 affects PRKACA
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2 |
hprd
No evidence text available
hprd
No evidence text available
KCNH2 affects PKC
| 2
| 1
sparser
"The direct interaction of the commonly used protein kinase C (PKC) inhibitor bisindolylmaleimide I (BIM I) with hERG, KvLQT1/minK, and I(Kr) currents was investigated in this study."
PKC binds KCNH2 and NEDD4. 1 / 1
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sparser
"The increase in hERG protein was associated with PKC-induced phosphorylation (inhibition) of Nedd4-2, an E3 ubiquitin ligase that mediates hERG degradation."
KCNH2 affects PAS
| 2
KCNH2 binds PAS.
| 1
| 1
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"Domiphen bromide, benzethonium chloride, and didecyl dimethylammonium bromide may bind to the PAS domain tightly to interrupt the interactions between PAS and HERG, which may further influence the deactivation behavior of the channel."
KCNH2 activates PAS.
| 1
KCNH2 activates PAS. 1 / 1
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"The majority of hERG trafficking studies target LQT2 clinically relevant missense mutations and PAS truncations XREF_BIBR."
KCNH2 affects NS1643
| 2
KCNH2 binds NS1643.
| 1
KCNH2 binds NS1643. 1 / 1
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"There are limited data available about the NS1643 binding to hERG (2,31)."
KCNH2 activates NS1643.
| 1
KCNH2 activates NS1643. 1 / 1
| 1
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"Interestingly, application of the selective hERG1 blocker E4031 in combination with NS1643 rescued the effect of NS1643 alone (XREF_FIG; G0/G1 = 52% +/-4% S = 28% +/-6% G2/M = 5% +/-2%) confirming the specificity of hERG1 channel in determining its agonist dependent inhibition of cell proliferation."
KCNH2 affects NFkappaB
| 1 2
| 1 1
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"Knockdown of hERG1 significantly suppressed cellular proliferation and invasion, and induced apoptosis, while inhibition of hERG1 significantly decreased activation of NF-kappaB."
KCNH2-I593R activates NFkappaB. 1 / 1
| 1
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"Expression of I593R HERG activates the unfolded protein response pathway and, separately, NF-kappaB signaling."
KCNH2 affects NDUFS6
1 1 |
1 1 |
hprd
No evidence text available
biogrid
No evidence text available
KCNH2 affects MYC
| 2
| 1
sparser
"Thus, rMinK and rMiRP1 could each assemble with HERG-cmyc."
KCNE1 binds KCNE2, KCNH2, and MYC. 1 / 1
| 1
sparser
"To compare the binding of MinK and MiRP1 to HERG-cmyc, an assay was performed using 35 S-labeled MinK and MiRP1 subunits synthesized in vitro."
KCNH2 affects Long QT Syndrome type 2
| 2
KCNH2 activates Long QT Syndrome type 2. 2 / 2
| 2
reach
"Rare mutations in KCNH2, a potassium channel involved in myocardial repolarization and drug induced arrhythmias, are known to underlie congenital Long QT Syndrome type 2 and Short QT Syndrome type 1."
reach
"Long QT Syndrome type 2 (LQT2) is caused by mutations in the KCNH2 gene that encodes for the alpha-subunit (hERG) of the ion channel conducting the rapid delayed rectifier potassium current (I Kr)."
KCNH2 affects LQTS Type 2
| 2
KCNH2 activates LQTS Type 2. 2 / 2
| 2
reach
"Using patch clamp to study Na + and Ca 2 + currents, as well as whole-cell current clamp to measure AP, they found that LQTS cells have tendencies toward prolonged AP duration, smaller Na + current density, slower time to inactivation, and increased time to peak.At least three groups have studied LQTS using pluripotent cells from patients with LQTS Type 2, caused by mutations in KCNH2 (hERG channel, responsible for inwardly rectifying potassium current I Kr)."
reach
"At least three groups have studied LQTS using pluripotent cells from patients with LQTS Type 2, caused by mutations in KCNH2 (hERG channel, responsible for inwardly rectifying potassium current I Kr)."
KCNH2 affects LQTS
| 2
KCNH2 activates LQTS. 1 / 1
| 1
reach
"More than 300 different mutations in KCNH2 have been reported to cause LQTS and only a fraction of these have been phenotypically characterized for mechanism or degree of severity in channel defect."
Mutated KCNH2 activates LQTS. 1 / 1
| 1
reach
"The current produced by HERG is not identical to IKr, however, and the mechanism by which HERG mutations cause LQTS remains uncertain."
KCNH2 affects LQT3
| 2
KCNH2 activates LQT3. 2 / 2
| 2
reach
"Among them most common are LQT1, LQT2, and LQT3, caused by mutations in KCNQ1, KCNH2, and SCN5A genes, respectively (Splawski etal."
reach
"LQT1, LQT2, and LQT3 are caused by mutations in KCNQ1 (LQT1), KCNH2 (LQT2), and SCN5A (LQT3), which account for approximately 90% of genotyped LQTS patients."
KCNH2 affects KCNJ2, KCNQ1, and PSMD4
| 2
| 2
sparser
"In addition, AF has been associated with rare gain of function mutations in KCNQ1, hERG and KCNJ2 causing the short QT syndrome and sudden death."
sparser
"This is largely due to reduced L-type Ca 2+ current, although rare gain-of-function mutations in KCNQ1 [ xref ], hERG [ xref ], Kir2.1 [ xref ] and KCNE ancillary subunits [ xref ] have also been associated with AF due to increases in channel conductance."
KCNH2 affects KCNH
| 2
| 2
sparser
"Cysteine mutagenesis of the charged R665, implicated in electrostatic interactions with the S4-S5 linker of a hERG-EAG chimera ( xref ), caused changes that are statistically significant but minor relative to other perturbations in the region."
sparser
"Previous studies have implicated the cNBD and S4-S5 linker as sites of interaction with the EAG domain of hERG ( xref , xref , xref )."
KCNH2 affects IGF1
| 1 1
KCNH2 activates IGF1. 2 / 2
| 1 1
sparser
"However, all three fusion proteins, but neither FLI-1 nor ERG-1 alone, activated the IGF1 promoter and induced IGF1 expression."
reach
"The present results indicate that IGF1, IGFBP3 and IGFBP5 are induced by all of the fusion proteins tested but not by FLI-1 and ERG-1 alone."
KCNH2 affects IC 50
| 2
KCNH2 inhibits IC 50.
| 1
KCNH2 inhibits IC 50. 1 / 1
| 1
reach
"Firstly, I Kr / hERG block aside, most of the IC 50 values from which the drug models were constructed were recorded from non human, mammalian species due to lack of human experimental data."
KCNH2 activates IC 50.
| 1
KCNH2-T618I activates IC 50. 1 / 1
| 1
reach
"In the present study, the T618I hERG mutation elevated the IC 50 for D-sotalol by ~ 3 fold under conventional voltage clamp, which is substantially less than that seen for N588K hERG XREF_BIBR."
KCNH2 affects Histone
| 1 1
KCNH2 binds Histone.
| 1
sparser
"To identify off-target effects we investigated whether sc1o interacts with safety-relevant molecules such as cytochrome P450 (CYP) enzymes, phosphodiesterases (PDE), histone deacteylases (HDAC) and human ether-a-go-go related gene ( h ERG)."
KCNH2 acetylates Histone.
| 1
Modified KCNH2 leads to the acetylation of Histone. 1 / 1
| 1
reach
"In summary, beyond demonstrating for the first time that HERG1A potassium channel subunit is the predominant and disease-relevant isoform associated to head and neck tumour progression and metastatic spread, this study provides novel insights into the underlying regulatory mechanisms of HERG1 expression in HNSCC with original evidence supporting the involvement of histone acetylation."
| 2
sparser
"The interaction between hERG and heat shock protein was evaluated to study the mechanism of trafficking inhibition through Co-Immunoprecipitation."
sparser
"Maturation of hERG protein in turn is inhibited by preventing the binding of hERG to HSP chaperone complexes, which is again mediated by ROS xref ."
KCNH2 affects HTR4
| 2
| 2
sparser
"From the network, we can find that 5-HT4 is interacting with the human ether-a-go-go related gene (HERG), since the two proteins share five compounds with pChEMBL above 6 ( Figure xref )."
sparser
"Several types of analogs were obtained and screened for 5-HT4 binding, hERG blocking, agonism, and gastric emptying assessment."
KCNH2 affects HLA-B
| 2
| 2
sparser
"Eight well-known PKC selective peptidomimmetics and general synthetic modulators were used to modulate the protein-protein interactions between hERG and the major PKC subtypes."
sparser
"Although the molecular mechanisms linking AP to QT prolongation have not been fully elucidated yet, there is evidence pointing to a direct effect on certain subtypes of myocardial ion channels, particularly the human ether-a-go-go-related gene (HERG) that encodes for a protein associated with a cardiac K + channel involved in regulating repolarizing currents [ xref – xref ]."
KCNH2 affects HIF
| 1 1
KCNH2 activates HIF. 2 / 2
| 1 1
sparser
"This signaling pathway has novel features in that the integrin- and hERG1-dependent activation of HIF (i) is triggered in normoxia, especially after CRC cells have experienced a hypoxic stage, (ii) involves NF-kB and (iii) is counteracted by an active p53."
reach
"In other words, when the p53 centered control of cellular apoptosis and shortage of HIF activity was impaired, the ECM and hERG1 dependent stimulation of HIF activity was stronger."
KCNH2 affects HDAC2
| 2
| 2
reach
"HDAC2 binds to several synaptic plasticity related genes- BDNF, Erg1, Creb1, CBP, nrn1, NMDA receptor subunit genes, and fos, as well as genes important for synapse formation."
reach
"XREF_BIBR found that HDAC2 binds to several synaptic plasticity related genes- BDNF, Erg1, Creb1, CBP, nrn1, NMDA receptor subunit genes, and fos, as well as genes important for synapse formation."
KCNH2 affects GOLGA2
| 1 1
| 1 1
sparser
"MiRP1 encoded by KCNE2 is thought to regulate KCNH2 in the human heart; MinK encoded by KCNE1 may also modulate KCNH2 in vivo; 14-3-3ε binding to KCNH2 channels shifts the activation curve towards more hyperpolarized potentials; GM130, a Golgi-associated protein, interacts with KCNH2 as the channel is transported between the endoplasmic reticulum and the plasma membrane [7–10] ."
reach
"MiRP1 encoded by KCNE2 is thought to regulate KCNH2 in the human heart; MinK encoded by KCNE1 may also modulate KCNH2 in vivo; 14-3-3epsilon binding to KCNH2 channels shifts the activation curve towards more hyperpolarized potentials; GM130, a Golgi associated protein, interacts with KCNH2 as the channel is transported between the endoplasmic reticulum and the plasma membrane [7-10]."
KCNH2 affects FlaG
| 2
| 2
sparser
"CHIP overexpression decreased both mature and immature forms of HERG-FLAG proteins in cells treated with GA."
sparser
"Overexpressed Hsp90 also inhibited the binding of endogenous C-terminus of Hsp70-interacting protein (CHIP) to HERG-FLAG proteins."
KCNH2 affects FPDc
| 2
KCNH2 inhibits FPDc. 2 / 2
| 2
reach
"Of note, the similar levels of hERG potassium channel block induced by 2-3 nM dofetilide and 6.9 muM ranolazine (approximately 52%) induced> 200 ms of APDc and FPDc prolongation and multiple arrhythmic events in dofetilide treated cells, but only APDc and FPDc prolongation (< 150 ms) without arrhythmias in ranolazine treated cells."
reach
"FPDc was prolonged by blockade of the hERG channel (E-4031 and dl-sotalol) and KvLQT1 channel (chromanol 293B and HMR1556), and by activation of the sodium channel (veratridine) and calcium channel (Bay K8644)."
| 1 1
| 1
sparser
"Ablation of the neural precursor cell–expressed developmentally down-regulated protein 4 long isoform (Nedd4-2) E3 ligase, which associates with the C-terminal PY motif of hERG ( xref ), failed to counteract the metabolic instability in the presence of glycosides or hERG mutations (Supplemental Figure S5, C and F, and unpublished data)."
KCNH2 activates E3_Ub_ligase.
| 1
| 1
reach
"This suggests that stimulation of hERG1 channel activates an E3 ligase."
KCNH2 affects DNA repair
| 2
| 2
reach
"Combined, the data indicate that hERG1 channels contribute to the stress response and clonogenic survival of irradiated K562 cells but do not promote DNA repair."
reach
"Combined, the data indicate that hERG1 channels contribute to the stress response and clonogenic survival of irradiated K562 cells but do not promote DNA repair."
| 2 2
KCNH2 inhibits Cell Survival.
| 1 1
| 1 1
reach
"It was found that shRNA-herg1 or shRNA-herg1/1b depressed the cellular growth rate, inhibited cell viability and reduced colony formation of SH-SY5Y cells."
KCNH2 activates Cell Survival.
| 1 1
| 1 1
reach
"Compared to control cells treated with the solvent (0.2% DMSO; n = 4; XREF_FIG), hERG siRNA reduced cell viability to 25.4 +/-2.1% (n = 5; p = 0.0008; XREF_FIG), whereas scrambled siRNA (24 h) did not significantly affect cell death (n = 4; p = 0.26; XREF_FIG)."
KCNH2 affects CRC
| 1 1
KCNH2 binds CRC.
| 1
| 1
sparser
"In conclusion, the present study demonstrated that HERG1 expression was notably associated with CRC and was absent in healthy control samples whereas the expression of CEA, CK19 and CK20 varied significantly in tumors and control tissues."
KCNH2 activates CRC.
| 1
KCNH2 activates CRC. 1 / 1
| 1
reach
"Notable are hERG1 upregulation in PC, gastric cancer (GC) and CRC, leading to enhanced cancer angiogenesis and invasion, and KCNQ1 down-regulation in CRC, where KCNQ1 expression is associated with enhanced disease-free survival in stage II, III, and IV disease."
KCNH2 affects CFP
| 2
| 2
sparser
"Furthermore, co-expression of untagged wt hERG-CFP subunits with L69P BBS-hERG-YFP at a 1:1 ratio did not alter L69P mutant trafficking, consistent with the data from whole-cell recordings of the heterozygous condition ( xref ))."
sparser
"Furthermore, co-expression of untagged wt hERG-CFP subunits with L69P BBS-hERG-YFP at a 1:1 ratio did not alter L69P mutant trafficking, consistent with the data from whole-cell recordings of the heterozygous condition ( xref ))."
KCNH2 affects CDKN1A
| 2
KCNH2 increases the amount of CDKN1A. 2 / 2
| 2
reach
"XREF_BIBR, XREF_BIBR However, in our experiments the hERG1 agonist dependent augmentation of p21 protein level occurred only many hours after that cyclin E2 disappeared."
reach
"HERG1 and Kv11.1 activation stimulates transcription of p21 waf and cip in breast cancer cells via a calcineurin dependent mechanism."
KCNH2 affects CDK1
| 2
KCNH2 activates CDK1. 2 / 2
| 2
reach
"Next, we analyzed by immunoblotting potential hERG stimulated signaling pathways in K562 cells by analyzing the activities of the Ca 2+ effector proteins CaMKIIs (Ca 2+ / calmodulin dependent protein kinase II isoforms) and their downstream target cdc2 (cyclin dependent kinase 1, CDK1) (XREF_FIG)."
reach
"Next, we analyzed by immunoblotting potential hERG stimulated signaling pathways in K562 cells by analyzing the activities of the Ca 2+ effector proteins CaMKIIs (Ca 2+ / calmodulin dependent protein kinase II isoforms) and their downstream target cdc2 (cyclin dependent kinase 1, CDK1) (XREF_FIG)."
KCNH2 affects CDH5
| 2
KCNH2 increases the amount of CDH5.
| 1
KCNH2 increases the amount of CDH5. 1 / 1
| 1
reach
"130 In a subsequent study, it was demonstrated that ERG1 directly induced the expression of CDH5 (vascular endothelial cadherin; cadherin 5, type 2) in HUVECs, 131 suggesting that ERG1 regulates endothelial cell-cell interaction possibly through formation of adherens junctions."
KCNH2 activates CDH5.
| 1
KCNH2 activates CDH5. 1 / 1
| 1
reach
"DHH and SFRP4 were both induced by wt fusion proteins but not by the DBDM, whereas PODXL, KRT119 and CDH5 were induced both by FLI-1 and ERG-1 alone and by the EWS-FLI-1 DBDM."
KCNH2 affects CDC73
1 1 |
1 1 |
biogrid
No evidence text available
hprd
No evidence text available
KCNH2 affects CD59
| 2
KCNH2 increases the amount of CD59. 2 / 2
| 2
reach
"HERG1 and Kv11.1 activation stimulates transcription of p21 waf and cip in breast cancer cells via a calcineurin dependent mechanism."
reach
"Stimulation of hERG1 and Kv11.1 channel activity increases p21 waf and cip protein level in molecularly diverse breast cancer cells."
KCNH2 affects CD31
| 2
KCNH2 increases the amount of CD31. 2 / 2
| 2
reach
"Moreover, as initial screening demonstrated that ERG1 accelerates the expression of CD31 compared to ERG2, we focused on ERG1 to drive ACs into mature iVECs."
reach
"ERG1 synergizes with FLI1 to enhance and sustain CD31 expression in maturing iVECs (XREF_FIG and XREF_FIG)."
KCNH2 affects CASP3
| 1 1
KCNH2 binds CASP3.
| 1
VEGF binds CASP3 and KCNH2. 1 / 1
| 1
sparser
"However, these results are still tentative and imperfect, and the question how hERG mRNA or hERG protein physiologically interacts with VEGF or caspase-3 is unanswered."
KCNH2 activates CASP3.
| 1
KCNH2 activates CASP3. 1 / 1
| 1
reach
"XREF_BIBR, XREF_BIBR In contrast, it also has been reported that a H 2 O 2 -dependent increase of hERG1 current activity promoted caspase-3 activation in several cancer cell lines including SKBr3."
KCNH2 affects Akap1
| 1 1
| 1 1
sparser
"If more than one AKAP could associate with HERG, adrenergic and PKA-mediated modification of channels may differentially occur at various stages of channel synthesis, assembly, trafficking and regulation of I Kr at the surface."
reach
"If more than one AKAP could associate with HERG, adrenergic and PKA mediated modification of channels may differentially occur at various stages of channel synthesis, assembly, trafficking and regulation of I Kr at the surface."
KCNH2 affects AZA-2
| 2
KCNH2 inhibits AZA-2. 2 / 2
| 2
reach
"The effects of AZA-2 on rat electrocardiogram (ECG) and cardiac biomarkers were evaluated for cardiotoxicity signs besides corroborating the hERG blocking activity of AZA-2."
reach
"Our results indicate that the hERG blocking activity of AZA-2 does not translate into in vivo QT prolongation in rats."
KCNH2 affects ALG10B
1 1 |
1 1 |
biogrid
No evidence text available
hprd
No evidence text available
KCNH2 affects ADRB2
| 1 1
| 1 1
sparser
"These results indicate that potential toxicities in this chemotype, as predicted by hERG and β2-adrenergic receptor interactions, can be addressed by suitable molecular modification."
reach
"These results indicate that potential toxicities in this chemotype, as predicted by hERG and beta2-adrenergic receptor interactions, can be addressed by suitable molecular modification."
| 1 2
| 1 1
reach
"Elevation of cAMP can modulate HERG K+ channels both by direct binding and indirect regulation through protein kinase A. To assess the physiological significance of cAMP binding to HERG, we introduced mutations to disrupt the cyclic nucleotide binding domain."
KCNH2 activates 3',5'-cyclic AMP.
| 1
reach
"We show that HERG associates with 14-3-3epsilon to potentiate cAMP and PKA effects upon HERG."
KCNH affects KCNH2
| 2
| 2
sparser
"Cysteine mutagenesis of the charged R665, implicated in electrostatic interactions with the S4-S5 linker of a hERG-EAG chimera ( xref ), caused changes that are statistically significant but minor relative to other perturbations in the region."
sparser
"Previous studies have implicated the cNBD and S4-S5 linker as sites of interaction with the EAG domain of hERG ( xref , xref , xref )."
KCNE3L affects KCNH2
| 2
KCNE3L inhibits KCNH2. 2 / 2
| 2
reach
"KCNE3L inhibits hERG; KCNE4L inhibits Kv1.1; neither affects HCN1."
reach
"As previously reported for short isoforms KCNE3S and KCNE4S, KCNE3L inhibited hERG; KCNE4L inhibited Kv1.1; neither form regulated the HCN1 pacemaker channel."
KCB-328 affects KCNH2
| 2
KCB-328 inhibits KCNH2. 2 / 2
| 2
reach
"After a 300-second resting period, HERG current inhibited by KCB-328 was recovered more at depolarized membrane potentials than at hyperpolarized ones, with a time constant of 179.9 seconds during the rest at -60 mV."
reach
"The decrease became more pronounced at more positive potential, suggesting that the block of HERG by KCB-328 is voltage dependent."
Ile-Ala affects KCNH2
| 2
| 2
reach
"Class Ia anti-arrhythmic drug ajmaline blocks HERG potassium channels : mode of action."
reach
"XREF_BIBR Quinidine, a class IA antiarrhythmic drug, blocks hERG channel, which is influenced by Tyr652 residue."
IK affects KCNH2
| 1 1
IK inhibits KCNH2.
| 1
IK inhibits KCNH2. 1 / 1
| 1
reach
"Red wine inhibited the hERG currents and induces a rightward shift of the activation curve."
IK binds KCNH2.
| 1
| 1
sparser
"The discovery that HERG forms the IK, channel provides a logical explanation for the obser- vation that block of IKr by certain drugs can provoke the same arrhythmia (torsades de pointe) as that observed in familial LQT."
Histone affects KCNH2
| 1 1
Histone increases the amount of KCNH2.
| 1
Histone phosphorylated on S10 increases the amount of KCNH2. 1 / 1
| 1
reach
"This favors Ser10 phosphorylation and Lys14 acetylation of histone 3 at the Erg-1 gene promoter, leading to relaxed chromatin compaction, changes in DNA methylation, and Erg-1 expression."
Histone binds KCNH2.
| 1
sparser
"To identify off-target effects we investigated whether sc1o interacts with safety-relevant molecules such as cytochrome P450 (CYP) enzymes, phosphodiesterases (PDE), histone deacteylases (HDAC) and human ether-a-go-go related gene ( h ERG)."
| 2
sparser
"The interaction between hERG and heat shock protein was evaluated to study the mechanism of trafficking inhibition through Co-Immunoprecipitation."
sparser
"Maturation of hERG protein in turn is inhibited by preventing the binding of hERG to HSP chaperone complexes, which is again mediated by ROS xref ."
HSP90 affects HSPA, and KCNH2
| 2
HSP90 binds HSPA and KCNH2. 2 / 2
| 2
sparser
"Mutations such as R752W and G601S strengthen the interaction of hERG with Hsp70 and Hsp90."
sparser
"It could be that hypoxia inhibits Hsp90 binding to hERG by reducing steady state expression levels of endogenous Hsp90 and/or Hsp70."
HPD affects KCNH2
| 2
HPD inhibits KCNH2.
| 1
HPD inhibits KCNH2. 1 / 1
| 1
reach
"PPD itself had no effect on HERG K + channel activity but antagonized Rg 3 -mediated HERG K + channel regulations."
HPD activates KCNH2.
| 1
HPD activates KCNH2. 1 / 1
| 1
reach
"PPD itself had no effects on deactivating-tail currents, whereas PPD inhibited ginsenoside Rg 3 -induced persistent I deactivating-tail and accelerated HERG K + channel deactivation in a concentration dependent manner."
HLA-B affects KCNH2
| 2
| 2
sparser
"Eight well-known PKC selective peptidomimmetics and general synthetic modulators were used to modulate the protein-protein interactions between hERG and the major PKC subtypes."
sparser
"Although the molecular mechanisms linking AP to QT prolongation have not been fully elucidated yet, there is evidence pointing to a direct effect on certain subtypes of myocardial ion channels, particularly the human ether-a-go-go-related gene (HERG) that encodes for a protein associated with a cardiac K + channel involved in regulating repolarizing currents [ xref – xref ]."
HDAC6 affects KCNH2
| 2
HDAC6 ubiquitinates KCNH2.
| 1
Modified HDAC6 leads to the ubiquitination of KCNH2. 1 / 1
| 1
reach
"Coexpression of HDAC6 decreased acetylation and, reciprocally, increased ubiquitination of hERG, resulting in its decreased expression."
HDAC6 deacetylates KCNH2.
| 1
HDAC6 leads to the deacetylation of KCNH2. 1 / 1
| 1
reach
"HDAC6 inhibition induced acetylation of hERG which counteracted ubiquitination leading its stabilization."
HDAC2 affects KCNH2
| 2
| 2
reach
"HDAC2 binds to several synaptic plasticity related genes- BDNF, Erg1, Creb1, CBP, nrn1, NMDA receptor subunit genes, and fos, as well as genes important for synapse formation."
reach
"XREF_BIBR found that HDAC2 binds to several synaptic plasticity related genes- BDNF, Erg1, Creb1, CBP, nrn1, NMDA receptor subunit genes, and fos, as well as genes important for synapse formation."
GLUL affects KCNH2
| 2
GLUL activates KCNH2. 2 / 2
| 2
reach
"During a cardiac action potential, GS increased the outward HERG current."
reach
"Crude saponins of Korean red ginseng (GS) induced a minimal increase of the maximal HERG conductance without changes in the voltage dependent HERG current activation and inactivation curves."
FlaG affects KCNH2
| 2
| 2
sparser
"CHIP overexpression decreased both mature and immature forms of HERG-FLAG proteins in cells treated with GA."
sparser
"Overexpressed Hsp90 also inhibited the binding of endogenous C-terminus of Hsp70-interacting protein (CHIP) to HERG-FLAG proteins."
ErgTx1 affects KCNH2
| 1 1
ErgTx1 inhibits KCNH2.
| 1
ErgTx1 inhibits KCNH2. 1 / 1
| 1
sparser
"ErgTx1 inhibit human and rat ERG1 in a similar manner (IC 50 4–7 nM), however, it was unable to affect human ERG2 current while completely blocked the rat ERG2 channel with poor recuperation (~IC 50 1 nM)."
ErgTx1 activates KCNH2.
| 1
ErgTx1 activates KCNH2. 1 / 1
| 1
reach
"Both BeKm-1 and ErgTx1 can suppress the HERG current in a concentration dependent and reversible manner."
ERG affects KCNH2
| 2
| 1
sparser
"Proliferation of arterial smooth muscle cells was associated with a marked increase in ERG1 expression and ERG blockers suppressed proliferation significantly."
AP1 binds ERG and KCNH2. 1 / 1
| 1
sparser
"C is -elements contributing to this inducibility were mapped to the proximal promoter region and these elements were shown to interact with transcription factors Erg-1, Erg-3, ATF-3/CREB and AP-1 upon stimulation ( xref )."
EPHA3 affects KCNH2
| 2
EPHA3 activates KCNH2. 2 / 2
| 2
reach
"We validate our microfluidics array platform in polystyrene (PS), cyclo-olefin polymer (COP) and poly (dimethylsiloxane) (PDMS) microchannels for drug induced disruption of hERG trafficking by culturing stably transfected HEK cells that overexpressed hERG (WT-hERG), and studying their morphology, proliferation rates, hERG protein expression, and response to drug treatment."
reach
"They validate their microfluidics array platform in polystyrene (PS), cyclo-olefin polymer (COP), and polydimethylsiloxane (PDMS) microchannels for drug induced disruption of hERG trafficking by culturing stably transfected HEK cells that overexpressed hERG (WT-hERG) and studying their morphology, proliferation rates, hERG protein expression, and response to drug treatment."
DNAJA2 affects KCNH2
| 2
DNAJA2 inhibits KCNH2. 1 / 1
| 1
reach
"Our observations are thus similar to those described by Walker and colleagues, who reported that DnaJA1, DnaJA2 and DnaJA4 reduced hERG channel maturation, whereas over-expression of Hsc70 alone had no effect on maturation events XREF_BIBR."
Mutated DNAJA2 inhibits KCNH2. 1 / 1
| 1
reach
"Folding-inactive DNAJA2 mutants were also unable to promote hERG degradation, suggesting that DNAJA2 dependent folding and degradation are in fact closely related mechanistically."
DDT affects KCNH2
| 1 1
DDT inhibits KCNH2. 2 / 2
| 1 1
reach
"Results with DDT in the current study suggest that hERG channel inhibition by DDT (IC 50 values of 22.2 muM in the thallium influx assay and 2.6 muM in the patch clamp assay) may be a factor in DDT associated cardiac arrhythmias."
sparser
"Results with DDT in the current study suggest that hERG channel inhibition by DDT (IC 50 values of 22.2 μM in the thallium influx assay and 2.6 μM in the patch clamp assay) may be a factor in DDT-associated cardiac arrhythmias."
| 1 1
reach
"Carvedilol (nonselective), propranolol (nonselective) and ICI 118551 (beta (2)-selective) inhibited HERG current in a concentration dependent manner (IC (50) 0.51, 3.9 and 9.2 microM, respectively)."
sparser
"Inhibition of HERG current by carvedilol, propranolol and ICI 118551 was partially but significantly attenuated in Y652A and F656C mutant channels."
CYP51A1 affects KCNH2
| 2
CYP51A1 increases the amount of KCNH2. 2 / 2
| 2
reach
"Inhibition of later steps in the ergosterol-biosynthetic pathway by ketoconazole, an inhibitor of the lanosterol-14alpha-demethylase, and U18666A, an inhibitor of the squalene-2,3-epoxide-lanosterol cyclase, also induce expression of ERG1, suggesting that ERG1 expression is positively regulated by diminished intracellular ergosterol levels."
reach
"Inhibition of a later step in the ergosterol biosynthetic pathway by ketoconazol, an inhibitor of the lanosterol-14alpha-demethylase (encoded by ERG11), also induces the expression of ERG1, indicating that ERG1 expression is positively regulated by diminished intracellular ergosterol levels."
CTR1p repressible promoters affects KCNH2
| 2
CTR1p repressible promoters decreases the amount of KCNH2. 2 / 2
| 2
reach
"AFT1p and CTR1p repressible promoters were also characterized and employed to downregulate the expression of ERG1, which also enhanced the production of squalene in FSE strain up to 42.85- (148.67 mg/L) and 73.49-fold (255.11 mg/L) respectively."
reach
"AFT1p and CTR1p repressible promoters were also characterized and employed to downregulate the expression of ERG1, which also enhanced the production of squalene in FSE strain up to 42.85- (148.67 mg/L) and 73.49-fold (255.11 mg/L) respectively."
CLOCK affects KCNH2
| 2
CLOCK activates KCNH2. 2 / 2
| 2
reach
"Furthermore, we investigated whether heterologous expression of BMAL1 and CLOCK could enhance the transcriptional activity of the cloned human Kcnh2 promoter."
reach
"Together the data suggest that the circadian expression of Kcnh2 is conserved, and BMAL1 and CLOCK can enhance the transcriptional activity of the human KCNH2 promoter."
CHMP3 affects KCNH2
| 2
CHMP3 inhibits KCNH2. 2 / 2
| 2
reach
"Consistently, overexpression of the endosomal deubiquitinating enzyme signal transducing adaptor molecule binding protein significantly accelerated whereas knockdown of endogenous signal transducing adaptor molecule binding protein impeded degradation of the mature hERG channels under low K (+) conditions."
reach
"Overexpression of Vps24 protein, also known as charged multivesicular body protein 3, significantly accelerated degradation of mature hERG channels, whereas knockdown of Vps24 impeded this process."
CFP affects KCNH2
| 2
| 2
sparser
"Furthermore, co-expression of untagged wt hERG-CFP subunits with L69P BBS-hERG-YFP at a 1:1 ratio did not alter L69P mutant trafficking, consistent with the data from whole-cell recordings of the heterozygous condition ( xref ))."
sparser
"Furthermore, co-expression of untagged wt hERG-CFP subunits with L69P BBS-hERG-YFP at a 1:1 ratio did not alter L69P mutant trafficking, consistent with the data from whole-cell recordings of the heterozygous condition ( xref ))."
CDC73 affects KCNH2
1 1 |
1 1 |
biogrid
No evidence text available
hprd
No evidence text available
BST2 affects KCNH2
| 2
BST2 inhibits KCNH2. 2 / 2
| 2
sparser
"To test for such a scenario, the population of K562 cells with degraded DNA (subG 1 population) was determined in dependence on hERG1 inhibition (0 or 1 µM E4031) by flow cytometry (propidium iodide Nicoletti staining) 24 h after irradiation with 0 or 5 Gy ( xref )."
sparser
"To test for such a scenario, the population of K562 cells with degraded DNA (subG 1 population) was determined in dependence on hERG1 inhibition (0 or 1 µM E4031) by flow cytometry (propidium iodide Nicoletti staining) 24 h after irradiation with 0 or 5 Gy ( xref )."
BRL-32872 affects KCNH2
| 2
BRL-32872 inhibits KCNH2. 2 / 2
| 2
reach
"Using the two-microelectrode voltage clamp technique, we found that BRL-32872 caused a high-affinity, state dependent block of open HERG channels (IC (50) = 241 nM) in a frequency dependent manner with slow unbinding kinetics."
reach
"BRL-32872 inhibited HERG currents in HEK 293 cells in a dose dependent manner, with an IC (50) value of 19.8 nM."
Ala-Pro affects KCNH2
| 2
Ala-Pro inhibits KCNH2.
| 1
| 1
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"Prolongation of AP correlates with potency to block hERG."
Ala-Pro activates KCNH2.
| 1
Ala-Pro activates KCNH2. 1 / 1
| 1
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"In this regard, the longer plateau phase of the AP in hiPSC-CMs compared to hESC-CMs would allow a higher number of HERG channels to inactivate, resulting in a different contribution of I Kr to AP repolarization."
AZD7009 affects KCNH2
| 2
AZD7009 inhibits KCNH2. 2 / 2
| 2
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"AZD7009 inhibited the hERG current with an IC50 of 0.6 +/- 0.07 microM (n = 6)."
reach
"AZD7009 has previously been shown to inhibit hERG and hNav1.5 currents."
ARNTL affects KCNH2
| 2
ARNTL activates KCNH2. 2 / 2
| 2
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"Furthermore, we investigated whether heterologous expression of BMAL1 and CLOCK could enhance the transcriptional activity of the cloned human Kcnh2 promoter."
reach
"Together the data suggest that the circadian expression of Kcnh2 is conserved, and BMAL1 and CLOCK can enhance the transcriptional activity of the human KCNH2 promoter."
APETx2 affects KCNH2
| 2
APETx2 activates KCNH2. 2 / 2
| 2
reach
"We show that APETx2 also inhibits the off-target hERG channel by reducing the maximal current amplitude and shifting the voltage dependence of activation to more positive potentials."
reach
"The structural characteristics of APETx2 are compared with that of PcTx1, another effector of ASIC channels but specific to the ASIC1a subtype and to APETx1, a toxin structurally related to APETx2, which targets the HERG potassium channel."
ALG10 affects KCNH2
1 | 1
ALG10 binds KCNH2.
1 |
1 |
hprd
No evidence text available
ALG10 activates KCNH2.
| 1
ALG10 activates KCNH2. 1 / 1
| 1
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"KCR1 and the yeast alpha-1,2-glucosyltransferase ALG10 exhibit sequence homology, and like KCR1, ALG10 diminished HERG block by dofetilide."
AG556 affects KCNH2
| 2
AG556 inhibits KCNH2.
| 1
AG556 inhibits KCNH2. 1 / 1
| 1
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"A Src family kinase inhibitor (PP2) and an EGFR kinase inhibitor (AG556) modulated hERG XREF_BIBR, but only the EGFR inhibitor regulated hEAG1 XREF_BIBR."
AG556 decreases the amount of KCNH2.
| 1
AG556 decreases the amount of KCNH2. 1 / 1
| 1
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"The reduction of hERG channel phosphorylation level by genistein, AG556 or PP2 was antagonized by orthovanadate."
AFT1p affects KCNH2
| 2
AFT1p decreases the amount of KCNH2. 2 / 2
| 2
reach
"AFT1p and CTR1p repressible promoters were also characterized and employed to downregulate the expression of ERG1, which also enhanced the production of squalene in FSE strain up to 42.85- (148.67 mg/L) and 73.49-fold (255.11 mg/L) respectively."
reach
"AFT1p and CTR1p repressible promoters were also characterized and employed to downregulate the expression of ERG1, which also enhanced the production of squalene in FSE strain up to 42.85- (148.67 mg/L) and 73.49-fold (255.11 mg/L) respectively."
| 1 1
reach
"In addition, HERG is not activated by 8-Br-cAMP, consistent with the finding that isoproterenol does not increase IKr in cardiac myocytes (Sanguinetti et al., 1991)."
sparser
"In addition, HERG is not activated by 8-Br-cAMP, consistent with the finding that isoproterenol does not increase IKr in cardiac myocytes (Sanguinetti et al., 1991)."
| 2
2-(4-hydroxyphenyl)ethanol increases the amount of KCNH2.
| 1
2-(4-hydroxyphenyl)ethanol increases the amount of KCNH2. 1 / 1
| 1
reach
"We found that growth in the presence of added tyrosol reduced the tri gene expression and increased erg1 gene expression, directing the pool of FPP towards biosynthesis of ergosterol, a primary metabolite, instead of towards the synthesis of secondary metabolites like trichothecenes, thus avoiding the repressing effect exerted by farnesol."
2-(4-hydroxyphenyl)ethanol decreases the amount of KCNH2.
| 1
2-(4-hydroxyphenyl)ethanol decreases the amount of KCNH2. 1 / 1
| 1
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"We found that growth in the presence of added tyrosol reduced the tri gene expression and increased erg1 gene expression, directing the pool of FPP towards biosynthesis of ergosterol, a primary metabolite, instead of towards the synthesis of secondary metabolites like trichothecenes, thus avoiding the repressing effect exerted by farnesol."
| 2
| 1
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"For example, 17beta-oestradiol inhibits I Ks [XREF_BIBR] and I Kr [XREF_BIBR] channels and enhances the effect of a KCNH2 blocker [XREF_BIBR]."
| 1
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"Similar to female predominance of arrhythmia in the acquired setting, which suggests interactions between hERG, dofetilide and oestradiol, the female predominance of inherited arrhythmia linked the the G604S mutations, suggests that oestradiol may differentially interact with the mutant hERG channel compared to WT."
| 2
| 1
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"The amide local anaesthetics bupivacaine, levobupivacaine and ropivacaine inhibited HERG channels at toxicologically relevant concentrations, with IC (50) values of 20 (SEM 2) micro M (n = 29), 10 (1) micro M (n = 40) and 20 (2) micro M (n = 49), respectively."
(S)-ropivacaine activates KCNH2.
| 1
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"Levobupivacaine, ropivacaine and bupivacaine accelerated HERG inactivation kinetics, slowed the recovery from inactivation and shifted the inactivation curve towards more negative membrane potentials."
| 2
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"Ginsenoside Rg3, a natural product isolated from ginseng root also dramatically slows hERG1 deactivation rate, but it also causes a modest negative shift in the voltage dependence of activation 75."
| 1
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"RPR260243 and ginsenoside Rg3 slow the rate of hERG1 channel deactivation."
~3 affects KCNH2
| 1
~3 activates KCNH2-T618I. 1 / 1
| 1
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"In the present study, the T618I hERG mutation elevated the IC 50 for D-sotalol by ~ 3 fold under conventional voltage clamp, which is substantially less than that seen for N588K hERG XREF_BIBR."
{Omega}-3 and {omega}-6 affects KCNH2
| 1
{Omega}-3 and {omega}-6 inhibits KCNH2. 1 / 1
| 1
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"{Omega} -3 and {omega} -6 polyunsaturated fatty acids block HERG channels."
YpkA affects KCNH2
| 1
YpkA activates KCNH2. 1 / 1
| 1
reach
"Protein kinase A and protein kinase C modulate cardiac hERG channels and/or I Kr [6,7]."
XMiRP2 affects KCNH2
| 1
XMiRP2 inhibits KCNH2. 1 / 1
| 1
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"The RNA interference mediated reduction of endogenous xMiRP2 expression increased macroscopic HERG current as much as 10-fold depending on HERG cRNA concentration."
Wine affects KCNH2
| 1
Wine inhibits KCNH2. 1 / 1
| 1
sparser
"Red wine inhibits hERG channels with pharmacological characteristics similar to tannic acid and teas."
Wild-type BeKm-1 affects KCNH2
| 1
Wild-type BeKm-1 inhibits KCNH2. 1 / 1
| 1
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"In electrophysiological patch-clamp recordings mono-[127I]-BeKm-1 had a concentration of half-maximal inhibition (IC50 value) of 27 nM, while wild-type BeKm-1 inhibited hERG channels with an IC50 value of 7 nM."
Wild-type B-RAF affects KCNH2
| 1
Wild-type B-RAF activates KCNH2. 1 / 1
| 1
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"Co-expression of wild-type B-RAF increased hERG channel protein abundance in the cell membrane and thus increased the respective hERG mediated current across the cell membrane in Xenopus oocytes."
Vasopressin affects KCNH2
| 1
Vasopressin increases the amount of KCNH2. 1 / 1
| 1
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"These findings demonstrated that vasopressin up-regulated the expression of c-Fos and Erg-1 via transactivation of two distinct EGF receptor dependent signalling pathways."
| 1
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"High expression of PU.1 antagonizes key regulators of other developmental pathways, such as GATA-1, GATA-2 and C/EBPalpha [XREF_BIBR - XREF_BIBR] and activates myeloid specific factors such as Interferon regulatory factor-8 (IRF8), Kruppel like Factor 4 (KLF-4) and Erg1 [XREF_BIBR - XREF_BIBR]."
Ubiquitin ligase Doa10 affects KCNH2
| 1
Ubiquitin ligase Doa10 inhibits KCNH2. 1 / 1
| 1
reach
"We show that the yeast ubiquitin ligase Doa10, along with the other components of the Doa10 complex, promotes the regulated degradation of the squalene monooxygenase Erg1."
Twi affects KCNH2
| 1
| 1
sparser
"In LQT2 patients (n = 16) occurrence of CE (n = 6) was also associated with a lower TWI (7.8±15.4 vs. 43.3±23.4 mV*ms, p = 0.007), a significantly lower QRSTI (29.5±23.8 vs. 83.3±34.6 mV*ms, p = 0.006) and a significantly lower T-wave amplitude in this particular area (0.08±0.04 vs. 0.2±0.14 mV, p = 0.03)."
| 1
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"This synergy occurs because TSA prevents up-regulation of the genes that code for the targets of azoles involved in ergosterol synthesis (ERG1 and ERG11) [123]."
| 1
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"In this study, protriptyline is shown to be another TCA that blocks the HERG channel with the IC 50 of 1.18 muM."
Telmisartan affects KCNH2
| 1
| 1
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"Telmisartan preferentially blocked open-state HERG channels."
Taxifolin glycoside affects KCNH2
| 1
Taxifolin glycoside inhibits KCNH2. 1 / 1
| 1
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"These results suggest that taxifolin glycoside blocks hERG K + channels that function by facilitating activation and inactivation process."
| 1
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"In human embryonic kidney 293 cells, however, only supratherapeutic tacrolimus concentrations (> 0.1 mumol/l) inhibited hERG K (+) current with a maximum inhibition of 28% at 10 mumol/l, indicating that other mechanisms might have also operated besides direct block of ionic channel function."
TKvLQT1 affects KCNH2
| 1
TKvLQT1 decreases the amount of KCNH2. 1 / 1
| 1
reach
"On the other hand, tKvLQT1 did not suppress the expression of Kv1.4, Kv4.3, or hERG."
T-AUCB affects KCNH2
| 1
T-AUCB increases the amount of KCNH2. 1 / 1
| 1
reach
"T-AUCB upregulated KCNQ1 and KCNH2 mRNA expression dose-dependently."
Synthetic BeKm-1 toxin affects KCNH2
| 1
Synthetic BeKm-1 toxin inhibits KCNH2. 1 / 1
| 1
reach
"We conclude that synthetic BeKm-1 toxin blocks HERG preferentially through a closed (resting) state channel blockade mechanism, although some open channel blockade also occurs."
Sw affects KCNH2
| 1
| 1
sparser
"KCNH2 was significantly associated with SW modulation."
Sustained protein kinase A affects KCNH2
| 1
Sustained protein kinase A activates KCNH2. 1 / 1
| 1
reach
"Previous work showed that sustained protein kinase A (PKA) activity augments HERG protein abundance by a mechanism that includes enhanced protein translation."
Sulpiride affects KCNH2
| 1
| 1
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"Sulpiride dose-dependently decreased the hERG tail current."
| 1
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"Both spironolactone (SP) and its main metabolite, canrenoic acid (CA), prolong cardiac action potential duration and decrease the Kv11.1 (HERG) current."
Small molecule activator ICA-105574 affects KCNH2
| 1
Small molecule activator ICA-105574 activates KCNH2. 1 / 1
| 1
reach
"Towards a structural view of hERG activation by the small molecule activator ICA-105574."
| 1
sparser
"Pharmacological K v 11.1 blockade (dofetilide) in rats had similar effect, and small interfering RNA inhibition of hERG in β and L cells increased insulin and GLP-1 secretion up to 50%."
Simvastatin affects KCNH2
| 1
| 1
reach
"Simvastatin and atorvastatin reduce hERG current by accelerating channel inactivation."
Similar model developed rabbit heart affects KCNH2
| 1
Similar model developed rabbit heart inhibits KCNH2. 1 / 1
| 1
eidos
"A similar model , developed in the rabbit heart , exhibits electrical remodeling with prolonged QT interval , spontaneous torsades des pointes ( TdP ) in 75 % of bradypaced rabbits , reduced I Ks and I Kr , and downregulated KvLQT1 , minK and HERG [ 12 ] ."
Sigma-1 receptors affects KCNH2
| 1
KCNH2 binds sigma-1 receptors. 1 / 1
| 1
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"The distribution of angles between pairs of sigma-1 receptors bound to hERG tetramers had two peaks, at ~ 90 and ~ 180degrees in a ratio of ~ 2:1, indicating that the sigma-1 receptor interacts with hERG with 4-fold symmetry."
Sigma affects KCNH2
| 1
Sigma inhibits KCNH2. 1 / 1
| 1
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"We show herein that sigma ligands inhibit hERG current density and cell adhesion to fibronectin in K562 myeloid leukemia cells."
Sertraline affects KCNH2
| 1
| 1
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"As demonstrated in XREF_FIG, sertraline concentration-dependently inhibited hERG channel currents."
Scorpion toxin peptides affects KCNH2
| 1
Scorpion toxin peptides inhibits KCNH2. 1 / 1
| 1
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"Compared to other HERG blockers (i.e. small molecules and drugs), the two known scorpion toxin peptides that potently block HERG are unusual in that they are thought to act from the extracellular side of the membrane."
Scorpion toxin BeKm-1 affects KCNH2
| 1
Scorpion toxin BeKm-1 activates KCNH2. 1 / 1
| 1
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"The scorpion toxin BeKm-1, which is known to selectively bind to the S5-pore linker of hERG, prevented hypoxia induced hERG reduction."
Saxagliptin affects KCNH2
| 1
| 1
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"Taken together, saxagliptin and 5-hydroxy saxagliptin had little effect on hERG and IKr currents and on Purkinje-fiber action potentials at concentrations up to 30microM (< = 9.5 microg/mL), suggesting that it is unlikely that either saxagliptin or 5-hydroxy saxagliptin would cause hERG- and IKr-mediated electrocardiographic effects at maximal plasma concentrations associated with the highest recommended saxagliptin therapeutic dose of 5mg [saxagliptin (0.024 mug/mL) and 5-hydroxy saxagliptin (0.047 mug/mL)] in humans."
SEHi t-AUCB affects KCNH2
| 1
SEHi t-AUCB increases the amount of KCNH2. 1 / 1
| 1
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"More important, we further demonstrated that sEHi t-AUCB could restore the expression of KCNQ1 and KCNH2 mRNA, which were repressed by the agonist miR-133 agomir."
SEHI t-AUCB affects KCNH2
| 1
SEHI t-AUCB activates KCNH2. 1 / 1
| 1
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"In conclusion, the sEHI t-AUCB increases KCNQ1 and KCNH2 mRNA and protein by suppressing miR-133 under ischemic arrhythmia conditions."
Ruboxistaurin affects KCNH2
| 1
Ruboxistaurin inhibits KCNH2. 1 / 1
| 1
reach
"Further in vitro experiments indicated that ruboxistaurin is able to block the hERG channel (human ether-a-go-go related gene) with an IC 50 of 35.6 nM, altering the repolarization of the myocardium and potentially contributing to the observed QTc prolongation [XREF_BIBR]."
Rpr affects KCNH2
| 1
Rpr activates KCNH2. 1 / 1
| 1
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"The first hERG1 activator to be discovered, RPR260243 ((3R,4 R)-4-[3-(6-methoxyquinolin-4-yl)-3-oxo-propyl]-1-[3-(2,3,5-trifluorophenyl)-prop-2-ynyl]-piperidine-3-carboxylic acid) (RPR) induces a pronounced, voltage dependent slowing of hERG1 deactivation."
Romidepsin affects KCNH2
| 1
| 1
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"At 10mug/mL, romidepsin was shown to inhibit the hERG related current by 37%."
Ritonavir affects KCNH2
| 1
| 1
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"Drug induced QT prolongation is usually caused by block of human ether-a-go-go-related gene (HERG) potassium channels, and we showed that lopinavir, nelfinavir, ritonavir, and saquinavir caused dose dependent block of HERG channels heterologously expressed in HEK293 cells in vitro."
RhoGAP affects KCNH2
| 1
RhoGAP increases the amount of KCNH2. 1 / 1
| 1
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"These data link a rhoGAP activated PLC pathway to HERG membrane expression and implicate this family of proteins as candidate genes in disorders involving HERG."
Relevant MMV665917 affects KCNH2
| 1
Relevant MMV665917 inhibits KCNH2. 1 / 1
| 1
eidos
"Although no toxicity in animals has been observed , in vitro patch clamp studies demonstrated partial inhibition of the human ether-a-go-go ( hERG ) potassium channel by physiologically relevant concentrations of MMV665917 , which indicates the possibility of cardiac toxicity ."
Related toxin APETx3 affects KCNH2
| 1
Related toxin APETx3 inhibits KCNH2. 1 / 1
| 1
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"The related toxin APETx3, which only differs from APETx1 by one amino acid and shows an 86% amino acid identity to APETx4, is also not able to inhibit the hERG current at concentrations up to 50 microM [XREF_BIBR]."
Recombinant BmKKx2 affects KCNH2
| 1
Recombinant BmKKx2 inhibits KCNH2. 1 / 1
| 1
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"The concentration dependent experiments further indicated the recombinant BmKKx2 could block hERG channel with an IC 50 of 6.7 +/-1.7 nM (XREF_FIG)."
RMiRP1 affects KCNH2
| 1
KCNH2 binds rMiRP1. 1 / 1
| 1
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"However, under these in vitro conditions, the presence of both peptides favored formation of stable rMiRP1 and HERG complexes in preference to those with rMinK.Based on the presumed molecular correlation of MiRP1 and HERG channel complexes and native cardiac I Kr channels, we cloned the gene for human MiRP1 (hKCNE2) to screen for the presence of mutations in patients with cardiac arrhythmias."
RMiRP affects KCNH2
| 1
KCNH2 binds rMiRP. 1 / 1
| 1
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"Subunit interaction between rMiRP and HERG was evaluated first by studying the proteins modified with epitope tags and expressed in mammalian tissue culture cells."
REag1 mutants affects KCNH2
| 1
REag1 mutants activates KCNH2. 1 / 1
| 1
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"Accordingly, in 3 mM KCl bath solution, the inactivating rEag1 mutants failed to produce hERG1 like hooked inward tail currents, a feature that was also observed in previously reported Eag1 chimeras containing hERG1 sequences in the pore-S6 region XREF_BIBR, XREF_BIBR."
REag1 eag domain affects KCNH2
| 1
REag1 eag domain activates KCNH2. 1 / 1
| 1
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"The presence of the rEag1 eag domain, nevertheless, did not abrogate the prominent inward tail currents in the reverse hERG1 chimeras (XREF_FIG; XREF_SUPPLEMENTARY)."
REag1 affects KCNH2
| 1
REag1 activates KCNH2. 1 / 1
| 1
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"Despite the presence of hERG1 like I-V relationship, neither of the rEag1 chimeras produced hERG1 like inward tail currents."
RBeKm-1 affects KCNH2
| 1
RBeKm-1 inhibits KCNH2. 1 / 1
| 1
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"Dose response relationship characterizations of verapamil and rBeKm-1 blockage of hERG currents provided IC (50) values similar to values reported in the literature."
Quetiapine affects KCNH2
| 1
| 1
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"Quetiapine and norquetiapine inhibited the hERG tail currents at -50 mV in a concentration dependent manner with IC 50 values of 8.3 and 10.8 muM, respectively, which suggested equal potency."
Ptk affects KCNH2
| 1
Ptk phosphorylates KCNH2 on tyrosine. 1 / 1
| 1
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"These results indicate that the membrane protein of hERG channels is phosphorylated by EGFR kinase and Src tyrosine kinases.The potential PTK phosphorylation sites were predicted with the software NetPhos 2.0 (www.cbs.dtu.dk/cgi-bin)."
Protein kinase C inhibitor affects KCNH2
| 1 1
Protein kinase C inhibitor activates KCNH2. 1 / 1
| 1 1
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"Direct block of hERG potassium channels by the protein kinase C inhibitor bisindolylmaleimide I (GF109203X)."
Proteasome inhibitor affects KCNH2
| 1
Proteasome inhibitor inhibits KCNH2. 1 / 1
| 1
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"MG132 (proteasome inhibitor) and bafilomycin (lysosome inhibitor) increased 135kDa hERG, which suggests that immature hERG undergoes both proteasome- and lysosome mediated degradation (XREF_FIG)."
| 1
| 1
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"H (1) antihistamine drug promethazine directly blocks hERG K (+) channel."
Prazosin affects KCNH2
| 1
| 1
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"In conclusion, this study demonstrates that HERG potassium channels are blocked by prazosin, doxazosin, and terazosin."
Ponatinib affects KCNH2
| 1
| 1
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"71 The exception seems to be ponatinib, which inhibited hERG at concentrations above 1muM, substantially in excess of the steady-state maximal concentrations observed in patients treated at the clinical dose of 45mg."
Polymorphism affects KCNH2
| 1
KCNH2 binds polymorphism. 1 / 1
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sparser
"Our studies demonstrate a primary LQT-3 (Na + channel) defect not influenced by the KCNH2 polymorphism and drug interactions unique to the proband that correlate with improved management of arrhythmias in the patient and provide support for this approach in developing patient-specific clinical regimens."
| 1
rlimsp
"Activation of cAMP-dependent protein kinase (PKA) causes phosphorylation of HERG accompanied by a rapid reduction in current amplitude, acceleration of voltage-dependent deactivation, and depolarizing shift in voltage-dependent activation."
Piperazine affects KCNH2
| 1
| 1
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"XREF_BIBR, XREF_BIBR Replacement of the N-methylpiperazine moiety in 6 with a morpholine ring (compound 10a) was beneficial in reducing affinity for hERG, consistent with our hypothesis that hERG affinity is driven by the presence of a piperazine basic center."
| 1
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"We conclude that PI (4,5) P 2 modulates hERG channels very modestly if at all and is not essential for hERG channel function."
| 1
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"Only one compound, trixylenyl phosphate, did not inhibit hERG channel activity in the patch clamp experiment; the potency (IC 50 of 16 muM) of this compound was relatively low in the thallium influx assay and, therefore, trixylenyl phosphate may have weak and inconsistent activity across these assays."
| 1
| 1
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"Thioridazine, perphenazine, trifluoperazine, and chlorpromazine blocked hERG potassium channels with the following IC (50) values : IC (50) values were 224 +/- 42 nM for thioridazine, 1003 +/- 71 nM for perphenazine, 1406 +/- 124 nM for trifluoperazine, and 1561 +/- 281 nM for chloropromazine."
Pergolide affects KCNH2
| 1
| 1
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"Stock solutions were prepared fresh daily and diluted into the bath solution containing a final concentration of 0.1% DMSO.The dopamine receptor agonists apomorphine, ropinirole, pergolide and sumanirole were each evaluated for the ability to block hERG K + channels stably expressed in CHO-K1 cells."
| 1
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"Pentobarbital induced HERG inhibition was not dependent on voltage but influenced the deactivation kinetics and shifted half-maximal activation to more negative voltages."
PAF-AGL-0185-30 affects KCNH2
| 1
PAF-AGL-0185-30 inhibits KCNH2. 1 / 1
| 1
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"Furthermore, we established in vitro that pAF-AGL-0185-30 does not significantly inhibit hERG or cytochrome P450 family enzymes (CYPs)."
| 1
| 1
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"Anticholinergic antiparkinson drug orphenadrine inhibits HERG channels : block attenuation by mutations of the pore residues Y652 or F656."
| 1
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"Nortriptyline dose-dependently blocked hERG current, with a tail IC (50) value of 2.20 +/- 0.09 muM (n = 4)."
Norfloxacin affects KCNH2
| 1
| 1
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"Sparfloxacin blocked HERG currents half-maximally (IC (50) value) at a concentration of 33.2 microM, whereas norfloxacin and lomefloxacin each tested at a concentration of 300 microM inhibited HERG currents only by 2.8 +/-3.6% and 12.3 +/-4.7%, respectively."
| 1
| 1
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"HERG channels (I Kr) are reportedly inhibited by NO in a cGMP independent manner when expressed in X. laevis oocytes, although S nitrosylation was not directly evaluated 63."
Nicorandil affects KCNH2
| 1
| 1
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"Preliminary results indicate that the hERG blocker E-4031 can stimulate irregular, arrhythmic beating patterns in the cardiomyocytes from both species, and that immediate subsequent treatment with the hERG enhancer nicorandil can rescue these back to regular beating patterns, similar to those observed when the cells were untreated."
Nickel(2+) affects KCNH2
| 1
| 1
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"Overall, these data suggest NI networks can modulate the activity of sensory, emotional and executive brain areas involved in social recognition, with a likely involvement of neuronal Egr-1 activation in amygdala, septum and hypothalamus, and Erg-1 inhibition in hippocampus."
Nelfinavir affects KCNH2
| 1
| 1
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"Drug induced QT prolongation is usually caused by block of human ether-a-go-go-related gene (HERG) potassium channels, and we showed that lopinavir, nelfinavir, ritonavir, and saquinavir caused dose dependent block of HERG channels heterologously expressed in HEK293 cells in vitro."
Nearby affects KCNH2
| 1
Mutated nearby inhibits KCNH2. 1 / 1
| 1
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"A modulatory effect of the T618I mutation on I hERG inactivation is not entirely unexpected, given that mutation of the nearby S620 residue (to S620T) has been established to abolish hERG channel inactivation, although in contrast to the S620T mutation it is clear that the T618I mutation produces a more modest, partial attenuation of I hERG inactivation."
Naloxone affects KCNH2
| 1
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"When hERG tail currents upon -50 mV repolarization following a 50 mV depolarization were analyzed, fentanyl and naloxone blocked hERG current (I hERG) with an IC 50 of 0.9 muM and 74.3 muM, respectively, while norfentanyl did not block."
NM toxin BmKKx2 affects KCNH2
| 1
NM toxin BmKKx2 inhibits KCNH2-S631A. 1 / 1
| 1
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"As shown in Figure XREF_FIG P, mutant hERG S631A channel currents could be inhibited by 100 nM toxin BmKKx2, and its IC 50 of toxin BmKKx2 was 698 +/-64.4 nM, making hERG-S631A approximately 104-fold less sensitive to BmKKx2 than wild-type hERG channel."
Myricetin affects KCNH2
| 1
| 1
reach
"It should be noted, however, that myricetin did not inhibit hERG1 channels, and luteolin was not examined XREF_BIBR."
Mutation affects KCNH2
| 1
Mutation-Y652A inhibits KCNH2. 1 / 1
| 1
reach
"As shown in XREF_FIG, the pore mutation Y652A abolished hERG1 activation by 50 muM KB130015 at negative voltages, but the channels were blocked in an almost voltage independent manner to 63 +/- 4% (n = 9)."
Multidrug resistance gene affects KCNH2
| 1
Multidrug resistance gene inhibits KCNH2. 1 / 1
| 1
reach
"In additional experiments, we also show that hERG blockade in HEK 293 cells was modulated by coexpression of efflux [breast cancer resistance protein (BCRP), multidrug resistance gene (MDR1)] and influx [organic anion transporting polypeptide (OATP) 2B1] transporters involved in the disposition and cardiac distribution of the drug."
MuM A-935142 affects KCNH2
| 1
MuM A-935142 activates KCNH2. 1 / 1
| 1
reach
"In whole-cell voltage clamp studies we found : 1) 60 muM A-935142 enhanced hERG current in the presence of 150 muM sotalol (57.5 +/-5.8%) to a similar extent as seen with A-935142 alone (55.6 +/-5.1%); 2) 150 muM sotalol blocked hERG current in the presence of 60 muM A-935142 (43.5 +/-1.5%) to a similar extent as that seen with sotalol alone (42.0 +/-3.2%) and 3) during co-application, hERG current enhancement was followed by current blockade."
Mu mol/L diC8-PIP 2 affects KCNH2
| 1
Mu mol/L diC8-PIP 2 activates KCNH2. 1 / 1
| 1
reach
"We observed that hERG was only weakly activated by addition of up to 100 mu mol/L diC8-PIP 2 on the cytosolic face of the membrane."
Morpholine affects KCNH2
| 1
| 1
reach
"Synergy with geldanamycin was also observed between the allylamine terbinafine (FIC 90 = 0.25), which targets Erg1, and the morpholine fenpropimorph (FIC 90 = 0.016), which targets Erg24 and Erg2 (XREF_FIG)."
Monoubiquitin affects KCNH2
| 1
Monoubiquitin inhibits KCNH2. 1 / 1
| 1
reach
"Thus, monoubiquitin dynamically mediates endocytic degradation of mature hERG channels under low K (+) conditions."
Mitochondrial dehydrogenase affects KCNH2
| 1
Mitochondrial dehydrogenase inhibits KCNH2. 1 / 1
| 1
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"Furthermore, AZAs increased mitochondrial dehydrogenase activity was almost totally suppressed in the K + -, Cl - -, and Na + -free media and sensitive to the specific inhibitors of K ATP and hERG potassium channels, Na + / K +, ATPase, and cystic fibrosis transmembrane conductance regulator (CFTR) chloride channels."
MiR-96 inhibitor affects KCNH2
| 1
MiR-96 inhibitor increases the amount of KCNH2. 1 / 1
| 1
reach
"The miR-96 inhibitor also significantly decreased HERG1 expression compared with SC."
MiR-362-3p affects KCNH2
| 1
MiR-362-3p activates KCNH2. 1 / 1
| 1
reach
"MiR-362-3p mediates the transcriptional regulation of hERG and is associated with survival in breast cancer."
MiR-17-5p inhibitor affects KCNH2
| 1
MiR-17-5p inhibitor activates KCNH2. 1 / 1
| 1
reach
"Application miR-17-5p inhibitor rescued H 2 O 2 -induced impairment of h-ERG trafficking."
MiR-133b affects KCNH2
| 1
MiR-133b inhibits KCNH2. 1 / 1
| 1
reach
"This evidence suggests that miR-133b might increase arsenic induced apoptosis in U251 glioma cells by targeting the hERG."
| 1
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"Both domperidone and metoclopramide concentration-dependently blocked HERG currents, and the following values were calculated for IC (50) (the concentrations causing half-maximal inhibition) and n (the Hill coefficient) : 57.0 nmol/l and 0.99 for domperidone, 5.4 micromol/l and 0.95 for metoclopramide."
Methylamine affects KCNH2
| 1
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"32 In fact replacing the methanesulfonamide with a methyl group enhances hERG block by almost 10-fold."
Methyl affects KCNH2
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Methyl inhibits KCNH2. 1 / 1
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"17 The methyl analogues 9-11 show weak inhibition of hERG (IC 50 = 2-5 muM), which can be rationalized by their inherent structural features : a basic center with pendant aromatic and lipophilic moieties."
Methanol affects KCNH2
| 1
| 1
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"Considering that K + channel has relatively high selectivity for the permeating ion, K + rather than Na +, Ca 2+, and Cl -, the MeOH extract at relatively high concentrations of 100 and 300 microg/mL, could perturb the ion-selectivity of HERG channel by inducing non specific membrane permeabilization or membrane leakage."
| 1
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"Due to the possibility that these small organic counterions contributed to the inhibition produced by pergolide and sumanirole, sodium methanesulfonate and maleic acid were tested for the ability to inhibit hERG mediated currents."
Metabolite affects KCNH2
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"Characterization of recombinant hERG K(+) channel inhibition by the active metabolite of amiodarone desethyl-amiodarone."
| 1
| 1
reach
"Mesoridazine blocked HERG currents in a concentration dependent manner (IC50 550 nM at 0 mV); block increased significantly over the voltage range where HERG activates and saturated at voltages eliciting maximal HERG channel activation."
Mercury(2+) affects KCNH2
| 1
| 1
sparser
"Mercury (10 microM) inhibited the K+-channels ROMK and HERG, the phosphate transporter NaPi-3, the amino acid transporter rBAT, the cation transporter OCT-2, and the osmolyte transporter BGT."
Maleic acid affects KCNH2
| 1
| 1
reach
"Due to the possibility that these small organic counterions contributed to the inhibition produced by pergolide and sumanirole, sodium methanesulfonate and maleic acid were tested for the ability to inhibit hERG mediated currents."
| 1
| 1
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"Modulation of HERG potassium channels by extracellular magnesium and quinidine."
MIDH1 inhibitors affects KCNH2
| 1
MIDH1 inhibitors activates KCNH2. 1 / 1
| 1
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"In vitro predictive toxicity assays were also utilized to determine if mIDH1 inhibitors may cause cytotoxicity in human hepatoyctes or inhibit hERG channels 48."
Lopinavir affects KCNH2
| 1
| 1
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"Drug induced QT prolongation is usually caused by block of human ether-a-go-go-related gene (HERG) potassium channels, and we showed that lopinavir, nelfinavir, ritonavir, and saquinavir caused dose dependent block of HERG channels heterologously expressed in HEK293 cells in vitro."
| 1
| 1
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"Sparfloxacin blocked HERG currents half-maximally (IC (50) value) at a concentration of 33.2 microM, whereas norfloxacin and lomefloxacin each tested at a concentration of 300 microM inhibited HERG currents only by 2.8 +/-3.6% and 12.3 +/-4.7%, respectively."
| 1
| 1
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"Levofloxacin inhibits the hERG K + channel, with an IC 50 of 915 microM8 and is not thought to affect other cardiac ion channels."
| 1
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"The amide local anaesthetics bupivacaine, levobupivacaine and ropivacaine inhibited HERG channels at toxicologically relevant concentrations, with IC (50) values of 20 (SEM 2) micro M (n = 29), 10 (1) micro M (n = 40) and 20 (2) micro M (n = 49), respectively."
| 1
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"However, other troubling side effects have led to substitution of other anti-epileptic drugs such as levetiracetam, which does not block hERG channels."
Lead(2+) affects KCNH2
| 1
| 1
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"We found that Pb (2+) obviously inhibits the current of the hERG K (+) channel, and delays the " activation " and " deactivation " of the hERG K (+) channel, indicating that Pb (2+) evidently decreases the function of the K (+) channel in the cell."
Lavendustin A affects KCNH2
| 1
Lavendustin A leads to the dephosphorylation of KCNH2 on tyrosine. 1 / 1
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"The constitutive tyrosine phosphorylation of the ERG1 protein, detected by co-immunoprecipitation, was reduced by the protein-tyrosine kinase inhibitors, lavendustin A, herbimycin A, or genistein (but not daidzein)."
Lamotrigine affects KCNH2
| 1
| 1
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"Lamotrigine blocks hERG potassium channels to a significant extent in vitro, but topiramate and gabapentin have considerably less effect [XREF_BIBR]."
Lactacystin affects KCNH2
| 1
Lactacystin inhibits KCNH2. 1 / 1
| 1
reach
"Interestingly, the protease inhibitor lactacystin inhibited the low K (+)-induced hERG endocytosis and concomitantly led to an accumulation of monoubiquitinated mature hERG channels, suggesting that deubiquitination is also required for the endocytic degradation."
Ketamine affects KCNH2
| 1
| 1
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"WT hERG is blocked in a concentration dependent manner with IC50 = 12.05 +/-1.38 mum by ketamine, and the steady-state inactivation curves are shifted to more negative potentials (about -27 mV)."
Ixazomib affects KCNH2
| 1
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"Nonclinical studies assessed (1) the in vitro binding of ixazomib to the hERG channel and (2) its effect on QT/QTc in dogs (N = 4) via telemetry."
Interaction.AF 3013 affects KCNH2
| 1
Interaction.AF 3013 inhibits KCNH2. 1 / 1
| 1
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"Inter-group comparison was performed using a two-way analysis of variance (group, time) with repeated measures at each time, followed by a one-way analysis of variance (group) at each time in case of significant groupxtime interaction.AF 3013 produced very little reduction of HERG current amplitude at 0.1 Hz."
In situ Fuc editing affects KCNH2
| 1
In situ Fuc editing inhibits KCNH2. 1 / 1
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"As a result, the normalized hERG maximal tail current of fucosylated group is approximately 25% lower than that of control group at the end of the 40-min perfusion (XREF_FIG, bottom), indicating that in situ Fuc editing suppressed hERG channel activity by inhibiting its current."
| 1
Immediate early response increases the amount of KCNH2. 1 / 1
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"Stimulation of c- fos and Erg1 expression in primary pituitary cells and pituitary gonadotrope cell lines (alphaT3-1 and LbetaT2) cell lines by GnRH has been reported previously (Abbas and Evans, 200; Wolfe and Call, 1999; Wurmbach et al., 2001; Dorn et al., 1999), suggesting that the GnRHA transcriptional effects could be mediated by these immediate early response genes."
Imidazolide affects KCNH2
| 1
| 1
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"Therefore, IM preferentially blocked the open HERG channel through F652 and Y656, providing a molecular mechanism for the cardiac side effects during the clinical administration of IM."
I- eag domains affects KCNH2
| 1
I- eag domains inhibits KCNH2-R56Q. 1 / 1
| 1
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"Adenoviral i- eag domains reduced the normalized I-V curve of hERG R56Q channels (XREF_FIG), similar to what we found in HEK293 cells (XREF_FIG)."
Hypoxia affects KCNH2
| 1
Hypoxia decreases the amount of KCNH2. 1 / 1
| 1
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"Recent studies demonstrated that hERG protein expression (human ether-a-go-go-related gene) is reversibly down-regulated by prolonged hypoxia XREF_BIBR XREF_BIBR, which was proposed to occur via the increased generation of ROS in mitochondria XREF_BIBR."
Hydroxide affects KCNH2
| 1
| 1
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"Changing a molecule with two amines into a system with one amine and a hydroxyl group reduces hERG inhibition by 4 to 6 fold, and increases SlogP and estimated lipophilicity."
1 |
Transcriptionally active hsa-miR-873-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
Hsa-miR-765 affects KCNH2
1 |
Transcriptionally active hsa-miR-765 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
Hsa-miR-762 affects KCNH2
1 |
Transcriptionally active hsa-miR-762 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-7111-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-7106-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-708-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-7-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-6870-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-6825-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-6814-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
Hsa-miR-637 affects KCNH2
1 |
Transcriptionally active hsa-miR-637 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-625-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-6085 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-5787 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-5703 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-5698 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-509-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-509-3-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-5010-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-5001-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4768-3p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4731-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4723-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4722-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4665-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4662b decreases the amount of KCNH2. 1 / 1
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biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4647 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4525 decreases the amount of KCNH2. 1 / 1
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biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4516 decreases the amount of KCNH2. 1 / 1
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biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4505 decreases the amount of KCNH2. 1 / 1
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biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4498 decreases the amount of KCNH2. 1 / 1
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biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4492 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4446-3p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4434 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4426 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4418 decreases the amount of KCNH2. 1 / 1
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biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-4281 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-34a-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-335-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-328-3p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-3139 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-28-5p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-1288-3p decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-1286 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-1275 decreases the amount of KCNH2. 1 / 1
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biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-1253 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
1 |
Transcriptionally active hsa-miR-1205 decreases the amount of KCNH2. 1 / 1
1 |
biopax:mirtarbase
No evidence text available
Homolog Doa10 affects KCNH2
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Homolog Doa10 inhibits KCNH2. 1 / 1
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reach
"Similarly to MARCH6, the yeast homolog Doa10 promotes degradation of ERG1, the SM homolog [43]; however, the first 100 amino acids of SM that are necessary and sufficient for cholesterol dependent degradation are lacking in lower organisms such as yeast, suggesting that the mechanism through which Doa10 regulates degradation of ERG1 is likely distinct [32]."
Histamine receptor affects KCNH2
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Histamine receptor inhibits KCNH2. 1 / 1
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"The non cardiotoxic histamine receptor antagonists chlorpheniramine and diphenhydramine blocked HERG channels with a much weaker potency with IC50 values of 20.9 2.1 1tM (n = 5) and 27.1 1.5 1tM (n = 5; Fig. 2B)."
Histamine affects KCNH2
| 1
| 1
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"Block of HERG k channel by classic histamine h (1) receptor antagonist chlorpheniramine."
Hexadecane affects KCNH2
| 1
| 1
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"Thus, conversion of a CNS drug into its non CNS counterpart, according to the theme of this commentary, may lead to diminished hERG toxicity."
Herbimycin affects KCNH2
| 1
Herbimycin leads to the dephosphorylation of KCNH2 on tyrosine. 1 / 1
| 1
reach
"The constitutive tyrosine phosphorylation of the ERG1 protein, detected by co-immunoprecipitation, was reduced by the protein-tyrosine kinase inhibitors, lavendustin A, herbimycin A, or genistein (but not daidzein)."
HKCNE4 affects KCNH2
| 1
KCNH2 binds hKCNE4. 1 / 1
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"In order to determine if hKCNE4 can interact with HERG and KCNQ1, similar to other KCNE subunits we coexpressed hKCNE1 with wild type (WT) KCNQ1 and with HERG in Xenopus oocytes and CHO cells.Cotransfection of hKCNE4 with WT-HERG did not modify the properties of WT-HERG channel mediated currents."
HERGAPDbase affects KCNH2
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HERGAPDbase activates KCNH2. 1 / 1
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reach
"In the future, hERGAPDbase might enable scientists to predict not only the hERG channel blocking potential of drugs but also the drugs ' influence on the QT interval in the early stages of drug research and development."
HERG1b-G628S channels affects KCNH2
| 1
HERG1b-G628S channels inhibits KCNH2. 1 / 1
| 1
reach
"The non functional hERG1a-G628S and hERG1b-G628S channels co-assembled with wild-type hERG1a and dominantly suppressed hERG1 current."
HERG1b-G628S affects KCNH2
| 1
HERG1b-G628S inhibits KCNH2. 1 / 1
| 1
reach
"HERG1a-G628S and hERG1b-G628S were both shown to decrease hERG1 current by 85% when co-expressed with hERG1a at a 1:1 ratio."
HERG1a(USO)-G628S channels affects KCNH2
| 1
HERG1a(USO)-G628S channels inhibits KCNH2. 1 / 1
| 1
reach
"HERG1a (USO)-G628S channels did not appreciably associate with hERG1a and did not significantly suppress hERG1 current when co-expressed at equivalent ratios or at ratios that approximate those found in cardiac tissue."
HERG1a USO -G628S channels affects KCNH2
| 1
HERG1a USO -G628S channels inhibits KCNH2. 1 / 1
| 1
reach
"HERG1a USO -G628S channels did not appreciably associate with hERG1a and did not significantly suppress hERG1 current when co-expressed at equivalent ratios or at ratios that approximate those found in cardiac tissue."
HERG-HEK293 affects KCNH2
| 1
HERG-HEK293 inhibits KCNH2. 1 / 1
| 1
reach
"Cardiotoxic readout of the hERG-HEK293 assay was evaluated through calculation of the half maximal inhibitory concentration (IC 50) to inhibit the hERG peak tail current, a surrogate measure for QT prolongation."
HERG-G572S affects KCNH2
| 1
HERG-G572S activates KCNH2. 1 / 1
| 1
reach
"To our knowledge, hERG-G572S induces trafficking defects of hERG channel protein from Golgi to the plasma membrane and results in a dominant negative suppression of hERG current density."
HERG inhibitor affects KCNH2
| 1
HERG inhibitor activates KCNH2. 1 / 1
| 1
reach
"This study characterized hERG channel inhibition by a minimally structured high affinity hERG inhibitor, Cavalli-2, composed of three phenyl groups linked by polymethylene spacers around a centralamino group, chosen to probe the spatial arrangement of side chain groups in the high-affinity drug binding site of the hERG pore."
Guanylyl cyclase-cGMP system.NO affects KCNH2
| 1
Guanylyl cyclase-cGMP system.NO activates KCNH2. 1 / 1
| 1
reach
"Altogether, these results suggest that the modulatory action of NO on KCNH2 channels is not mediated via the activation of the guanylyl cyclase-cGMP system.NO modulation of KCNH2 channels could at least in part be determined by the dynamic interplay between RNS and ROS : RNS could act as ROS scavengers [75], thus affecting channel modulation by ROS themselves."
Gsk affects KCNH2
| 1
Gsk decreases the amount of KCNH2. 1 / 1
| 1
reach
"The inhibition of GSK and S6 (RPS6KB1) kinases results in a small increase in PMA induced Erg1 expression only during the early time points."
Group affects KCNH2
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Group inhibits KCNH2. 1 / 1
| 1
reach
"Notably this later study examined the effects of 1294 on host enzymes and detected an undesirable hERG activity, which was abrogated by modification of the R2 group to a pyran 91."
Glyburide affects KCNH2
| 1
| 1
reach
"Glibenclamide concentrations inhibiting I HERG, I Kr and I Ks were higher than those active on I KATP in pancreatic beta-cells (in the nM range) [24], but closer to those required to inhibit cardiac I KATP (1-100 muM) [25-27]."
Glucocorticoid-inducible kinase affects KCNH2
| 1
Glucocorticoid-inducible kinase activates KCNH2. 1 / 1
| 1
reach
"In the present study, we demonstrated that overexpression of the stress responsive serum- and glucocorticoid inducible kinase (SGK) isoforms SGK1 and SGK3 increased the current and expression level of the membrane localized mature proteins of hERG channels stably expressed in HEK 293 (hERG-HEK) cells."
Glucocorticoid inducible kinase 3 affects KCNH2
| 1
Glucocorticoid inducible kinase 3 activates KCNH2. 1 / 1
| 1
reach
"Interestingly, it has been reported that the serum and glucocorticoid inducible kinase 3 (SGK3) up-regulates I hERG1 by increasing protein levels in the plasma membrane, without affecting the K + channel activating kinetics [31]."
Ginseng saponins affects KCNH2
| 1
Ginseng saponins activates KCNH2. 1 / 1
| 1
reach
"Consistently, ginseng saponins increased the HERG deactivation time constants with the order of potency of Rg1 (a major component of PT)> Rf1> Rb1 (a major component of PD)."
| 1
| 1
sparser
"The IC 50 value of GFLX-induced hERG inhibition was reported to be 130 µ mol/L (approximately 50 µ g/ml) [ xref ], which is somewhat higher than the plasma GFLX concentrations showing QT/QTc prolongation (approximately 30 µ g/ml)."
Gamma-KTx peptides affects KCNH2
| 1
Gamma-KTx peptides inhibits KCNH2. 1 / 1
| 1
reach
"Thus BmTx3 is the first reported alpha-KTx peptide also showing HERG blocking activity, like gamma-KTx peptides."
GacH affects KCNH2
| 1
GacH activates KCNH2. 1 / 1
| 1
reach
"The ALG10B gene (also known as KCR1) modulates HERG, reducing the sensitivity of cardiac cells to arrhythmic disturbance [XREF_BIBR, XREF_BIBR]."
| 1
| 1
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"Block of hERG K+ channel and prolongation of action potential duration by fluphenazine at submicromolar concentration."
Fluoxetine affects KCNH2
| 1
Fluoxetine inhibits KCNH2. 1 / 1
| 1
reach
"Voltage clamp analyses employing square pulse or ventricular action potential waveform protocols showed that fluoxetine and norfluoxetine caused direct, concentration dependent, block of hERG current (IhERG)."
Fluoride affects KCNH2
| 1
| 1
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"We found that (1) F (-) slightly shifts the voltage dependence of hERG channel activation to more positive voltages, while Br (-) shifts it to more negative voltages; (2) Br (-) shifts to more positive voltages both the inactivation-voltage relationship and the peak position of channel full activation of hERG; (3) F (-) slows hERG activation, while both F (-) and Br (-) make the channel close faster; (4) neither F (-) nor Br (-) have any effect on hERG inactivation kinetics."
Fingolimod affects KCNH2
| 1
| 1
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"Meanwhile, fingolimod significantly inhibited hERG current, which was not observed by siponimod."
| 1
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"Superparamagnetic iron oxide nanoparticles (SPIONs) modulate hERG ion channel activity."
Extracellular [H+] affects KCNH2
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Extracellular [H+] inhibits KCNH2. 1 / 1
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"Increasing extracellular [H+] accelerates HERG deactivation."
Extracellular K(+) affects KCNH2
| 1
Extracellular K(+) inhibits KCNH2. 1 / 1
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"Raising extracellular K (+) revealed a slowly deactivating inward tail current indicative of HERG like K (+) current."
Ether-a-go-go-related gene affects KCNH2
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Ether-a-go-go-related gene inhibits KCNH2. 1 / 1
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"L539fs/47, a truncated mutation of human ether-a-go-go-related gene (hERG), decreases hERG ion channel currents in HEK 293 cells."
Ethanol affects KCNH2
| 1
| 1
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"Ethanol with 50.0 mM could inhibit rapid delayed rectifier potassium currents (I hERG)."
Eprosartan affects KCNH2
| 1
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"Eprosartan inhibited the tail amplitude of HERG currents elicited on repolarization after pulses to +60 mV from 239 +/- 78 to 179 +/- 72 pA."
Endogenous signal transducing adaptor molecule-binding protein affects KCNH2
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Endogenous signal transducing adaptor molecule-binding protein inhibits KCNH2. 1 / 1
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"Consistently, overexpression of the endosomal deubiquitinating enzyme signal transducing adaptor molecule binding protein significantly accelerated whereas knockdown of endogenous signal transducing adaptor molecule binding protein impeded degradation of the mature hERG channels under low K (+) conditions."
Doxorubicin affects KCNH2
| 1
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"Doxorubicin (30 microM) also prolonged QTc by 13%, did not significantly block hERG channels and specifically inhibited I (Ks) (IC (50) : 4.78 microM)."
Dopamine-beta-hydroxylase inhibitor affects KCNH2
| 1
Dopamine-beta-hydroxylase inhibitor inhibits KCNH2. 1 / 1
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"Etamicastat, a peripheral reversible dopamine-beta-hydroxylase inhibitor, blocked the hERG current amplitude with an IC50 value of 44.0 microg/ml in HEK 293 cells."
Domperidone affects KCNH2
| 1
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"Both domperidone and metoclopramide concentration-dependently blocked HERG currents, and the following values were calculated for IC (50) (the concentrations causing half-maximal inhibition) and n (the Hill coefficient) : 57.0 nmol/l and 0.99 for domperidone, 5.4 micromol/l and 0.95 for metoclopramide."
Dominant negative LQT2 mutation affects KCNH2
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Dominant negative LQT2 mutation-A561V increases the amount of KCNH2. 1 / 1
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"The dominant negative LQT2 mutation A561V reduces wild-type HERG expression."
DnPKB affects KCNH2
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DnPKB inhibits KCNH2. 1 / 1
| 1
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"Consistent with an important role for PKB, caPKB increased and dnPKB decreased I HERG."
| 1
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"Of the PDE inhibitors tested, vinpocetine, erythro-9-(2-hydroxy-3-nonyl) adenine (EHNA), vesnarinone, rolipram and dipyridamole decreased hERG currents in a concentration dependent manner."
| 1
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"The non cardiotoxic histamine receptor antagonists chlorpheniramine and diphenhydramine blocked HERG channels with a much weaker potency with IC50 values of 20.9 2.1 1tM (n = 5) and 27.1 1.5 1tM (n = 5; Fig. 2B)."
Digitoxin affects KCNH2
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Digitoxin inhibits KCNH2. 1 / 1
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"Furthermore, there is evidence that cardiac glycosides can reduce trafficking of the hERG channel, which conducts I Kr in humans, and in particular, that digitoxin could cause a significant reduction in hERG trafficking at therapeutic concentrations."
Details molecular interactions affects KCNH2
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Details molecular interactions inhibits KCNH2. 1 / 1
| 1
eidos
"Homology models of hERG , which are based on the X-ray crystal structures of the bacterial KcsA [ 82 ] and MthK channels [ 83 ] , have already shed light on some details of the molecular interactions that initiate hERG inhibition ."
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"Desloratadine did not inhibit IKr channel human ether-a-go-go-related gene (HERG)-induced current in a study in which HERG was expressed in Xenopus oocytes."
Cyclase affects KCNH2
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Cyclase increases the amount of KCNH2. 1 / 1
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"Inhibition of later steps in the ergosterol-biosynthetic pathway by ketoconazole, an inhibitor of the lanosterol-14alpha-demethylase, and U18666A, an inhibitor of the squalene-2,3-epoxide-lanosterol cyclase, also induce expression of ERG1, suggesting that ERG1 expression is positively regulated by diminished intracellular ergosterol levels."
Crt affects KCNH2
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Crt activates KCNH2. 1 / 1
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"HERG, downregulated during heart failure, can be restored by CRT XREF_BIBR."
Crizotinib affects KCNH2
| 1
| 1
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"QTc prolongation has been observed in patients receiving crizotinib (Xalkori, 2011) and the clinical review (Pfizer I, 2011a) reported that crizotinib inhibits hERG at concentrations consistent with the results reported in this study."
Cortisol affects KCNH2
| 1
| 1
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"In an overexpression system of Xenopus oocytes, hydrocortisone increased hERG K + currents and reduced Kv1.5 K + currents; these effects were negated by pretreatment with staurosporine."
Conotoxin affects KCNH2
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sparser
"The docking studies suggest that the conotoxin binds stably to the HERG protein."
ComCA affects KCNH2
| 1
| 1
sparser
"SQTS has been associated with mutations in six genes ( KCNQ1, KCNH2, KCNJ2, CACNA1C, CACNB2 , and CACNA2D1 ) with GOF mutations in KCNH2 (SQTS1) being the most prevalent subtype xref , xref ."
Cisplatin affects KCNH2
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Cisplatin increases the amount of KCNH2. 1 / 1
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"Our results show that cisplatin increased the expression of HERG in gastric cancer cells."
| 1
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"Cholesterol enrichment inhibited the HERG K + current as shown in XREF_FIG for typical recordings."
| 1
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"The non cardiotoxic histamine receptor antagonists chlorpheniramine and diphenhydramine blocked HERG channels with a much weaker potency with IC50 values of 20.9 2.1 1tM (n = 5) and 27.1 1.5 1tM (n = 5; Fig. 2B)."
Cation affects KCNH2
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Cation inhibits KCNH2. 1 / 1
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sparser
"Modulation of HERG channel inactivation by external cations."
CasE affects KCNH2
| 1
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sparser
"However, this is not the case, and KCNH2 mutations have only rarely been associated with drug-induced LQTS."
Cardiac G protein-coupled receptors affects KCNH2
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Cardiac G protein-coupled receptors activates KCNH2. 1 / 1
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"Little is known about channel and receptor cross talk, although considerable evidence exists that cardiac G protein coupled receptors can modulate hERG channel function."
| 1
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"Both spironolactone (SP) and its main metabolite, canrenoic acid (CA), prolong cardiac action potential duration and decrease the Kv11.1 (HERG) current."
Cannabinoid affects KCNH2
| 1
| 1
sparser
"In addition to their weak inhibition of 5-HT 2B receptor activation, some of the synthetic cannabinoids also inhibited hERG channels ( xref )."
Calmodulin inhibitor affects KCNH2
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Calmodulin inhibitor activates KCNH2. 1 / 1
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"It was found that the calmodulin inhibitor W-7 blocked hERG, hK (v) 1.5 and hK (IR) 2.1 channels."
| 1
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"Cesium chloride blocks HERG potassium channels, prolonging the QT interval and inducing TdP [XREF_BIBR]."
Cadmium(2+) affects KCNH2
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"Extracellular Cd (2+) modulates hERG channel activation by binding to a coordination site formed, at least in part, by three Asp residues."
CaPKB affects KCNH2
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CaPKB activates KCNH2. 1 / 1
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"In addition, while caPI3K produced only slight enhancement (~ 18%) of I HERG function, caPKB strikingly increased I HERG density (~ 52%)."
CGMP affects KCNH2
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CGMP inhibits KCNH2. 1 / 1
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"HERG channels (I Kr) are reportedly inhibited by NO in a cGMP independent manner when expressed in X. laevis oocytes, although S nitrosylation was not directly evaluated 63."
Brief (2 ms affects KCNH2
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Brief (2 ms activates KCNH2. 1 / 1
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"After an initial depolarising command to +40 mV to activate and inactivate I hERG, brief (2 ms) repolarising commands to a range of membrane potentials (in 10 mV increments down to -140 mV) were used to alleviate I hERG inactivation to differing extents and then the amplitude of the rapid I hERG transient during the third step (to +40 mV) was measured."
| 1
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"Given that PBA inhibition is already weaker than activation for KCNQ channels, it should be possible to design second generation boronic acid activators that do not inhibit hERG and other Kv channels."
Beta1 integrins affects KCNH2
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KCNH2 binds beta1 integrins. 1 / 1
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"More recently it was also shown that hERG1 interaction with beta1 integrins mediates BC metastatization in immunodeficient mice [XREF_BIBR]."
Beta-adrenoceptor affects KCNH2
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Beta-adrenoceptor activates KCNH2. 1 / 1
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"These data showed that HERG blockade by beta-adrenoceptor blockers occurred only at high micromolar concentrations, which are significantly above the recently established safe margin of 100 (Redfern et al., 2003)."
Beta(1) integrins affects KCNH2
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KCNH2 binds beta(1) integrins. 1 / 1
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"On the whole, these data indicate that the hERG1 protein associates with beta (1) integrins and modulates adhesion receptor signaling."
Benzamide affects KCNH2
| 1
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"ICA-105574 (ICA), a 3-Nitro-n-(4-phenoxyphenyl) benzamide derivative activates hERG1 by strongly attenuating pore-type inactivation."
Bedaquiline affects KCNH2
| 1
| 1
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"Both bedaquiline and M2 inhibit the cardiac hERG and IKr potassium channels in vitro, 30 and modest QT prolongation has been observed during clinical trials."
BEAG S4-S5 affects KCNH2
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BEAG S4-S5 inhibits KCNH2. 1 / 1
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"Furthermore, transfer of bEAG S4-S5 linker to the hERG disrupted the complete hERG channel closure."
Azelastine affects KCNH2
| 1
| 1
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"Azelastine induced a concentration dependent decrease of the hERG current amplitude at the end of the voltage steps and tail currents."
Ayr1 affects KCNH2
| 1
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sparser
"We have reported for the first time that KCNH2 (1956, C>T) polymorphism is associated with efficacy of antihypertensive drugs CCBs and ADR blockers, and may serve as a novel biomarker for individualized therapy for certain antihypertensive drugs."
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"Simvastatin and atorvastatin reduce hERG current by accelerating channel inactivation."
Atazanavir affects KCNH2
| 1
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"Atazanavir blocks hERG K + channels directly and also interferes with the trafficking of channels [XREF_BIBR]."
| 1
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"However, we observed transcriptional changes for several iron-channel genes, including KCNE1, KCNH2, and CADA1C in cardiomyocytes treated with arsenite."
| 1
Arsenic atom decreases the amount of KCNH2. 1 / 1
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"Expression of the ion-channel genes CACNA1, KCNH2, KCNQ1 and KCNE1 were down-regulated by 1-muM arsenic."
Apremilast affects KCNH2
| 1
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"In-vitro studies in HEK293 cells showed that apremilast inhibited the hERG current with an estimated half maximal inhibitory concentration (IC 50) of 184.2 microM (84.8 microg/mL) and Hill coefficient of 0.9."
Anti-miR-133b oligonucleotide affects KCNH2
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Anti-miR-133b oligonucleotide activates KCNH2. 1 / 1
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"The transfection of anti-miR-133b oligonucleotide (AMO-133b) remarkably prevented the decrease of hERG protein by 5muM ATO treatment for 24h in U251 cells, whereas anti-miR-34a oligonucleotide (AMO-34a) did not exhibit recuperated effect."
Amoxapine affects KCNH2
| 1
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"Amoxapine caused acute hERG blockade in oocytes (IC (50) = 21.6 microM) and in HEK 293 cells (IC (50) = 5.1 microM)."
Amisulpride affects KCNH2
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"Amisulpride, in common with some other substituted benzamides, was found to inhibit hERG current with an IC 50 of around 100muM 15, a markedly lower potency than some D 2 antagonists."
Alpha1A-AR affects KCNH2
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Alpha1A-AR activates KCNH2. 1 / 1
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"Stimulation of alpha1A-AR with phenylephrine or direct activation of PKC with phorbol ester increased HERG channel protein abundance and K (+) current density in a time- and dose dependent manner."
Alpha-hERG1-MoAb affects KCNH2
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Alpha-hERG1-MoAb activates KCNH2. 1 / 1
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"The possibility to exploit the alpha-hERG1-MoAb to target hERG1 in vivo could have an immediate clinical fallout for the diagnosis and clinical follow-up of PDAC."
Adenine affects KCNH2
| 1
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"Of the PDE inhibitors tested, vinpocetine, erythro-9-(2-hydroxy-3-nonyl) adenine (EHNA), vesnarinone, rolipram and dipyridamole decreased hERG currents in a concentration dependent manner."
[K~ affects KCNH2
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[K~ activates KCNH2. 1 / 1
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"The mechanism of HERG modulation by [K ~ is un- known, but the phenomenon has been observed in an- other cloned K+ channel, RCK4."
[ 1 , 2 , 4 ]-triazolo- [ 1 affects KCNH2
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[ 1 , 2 , 4 ]-triazolo- [ 1 inhibits KCNH2. 1 / 1
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"[1, 2, 4]-triazolo- [1, 4]-oxazepine were found to decrease hERG activity and 2-fold decrease in GPR142 potency."
ZnFLC affects KCNH2
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ZnFLC increases the amount of KCNH2. 1 / 1
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"The expression of ERG1, ERG7, ERG11 ERG27, and ERG28, which have effects on the synthesis of ergosterol, were all significantly upregulated by ZnFLC."
YWHAH affects KCNH2
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1 |
hprd
No evidence text available
YFP fragments affects KCNH2
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YFP fragments inhibits KCNH2. 1 / 1
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"Thus, the FRET levels were minimized not only in the presence of a mutation that fully knocked out the ability of the recombinant eag to restore deactivation kinetics of the hERG Delta2-135 channels (XREF_FIG), but also with the V3C and V8C mutated N1-135 and YFP fragments, which were able to partially restore hERG Delta2-135 deactivation gating."
XSN affects KCNH2
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XSN inhibits KCNH2. 1 / 1
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"In this study, we revealed that XSN blocks hNaV1.5 sodium channel and hERG potassium channel, which has placed XSN as a class I and III antiarrhythmic medicine as the widely used antiarrhythmic drug amiodarone."
XPNPEP2 affects KCNH2
| 1
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sparser
"Similar to Kv1.5, the mature membrane-bound (155 kDa) form of hERG was selectively cleaved by PK."
XE991 affects KCNH2
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XE991 inhibits KCNH2. 1 / 1
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"Because high concentrations (100smuM) of XE991 can block HERG channels XREF_BIBR, we applied XE991 (3muM) in the presence of the HERG blocker terfenadine (1muM)."
Wortmannin affects KCNH2
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Wortmannin increases the amount of KCNH2. 1 / 1
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"Wortmannin (a phosphoinositide 3-kinase (PI3K) inhibitor) caused approximately 30% reduction of HERG current (I (HERG)) stably expressed in HEK293 cells."
Way123 affects KCNH2
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Way123 activates KCNH2. 1 / 1
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"Pharmacological experiments showed that the hERG channels could be blocked by the chemical molecule blockers of E-4031 or Way123,398."
WW affects KCNH2
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"It is possible that several PY motifs of hERG1 interact with several WW domains of Nedd4-2 simultaneously."
WAY 123,398 affects KCNH2
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WAY 123,398 inhibits KCNH2. 1 / 1
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"Blockade of HERG by WAY 123,398 is voltage independent unlike that of E4031 and dofetilide (Faravelli et al., 1996) and WAY 123,398 works faster than dofetilide when applied extracellularly in SHSY5Y cells."
W-7 affects KCNH2
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W-7 inhibits KCNH2. 1 / 1
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"Here, we have determined whether W-7 would inhibit human ether gene (hERG or K (v) 11.1) potassium channels, hK (v) 1.5 channels or hK (IR) 2.1 channels expressed in human embryonic kidney (HEK) 293 cells."
VRT-325 affects KCNH2
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VRT-325 inhibits KCNH2-G601S. 1 / 1
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"PARP-1 inhibition did not improve the processing of the mutant form of hERG whereas VRT-325 increased the amount of processed hERG G601S."
VCE-003.2 affects KCNH2
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VCE-003.2 inhibits KCNH2. 1 / 1
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"In addition, VCE-003.2 administration did not inhibit hERG channel activity, suggesting a potential lack of cardiotoxicity (Additional file 3), and it was not genotoxic as assessed by AMES assays (Additional file 4)."
U18666A affects KCNH2
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U18666A decreases the amount of KCNH2. 1 / 1
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"Inhibition of later steps in the ergosterol-biosynthetic pathway by ketoconazole, an inhibitor of the lanosterol-14alpha-demethylase, and U18666A, an inhibitor of the squalene-2,3-epoxide-lanosterol cyclase, also induce expression of ERG1, suggesting that ERG1 expression is positively regulated by diminished intracellular ergosterol levels."
Taxifolin glycoside affects KCNH2
| 1
Taxifolin glycoside activates KCNH2. 1 / 1
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"Taxifolin glycoside induced 2 distinct changes in hERG K + channel gating : (1) facilitating activation (negative shift of the voltage-dependence of activation and accelerated activation time constant) and (2) facilitating of inactivation (reduced onset of inactivation time constant)."
Taxifolin affects KCNH2
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Taxifolin inhibits KCNH2. 1 / 1
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"Taxifolin glycoside reduced tail currents of hERG K + channels during the repolarizing pulse (XREF_FIG)."
TXNRD2 affects KCNH2
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TXNRD2 activates KCNH2. 1 / 1
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"Here, we present direct molecular evidence for potassium channel stimulation in a rat pituitary cell line (GH (4) C (1)) by a nuclear receptor for thyroid hormone, TRbeta, acting rapidly at the plasma membrane through phosphatidylinositol 3-kinase (PI3K) to slow the deactivation of KCNH2 channels already in the membrane."
TSG101 affects KCNH2
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TSG101 inhibits KCNH2. 1 / 1
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"Hrs, Stam1, or Tsg101 ablation profoundly attenuated the rapid PM removal of wt hERG in ouabain- or digoxin treated cells (XREF_FIG)."
TRX-E-002-1 affects KCNH2
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TRX-E-002-1 inhibits KCNH2. 1 / 1
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"A patch-clamp electrophysiological assay in hERG transfected mammalian cells showed that TRX-E-002-1 concentration-dependently inhibited hERG current with IC 50 of 17.0 muM."
TRPM channels affects KCNH2
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TRPM channels activates KCNH2. 1 / 1
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"TRPM channels in islets are thought to be key players in the regulated release of insulin XREF_BIBR, XREF_BIBR and TRPM3 in particular is known to mediate the regulated uptake of zinc from the extracellular space mouse beta cells 38, when engaged by the neurosteroid hormone pregnenolone sulphate, to potentiate insulin secretion 39, and activate an Erg-1 dependent transcriptional pathway leading to PDX1, and in turn insulin, up-regulation 40."
TRIM39 affects KCNH2
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TRIM39 inhibits KCNH2. 1 / 1
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"Others have reported that TFP inhibits the cardiac hERG K channel with an IC 50 between 9 and 21 muM [XREF_BIBR]."
TNFRSF1A affects KCNH2
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TNFRSF1A decreases the amount of KCNH2. 1 / 1
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"We conclude that the TNF-alpha and TNFR1 system impairs HERG/I (Kr) function mainly by stimulating reactive oxygen species, particularly superoxide anion, but not by altering HERG expression; the effect may contribute to APD prolongation by TNF-alpha and may be a novel mechanism for electrophysiological abnormalities and sudden death in CHF."
TNFRSF11A affects KCNH2
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"We conclude that the rank order of potency of 5-HT4 agonists to block HERG is cisapride> renzapride> prucalopride> mosapride."
THPO affects KCNH2
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THPO inhibits KCNH2. 1 / 1
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"10 microg mL -1 ZnO uniquely increases the amplitude of the steady-state current, decreases the rate of hERG current inactivation during steady-state depolarization, accelerates channel deactivation during resurgent tail currents, and shows no significant alteration of current activation rate or voltage dependence."
TGFB affects KCNH2
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TGFB decreases the amount of KCNH2. 1 / 1
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"It can be concluded that TGF-beta reduced HERG channel expression through PKA activation, possibly independent of the cAMP levels."
TGF-beta1 (5 ng/mL affects KCNH2
| 1
TGF-beta1 (5 ng/mL inhibits KCNH2. 1 / 1
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"In our study, we showed that TGF-beta1 (5 ng/mL) for 24 h increased PKA activity and significantly reduced HERG abundance in NMCMs."
TECR affects KCNH2
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TECR inhibits KCNH2. 1 / 1
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"These include terbinafine (TER) that inhibits the ERG1 gene product, fenpropimorph (FEN) that inhibits Erg2p, and lovastatin (LOV) that inhibits Hmg1p."
TCF21 affects KCNH2
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TCF21 activates KCNH2. 1 / 1
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"POD 1 upregulation of PDGFA, ERG1, and HMGB1 mRNA correlated significantly with worse prognosis."
TCA007 affects KCNH2
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TCA007 inhibits KCNH2. 1 / 1
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"TCA007 does not inhibit hERG potassium channel in a patch-clamp assay (IC 50> 30mum), suggesting a low risk of cardiotoxicity."
TAM16 affects KCNH2
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TAM16 inhibits KCNH2. 1 / 1
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"The potential of TAM16 to inhibit the human cardiac hERG and IKr potassium channel functional activity was measured in an inducible hERG T-RExTM-CHO Cell line (ThermoFisher) using thallium influx as a surrogate indicator of potassium ion channel activity at AbbVie, USA."
Sunitinib affects KCNH2
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1 |
tas
No evidence text available
| 1
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"Sulfonylureas blockade of neural and cardiac HERG channels."
Src40-58 affects KCNH2
| 1
Src40-58 activates KCNH2. 1 / 1
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"First, we show that tyrosine kinase inhibitor, PP1, and the selective Src inhibitory peptide, Src40-58, reduce the hERG current amplitude, without altering its voltage dependence or kinetics."
Src-family kinases affects KCNH2
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Src-family kinases activates KCNH2. 1 / 1
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"These results suggest that reduction of cardiac I hERG.tail by AG556 is likely mediated by EGFR kinase.The Src family kinase inhibitor PP2 was applied to determine whether Src family kinases modulate hERG current."
SrbA affects KCNH2
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SrbA activates KCNH2. 1 / 1
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"Chromatin immunoprecipitation sequencing (ChIP-seq) analysis of SrbA in A.fumigatus, combined with the expression pattern of ergosterol biosynthesis genes for N.crassa (XREF_FIG), supports the hypothesis that SAH-2 directly regulates erg-1, erg-3, erg-5, erg-11, and erg-25 and that the increased expression of these direct target genes is a good indicator of SAH-2 activation."
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sparser
"While less selective sodium channel inhibitors (quinidine, procainamide) also interact with hERG channels and lead to prolongation in RT, this is not expected for lidocaine."
Small molecules affects KCNH2
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Small molecules inhibits KCNH2. 1 / 1
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"Small molecules can remarkably inhibit hERG channels by binding to a few aromatic side chains in helixes of the alpha subunits of the channels, which could lead to deleterious consequences such as torsade de pointes and even sudden cardiac death [XREF_BIBR]."
SlogP affects KCNH2
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SlogP activates KCNH2. 1 / 1
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"Hence, high lipophilicity (SlogP) increases the hERG liability."
SiW-5 affects KCNH2
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SiW-5 activates KCNH2. 1 / 1
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"Real-time PCR showed that ERG1, ERG7, ERG11 and ERG28 were all significantly upregulated by SiW-5."
Scorpion toxin BmKKx2 affects KCNH2
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Scorpion toxin BmKKx2 inhibits KCNH2. 1 / 1
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"Scorpion toxin BmKKx2 blocking hERG channel currents in K562 cells."
SUN-1334H affects KCNH2
| 1
SUN-1334H activates KCNH2. 1 / 1
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"In CHO-K1 and hERG cells, SUN-1334H did not modulate hERG K (+)-currents at concentrations as high as 100 micromol/L."
STIP1 affects KCNH2
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biogrid
No evidence text available
STAT1 affects KCNH2
| 1
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sparser
"Molecular docking attempts suggest two possible protein-protein interactions of HERG with the ß1-integrin receptor and the transcription factor STAT-1 as novel HERG-directed therapeutic targeting which avoids possible cardiotoxicity."
STAM affects KCNH2
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STAM inhibits KCNH2. 1 / 1
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"Hrs, Stam1, or Tsg101 ablation profoundly attenuated the rapid PM removal of wt hERG in ouabain- or digoxin treated cells (XREF_FIG)."
SSE2 affects KCNH2
| 1
SSE2 activates KCNH2. 1 / 1
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"There are three possible mechanisms for the pilsicainide induced increase of hERG proteins via post-translational modifications : (1) phosphorylation of Akt, (2) activation of hsp expressions, and (3) direct action as a chemical chaperone."
SQT1 affects KCNH2
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sparser
"It has been suggested that class IA drugs may provide the best therapeutic avenue for treatment of SQT1 form of SQTS caused by N588K mutation in HERG ."
SP1 affects KCNH2
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SP1 activates KCNH2. 1 / 1
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"It has been reported that the transcription factor Sp1 modulates the activities of the KCNQ1 (which encodes KvLQT1) and KCNH2 (which encodes HERG1) promoters, suggesting that the differential expression of Sp1 (RV> LV) may account for the interventricular gradients of KvLQT1 and HERG1 protein expression [XREF_BIBR, XREF_BIBR]."
SNP affects KCNH2
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| 1
sparser
"The KCNH2 intronic SNP rs3807375 was associated with a 1.6 ms (SE 0.4) increase of adjusted QT interval per minor allele QT Nc (p=4.7×10 −5 )."
SM-21 affects KCNH2
| 1
SM-21 inhibits KCNH2. 1 / 1
| 1
reach
"In HERG transfected COS-7 cells, SM-21 potentiated the ifenprodil induced blockade of the HERG current."
SLC5A7 affects KCNH2
| 1
SLC5A7 inhibits KCNH2. 1 / 1
| 1
reach
"ChT (300 microM) significantly decreased whole-cell hERG current in both HEK 293 and SH-SY5Y cells."
SKF-96365 affects KCNH2
| 1
SKF-96365 inhibits KCNH2. 1 / 1
| 1
reach
"It was found that SKF-96365 inhibited hERG current in a concentration dependent manner (IC50, 3.4 muM)."
SJ1 affects KCNH2
| 1
SJ1 inhibits KCNH2. 1 / 1
| 1
reach
"Although subsequent chemical optimization work improved the pharmacological properties of SJ1, including increased potency, reduced cytotoxicity, and elimination of hERG potassium channel activity 16, these analogs still exhibit ion channel binding."
SISR affects KCNH2
| 1
SISR inhibits KCNH2. 1 / 1
| 1
reach
"Voltage-clamp electrophysiological studies have shown that SISR, such as fluoxetine and norfluoxetine, one of its metabolites, selectively block hERG channels via two different mechanisms : (i) direct channel blockade, and (ii) disruption of channel protein trafficking."
SHP-1 mutant affects KCNH2
| 1
SHP-1 mutant inhibits KCNH2. 1 / 1
| 1
reach
"Both hERG and hEAG1 currents were decreased by applying active recombinant SHP-1, and increased by the inhibitory substrate trapping SHP-1 mutant."
SERHL affects KCNH2
| 1
SERHL inhibits KCNH2. 1 / 1
| 1
reach
"SHL significantly suppressed L-type Ca (2+) current from left ventricular myocytes of guinea pig, hNav1.5 current and hERG current with 50% inhibiting concentrations (IC (50)) of 6.0, 3.0 and 10.7 times CRC, respectively."
SERCA inhibitors affects KCNH2
| 1
SERCA inhibitors inhibits mutated KCNH2. 1 / 1
| 1
reach
"Intriguingly, other SERCA inhibitors can not rescue these hERG mutants, suggesting thapsigargin might have broad activity to modulate trafficking for particular protein classes 62."
SEC23A affects KCNH2
| 1
| 1
sparser
"This ratio may reflect how isoforms and homologues of KCNH2 co-assemble to create heteromeric potassium channels with unique electrophysiological properties xref , xref ."
SC83288 affects KCNH2
| 1
SC83288 inhibits KCNH2. 1 / 1
| 1
reach
"SC81458 and SC83288 did not block human cardiac hERG mediated K + conductance."
SC81458 affects KCNH2
| 1
SC81458 inhibits KCNH2. 1 / 1
| 1
reach
"SC81458 and SC83288 did not block human cardiac hERG mediated K + conductance."
SAR1A affects KCNH2
| 1
SAR1A inhibits KCNH2. 1 / 1
| 1
reach
"Expression of DN Sar1 inhibited the Golgi processing of hERG, decreased hERG current (I (hERG)) by 85% (n> or = 8 cells per group, *, p < 0.01), and reduced the plasmalemmal staining of hERG."
SAH-2 affects KCNH2
| 1
SAH-2 activates KCNH2. 1 / 1
| 1
reach
"Chromatin immunoprecipitation sequencing (ChIP-seq) analysis of SrbA in A.fumigatus, combined with the expression pattern of ergosterol biosynthesis genes for N.crassa (XREF_FIG), supports the hypothesis that SAH-2 directly regulates erg-1, erg-3, erg-5, erg-11, and erg-25 and that the increased expression of these direct target genes is a good indicator of SAH-2 activation."
S4-S5 L peptide affects KCNH2
| 1
S4-S5 L peptide inhibits KCNH2. 1 / 1
| 1
reach
"One S4-S5 L peptide inhibits hERG channels."
S4-S5 affects KCNH2
| 1
S4-S5 activates KCNH2. 1 / 1
| 1
reach
"In contrast to HCN channel inactivation, however, HERG inactivation is not mediated by a loose coupling of S4-S5 linker and S6 T but by conformational changes at the outer pore region."
S1 affects KCNH2
| 1
S1 inhibits KCNH2. 1 / 1
| 1
reach
"found evidence for interactions between K1 and D456 (equivalent to the proposed R1-E283 interaction in Shaker) and between K6 and D411 at the base of S1, both of which were proposed to stabilize the closed state and contribute to slow hERG activation."
Rhy affects KCNH2
| 1
Rhy inhibits KCNH2. 1 / 1
| 1
reach
"The findings indicate that Rhy inhibits HERG encoded potassium channels."
Rg3 affects KCNH2
| 1
Rg3 inhibits KCNH2. 1 / 1
| 1
reach
"Rg3 also induced slowing of ERG1, ERG3, and ELK1 channel deactivation and accelerated the rate of EAG1 channel activation."
Recombinant System affects KCNH2
| 1
Recombinant System increases the amount of KCNH2. 1 / 1
| 1
reach
"Importance of the Choice of a Recombinant System to Produce Large Amounts of Functional Membrane Protein hERG."
Rb+ affects KCNH2
| 1
Rb+ activates KCNH2. 1 / 1
| 1
reach
"In combination with the effects of elevated extracellular ion concentrations, it is likely that Rb+ modulation of hERG channel inactivation is largely responsible for the reduced drug potencies observed in the Rb+ efflux assay."
Rb affects KCNH2
| 1
Rb activates KCNH2. 1 / 1
| 1
reach
"Interestingly, Rb + not only activated all NCA responsive K 2P channels, but also led to robust activation of BK Ca and hERG channels (XREF_FIG)."
Ranolazine affects KCNH2
| 1
KCNH2 binds Ranolazine. 1 / 1
| 1
reach
"Ranolazine binds to the promiscuous drug target hERG."
RPS6KB1 affects KCNH2
| 1
RPS6KB1 decreases the amount of KCNH2. 1 / 1
| 1
reach
"The inhibition of GSK and S6 (RPS6KB1) kinases results in a small increase in PMA induced Erg1 expression only during the early time points."
RP58866 affects KCNH2
| 1
RP58866 inhibits KCNH2. 1 / 1
| 1
reach
"RP58866 significantly inhibited the HERG channels in a concentration dependent manner, with approximately 50% decrease in the current amplitude at a concentration of 1 microM."
RNF139 affects KCNH2
1 |
1 |
biogrid
No evidence text available
RHOH affects KCNH2
1 |
1 |
hprd
No evidence text available
RFFL affects KCNH2
| 1
RFFL activates KCNH2. 1 / 1
| 1
reach
"Blocking the ER associated degradation (ERAD) pathway with a dominant negative form of the ERAD core component, valosin containing protein (VCP), in 293A cells partially abolished RFFL mediated hERG degradation."
RB1 affects KCNH2
| 1
RB1 inhibits KCNH2. 1 / 1
| 1
reach
"Rb + reduces I hERG inactivation at potentials relevant to the efflux assay, which may impair binding of drugs for which channel inactivation influences block (Rezazadeh et al., 2004)."
RAB4A affects KCNH2
| 1
Modified RAB4A decreases the amount of KCNH2. 1 / 1
| 1
reach
"Our data revealed that overexpression of Rab4 decreases the expression level of hERG in the plasma membrane."
RAB11B affects KCNH2
| 1
RAB11B inhibits KCNH2. 1 / 1
| 1
reach
"Surprisingly, the coexpression of DN Rab11B, which regulates the endosomal recycling, inhibited the Golgi processing of hERG, decreased I (hERG) by 79% (n> or = 8 cells per group; *, p < 0.01), and reduced the plasmalemmal staining of hERG."
R863X affects KCNH2
| 1
R863X activates KCNH2. 1 / 1
| 1
reach
"Coexpression of R863X with wild-type HERG showed reduced current densities and accelerated voltage dependent inactivation of HERG channels."
R)-3-amino-3-phenylpropan-1-ol at C-4 affects KCNH2
| 1
R)-3-amino-3-phenylpropan-1-ol at C-4 activates KCNH2. 1 / 1
| 1
reach
"However, some of the privileged structures in terms of potency had ADME short-comings : compounds containing amides, sulfonamides, amine and hydroxymethyl substituents in the 6-aryl group had low permeability and high efflux, derivatives having (R)-3-amino-3-phenylpropan-1-ol at C-4 induced hERG inhibition properties, and metabolic lability was seen for compounds having (S)-2-methoxy-1-phenylethan-1-amine at C-4."
QTPROL affects KCNH2
| 1
QTPROL inhibits KCNH2. 1 / 1
| 1
reach
"First, we were able to confirm the widely accepted mechanism proposed for drug induced QTPROL, in which the drug blocks the potassium channel HERG (encoded by the KCNH2 gene) and this blockade leads to a prolongation of the QT interval XREF_BIBR, XREF_BIBR."
QTCI affects KCNH2
| 1
QTCI inhibits KCNH2. 1 / 1
| 1
reach
"Most QTCI prolonging drugs can inhibit the function of recombinant hERG K+ channels, consequently in vitro hERG assays are used widely as front-line screens in cardiac safety testing of novel chemical entities."
QPCT affects KCNH2
| 1
QPCT activates KCNH2. 1 / 1
| 1
reach
"Having established the possible role of the peripheral QC in glycoside induced hERG PM down-regulation from the PM, we asked whether a similar mechanism might contribute to the loss-of-expression phenotype of G601S and F805C hERG mutants identified in inherited LQT2 syndrome."
Q738X affects KCNH2
| 1
Mutated Q738X activates KCNH2. 1 / 1
| 1
reach
"Western blot analysis and confocal microscopy revealed that the Q738X mutation caused defective trafficking of hERG channel proteins."
Proteasome inhibitors affects KCNH2
| 1
Proteasome inhibitors activates KCNH2. 1 / 1
| 1
reach
"Proteasome inhibitors, N-acetyl-L-leucyl-L-leucyl-L-norleucinal and MG132 prevented the 5alpha-DHT- dependent enhancement of HERG, as did the lysosome inhibitor, bafilomycin A1."
Protease affects KCNH2
| 1
| 1
reach
"To study the cell surface expression of hERG channel proteins, the intact cells transfected with WT hERG or the splice mutant were treated with proteinase K."
Pred-hERG web server affects KCNH2
| 1
Pred-hERG web server inhibits KCNH2. 1 / 1
| 1
reach
"The Pred-hERG web server allows users to identify putative hERG blockers and non blockers through a fast and user-friendly interface."
Pka-R2 affects KCNH2
| 1
Pka-R2 leads to the phosphorylation of KCNH2. 1 / 1
| 1
reach
"Transfection with AKAP-IS, however, resulted in an increase in the amount of back phosphorylation after treatment of cells with CPT-cAMP, indicating that disruption of AKAP and PKA-RII targeting reduced intracellular phosphorylation of HERG."
Phosphatidylinositol4-phosphate 5-kinase affects KCNH2
| 1
Phosphatidylinositol4-phosphate 5-kinase activates KCNH2. 1 / 1
| 1
reach
"Phosphatidylinositol4-phosphate 5-kinase prevents the decrease in the HERG potassium current induced by Gq protein coupled receptor stimulation."
Peimine affects KCNH2
| 1
Peimine inhibits KCNH2. 1 / 1
| 1
reach
"We found that Peimine inhibited the hERG peak tail currents in a concentration dependent manner with an IC 50 value of 43.7 muM (n = 4) by whole cell patch clamp techniques."
Pal-LPC affects KCNH2
| 1
Pal-LPC activates KCNH2. 1 / 1
| 1
reach
"Bath application of Pal-LPC consistently and reversibly increased HERG current (I (HERG))."
PTPN12 affects KCNH2
| 1
PTPN12 inhibits KCNH2. 1 / 1
| 1
reach
"Overexpression of PTPN12 significantly decreased HERG current density in HEK293 and HERG cells, and this change was significantly weakened in the inhibitor group and herg mutant group."
PTK inhibitor affects KCNH2
| 1
PTK inhibitor activates KCNH2. 1 / 1
| 1
reach
"This observation makes it unlikely that the broad-spectrum PTK inhibitor genistein directly blocks hERG channels."
PPP3 affects KCNH2
| 1
| 1
sparser
"In conclusion, our study demonstrated that clinical dosage of isoflurane blocked fear memory formation partly through CaN/p-ERK/Erg-1 signaling pathway in both hippocampus and amygdala."
PPARD affects KCNH2
| 1
PPARD inhibits KCNH2. 1 / 1
| 1
reach
"By modifying the basicity of the imidazole core, potent and selective PPARdelta modulators that do not inhibit hERG channel were identified."
PMCH affects KCNH2
| 1
PMCH inhibits KCNH2. 1 / 1
| 1
reach
"Biological evaluation confirmed that these new analogs retained MCH R1 activity with greatly attenuated hERG liabilities as indicated in the Rb efflux assay."
PLC affects KCNH2
| 1
PLC inhibits KCNH2. 1 / 1
| 1
reach
"These results suggest that cholesterol enrichment inhibits either endogenous MIC current or exogenous HERG current via the membrane PIP 2 depletion by PLC activation."
PKC Isoforms affects KCNH2
| 1
PKC Isoforms activates KCNH2. 1 / 1
| 1
reach
"Roles of PKC Isoforms in PMA Induced Modulation of the hERG Channel (Kv11.1)."
PKA inhibitor affects KCNH2
| 1
PKA inhibitor activates KCNH2. 1 / 1
| 1
reach
"A PKA inhibitor targeted to the ER surface (termed p4PKIg) completely abolished PKA mediated augmentation of HERG in HEK293 cells as well as rat neonatal cardiomyocytes."
PK-THPP affects KCNH2
| 1
PK-THPP inhibits KCNH2. 1 / 1
| 1
reach
"PK-THPP inhibits TREK-1, Kv1.5, hERG and K ATP potassium channels with IC 50 s (in muM) of> 10, ~ 5,> 15, and> 10, respectively."
PI affects KCNH2
| 1
PI activates KCNH2. 1 / 1
| 1
reach
"A PI pulse to +50 mV was initially applied for 600 ms to fully activate h-erg, which 170 was followed by a P2 pulse to -80 mV for 60 ms to remove inactivation without allowing sufficient time for deactivation to occur."
PDE5 inhibitors affects KCNH2
| 1
PDE5 inhibitors activates KCNH2. 1 / 1
| 1
reach
"Since it is known that current PDE5 inhibitors block hERG1 K channels in concentration dependent manner, the cardiotoxicity prediction of the hit molecules was also tested."
PDE inhibitors affects KCNH2
| 1
PDE inhibitors activates KCNH2. 1 / 1
| 1
reach
"Interestingly, most PDE inhibitors decreases hERG current directly or indirectly while two PDE3 inhibitors (amrinone and milrinone) fail to exhibit any hERG inhibitory effects XREF_BIBR."
PD118057 affects KCNH2
| 1
PD118057 activates KCNH2-E637K. 1 / 1
| 1
reach
"Additionally, our study is the first to demonstrate that PD118057 is unable to rescue the dominant negative suppression of the E637K hERG mutant on WT-hERG channel function."
PAT affects KCNH2
| 1
PAT inhibits KCNH2. 1 / 1
| 1
reach
"In this study, we report that PAT does not block hERG currents on short-term exposure but reduces current density on long-term exposure (IC50, 11.8 microM) and inhibits hERG maturation on Western blots (IC50, 62 microM)."
PAS affects KCNH2
| 1
| 1
reach
"Domiphen bromide, benzethonium chloride, and didecyl dimethylammonium bromide may bind to the PAS domain tightly to interrupt the interactions between PAS and HERG, which may further influence the deactivation behavior of the channel."
PAOX affects KCNH2
| 1
PAOX activates KCNH2. 1 / 1
| 1
reach
"HERG channel current in cells expressing HERG alone (HEK293 and HERG cells), cells overexpressing PTPN12 (HEK293 and HERG cells transfected with pCDNA3.1-PTPN12-RFP), PAO treated cells (PTPN12 and HERG cells treated with PAO), and herg mutant cells (HEK293 and HERGY327A-Y 700A-Y845A cells transfected with pcDNA3.1-PTPN12-RFP) were recorded by patch-clamp technique."
P926AfsX14 affects KCNH2
| 1
Modified P926AfsX14 decreases the amount of KCNH2. 1 / 1
| 1
reach
"13 However, coexpression of P926AfsX14 with a common hERG polymorphism, K897T, led to a significant loss of hERG current, much greater than what was seen with expression of K897T or P926AfsX14 alone."
P7C3-A20 affects KCNH2
| 1
P7C3-A20 inhibits KCNH2. 1 / 1
| 1
reach
"Neither P7C3-A20 nor (-)-P7C3-S243 inhibits the hERG channel or shows toxicity towards cultured human cell lines (IC 50> mu10 M)."
Ondansetron affects KCNH2
| 1
| 1
reach
"Ondansetron (3 microM) also slowed decay of HERG tail currents."
NTRK1 affects KCNH2
1 |
1 |
biogrid
No evidence text available
NS5B inhibitors affects KCNH2
| 1
NS5B inhibitors inhibits KCNH2. 1 / 1
| 1
reach
"By reducing the basicity of the core heterocycle in a series of HCV NS5B inhibitors, the hERG liability was reduced."
NS1643 drug affects KCNH2
| 1
NS1643 drug activates KCNH2. 1 / 1
| 1
reach
"To maximize the effects we decided to use a NS1643 drug concentration of 50muM which corresponds to at least twice the EC 50 value to activate the hERG1 channel."
NRPS3 affects KCNH2
| 1
| 1
sparser
"Despite the many beneficial effects demonstrated in animal models, many alpha7 ligands have also shown a propensity for 5HT3 or hERG interactions, which could lead to unwanted side effects [ xref , xref ]."
NPs affects KCNH2
| 1
NPs activates KCNH2. 1 / 1
| 1
reach
"Real-time PCR analysis showed an increase in the expression of the ERG1 gene in C. albicans cells, which were treated with Te NPs (0.2 mg/mL)."
NOS3 affects KCNH2
| 1
| 1
sparser
"NOS3 rs1800779 and KCNH2 rs3807370 polymorphisms were significantly associated with word pair recognition, but only for dominant models, i.e., when pooling the uncommon genotype with the heterozygote."
NCE affects KCNH2
| 1
NCE inhibits KCNH2. 1 / 1
| 1
reach
"For front-line evaluation of the propensity of a NCE to block hERG, measurements of native I Kr or recombinant hERG channel current (I hERG) are necessary, in line with recommendations in the ICH S7B guidelines (ICH, 2005)."
| 1
reach
"Ceramide modulates HERG potassium channel gating by translocation into lipid rafts."
N-eag-CFP affects KCNH2
| 1
N-eag-CFP activates KCNH2. 1 / 1
| 1
reach
"To further examine the effect of individual S4-S5 linker alanine mutations on channel deactivation, and test whether N-eag-CFP could induce slow deactivation in the hERG Deltaeag [S4-S5] Ala ind mutant channels at different voltages, we measured kinetics of deactivation over a range of potentials using a two-pulse voltage command protocol."
1 |
N-Cap affects KCNH2
| 1
N-Cap activates KCNH2. 1 / 1
| 1
reach
"Moreover, the N-terminal extremity of the channel, called N-Cap, has been suggested to interact with S4-S5 L to modulate channel voltage dependent gating, as N-Cap deletion drastically accelerates hERG channel deactivation."
Mutant MiRP1 subunits affects KCNH2
| 1
Mutant MiRP1 subunits activates KCNH2. 1 / 1
| 1
reach
"Mutant MiRP1 subunits modulate HERG K+ channel gating : a mechanism for pro arrhythmia in long QT syndrome type 6."
Muscarinic receptor affects KCNH2
| 1
Muscarinic receptor increases the amount of KCNH2. 1 / 1
| 1
reach
"Muscarinic receptor activation increases hERG channel expression through phosphorylation of ubiquitin ligase Nedd4-2."
Mitragynine affects KCNH2
| 1
Mitragynine inhibits KCNH2. 1 / 1
| 1
reach
"In summary, our study using transgenic hERG-HEK293 and human cardiomyocytes indicate that Mitragynine and its analogues may induce potentially fatal TdP by suppressing hERG mediated K + currents and prolonging APD."
MirP1 affects KCNH2
| 1
MirP1 activates KCNH2. 1 / 1
| 1
reach
"So far, KCNE2 (MirP1) has only been shown to modulate HERG current."
MicroRNA 362-3p affects KCNH2
| 1
MicroRNA 362-3p inhibits KCNH2. 1 / 1
| 1
reach
"MicroRNA 362-3p Reduces hERG related Current and Inhibits Breast Cancer Cells Proliferation."
MiRP1 mutation affects KCNH2
| 1
MiRP1 mutation activates KCNH2. 1 / 1
| 1
reach
"This first example of a MiRP1 mutation associated with auditory stimulus induced arrhythmia is supportive of the hypothesis that MiRP1 regulates hERG in the human heart."
MiR-96 affects KCNH2
| 1
MiR-96 decreases the amount of KCNH2. 1 / 1
| 1
reach
"MiR-96 suppresses tumorigenicity, metastasis and HERG1 expression in vivo."
MiR-493 affects KCNH2
| 1
MiR-493 activates KCNH2. 1 / 1
| 1
reach
"MiR-493 is downregulated in PC and directly targets hERG1."
Met-Tyr affects KCNH2
| 1
| 1
reach
"potential of 0 mY, 10 pM La3+ reduced HERG current by 92% + 3% (n = 4; Figure 6)."
MMUT affects KCNH2
| 1
| 1
sparser
"Based on observations that gene knockdown levels correlate to protein knockdown (Figure  xref C), statistical modelling fitted to the binomial distribution was used to predict the likelihood of functional hERG tetramer formation following Mut hERG knockdown."
MMP14 affects KCNH2
| 1
MMP14 activates KCNH2. 1 / 1
| 1
reach
"These siRNA pools abrogated the ER-G1-induced increase in gelatin degradation, suggesting that MMP14 is mediating the ER-G1 effect."
MIR23A mRNA affects KCNH2
1 |
Transcriptionally active MIR23A mRNA increases the amount of KCNH2. 1 / 1
1 |
biopax:ctd
No evidence text available
MIR21 mRNA affects KCNH2
1 |
Transcriptionally active MIR21 mRNA increases the amount of KCNH2. 1 / 1
1 |
biopax:ctd
No evidence text available
MC450 affects KCNH2
| 1
MC450 activates KCNH2. 1 / 1
| 1
reach
"Using patch-clamp recordings, we found that MC450 increased the activation current of hERG channel, with an EC 50 of 41 +/-4muM."
MAPK1 affects KCNH2
| 1
MAPK1 increases the amount of KCNH2. 1 / 1
| 1
reach
"Interestingly, Erk2 inhibition induced the strongest disruption of Erg1 expression."
MAPK affects KCNH2
| 1
MAPK inhibits KCNH2. 1 / 1
| 1
reach
"Pitavastatin suppresses mitogen activated protein kinase mediated Erg-1 induction in human vascular smooth muscle cells."
M3D-arr affects KCNH2
| 1
M3D-arr increases the amount of KCNH2. 1 / 1
| 1
reach
"By exclusively activating M3D-arr using the otherwise inert compound, clozapine-N-oxide, we found that M3D-arr activation increased mature hERG expression and current."
M3-mAChR affects KCNH2
| 1
M3-mAChR activates mutated KCNH2. 1 / 1
| 1
reach
"M3-mAChR activation leads to enhancement of hsp expression via PKC dependent phosphorylation of HSF1, thereby stabilizing the mutant hERG FLAG protein."
Lys-Phe affects KCNH2
| 1
Lys-Phe activates KCNH2. 1 / 1
| 1
reach
"In this study we show that (1) the biophysical and pharmacological properties of hERG current recorded with KF are similar to those with standard potassium chloride solutions, (2) use of KF significantly improves the success rate of hERG screening using PatchXpress without compromising data quality, and (3) utilization of KF can significantly increase the throughput of hERG screening with PatchXpress."
Lindera erythrocarpa affects KCNH2
| 1
Lindera erythrocarpa inhibits KCNH2. 1 / 1
| 1
reach
"Our findings suggest that Lindera erythrocarpa, a traditional medicine, blocks HERG channel, which could contribute to its anticancer and cardiac arrhythmogenic effect."
LY 364947 affects KCNH2
| 1
LY 364947 decreases the amount of KCNH2. 1 / 1
| 1
reach
"Finally, in vivo administration of LY364947, a pharmacological antagonist of TGF-beta signalling, dramatically prevented interstitial fibrosis and LQTS and abolished aberrant expression of TGF-beta1, HERG, and Kir2.1 in ATO treated guinea pigs."
LQTS2 affects KCNH2
| 1
LQTS2 activates KCNH2. 1 / 1
| 1
reach
"In particular, the correction of the trafficking of KCNH2 (LQTS2) potassium channel through intracellular mechanisms restored hERG currents and reduced arrhythmia in LQTS2 patient derived cardiomyocytes, also documenting the usefulness of iPSC-cardiomyocytes in LQTS2 modeling and drug testing."
LQTS mutations affects KCNH2
| 1
LQTS mutations inhibits KCNH2. 1 / 1
| 1
reach
"Mutations in the intrinsic ligand affected hERG channel gating and LQTS mutations abolished hERG currents and altered trafficking of hERG channels, which explains the LQT phenotype."
LQTS affects KCNH2
| 1
LQTS bound to KCNE2 inhibits KCNH2. 1 / 1
| 1
reach
"Importantly, inherited gene variants in human KCNE2 that are associated with LQTS impair hERG gating, which would be predicted to delay ventricular repolarization as is seen in LQTS."
LQT-2 affects KCNH2
| 1
Mutated LQT-2 activates KCNH2. 1 / 1
| 1
reach
"We used electrophysiological, biochemical, and immunohistochemical methods to study the molecular mechanisms of HERG channel dysfunction caused by LQT-2 mutations."
LQT affects KCNH2
| 1
KCNH2 binds LQT. 1 / 1
| 1
reach
"Three HERG Point Mutations Associated with LQT To identify additional HERG mutations in LQT2, we contin- ued SSCP analyses in linked kindreds and sporadic cases."
LOF affects KCNH2
| 1
LOF inhibits KCNH2. 1 / 1
| 1
reach
"LQT2 is caused by loss of function (LOF) mutations in KCNH2 (also known as the human Ether-a-go-go-Related Gene or hERG)."
LGI1 affects KCNH2
| 1
LGI1 increases the amount of KCNH2. 1 / 1
| 1
reach
"The production of EPT by the transgenic tri4 strain raised levels of erg1 expression and reduced squalene accumulation while not affecting levels of ergosterol."
L affects KCNH2
| 1
L decreases the amount of KCNH2. 1 / 1
| 1
reach
"As shown in Fig. 4 A, DPI, which interferes with FAD binding to the oxidase, modestly decreased hERG expression under normoxic conditions and most importantly was ineffective in restoring hERG down-regulation by hypoxia."
Kv7.1 affects KCNH2
| 1
Kv7.1 inhibits KCNH2. 1 / 1
| 1
reach
"Trafficking deficiency of the alpha subunit of Kv7.1 can, in some cases such as the KCNQ1-T587M, a known trafficking mutation that caused haploinsufficiency, reduce localization of KCNH2 (HERG) to the cell membrane [XREF_BIBR]."
KN-93 affects KCNH2
| 1
KN-93 inhibits KCNH2. 1 / 1
| 1
reach
"Model studies reproduced this feature in studies of hERG blockers such as dofetilide, KN-93 and other common high-affinity blockers (Durdagi etal."
KMS88009 affects KCNH2
| 1
KMS88009 inhibits KCNH2. 1 / 1
| 1
reach
"We found that KMS88009 weakly inhibited the hERG potassium channel (IC 50 = 52.14 microM) (XREF_SUPPLEMENTARY) and was well tolerated with no side effects after single and 2-week repeated administration in rats (XREF_SUPPLEMENTARY)."
KL affects KCNH2
| 1 1
KL activates KCNH2. 1 / 1
| 1 1
reach
"Coexpression of klotho increased cell membrane hERG protein abundance and hERG current at any given voltage without significantly modifying the voltage required to activate the channel."
KIOM-79 affects KCNH2
| 1
KIOM-79 activates KCNH2. 1 / 1
| 1
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"However, as was found in the AP measurement and also in the computer simulation, the moderate changes of hERG current induced by KIOM-79 is reflected as only weak changes of AP."
KDR affects KCNH2
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KDR activates KCNH2. 1 / 1
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"VEGFR-2 activation increased cell proliferation and survival via multiple pathways by upregulating Erg-1 and cJun transcription factors and downregulating thrombospondin-1 (TSP-1) on mRNA and protein levels [XREF_BIBR]."
KCNQ1-T587M affects KCNH2
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KCNH2 binds KCNQ1-T587M. 1 / 1
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"Consistent with this result, FRET experiments demonstrated that both KCNQ1-WT and -R259C interacted with hERG in the cytosol and on the plasma membrane; however, the interaction between KCNQ1-T587M and hERG was observed only in the cytosol, and hERG proteins were seldom transported to the cell membrane, suggesting that the KCNQ1 T587M mutation impaired the trafficking of hERG to the cell membrane."
KCNH2 affects zELKDelta740-742 channels
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KCNH2 activates zELKDelta740-742 channels. 1 / 1
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"This difference might partially explain why the hERG1 peptide is unable to modulate zELKDelta740-742 channels."
KCNH2 affects voltage-
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KCNH2 activates voltage-. 1 / 1
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"Sin- gle-channel analysis of expressed HERG will enable a more detailed description of voltage- dependent gating and the mechanism of negative conductance of the I-V rela- tionship."
KCNH2 affects vascular endothelial growth factor receptor-1-dependent
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KCNH2 activates vascular endothelial growth factor receptor-1-dependent. 1 / 1
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"For instance, in human acute myeloid leukemia cells, hERG1 channels appear to mediate the vascular endothelial growth factor receptor-1-dependent cell migration and invasion, both in vitro and in vivo."
KCNH2 affects vandetanib
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"The binding of vandetanib to hERG channel is further stabilized by T shaped pi-pi interactions with F656."
KCNH2 affects unfolded protein response
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KCNH2 activates unfolded protein response. 1 / 1
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"Indeed, it has been demonstrated that hERG trafficking mutants activate the unfolded protein response (UPR), an ER stress pathway associated with numerous disease states [ xref ]."
KCNH2 affects type-2 long QT syndrome [
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KCNH2 activates type-2 long QT syndrome [. 1 / 1
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"Mutations in several ion channel genes are known to cause this disorder XREF_BIBR, mutations in the KCNQ1 gene causing type-1 long QT syndrome [XREF_BIBR, XREF_BIBR] and in the human ether-a-go-go-related gene (HERG) causing type-2 long QT syndrome [XREF_BIBR]."
KCNH2 affects type II hereditary long QT syndrome
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Mutated KCNH2 activates type II hereditary long QT syndrome. 1 / 1
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"Mutations of the HERG gene can cause type II hereditary long QT syndrome (LQT2), characterized by prolongation of the QT interval, abnormal T wave, torsade de pointes, syncope and sudden cardiac death."
KCNH2 affects type 2 long QT (LQT2) [
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KCNH2 activates type 2 long QT (LQT2) [. 1 / 1
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"Among some 200 hereditary mutations in KCNH2 that cause type 2 long QT (LQT2) [XREF_BIBR], about 67% are missense alterations, the majority of which cause trafficking defects; that is, an overall reduction of cell surface hERG protein [XREF_BIBR]."
KCNH2 affects type 2 Long QT syndrome
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KCNH2 activates type 2 Long QT syndrome. 1 / 1
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"Similarly, abnormal splicing of KCNH2, resulting from intronic branch point [XREF_BIBR] or 5 ' splice site [XREF_BIBR] mutations, impairs the functioning of the resulting HERG encoded I Kr channels, causing type 2 Long QT syndrome (LQT2)."
KCNH2 affects twi
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"In LQT2 patients (n = 16) occurrence of CE (n = 6) was also associated with a lower TWI (7.8±15.4 vs. 43.3±23.4 mV*ms, p = 0.007), a significantly lower QRSTI (29.5±23.8 vs. 83.3±34.6 mV*ms, p = 0.006) and a significantly lower T-wave amplitude in this particular area (0.08±0.04 vs. 0.2±0.14 mV, p = 0.03)."
KCNH2 affects translation
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"In the hERG-Lite assay 47, amiodarone inhibits hERG surface expression which may result from impaired forward or enhanced backward trafficking or translation interference."
KCNH2 affects toxin
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KCNH2 activates toxin. 1 / 1
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"We suggest this reflects destabilization of the outer pore (turret region) of hERG allowing access of the toxin molecule to directly plug the conduction pathway."
KCNH2 affects sw
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"KCNH2 was significantly associated with SW modulation."
KCNH2 affects stress-activated chaperone Sigma 1 receptor
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KCNH2 binds stress-activated chaperone Sigma 1 receptor. 1 / 1
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"HERG channel protein maturation, stability, and current density can be enhanced by the stress activated chaperone Sigma 1 receptor, which physically associates with HERG and represents a novel pharmacological target in a membrane signaling channel macrocomplex that is involved in cancer progression."
KCNH2 affects sqt-3
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KCNH2 activates sqt-3. 1 / 1
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"SQTS has been associated with the gain-of-function mutations in 3 distinct potassium channels, KCNH2, KCNQ1 and KCNJ2, which cause SQT1, SQT2 and SQT3, respectively [111-114]."
KCNH2 affects sotalol
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"Cellular expression studies showed that the N588K mutation in KCNH2 in these patients reduced binding of sotalol to the I kr channel [XREF_BIBR]."
KCNH2 affects sodium(1+)
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"Moreover, the KCNH2 potassium channels may directly regulate the characteristics of sodium and calcium channels XREF_BIBR."
KCNH2 affects snail
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KCNH2 decreases the amount of snail. 1 / 1
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"Our data revealed that NF-kappaB siRNA almost completely abolished PDGF induced snail expression, while Erg-1 siRNA only slightly attenuated snail expression, suggesting that NF-kappaB is critical for PDGF-AB-induced snail expression."
KCNH2 affects sigma-1 receptors
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KCNH2 binds sigma-1 receptors. 1 / 1
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"The distribution of angles between pairs of sigma-1 receptors bound to hERG tetramers had two peaks, at ~ 90 and ~ 180degrees in a ratio of ~ 2:1, indicating that the sigma-1 receptor interacts with hERG with 4-fold symmetry."
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"Using the whole-cell patch-clamp technique, interaction between rosiglitazone and HERG in HEK293 cells was studied."
KCNH2 affects rectifier K channels
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KCNH2 activates rectifier K channels. 1 / 1
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"In addition, both sodium voltage gated channel alpha subunit 5 (SCN5A), voltage gated sodium channels and potassium voltage gated channel subfamily H member 2 (KCNH2), rapidly activating delayed rectifier K channels, which are critical for cardiac depolarization and repolarization [XREF_BIBR], have PY-motif in their C-terminal that Nedd4-2 interact with [XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR]."
KCNH2 affects rMiRP1
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KCNH2 binds rMiRP1. 1 / 1
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"However, under these in vitro conditions, the presence of both peptides favored formation of stable rMiRP1 and HERG complexes in preference to those with rMinK.Based on the presumed molecular correlation of MiRP1 and HERG channel complexes and native cardiac I Kr channels, we cloned the gene for human MiRP1 (hKCNE2) to screen for the presence of mutations in patients with cardiac arrhythmias."
KCNH2 affects rMiRP
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KCNH2 binds rMiRP. 1 / 1
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"Subunit interaction between rMiRP and HERG was evaluated first by studying the proteins modified with epitope tags and expressed in mammalian tissue culture cells."
KCNH2 affects rEag1 K
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KCNH2 activates rEag1 K. 1 / 1
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"A common structural feature shared by our three inactivating rEag1 mutant constructs is the lack of the rEag1 eag domain, which implies that the rEag1 eag domain, but not the hERG1 eag domain, may somehow modulate an inherent voltage dependent inactivation of rEag1 K + channels."
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Ubiquitinated KCNH2-F805C decreases the amount of pyridoxamine. 1 / 1
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"For comparison, we also determined the ubiquitination of the F805C hERG, which exhibits more severe ER retention and diminished PM expression than G601S hERG."
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"Computer simulation of HERG blocking by protriptyline suggested that protriptyline binds the HERG channel at the internal chamber and makes a hydrogen bond to the carbonyl oxygen of Leu622."
KCNH2 affects primer 5'-ggaattc catatg gaattgtacatctgcgctccagc-3'
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KCNH2 inhibits primer 5'-ggaattc catatg gaattgtacatctgcgctccagc-3'. 1 / 1
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"Normal and mutated (T1945 +6 C change) sequences of the KCNH2 gene were amplified from genomic deoxyribonucleic acid of an individual heterozygous for the mutation using forward primer 5 '-ggaattc catatg gaatcactgcacctgtcagtgc-3 ' and reverse primer 5 '-ggaattc catatg gaattgtacatctgcgctccagc-3 '."
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"mRNA levels of the KCNH2 unit of the rapidly (I Kr) activating delayed rectifier potassium channel and KCNQ1/2 [(two members of the potassium voltage gated channel subfamily Q of the slowly (I Ks) activating delayed rectifier potassium channels)] were differentially regulated when hPSCs-CLCs were cultured on matrigel or vdECMs conditions."
KCNH2 affects polymorphism
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KCNH2 binds polymorphism. 1 / 1
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"Our studies demonstrate a primary LQT-3 (Na + channel) defect not influenced by the KCNH2 polymorphism and drug interactions unique to the proband that correlate with improved management of arrhythmias in the patient and provide support for this approach in developing patient-specific clinical regimens."
KCNH2 affects pimozide
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"Although the quantitative characteristics are very close, the three neuroleptics may be placed in the following order of HERG blocking potency : haloperidol> = pimozide> fluspirilene."
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"Due to its fundamental role in controlling repolarisation of the ventricular action potential, hERG channel block leads to a lengthening of the Action Potential Duration (APD) of a single cell, manifested as QT prolongation on the ECG."
KCNH2 affects pdaC
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KCNH2 activates pdaC. 1 / 1
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"For example, hERG1 potassium channels have been shown to drive PDAC tumor malignancy [XREF_BIBR], the neurotransmitter GABA was identified as a promising agent for the prevention of PDAC in individuals at risk due to chronic alcohol consumption [XREF_BIBR], the transient receptor potential melastatin related 7 channel was found to regulate tumor migration [XREF_BIBR], the store operated calcium channels (SOCs) were shown to contribute to PDAC apoptosis resistance [XREF_BIBR] while the P2x7 receptor regulates cell survival, migration and invasion [XREF_BIBR]."
KCNH2 affects pT37
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KCNH2 leads to the phosphorylation of pT37. 1 / 1
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"The up-regulation of HIF-1alpha did not depend on the regulation of HIF protein synthesis by mTORC1 and mTORC2 complex XREF_BIBR, as neither inhibition or silencing of hERG1 decreased p70S6K or pT37 phosphorylation (XREF_FIG)."
KCNH2 affects p21waf
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KCNH2 increases the amount of p21waf. 1 / 1
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"HERG1 and Kv11.1 activation stimulates transcription of p21waf and cip in breast cancer cells via a calcineurin dependent mechanism."
KCNH2 affects olanzapine
| 1
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"The hERG blocking liability of olanzapine was confirmed to be theoretically low also in the context of pharmacokinetic data such as myocardial distribution [XREF_BIBR]."
KCNH2 affects nifekalant
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KCNH2 binds nifekalant. 1 / 1
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"These findings suggest that nifekalant binds to HERG channels that are in the open state.The magnitude of HERG current inhibition by nifekalant decreased at more depolarizing potentials, where the fraction of the inactivated HERG channels increased."
KCNH2 affects nicorandil
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"Preliminary results indicate that the hERG blocker E-4031 can stimulate irregular, arrhythmic beating patterns in the cardiomyocytes from both species, and that immediate subsequent treatment with the hERG enhancer nicorandil can rescue these back to regular beating patterns, similar to those observed when the cells were untreated."
KCNH2 affects mutant Kv11.1 alpha-subunits
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Mutated KCNH2 activates mutant Kv11.1 alpha-subunits. 1 / 1
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"[XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR] While the majority of LQT1-causative KCNQ1 mutations appear to form functional Kv7.1 alpha-subunits capable of co-assembling with wild-type Kv7.1 alpha-subunits and thereby exerting a dominant negative effect on the I Ks current (> = 50% reduction), the majority of LQT2-causative KCNH2 mutations produce mutant Kv11.1 alpha-subunits that are improperly folded, retained in the endoplasmic reticulum, or otherwise fail to make it to the cell surface resulting in haploinsufficiency and < = 50% reduction in the I Kr current."
KCNH2 affects motility
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KCNH2 inhibits motility. 1 / 1
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"In order to determine the mechanism by which Kv11.1 inhibits cancer cell motility, we pursued the regulation of EMT."
KCNH2 affects miR-493
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KCNH2 binds miR-493. 1 / 1
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"Then we conducted luciferase assay to investigate the direct interaction between miR-493 and hERG1."
KCNH2 affects miR-141
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KCNH2 increases the amount of miR-141. 1 / 1
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"Ho and collaborators have shown by Chromatin ImmunoPrecipitation (ChIP) assays that the early growth response 1 (ERG1) transcription factor, which is induced upon infection, enhances miR-141 expression leading to the silencing of eIF4E, promotion of translational switch and increased viral production."
KCNH2 affects mexiletine
| 1
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"For the dosage required for therapeutic block of the I NaL in the proband, concomitant block of hERG limits the ability of mexiletine to fully correct the repolarization defect."
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"In this review we discuss the utility of protein-structure-based design and docking approaches aimed at overcoming issues related to plasma protein binding, active transport via P-glycoprotein, hERG channel mediated cardiotoxicity and cytochrome P450 inhibition, metabolism and induction."
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"Although these drugs are associated with a higher risk for QT prolongation, the literature is poor regarding their respective effects on cardiac ion currents in relation to their chemical structure and no clear structure activity relationships related to a risk of I hERG inhibition have yet been elucidated.The purpose of the present study was to assess the proarrhythmic potential and the structure activity relationships with regard to I hERG inhibition of the antimalarial drugs lumefantrine, desbutyl-lumefantrine in comparison with halofantrine, chloroquine and mefloquine."
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"C unbound plasma concentration E maximal hERG mediated QT prolongation f fraction unbound hERGhuman ether-a-go-go-related gene I repolarizing potassium current mediated by the delayed rectifier potassium channel K receptor affinity Lligand LRligand and receptor complex (receptor occupancy) LR ligand and receptor complex concentration leading to half-maximal system effect NONMEMnonlinear mixed effect modeling QTcQT interval corrected for heart rate and circadian variation DeltaQTcdrug induced QTc prolongation R receptor density gammaslope (sigmodicity) of transducer function DeltaOFVdifference in NONMEM objective function value tautransducer ratio f relative transducer ratio Introduction."
KCNH2 affects lanosterol
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"The overexpression of the gene ERG1 (squalene epoxidase) induced a significant decrease of the direct substrate squalene, a high increase of lanosterol, and a small increase of later sterols."
KCNH2 affects ixazomib
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"Nonclinical studies assessed (1) the in vitro binding of ixazomib to the hERG channel and (2) its effect on QT/QTc in dogs (N = 4) via telemetry."
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"42 The modest effect of the hERG S624A mutation (XREF_FIG) and lack of close proximity of the drug to S624 in docking simulations (XREF_FIG) are consistent with an indirect role for this residue in ivabradine binding to hERG."
KCNH2 affects hsps
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KCNH2 activates hsps. 1 / 1
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"However, tolerance to heat and ethanol was consistently lower in the erg1 -disruptant cells supplemented with low as compared to high levels of ergosterol.In summary, the current study demonstrated that while the stress response was not compromised in the erg1 -disruptant cells as judged by the ability of cells to synthesise trehalose and hsps under heat shock conditions, these parameters did not closely relate to stress tolerance."
KCNH2 affects hexadecane
| 1
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"Although it might seem intuitively obvious that mutations in KCNH2 might cause CNS disorders, it was not until very recently that a clear link was made between hERG1 mutations and epilepsy."
KCNH2 affects heat shock protein 70
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KCNH2 binds heat shock protein 70. 1 / 1
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"We found that rosuvastatin reduces the interaction of heat shock protein 70 (Hsp70) with the hERG protein, thereby affecting the folding of the hERG channel."
KCNH2 affects hKCNE4
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KCNH2 binds hKCNE4. 1 / 1
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"In order to determine if hKCNE4 can interact with HERG and KCNQ1, similar to other KCNE subunits we coexpressed hKCNE1 with wild type (WT) KCNQ1 and with HERG in Xenopus oocytes and CHO cells.Cotransfection of hKCNE4 with WT-HERG did not modify the properties of WT-HERG channel mediated currents."
KCNH2 affects hERG1a USO to homomeric hERG1a
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KCNH2 activates hERG1a USO to homomeric hERG1a. 1 / 1
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"The co-expression of differentially tagged hERG1 isoforms using the Flp-Cre system allowed us to directly compare the assembly of hERG1a and hERG1a USO to homomeric hERG1a and heteromeric hERG1a and hERGb channels."
KCNH2 affects fluconazole
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Mutated KCNH2 activates fluconazole. 1 / 1
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"Each of these genes are linked to drug resistance or the oxidative stress response; for example, ERG1 mutants have increased fluconazole susceptibility in Candida glabrata, ERG25 has a moderate susceptibility to hypoxia and the endoplasmic reticulum (ER) stress inducing agent dithiothreitol (DTT) in Aspergillus fumigatus, and SRE1 is required for hypoxic induction of genes coding for oxygen dependent enzymes involved in ergosterol synthesis in C. neoformans."
KCNH2 affects flag
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KCNH2 inhibits flag. 1 / 1
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"Inhibition of hERG and Kv1.5 channels could raise a flag of potential cardiac safety concern for this compound."
KCNH2 affects fatal pathologies
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KCNH2 inhibits fatal pathologies. 1 / 1
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"HERG inhibition can lead to fatal pathologies such as cardiac diseases , and this is the principal cause of the development of acquiring long QT syndrome and fatal arrhythmia [ 97 ] ."
KCNH2 affects ether-a-go-go-related gene
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KCNH2 activates ether-a-go-go-related gene. 1 / 1
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"Recent in vitro studies have indicated that probucol reduces hERG expression in the plasma membrane and does not directly block human ether-a-go-go-related gene (hERG) channels."
KCNH2 affects ether-a-go-go related gene
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KCNH2 activates ether-a-go-go related gene. 1 / 1
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"101 Type 2 LQTS (LQT2) is the second most common LQTS following LQT1 characterized by mutations in the KCNH2 gene that lead to disruption of the human ether-a-go-go related gene (hERG) potassium channel and consequent reduction in the rapidly activating delayed rectifier potassium current (I ks)."
KCNH2 affects ether-A -go-go- related gene
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KCNH2 activates ether-A -go-go- related gene. 1 / 1
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"LQTS2 is caused by mutations in the KCNH2 gene, encoding the alpha subunit of the human ether-A -go-go - related gene (hERG) potassium channel underlying the rapidly activating delayed rectifier K + current (I Kr)."
KCNH2 affects endocytosis
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"Cell surface expression and degradation of HERG is also controlled by caveolin-3 via a complex of these two proteins with the Nedd4-2 ubiquitin ligase and via dynamin mediated endocytosis."
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"8 Data for guinea pig DSM, 26 along with data from our group for rat DSM (G. V. Petkov, unpublished data), show that E4031, a specific inhibitor of the Kv11.1 channel (also known as ERG1, hERG, or KCNH2), increases DSM contractility, indicating a functional role for this K + channel."
KCNH2 affects core protein monomers
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KCNH2 leads to the glycosylation of core protein monomers. 1 / 1
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"HERG mRNA synthesizes a protein monomer and core glycosylation (immature HERG protein showed the 135 kDa bands in Western blot) and core protein monomers into a dimer of four Ikr channels at the ER ribosome, which were transported to the Golgi complex of glycosylation (mature HERG protein showed the 155 kDa bands in Western blot)."
KCNH2 affects copper(2+)
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"Furthermore the enhancement of HERG outward K current, induced by ROS, was prevented by the presence of a ROS scavenging mixture containing Cu, Zn SOD [22]."
KCNH2 affects conotoxin
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"The docking studies suggest that the conotoxin binds stably to the HERG protein."
KCNH2 affects comCA
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"SQTS has been associated with mutations in six genes ( KCNQ1, KCNH2, KCNJ2, CACNA1C, CACNB2 , and CACNA2D1 ) with GOF mutations in KCNH2 (SQTS1) being the most prevalent subtype xref , xref ."
KCNH2 affects class 2 LQT2 channel proteins
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KCNH2 activates class 2 LQT2 channel proteins. 1 / 1
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"Drugs that associate with pore-S6 intracellular drug binding domain of KCNH2 channel proteins to cause high-affinity block of I (KCNH2) also can increase the processing of class 2 LQT2 channel proteins through the secretory pathway."
KCNH2 affects clamp
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KCNH2 activates clamp. 1 / 1
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"Our data showed that unbound ICA-105574 caused QT shortening in dogs at concentrations comparable to the half maximal effective concentration (EC (50), 0.42 microM) of hERG activation in the patch clamp studies."
KCNH2 affects cholesterol
| 1
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"Depleting cholesterol concentration in cardiomyocytes by administration of probucol, a cholesterol synthesis inhibitor, interrupts cholesterol and caveolin -1 interaction in the plasma membrane, leading to accelerated degradation of human ether related gogo (hERG) channels, thereby prolonging action potential duration."
KCNH2 affects chloroquine
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KCNH2-F656A activates chloroquine. 1 / 1
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"Thus, Cavalli-2 should be a useful probe of the spatial configuration of drug binding groups, especially the aromatic side chains of Tyr 652 and Phe 656; substantial interactions with multiple (at least two) Phe 656 side chains seem to be required to understand the large attenuations of block seen with several high-affinity blockers, including flecainide, Cavalli-2 (this study), E-4031, and cisapride in hERG F656A overexpressing mammalian cells and MK-499, cisapride, chloroquine, and clofilium in hERG F656A overexpressing oocytes."
KCNH2 affects channel protein
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KCNH2 leads to the phosphorylation of channel protein. 1 / 1
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"Previous studies have revealed that activation of the beta-adrenergic system and consecutive elevation of the intracellular cAMP concentration regulate HERG channels via protein kinase A mediated phosphorylation of the channel protein and via direct interaction with the cAMP binding site of HERG."
KCNH2 affects channel
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KCNH2 inhibits channel. 1 / 1
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"In contrast with findings described by others (Matsa etal, 2011), hERG modulation by LUF7346 completely reversed the severe effects of the potassium channel blocker AST in LQT2 N996I hiPSC-CMs, confirming the efficacy of LUF7346 compared to other molecules reported so far in the literature."
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"Accumulating evidence suggests that most disease related hERG mutations reduce the function of the channel by disrupting protein biogenesis of the channel in the endoplasmic reticulum (ER)."
KCNH2 affects cells.SDF-1
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KCNH2 activates cells.SDF-1. 1 / 1
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"In conclusion, our data showed a trend of correlation between the function of hERG1 expressed and the invasion potential in HEK293T, suggesting that the function of hERG1 K + channels could somehow modulate the invasive capacity of cells.SDF-1 may also function as paracrine growth factor and support the survival of leukemic cells [5]."
KCNH2 affects cell proliferation
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KCNH2 activates cell proliferation. 1 / 1
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"re, we show that HERG conductance markedly promotes H2O2-induced apoptosis of various tumor cells, whereas HERG expression facilitates the tumor cell proliferation caused by tumor necrosis factor (TNF) ligand (TNF-alpha)."
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"K V 11.1 (hERG1) Channels in Leukemic Cells Mediate Cell Interaction with MSCs."
KCNH2 affects casE
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"However, this is not the case, and KCNH2 mutations have only rarely been associated with drug-induced LQTS."
KCNH2 affects cardiac rapid delayed rectifier K(+) current
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KCNH2 activates cardiac rapid delayed rectifier K(+) current. 1 / 1
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"Potassium channels encoded by human ether-a-go-go-related gene (hERG) mediate the cardiac rapid delayed rectifier K (+) current (IKr), which participates in ventricular repolarization and has a protective role against unwanted premature stimuli late in repolarization and early in diastole."
KCNH2 affects cardiac delayed rectifier K
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KCNH2 activates cardiac delayed rectifier K. 1 / 1
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"The hERG (or " Kv11.1 ") potassium channel (encoded by human Ether-a-go-go Related Gene; alternative nomenclature KCNH2) mediates the rapid component of cardiac delayed rectifier K + current (also known as I Kr)."
KCNH2 affects cardiac arrhythmia
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KCNH2 activates cardiac arrhythmia. 1 / 1
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"By contrast, human Erg (hERG1) K + channels play a critical role in the membrane repolarization of heart muscles and have been clearly associated with both the inherited and the drug induced forms of cardiac arrhythmia XREF_BIBR, XREF_BIBR, XREF_BIBR."
KCNH2 affects caffeine
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KCNH2-F656A activates caffeine. 1 / 1
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"Furthermore, caffeine inhibition is greatly reduced by the pore mutants Y562A and F656A hERG, which disrupt block of most previously tested hERG antagonists."
| 1
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"This indicates that 200 μ M approaches a threshold concentration beyond which Cd 2+ affected HERG activation gating."
KCNH2 affects branch
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KCNH2 activates branch. 1 / 1
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"In a tree including the whole family (XREF_FIG), the ERG1 homologues of the four sterol producing bacteria branch basally, but do not appear to be more closely related to eukaryotic ERG1 than they are to the other bacterial monooxygenases, and they share no specific sequence signature with eukaryotic ERG1 (XREF_FIG)."
KCNH2 affects beta1 integrins
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KCNH2 binds beta1 integrins. 1 / 1
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"More recently it was also shown that hERG1 interaction with beta1 integrins mediates BC metastatization in immunodeficient mice [XREF_BIBR]."
KCNH2 affects beta(1) integrins
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KCNH2 binds beta(1) integrins. 1 / 1
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"On the whole, these data indicate that the hERG1 protein associates with beta (1) integrins and modulates adhesion receptor signaling."
KCNH2 affects betA1
| 1
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"Hence, both an activated integrin and a functional channel are required for the hERG1 and beta 1 complex formation (see the cartoon bottom right in XREF_FIG)."
KCNH2 affects ayr1
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"We have reported for the first time that KCNH2 (1956, C>T) polymorphism is associated with efficacy of antihypertensive drugs CCBs and ADR blockers, and may serve as a novel biomarker for individualized therapy for certain antihypertensive drugs."
KCNH2 affects antagonist
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"The in vitro ADMET properties —microsomal metabolism, CYP2D6 inhibition, HSA binding, cell permeability, and hERG inhibition— of the 5-HT 6 R antagonist newly identified herein 7 excluded important pharmacokinetic issues and possible lethal side effects related with cardiac toxicity (see Results section)."
| 1
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"HERG1 channels modulate integrin signaling to trigger angiogenesis and tumor progression in colorectal cancer."
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sparser
"Tetrasubstituted pyridines as potent and selective AKT inhibitors: Reduced CYP450 and hERG inhibition of aminopyridines."
| 1
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"Overall, these data confirm the hypothesis that hERG1 modulates the autophagic flux in AL cells, and that pharmacologically blocking the channel triggers autophagy, but blocks the autophagic flux, thus inducing both autophagic and apoptotic cell death, in analogy to MAs."
KCNH2 affects alpha-KTx 15 peptides
| 1
KCNH2 inhibits alpha-KTx 15 peptides. 1 / 1
| 1
reach
"After several point mutations in AmmTX3 and introduction of positive charged residues in Discrepin, it was finally demonstrated that a common " hot spot " composed of two basic residues (Arg 18 and Lys 19 near the end of the alpha-helix) conferred hERG blockade activity of alpha-KTx 15 peptides [XREF_BIBR]."
| 1
reach
"However, tolerance to heat and ethanol was consistently lower in the erg1 -disruptant cells supplemented with low as compared to high levels of ergosterol.In summary, the current study demonstrated that while the stress response was not compromised in the erg1 -disruptant cells as judged by the ability of cells to synthesise trehalose and hsps under heat shock conditions, these parameters did not closely relate to stress tolerance."
KCNH2 affects ZNF365
| 1
KCNH2 activates ZNF365. 1 / 1
| 1
reach
"[XREF_BIBR - XREF_BIBR] Similar scenarios could also be seen in cases of acquired long QT syndrome and ischemic cardiomyopathy, in which rare variants (KCNH2, KCNE1, KCNE2, KCNQ2, SCN5A, and RyR2 in drug induced long QT syndrome and CASQ2, RAB3GAP1, ZNF365, CXADR, GPC5, GPD1L, NOS1AP, and SCN5A in ischemic cardiomyopathy) were associated with higher risk of malignant arrhythmia and SCD."
KCNH2 affects YWHAH
1 |
1 |
hprd
No evidence text available
KCNH2 affects XPNPEP2
| 1
| 1
sparser
"Similar to Kv1.5, the mature membrane-bound (155 kDa) form of hERG was selectively cleaved by PK."
KCNH2 affects WW
| 1
| 1
sparser
"It is possible that several PY motifs of hERG1 interact with several WW domains of Nedd4-2 simultaneously."
KCNH2 affects WT I
| 1
KCNH2 activates WT I. 1 / 1
| 1
reach
"Two S6 domain mutants, F652A and Y656A, attenuated IM induced inhibition of WT I (HERG)."
KCNH2 affects VT/VF (+)
| 1
KCNH2 activates VT/VF (+). 1 / 1
| 1
reach
"KCNH2 tail currents were similar in the control and VT/VF (-) group but were significantly increased in the VT/VF (+) group (P < 0.05 : VT/VF (+) vs. control and VT/VF (-)) (XREF_FIG)."
KCNH2 affects VEGF-1
| 1
KCNH2 activates VEGF-1. 1 / 1
| 1
reach
"Furthermore, hERG1 modulates VEGF-1 secretion through an AKT dependent pathway [XREF_BIBR, XREF_BIBR]."
KCNH2 affects VCL
| 1
KCNH2 activates VCL. 1 / 1
| 1
reach
"After hERG current was activated with a conditioning pulse of 2 s duration at + 40 mV, we applied a test pulse at voltages from - 120 mV to + 20 mV in + 10 mV increments."
KCNH2 affects Type 2 LQTS
| 1
KCNH2 activates Type 2 LQTS. 1 / 1
| 1
reach
"Type 2 LQTS (LQT2) is the second most common subtype of LQTS and caused by mutations in KCNH2 gene."
KCNH2 affects TRIOBP-1
| 1
KCNH2 binds TRIOBP-1. 1 / 1
| 1
reach
"These findings establish that TRIOBP-1 interacts directly with hERG and can affect protein levels, I Kr magnitude, and cardiac membrane excitability."
KCNH2 affects TNF
| 1
KCNH2 activates TNF. 1 / 1
| 1
reach
"In hERG positive SKBr3, SH-SY5Y, and HL-1 cells, apoptosis occurs via a caspase 3 dependent pathway in response to extracellular administration of H 2 O 2 or TNFalpha (tumor necrosis factor alpha), whereas selective inhibition of hERG conductance by dofetilide attenuates the proapoptotic effect of H 2 O 2 and TNFalpha."
KCNH2 affects THOC1
| 1
KCNH2 inhibits THOC1. 1 / 1
| 1
reach
"As can be seen in XREF_FIG in both the HeRG stable cell line transfected with siRNA to deplete THOC1 (XREF_FIG) and in HeTH4 cells (+ DOX) transfected with the pIREC system (XREF_FIG), the spontaneous recombination frequency increased with respect to their respective controls, consistent with an increase in DNA breaks and subsequent recombination events taking place upon THO depletion."
KCNH2 affects TGFB1
| 1
KCNH2 increases the amount of TGFB1. 1 / 1
| 1
reach
"ERG1, in turn is long known to directly stimulate TGFB1 expression 57."
KCNH2 affects TGFB
| 1
KCNH2 activates TGFB. 1 / 1
| 1
reach
"As shown by Teng et al, KCNH2 mediates integrin and TGFbeta signaling."
KCNH2 affects TFAM
| 1
KCNH2 decreases the amount of TFAM. 1 / 1
| 1
reach
"Furthermore, the high-glucose-induced inhibition of hERG channel trafficking could activate the unfolded protein response (UPR) by up-regulating the expression levels of activating transcription factor-6 (ATF-6) and the ER chaperone protein calnexin."
KCNH2 affects TAM16
| 1
KCNH2 inhibits TAM16. 1 / 1
| 1
reach
"HERG inhibition activity of TAM16 was evaluated by thallium (Tl +) flux assay displaying an IC 50 of 21muM."
KCNH2 affects TAC1
| 1
| 1
sparser
"We collected evidence to support that bufadienolides such as BF possess NKA inhibition-independent proarrhythmic effects associated with LTCC and hERG blocking."
| 1
sparser
"While less selective sodium channel inhibitors (quinidine, procainamide) also interact with hERG channels and lead to prolongation in RT, this is not expected for lidocaine."
KCNH2 affects Short QT Syndrome type 1
| 1
KCNH2 activates Short QT Syndrome type 1. 1 / 1
| 1
reach
"Rare mutations in KCNH2, a potassium channel involved in myocardial repolarization and drug induced arrhythmias, are known to underlie congenital Long QT Syndrome type 2 and Short QT Syndrome type 1."
KCNH2 affects STIP1
1 |
1 |
biogrid
No evidence text available
KCNH2 affects STAT1
| 1
| 1
sparser
"Molecular docking attempts suggest two possible protein-protein interactions of HERG with the ß1-integrin receptor and the transcription factor STAT-1 as novel HERG-directed therapeutic targeting which avoids possible cardiotoxicity."
KCNH2 affects ST8SIA2
| 1
| 1
reach
"Large depolarizations, e.g., 50 mV, applied to the STX bound hERG K + channel, caused the STX bound channel to open."
KCNH2 affects SRC
| 1
KCNH2 inhibits SRC. 1 / 1
| 1
reach
"Inhibiting Src action with PP1 or Src40-58 inhibited hERG (XREF_FIG - XREF_FIG), supporting the hypothesis that de-phosphorylation of one or more tyrosine residues reduce channel activity."
KCNH2 affects SQTS variant 1
| 1
Mutated KCNH2 activates SQTS variant 1. 1 / 1
| 1
reach
"To date, four gain-of-function mutations of hERG have been reported to cause SQTS variant 1 (SQT1)."
KCNH2 affects SQT2
| 1
KCNH2 activates SQT2. 1 / 1
| 1
reach
"SQTS has been associated with the gain-of-function mutations in 3 distinct potassium channels, KCNH2, KCNQ1 and KCNJ2, which cause SQT1, SQT2 and SQT3, respectively [111-114]."
KCNH2 affects SQLE
| 1
KCNH2 inhibits SQLE. 1 / 1
| 1
reach
"Terbinafine belongs to the allylamine class of antifungals that inhibit squalene epoxidase (Erg1)."
KCNH2 affects SP2
| 1
KCNH2 inhibits SP2. 1 / 1
| 1
reach
"Our largest observed reduction in hERG inhibition lowers hERG inhibition by 15 fold by adding sp2 nitrogens to the slightly basic imidazole to obtain the somewhat less lipophilic methyl tetrazole."
KCNH2 affects SNP
| 1
| 1
sparser
"The KCNH2 intronic SNP rs3807375 was associated with a 1.6 ms (SE 0.4) increase of adjusted QT interval per minor allele QT Nc (p=4.7×10 −5 )."
KCNH2 affects SLC17A5
| 1
| 1
reach
"In contrast with findings described by others (Matsa etal, 2011), hERG modulation by LUF7346 completely reversed the severe effects of the potassium channel blocker AST in LQT2 N996I hiPSC-CMs, confirming the efficacy of LUF7346 compared to other molecules reported so far in the literature."
KCNH2 affects SEC23A
| 1
| 1
sparser
"This ratio may reflect how isoforms and homologues of KCNH2 co-assemble to create heteromeric potassium channels with unique electrophysiological properties xref , xref ."
KCNH2 affects SAR
| 1
| 1
reach
"HERG binding SAR shows that variation in the RCQ structure can be used to minimize potential cardiotoxicity issues."
| PMC
KCNH2 affects S4
| 1
KCNH2 inhibits S4. 1 / 1
| 1
reach
"Gating current studies suggest that a slow component of hERG gating charge, Q on, underlies S4 voltage sensor movement with a time constant of ~ 50 ms at +10 mV which is slightly faster than channel activation, and a V (1/2) that is about 20 mV hyperpolarized compared to the conductance-voltage (G-V) relationship in both WT and S631A inactivation removed channels XREF_BIBR."
KCNH2 affects S1
| 1
Mutated KCNH2 activates S1. 1 / 1
| 1
reach
"This hypothesis is supported by the finding that arrhyth- HERG Mutations Cause Long QT Syndrome 801 S1 S2 $ 3 $ 4 $ 5 Pore $ 6 Extracel [ular Frameshift Intracellular domain Splice error Figure 7."
KCNH2 affects Ranolazine
| 1
KCNH2 binds Ranolazine. 1 / 1
| 1
reach
"Ranolazine binds to the promiscuous drug target hERG."
KCNH2 affects RPS6KB1
| 1
KCNH2 leads to the phosphorylation of RPS6KB1. 1 / 1
| 1
reach
"The up-regulation of HIF-1alpha did not depend on the regulation of HIF protein synthesis by mTORC1 and mTORC2 complex XREF_BIBR, as neither inhibition or silencing of hERG1 decreased p70S6K or pT37 phosphorylation (XREF_FIG)."
KCNH2 affects RPS6, and cooH
| 1
RPS6 binds KCNH2 and cooH. 1 / 1
| 1
sparser
"Furthermore, other channel segments might be involved in gating since several studies have provided evidence for interactions between the S4–S5 linker and residues in the COOH-terminal part of S6 in HERG, HCN, and Shaker ( xref ; xref ; xref ; xref )."
KCNH2 affects RNF139
1 |
1 |
biogrid
No evidence text available
KCNH2 affects RHOH
1 |
1 |
hprd
No evidence text available
KCNH2 affects RENBP
| 1
KCNH2 activates RENBP. 1 / 1
| 1
reach
"Age dependent electrical and morphological remodeling of the Drosophila heart caused by hERG and seizure mutations."
KCNH2 affects RAC
| 1
KCNH2 activates RAC. 1 / 1
| 1
sparser
"HERG1 recruits and activates PI3K and Akt."
KCNH2 affects RAB3GAP1
| 1
| 1
reach
"[XREF_BIBR - XREF_BIBR] Similar scenarios could also be seen in cases of acquired long QT syndrome and ischemic cardiomyopathy, in which rare variants (KCNH2, KCNE1, KCNE2, KCNQ2, SCN5A, and RyR2 in drug induced long QT syndrome and CASQ2, RAB3GAP1, ZNF365, CXADR, GPC5, GPD1L, NOS1AP, and SCN5A in ischemic cardiomyopathy) were associated with higher risk of malignant arrhythmia and SCD."
KCNH2 affects QT syndrome 2
| 1
KCNH2 activates QT syndrome 2. 1 / 1
| 1
reach
"Long QT syndrome 2 (LQTS2) caused by missense mutations in hERG channel is clinically associated with abnormally prolonged ventricular repolarization and sudden cardiac deaths."
KCNH2 affects QT syndrome
| 1
Mutated KCNH2 activates QT syndrome. 1 / 1
| 1
reach
"To date, over 200 known KCNH2 mutations have been described causing a variant of long QT syndrome, known as LQT2."
KCNH2 affects QT (LQT) type 2
| 1
Mutated KCNH2 activates QT (LQT) type 2. 1 / 1
| 1
reach
"Long QT (LQT) type 2 (LQT2) is caused by HERG mutation."
KCNH2 affects Proteasome
| 1
KCNH2-E637K activates Proteasome. 1 / 1
| 1
reach
"We demonstrated that trafficking deficient G572R-hERG and E637K hERG mutant proteins activate ER stress pathways and target the proteasome for degradation."
| 1
reach
"Patients With Long-QT Syndrome Caused by Impaired hERG Encoded K v 11.1 Potassium Channel Have Exaggerated Endocrine Pancreatic and Incretin Function Associated With Reactive Hypoglycemia."
| 1
reach
"(Additional file XREF_SUPPLEMENTARY : Table S1) While the removal of some functional groups from cisapride did not significantly reduce the docking scores of compounds at A 2A, their hERG PD bindings were still too high (i.e., Cisapride-D4, Cisapride-D5)."
KCNH2 affects PTCH1, and spef1
| 1
| 1
sparser
"Such cleavage is associated with a complete loss of hERG function as revealed by patch clamp analysis [10] ."
KCNH2 affects PROC
| 1
| 1
reach
"Therefore, in this study, interactions between PROC and HERG K (+) channels were investigated, with particular reference to potency and mechanism of drug action."
KCNH2 affects PODXL
| 1
KCNH2 activates PODXL. 1 / 1
| 1
reach
"DHH and SFRP4 were both induced by wt fusion proteins but not by the DBDM, whereas PODXL, KRT119 and CDH5 were induced both by FLI-1 and ERG-1 alone and by the EWS-FLI-1 DBDM."
KCNH2 affects PML
| 1
Modified KCNH2 leads to the sumoylation of PML. 1 / 1
| 1
reach
"Primarily, it was found that : (1) exposure of cells to ATO and Ang II significantly reduced the expression of HERG protein; (2) both ATO and Ang II stimulation increased PML SUMOylation and NBs aggregation, promoting recruitment with Pin1; (3) translocation of Pin1 into PML-NBs led to upregulation of TGF-beta1, eventually inhibiting HERG expression through PKA activation."
KCNH2 affects PLD
| 1
KCNH2 inhibits PLD. 1 / 1
| 1
reach
"In other words, a positively charged PLD inducer is most likely a hERG blocker, while a positively charged hERG blocker may not induce PLD; 4."
KCNH2 affects PLA1A
| 1
| 1
sparser
"When combined with environmental triggers and genetic modifiers, LQT2 frameshift mutations associated with NMD can manifest with a severe clinical phenotype."
KCNH2 affects PI3K, and PI3K_p85
| 1
| 1
sparser
"Furthermore, by sequestering the channel in the closed conformation, Cla inhibited the formation of a macromolecular complex between hERG1 and the p85 subunit of PI3K. This strongly reduced Akt phosphorylation, and stimulated the p53-dependent cell apoptosis, as witnessed by late caspase activation."
KCNH2 affects PI3-kinase
| 1
| 1
sparser
"HERG1 recruits and activates PI3K and Akt."
KCNH2 affects PDGF_BB
| 1
KCNH2 increases the amount of PDGF_BB. 1 / 1
| 1
reach
"This in turn triggers the release of Erg-1 transcription factor that enters the nucleus and stimulates PDGF-BB expression."
KCNH2 affects PC
| 1
KCNH2 activates PC. 1 / 1
| 1
reach
"Notable are hERG1 upregulation in PC, gastric cancer (GC) and CRC, leading to enhanced cancer angiogenesis and invasion, and KCNQ1 down-regulation in CRC, where KCNQ1 expression is associated with enhanced disease-free survival in stage II, III, and IV disease."
KCNH2 affects PATHWAY
| 1
KCNH2 activates PATHWAY. 1 / 1
| 1
trips
"Expression of I593R HERG activates the unfolded protein response pathway and, separately, NF-kappaB signaling."
KCNH2 affects PAFAH1B1
| 1
| 1
reach
"In addition, the CCK-8 assay, apoptosis and cell cycle analysis were performed and showed that blockage of HERG K + channels decreased the proliferation of MDS cells but rarely had effects on cell apoptosis and cell cycle distribution."
KCNH2 affects Ondansetron
| 1
| 1
reach
"The potent hERG channel blocking drug ondansetron is used off-label for treatment of nausea and vomiting in early pregnancy."
KCNH2 affects NTRK1
1 |
1 |
biogrid
No evidence text available
KCNH2 affects NRVM
| 1
KCNH2 activates NRVM. 1 / 1
| 1
reach
"Computer simulations and single cell action potential recordings demonstrated that APD shortening and the transient hyperpolarization after each AP in hERG overexpressing NRVM increased the INa availability, which contribute to the increased rotor frequency."
KCNH2 affects NRPS3
| 1
| 1
sparser
"Despite the many beneficial effects demonstrated in animal models, many alpha7 ligands have also shown a propensity for 5HT3 or hERG interactions, which could lead to unwanted side effects [ xref , xref ]."
KCNH2 affects NR1H4, NR3C1, and NR3C2
| 1
| 1
sparser
"The same results were observed when examining its potential to bind to GR, MR, FXR or hERG."
KCNH2 affects NOS3
| 1
| 1
sparser
"NOS3 rs1800779 and KCNH2 rs3807370 polymorphisms were significantly associated with word pair recognition, but only for dominant models, i.e., when pooling the uncommon genotype with the heterozygote."
KCNH2 affects NOS1AP
| 1
KCNH2 activates NOS1AP. 1 / 1
| 1
reach
"[XREF_BIBR - XREF_BIBR] Similar scenarios could also be seen in cases of acquired long QT syndrome and ischemic cardiomyopathy, in which rare variants (KCNH2, KCNE1, KCNE2, KCNQ2, SCN5A, and RyR2 in drug induced long QT syndrome and CASQ2, RAB3GAP1, ZNF365, CXADR, GPC5, GPD1L, NOS1AP, and SCN5A in ischemic cardiomyopathy) were associated with higher risk of malignant arrhythmia and SCD."
KCNH2 affects NKX3-1
| 1
KCNH2 increases the amount of NKX3-1. 1 / 1
| 1
reach
"Another oncoprotein NF-kappaB transactivated, while tumor suppressor Nkx3.1 repressed HERG promoter activity and endogenous HERG transcription."
KCNH2 affects NH
| 1
KCNH2 binds NH. 1 / 1
| 1
sparser
"We tested the hypothesis that the HERG NH 2 terminus interacts with the S4–S5 linker in a manner analogous to the interaction of the Shaker NH 2 terminus with the corresponding residues at the internal mouth of the pore."
KCNH2 affects NEDD4, and PKC
| 1
PKC binds KCNH2 and NEDD4. 1 / 1
| 1
sparser
"The increase in hERG protein was associated with PKC-induced phosphorylation (inhibition) of Nedd4-2, an E3 ubiquitin ligase that mediates hERG degradation."
KCNH2 affects NBN
| 1
Modified KCNH2 leads to the sumoylation of NBN. 1 / 1
| 1
reach
"Primarily, it was found that : (1) exposure of cells to ATO and Ang II significantly reduced the expression of HERG protein; (2) both ATO and Ang II stimulation increased PML SUMOylation and NBs aggregation, promoting recruitment with Pin1; (3) translocation of Pin1 into PML-NBs led to upregulation of TGF-beta1, eventually inhibiting HERG expression through PKA activation."
KCNH2 affects NAV1
| 1
KCNH2 activates NAV1. 1 / 1
| 1
reach
"Human embryonic stem cell derived cardiac myocytes detect hERG mediated repolarization effects, but not Nav1.5 induced depolarization delay."
KCNH2 affects N-terminus
| 1
KCNH2 activates N-terminus. 1 / 1
| 1
reach
"Alternative transcription of hERG1 leads to a protein with a 56 amino acid shorter N-terminus, known as hERG1b."
| 1
| 1
reach
"A561P KCNH2 Mutation Causes a Trafficking Defect of the HERG Channel in Human CMs."
| 1
reach
"Maturation of hERG protein in turn is inhibited by preventing the binding of hERG to HSP chaperone complexes, which is again mediated by ROS XREF_BIBR."
KCNH2 affects MYB
| 1
KCNH2 inhibits MYB. 1 / 1
| 1
reach
"In this case, a deletion encompassing the last intron and part of exon 15 of MYB, including the binding site of ERG-1, a transcription factor that may down-regulate MYB, and the exon 15 splice site, was detected."
KCNH2 affects MMUT
| 1
| 1
sparser
"Based on observations that gene knockdown levels correlate to protein knockdown (Figure  xref C), statistical modelling fitted to the binomial distribution was used to predict the likelihood of functional hERG tetramer formation following Mut hERG knockdown."
KCNH2 affects MAP6
| 1
KCNH2 activates MAP6. 1 / 1
| 1
reach
"Direct sequencing of the KCNH2, KCNQ1 and SCN5A genes revealed a novel heterozygous frameshift mutation in the sixth exon of the KCNH2 gene producing a premature STOP codon : c. 1232_1234delinsTTTGAA (p.Asp411Valfs * 2)."
KCNH2 affects Lys-Asp
| 1
KCNH2 activates Lys-Asp. 1 / 1
| 1
reach
"At 72 hours the quantity of both 135 kD and 155 kD HERG increased for WT HERG, whereas for G816V HERG, only the 135 kD band increased while the 155 kD band was still absent."
KCNH2 affects Long-QT syndrome type 2
| 1
KCNH2 activates Long-QT syndrome type 2. 1 / 1
| 1
reach
"Long-QT syndrome type 2 is caused by mutations in KCNH2 encoding alpha subunit of the hERG K + channel generating the rapid component of the delayed rectifier potassium current (I Kr)."
KCNH2 affects LQTS1
| 1
KCNH2 activates LQTS1. 1 / 1
| 1
reach
"Mutations in KCNQ1 and HERG cause the congenital LQTS1 XREF_BIBR and LQTS2, XREF_BIBR respectively."
KCNH2 affects LQTS-type 2
| 1
KCNH2 activates LQTS-type 2. 1 / 1
| 1
reach
"3 Of LQTS cases, 45% are classified as LQTS-type 2 (LQT2), caused by mutations in KCNH2 (also known as hERG), which encodes the alpha-subunit of a tetrameric complex forming part of the rapid acting inward rectifying potassium (I kr) channel."
KCNH2 affects LQTS mutant channels
| 1
KCNH2 inhibits LQTS mutant channels. 1 / 1
| 1
reach
"Some hERG blockers have been reported to promote protein trafficking of LQTS mutant channels XREF_BIBR, XREF_BIBR, however, the blockage action of drugs may diminish the current conducted by rescued hERG K + channels, consequently nullify their therapeutic potential."
KCNH2 affects LQT2-causing mutants
| 1
KCNH2 increases the amount of LQT2-causing mutants. 1 / 1
| 1
reach
"It has been reported that low temperature could correct hERG defective protein trafficking, thus increase the surface expression of some LQT2 causing mutants, such as G601S, K28E, N407D, and A422T."
KCNH2 affects LQT2 mutations
| 1
KCNH2 activates LQT2 mutations. 1 / 1
| 1
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"Our previous studies have shown that many trafficking defective LQT2 mutations can be rescued by low temperature or hERG channel blocking agent E-4031 [21,22]."
KCNH2 affects LQT2 16
| 1
KCNH2 activates LQT2 16. 1 / 1
| 1
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"Notably, R57 and D642 are conserved throughout the KCNH family (XREF_SUPPLEMENTARY), and mutation of the R57 position in hERG1 (hERG1 R56Q) causes LQT2 16."
KCNH2 affects LQT syndrome type 2
| 1
KCNH2 activates LQT syndrome type 2. 1 / 1
| 1
reach
"LQT syndrome type 2 (LQT2) is caused by a mutation in KCNH2 (also known as human ether-a-go-go, HERG), which encodes the alpha subunits of channels that generate I Kr, a rapid component of the delayed rectifier potassium current."
KCNH2 affects LQT mutation
| 1
KCNH2 activates LQT mutation. 1 / 1
| 1
reach
"In addition, 100nM AST was also added to the hiPSC-CMs carrying LQTS mutations, thus simulating invitro what happens to LQT mutation carriers treated with hERG blocking drugs (Kannankeril etal, 2010; Schwartz, 2015)."
KCNH2 affects L. erythrocarpa
| 1
KCNH2 inhibits L. erythrocarpa. 1 / 1
| 1
reach
"We have also examined the HERG blocking effects of several fractions of L. erythrocarpa, and the H 2 O and BuOH fractions exhibited the strongest changes in V 1/2 (the potential required for half-maximal activation) and g max (maximum conductance) among the solvent fractions."
KCNH2 affects Krt19
| 1
KCNH2 activates Krt19. 1 / 1
| 1
reach
"DHH and SFRP4 were both induced by wt fusion proteins but not by the DBDM, whereas PODXL, KRT119 and CDH5 were induced both by FLI-1 and ERG-1 alone and by the EWS-FLI-1 DBDM."
KCNH2 affects Kcnh2
| 1
KCNH2 inhibits Kcnh2. 1 / 1
| 1
reach
"Loss of minK, a protein subunit that interacts with KvLQT1, results in a marked reduction of I (Ks) giving rise to the Jervell and Lange-Nielsen syndrome and the reduced KCNH2 gene reduces MERG and I (Kr)."
KCNH2 affects KCNQ1-T587M
| 1
KCNH2 binds KCNQ1-T587M. 1 / 1
| 1
reach
"Consistent with this result, FRET experiments demonstrated that both KCNQ1-WT and -R259C interacted with hERG in the cytosol and on the plasma membrane; however, the interaction between KCNQ1-T587M and hERG was observed only in the cytosol, and hERG proteins were seldom transported to the cell membrane, suggesting that the KCNQ1 T587M mutation impaired the trafficking of hERG to the cell membrane."
KCNH2 affects KCNQ1, and voltage-gated potassium channel
| 1
KCNH2 binds KCNQ1 and voltage-gated potassium channel. 1 / 1
| 1
sparser
"Both LQT1 and LQT2 are associated with loss of function of voltage-gated potassium channels (I Ks and I Kr ). xref "
KCNH2 affects KCNQ1, and ion channel
| 1
sparser
"The KCNH2 and KCNQ1 mutations are associated with different ion channel dysfunctions, xref , xref and gene specific triggers of arrhythmias. xref In LQT-1, it is recognized that exercise (catecholamine) is the primary trigger because of the malfunctioning I Ks channels that leads to less effective shortening of the QT intervals during tachycardia than in normal individuals."
| 1
sparser
"Peptide N-glycosidase F-sensitive forms of horse ERG1 (145 kDa) and KCNQ1 (75 kDa) were detected."
KCNH2 affects KCNQ1, and Q1
| 1
KCNH2 binds KCNQ1 and Q1. 1 / 1
| 1
reach
"We have previously reported a physiologically relevant interaction between KCNQ1 (Q1) and KCNH2 (H2)."
KCNH2 affects KCNH2-3.1
| 1
KCNH2 activates KCNH2-3.1. 1 / 1
| 1
reach
"A genetic variant (rs3800779; M30) in the KCNH2 gene has been associated with schizophrenia, a lower intelligence quotient (IQ) and processing speed scores, altered brain functions and increased KCNH2-3.1."
KCNH2 affects KCNE2-ER
| 1
KCNH2 binds KCNE2-ER. 1 / 1
| 1
reach
"BFA treatment also resulted in enhanced KCNE2-ER binding to HERG but to a much lower degree than that seen with wild type KCNE2 (XREF_FIG)."
KCNH2 affects KCNE protein
| 1
KCNH2 binds KCNE protein. 1 / 1
| 1
reach
"We quantified the amount of KCNE protein that associated with HERG by taking the densitometry value of precipitated KCNE proteins divided by total KCNE protein expressed in the cell lysates normalized to tubulin."
KCNH2 affects KCNE
| 1
KCNH2 binds KCNE. 1 / 1
| 1
reach
"Such differences may help explain some of the discrepancies among groups investigating HERG and KCNE interactions."
KCNH2 affects KB130015
| 1
KCNH2 binds KB130015. 1 / 1
| 1
reach
"It is conceivable that KB130015 binding to hERG1 induces either activation or inhibition, depending on the " gating status " of the channel, which may be affected by mutation (Y652A / Delta2-373) or drug (mallotoxin) binding."
KCNH2 affects J-Tpeakc
| 1
KCNH2 inhibits J-Tpeakc. 1 / 1
| 1
reach
"While predominant hERG blockers prolonged QTc and J-Tpeakc, " balanced " ion channel blocking drugs (hERG+ late sodium and/or calcium block) prolonged QTc without prolonging J-Tpeakc."
KCNH2 affects Ile-Ala
| 1
KCNH2-N588K inhibits Ile-Ala. 1 / 1
| 1
reach
"The N588K hERG mutation is well established to attenuate markedly the inhibitory actions of Class III but not Class Ia antiarrhythmic drugs (which depend less than do Class III I Kr -selective drugs on channel inactivation to bind) XREF_BIBR."
KCNH2 affects Ibogaine
| 1
| 1
sparser
"After having characterised ibogaine's hERG channel inhibition and the drug's lower affinity inhibitory action on cardiac voltage-gated sodium channels, we next studied the effects of ibogaine on the cardiac action potential (AP)."
KCNH2 affects IK
| 1
| 1
sparser
"The discovery that HERG forms the IK, channel provides a logical explanation for the obser- vation that block of IKr by certain drugs can provoke the same arrhythmia (torsades de pointe) as that observed in familial LQT."
KCNH2 affects IGFBP5
| 1
KCNH2 activates IGFBP5. 1 / 1
| 1
reach
"The present results indicate that IGF1, IGFBP3 and IGFBP5 are induced by all of the fusion proteins tested but not by FLI-1 and ERG-1 alone."
KCNH2 affects IGFBP3
| 1
KCNH2 activates IGFBP3. 1 / 1
| 1
reach
"The present results indicate that IGF1, IGFBP3 and IGFBP5 are induced by all of the fusion proteins tested but not by FLI-1 and ERG-1 alone."
KCNH2 affects Hsp90alpha
| 1
KCNH2 activates Hsp90alpha. 1 / 1
| 1
reach
"In addition, we observed a reduction in the total amount of hERG (fg+ cg) in these cells following shRNA mediated Hsp90alpha reduction (XREF_FIG)."
KCNH2 affects Hippo
| 1
KCNH2 activates Hippo. 1 / 1
| 1
reach
"[Downregulation of Herg1 suppresses osteosarcoma proliferation and invasion by targeting Hippo signaling pathway]."
KCNH2 affects HSPA4
1 |
1 |
biogrid
No evidence text available
KCNH2 affects HSPA1A
1 | 2
1 | 2
biogrid
No evidence text available
KCNH2 affects HSP90B1
| 1
| 1
sparser
"Although cytosolic Hsp90 was reported to interact with and promote the maturation of human ether-a-gogo -related gene (hERG) potassium channels, Grp94 (Hsp90 in the ER) did not interact with hERG channels xref , which might be because hERG channels contain very short ER lumen components."
KCNH2 affects HR HF
| 1
KCNH2 inhibits HR HF. 1 / 1
| 1
reach
"HR HF rhythm enhancement by several arrhythmic hERG blockers in beagle dogs."
KCNH2 affects HIF-alpha(s)
| 1
KCNH2 activates HIF-alpha(s). 1 / 1
| 1
reach
"On the whole, increased transcription of the HIF-alpha gene (s) seems the main regulatory mechanism sustaining the beta 1 and hERG1 dependent up-regulation of HIF-alpha (s) in CRC cells."
KCNH2 affects HIF(s)
| 1
KCNH2 bound to PI3K activates HIF(s). 1 / 1
| 1
reach
"The beta 1 / hERG1 and PI3K complex, through Akt, induces HIF (s) transcriptional activation."
KCNH2 affects HIF protein
| 1
KCNH2 activates HIF protein. 1 / 1
| 1
reach
"However, the integrin and hERG1 triggered pathway affects HIF protein synthesis through the activity of NF-kB, which has been reported to be one of the main regulators of HIF transcription in different cellular systems XREF_BIBR XREF_BIBR XREF_BIBR XREF_BIBR."
KCNH2 affects HIF (i)
| 1
KCNH2 activates HIF (i). 1 / 1
| 1
reach
"This signaling pathway has novel features in that the integrin- and hERG1 dependent activation of HIF (i) is triggered in normoxia, especially after CRC cells have experienced a hypoxic stage, (ii) involves NF-kB and (iii) is counteracted by an active p53."
KCNH2 affects HGF
| 1
| 1
sparser
"Finally, the high affinity of the cardiotoxic drugs for the lipid membrane as well as their effect on the membrane interaction of hERG's SF segment supports the possibility of an indirect role of the membrane in the ALQTS."
KCNH2 affects HFHR
| 1
KCNH2 activates HFHR. 1 / 1
| 1
reach
"Likewise, several hERG blocking drugs (e.g. dofetilide, thioridazine) known for their association with torsades de pointes in humans have been demonstrated to increase HFHR oscillations in animal studies (Champeroux et al., 2015) which in turn increased the beat-to-beat ventricular repolarisation variability, a situation that favours occurrence of torsades de pointes (Champeroux et al., 2016)."
KCNH2 affects HERG1ratio
| 1
KCNH2 activates HERG1ratio. 1 / 1
| 1
reach
"When the oxygen supply was restored, the HERG1B and HERG1ratio could be increased by a remodeling of HERG channels on the plasma membrane, thus leading to depolarize V m and sustain cell growth (Crociani et al., 2003)."
KCNH2 affects HERG1B
| 1
KCNH2 activates HERG1B. 1 / 1
| 1
reach
"When the oxygen supply was restored, the HERG1B and HERG1ratio could be increased by a remodeling of HERG channels on the plasma membrane, thus leading to depolarize V m and sustain cell growth (Crociani et al., 2003)."
KCNH2 affects HA
| 1
KCNH2 binds HA. 1 / 1
| 1
sparser
"The decision to use HA-hERG hERG was reinforced by the finding that HA-hERG tetramers have slightly elevated surface levels, with respect to total channel expression, in comparison with channels formed following co-expression of HA-hERG with wild type hERG; the inclusion of hERG yielded consistent surface levels irrespective of the ratio between the two constructs ( xref )."
KCNH2 affects GPD1L
| 1
KCNH2 activates GPD1L. 1 / 1
| 1
reach
"[XREF_BIBR - XREF_BIBR] Similar scenarios could also be seen in cases of acquired long QT syndrome and ischemic cardiomyopathy, in which rare variants (KCNH2, KCNE1, KCNE2, KCNQ2, SCN5A, and RyR2 in drug induced long QT syndrome and CASQ2, RAB3GAP1, ZNF365, CXADR, GPC5, GPD1L, NOS1AP, and SCN5A in ischemic cardiomyopathy) were associated with higher risk of malignant arrhythmia and SCD."
KCNH2 affects GPD1
| 1
KCNH2 activates GPD1. 1 / 1
| 1
reach
"We also demonstrate that hERG blockers reduced GPDC proliferation, and improved survival in patients who received one or more hERG blocking drugs but only if their tumors exhibited high hERG expression levels."
KCNH2 affects GPC5
| 1
KCNH2 activates GPC5. 1 / 1
| 1
reach
"[XREF_BIBR - XREF_BIBR] Similar scenarios could also be seen in cases of acquired long QT syndrome and ischemic cardiomyopathy, in which rare variants (KCNH2, KCNE1, KCNE2, KCNQ2, SCN5A, and RyR2 in drug induced long QT syndrome and CASQ2, RAB3GAP1, ZNF365, CXADR, GPC5, GPD1L, NOS1AP, and SCN5A in ischemic cardiomyopathy) were associated with higher risk of malignant arrhythmia and SCD."
KCNH2 affects GDNF
| 1
KCNH2 inhibits GDNF. 1 / 1
| 1
reach
"Furthermore, knockdown of ERG-1 by siRNA abolished hyperglycemia suppressed GDNF induced migration of HRPTE cells."
KCNH2 affects GC
| 1
KCNH2 inhibits GC. 1 / 1
| 1
reach
"Since nothing is known of how mRNA structural elements factor in channel processing, we synthesized a codon modified HERG cDNA (HERG-CM) where the codons were synonymously changed to reduce GC content, secondary structure, and rare codon usage."
KCNH2 affects G1006fs/49 heterotetrameric channels
| 1
KCNH2 activates G1006fs/49 heterotetrameric channels. 1 / 1
| 1
reach
"Major findings of this work are as follows : (a) G1006fs/49 is functional at the plasma membrane even when co-expressed with KCNH2, (b) G1006fs/49 exerts a dominant negative effect on KCNH2 conferring specific biophysical properties to the heterotetrameric channel such as a significant delay in the voltage sensitive transition to the open state, faster kinetics of both inactivation and recovery from the inactivation and (c) the activation kinetics of the G1006fs/49 heterotetrameric channels is partially restored by a specific KCNH2 activator."
KCNH2 affects FPP
| 1
KCNH2 activates FPP. 1 / 1
| 1
reach
"Thus, the increase in the level of expression of erg1 gene will direct the FPP towards the ergosterol biosynthesis, which is needed for the fungal cell growth, one of the stimulating effects exerted by the tyrosol."
KCNH2 affects FPD
| 1
KCNH2 inhibits FPD. 1 / 1
| 1
reach
"Inhibition of hERG channels prolonged FPD only at low heart rates whereas Ca 2+ channel block shortened FPD at all heart rates."
KCNH2 affects FLI1
| 1
| 1
sparser
"Constitutive expression of FLI1 and ERG1 is not associated with malignant transformation."
KCNH2 affects FIDAS
| 1
KCNH2 binds FIDAS. 1 / 1
| 1
reach
"21 We utilized a [3 H]-dofetilide binding assay to evaluate FIDAS agent interaction with hERG."
KCNH2 affects Erg2p
| 1
KCNH2 inhibits Erg2p. 1 / 1
| 1
reach
"These include terbinafine (TER) that inhibits the ERG1 gene product, fenpropimorph (FEN) that inhibits Erg2p, and lovastatin (LOV) that inhibits Hmg1p."
KCNH2 affects Epsilon
| 1
| 1
sparser
"It has been reported that the PPARδ pathway targets protein 14-3-3 epsilon, which in turn interacts with HERG to stabilize the PKA-phosphorylated state of the channel by shielding phosphates from degradation [ xref ]."
| 1
reach
"Future studies should establish whether Eng is a mediator of the ERG1 induced EC differentiation."
KCNH2 affects ESR1
| 1
| 1
sparser
"Moreover, hERG1 scoring was significantly associated with ER expression, with higher hERG1 scoring in ER-positive samples (p = 0.008), and inversely associated with Ki67 (higher hERG1 scoring in samples with Ki67 index lower to 15%, p = 0.038)."
KCNH2 affects EPHA3
| 1
KCNH2 activates EPHA3. 1 / 1
| 1
reach
"Specifically doxazosin induced apoptosis in hERG overexpressing HEK cells, but did not produce apoptosis in untransfected control cells."
KCNH2 affects ENOPH1
| 1
KCNH2 inhibits ENOPH1. 1 / 1
| 1
reach
"Stimulation of hERG1 channel activity promotes a calcium dependent degradation of cyclin E2, but not cyclin E1, in breast cancer cells."
KCNH2 affects ENG
| 1
KCNH2 increases the amount of ENG. 1 / 1
| 1
reach
"It is also consistent with the recent finding that ERG1 induces Eng expression and the differentiation of ESC into EC."
KCNH2 affects ELANE
| 1
| 1
sparser
"MS analysis revealed the formation of 4-HNE-hERG adduct on specific amino acid residues, including C276, K595, H70, and H687."
KCNH2 affects EGR1
| 1
KCNH2 activates EGR1. 1 / 1
| 1
reach
"ERG1 acetylation increases EGR1 protein stability [XREF_BIBR] and sumoylated EGR1 induces of the tumor suppressor phosphatase and tensin homologue."
| 1
reach
"An HDAC inhibitor that structurally can not inhibit HDAC3 and can not bind hERG, then, would be of considerable therapeutic interest."
KCNH2 affects EC
| 1
KCNH2 activates EC. 1 / 1
| 1
reach
"The small molecule hERG ligand doxazosin induced concentration dependent apoptosis of human LNT-229 (EC 50 = 35 microM) and U87MG (EC 50 = 29 microM) GB cells, accompanied by cell cycle arrest in the G0/G1 phase."
KCNH2 affects E-4031
| 1
KCNH2 inhibits E-4031. 1 / 1
| 1
reach
"Ranolazine could not reverse the effect of E-4031 to inhibit human ether-a-go-go-related gene (HERG) K (+) current; thus, the reversal by ranolazine of effects of E-4031 was likely due to inhibition of late I (Na) and not to antagonism of the HERG blocking action of E-4031."
KCNH2 affects DNAJB14
| 1
KCNH2 activates DNAJB14. 1 / 1
| 1
reach
"Overexpressing DNAJB14 significantly rescued the defective function of human ether-a-go-go-related gene (hERG) mutant channels associated with long QT syndrome (LQTS), a condition that predisposes to life threatening arrhythmia, by stabilizing the mutated proteins."
KCNH2 affects DNAJA1
1 |
1 |
biogrid
No evidence text available
KCNH2 affects DHB
| 1
KCNH2 binds DHB. 1 / 1
| 1
reach
"We speculated that DHB was bound to the hERG channels and caused a conformational change that led to abnormal trafficking."
KCNH2 affects DBP
| 1
KCNH2 binds DBP. 1 / 1
| 1
sparser
"There were statistically significant interactions between KCNH2 (1956, C>T) polymorphism and DBP change (P = 0.010), MAP change (P = 0.014) on azelnidipine or nitrendipine therapy patients at the end of 6 weeks."
KCNH2 affects Coptidis rhizoma
| 1
KCNH2 inhibits Coptidis rhizoma. 1 / 1
| 1
reach
"HERG channel inhibitors in extracts of Coptidis rhizoma."
KCNH2 affects Class III
| 1
KCNH2-N588K inhibits Class III. 1 / 1
| 1
reach
"The N588K hERG mutation is well established to attenuate markedly the inhibitory actions of Class III but not Class Ia antiarrhythmic drugs (which depend less than do Class III I Kr -selective drugs on channel inactivation to bind) XREF_BIBR."
KCNH2 affects Cavalli-2
| 1
KCNH2 binds Cavalli-2. 1 / 1
| 1
reach
"Cavalli-2 interaction with WT hERG and inactivation deficient mutants."
KCNH2 affects CYP450
| 1
KCNH2 binds CYP450. 1 / 1
| 1
reach
"Machine learning algorithms for the prediction of hERG and CYP450 binding in drug development."
KCNH2 affects CYP3A4
| 1
| 1
sparser
"In conclusion, the progesterone metabolites formed via CYP3A cause inhibitory effects on hERG channels and predict QTcI intervals in healthy women pretreated with progesterone."
KCNH2 affects CYP2C9
| 1
| 1
sparser
"However, the compound displayed greater promiscuity by strongly binding to hERG and CYP2C9."
KCNH2 affects CYP
| 1
| 1
sparser
"This review summarizes the state of modeling hERG and CYP binding towards this goal since 2003 using ML algorithms."
KCNH2 affects CYCS
| 1
KCNH2 activates CYCS. 1 / 1
| 1
reach
"By facilitating expression of channel protein HERG, potassium ions may prevent cells from being shunted to procancerous pathways and overbalance the mitochondrial membrane potential through upregulating expression of VDAC1 or breaking the balance of Bcl-2 and Bax ratio and then induced cytochrome c released from mitochondria, caspase activation, and caspase-3/7 ration imbalance, finally resulting in cell apoptosis."
KCNH2 affects CXADR
| 1
KCNH2 activates CXADR. 1 / 1
| 1
reach
"[XREF_BIBR - XREF_BIBR] Similar scenarios could also be seen in cases of acquired long QT syndrome and ischemic cardiomyopathy, in which rare variants (KCNH2, KCNE1, KCNE2, KCNQ2, SCN5A, and RyR2 in drug induced long QT syndrome and CASQ2, RAB3GAP1, ZNF365, CXADR, GPC5, GPD1L, NOS1AP, and SCN5A in ischemic cardiomyopathy) were associated with higher risk of malignant arrhythmia and SCD."
KCNH2 affects CUL1
1 |
1 |
biogrid
No evidence text available
KCNH2 affects CHRN
| 1
| 1
sparser
"In addition, other α7 nAChR agonists that are not associated with the negative effects on hERG channels in the heart were also found to prevent the loss of RGCs under glaucoma-like conditions, though to a lesser degree than PNU-282987 (Birkholz et al., 2016)."
KCNH2 affects CH
| 1
| 1
sparser
"ER retention of hERG 125kDa form by CH was due to defective trafficking and was rescued by exposing cells to hypoxia at low temperatures or treatment with E-4031, a hERG channel blocker."
KCNH2 affects CFH
| 1
KCNH2 activates CFH. 1 / 1
| 1
reach
"On the other hand, the other hERG blockers had either no effect or reduced endogenous HF oscillations in HR in beagle dogs."
KCNH2 affects CASQ2
| 1
KCNH2 activates CASQ2. 1 / 1
| 1
reach
"[XREF_BIBR - XREF_BIBR] Similar scenarios could also be seen in cases of acquired long QT syndrome and ischemic cardiomyopathy, in which rare variants (KCNH2, KCNE1, KCNE2, KCNQ2, SCN5A, and RyR2 in drug induced long QT syndrome and CASQ2, RAB3GAP1, ZNF365, CXADR, GPC5, GPD1L, NOS1AP, and SCN5A in ischemic cardiomyopathy) were associated with higher risk of malignant arrhythmia and SCD."
KCNH2 affects BmKKx2
| 1
KCNH2 binds BmKKx2. 1 / 1
| 1
sparser
"Here, the roles of these three regions were respectively investigated during the toxin BmKKx2-hERG channel interaction."
KCNH2 affects BeKm-1 scorpion toxin
| 1
KCNH2 inhibits BeKm-1 scorpion toxin. 1 / 1
| 1
reach
"Preferential closed channel blockade of HERG potassium currents by chemically synthesised BeKm-1 scorpion toxin."
KCNH2 affects BAG2
1 |
1 |
biogrid
No evidence text available
KCNH2 affects Arg-Trp
| 1
KCNH2 activates Arg-Trp. 1 / 1
| 1
reach
"This behavior has been used in the treatment in LQT2 patients with K + intake that has shown to correct some electrocardiographic abnormalities.Mutations in KCNH2 have been shown to induce an autosomal dominant RW syndrome in six families affected with congenital LQT syndrome (Curran et al., 1995)."
KCNH2 affects Apoptosis
1 |
KCNH2 activates Apoptosis. 1 / 1
1 |
bel
"re, we show that HERG conductance markedly promotes H2O2-induced apoptosis of various tumor cells, whereas HERG expression facilitates the tumor cell proliferation caused by tumor necrosis factor (TNF) ligand (TNF-alpha)."
KCNH2 affects AZA3
| 1
KCNH2 binds AZA3. 1 / 1
| 1
reach
"AZA1, AZA2, and AZA3 bind to hERG channels."
KCNH2 affects AZA1
| 1
KCNH2 binds AZA1. 1 / 1
| 1
reach
"Relative to vehicle controls, hERG binding by AZA1, AZA2, and AZA3 (10 muM) was reduced to 19.7 +/- 1.4% (n = 2), 22.3 +/- 1.0% (n = 3), and 29.3 +/- 1.6% (n = 3) with IC 50 values of 2.1 muM, 2.6 muM, and 6.6 muM; respectively (XREF_TABLE)."
KCNH2 affects ATF3
| 1
KCNH2 increases the amount of ATF3. 1 / 1
| 1
reach
"As would be expected, c-Jun/AP-1, ATF2, ATF4, ATF6, CREB, Myc, C/EBPB, Erg-1, and other transcription factors have all been shown to induce ATF3 expression."
KCNH2 affects ARNT
| 1
| 1
sparser
"This paper describes one of several strategies incorporated to limit hERG binding via modifications of a terminal aryl group in an otherwise promising bicyclohexyl urea series."
KCNH2 affects APDc
| 1
KCNH2 inhibits APDc. 1 / 1
| 1
reach
"Of note, the similar levels of hERG potassium channel block induced by 2-3 nM dofetilide and 6.9 muM ranolazine (approximately 52%) induced> 200 ms of APDc and FPDc prolongation and multiple arrhythmic events in dofetilide treated cells, but only APDc and FPDc prolongation (< 150 ms) without arrhythmias in ranolazine treated cells."
KCNH2 affects APD30-90
| 1
KCNH2 activates APD30-90. 1 / 1
| 1
reach
"All the 15 IKr and/or hERG current inhibitors that have been reported (9 compounds) or not reported (6 compounds) to inhibit calcium currents prolonged APD30-60, APD60-90, and/or APD30-90; and 8 of the 15 inhibitors prolonged APD30-60, APD60-90, and/or APD30-90 more potently than APD90."
KCNH2 affects APD30-60
| 1
KCNH2 activates APD30-60. 1 / 1
| 1
reach
"All the 15 IKr and/or hERG current inhibitors that have been reported (9 compounds) or not reported (6 compounds) to inhibit calcium currents prolonged APD30-60, APD60-90, and/or APD30-90; and 8 of the 15 inhibitors prolonged APD30-60, APD60-90, and/or APD30-90 more potently than APD90."
KCNH2 affects APC
| 1
KCNH2 activates APC. 1 / 1
| 1
reach
"When Apc min/+ mice were treated with the specific hERG1 blocker E4031, daily for 3months, such long-term mERG1 current inhibition XREF_BIBR - XREF_BIBR, that, in agreement with a previous paper XREF_BIBR, did not lead to drug induced torsades de pointes in E4031 treated mice, produced an impairment in colonic lesion development."
KCNH2 affects ALG10
1 |
1 |
hprd
No evidence text available
KCNH2 affects AGT
| 1
| 1
reach
"The inhibition of I kr was realized via its phosphorylation by ANGII-AT1R-PKC pathway or Ang II directly interact with KCNH2, and that was not influenced by the change of Ca 2+ concentration or PKA pathway."
KCNH2 affects AGL1
| 1
KCNH2 activates AGL1. 1 / 1
| 1
reach
"Of note, then, only when tyrosine phosphorylated, the ITIM region of hERG1 activated SHP-1."
KCNH2 affects ADAMTS4
| 1
KCNH2 increases the amount of ADAMTS4. 1 / 1
| 1
reach
"The absence of any effect of EGR1-knock-down on ADAMTS4 mRNA levels in response to IL-1beta, suggests that ERG1 does not directly regulate ADAMTS4 expression levels and is congruent with the absence of EGR1 binding sites in its promoter."
KCNH2 affects 3D
| 1
| 1
reach
"All models delineated similar 3D hERG binding features, however, small deviations of about ~ 0.4 A were observed between important hotspots of molecular interaction fields (MIFs) between solvated and non solvated hERG models."
KCNH2 affects 1b-specific
| 1
KCNH2 activates 1b-specific-A8V. 1 / 1
| 1
reach
"The importance of hERG 1b in vivo is supported by the identification of a 1b specific A8V missense mutation in 1/269 unrelated genotype negative LQTS patients that was absent in 400 control alleles."
| 1
reach
"Similar to female predominance of arrhythmia in the acquired setting, which suggests interactions between hERG, dofetilide and oestradiol, the female predominance of inherited arrhythmia linked the the G604S mutations, suggests that oestradiol may differentially interact with the mutant hERG channel compared to WT."
KCNH2 affects -R259C
| 1
KCNH2 binds -R259C. 1 / 1
| 1
reach
"Consistent with this result, FRET experiments demonstrated that both KCNQ1-WT and -R259C interacted with hERG in the cytosol and on the plasma membrane; however, the interaction between KCNQ1-T587M and hERG was observed only in the cytosol, and hERG proteins were seldom transported to the cell membrane, suggesting that the KCNQ1 T587M mutation impaired the trafficking of hERG to the cell membrane."
| 1
reach
"For example, (S) -2,3-epoxysqualene and 5alpha-cholesta-8,24-dien-3-one specifically associated only with Erg1 (XREF_FIG), whereas lanosterol, ergosterol and episterol consistently co-purified with 5, 5 and 3 Erg proteins, respectively, above the control (XREF_TABLE)."
| 1
reach
"Two arguments suggest that the binding of ketoconazole to hERG is not modified by the S3-S4 substitution."
KCNE3S affects KCNH2
| 1
KCNE3S inhibits KCNH2. 1 / 1
| 1
reach
"Previous studies also showed that in oocytes and in CHO cells, KCNE3S inhibits hERG XREF_BIBR XREF_BIBR, which generates the major human cardiac repolarization current, I Kr XREF_BIBR."
KCNE2-ER affects KCNH2
| 1
KCNH2 binds KCNE2-ER. 1 / 1
| 1
reach
"BFA treatment also resulted in enhanced KCNE2-ER binding to HERG but to a much lower degree than that seen with wild type KCNE2 (XREF_FIG)."
KCNE2 affects KCNH2, and TM
| 1
KCNE2 binds KCNH2 and TM. 1 / 1
| 1
sparser
"This is well illustrated by the interaction between the cardiac K channel HERG and a single TM protein, MiRP1 ."
KCNE1 affects KCNE2, KCNH2, and MYC
| 1
KCNE1 binds KCNE2, KCNH2, and MYC. 1 / 1
| 1
sparser
"To compare the binding of MinK and MiRP1 to HERG-cmyc, an assay was performed using 35 S-labeled MinK and MiRP1 subunits synthesized in vitro."
| 1
sparser
"To our knowledge, only one study has utilized sequencing to examine rare variation in unselected SCD cases from adult populations. xref , xref The entire coding sequence and splice junctions of five ion channel genes associated with IADS, SCN5A, KCNE1, KCNE2, KCNQ1 and KCNH2 , were directly sequenced in 113 cases of SCD. xref No unique or rare coding sequence variants were identified in any of the ion channel genes in 53 men. xref In 60 women with SCD, 6 rare missense variants (10%) were identified in the cardiac sodium channel gene (SCN5A) . xref The overall frequency of these rare variants in SCN5A was significantly higher in the SCD cases compared to 733 controls from the same population (1.6%; P=0.001), and subtle alterations in ion channel function were observed for 4 of the 5 variants."
KCNE protein affects KCNH2
| 1
KCNH2 binds KCNE protein. 1 / 1
| 1
reach
"We quantified the amount of KCNE protein that associated with HERG by taking the densitometry value of precipitated KCNE proteins divided by total KCNE protein expressed in the cell lysates normalized to tubulin."
KCNE affects KCNH2
| 1
KCNH2 binds KCNE. 1 / 1
| 1
reach
"Such differences may help explain some of the discrepancies among groups investigating HERG and KCNE interactions."
KCN affects KCNE2, and KCNH2
| 1
KCN binds KCNE2 and KCNH2. 1 / 1
| 1
sparser
"KvLQT1 and minK associate to form the functional slowly activated delayed rectifier potassium channel ( I Ks ) [12,13] while HERG and MiRP1 associate to form the rapidly activated delayed rectifier potassium channel ( I Kr ) [10] ."
K(+) channel regulator 1 affects KCNH2
| 1
K(+) channel regulator 1 inhibits KCNH2. 1 / 1
| 1
reach
"Previous reports demonstrated that K (+) channel regulator 1 (KCR1) diminishes KCNH2 drug sensitivity and may protect susceptible patients from developing aLQTS."
K V 4.3 affects KCNH2
| 1
K V 4.3 activates KCNH2. 1 / 1
| 1
reach
"This study together with our findings strongly suggest that the overexpression or knock-down of K V 4.3 in cardiomyocytes may lead to a complex modulation of ion channels initially seen as unrelated including Na V 1.5, hERG, and Kir2.1 channels."
K V 10.1 affects KCNH2
| 1
K V 10.1 activates KCNH2. 1 / 1
| 1
reach
"Since most inhibitors of K V 10.1 also inhibit the cardiac hERG channel, the effect of APETx4 on hERG was further investigated."
J-Tpeakc.41 Ranolazine affects KCNH2
| 1
J-Tpeakc.41 Ranolazine activates KCNH2. 1 / 1
| 1
reach
"In a prior study, a single dose of 1,500 mg resulted in 2.3 mug/mL C max and caused a mean QTc prolongation of ~ 10 ms without prolonging J-Tpeakc.41 Ranolazine causes approximately equipotent hERG and late sodium block."
Integrins affects KCNH2, and PI3K_p85
| 1
sparser
"These results indicate that the p85 subunit of PI3K associates with hERG1 and the β 1 integrin, to constitute a single macromolecular complex and that its phosphorylation depends on (i) integrin activation and (ii) hERG1 channel activity."
IQB-9302 affects KCNH2
| 1
IQB-9302 inhibits KCNH2. 1 / 1
| 1
reach
"These results suggest that 1) bupivacaine and IQB-9302 block the open state of hKv1.5, Kv2.1, Kv4.3, and HERG channels; and 2) small differences at the N-substituent of these drugs do not affect the drug induced block of Kv2.1, Kv4.3, or HERG, but specifically modify block of hKv1.5 channels."
IOT101 affects KCNH2
| 1
IOT101 inhibits KCNH2. 1 / 1
| 1
reach
"The problem, however, is that IOT101 also blocks hERG (human EAG related gene) potassium channels, which is not surprising, given the similarity of these channels."
IL6 affects KCNH2
| 1
IL6 inhibits KCNH2. 1 / 1
| 1
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"Interleukin-6 inhibition of hERG underlies risk for acquired long QT in cardiac and systemic inflammation."
IC 50 of 75 muM affects KCNH2
| 1
IC 50 of 75 muM inhibits KCNH2. 1 / 1
| 1
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"Although the drug also partly inhibited the slow component of the cardiac delayed rectifier current (I Ks), its effects on the HERG type channel (I Kr, I HERG) were more prominent and likely to account for most of the APD prolongation.Glibenclamide inhibited I HERG in neuroblastoma cells with a threshold concentration of 10 muM and an IC 50 of 75 muM."
IC 50 of 2.2 muM affects KCNH2
| 1
IC 50 of 2.2 muM inhibits KCNH2. 1 / 1
| 1
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"In our hands AZA-2 blocked hERG activity with an IC 50 of 2.2 muM, which attending to hERG blocking drugs classification would place AZA-2 among low-potency blockers (IC 50> 1 muM)."
I hERG IC 50 affects KCNH2
| 1
I hERG IC 50 inhibits KCNH2. 1 / 1
| 1
reach
"With mammalian expression systems, I hERG IC 50 values for amiodarone of between ~ 26 and 300nM were reported XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR, XREF_BIBR and its metabolite desethyl-amiodarone (DEA) has been shown also to inhibit I hERG, with an IC 50 of ~ 160nM XREF_BIBR."
I NaL affects KCNH2
| 1
I NaL inhibits KCNH2. 1 / 1
| 1
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"With regard to our data and in accordance to the literature, we can speculate that the low documented cardiotoxicity of mexiletine could be due to the fact that mexiletine inhibition of I NaL may counteract any simultaneous prolongation of the QT interval induced by the block of I Kr / hERG channel."
Hsp90alpha affects KCNH2
| 1
Hsp90alpha decreases the amount of KCNH2. 1 / 1
| 1
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"8 Knockdown of Hsp90alpha (60% reduction) caused approximately a 70% reduction in the trafficking efficiency of hERG and a 55% reduction in the total amount of hERG (XREF_FIG)."
| 1
sparser
"To identify off-target effects we investigated whether sc1o interacts with safety-relevant molecules such as cytochrome P450 (CYP) enzymes, phosphodiesterases (PDE), histone deacteylases (HDAC) and human ether-a-go-go related gene ( h ERG)."
| 1
sparser
"Maturation of hERG protein in turn is inhibited by preventing the binding of hERG to HSP chaperone complexes, which is again mediated by ROS xref ."
Heat affects KCNH2
| 1
Heat activates KCNH2. 1 / 1
| 1
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"Heat shock protein (Hsp) 70 is known to promote maturation of hERG."
HbetaC affects KCNH2
| 1
HbetaC inhibits KCNH2. 1 / 1
| 1
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"HbetaC inhibited hERG activation and tail current and accelerated current deactivation in a concentration dependent manner."
HSPA4 affects KCNH2
1 |
1 |
biogrid
No evidence text available
HSPA1A affects KCNH2
1 | 2
1 | 2
biogrid
No evidence text available
HSPA affects KCND3, and KCNH2
| 1
HSPA binds KCND3 and KCNH2. 1 / 1
| 1
sparser
"In addition, Hsp70 interacted with hERG and Kv4.3 respectively, and formed complexes with hERG and Kv4.3."
HSPA affects HSPA8, and KCNH2
| 1
HSPA binds HSPA8 and KCNH2. 1 / 1
| 1
sparser
"Interestingly, although both Hsp70 and Hsc70 associated with hERG channels, it was reported that Hsp70 enhanced the maturation of hERG channels while Hsc70 suppressed their maturation xref ."
HSP90B1 affects KCNH2
| 1
| 1
sparser
"Although cytosolic Hsp90 was reported to interact with and promote the maturation of human ether-a-gogo -related gene (hERG) potassium channels, Grp94 (Hsp90 in the ER) did not interact with hERG channels xref , which might be because hERG channels contain very short ER lumen components."
HSP90 affects KCNH2, and NCIT:C17764
| 1
sparser
"For example, the reactive oxygen species (ROS) generated during hypoxia have been shown to inhibit protein folding and maturation by interfering with the interaction between hERG and the Hsp90 chaperone complex [ xref ]."
HSP90 affects HSPA, KCNH2, and chaperones
| 1
| 1
sparser
"Using biochemical and electrophysiological assays we show that the cytosolic chaperones Hsp70 and Hsp90 interact transiently with wild-type hERG."
HM5023507 affects KCNH2
| 1
HM5023507 inhibits KCNH2. 1 / 1
| 1
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"HM5023507 inhibited hERG K channel activity measured in an electrophysiological assay with IC 50 values ranging from 2.3 to 2.9 mumol/L."
HGS affects KCNH2
| 1
HGS inhibits KCNH2. 1 / 1
| 1
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"Hrs, Stam1, or Tsg101 ablation profoundly attenuated the rapid PM removal of wt hERG in ouabain- or digoxin treated cells (XREF_FIG)."
HERG-A422T affects KCNH2
| 1
HERG-A422T activates KCNH2. 1 / 1
| 1
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"Associated with LQT2, HERG-A422T produces trafficking defective HERG K + channels (K v 11.1) that decrease the rapidly activating delayed rectifier current (I Kr), which is normally responsible for the bulk of ventricular repolarization."
HCQ affects KCNH2
| 1
HCQ inhibits KCNH2. 1 / 1
| 1
eidos
"HCQ is known to block Kv11.1 ( HERG ) and can cause drug-induced LQT ."
HCN channel inhibitor affects KCNH2
| 1
HCN channel inhibitor activates KCNH2. 1 / 1
| 1
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"HERG potassium channel blockade by the HCN channel inhibitor bradycardic agent ivabradine."
HC-030031 affects KCNH2
| 1
HC-030031 inhibits KCNH2. 1 / 1
| 1
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"HC-030031 is selective for TRPA1 channels and does not inhibit TRPV1, TRPV3, TRPV4, hERG, or Na V 1.2 channel activity in the concentration range used for the current study (IC 50 for these channels> 10-20 muM) XREF_BIBR."
HA affects KCNH2
| 1
KCNH2 binds HA. 1 / 1
| 1
sparser
"The decision to use HA-hERG hERG was reinforced by the finding that HA-hERG tetramers have slightly elevated surface levels, with respect to total channel expression, in comparison with channels formed following co-expression of HA-hERG with wild type hERG; the inclusion of hERG yielded consistent surface levels irrespective of the ratio between the two constructs ( xref )."
H2 affects KCNH2, and KCNQ1
| 1
KCNH2 binds KCNQ1 and H2. 1 / 1
| 1
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"We have previously reported a physiologically relevant interaction between KCNQ1 (Q1) and KCNH2 (H2)."
Green tea flavonoid epigallocatechin-3-gallate affects KCNH2
| 1
Green tea flavonoid epigallocatechin-3-gallate inhibits KCNH2. 1 / 1
| 1
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"Green tea flavonoid epigallocatechin-3-gallate (EGCG) inhibits cardiac hERG potassium channels."
Gly-Gln affects KCNH2
| 1
Gly-Gln activates KCNH2. 1 / 1
| 1
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"Phosphatidylinositol4-phosphate 5-kinase prevents the decrease in the HERG potassium current induced by Gq protein coupled receptor stimulation."
Glucose affects KCNH2
| 1
| 1
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"High Glucose Represses hERG K+ Channel Expression through Trafficking Inhibition."
Ginseng saponins affects KCNH2
| 1
Ginseng saponins activates KCNH2. 1 / 1
| 1
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"Ginseng saponins enhance HERG currents, which could be in part a possible mechanism of the shortening cardiac action potential of ginseng saponins."
Gbeta76C affects KCNH2
| 1
| 1
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"In the present study, we found that a low concentration of GBE (0.005 mg/ml) increased hERG currents, but the high concentration of GBE (from 0.05 to 0.25 mg/ml) reduced hERG currents."
G_i affects KCNH2, and SCN5A
| 1
G_i binds SCN5A and KCNH2. 1 / 1
| 1
sparser
"The aim of this study was to determine if the cardiac channelopathy-associated mutations in SCN5A or KCNH2 are associated with GI symptom complexes."
GZ-793A affects KCNH2
| 1
GZ-793A inhibits KCNH2. 1 / 1
| 1
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"However, GZ-793A inhibited human hERG channels, suggesting cardiotoxicity and prohibiting clinical development."
GSK1702934A affects KCNH2
| 1
GSK1702934A activates KCNH2. 1 / 1
| 1
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"GSK1702934A (GSK-2934A) is a potent TRPC3/6 agonist and does not stimulate TRPV4, TRPA1, M1, M4, CaV1.2, hERG, NaV1.5, or CXCR5 receptors at concentrations < 10mumol/L."
GSK-2934A affects KCNH2
| 1
GSK-2934A activates KCNH2. 1 / 1
| 1
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"GSK1702934A (GSK-2934A) is a potent TRPC3/6 agonist and does not stimulate TRPV4, TRPA1, M1, M4, CaV1.2, hERG, NaV1.5, or CXCR5 receptors at concentrations < 10mumol/L."
GLYCAM1 affects KCNH2
| 1
| 1
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"The Src family kinase inhibitor PP2, but not the PTK-inactive analogue PP3, reversibly suppressed hERG channels, and the effect was significantly antagonized by the PTP inhibitor orthovanadate."
GFLX affects KCNH2
| 1
GFLX inhibits KCNH2. 1 / 1
| 1
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"The IC 50 value of GFLX induced hERG inhibition was reported to be 130 micromol/L (approximately 50 microg/ml) [XREF_BIBR], which is somewhat higher than the plasma GFLX concentrations showing QT/QTc prolongation (approximately 30 microg/ml)."
GAPDH affects KCNH2
| 1
GAPDH activates KCNH2-K311R. 1 / 1
| 1
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"Remarkably, constitutive expression from the GAPDH promoter of ERG1 (K311R) in are1Delta are2Delta cells led to a cold phenotype comparable to that observed in are1Delta are2Delta doa10Delta mutant (XREF_FIG)."
G965X affects KCNH2
| 1
G965X inhibits KCNH2. 1 / 1
| 1
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"Similarly, neither G965X nor R1014PfsX39 or V1038AfsX21, three other C-terminal deletions found in LQT2 patients, changed current kinetics, with only G965X decreasing current amplitudes (33% of WT hERG) XREF_BIBR."
G572R-hERG affects KCNH2
| 1
G572R-hERG inhibits KCNH2. 1 / 1
| 1
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"Furthermore, G572R-hERG causes a loss of function in hERG by a strong dominant negative effect on the WT-hERG channel."
FUT1 affects KCNH2
| 1
FUT1 activates KCNH2. 1 / 1
| 1
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"The Hsp70 family, including stress induced Hsp70 and constitutively expressed heat shock cognate protein (Hsc) 70, was shown to interact with the core glycosylated form of hERG XREF_BIBR, XREF_BIBR and increases the levels of mature form of hERG 27."
FSD1 affects KCNH2
| 1
FSD1 activates KCNH2. 1 / 1
| 1
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"MiR-1 overexpression also upregulated Kir2.1, Kv1.4, HERG and dihydropyridine receptors (VGCC; voltage gated calcium channels) while downregulating HCN4."
FLT1 affects KCNH2, PDGFRB, and VEGFA
| 1
| 1
sparser
"All the proteins were expressed in the samples, with statistically significant associations of VEGF-A with PDGFRβ and Flt1 and hERG1 with CA IX."
FLT1 affects Integrins, KCN, and KCNH2
| 1
| 1
sparser
"In acute myeloid leukemia cells, β1 integrin, VEGFR1 and hERG potassium channel form a macromolecular signaling complex that promotes cell migration and metastasis [ xref ]."
FLI1 affects KCNH2
| 1
| 1
sparser
"Constitutive expression of FLI1 and ERG1 is not associated with malignant transformation."
FIDAS affects KCNH2
| 1
KCNH2 binds FIDAS. 1 / 1
| 1
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"21 We utilized a [3 H]-dofetilide binding assay to evaluate FIDAS agent interaction with hERG."
FEBS 16966 FEBS Letters 385 affects KCNH2
| 1
FEBS 16966 FEBS Letters 385 inhibits KCNH2. 1 / 1
| 1
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"FEBS 16966 FEBS Letters 385 (1996) 77-80 Blockade of HERG channels expressed in Xenopus oocytes by the histamine receptor antagonists terfenadine and astemizole H. Suessbrich, S. Waldegger, F. Lang, A.E. Busch * Physiologisches Institut I, Eberhard-Karls- Dniversit Tingen, Gmelinstr."
FADH2 affects KCNH2
| 1
FADH2 activates KCNH2. 1 / 1
| 1
reach
"Second, with more than 15,000 references of FA in drug discovery as of April 2015, instead of reviewing numerous publications, the authors illustrate the application of steady-state FA to the FDA accepted hERG assay."
F508del-CFTR correctors affects KCNH2
| 1
F508del-CFTR correctors activates KCNH2-G601S. 1 / 1
| 1
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"We tested whether F508del-CFTR correctors could restore hERG G601S trafficking and function."
Extracellular K affects KCNH2
| 1
Extracellular K inhibits KCNH2. 1 / 1
| 1
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"Extracellular K + -depletion and high salt or acidity also triggered Ub dependent degradation of the wild-type HERG channel and LDL receptor, respectively, presumably by conformational destabilization [XREF_BIBR, XREF_BIBR]."
External H+ affects KCNH2
| 1
External H+ inhibits KCNH2. 1 / 1
| 1
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"External H+ is known to inhibit HERG current by shifting V (1/2) to the right and decreasing I (tail, max)."
Epsilon affects KCNH2
| 1
| 1
sparser
"It has been reported that the PPARδ pathway targets protein 14-3-3 epsilon, which in turn interacts with HERG to stabilize the PKA-phosphorylated state of the channel by shielding phosphates from degradation [ xref ]."
EZH2 affects KCNH2
| 1
EZH2 increases the amount of KCNH2. 1 / 1
| 1
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"XREF_BIBR In particular, EZH2 mediates the expression of the tumor suppressor ERG1 via SYT-SSX in SS."
ETV6 affects KCNH2
| 1
ETV6 inhibits KCNH2. 1 / 1
| 1
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"TEL mediated prolongation of AP was attenuated in KCNH2 siRNA transfected HL-1 cells."
ESR1 affects KCNH2
| 1
| 1
sparser
"Moreover, hERG1 scoring was significantly associated with ER expression, with higher hERG1 scoring in ER-positive samples (p = 0.008), and inversely associated with Ki67 (higher hERG1 scoring in samples with Ki67 index lower to 15%, p = 0.038)."
ERK affects KCNH2
| 1
ERK activates KCNH2. 1 / 1
| 1
reach
"Specifically, we previously showed in striatal cultures XREF_BIBR XREF_BIBR XREF_BIBR that cell surface mGluR5 stimulates CAMKIV, p-CREB and c-jun, while intracellular mGluR5 phosphorylates ERK1/2 and Elk-1, and enhances c-fos, erg-1 and Arc and Arg3.1."
ER affects KCNE2, and KCNH2
| 1
KCNE2 binds KCNH2 and ER. 1 / 1
| 1
sparser
"BFA treatment also resulted in enhanced KCNE2-ER binding to HERG but to a much lower degree than that seen with wild type KCNE2 ( xref )."
ER affects KCNE1, KCNE2, and KCNH2
| 1
KCNE1 binds KCNE2, KCNH2, and ER. 1 / 1
| 1
sparser
"The overall degree of association of HERG with KCNE1-ER and KCNE2-ER was comparable however, the increase over wild type was greater for KCNE2 than for KCNE1."
ELK1 affects KCNH2
| 1
ELK1 activates KCNH2. 1 / 1
| 1
reach
"Specifically, we previously showed in striatal cultures XREF_BIBR XREF_BIBR XREF_BIBR that cell surface mGluR5 stimulates CAMKIV, p-CREB and c-jun, while intracellular mGluR5 phosphorylates ERK1/2 and Elk-1, and enhances c-fos, erg-1 and Arc and Arg3.1."
ELANE affects KCNH2
| 1
| 1
sparser
"MS analysis revealed the formation of 4-HNE-hERG adduct on specific amino acid residues, including C276, K595, H70, and H687."
EGFR inhibitor affects KCNH2
| 1
EGFR inhibitor activates KCNH2. 1 / 1
| 1
reach
"The hERG current was decreased by an EGFR inhibitor (AG556) and a broad-spectrum inhibitor of Src family tyrosine kinases (PP2) XREF_BIBR."
EGF affects KCNH2
| 1
EGF activates KCNH2. 1 / 1
| 1
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"ERG1.2 is a cell-cycle-regulated gene, and both ERG1.2 and STAG1 are induced by EGF and other growth factors at the transcript and protein levels."
EDAR affects KCNH2
| 1
EDAR inhibits KCNH2. 1 / 1
| 1
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"This analysis shows that enhancements of endogenous HF oscillations in HR were also found in beagle dogs with dofetilide and with other hERG blockers such as cisapride, haloperidol, risperidone, DL sotalol, terfenadine and thioridazine."
| 1
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"We also observed inhibitor specific effects : FGFR inhibitor caused upregulation of Gata3 and Gata2 and downregulation of Myc; MEK inhibitor caused upregulation of Gbp3 and downregulation of Erg1 and Nr4a3; and GSK inhibitor caused upregulation of T, Nkx1-2, Msx1, and Evx1 and downregulation of Tcfec and Rfx4."
E-4031 K affects KCNH2
| 1
E-4031 K inhibits KCNH2. 1 / 1
| 1
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"In CHO cells, HERG channels were strongly blocked by E-4031 K i = 8.8 +/- 0.8 nM; again, channels formed with hMiRP1 were ~ 2-fold more sensitive (K i = 4.6 +/- 0.6 nM; n = 6 cells)."
Dofe54 affects KCNH2
| 1
Dofe54 inhibits KCNH2. 1 / 1
| 1
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"HERG current inhibition by Dofe54 is illustrated in Figure XREF_FIG A."
Dofe45 affects KCNH2
| 1
Dofe45 inhibits KCNH2. 1 / 1
| 1
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"The ' selective inhibition ' of the hERG channels by Dofe45 would induce a substantial prolongation of the AP."
Dll affects KCNH2
| 1
Dll inhibits KCNH2. 1 / 1
| 1
reach
"Danielsson BR, Lansdell K, Patmore L, Tomson T. Phenytoin and phenobarbital inhibit human HERG potassium channels."
DeltaAT mutation affects KCNH2
| 1
DeltaAT mutation inhibits KCNH2. 1 / 1
| 1
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"The DeltaAT mutation may decrease the number of functional hERG channels by impairing the posttranscriptional and posttranslational processing of the mutant product."
DRD affects KCNH2
| 1
DRD inhibits KCNH2. 1 / 1
| 1
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"This study establishes that in conscious dogs, the selective dopamine receptor agonist PNU-142774E has fewer cardiovascular and emetic effects than ropinirole and apomorphine and supports prior in vitro findings that ropinirole and apomorphine but not the PNU-142774E imidazoquinolin analog sumanirole reduces the delayed rectifier current in HERG transfected cells."
DPP6 affects KCNH2
| 1
DPP6 activates KCNH2. 1 / 1
| 1
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"3.7 Effect of KChIP2 and DPP6 in the NS3623 mediated I hERG activation."
DNM2 affects KCNH2
| 1
DNM2 activates KCNH2. 1 / 1
| 1
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"In addition, knockdown of dynamin 2 using siRNA transfection significantly impeded hERG internalization and degradation under low K (+) (o) conditions."
DNAJB1 affects KCNH2
| 1
DNAJB1 inhibits KCNH2. 1 / 1
| 1
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"Hsp40 chaperones promote degradation of the HERG potassium channel."
DNAJA4 affects KCNH2
| 1
DNAJA4 inhibits KCNH2. 1 / 1
| 1
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"Our observations are thus similar to those described by Walker and colleagues, who reported that DnaJA1, DnaJA2 and DnaJA4 reduced hERG channel maturation, whereas over-expression of Hsc70 alone had no effect on maturation events XREF_BIBR."
DISO affects KCNH2
| 1
DISO inhibits KCNH2. 1 / 1
| 1
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"We conclude (a) that DISO inhibits HERG encoded potassium channels at clinically relevant concentrations and (b) that this action may constitute the molecular basis for acquired LQTS associated with this drug."
DEF affects KCNH2
| 1
DEF inhibits KCNH2. 1 / 1
| 1
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"Besides Kv1.3 channel, plectasin could less inhibit Kv1.1, Kv1.2, IKCa, SKCa3, hERG and KCNQ channels at the concentration of 1 muMu."
DBP affects KCNH2
| 1
KCNH2 binds DBP. 1 / 1
| 1
sparser
"There were statistically significant interactions between KCNH2 (1956, C>T) polymorphism and DBP change (P = 0.010), MAP change (P = 0.014) on azelnidipine or nitrendipine therapy patients at the end of 6 weeks."
DA-8031 affects KCNH2
| 1
DA-8031 inhibits KCNH2. 1 / 1
| 1
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"XREF_BIBR In a preclinical study, a high dose of DA-8031 induced hERG current inhibition and QT prolongation."
D456 affects KCNH2, and magnesium atom
| 1
Magnesium atom binds KCNH2 and D456. 1 / 1
| 1
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"In contrast, Mg 2+ binding to hERG1 was largely determined by D456, with a lesser contribution from D460 and D509."
Cyclovirobuxine D affects KCNH2
| 1
Cyclovirobuxine D inhibits KCNH2. 1 / 1
| 1
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"Cyclovirobuxine D inhibits the currents of HERG potassium channels stably expressed in HEK293 cells."
Cterm-MinK affects KCNH2
| 1
Cterm-MinK activates KCNH2. 1 / 1
| 1
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"MiRP1 and Cterm-MinK modulated HERG much like wild-type MiRP1 (XREF_FIG C, right), suggesting that our chimera is indeed expressed and that it can not modulate KvLQT1."
Compound 3 affects KCNH2
| 1
Compound 3 activates KCNH2. 1 / 1
| 1
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"It was shown that E4031 (Compound 3, XREF_FIG), an antagonist of hERG channels, promoted the trafficking of hERG channels harboring the N470D mutation."
Clathrin affects KCNH2
| 1
| 1
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"A reduction in extracellular K + concentration has been shown to induce endocytic degradation of the cell surface hERG channel protein, which is mediated by caveolin, but not by clathrin."
Class III affects KCNH2
| 1
Class III inhibits KCNH2. 1 / 1
| 1
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"Class III antiarrhythmic drugs block HERG, a human cardiac delayed rectifier K+ channel."
Changrolin affects KCNH2
| 1
Changrolin inhibits KCNH2. 1 / 1
| 1
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"Changrolin inhibited hERG channels in a concentration dependent and reversible manner (IC (50) = 18.23 mumol/L, 95% CI : 9.27-35.9 mumol/L; Hill coefficient = -0.9446)."
Certain mutant proteins affects KCNH2
| 1
Certain mutant proteins activates KCNH2. 1 / 1
| 1
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"Certain mutant proteins cause dominant negative suppression of WT-hERG."
Cavalli-2 affects KCNH2
| 1
KCNH2 binds Cavalli-2. 1 / 1
| 1
reach
"Cavalli-2 interaction with WT hERG and inactivation deficient mutants."
CYP450 affects KCNH2
| 1
KCNH2 binds CYP450. 1 / 1
| 1
reach
"Machine learning algorithms for the prediction of hERG and CYP450 binding in drug development."
CYP3A4 affects KCNH2
| 1
| 1
sparser
"In conclusion, the progesterone metabolites formed via CYP3A cause inhibitory effects on hERG channels and predict QTcI intervals in healthy women pretreated with progesterone."
CYP3A inhibitor affects KCNH2
| 1
CYP3A inhibitor activates KCNH2. 1 / 1
| 1
reach
"Verapamil was discontinued and diltiazem, a CYP3A inhibitor that weakly blocks hERG, was started."
CYP2C9 affects KCNH2
| 1
| 1
sparser
"However, the compound displayed greater promiscuity by strongly binding to hERG and CYP2C9."
CYP affects KCNH2
| 1
| 1
sparser
"This review summarizes the state of modeling hERG and CYP binding towards this goal since 2003 using ML algorithms."
CXCR4 affects FLT1, ITGB1BP1, Integrins, and KCNH2
| 1
sparser
"Importantly, they demonstrated that upon β1 integrin stimulation, hERG forms signaling macro-complexes with β1-integrin, the VEGF receptor Flt-1 or the cytokine receptor CXCR4 in lipid rafts."
CXB affects KCNH2
| 1
CXB inhibits KCNH2. 1 / 1
| 1
reach
"For example, the voltage gated sodium channel in rat retinal neurons XREF_BIBR and dorsal root ganglia (DRG) neurons XREF_BIBR, XREF_BIBR, the L-type calcium channel in rat pheochromocytoma (PC12) cells XREF_BIBR and A7r5 rat aortic smooth muscle cells XREF_BIBR, Kv2.1 channels expressed in HEK293 cells XREF_BIBR, cardiac Kv1.5, Kv4.3 and Kv7.1 channels in guinea pig cardiomyocytes XREF_BIBR and human eag related gene (HERG) potassium channels XREF_BIBR were all reported to be inhibited by CXB."
CUL1 affects KCNH2
1 |
1 |
biogrid
No evidence text available
CTSG affects HSP90, and KCNH2
| 1
HSP90 binds CTSG and KCNH2. 1 / 1
| 1
sparser
"More importantly, addition of MnTMPyP during hypoxia restored Hsp90 interaction with cg form of hERG (lane 3 vs lane 4, xref )."
CTSD affects KCNH2
| 1
CTSD inhibits KCNH2. 1 / 1
| 1
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"Of particular concern for this target is inhibition of hERG, 8 as well as related aspartyl proteases including cathepsin D (CatD), which has confounded early generations of BACE1 inhibitors."
CREB affects KCNH2
| 1
CREB increases the amount of KCNH2. 1 / 1
| 1
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"Since the HERG promoter also shows a response to CREB, the increase in QT interval seen in obese humans may be the result of reduced cardiac CREB, causing a decrease in HERG expression and impaired repolarization in the ventricles."
CRC affects KCNH2
| 1
| 1
sparser
"In conclusion, the present study demonstrated that HERG1 expression was notably associated with CRC and was absent in healthy control samples whereas the expression of CEA, CK19 and CK20 varied significantly in tumors and control tissues."
CPT-cAMP affects KCNH2
| 1
CPT-cAMP inhibits KCNH2. 1 / 1
| 1
reach
"CPT-cAMP reduced HERG current by about 40% at all potentials."
CPP-115 affects KCNH2
| 1
CPP-115 inhibits KCNH2. 1 / 1
| 1
reach
"CPP-115 inhibited hERG current by (mean +/- SEM) 1.1 +/- 0.2% at 10 muM (n = 3) and 1.5 +/- 0.2% at 300 muM (n = 3) versus 0.8 +/- 0.3% (n = 3) in control."
CHRN affects KCNH2
| 1
| 1
sparser
"In addition, other α7 nAChR agonists that are not associated with the negative effects on hERG channels in the heart were also found to prevent the loss of RGCs under glaucoma-like conditions, though to a lesser degree than PNU-282987 (Birkholz et al., 2016)."
CHK1 inhibitor affects KCNH2
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CHK1 inhibitor activates KCNH2. 1 / 1
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"b Abrogation of etoposide induced G2 checkpoint arrest in HT29 human colon cancer c Ratio of cytotoxicity GI50 (measured by SRB assay) to IC50 for CHK1 mediated abrogati d Potentiation by CHK1 inhibitor of gemcitabine cytotoxicity in HT29 or SW620 huma e Inhibition of hERG ion current in HEK cells overexpressing hERG ion channel (Patch f 7-HS : 7-Hydroxystaurosporine."
CH affects KCNH2
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"ER retention of hERG 125kDa form by CH was due to defective trafficking and was rescued by exposing cells to hypoxia at low temperatures or treatment with E-4031, a hERG channel blocker."
CDIPT affects KCNH2
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CDIPT inhibits KCNH2. 1 / 1
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"Although PIs block in vitro hERG current, they are not independently associated with QTc interval prolongation."
CCT365623 affects KCNH2
| 1
CCT365623 inhibits KCNH2. 1 / 1
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"First, we show that CCT365623 displays good stability in mouse liver microsomes and does not inhibit the cardiac potassium channel hERG."
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"The human inward rectifying voltage-gated HERG K + channel (Trudeau et al., xref ) interacts with caveolin-1 and reduces its activity when caveolin is up-regulated (Lin et al., xref )."
CAV1 affects HCN4, KCNH2, and KCNJ2
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CAV1 binds HCN4, KCNH2, and KCNJ2. 1 / 1
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"Together with the findings that caveolin-1 interacts with potassium channels Kir2.1, KCNH2, and HCN4 and sodium channels Nav1.5 and Nav1.8, CAV1 becomes a strong candidate susceptibility gene for AF across different ethnic populations."
CAV affects KCNH2
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CAV activates KCNH2. 1 / 1
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"A reduction in extracellular K + concentration has been shown to induce endocytic degradation of the cell surface hERG channel protein, which is mediated by caveolin, but not by clathrin."
CAT affects KCNH2
| 1
CAT inhibits KCNH2. 1 / 1
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"In addition, the two iron chelators desferrioxamine (1 mm) and o-phenanthroline (0.2 mm) significantly inhibited hERG1 outward K (+) currents and prevented hERG1 inhibition induced by the ROS scavenging enzyme catalase (1000 units/ml)."
CASQ2 affects KCNH2
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CASQ2 activates KCNH2. 1 / 1
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"As a result, CASQ2 wild type and CASQ2-mutants modulated hERG functions differently."
CASP3 affects KCNH2, and VEGF
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VEGF binds CASP3 and KCNH2. 1 / 1
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"However, these results are still tentative and imperfect, and the question how hERG mRNA or hERG protein physiologically interacts with VEGF or caspase-3 is unanswered."
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"Coimmunoprecipitation assays showed that Calnexin only interacted with the ER-residing form of hERG proteins ( xref ), suggesting that Calnexin interacts with hERG proteins in the ER."
CALR affects CANX, KCNH2, and NCIT:C17764
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"Furthermore, the interaction between mutant hERG proteins and chaperone proteins, Calnexin and Calreticulin, play crucial roles in these processes."
CALR affects CANX, and KCNH2
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CALR binds CANX and KCNH2. 1 / 1
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"As shown in xref , treatment with lactacystin or ALLN but not leupeptin (a lysosome inhibitor) results in an increase in the levels of core-glycosylated, immature form of hERG, Calnexin and Calreticulin."
CACNA1C affects COMT, DRD2, GAD1, GRM3, KCNH2, MTHFR, and RGS4
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"Illustrative of genetic vulnerability maps of brain function based on imaging genetics approaches, Rasetti et al reviewed neuroimaging intermediate phenotypes of schizophrenia and the gene variants associated with them, catalogued by cognitive task. xref For example, working memory tasks have revealed abnormal engagement of: dorsolateral prefrontal cortex associated with CACNA1C, COMT, GAD1, GRM3, DRD2, KCNH2, MTHFR, and RGS4; ventrolateral prefrontal cortex associated with COMT, PRODH, and RGS4; thalamus and hippocampus associated with NRG1, DAOA/G72, and DISCI; and parietal lobe associated with PRODH."
C6-CF affects KCNH2
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C6-CF activates KCNH2. 1 / 1
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"The C6-CF (3) group decreased hERG inhibition, probably as a result of decreased amine basicity at C2/C4."
C-type affects KCNH2
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C-type inhibits KCNH2. 1 / 1
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"It has been well established that C-type inactivation of hERG channel is retarded by external QA blockers but not by internal QA blockers [9]."
Bufalin affects KCNH2
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Bufalin inhibits KCNH2. 1 / 1
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"Bufalin, a bufanolide steroid from the parotoid glands of the Chinese toad, suppresses hERG K"
BmTx3 affects KCNH2
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BmTx3 inhibits KCNH2. 1 / 1
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"An exception to the rule is BmTx3 which belongs to subfamily alpha-KTx15 and can block hERG channels."
Basic affects KCNH2
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Basic activates KCNH2. 1 / 1
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"DNA coding human ERG1 (KCNH2, hERG) was synthesized by Bio Basic Inc.."
Bacterial Topoisomerase Inhibitors affects KCNH2
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Bacterial Topoisomerase Inhibitors inhibits KCNH2. 1 / 1
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"1,3-Dioxane-linked Bacterial Topoisomerase Inhibitors with Enhanced Antibacterial Activity and Reduced hERG Inhibition."
BIM-I affects KCNH2
| 1
BIM-I inhibits KCNH2. 1 / 1
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"Of interest, the non selective PKC inhibitor, BIM-I blocks hERG currents in a PKC independent manner."
BEA affects KCNH2
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BEA inhibits KCNH2. 1 / 1
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"The hERG test of BEA showed that 0.3 microM and higher concentration of BEA could inhibit the hERG potassium channel in a dose dependent manner; the IC 50 of BEA is about 2.55 microM (XREF_FIG), which is considered controllable cardiac risk."
BDNF affects COMT, GRM3, and KCNH2
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BDNF binds COMT, GRM3, and KCNH2. 1 / 1
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"Cognitive control tasks (designed to challenge executive function of goal-directed behavior in the presence of conflict) have identified abnormal engagement of the anterior cingulate cortex associated with COMT,DRD2, and MAOA; of the dorsolateral prefrontal cortex (DLPFC) associated with DTNBPl,DRD2,MAOA, COMT: and of the parietal cortex associated with DRD2, andMAOA. xref Memory encoding tasks recently identified abnormal engagement of hippocampus parahlppocampus region xref and association of the hippocampus with BDNF, COMT, DISCI, GRM3, and KCNH2."
BAPTA-AM affects KCNH2
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BAPTA-AM inhibits KCNH2. 1 / 1
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"The present study found that BAPTA-AM rapidly and reversibly suppressed human ether a-go-go-related gene (hERG or Kv11.1) K (+) current, human Kv1.3 and human Kv1.5 channel currents stably expressed in HEK 293 cells, and the effects were not related to Ca (2+) chelation."
BAG2 affects KCNH2
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biogrid
No evidence text available
BAG1 affects KCNH2
| 1
BAG1 inhibits KCNH2. 1 / 1
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"Here, we demonstrate that the Hsp70 nucleotide exchange factor Bag1 promotes hERG degradation by the ubiquitin-proteasome system at the endoplasmic reticulum to regulate hERG levels and channel activity."
Arf6-T27N-eGFP affects KCNH2
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Arf6-T27N-eGFP activates KCNH2. 1 / 1
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"Arf6-T27N-eGFP increased hERG current density in HEK-MSR cells by 82.6 +/- 30.5% (XREF_FIG)."
Apocyanin affects KCNH2
| 1
Apocyanin inhibits KCNH2. 1 / 1
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"Apocyanin, which inhibits NOX by preventing the assembly of subunits of the oxidase complex, had no effect on hERG expression under normoxic conditions and, like DPI, did not prevent down-regulation of hERG by hypoxia.To examine the role of ROS generated by mitochondria on hERG expression, the effects of hypoxia were examined in 143Brho0 cells, which were devoid of mitochondrial DNA, and therefore lacked a functional ETC.."
AmmTx3 affects KCNH2
| 1
AmmTx3 inhibits KCNH2. 1 / 1
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"AmmTx3 induced a hERG channel block with no alteration of the gating kinetics."
Amin affects KCNH2
| 1
Amin activates KCNH2-A558P. 1 / 1
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"XREF_BIBR Amin et al. studied the mechanism of fever induced QT prolongation and ventricular arrhythmias in LQT2 patients by heterologously expressing the A558P HERG missense mutation in HEK-293 cells."
AZA3 affects KCNH2
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KCNH2 binds AZA3. 1 / 1
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"AZA1, AZA2, and AZA3 bind to hERG channels."
AZA affects KCNH2
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AZA inhibits KCNH2. 1 / 1
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"In order to evaluate the functional implications of AZA induced hERG blockage and other cardiotoxic effects not related to hERG, AZA-2 was selected due to its higher toxicity and higher hERG blocking potency."
AVR-25 affects KCNH2
| 1
AVR-25 inhibits KCNH2. 1 / 1
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"AVR-25 did not inhibit the hERG channel and IC 50 was> 300microM, thus confirming no adverse cardiac effects."
AVN-101 affects KCNH2
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AVN-101 inhibits KCNH2. 1 / 1
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"It was shown that both AVN-101 and M1 can block the hERG channel with IC 50 of 0.58 muM and 1.63 muM, respectively."
ATPase inhibitor affects KCNH2
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ATPase inhibitor inhibits KCNH2. 1 / 1
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"Interestingly, Delisle et al reported that the sarco and endoplasmic reticulum ATPase inhibitor thapsigargin can rescue trafficking of mutated hERG channels possibly through altered Ca 2+ -dependent chaperone activity in the ER XREF_BIBR."
ATP1B1 affects CACNA1C, CAV3, KCNH2, and KCNQ1
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"We showed that ATP1B1 interacts with KCNH2, CACNA1C, KCNQ1and CAV3."
AT1 receptors affects KCNH2
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AT1 receptors inhibits KCNH2. 1 / 1
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"The results indicate that sustained stimulation of AT1 receptors by Ang II reduces the mature hERG channel protein via accelerating channel proteasomal degradation involving the PKC pathway."
AT 1 receptor affects KCNH2
| 1
AT 1 receptor inhibits KCNH2. 1 / 1
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"Future studies are necessary to determine which isoform of PKC is involved with sustained stimulation of AT 1 receptor on mature hERG channel protein.In summary, our data demonstrate that the sustained stimulation of AT 1 receptor by Ang II reduces the mature hERG channel protein through degradation by PKC activation."
ARNT affects KCNH2
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sparser
"This paper describes one of several strategies incorporated to limit hERG binding via modifications of a terminal aryl group in an otherwise promising bicyclohexyl urea series."
ARHGAP6 affects KCNH2
| 1
ARHGAP6 decreases the amount of KCNH2. 1 / 1
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"Biochemical measurements of cell-surface associated HERG revealed that ARHGAP6 reduced membrane expression of HERG by 35%, which correlates well with the reduction in current."
AR45 receptors affects KCNH2
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AR45 receptors activates KCNH2. 1 / 1
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"In conclusion, these data provide evidence that stimulation of AR45 receptors by androgens up-regulates HERG K+ channel abundance and activity mainly through stabilizing HERG protein in an ERK1/2 dependent mechanism, and suggest a mechanism to explain the sex difference in the long QT syndrome."
APETx4 affects KCNH2
| 1
APETx4 inhibits KCNH2. 1 / 1
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"A 300-fold concentration of APETx4 is not able to inhibit the inward hERG current."
APETx1 affects KCNH2
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APETx1 inhibits KCNH2. 1 / 1
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"APETx1 inhibits HERG currents in a heterologous system with an IC50 value of 34 nM by modifying the voltage dependence of the channel gating."
AP14145 affects KCNH2
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AP14145 inhibits KCNH2. 1 / 1
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"AP14145 inhibited hERG (K V 11.1) with an IC 50 of 71.8 +/-0.5 micromol/L and K ir 3.1/K ir 3.4 (I KACh) with an IC 50 of 9.3 +/-0.4 micromol/L and did not produce any significant effects on K V 1.5 (I Kur), K V 7.1/KCNE1 (I Ks), K V 4.3/KChiP2 (I to), and K ir 2.1 (I K1) in 30 micromol/L or on Na V 1.5 (15 micromol/L; I Na; Figure XREF_FIG, middle)."
AP1 affects ERG, and KCNH2
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AP1 binds ERG and KCNH2. 1 / 1
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"C is -elements contributing to this inducibility were mapped to the proximal promoter region and these elements were shown to interact with transcription factors Erg-1, Erg-3, ATF-3/CREB and AP-1 upon stimulation ( xref )."
ANKRD1 affects KCNH2
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ANKRD1 activates KCNH2. 1 / 1
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"We noted that Ankrd1 overexpression significantly upregulated erg-1 (XREF_FIG D)."
AMO-133b affects KCNH2
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AMO-133b activates KCNH2. 1 / 1
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"The transfection of anti-miR-133b oligonucleotide (AMO-133b) remarkably prevented the decrease of hERG protein by 5muM ATO treatment for 24h in U251 cells, whereas anti-miR-34a oligonucleotide (AMO-34a) did not exhibit recuperated effect."
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"The Romano-Ward syndrome, which occurs commonly in an autosomal dominant fashion, encompasses heterozygous mutations associated with KCNQ1 (LQT1), KCNH2 (LQT2), SCN5A (LQT3), KCNE1 (LQT5), KCNE2 (LQT6), CAV3 (LQT9), SCN4B (LQT10), AKAP9 (LQT11), SNTA1 (LQT12) and KCNJ5 (LQT13)."
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"Compound C significantly enhanced whereas AICAR tended to inhibit hERG currents in RD rhabdomyosarcoma cells."
AGTR1 affects KCNH2
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AGTR1 inhibits KCNH2. 1 / 1
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"The results indicate that sustained stimulation of AT1 receptors by Ang II reduces the mature hERG channel protein via accelerating channel proteasomal degradation involving the PKC pathway."
ADRB1 affects KCNH2
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Catalytically active ADRB1 activates KCNH2. 1 / 1
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"Previous studies have revealed that hERG channel activation is modulated by activation of the beta-adrenergic system."
ADRB affects KCNH2, and p14_3_3
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"Our results suggest that the dynamic association of 14-3-3 proteins to both beta(1)AR and Kv11.1 channels is involved in the adrenergic modulation of this critical regulator of cardiac repolarization and refractoriness."
ACVR1C affects KCNH2
| 1
ACVR1C increases the amount of KCNH2. 1 / 1
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"mRNA levels of KCNH2 (Erg) and KCNQ1 (Kv7.1), the pore forming subunit for I Kr and I Ks respectively, were moderately increased by 20% in Alk7 -/- mice relative to controls (XREF_FIG)."
ACO affects KCNH2
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ACO inhibits KCNH2. 1 / 1
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"ACO has also been found capable of blocking the Kv1.5 channels that mediate the outward ultra-rapidly activating delayed rectifier K + current (I Kur ) in neonatal rat ventricular myocytes [ xref , xref ] while studies also demonstrated that ACO inhibited hERG in Xenopus laevis oocytes [ xref ] and HEK293 cells [ xref ]."
ABCG2 affects KCNH2
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ABCG2 inhibits KCNH2. 1 / 1
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"In additional experiments, we also show that hERG blockade in HEK 293 cells was modulated by coexpression of efflux [breast cancer resistance protein (BCRP), multidrug resistance gene (MDR1)] and influx [organic anion transporting polypeptide (OATP) 2B1] transporters involved in the disposition and cardiac distribution of the drug."
ABCB1 affects KCNH2
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ABCB1 inhibits KCNH2. 1 / 1
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"Influence of the G2677T and C3435T haplotype of MDR1 on P-glycoprotein trafficking and ibutilide induced block of HERG."
ABCA4 affects KCNH2
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ABCA4 inhibits KCNH2. 1 / 1
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"As IC 50 values for chloroquine inhibition of both Kir2.1 and hERG seen under our conditions (and cf xref ) fall within this clinical range, it seems likely that inhibition of both these channel types may contribute to observed QT C interval prolongation."
A-kinase affects KCNH2
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A-kinase activates KCNH2. 1 / 1
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"A-kinase anchoring protein targeting of protein kinase A and regulation of HERG channels."
9-ING-41 affects KCNH2
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9-ING-41 inhibits KCNH2. 1 / 1
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"The IC 50 value for hERG inhibition (patch-clamp) by 9-ING-41 was found to be 21 muM, indicating a low potential for cardiac toxicity."
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"The Human Ether-a-go-go-Related Gene (HERG) K + channel has been implicated in this gender bias, and DHT mediated stabilization of HERG protein was observed in cells transfected with AR45 but not full-length AR."
5-HT4 receptor affects KCNH2
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5-HT4 receptor inhibits KCNH2. 1 / 1
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"Cisapride is a serotonin 5-HT4 receptor agonist that has been reported to block the hERG potassium channel."
3D affects KCNH2
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"All models delineated similar 3D hERG binding features, however, small deviations of about ~ 0.4 A were observed between important hotspots of molecular interaction fields (MIFs) between solvated and non solvated hERG models."
1b affects KCNH2
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1b activates KCNH2. 1 / 1
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"If hERG 1a/1b heteromers represent a significant fraction of channels contributing to I Kr, down-regulation of 1b would enhance sensitivity to hERG blockers up to four-fold and increase the risk for arrhythmia by having a predominant population of more drug sensitive hERG 1a channels rather than the relatively less sensitive hERG 1a/1b channels."
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"Imidazole containing H3-receptor inverse agonists inhibit not only cytochrome P450 but also hERG potassium channels (encoded by the human ether-a-go-go-related gene)."
18-MC affects KCNH2
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18-MC inhibits KCNH2. 1 / 1
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"We found that, similar to ibogaine, 18-MC inhibits hERG and hNa v 1.5 channels heterologously expressed in TSA-201 cells."
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"In a concentration dependent manner (10 (-9) to 10 (-6) M for 24 h), 5alpha-dihydrotestosterone (5alpha-DHT) increased HERG protein abundance in HEK293 cells stably expressing HERG in the presence of coexpressed cardiac androgen receptor (AR) variant [N-terminal truncated isoform of AR (AR45)]."
10muM BIRB0796 affects KCNH2
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10muM BIRB0796 inhibits KCNH2. 1 / 1
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"In addition, 10muM BIRB0796 inhibited five GPCRs and two of seven Cardiac Ion Channels, hERG, and Kv1.5, by> = 50%."
10muM affects KCNH2
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10muM increases the amount of KCNH2. 1 / 1
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"As shown in XREF_FIG, 10muM E4031 as well as 3muM pilsicainide increased WT-hERG expression levels, as expected."
10e affects KCNH2, and dofetilide
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Dofetilide binds KCNH2 and 10e. 1 / 1
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"10e blocks hERG channel current in electrophysiological patch clamp experiments, and computational docking experiments predict that the dofetilide core of 10e binds hERG channel in a conformation similar to that previously predicted for 1."
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"DTT treatment does not induce any significant changes in the kinetics or tail I-V relationship of WT HERG, confirming that the native cysteine side chains in the HERG channel do not engage in disulfide formation."
-R259C affects KCNH2
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KCNH2 binds -R259C. 1 / 1
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"Consistent with this result, FRET experiments demonstrated that both KCNQ1-WT and -R259C interacted with hERG in the cytosol and on the plasma membrane; however, the interaction between KCNQ1-T587M and hERG was observed only in the cytosol, and hERG proteins were seldom transported to the cell membrane, suggesting that the KCNQ1 T587M mutation impaired the trafficking of hERG to the cell membrane."
(S)-naringenin affects F656, and KCNH2
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(S)-naringenin binds KCNH2 and F656. 1 / 1
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"Naringenin binding to HERG required aromatic residue F656 in the putative pore binding site."
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"For example, (S) -2,3-epoxysqualene and 5alpha-cholesta-8,24-dien-3-one specifically associated only with Erg1 (XREF_FIG), whereas lanosterol, ergosterol and episterol consistently co-purified with 5, 5 and 3 Erg proteins, respectively, above the control (XREF_TABLE)."
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"Selective noradrenaline reuptake inhibitor atomoxetine directly blocks hERG currents."
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"Taken together, 4-HNE 100S and 4-HNE 10L suppressed I hERG via functional inhibition and downregulation of membrane expression of hERG, respectively."
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"This study assesses whether there are sex differences in the ECG changes induced by four different hERG potassium channel blocking drugs."
(-)-P7C3-S243 affects KCNH2
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(-)-P7C3-S243 inhibits KCNH2. 1 / 1
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"Neither P7C3-A20 nor (-)-P7C3-S243 inhibits the hERG channel or shows toxicity towards cultured human cell lines (IC 50> mu10 M)."
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"Vitamin E restored the depressed I (Kr) and HERG by its antioxidant actions which likely underlie its beneficial effects on diabetic QT prolongation and the associated arrhythmias."